Ɛtɔ da bi a, nyarewa a yɛn mma nya no bi yɛ nea emu yɛ den yiye. Na nnuru a wɔde ma wɔn no nso yɛ soronko. Ɛnnɛ yɛrebɛka aduru titiriw a ɛte saa biako ho asɛm. Wɔfrɛ saa aduru yi Odevixibat, a wɔde ma mmofra binom de sa honam ani yaw a wontumi nnyina ano a mmerɛbo mu yare bi a wɔntaa nhu de ba no. Sɛ oduruyɛfo no akyerɛw wo ba no aduru yi a, ɛnde asɛm yi bɛyɛ nea ɛho hia wo kɛse.
Aduru bɛn na Odevixibat yɛ?
Sɛ yɛbɛka no tiawa a, Odevixibat yɛ aduru a wɔde ma de siw ɛyaw a ɛboro so a ɔhaw bi a ɛwɔ wo ba mmerɛbo mu de ba no ano. Wɔde gua so din Bylway frɛ no.
Wɔ aduruyɛ mu no, eyi ka nnuru bi a wɔfrɛ no ileal bile acid transporter (IBAT) inhibitors ho . Eyi kyerɛ sɛ saa aduru yi hwɛ sɛnea bile acid a ɛwɔ yɛn dwensɔtwaa mu no san kɔ nipadua no mu no so.
Wɔde saa aduru yi di dwuma titiriw de siw ɛyaw ano wɔ ayarefo a wɔwɔ tebea bi a wɔfrɛ no Progressive Familial Intrahepatic Cholestasis (PFIC) mu . PFIC yɛ awosu mu tebea a ɛntaa nsi a esiw bile a efi mmerɛbo mu nkwammoaa mu no kwan. Eyi ma bile boaboa ano wɔ nipadua no mu, na ɛma ɛyɛ yaw a wontumi nnyina ano. Odevixibat yɛ adwuma denam nea ɛde ɛyaw no ba titiriw a ɛhyɛ so no so.
Nneɛma a ɛsɛ sɛ woka kyerɛ wo duruyɛfo ansa na woafi ase anom nnuru
Ansa na wode saa aduru yi bedi dwuma no, ɛho hia sɛ wode wo anaa wo ba no akwahosan ho nkyerɛkyerɛmu a edi mũ ma wo duruyɛfo. Hwɛ hu sɛ wobɛka nea edidi so yi ho asɛm titiriw:
- Vitamin a enni mu: Sɛ oduruyɛfo bi aka akyerɛ wo sɛ vitamin A, D, E, anaa K sua wɔ wo mogya mu a, ka kyerɛ wɔn.
- Nyinsɛn: Sɛ woanyinsɛn, anaasɛ woreyɛ nhyehyɛe sɛ wobɛwo akokoaa nnansa yi ara a, ɛsɛ sɛ woka kyerɛ wo duruyɛfo.
- Sɛ woyɛ ɛna a ɔma nufu a: Sɛ woyɛ ɛna a ɔma nufu a, hwɛ hu sɛ wobɛbɔ ɔyarehwɛfo no amanneɛ.
Sɛ wo ne oduruyɛfo bɛkasa a womfa nsɛm a ɛte sɛɛ nsie a, ɛho hia yiye ma wo ne wo ba no ahobammɔ.
Ɔkwan pa a wɔfa so de aduru no di dwuma
Sɛnea ɛbɛyɛ na woanya aduru yi so mfaso kɛse no, ɛho hia yiye sɛ wode di dwuma yiye. Fa dodow a ɛfata, wɔ bere a ɛfata mu, sɛnea wo duruyɛfo akyerɛ wo no.
| Afutuo | Sɛnea wɔyɛ no |
|---|---|
| Nnuru a wɔnom | Fa bere koro no ara da biara, fa nsu kuruwa pa. Ɛyɛ papa sɛ wode bɛka adidi ho. |
| Capsule no a wobɛmene | Mene capsule no nyinaa . Mmubu, nbubu, anaa nwe esiane biribiara nti. |
| Sɛ ɛyɛ den sɛ wobɛmene a | Sɛ ɛyɛ den ma wo sɛ wobɛmene capsule no a, fa ahwɛyiye bue mu, fa powder a ɛwɔ mu no fra aduan a ɛyɛ den te sɛ yogurt anaa apɔw-mu-teɛteɛ nkaribo abien, na mene ntɛm a wunwe. Mfa saa aduru yi nfra nsuo (nsuo, nufusuo, nsuo) mu da. |
| Ne nnuru afoforo | Sɛ worenom nnuru a ɛtew srade so (bile acid binding resins) te sɛ Cholestyramine, Colesevelam, anaa Colestipol a, fa nnɔnhwerew 4 ansa na woanom Odevixibat anaa nnɔnhwerew 4 akyi. |
Bere bɛn na ɛsɛ sɛ wɔde saa aduru yi ma mmofra?
Nnuruyɛfo kamfo saa aduru yi kyerɛ nkokoaa a wɔadi asram 3 wɔ nsɛm titiriw bi mu. Nanso, nneɛma bi wɔ hɔ a ɛsɛ sɛ yɛhwɛ yiye wɔ ho. Enti, sɛ wode aduru yi rema wo ba a, di oduruyɛfo no akwankyerɛ akyi pɛpɛɛpɛ.
Sɛ wonom nnuru pii a, dɛn na ɛsɛ sɛ woyɛ?
Sɛ wususuw sɛ wo anaa wo ba no anom aduru yi dodo a, ntwentwɛn wo nan ase.
Frɛ Ɔman Awuduru Ho Amanneɛbɔbea a ɛwɔ Colombo Ɔman Ayaresabea hɔ ntɛm ara . Anaasɛ kɔ ayaresabea a ɛbɛn wo no Emergency Treatment Unit (ETU) .
Na sɛ mepa nnuru dodow bi nso ɛ?
Sɛ wo werɛ fi sɛ wobɛnom dose bi a, fa no bere a woakae ara pɛ. Nanso, sɛ ɛkame ayɛ sɛ bere aso sɛ wobɛma wo dodow a edi hɔ no a, twa dodow a woayera no so na fa dodow a edi hɔ no wɔ bere a woahyɛ da ayɛ no mu.Mfa nnuru mmɔho abien da mfa nsiesie dodow a wo werɛ afi no.
Nneɛma afoforo a ebia ɛne aduru yi bedi nkitaho
Nnuru bi betumi ne Odevixibat adi nkitaho, titiriw sɛnea yɛadi kan aka no, ne nnuru a ɛwɔ bile acid binding resins kuw no mu.
- Cholestyramine a wɔde yɛ aduru
- Colesevelam na ɔkyerɛwee
- Colestipol na ɔkyerɛwee
Saa list yi nwie pɛyɛ. Enti, ɛho hia yiye sɛ wobɛka nnuru a worenom nyinaa (a nnuru a wɔde sa tebea afoforo, vitamin, ne nhabannuru a wɔde di dwuma wɔ amanne kwan so ka ho) kyerɛ wo duruyɛfo.
Nneɛma a ɛsɛ sɛ wohwɛ yiye wɔ ho bere a worenom nnuru no
- Hwɛ a wobɛkɔ akɔhwɛ wo daa: Hwɛ hu sɛ wobɛkɔ wo duruyɛfo nhyehyɛe a wɔayɛ ama wo anaa wo ba no nkyɛn. Wo ne wo duruyɛfo nkasa mfa nkyerɛ sɛ ebia wo yare no ho sɛnkyerɛnne no reyɛ yiye anaasɛ ɛresɛe.
- Vitamins: Ɛho hia sɛ wohwɛ hu sɛ worenya vitamin ahorow a wuhia (titiriw vitamin A, D, E, ne K a srade wom) bere a worenom saa aduru yi no. Wo ne wo duruyɛfo nkasa mfa nnuan a wudi ne nnuru biara a wode bɛka ho a worenom ho asɛm.
- Mogya mu nhwehwɛmu: Bere a woresa yare no, ebia wo duruyɛfo bɛhyɛ sɛ wɔmfa mogya nyɛ adwuma bi mfa nhwɛ nneɛma te sɛ wo mmerɛbo dwumadi. Mma nntwa wɔn so.
Dɛn ne nsunsuanso bɔne a ebetumi afi mu aba?
Te sɛ aduru biara no, Odevixibat betumi de ɔhaw ahorow bi aba. Eyinom bi betumi ayɛ aniberesɛm, enti ɛho hia sɛ wohu.
| Nsunsuanso bɔne no su | Mpopoeɛ |
|---|---|
| Nneɛma bɔne a ɛsɛ sɛ wɔbɔ ho amanneɛ kyerɛ oduruyɛfo no ntɛm ara | |
| Nneɛma a ɛma obi ho yɛ no hyew | Honam ani akisikuru, ɛyaw a emu yɛ den, anim, ano anaa tɛkrɛma a ɛho ahonhon. |
| Nsɛnkyerɛnne a ɛkyerɛ sɛ mmerɛbo apira | Nsu a ɛyɛ kɔkɔɔ anaa bruu tuntum, atenka a ɛyɛ mmerɛw, atiridiinini, aduan ho akɔnnɔ a ɛyera, ɛyaw wɔ yafunu no atifi nifa so, na aniwa anaa honam ani yɛ kɔkɔɔ (jaundice). |
| Ayamtuo | Atiridiinini a ɛkɔ so daa. |
| Nneɛma a ɛsɛ sɛ woka kyerɛ wo duruyɛfo sɛ ɛkɔ so anaasɛ ɛhaw adwene a | |
| Yafunu mu yaw | Yafunu mu yaw wɔ ɔkwan a ɛkɔ akyiri so. |
| Ɔfe a wɔfe | Ɔfe a wɔfe. |
Ɔkwan bɛn so na ɛsɛ sɛ wode w’aduru sie?
- Fa sie baabi a mmofra ne afieboa ntumi nkɔ hɔ .
- Fa sie wɔ dan mu hyew (a ɛwɔ digrii Celsius 20 kosi 25 ntam) , wɔ baabi a ɛhɔ yɛ kusuu.
- Mfa nnuru a ne bere atwam nni dwuma. Tow wɔn gu.
Wobɛyɛ dɛn ayi nnuru a wɔmfa nni dwuma no afi hɔ?
Ɛnyɛ adwene pa sɛ wobɛtow nnuru a ne bere atwam anaa nea wompɛ agu nwura mu anaa tiafi mu. Bisa wo duruyɛfo ma ɔmma no afotu. Sɛ wɔka sɛ ɛnyɛ hwee sɛ wɔbɛtow aduru no agu nwura mu a, yi nnuru no fi toa no mu, de fra biribi te sɛ tii nhaban a wɔde adi dwuma, kɔfe a wɔayam, anaa dɔte mu, na fa gu kotoku a wɔatoto mu denneennen mu.
Nkrasɛm a Wɔde Kɔ Fie
- Odevixibat yɛ aduru a wɔkyerɛw ma ɛyaw a mmerɛbo mu yare pɔtee bi a wɔfrɛ no PFIC de ba na ɛsɛ sɛ wɔde di dwuma bere a oduruyɛfo akamfo akyerɛ nkutoo.
- Mene capsule no nyinaa. Mma nntutu anaa nwe. Sɛ ɛyɛ den ma wo sɛ wobɛmene nkutoo a, fa fra aduan a ɛyɛ den.
- Ka nnuru afoforo a wonom nyinaa ne w’ayaresa tebea kyerɛ wo duruyɛfo.
- Sɛ wuhu nneɛma bɔne bi a anibere wom, te sɛ akisikuru ho sɛnkyerɛnne anaa mmerɛbo a asɛe ho sɛnkyerɛnne (aniwa a ɛyɛ kɔkɔɔ, nsu a ɛyɛ tuntum) a, ka kyerɛ wo duruyɛfo ntɛm ara.
- Sɛ wonom boro so a, kɔ National Poison Information Center anaa ETU ntɛm ara.
- Sɛ wowɔ nsɛmmisa bi fa saa aduru yi ho a, hwɛ hu sɛ wo ne wo duruyɛfo bɛkasa.











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