Ebia wontee asɛmfua ‘Medullary Sponge Kidney’ ho asɛm da. Bere a ebia ɛbɛyɛ te sɛ nea ɛyɛ den kakra sɛ wɔbɛka ho asɛm no, nokwarem no, ɛyɛ awo mu tebea a ɛfa asaabo ho. Sɛ yɛbɛka no tiawa a, ɛhɔ na nsu nketenkete a wɔfrɛ no cysts no ba w’asaabo mu, titiriw wɔ asaabo no mfinimfini fã (medulla). Momma yɛnka eyi ho asɛm nkɔ akyiri nnɛ, ɛnte saa?
Dɛn ankasa ne Medullary Sponge Asaabo?
Momma yenni kan nhwɛ nea asaabo no yɛ ne sɛnea ɛyɛ adwuma. Sɛnea wunim no, asaabo yɛ yɛn nipadua mu nsu a ɛkɔ yɛn nipadua mu no fã a ɛho hia yiye. Asaabo biara wɔ mfinimfini fã bi, na yɛfrɛ no medulla. Saa medulla yi wɔ akwan a ɛyɛ fɛ yiye a wɔfrɛ no tubules nketenkete. Saa akwan yi boaboa nwura a wɔayi afi mogya no mu ano na ɛyɛ nsu. Afei saa akwan yi bom na ɛka akwan akɛse kakra a wɔfrɛ no collecting ducts ho. Eyinom mu no, nsu no kɔ baabi titiriw a wɔboaboa ano wɔ asaabo no mfinimfini, adwene no akyi berɛmo no. Efi hɔ no, nsu no fa nsukorabea no mu kɔ akisikuru no mu, na afei ɛfa nsukorabea no mu kɔ nipadua no mu.
Okay, afei deɛ ɛto obi a ɔwɔ `Medullary Sponge Kidney` ne sɛ collecting ducts a mekaa ho asɛm no nya cysts nketewa, na saa ducts no hohoro na ɛyɛ kɛseɛ. Wɔte sɛ ɔponkɛse. Ɛno nti na wɔfrɛ no `Sponge Kidney`. Saa tebea yi taa ka asaabo abien no nyinaa, nanso ɛtɔ mmere bi a ebetumi aka asaabo biako pɛ.
Ɔkwan bɛn so na saa medullary sponge asaabo tebea yi nyin?
Seesei wowɔ asɛmmisa bi a ɛfa nea ɛba bere a saa akisikuru yi ba no ho. Sɛ saa akisikuru yi ba a, saa akwan fɛfɛ (tubules) no ntumi nyɛ adwuma yiye. Afei, nneɛma te sɛ calcium fi ase kɔhyɛ saa akwan yi mu. Yɛfrɛ eyi (nephrocalcinosis). Ɛnyɛ calcium nko, na mmom nneɛma afoforo te sɛ phosphate ne oxalate nso betumi aboaboa ano wɔ saa kwan yi so. Bere kɔ so no, nneɛma a aboaboa ano yi bata ho na ɛyɛ asaabo mu abo .
`(cysts)` `(stones)` . `(Urinary Tract Infections or UTIs)` .
Nsonsonoe bɛn na ɛda eyi ne Polycystic Kidney Disease ntam?
Ebia woate Polycystic Kidney Disease (PKD) ho asɛm. Ɛsan nso yɛ yare a asaabo mu akisikuru ba. Enti nsonsonoe bɛn na ɛda abien no ntam?
Polycystic kidney disease (PKD) yɛ awosu mu yare a mpɛn pii no wonya fi awo mu. Ɛma asaabo no yɛ kɛse, na akisikuru pii ba nipadua no nyinaa mu. Ɛtɔ mmere bi a, PKD betumi de nsɛnnennen a emu yɛ den aba.Ebetumi de ɔhaw ahorow aba nkwa nna nyinaa mu. Nnipa pii a wɔwɔ PKD no nya asaabo a entumi nyɛ adwuma yiye na ɛsɛ sɛ wɔyɛ dialysis na ama wɔn mogya ho atew.
Nanso, asaabo a entumi nyɛ adwuma yiye no ntaa mma wɔ nnipa a wɔwɔ medullary sponge kidney (MSK) no mu. Ɛno ne nsonsonoe titiriw no.
Henanom na tebea yi ka no kɛse? Ɛtaa ba dɛn?
Mprempren wosusuw sɛ saa ``medullary sponge kidney (MSK)'' tebea yi ba kwa. Ɛne sɛ, enni nea ɛde ba pɔtee biara. Nanso, esiane sɛ epue wɔ mmusua bi mu nti, ebia agyapade bi betumi aba. Nanso, wonnya nhuu awosu mu nhyehyɛe a emu da hɔ mma no.
Nnipa dodow no ara hu sɛ wɔwɔ yare no bere a yare no ho sɛnkyerɛnne ada adi akyi nkutoo, mpɛn pii no wɔ wɔn mfe 20 mu. Wɔkyerɛ nso sɛ mmea wɔ asiane mu kakra sen mmarima .
It is very common, with an average of one in 5,000 people having MSK. Nanso, ɛtaa ba nnipa a wɔwɔ asaabo mu abo mu kɛse. Wei kyerɛ sɛ ebia nnipa a wɔte saa no mu 12% kɔsi 20% na wɔwɔ MSK.
So medullary sponge asaabo no ma mogya mmoroso ba?
Ebia ebinom besusuw sɛ ebia saa ``MSK'' yi de mogya mmoroso anaa nhyɛso ba anaa. Sɛnea mprempren nhwehwɛmu kyerɛ no, adanse biara nni hɔ a ɛkyerɛ sɛ ``medullary sponge kidney'' de mogya mmoroso ba.
Dɛn na ɛde medullary sponge asaabo ba?
Nnuruyɛfo da so ara nnim nea enti a nnipa binom nya saa tebea yi ankasa. Wosusuw sɛ ɔhaw bi a ɛwɔ asaabo nyin mu wɔ awotwaa mu, bere a akokoaa no da so ara wɔ awotwaa mu no na ɛde ba .
Dɛn ne yare yi ho sɛnkyerɛnne?
Nea ɛyɛ nwonwa no, nnipa pii a wɔwɔ Medullary Sponge Kidney (MSK) no nhu sɛnkyerɛnne biara . Eyi kyerɛ sɛ wɔtra ase a wonnim mpo sɛ wɔwɔ yare no. Ɔha biara mu kakraa bi pɛ, bɛyɛ 10%, na wonya yare no ho sɛnkyerɛnne.
Sɛ sɛnkyerɛnne a ɛte saa ba a, mpɛn pii no ɛne nsu mu yare (UTIs) ne asaabo mu abo wɔ abusuabɔ. Eyinom ne sɛnkyerɛnne atitiriw no:
- Mogya a ɛwɔ nsu mu (hematuria): Eyi kyerɛ sɛ nsu no betumi ayɛ kɔkɔɔ, ɛtɔ mmere bi a ɛbɛyɛ tii nsu kɔla.
- Flank pain: Ɛyaw a ɛba w’akyi afã abien no nyinaa, wɔ wo mpampam ase.
- Ɛyaw a ɛba bere a woretow nsu (dysuria): Ebia ɔhyew ne ɛyaw bɛba bere a woretow nsu no.
- Asaabo mu abo: Eyi yɛ biribi a nnipa pii ahyia. Ebetumi de akyi yaw a emu yɛ den aba.
- Nsuo mu yareɛ: Nsɛnkyerɛnneɛ te sɛ nsuo a ɔtaa to ne atiridiinini betumi aba.
Ɔkwan bɛn so na wohu sɛ medullary sponge asaabo no wɔ hɔ?
Sɛ wowɔ saa sɛnkyerɛnne ahorow yi a, wo duruyɛfo bedi kan ayɛ wo nipadua mu nhwehwɛmu. Wobebisa w’ayaresa ho abakɔsɛm, w’abusua abakɔsɛm, ne sɛnkyerɛnne biara a worehyia ho asɛm.
Sɛ wo duruyɛfo susuw sɛ wowɔ asaabo mu yare a, ɛda adi sɛ ɔbɛhyɛ sɛ wɔnyɛ mogya ne nsu mu nhwehwɛmu mpɛn pii . Eyinom bɛhwɛ:
- So mogya wɔ nsu mu?
- Ɔkwan bɛn so na asaabo no yɛ adwuma?
- So ɔyare bi wɔ hɔ a ɛma obi ho yɛ hyew?
Nea ɛka ho no, wobetumi ayɛ mfoninitwa nhwehwɛmu titiriw de ahwɛ sɛ saa akisikuru a mekaa ho asɛm wɔ asaabo no mu no wɔ hɔ anaa. Scan ahorow a wɔtaa yɛ ne:
- CT scan: Eyi de X-ray di dwuma de yɛ asaabo no mfonini a ɛwɔ afã abiɛsa (3D).
- Intravenous Pyelogram (IVP): Nea ɛka eyi ho ne sɛ wode aduru soronko bi bɛhyɛ wo ntini mu. Afei, wɔtwe X-ray mfonini ahorow pii. Wɔde aduru no fa mogya a efi asaabo no mu na ɛkɔ nsu mu, enti X-ray mfonini ahorow no kyerɛ ɔkwan a nsu no fa so pefee. Eyi betumi aboa ma wɔahu akisikuru ne mmeae a nsu no asiw.
- Ultrasound scan: Eyi de nnyigyei asorɔkye di dwuma de twa asaabo no mfonini.
Ɔkwan bɛn so na wɔsa medullary sponge asaabo?
Mprempren wonni ayaresa pɔtee biara a wɔde sa tebea a wɔfrɛ no medullary sponge kidney (MSK) no. Ayaresa no atirimpɔw titiriw ne sɛ wobesiw nsu mu yare (UTIs) ne asaabo mu abo so na wɔasa.
Ayaresa titiriw a wɔde sa ɔyare a ɛma obi nya ɔyare a ɛma obi ho yɛ hyew ne nnuru a ekum ɔyare mmoawa .
Asaabo mu abo a wɔsa no gyina ɔbo no kɛse so. Abo nketewa taa fa nsu mu ankasa. Ebia wo duruyɛfo bɛka akyerɛ wo sɛ nom nsu pii na aboa ma ɔbo no atwam ntɛmntɛm. Ebia wɔbɛkyerɛw nnuru a wɔde kum ɛyaw ne nnuru nso a ɛbɛma ntini a ɛwɔ wo ureters mu no adwo.
Ebia abo akɛse bɛhwehwɛ sɛ wɔyɛ ho adwuma kakra. Nhwɛso kakraa bi ni:
- Shock Wave Lithotripsy: Eyi yɛ ayaresa a ɛnyɛ nea wɔde hyɛ nipadua mu a wɔde shock wave a ahoɔden kɛse wom di dwuma de bubu asaabo mu abo. Afei wɔde asinasin a abubu no fi nipadua no mu wɔ nsu no mu.
- Ureteroscopy: Nea ɛka eyi ho ne sɛ wɔde afiri tenten a ɛyɛ tratraa bi a wɔfrɛ no ureteroscope bedi dwuma de ahwɛ baabi a ɔbo no wɔ. Wobetumi de saa adwinnade yi ayi abo nketewa, anaasɛ wobetumi de laser abubu abo akɛse.
- Nephrolithotomy a Wɔde Fa Honam ani:Nnuruyɛfo de saa kwan yi di dwuma bere a akwan foforo no ntumi nyɛ yiye nkutoo. Nea ɛka eyi ho ne sɛ wobetwa n’akyi ketewaa bi na wɔabubu asaabo mu ɔbo no afa mu na wɔatwe afi mu. Eyi nso yɛ oprehyɛn a wɔmfa biribiara nhyɛ mu.
So wobetumi asiw medullary sponge asaabo ano?
Medullary sponge kidney (MSK) yɛ awo mu yare a wonnim nea ɛde ba, enti wontumi nsiw ano . Nanso, wubetumi ayɛ nneɛma bi de asiw nsu mu yare (UTI) ne asaabo mu abo a ebetumi afi mu aba no ano.
Ebia wo duruyɛfo bɛkyerɛw nnuru te sɛ eyinom:
- Nnuru a wɔde kum ɔyare mmoawa a wɔmfa nni dwuma pii de siw ɔyare mmoawa a ɛsan ba wɔ nsu mu no ano.
- Nnuru te sɛ potassium citrate anaa thiazide (a wɔsan frɛ no nsu aduru) betumi atew calcium dodow a ɛwɔ nsu mu no so na asiw asaabo mu abo a ɛbɛba no ano.
Sɛ wosakra w’aduan nso a, ebetumi aboa ma woasiw nsu mu yare ne asaabo mu abo ano:
- Calcium: Sɛ wunya calcium a ɛdɔɔso fi w’aduan mu a, ebetumi aboa ma asiane a ɛwɔ hɔ sɛ asaabo mu abo bɛba no so atew. (Ebia nnipa binom besusuw sɛ sɛ wɔnom calcium pii a, ɛbɛma asiane a ɛwɔ hɔ sɛ obi benya abo no ayɛ kɛse, nanso eyi nte saa. Ɛsɛ sɛ wonom no sɛnea ɛsɛ. Kɔ wo duruyɛfo nkyɛn.)
- Nsu: Nsu pii a wobɛnom ho hia paa. Eyi ma nsu no mu yɛ mmerɛw na ɛtew asiane a ɛwɔ hɔ sɛ abo bɛba no so. Ɛboa nso ma mmoawa fi asaabo no mu. Bɔ mmɔden sɛ anyɛ yiye koraa no wobɛnom nsu lita 2-3 da biara.
- Nnuan a protein pii wom: Sɛ woto nnuan a protein pii wom te sɛ nam, mpataa, ne nkesua ano a, ebetumi aboa ma wɔasiw asaabo mu abo ano.
- Nkyene: Nkyene a wobɛtew so wɔ w’aduan mu nso ho hia yiye. Nkyene pii a wodi no ma asiane a ɛwɔ hɔ sɛ obi benya asaabo mu abo no yɛ kɛse. Enti hwɛ yiye wɔ nkyene dodow a wode bɛka w’aduan ho no ho. Nneɛma te sɛ nnuan a wɔde ahyɛ toa mu ne noodles a wɔde di dwuma ntɛm ara no wɔ nkyene pii.
Nea ɛho hia: Bere nyinaa kɔ wo duruyɛfo anaa aduan ho ɔbenfo nkyɛn ansa na woayɛ nsakrae biara wɔ w’aduan mu.
Dɛn ne obi a ɔwɔ medullary sponge kidney daakye?
Ebia nnipa pii besuro sɛ wɔbɛte eyi, nanso nnipa dodow no ara a wɔwɔ Medullary Sponge Kidney (MSK) no betumi akura asaabo mu dwumadi pa mu wɔ wɔn nkwa nna nyinaa mu .
Nanso, nnipa kakraa bi, bɛyɛ 10%, betumi anya asaabo a entumi nyɛ adwuma yiye. Nea ɛde ba titiriw ne nsu mu yare a ɛtaa ba, a ɛsan ba bio (UTIs) ne asaabo mu abo.
Ɛyaw a enni sabea yɛ ɔhaw foforo a ɛntaa nsi a ebetumi aba nnipa a wɔtaa nya asaabo mu abo no so. Wobetumi adi tebea yi so denam nneɛma a wɔbɛyɛ de asiw asaabo mu abo ano no so.
Medullary sponge kidney (MSK) betumi ama calcium a ɛwɔ mogya no mu no so atew. Eyi betumi ama nnompe no ayɛ mmerɛw . Eyi ma asiane a ɛwɔ hɔ sɛ obi benya nyarewa a efi nnompe mu no yɛ kɛse. Nhwɛsoɔ:
- Osteoporosis (yare a ɛma nnompe yɛ teateaa na ɛyɛ mmerɛw) .
- Secondary hyperparathyroidism (hormone ahorow a parathyroid ntini ahorow no yi fi nipadua no mu dodo) .
Nea ɛbɛyɛ na woasiw nnompe a ɛsɛe bere tenten yi ano no, ebia wo duruyɛfo bɛkyerɛw nnuru te sɛ potassium citrate ama wo.
Ɔkwan bɛn so na wobɛtra ase ne medullary sponge asaabo?
Wo duruyɛfo bɛhwɛ w’asaabo dwumadi so daa na wama wo ɔhwɛ a ɛboa sɛnea ɛho hia. Ɛho hia sɛ wonom nnuru sɛnea wɔakyerɛw ama wo no pɛpɛɛpɛ, di w’aduan akyi, na wokɔ so yɛ nhyehyɛe a wode bedi w’akyi no . Saa nneɛma yi betumi aboa ma wɔasiw nsu mu yare ne asaabo mu abo ano.
Aduru biara nni hɔ a wɔde sa Medullary Sponge Kidney (MSK). Nanso sɛnea madi kan aka no, nnipa pii a wɔwɔ saa tebea yi nni sɛnkyerɛnne biara, na ebinom mpo nnim sɛ wɔwɔ bi. Sɛ sɛnkyerɛnne ahorow no ba ampa a, mpɛn pii no, nea efi nsu mu yare anaa asaabo mu abo. Eyinom abien nyinaa yɛ nea wotumi sa no yiye . Wubetumi nso asiw nsu mu yare ne asaabo mu abo ano denam nsakrae a wobɛyɛ wɔ w’aduan ne w’asetra kwan mu no so. Sɛ wowɔ nsɛmmisa anaa biribi a ɛhaw wo a, ntwentwɛn wo nan ase sɛ wo ne wo duruyɛfo bɛkasa .
Nkrasɛm a Wɔde Kɔ Fie
Okay, enti mewɔ anidaso sɛ seesei woanya ntease pa wɔ `Medullary Sponge Kidney` a yɛkaa ho asɛm no ho. Momma yɛnkae yɛn ho nsɛntitiriw a ɛho hia sen biara no bio:
- Eyi yɛ awo mu tebea a ɛma asaabo nketenkete nyin wɔ asaabo no mfinimfini fã (medulla).
- Nnipa dodow no ara nni sɛnkyerɛnne biara . Sɛ wɔyɛ saa a, ɛyɛ urinary tract infections (UTIs) anaa asaabo mu abo.
- Ayaresa pɔtee biara nni hɔ a wɔde sa eyi, nanso wobetumi asa yare no ho sɛnkyerɛnne ne nsɛnnennen no yiye.
- Ɛho hia yiye sɛ wosiw asaabo mu abo ne nsu mu yare ano. Sɛ wobɛyɛ eyi a, nom nsu pii, hwɛ yiye wɔ nea wudi ho, na di wo duruyɛfo akwankyerɛ akyi.
- Nnipa dodow no ara betumi akura asaabo dwumadi mu yiye wɔ wɔn nkwa nna nyinaa mu . Asaabo a entumi nyɛ adwuma yiye no ntaa mma.
- Sɛ wowɔ nsɛmmisa bi fa eyi ho a, akyinnye biara nni ho sɛ kɔ oduruyɛfo nkyɛn .
Mma ɛnhaw wo, nnipa pii betumi atra ase sɛnea ɛsɛ, apɔwmuden wɔ tebea yi mu!
`Medullary Sponge Asaabo, Cacchi-Ricci Yareɛ, asaabo mu yareɛ, asaabo mu aboɔ, nsuo mu yareɛ, asaabo mu akisikuru, asaabo mu yareɛ a wɔawo no, asaabo mu akisikuru, nephrocalcinosis, hematuria, asaabo akwahosan Sinhala











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