So woate sɛ aberante, apɔwmuden, agumadifo bi a komayare awu mpofirim pɛn? Ɛyɛ awerɛhow ankasa. Mpɛn pii no, yesusuw komayare ho sɛ biribi a ɛba bere a obi nyin no. Nanso ɛtɔ da bi a, nea ɛde nsɛm a esisi a wontumi nsusuw ho yi ba no yɛ tebea a ɛntaa nsi koraa a yennim ho hwee. Ɛnnɛ, yɛrebɛka komayare a ɛte saa biako a ebetumi aka mmerante ne mmabaa titiriw ho asɛm. Eyi ne ARVC.
Dɛn ankasa ne ARVC?
Sɛ yɛbɛka no tiawa a, ARVC yɛ komayare a ɛntaa nsi a wonya fi awosu mu , a ɛkyerɛ sɛ wobetumi de akɔ awo ntoatoaso ahorow mu. Nea ɛba ne sɛ yɛn koma mu ntini no sɛe.
Fa yɛn koma sɛ pɔmpɛ a ahoɔden wom a adan anan na ɛwom. Eyi ne nea ɛma mogya fa nipadua no nyinaa mu. Wɔ saa adan anan yi mu no, wɔfrɛ nea ɛwɔ fam nifa so no sɛ Nifa Ventricle. Wɔ ARVC mu no, koma ntini nkwammoaa a ɛte apɔw a ɛwɔ saa ahurututu nifa yi mu no wuwu na srade ne ntini a ɛyɛ nhama (akuru ntini) si ananmu .
Ɛte sɛ birikisi a efi ɔfasu pa mu rehwe ase na atɛkyɛ ahyɛ nsonsonoe no ma. Dɛn na ɛba? Saa koma dan no fasu yɛ teateaa, ɛyɛ mmerɛw, na ɛtrɛw. Afei entumi ntwetwe no yiye na ɛbɔ mogya. Eyi betumi ama nneɛma te sɛ ahome a ɛyɛ tiaa ne akisikuru aba.
Nea ɛyɛ hu kɛse mpo ne sɛ srade ne akuru ntini a ayɛ foforo no siw anyinam ahoɔden nsɛnkyerɛnne a ɛwɔ koma no mu no kwan. Eyi ma koma no bɔ a ɛnteɛ. Yɛfrɛ eyi arrhythmia . Eyi ne tebea a ɛyɛ hu sen biara wɔ yare yi mu. Efisɛ ebetumi ama koma no agyae mpofirim na wawu mpo.
Wɔsan frɛ saa yare yi ARVC, Arrhythmogenic Right Ventricular Dysplasia (ARVD). Ɛtɔ mmere bi a wɔsan frɛ no Arrhythmogenic Cardiomyopathy (ACM) efisɛ ɛka benkum so ahurututu nso.
Dɛn ne tebea yi ho sɛnkyerɛnne?
Ɔhaw biako a ɛwɔ saa yare yi ho ne sɛ ebetumi ayɛ nea enni sɛnkyerɛnne biara wɔ ne mfiase. Mpɛn pii no, yare no ho sɛnkyerɛnne fi ase da adi ansa na wadi mfe 40, ɛtɔ mmere bi a mpo wɔ mpanyin afe so.
Nea ɛyɛ hu sen biara ne sɛ, wɔ nnipa binom fam no, sɛnkyerɛnne a edi kan ne nea ɛma wohu sɛ wɔwɔ saa yare yi ne koma mu wu mpofirim.
Enti, ɛho hia paa sɛ wohu sɛnkyerɛnne ahorow a edidi so yi.
| Nsɛnkyerɛnne a ɛkyerɛ | Nkyerɛkyerɛmu a ɛnyɛ den |
|---|---|
| Koma a ɛbɔ a ɛnteɛ (Arrhythmias) . | Nsakrae a ɛnteɛ a ɛba koma a ɛbɔ mu. Ebetumi ayɛ te sɛ nea worehuruhuruw anaasɛ worepiapia wo koko. Titiriw wɔ tebea horow te sɛ (Atrial Fibrillation) . |
| Adwene a ɛyɛ basaa anaasɛ obi a ɔtotɔ piti | Ɛte sɛ nea n’adwene mu yɛ no naa esiane sɛ amemene no nnya mogya a ɛdɔɔso nti. |
| Ɔbrɛ | Bere nyinaa a wɔte nka sɛ wabrɛ kɛse esiane sɛ nipadua no ntumi nkɔ mogya yiye nti. |
| Koko mu yaw | Koko mu yaw esiane nhyɛso a ɛba koma no so nti. |
| Ɔhome a ɛyɛ den | Ahome a ɛyɛ tiaa a mogya a ɛnnɔɔso mma ahurututu no mu ba. |
| Nipadua a ɛho ahonhon | Nan, anan, anan, anaa yafunu mu a ɛho ahonhon. |
| Koma a Ɛnyɛ Den | Bere kɔ so no, ɛkame ayɛ sɛ tumi a koma no tumi de pɔmpɔ no yɛ mmerɛw koraa. |
Nea ɛde ARVC ba ne nea wonya fi awo mu
Mpɛn pii no, awosu mu nsakrae bi na ɛde ARVC ba . Eyi yɛ mfomso ketewaa bi a ɛwɔ nhyehyɛe anaa awosu mu nkwaadɔm a ɛka bom yɛ yɛn nipadua mu nkwammoaa no mu. Saa tebea yi ba bere a mfomso bi wɔ awosu mu nkwaadɔm a ɛka protein ahorow a ɛboa ma koma mu ntini nkwammoaa kɔ so nya abusuabɔ mu no.
Sɛ saa abusuabɔ yi yɛ mmerɛw a, koma ntini mu nkwammoaa fi ase tetew wɔn ho wɔn ho na wowuwu. Eyi betumi asi titiriw wɔ mmere a adwennwen wɔ koma no so, te sɛ bere a wɔreyɛ apɔw-mu-teɛteɛ no.
ARVC ayarefo bɛyɛ fã wɔ abusua abakɔsɛm a ɛfa tebea no ho. Eyi kyerɛ sɛ awosu mu abakɔsɛm bi wɔ hɔ .
Enti, sɛ wɔahu sɛ obi wɔ w’abusua mu a ɔwɔ ARVC a, ɛho hia paa sɛ saa onipa no abusuafo a wɔbɛn no (awofo, nuanom, mma, mmanana, papa nua barima, maame nuabeanom, ne nuabeanom mma, ne nuabeanom) yɛ aduruyɛ mu nhwehwɛmu. Sɛ yare no ho sɛnkyerɛnne biara nni hɔ mpo a, ɛsɛ sɛ wɔn a wɔyɛ mmofra mpo kɔ oduruyɛfo nkyɛn na wɔka eyi ho asɛm.
Akwan titiriw abien na ɛwɔ hɔ a wobetumi afa so de ARVC akɔ awo ntoatoaso ahorow mu:
- Autosomal Dominant: Eyi ne ɔkwan a ɛtaa ba. Eyi kyerɛ sɛ awofo no mu biako wɔ awosu mu nkwaadɔm mu nsakrae no. Afei wɔn ba no wɔ hokwan 50% sɛ obenya yare no fi awo mu. Nanso, yare no ho sɛnkyerɛnne ne mfe a wɔde fi ase no betumi ayɛ soronko wɔ abusua no mufo mu.
- Autosomal Recessive: Eyi yɛ nea ɛntaa nsi kakra. Ɛha yi, awofo baanu no nyinaa wɔ awosu mu nkwaadɔm mu nsakrae no, nanso wonni sɛnkyerɛnne biara. Wɔn ba no wɔ hokwan 25% sɛ obenya yare no. Tebea pɔtee biako a ɛfa eyi ho ne Naxos yare , a ebetumi ama honam ani a ɛwɔ nsateaa ne nan ase no ayɛ den na nhwi a ɛyɛ den na ayɛ aboa nhoma ayɛ no.
Ɔkwan bɛn so na wobetumi ahu yare no?
Oduruyɛfo betumi agyina wo sɛnkyerɛnne ahorow, w’abusua abakɔsɛm, ne aduruyɛ mu nhwehwɛmu kakraa bi so ahu ARVC. Nneɛma pɔtee pii wɔ hɔ a wɔde hu ARVC. Nnuruyɛfo hwɛ gyinapɛn ahorow yi mu dodow a wudu ho.
Nsɛntitiriw a nnuruyɛfo de wɔn adwene si so:
- Sɛnea ɛbɛyɛ a wɔbɛhwɛ sɛ right ventricular function a ɛnteɛ ( Wɔde Echocardiogram anaa MRI nhwehwɛmu di dwuma ma eyi).
- Sɛnea ɛbɛyɛ a wobehu sɛ srade anaa akuru bi wɔ koma ntini no mu anaa ( MRI ho hia yiye ma eyi).
- Sɛnea ɛbɛyɛ a wobɛhwɛ sɛ nneɛma bi a ɛnteɛ wɔ ECG nhwehwɛmu mu ( Electrocardiogram - ECG/EKG ).
- Koma mu nnyigyei a ɛnkɔ so pɛpɛɛpɛ, titiriw bere a wɔreyɛ apɔw-mu-teɛteɛ no.
- Sɛ́ ebia obi wɔ abusua no mu a ɔwɔ ARVC.
Oduruyɛfo no gyina saa nneɛma yi so besi gyinae sɛ ebia "akyinnye biara nni ho" wowɔ yare no, "ebia" wowɔ bi, anaasɛ "ebia" wowɔ bi. Ebia wɔde wo nso bɛkɔ akɔyɛ awosu mu nhwehwɛmu sɛ ɛho hia a.
Sɔhwɛ afoforo a wɔde dii dwuma:
- Cardiac Computed Tomography (CT ) mfonini a wɔde hwɛ koma no
- ECG nhwehwɛmu bere a wɔreyɛ apɔw-mu-teɛteɛ ( Stress Test ) .
- Koma no anyinam ahoɔden dwumadi ho adesua ( Electrophysiology Testing ) .
- Koma mu ntini ketewaa bi a wɔde kɔyɛ nhwehwɛmu ( Biopsy ) .
Dɛn ne ayaresa ahorow a wɔde sa ARVC?
Nea ɛyɛ awerɛhow no, wonni aduru biara a wɔde sa ARVC. Nanso, ayaresa a etu mpɔn pii wɔ hɔ a ebetumi aboa wo ma woadi wo yare no ho sɛnkyerɛnne so, asiw ɔhaw ahorow a asiane wom ano, na woabɔ bra sɛnea ɛsɛ. Wo duruyɛfo botae titiriw ne sɛ ɔbɛhwɛ koma no nnyigyei ne koma tebea horow so.
| Ɔkwan a wɔfa so sa yare | Dɛn na ɛba? |
|---|---|
| Nnuru a wɔde yɛ nnuru | Wɔma nnuru te sɛ nnuru a ekum mogya a ɛtɔ kɔ nipadua no mu , beta-blockers , ne nnuru a ekum mogya a ɛtwetwe mogya . |
| Catheter a Wɔde Yiyi Afiri Mu | Sɛ wowɔ koma a ɛbɔ a ɛnteɛ a wuntumi mfa nnuru nni so a, adeyɛ a ɛhyew koma no mmeae a anyinam ahoɔden nsɛnkyerɛnne a ɛnteɛ ba no. |
| ICD afiri (Afiri a Wɔde Sisi Koma Mu-Defibrillator a Wɔde Si Nnipa Mu) . | Eyi yɛ ayaresa a ɛho hia sen biara no mu biako. Wɔ nnipa a asiane kɛse wom sɛ wobewuwu esiane komayare mpofirim nti fam no, wɔde afiri ketewaa bi hyɛ wɔn koko ho were ase. Sɛ koma no mu yare a ɛyɛ hu ba a, saa afiri yi de anyinam ahoɔden bi ma na ama koma no asan ayɛ sɛnea na ɛte kan no. |
| Koma a Wɔde Ma Afoforo | Wobu no sɛ ɛyɛ ɔkwan a etwa to sɛ ayaresa afoforo nyinaa di nkogu a, nanso enhia sɛ nnipa dodow no ara a wɔwɔ ARVC no kɔ akyiri saa. |
Nneɛma a ɛsɛ sɛ wususuw ho bere a wo ne ARVC te no
Sɛ wohu sɛ wowɔ ARVC wie a, ɛho behia sɛ woyɛ nsakrae bi wɔ w’asetra kwan mu. Saa nneɛma yi betumi aboa ma nhyɛso a ɛwɔ wo koma so no so atew.
- To apɔw-mu-teɛteɛ ano hye: ARVC betumi asɛe denam apɔw-mu-teɛteɛ so. Enti, ebia ebehia sɛ wokwati akansi agumadi koraa. Hwɛ hu sɛ wo ne wo duruyɛfo bɛkasa afa apɔw-mu-teɛteɛ dodow ne ko a wubetumi ayɛ da biara da ho.
- Asetra a ahoɔden wom: Ɛho hia yiye sɛ wobɛtew nsa a wɔnom so, kwati sigaretnom, di aduan a ahoɔden wom, na woto anonne a caffeine wom (kɔfe, tii) ano hye.
- Fa wo nnuru sɛnea wɔakyerɛw ama wo no: Mma nntwa nnuru a wo duruyɛfo akyerɛw ama wo no so da.
- Aduruyɛ mu nhwehwɛmu a wɔyɛ no daa: Ɛho behia sɛ wokɔ wo duruyɛfo nkyɛn wo nkwa nna nyinaa . Sɛ wowɔ ICD a, ɛho behia sɛ wɔma wɔhwɛ mu daa .
Sɛ wuhu sɛ wowɔ komayare a, ebetumi ayɛ ade a ɛyɛ den yiye sɛ wubedi ho dwuma, titiriw wɔ wo mmofraase. Sɛ woyɛ ogumadifo a, ebetumi ayɛ awerɛhow sɛ ɛsɛ sɛ wugyae saa nipasu no. Nanso kae sɛ wo nkwa som bo sen saa koraa. Sɛ wonya ayaresa ne asetra kwan a ɛfata a, wubetumi abɔ bra pa.
Nkrasɛm a Wɔde Kɔ Fie
- ARVC yɛ tebea a ɛntaa nsi, a wonya fi awosu mu a ɛka koma no fã nifa titiriw.
- Ade a ɛyɛ hu sen biara wɔ yare yi ho ne asiane a ɛwɔ hɔ sɛ koma no bɛtɔ mpofirim na wawu a enni sɛnkyerɛnne biara.
- Sɛ wuhu sɛnkyerɛnne ahorow te sɛ wo koko a ɛyɛ wo yaw, wo tirim yɛ wo yaw, anaasɛ ɛyɛ den sɛ wobɛhome a, kɔ oduruyɛfo nkyɛn ntɛm ara.
- Sɛ obi a ɔwɔ w’abusua mu wɔ ARVC a, akyinnye biara nni ho sɛ ɛsɛ sɛ wokɔ aduruyɛ mu nhwehwɛmu.
- Ɛwom sɛ wontumi nsa yare no koraa de, nanso wobetumi de nnuru, mfiri a wɔde yɛ ICD, ne asetra mu nsakrae asiw ano yiye na wɔatra ase yiye.
- Ɛho hia yiye sɛ ayarefo yi kwati apɔw-mu-teɛteɛ a emu yɛ den na akansi wom.
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