So wunya nsateaa ne nansoaa a ɛyɛ bruu, kɔkɔɔ, ne yaw nso wɔ awɔw bere mu, titiriw bere a wokɔ baabi te sɛ Nuwara Eliya no? So ɛtɔ mmere bi a wunya akuru nketenkete? Ɛwom sɛ nnipa pii susuw sɛ eyi yɛ atiridiinini ara kwa de, nanso ɛtɔ mmere bi a eyi betumi ayɛ tebea a ehia sɛ wɔde wɔn adwene si so kakra. Ɛnnɛ yɛreka ‘Chilblain Lupus’, lupus a ɛntaa nsi nanso ɛho hia paa ho asɛm.
Dɛn ne Chilblain Lupus?
Sɛ yɛbɛka no tiawa a, Chilblain Lupus yɛ lupus a ɛntaa nsi a ɛka yɛn honam ani. Wɔ aduruyɛ mu no, yɛfrɛ no ``cutaneous lupus erythematosus anaa CLE.`` Obi a ɔwɔ saa tebea yi nya akuru kɔkɔɔ anaa kɔkɔɔ a ɛyɛ yaw, plaques, wɔ ne honam ani bere a ɔwɔ awɔw mu no.
Asɛmfua "chilblain" no kyerɛ ankasa sɛ "awɔw a ɛyɛ kuru." Eyi ne nea ɛkɔ so wɔ tebea yi mu pɛpɛɛpɛ. Wim tebea a ɛyɛ nwini betumi de saa sɛnkyerɛnne ahorow yi aba, anaasɛ ama tebea bi a ɛwɔ hɔ dedaw no asɛe kɛse.
Mpɛn pii no, nnipa binom nya Chilblain Lupus bere a wɔahu sɛ wɔwɔ lupus titiriw, ``systemic lupus erythematosus'' akyi. Nanso, afoforo betumi anya tebea no a wonni kan nhu sɛ wɔwɔ bi. Nanso, ɛyaw ne ɔhaw a tebea yi de ba no mu yɛ den koraa. Sɛ wuhu sɛ wo nsateaa a ɛyɛ wo yaw na ɛkɔ soro, titiriw wɔ wo nsateaa ne wo nansoaa so a, ɛbɛyɛ papa sɛ wobɛkɔ oduruyɛfo nkyɛn ntɛm ara na woanya ayaresa.
Dɛn ne tebea yi ho sɛnkyerɛnne?
Chilblain Lupus titiriw ne nsensanee kɔkɔɔ anaa kɔkɔɔ anaa akuru a ɛwɔ honam ani. Wɔtaa hu eyinom wɔ:
- Wɔ nsateaa so
- Wɔ asen no so
- Wɔ nan ase
- Wɔ nansoaa mu
Nanso ɛntaa mma koraa sɛ saa akuru yi betumi aba nsateaa, nkotodwe, hwene, anaa aso nso so. Eyinom nyinaa mu yɛ den kɛse wɔ awɔw anaa nwini mu.
Wɔ sɛnkyerɛnne atitiriw yi akyi no, sɛnkyerɛnne afoforo pii wɔ hɔ a wobetumi ahu. Ma yɛnhwɛ nea wɔyɛ.
| Nsɛnkyerɛnne a ɛkyerɛ | Nkyerɛkyerɛmu a ɛnyɛ den |
|---|---|
| Akisikuru anaa akuru a ɛyɛ kurukuruwa | Akuru a ɛnsa wɔ honam ani esiane mogya a ɛnkɔ yiye nti. |
| Honam ani kɔla a ɛsakra (Depigmentation) . | Honam ani mmeae bi kɔla hwere na ɛyɛ fitaa. |
| Asen mu mpaapaemu | Mpaapaemu a emu dɔ wɔ asen no honam ani. |
| Wora a ɛyɛ den (Hyperkeratosis) . | Wora a ɛyɛ den wɔ baabi a honam ani akuru ayɛ no. |
| Raynaud adeyɛ a ɛyɛ nwonwa no | Sɛ wɔde wɔn ho to awɔw mu a, mogya no nkɔ nsateaa ne nansoaa no mu bere tiaa bi. Eyi betumi ama nsateaa no ayɛ fitaa, bruu, anaa kɔkɔɔ. |
Dɛn nti na Chilblain Lupus nya? Dɛn na ɛde ba?
Nneɛma atitiriw abien na ɛde Chilblain Lupus ba. Baako fi awosu mu , na biako nso yɛ nea ɛba bere ne bere mu .
Nneɛma a efi awosu mu ba
Saa tebea yi betumi afi nsakrae bi a ɛba yɛn awosu mu nkwaadɔm mu. Titiriw no, wɔahu sɛ nsakrae a ɛba awosu mu nkwaadɔm `(TREX1)` ne `(SAMHD1)` mu no ka eyi. Sɛ yɛbɛka no tiawa a, `TREX1` awosu mu abɔde no boa ma yesiesie yɛn DNA, na `SAMHD1` awosu mu abɔde no ka yɛn nipadua mu nkwaadɔm a ɛko tia nyarewa no dwumadi ho. Sɛ sintɔ bi wɔ saa awosu mu nkwaadɔm yi mu a, ebetumi ayɛ nea ɛde Chilblain Lupus ba wɔ abusua no mu ne mmofra nkumaa mu.
Ɛba a ntease biara nni mu
Wɔ nnipa binom fam no, eyi nyɛ awosu. Ebetumi ada adi mpofirim wɔ mpanyin afe so. Wonnya nhuu nea ɛde ba ankasa.
Hena na ɔwɔ asiane kɛse mu sɛ obenya eyi?
Ɛwom sɛ tebea yi betumi aka obiara de, nanso ɛtaa ba mpanyimfo a wɔn mfe akɔ anim mu . Nnipa a wɔte mmeae a wim yɛ nwini na ɛhɔ yɛ nwini bere nyinaa nso wɔ asiane kɛse mu.
Nea ɛka ho no, ayaresa mu tebea afoforo bi betumi ama asiane a ɛwɔ hɔ sɛ obi benya Chilblain Lupus no ayɛ kɛse.
- Anorexia nervosa: Eyi yɛ adidi mu haw a emu yɛ den a ɛde ne nkwa to asiane mu.
- Intestinal lymphoma: Eyi yɛ kokoram a ɛntaa nsi a ɛba yɛn dwensɔtwaa ketewa no mu ntini nhyehyɛe mu.
- Nyinsɛn: Mmea binom wɔ asiane mu sɛ wobenya saa tebea yi bere a wɔyem mpo.
Sɛ wɔansa a, nsɛnnennen bɛn na ebetumi aba?
Sɛ wɔansa tebea yi yiye a, mmoawa betumi anya honam ani akuru no . Saa nkurɔfo yi wɔ asiane kɛse mu sɛ wobenya honam ani yare te sɛ ``cellulitis``.
Afei nso, awiei koraa no, obi a ɔwɔ Chilblain Lupus betumi anya systemic lupus erythematosus, lupus a emu yɛ den sen biara a ɛka nipadua no nhyehyɛe ahorow pii.
Eyi nti na yɛka sɛ sɛ wuhu biribi a ɛyɛ soronko wɔ wo honam ani, titiriw kuru a ɛnsa a, ɛnsɛ sɛ wubu w’ani gu so na wokɔ oduruyɛfo nkyɛn.
Ɔkwan bɛn so na oduruyɛfo hu eyi pɛpɛɛpɛ?
Sɛ wowɔ saa sɛnkyerɛnne ahorow yi a, wobetumi de wo akɔ honam ani yare ho oduruyɛfo anaa ntini mu yare ho oduruyɛfo nkyɛn .
Sɔhwɛ titiriw a wɔde hu yare yi ne honam ani nipadua mu nhwehwɛmu . Nea ɛka eyi ho ne sɛ wubeyi honam ani fã ketewaa bi afi akuru bi a ɛwɔ wo honam ani mu na wode afiri a wɔde hwɛ nneɛma nketenkete ahwɛ mu wɔ aduruyɛdan mu. Saa nhwehwɛmu yi betumi akyerɛ sɛ wowɔ Chilblain Lupus anaa honam ani yare foforo.
Dɛn ne ayaresa ahorow a wɔde sa eyi?
Sɛ wo Chilblain Lupus no mu nyɛ den dodo a, ebia ɛho behia sɛ wobɔ wo ho ban fi awɔw ho ara kwa. Afei nso, sɛ wonom sigaret a, akyinnye biara nni ho sɛ wo duruyɛfo betu wo fo sɛ gyae. Sigaretnom ma yɛn mogya ntini mu yɛ den, na ɛno betumi ama saa sɛnkyerɛnne ahorow yi asɛe kɛse.
Sɛ yare no ho sɛnkyerɛnne no yɛ nea ɛfata anaasɛ emu yɛ den a, oduruyɛfo no betumi akyerɛw nnuru ahorow ama obi.
| Nnuru ahorow a wɔde di dwuma | Adwuma a ɛyɛ |
|---|---|
| Nnuru a ekum ɔyare mmoawa | Sɛnea ɛbɛyɛ a wɔbɛsa mmoawa a wɔde nyarewa ba wɔ honam ani akuru mu. Sɛ nhwɛso no: `dicloxacillin`, `erythromycin`. |
| Nnuru a wɔde ko tia asramma | Sɛnea ɛbɛyɛ a ɛbɛtew ɔfe, ɔbrɛ, ne nkwaa mu yaw a ɛwɔ nipadua no mu so. Sɛ nhwɛso no: `hydroxychloroquine`. |
| Nnuru a ɛma nipadua no tumi ko tia nyarewa (Calcineurin inhibitors) . | Sɛnea ɛbɛyɛ a wɔbɛtew nipadua no mu tumi a ɛko tia nyarewa no dwumadi so na wɔadi ɔfe so. Sɛ nhwɛso no: `tacrolimus`, `mycophenolate mofetil`. |
| Nnuru a esiw calcium kwan | Sɛnea ɛbɛyɛ a mogya ntini bebue na ama mogya akɔ ntɛmntɛm. Sɛ nhwɛso no: `nifedipine`. |
| Steroid srade a wɔde yɛ nnuru | Sɛnea ɛbɛyɛ a honam ani ahonhon ne ɔfe so bɛtew. Sɛ nhwɛso no: `fluocinolone acetonide`. |
| Steroid a wɔde di dwuma wɔ nipadua mu | Sɛnea ɛbɛyɛ a ɛbɛtew ɔfe ne ɔfe so wɔ nipadua no nyinaa mu. Sɛ nhwɛso no: `prednisone`. |
Ɛntaa mma koraa sɛ ebia wo duruyɛfo bɛkamfo akyerɛ sɛ wɔnyɛ oprehyɛn. Eyi hwehwɛ sɛ wɔyɛ oprehyɛn yi akuru no na wɔde honam ani aduru a efi nipadua no fã foforo a ɛwɔ apɔwmuden mu si ananmu.
Bere bɛn na ɛsɛ sɛ mekɔ oduruyɛfo nkyɛn?
Sɛ wuhu sɛ wo nsateaa anaa wo nansoaa, wo nan ase, anaa wo nan ase akuru kɔkɔɔ anaa kɔkɔɔ, ɛyɛ wo yaw, anaasɛ ɛyɛ yaw a, kɔ oduruyɛfo nkyɛn ntɛm . Obetumi ahu wo tebea no na wafi ayaresa a ɛho hia ase.
Sɛ wokɔ oduruyɛfo nkyɛn a, wubetumi abisa nsɛm yi nso:
- "Oduruyɛfo, dɛn na ebetumi ayɛ ade kɛse a enti mereyɛ eyi?"
- "So ebetumi aba sɛ menya systemic lupus?"
- "Dɛn na ɛsɛ sɛ meyɛ na amma saa apirakuru yi amma?"
- "Dɛn na wobetumi ayɛ wɔ mprempren apirakuru no ho?"
So wobetumi asiw Chilblain Lupus ano?
Ade a eye sen biara a wubetumi ayɛ de atew asiane a ɛwɔ hɔ sɛ wubenya tebea yi so ne sɛ wobɛbɔ wo ho ban afi awɔw ho . Sɛ wobɛyɛ eyi a, wubetumi adi saa nneɛma yi akyi.
- Yɛ apɔw-mu-teɛteɛ daa:Apɔw-mu-teɛteɛ ma mogya no tu mpɔn na ɛma nipadua no hyew yɛ adwuma yiye.
- Ma wo fie ne w’adwumam nyɛ hyew: Yɛ nsakrae wɔ baabi a wote no na ama woabɔ wo ho ban afi awɔw ho.
- Fa wo nsa ne wo nan gu nsu a ɛyɛ hyew mu: Sɛ woyɛ eyi mpɛn pii da biara a, ɛbɛma mogya no atu mpɔn.
- Ma akwaa a ɛyɛ nwini no hyew nkakrankakra: Nnyɛ nneɛma te sɛ mpofirim a wode wo nsa bɛka no ma ogya. Fa wo ho hyew nkakrankakra na ama mogya asan akɔ.
- Hyɛ ntade a ɛyɛ hyew: Hyɛ sɔks a ɛyɛ den, nsateaa, ne mpaboa a ɛyɛ hyew bere a wowɔ mmeae a awɔw wom no.
Te sɛ honam ani yare afoforo no, Chilblain Lupus betumi de sɛnkyerɛnne a emu yɛ den aba na ɛtɔ mmere bi a egye bere kakra ansa na wɔanya ayaresa a ɛfata. Nanso mma anidasoɔ nnyae. Sɛ wo ne oduruyɛfo bi a wowɔ ne mu ahotoso yɛ adwuma a, ebetumi aboa wo ma woanya ano aduru a ɛbɛyɛ adwuma ama wo. Saa bere yi de, sɛ wode wo ho hyɛ kuw a wɔboa nkurɔfo a wubetumi ne afoforo a wɔwɔ tebea koro no ara akasa a, ebetumi aboa kɛse.
Nkrasɛm a Wɔde Kɔ Fie
- Chilblain Lupus yɛ honam ani yare a ɛntaa nsi a ɛde akuru kɔkɔɔ/kɔkɔɔ a ɛyɛ yaw ba honam ani a awɔw ma ɛyɛ kɛse.
- Sɛ wuhu saa sɛnkyerɛnne ahorow yi wɔ wo akwaa mu a, mmu w’ani ngu so sɛnea ɛte daa na hwehwɛ aduruyɛfo afotu ntɛm ara sɛnea wubetumi.
- Ade a ɛho hia sen biara a wode besiw tebea yi ano na woadi so ne sɛ wobɛbɔ wo ho ban afi awɔw ho.
- Ɛho hia yiye sɛ wobɛkwati sigaretnom koraa, efisɛ sigaretnom ma mogya ntini mu yɛ den na ɛma yare no ho sɛnkyerɛnne no mu yɛ den.
- Ɛwom sɛ eyi yɛ nkwa nna nyinaa tebea de, nanso sɛ wɔsa yare no yiye na wɔhwɛ no yiye a, wobetumi adi sɛnkyerɛnne ahorow no so yiye na wɔatra ase sɛnea ɛsɛ.











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