Uyazi ukuba sonke sinezintso ezimbini, enye kwicala ngalinye lomqolo wethu? Ezi zifana nezihluzo ezimbini emzimbeni wethu. Umsebenzi wazo ophambili kukucoca igazi nokususa inkunkuma njengomchamo. Nangona kunjalo, abanye abantu bazalwa benezintso ezimbini ezingahlukananga, kodwa zidibene ezantsi, njengesihlangu sehashe. Yiyo loo nto sizibiza ngokuba yi "Horseshoe Kidney" kunyango. Musa ukoyika xa usiva eli gama. Oku akuyongozi njengoko ucinga. Kodwa kubaluleke kakhulu ukuba uqaphele oku.
Ngamafutshane, yintoni le Horseshoe Kidney?
Le yimeko ekhoyo xa umntwana ezalwa. Kwizonyango, ezi zinto sizibiza ngokuba "yi-congenital anomaly." Ngamafutshane, yinto eyenzekayo ngelixa umntwana esakhula esibelekweni.
Cinga ngale ndlela. Xa umntwana eqala ukukhula esibelekweni, izintso ezimbini zokuqala zenzeka ngaphantsi kakhulu esiswini, kwindawo ye-pelvic. Emva koko, njengoko umntwana ekhula, ezi zintso zimbini zihamba kancinci kancinci ziye kwiindawo zazo ezifanelekileyo kumacala omabini omqolo.
Nangona kunjalo, kwenzeka into eyahlukileyo kumntu onesifo seHorseshoe Kidney. Njengoko izintso ezimbini zihamba zinyuka, iziphelo zazo ezisezantsi ziyadibana. Njengonobumba "U". Xa zidibana ngolu hlobo, azikwazi ukunyuka ngqo. Ngoko ke izintso ezidibene zibekwe ngaphantsi kancinci kunesiqhelo, ngaphambili kwesisu. Oku kukwabizwa ngokuba yi-renal fusion .
Ingaba le meko imbi kakhulu? Ngaba kukho into endiyixhalabeleyo?
Le yeyona ngxaki inkulu abantu abaninzi abanayo. Enyanisweni, uninzi lwabantu abaneHorseshoe Kidney abanazo naziphi na iingxaki zempilo ezinzulu. Abantu abaninzi abanale meko baphila ubomi obuqhelekileyo nobusebenzayo ngaphandle kweengxaki.
Into ebalulekileyo kukuba iHorseshoe Kidney ayisoloko ichaphazela ubomi bakho. Ungaphila ubomi obude nobunempilo njengaye nabani na.
Nangona kunjalo, kukho into encinci ekufuneka siyiqaphele. Abantu abanale meko basengozini enkulu yokuba nomhlaza wezintso kunabantu ngokubanzi. Ngoku, musani ukoyika xa nisiva oku. Oku akuthethi ukuba wonke umntu uza kufumana umhlaza, kuthetha nje ukuba "umngcipheko uphezulu kancinci." Yiyo loo nto kubalulekile ukuba uhlolwe rhoqo njengoko ugqirha wakho ecebisa. Ukuba ufunyenwe kwangethuba, umhlaza wezintso sisifo esinyangekayo.
Le meko ayixhaphakanga kangako. Ichaphazela malunga nomntu omnye kwabangama-500. Ikwaxhaphake kancinci kumadoda kunakwabasetyhini.
Ngaba kukho ezinye iimeko ezinxulumene neHorseshoe Kidney?
Ewe. Ngamanye amaxesha iHorseshoe Kidney inokwenzeka yodwa. Nangona kunjalo, kwezinye iimeko, ibonakala kunye nezinye iimeko zemfuza okanye ze-chromosome. Kulungile ukuqaphela oku.
| Udidi lwezifo | Iimeko zempilo ezinokubakho ezinxulumene noko |
|---|---|
| Iimeko zeChromosome |
|
| Ezinye iimeko zemfuza (iimeko ezingezizo eze-chromosome) |
Zithini iimpawu zale meko?
Nantsi into emangalisayo. Uninzi lwabantu abaneHorseshoe Kidney ababi nazimpawu ebomini babo bonke. Ixesha elininzi, le meko ifunyanwa ngengozi ngexesha lokuhlolwa kwesifo ukuze kufunyanwe enye into.
Nangona kunjalo, abanye abantu banokuba neempawu. Ukuba benjenjalo, ezona mpawu zixhaphakileyo zezi:
| Uphawu | Ingcaciso elula |
|---|---|
| Usulelo oluqhelekileyo lwendlela yomchamo (UTIs) | Usulelo lomchamo (UTIs) ludla ngokuvela ngeempawu ezifana nokutsha, iintlungu (dysuria) , kunye nomkhuhlane xa uchama. |
| Amatye ezintso | Iimpawu zingabandakanya iintlungu zesisu, iintlungu ezisezantsi komqolo, igazi kumchamo (i-hematuria) , kunye nentlungu xa uchama. |
| Isicaphucaphu nokuhlanza | Abanye abantu banokuba nesicaphucaphu nokuhlanza ngenxa yokusebenza kakubi kwezintso. |
Kutheni oku kusenzeka?
Oogqirha nabaphandi abakaqiniseki ukuba yintoni ebangela oku. Konke oku kungenxa yotshintsho kwindlela ii-genes ezisebenza ngayo ngelixa umntwana esakhula esibelekweni.
Xa usana olusandul’ ukuzalwa lufunyaniswa ukuba lunesifo seHorseshoe Kidney, abazali badla ngokuzibuza ukuba ngaba benze into engalunganga ngexesha lokukhulelwa. Akukho nto imbi ngaloo nto. Asikuko ukuba unetyala. Le yinto eyenzekayo ngamanye amaxesha, kwaye asikayazi isizathu okwangoku. Ngoko ke ungakhathazeki ngayo.
Zeziphi iingxaki ezinokubangela oku?
Nokuba akukho zimpawu, ukuba neHorseshoe Kidney kukubeka emngciphekweni omkhulu wokuba neengxaki ezithile.
- Eyona ngxaki ixhaphakileyo: Le yimeko ebizwa ngokuba yi -ureteropelvic junction (UPJ) obstruction . Ngamafutshane, kukuvaleka ekuqaleni kwe-ureter, ityhubhu ethwala umchamo ukusuka kwintso ukuya kwisinyi. Ukuma kwentso kunokuthintela ukuhamba komchamo. Le meko yenzeka malunga nesinye kwisithathu (33%) sabantu abanezintso ezinamazinyo aqinileyo.
- Ezinye iingxaki:
- I-Vesicoureteral reflux (VUR): Ukuhamba komchamo usuka kwisinyi usiya kwizintso.
- I-Hydronephrosis: Ukudumba kwezintso ngenxa yokungaphumi kakuhle komchamo.
- Isifo sezintso esinePolycystic (PKD): Ukwakheka kwee-cysts ezizaliswe lulwelo kwizintso.
- Uxinzelelo lwegazi oluhlaziyiweyo: Uxinzelelo lwegazi oluphezulu olubangelwa kukucutheka kwemithambo yegazi ehambisa igazi ezintso.
- Umhlaza wezintso: Njengoko bekutshiwo ngaphambili, umngcipheko uphezulu kancinci.
Ngoko ke, ukuba uneHorseshoe Kidney, kulungile ukuba uqaphele iimpawu zomhlaza wezintso.
- Igazi kumchamo
- Ukuva iqhuma okanye ukudumba okungaqhelekanga esiswini
- Intlungu engaqhelekanga evela kwicala lomqolo ongezantsi
Ukuba ubona into efana nale, bona ugqirha wakho ngoko nangoko.
Ungayibona njani le meko?
Njengoko bekutshiwo ngaphambili, oku kudla ngokufunyaniswa ngengozi. Nangona kunjalo, ukuba uneempawu ezinxulumene nezintso zakho, ugqirha wakho uza kukuhlola. Ukongeza, banokwenza uvavanyo olufana nolu.
- Uvavanyo lomchamo: Ukujonga igazi okanye usulelo kumchamo.
- Uvavanyo lwegazi: Uvavanyo lokujonga ukuba izintso zisebenza kakuhle kangakanani.
- Izinga lokuhluza eliqikelelweyo le-glomerular (eGFR)
- Uvavanyo lwe-urea nitrogen egazini (BUN)
- Uvavanyo lokucacisa i-creatinine
- Uvavanyo Lokufota (IiSkeni): Olu vavanyo lunceda ekuchongeni ngokuchanekileyo imo, indawo, kunye nomsebenzi wezintso.
- I-ultrasound yezintso: Uvavanyo oluqhelekileyo olwenziwayo, olungenazintlungu.
- I-voiding cystourethrogram (VCUG): Uvavanyo olukhethekileyo lwe-X-ray lokujonga i-urinary reflux (VUR).
- Iskeni yeRadionuclide: Uvavanyo lokujonga ukuba izintso zisebenza kakuhle kangakanani na kwaye zivelisa umchamo kakuhle kangakanani na.
- Uvavanyo oluneenkcukacha ezithe vetshe olufana ne -MRI scan (Magnetic resonance imaging): kunye ne -CT scan (Computed tomography scan) .
Ingaba unyango luyimfuneko? Yintoni enokwenziwa?
Kuxhomekeke ekubeni unazo na iimpawu okanye awunazo.
I-Horseshoe Kidney ayinakunyangwa okanye isuswe kuba yinxalenye yomzimba ekhoyo ekuzalweni. Ke ngoko, ukuba akukho zimpawu, awuyi kufuna naluphi na unyango.
Nangona kunjalo, ukuba uneempawu okanye iingxaki, zinokunyangwa.
- Kwizifo zomchamo (UTIs): Ugqirha wakho uza kukunika amayeza okubulala iintsholongwane .
- Xa kukho amatye ezintso okanye ukuvaleka: Ngamanye amaxesha, kunokufuneka utyando ukuze kususwe amatye ezintso okanye ukuze kube lula ukuba umchamo uphume.
Oogqirha abadli ngakuzami ukwahlula okanye ukususa izintso ngenkqubo yotyando (i-nephrectomy) kuba azinamhlaza, kwaye abantu abaninzi baphila nazo ngaphandle kweengxaki.
Ndingaphila njani ngokukhuselekileyo nale meko?
Ukuphila nale nto akunzima kangako. Nangona kunjalo, kufuneka sithathe amanyathelo okhuseleko ambalwa. Ekubeni iHorseshoe Kidney ikwindawo engaphambili esiswini kunezintso eziqhelekileyo,Amathuba okwenzakala emzimbeni aphezulu kancinci.
Ngoko ke, lumka ngezi zinto:
1. Nxiba isongo sesilumkiso sezonyango: Gcina isongo okanye ikhadi elibonisa ukuba uneHorseshoe Kidney. Kwimeko yongxamiseko, kuya kunceda oogqirha abanyangayo kunye neenkonzo zongxamiseko ukuba bazi ngemeko yakho.
2. Kuphephe imidlalo yokudibanisa: Oku kubaluleke kakhulu ebantwaneni. Imidlalo ebandakanya ukudibana ngqo, efana neragbi, ibhola ekhatywayo, ikarati, kunye nebhokisi, inokonakalisa izintso.
3. Nxiba ibhanti yokukhusela: Ukuba wena (okanye umntwana wakho) nibandakanyeka kumdlalo okanye kwisenzo esinokubangela umonakalo kwizintso, nxiba iphedi yokukhusela ekhethekileyo egubungela isisu (isivikelo sezintso okanye isivikelo sezintso) .
Kungcono ukuhlala unxibelelana rhoqo nogqirha wakho kwaye ufumane uhlolo rhoqo kunye neeskeni njengoko ecebisa.
Umyalezo Wokuya Ekhaya
- IHorseshoe Kidney yimeko yokuzalwa apho izintso ezimbini zidibene khona ezantsi. Oku akuyongozi njengoko unokucinga.
- Abantu abaninzi abanazo iimpawu kwaye baphila ubomi obuqhelekileyo nobusempilweni.
- Abanye abantu banokuba neengxaki ezifana nosulelo oluqhelekileyo lwendlela yomchamo (UTIs) okanye amatye ezintso. Kukho unyango olufanelekileyo loku.
- Le meko ingonakalisa izintso ngokulula. Kungoko ke, kubaluleke kakhulu ukuphepha imidlalo ebandakanya ukudibana nomzimba kwaye uhlale ukhuselekile.
- Ukuba unemibuzo, iinkxalabo, okanye amathandabuzo malunga noku, okanye ukuba ufumana iimpawu ezifana neentlungu zesisu okanye usulelo lomchamo, eyona nto ingcono onokuyenza kukuthetha nogqirha wakho ngayo.











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