Wake wazizwa sengathi amhlophe amehlo akho aphuzi kancane? Noma ukuthi isikhumba sakho sinombala ophuzi kancane? Mhlawumbe kubonakala kakhulu uma unomkhuhlane, uma ucindezelekile ngokuhlolwa, noma uma ungadlanga ngokwanele. Abantu abaningi bayasaba ngokushesha lapho bebona lokhu, becabanga ukuthi, "O, ingabe isibindi sami siyagula ngempela?" Kodwa lokhu akukubi ngaso sonke isikhathi. Namuhla sikhuluma nge-Gilbert's Syndrome, isimo esivame kakhulu esibonisa lezi zimpawu, kodwa ngokuvamile asiyona ingozi.
Kalula nje, iyini i-Gilbert's Syndrome?
I-Gilbert's syndrome yisimo sofuzo esithinta isibindi sethu. Kuyinguquko encane kakhulu endleleni umzimba wethu osebenza ngayo kunokuba kube ukugula okungathi sína. Kwenzeka lapho umzimba wethu ungakwazi ukucubungula kahle into ebizwa ngokuthi i-bilirubin.
Manje ungase uzibuze ukuthi iyini le bilirubin. Cabanga nje, amangqamuzana abomvu egazi emzimbeni wethu nawo aphila isikhathi esithile. Lapho lawa maseli abomvu egazi amadala ewohloka, kukhiqizwa into ephuzi njengomkhiqizo olandelanayo. Yilokho esikubiza ngokuthi i-bilirubin .
Ngokuvamile, kumuntu ophilile, le bilirubin ithathwa esibindini, ihlanganiswe ne-bile, bese isuswa emzimbeni. Kufana 'nohlelo lokulawula udoti' lomzimba wethu. Kodwa-ke, kumuntu onesifo sikaGilbert, isibindi asikhiqizi i-enzyme eyanele eyenza lo msebenzi. Isizathu salokhu ukuthi kukhona ushintsho oluncane ku-gene (`UGT1A1` gene) oluyala umzimba ukuthi wenze leyo enzyme. Ngenxa yalokho, i-bilirubin ethile iqoqana egazini, engenakukwazi ukususwa ngokuphelele emzimbeni. Lokhu kwanda kwenani le-bilirubin egazini kubizwa ngokwezokwelapha ngokuthi i-hyperbilirubinemia . I-bilirubin eyengeziwe eqoqana egazini ibangela amehlo nesikhumba ukuba kuphenduke ophuzi.
Into ebalulekile ukuthi i-Gilbert's syndrome akuyona isifo esonakalisa isibindi noma esibangela ukuba siyeke ukusebenza. Kumane nje kuyishintsho elincane, elingenangozi ekusebenzeni kwesibindi.
Ingabe lesi simo sivamile emphakathini?
Yebo. Nakuba abantu abaningi bengakaze bezwe ngakho, i-Gilbert's syndrome iyisimo esivame kakhulu kunalokho ongase ucabange. Ngokweminye imibiko, phakathi kwabantu abangu-3 no-7 kwabayi-100 emhlabeni wonke bangase babe nalesi simo. Lokho kusho ukuthi abantu abaningana abaseduze nawe bangase babe naso. Ezimweni eziningi, laba bantu abazi nokuthi bayakwazi.
Lesi simo ngokuvamile sivame kakhulu kwabesilisa kunabesifazane. Singathinta abantu banoma yimuphi ubudala nohlanga.
Ziyini izimpawu ze-Gilbert's syndrome?
Into emangazayo lapha ukuthi cishe umuntu oyedwa kwabathathu abane-Gilbert's syndrome akabonisi zimpawu. Bathola ngakho kuphela lapho udokotela ethi amazinga abo e-bilirubin aphakeme kancane uma behlolwa igazi ngesinye isizathu.
Uphawu oluyinhloko noluvame kakhulu olubonakala kulabo ababonisa izimpawu yi -jaundice . Okusho ukuthi,
- Ukuphuzi kwamehlo amhlophe.
- Ukuphuzi kwesikhumba.
Lo mbala ophuzi uvame ukuhlala izinsuku ezimbalwa kuphela. Uyafika uphinde udlule. Awubangeli monakalo emzimbeni. Nakuba kungase kungakhululeki kancane ngoba kushintsha ukubukeka kancane, akuyona ingozi empilweni.
Akuvamile ukuthi abanye abantu babhekane nezinye izinkinga ezincane ngaphezu kwalesi sibonakaliso esiyinhloko. Lokhu kubalwe kuthebula elingezansi.
| Ezinye izimpawu ezingase zivele kaningi | Incazelo elula |
|---|---|
| Umchamo omnyama noma indle enombala wobumba | Umbala womchamo ungashintsha njengoba amazinga e-bilirubin ekhuphuka. |
| Ukukhathala | Ukuzizwa ukhathele ngaso sonke isikhathi ngaphandle kwesizathu esithile. |
| Izinkinga zesistimu yokugaya ukudla | Ubuhlungu besisu, isicanucanu, ukuqunjelwa, njll. |
| Ubunzima bokufinyelela esivumelwaneni | Ukuzizwa kunzima ukugxila kokuthile. |
| Ikhanda elibuhlungu kanye nesiyezi | Abanye abantu bangase babike nezimpawu ezinjengalezi. |
Yiziphi izimbangela zokwanda kokuphuzi kwamehlo?
Umuntu onesifo sikaGilbert's syndrome akahlali enamazinga aphezulu e-bilirubin. Ezinye izinto zingabangela ukuthi la mazinga akhuphuke okwesikhashana, okubangela ukuthi amehlo nesikhumba kubonakale kakhulu (i-jaundice). Lezi zibizwa ngokuthi 'izibangela'. Uma unalesi simo, kubalulekile ukuqaphela lezi zinto.
| Isiqalisi | Lokhu kukhulisa kanjani i-bilirubin? |
|---|---|
| Ukuphelelwa amanzi emzimbeni | Uma ungaphuzi amanzi anele emini, ukugcwala kwe-bilirubin egazini kuyanda. |
| Ukuzila ukudla noma ukweqa ukudla | Uma uchitha isikhathi eside ungadli, umzimba wakho usebenzisa ezinye izindlela zokuthola amandla. Kule nqubo, amazinga e-bilirubin ayakhuphuka. |
| Izifo kanye nezifo | Noma yikuphi ukugula, njengomkhuhlane noma umkhuhlane, kubeka ingcindezi emzimbeni. Lokhu kucindezeleka kungalibazisa inqubo yokucubungula i-bilirubin yesibindi. |
| Ukucindezeleka | Ukucindezeleka okubangelwa izinto ezifana nokuhlolwa, izinkinga zomsebenzi, kanye nezinkinga zomuntu siqu nakho kungathinta ama-hormone omzimba futhi kwandise amazinga e-bilirubin. |
| Ukuzikhandla ngokweqile | Ukuzikhandla ngokweqile kanye nokuzivocavoca ngokweqile nakho kungabangela amazinga e-bilirubin ukuba akhuphuke okwesikhashana. |
| Ukuya esikhathini kwabesifazane | Amazinga e-Bilirubin angakhuphuka nakwabanye besifazane ngenxa yezinguquko zama-hormone ngesikhathi sokuya esikhathini. |
Udokotela usithola kanjani lesi simo?
Nakuba i-Gilbert's syndrome iyisimo sokuzalwa, ivame ukutholakala ngesikhathi sobusha noma ubuntwana. Lokhu kungenxa yokuthi izinguquko zamahomoni ezenzeka ngesikhathi sobusha zingabangela ukwanda kokukhiqizwa kwe-bilirubin, okungabangela izimpawu zivele okokuqala.
Esikhathini esiningi, lokhu kutholakala ngengozi. Uma kwenziwa ukuhlolwa kwegazi ngesizathu esithile, udokotela uqaphela ukuthi izinga le-bilirubin liphakeme kancane kunokuvamile.
Ngemuva kwalokho, kwenziwa ezinye izivivinyo eziningana ukuthola ukuthi ikhona yini enye imbangela enkulu yaleli zinga eliphezulu le-bilirubin (isib., isifo sesibindi njenge-hepatitis).
- Ukuhlolwa Kokusebenza Kwesibindi: Lokhu kunganikeza umbono omuhle ngempilo yesibindi. Ku-Gilbert's syndrome, konke ngaphandle kwe-bilirubin kuvame ukuba yinto evamile.
- Ukuhlolwa Kwezakhi Zofuzo: Kwezinye izimo, uma kudingeka ukuqinisekisa ukuxilongwa, ukuhlolwa kwezakhi zofuzo kungenziwa ukuze kuhlolwe ukuguquka kwezakhi zofuzo ze-`UGT1A1`. Kodwa-ke, lokhu akudingeki ngaso sonke isikhathi.
Uma yonke eminye imiphumela yokuhlolwa ijwayelekile futhi ungenazo ezinye izimpawu ezinkulu, udokotela uzophetha ngokuthi une-Gilbert's syndrome.
Ingabe lesi simo sidinga ukwelashwa? Ingabe ikhona imiphumela yesikhathi eside?
Nansi into ebaluleke kakhulu okudingeka uyazi:
I-Gilbert's syndrome iyisimo esingenangozi esingadingi ukwelashwa.
Yebo, uzwile kahle. Lokhu akudingi imithi noma ukwelashwa okukhethekile. Ngoba akubanga umonakalo wesikhathi eside esibindini sakho noma kunoma yisiphi esinye isitho emzimbeni wakho. Umuntu one-Gilbert's syndrome angaphila impilo enempilo nende, njengomuntu ongenalo lesi simo.
Nakuba amehlo aphuzi engase angakhululeki ukuwabuka, awabeki ingozi empilweni. Ngokugwema izinto ezibangela lokhu okukhulunywe ngakho ngenhla, ungalawula amehlo aphuzi avamile.
Ngakho-ke kufanele ngibone udokotela nini?
Nakuba i-Gilbert's syndrome ingenangozi, uphawu lokuphuzi kwamehlo (i-jaundice) lungaba uphawu lwezinye izifo ezinkulu zesibindi. Ngakho-ke,Uma ubona amehlo ephuzi okokuqala noma uma unezinye zezimpawu ezilandelayo, kubalulekile ukufuna iseluleko sikadokotela. Lokhu kuzosiza ekunqumeni ukuthi unesifo sikaGilbert noma esinye isimo.
Isikhathi sokubona udokotela wakho:
- Uma isikhumba noma amehlo akho eba phuzi ngokuphawulekayo (i-jaundice).
- Uma uzwa ubuhlungu besisu noma isicanucanu njalo.
- Uma umzimba uzizwa ukhathele kakhulu.
- Uma umbala womchamo unombala onsundu/i-cola.
- Uma unezimpawu ezifana nomkhuhlane kanye nokubanda.
Lezi zimpawu akufanele zinganakwa ngoba zingaba izimpawu zezinye izifo. Udokotela wakho uzokwenza izivivinyo ezidingekayo futhi akunike iseluleko esifanele kakhulu.
Umlayezo Wokuya Nawe Ekhaya
- I-Gilbert's Syndrome akuyona isifo okufanele sesatshwe. Yisimo esivamile kakhulu, esingenangozi esitholakala emindenini.
- Lokhu kungenxa yokuthi isibindi asikwazi ukucubungula into ebizwa ngokuthi i-bilirubin ngesivinini esijwayelekile.
- Uphawu oluyinhloko ukuphuzi kwamehlo nesikhumba (i-jaundice). Lokhu kuyafika kudlule. Futhi akulimazi umzimba.
- Lombala ophuzi unganda okwesikhashana ngenxa yezinto ezifana nokucindezeleka, ukugula, kanye nokweqa ukudla.
- Lesi simo asidingi ukwelashwa. Ungaphila impilo enempilo ngokuphelele.
- Uma ubhekene namehlo aphuzi okokuqala noma unezinye izimpawu ezingavamile, qiniseka ukuthi ubona udokotela wakho ukuze uthole ukuxilongwa okunembile.











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