Ɛyɛ ade a ɛfata sɛ wobɛhaw wo ho kakra sɛ wo ba no hu mpofirim sɛ nsensanee nketenkete a ɛyɛ kɔkɔɔ wɔ ne nipadua so, titiriw wɔ ne nan ne ne nan ase, bere a wadi agoru anigye so awie no. Ɛtɔ mmere bi a, yafunu mu yaw ne nkwaa mu yaw betumi aka saa nsensanee yi ho. Sɛ yehu biribi a ɛte sɛɛ a, yɛdwene nneɛma baako akyi. Enti ɛnnɛ yɛbɛka tebea bi a ebetumi de saa sɛnkyerɛnne ahorow yi aba ho asɛm, nanso mpɛn pii no ɛnyɛ biribiara a ɛsɛ sɛ wohaw wo ho, nanso ɛho hia yiye sɛ wohwɛ yiye. Ɛno ne Henoch-Schonlein Purpura, anaasɛ HSP tiawa.
Dɛn ne Henoch-Schönlein Purpura (HSP)?
Sɛ yɛbɛka no tiawa a, Henoch-Schonlein Purpura (HSP) yɛ tebea a ɛma mogya ntini nketenkete a ɛwɔ yɛn nipadua mu no hohoro anaasɛ ɛyɛ hyew. Nnuruyɛfo frɛ eyi `` vasculitis .'' Fa no sɛ mogya ntini nketenkete a ɛwɔ yɛn nipadua nyinaa mu no bo fuw na ɛho ahonhon. Saa ɔfe yi na ɛde ɔhaw ahorow yi nyinaa ba.
Sɛ mogya ntini ahonhon saa kwan yi so a, mogya mu nkwammoaa nketenkete fi ase pue. Te sɛ nea nsu paipu ma nsu fi mu no ara pɛ. Saa mogya mu nkwammoaa yi betumi akɔ honam ani, ntini a ɛyɛ nwini (te sɛ ntini a ɛyɛ nwini a ɛwɔ yɛn ano ne yɛn hwene mu), anaa akwaa a ɛwɔ yɛn mu no mu. Sɛ ɛtu kɔ honam ani a, ɛma saa nsensanee a ɛyɛ kɔkɔɔ a ɛte sɛ akuru no ba. Yɛfrɛ saa nsensanee no `(purpura)`.
Mpɛn pii no, saa HSP tebea yi ka mogya ntini a ɛwɔ honam ani, nkwaa, dwensɔtwaa (dwensɔtwaa), ne asaabo mu. Nanso asɛmpa no ne sɛ mmofra dodow no ara a wonya HSP no ho tɔ wɔn koraa wɔ adapɛn kakraa bi mu a wonhyia ɔhaw biara a ɛtra hɔ kyɛ . Enti ɛho hia sɛ wuhu nokware no ansa na woabɔ hu.
Dɛn ne nneɛma a ɛde HSP ba?
Nnuruyɛfo da so ara ntumi nka nea ɛde HSP ba no yiye. Nanso wosusuw sɛ ɛda adi kɛse sɛ efi ase wɔ ɔyare mmoawa bi akyi . Ebetumi ayɛ ɔyare mmoawa, mmoawa, anaa mmoawa a wɔsɛe nnɔbae. Sɛ nhwɛso no, mmofra binom betumi anya tebea no bere a wɔn menewa mu ayɛ wɔn yaw akyi.
Sɛ ɛno da nkyɛn a, wosusuw sɛ nnuru bi ne aduan ho akisikuru betumi afi mu aba . Ebia nnipa binom nso wɔ awosu mu su bi. Nhwehwɛmufo da so ara rehwehwɛ nea ɛde HSP ba ankasa.
HSP ba bere a yɛn nipadua mu tumi a ɛko tia nyarewa no ntumi nyɛ adwuma yiye no. Yɛwɔ protein soronko bi a wɔfrɛ no `(Immunoglobulin A - IgA)` wɔ yɛn nipadua mu. N’adwuma titiriw ne sɛ ɛbɛko atia nyarewa na abɔ yɛn ho ban afi nyarewa ho. Nanso nea ɛkɔ so wɔ obi a ɔwɔ HSP nipadua mu ne sɛ saa `(IgA)` protein yi kɔ saa mogya ntini nketewa no mu. Ɛno ne bere a saa `(vasculitis)` tebea no ba, a ɛma mogya ntini no hohoro.
HSP ne ntini mu yare a ɛtaa ba mmofra so . Ɛwom sɛ ebetumi aba wɔ mfe biara mu de, nanso ɛtaa ba mmofra a wɔadi fi mfe 2 kosi 6. Ɛtaa ba mmarimaa so sen mmeawa bɛyɛ mmɔho abien. Ɛtaa nso taa ba wɔ osutɔbere ne awɔw bere mu (i.e., ɛrekɔ afe no awiei).
Dɛn ne HSP ho sɛnkyerɛnne ahorow?
Afei ma yɛnhwɛ sɛnkyerɛnne ahorow a abofra bi betumi ada no adi sɛ ɔwɔ HSP a.
Honam ani nsensanee `(Purpura)`
Eyi ne HSP ho sɛnkyerɛnne titiriw a ɛda adi kɛse . Nsonsonoe nketenkete a ɛyɛ kɔkɔɔ a ɛte sɛ akuru pue wɔ honam ani. Saa nsensanee yi nnyɛ mmerɛw bere a wohwɛ no (akisikuru a ɛnyɛ blanching).
- Wɔtaa hu saa nsensanee yi wɔ nan ase ne akyi .
- Ɛtɔ da bi a, wotumi hu saa nsensanee yi nso wɔ nsa, anim, ne nipadua no afã horow a ɛwɔ mfinimfini te sɛ koko ne yafunu mu.
- Saa nsensanee yi betumi apue mpofirim, anaasɛ ɛbɛdɔɔso nkakrankakra.
Nkwaa mu yaw ne ɛho ahonhon
Wɔ mmofra pii fam no, nkwaa mu yaw ne ɔfe betumi aba bɛyɛ dapɛn biako anaa abien ansa na honam ani akisikuru no ada adi.
- Ɛtaa ka nkotodwe ne nansoaa nkwaa .
- Ɛtɔ da bi a nkwaa te sɛ nsateaa ne nsateaa nso betumi aka.
- Ebia ɛyaw yi bɛma ayɛ den ama abofra no sɛ ɔbɛnantew.
Yafunu mu yaw
Yafunu mu yare taa ba bere a honam ani akisikuru apue akyi.
- Ebia wubenya yafunu mu akisikuru.
- Akisikuru ne ɔfe .
- Mmofra binom nso betumi anya mogya wɔ wɔn nsu mu (mogya a ɛwɔ BM/nsu mu). Eyi yɛ sɛnkyerɛnne a ɛsɛ sɛ wodwen ho.
Nkɛntɛnso a enya wɔ asaabo so
Wɔ tebea horow bi mu no, HSP nso betumi aka asaabo no .
- Wobetumi de mogya anaa protein kakraa bi aka nsu no ho .
- Ɛtɔ mmere bi a, nsu no kɔla betumi ayɛ kɔkɔɔ (hematuria).
- Ɛwom sɛ eyi nyɛ aniberesɛm wɔ nsɛm dodow no ara mu de, nanso ɛho hia yiye sɛ wobɛkɔ oduruyɛfo nkyɛn akɔhwɛ sɛ ebia nkɛntɛnso bi wɔ asaabo no so anaa.
HSP ho sɛnkyerɛnne taa di bɛyɛ ɔsram biako , na ɛno akyi no mmofra dodow no ara ankasa ho tɔ wɔn.
Ɔkwan bɛn so na nnuruyɛfo hu HSP pɛpɛɛpɛ?
Sɛ wode wo ba kɔ oduruyɛfo nkyɛn a, ade a edi kan a wɔyɛ ne sɛ wɔbɛhwehwɛ abofra no mu yiye. Esiane sɛ ɛkame ayɛ sɛ saa purpura nsensanee no wɔ HSP ayarefo nyinaa mu nti, ɛboa nnuruyɛfo kɛse ma wohu yare no.
Bio nso, oduruyɛfo no betumi ayɛ nhwehwɛmu ahorow te sɛ:
- Mogya mu nhwehwɛmu: Wobetumi de eyinom ahwɛ sɛnea asaabo no yɛ adwuma, ahwɛ sɛ ɔyare mmoawa bi wɔ hɔ anaa, na wɔahwɛ sɛ mogya a ɛtwetwe no ho haw bi wɔ hɔ anaa.
- Nsu mu nhwehwɛmu: Hwɛ sɛ mogya anaa protein wɔ nsu mu anaa. Eyi betumi ama yɛanya adwene sɛ ebia asaabo no aka no anaa.
- Nsu mu nhwehwɛmu: Hwɛ sɛ mogya wɔ nsu mu anaa.
- Ultrasound scan: Sɛ wo ba no yafunu mu yɛ no yaw kɛse a, eyi betumi aboa ma wɔayi ɔhaw afoforo a ɛwɔ yafunu no mu afi hɔ, titiriw tebea bi a wɔfrɛ no intussusception.
Bere a oduruyɛfo no ayɛ nhwehwɛmu ahorow yi nyinaa awie no, ɔkyerɛ sɛ ebia wowɔ HSP ne sɛnea emu yɛ den anaa.
Dɛn ne ayaresa ahorow a wɔde sa HSP?
Mpɛn pii no, HSP ankasa siesie a enni ayaresa pɔtee biara . Ɛno ne asɛmpa no. Nanso, sɛ HSP aka w’asaabo a, ɛnde ebia ɛho behia sɛ wɔsa wo yare.
Nea ɛbɛyɛ na wo ba no ho atɔ no na wadi ne yare no ho sɛnkyerɛnne so no, ebia wo duruyɛfo bɛkamfo nnuru te sɛ:
- Nnuru a ekum ɔyare mmoawa: Sɛ wosusuw sɛ ɔyare mmoawa bi na ɛde HSP no ba nkutoo a, wɔde eyinom ma.
- Nnuru a ɛma ɛyaw ano brɛ ase: Sɛ nhwɛso no, acetaminophen (te sɛ paracetamol) betumi aboa ma nkwaa mu yaw ne nipadua mu yaw so atew.
- Nnuru a ɛko tia ɔyare mmoawa: Sɛ nhwɛso no, nnuru te sɛ ibuprofen betumi aboa ma ɛyaw ne nkwaa a ɛho ahonhon no so atew.
- Corticosteroids: Sɛ nhwɛso no, nnuru te sɛ prednisone. Sɛ abofra no yafunu mu yɛ no yaw kɛse anaasɛ ɔwɔ asaabo mu yare nkutoo a, wɔde eyinom ma. Ɛsɛ sɛ wɔde eyinom di dwuma wɔ oduruyɛfo hwɛ ase nkutoo.
Nneɛma a wubetumi ayɛ wɔ fie
Wɔ nnuru akyi no, nneɛma bi wɔ hɔ a wubetumi ayɛ wɔ fie na ama wo ba no ho atɔ no:
- Ma wo ba no nnye n’ahome yiye: Tew mmirikatu ne agoru a ɔde di agoru no so, na hyɛ no nkuran sɛ ɔntra mpa so nkenkan nhoma.
- Ma nsu pii ma nom:Sɛ wode nneɛma te sɛ nsu ne nnuaba mu nsu ma a, ebetumi aboa ma woasiw nsu a ɛho ayɛ fĩ ano.
- Sɛ wo nkwaa ahonhon na ɛyɛ yaw a: Wubetumi ama akɔ soro kakra, na ebia sɛ wo duruyɛfo ka kyerɛ wo a, wode nsukyenee mpo ahyɛ so.
Ade a ɛho hia paa ne sɛ wode wo ba no bɛkɔ oduruyɛfo nkyɛn ntɛm ara sɛ ɔpow sɛ obedidi anaa ɔbɛnom, sɛ ne yafunu mu yɛ no yaw kɛse, anaasɛ ɔda asaabo mu haw ho sɛnkyerɛnne adi (sɛ nhwɛso no, ne nsu a ɛso tew, ne ho ahonhon). Ebia ɛho behia sɛ wɔde wɔn kɔ ayaresabea ma wɔsa wɔn yare.
So nsɛnnennen afoforo wɔ hɔ a ebetumi aba esiane HSP nti?
Ebia mmofra a wɔwɔ HSP no mu bɛyɛ fã benya wɔn asaabo so nkɛntɛnso bi. Mpɛn pii no, eyi yɛ nkɛntɛnso ketewaa bi pɛ na ɛsa a wɔmfa ayaresa titiriw biara nka ho. Nanso, ɛntaa mma koraa sɛ mmofra binom betumi anya tebea horow a emu yɛ den te sɛ asaabo a entumi nyɛ adwuma yiye. Ebia ɛho behia sɛ mmofra a wɔte saa kɔ asaabo ho ɔbenfo (nephrologist) nkyɛn kɔyɛ nhwehwɛmu foforo.
Aduruyɛ mu tebea foforo a ɛntaa nsi nanso emu yɛ den yiye ne intussusception. Eyi ne bere a dwensɔtwaa no fã biako hwɛ akyirikyiri kɔ ɔfã foforo mu no . Eyi betumi atwa mogya a ɛkɔ saa ɔfã no mu na ama asiw kwan. Eyi yɛ tebea a egye ntɛmpɛ a ɛsɛ sɛ wɔsa no ntɛm ara. Sɛ mpofirim ara wo ba no yafunu mu yɛ no yaw a emu yɛ den a ɛba bere ne bere mu, ɔrefe, anaasɛ mogya a ɛte sɛ jelly wɔ ne nsu mu a, ɛsɛ sɛ wususuw sɛ eyi te saa.
Nneɛma foforo a ɛho hia a ɛsɛ sɛ yehu
- Nea eye sen biara ne sɛ, mmofra dodow no ara a wonya HSP no ho tɔ wɔn koraa wɔ ɔsram biako mu na wonnya ɔhaw biara a ɛtra hɔ kyɛ.
- Ebia mmofra binom benya HSP bio. Eyi taa ba wɔ asram kakraa bi wɔ adeyɛ a edi kan no akyi. Nanso, sɛ ɛsan ba bio a, mpɛn pii no ɛnyɛ den kɛse te sɛ nea edi kan no .
Enti, dɛn ne nkrasɛm a wɔde kɔ fie fi eyinom nyinaa mu?
Okay, enti, sɛnea yɛaka ho asɛm no, eyinom ne nneɛma a ɛho hia sen biara a ɛsɛ sɛ yɛma ɛtra yɛn adwenem:
- HSP yɛ tebea a ebetumi aka mmofra nkumaa, na ama mogya ntini ahonhon. Nsɛnkyerɛnne titiriw ne nsensanee a ɛyɛ kɔkɔɔ.
- Mpɛn pii no, eyi ankasa bɛsa.
- Nkwaa mu yaw, yafunu mu yaw, ne asaabo a asɛe betumi aba.
- Sɛ wuhu nsensanee a ɛyɛ nwonwa wɔ wo ba nipadua so, sɛ onwiinwii wɔ yafunu mu yaw ho, anaasɛ wɔn nkwaa yɛ wɔn yaw a, akyinnye biara nni ho sɛ fa kɔ oduruyɛfo nkyɛn. Mma wo ho nnpopo, na mmom hwehwɛ aduruyɛ mu afotu ntɛm ara.
- Di oduruyɛfo no akwankyerɛ akyi yiye. Ma wo ba no ahomegye ne nsu pii.
- Mmofra dodow no ara ho tɔ wɔn koraa. Hu nsɛnnennen a ɛntaa nsi.
Kae sɛ ɛnyɛ wo nko ara. Nnuruyɛfo wɔ hɔ sɛ wɔbɛboa wo ne wo ba no. Sɛ wunim nsɛm a ɛte sɛɛ a, ɛbɛma woanya ahoɔden kɛse de ayɛ ho biribi wɔ bere a ɛsɛ mu.
Enti, mewɔ anidaso sɛ saa nsɛm yi bɛboa wo. Mepɛ sɛ wo ba no ho tɔ no ntɛm!
👩🏽 ⚕️ Nsɛmmisa foforo (FAQs)
💬 Dɛn ne mpofirim red rash (HSP) a ɛba mmofra nsa ne wɔn nan so?
Henoch-Schonlein Purpura (HSP) yɛ yare a mogya ntini nketenkete (capillaries) a ɛde mogya kɔ mmofra nkumaa nipadua mu no hohoro mpofirim na ɛpae te sɛ akutu, na ɛma mogya tu wɔ honam ani. Eyi ma honam ani nsensanee a ɛyɛ kɔkɔɔ/kɔkɔɔ.
💬 So saa yareɛ a wɔfrɛ no Henoch-Schonlein Purpura yi sɛe asaaboɔ?
Aane! Ɛnyɛ honam ani nko na mogya ntini a ɛpae yi betumi aba na mmom nipadua no mu nso (wɔ yafunu ne asaabo mu). Enti, sɛ mmofra a wɔwɔ saa yare yi nsu mu yɛ kɔkɔɔ a, ɛkyerɛ sɛ asaabo no asɛe na mogya retu.
💬 Ɔkwan bɛn so na wɔsa eyi? So ɛsɛ sɛ wɔde me kɔ ayaresabea?
Mpɛn pii no, eyi ankasa besiesie wɔ adapɛn kakraa bi mu. Nanso, ɛho hia sɛ wokɔ mmofra oduruyɛfo nkyɛn efisɛ ɛho hia sɛ wɔyɛ nsu mu nhwehwɛmu de hwɛ sɛ asaabo asɛe anaa na nkwaa/yafunu mu yaw a emu yɛ den yɛ nea ɛsɛ sɛ woyɛ.
` Henoch-Schonlein purpura, HSP, mmofra nyarewa, honam ani nsensanee, ntini mu yare, IgA ntini mu yare, mmofra nyarewa











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