So wo ba no reyɛ bruu mpofirim? Ebetumi ayɛ Tetralogy of Fallot.

So woasuro pɛn bere a wo ba ketewa no dan bruu mpofirim no? Anaasɛ ɛyɛ den ma no sɛ ɔbɛhome bere a ɔrema nufu, ɔresu, anaa ɔredan ne ho? Ɛyɛ ade a ɛfata sɛ ɛna anaa agya biara besuro bere a ohu nneɛma a ɛte sɛɛ no. Ɛnnɛ yɛreka Tetralogy of Fallot , komayare a wɔde awo obi a ebetumi de sɛnkyerɛnne ahorow te sɛ eyinom aba ho asɛm. Ɛwom sɛ ebia edin no bɛyɛ te sɛ nea ɛyɛ den kakra de, nanso momma yɛnkyerɛkyerɛ mu tiawa.

Dɛn ankasa ne Tetralogy of Fallot?

Sɛ yɛbɛka no tiawa a, Tetralogy of Fallot yɛ koma mu dɛmdi anan a ɛwɔ awo mu a wɔaka abom. Wɔsan frɛ no komayare a wɔde awo obi. Ɛyɛ ɔhaw a ɛba bere a koma no nyin bere a akokoaa no renyin wɔ awotwaa no mu no. Eyi ma mogya a oxygen pii wom (mogya kɔkɔɔ) no frafra mogya a oxygen nni mu (mogya bruu) no mu. Afei mogya a wɔadi afra yi na koma no de kɔ nipadua no mu. Ne saa nti, akwaa a ɛwɔ nipadua no mu no nnya mframa pa a ɛdɔɔso. Wɔ nnuruyɛ mu no, yɛfrɛ tebea yi hypoxemia . Nea ɛbɛyɛ na yɛate eyi ase yiye no, momma yɛnhwɛ sɛnea koma a ɛte apɔw yɛ adwuma.

Sɛnea koma a ɛte apɔw yɛ adwuma

Fa no sɛ yɛn koma te sɛ ofie a ɛwɔ adan anan. Pia abien na ɛwɔ abansoro a ɛwɔ soro no so (atria) ne adan akɛse abien wɔ abansoro a ɛwɔ fam no so (ventricles). Valve ahorow wɔ saa adan yi ntam te sɛ apon. Ɔfasu (septum) na ɛtete koma no nifa ne benkum ntam. 1. Nifa so: Nipadua no mogya bruu a oxygen nni mu no fa ntini a ɛwɔ soro ne ntini a ɛwɔ fam no mu kɔ ahurututu nifa no mu. 2. Efi hɔ no, mogya no fa valve (tricuspid valve) bi mu kɔ nifa so ventricle no mu. 3. Wofi nifa so ahurututu no mu no, wɔde mogya bruu yi fa valve foforo (pulmonic valve) mu kɔ ntini titiriw (pulmonary artery) a ɛkɔ ahurututu no mu no mu. 4. Ahurututu no mu: Wɔde mframa pa ahyɛ mogya yi mu foforo, na ɛbɛyɛ mogya kɔkɔɔ kronkron. 5. Benkum so: Mogya kɔkɔɔ a oxygen pii wom yi san kɔ koma no benkum so. 6. Efi hɔ no, ɛfa valve (mitral valve) bi mu kɔ benkum ventricle no mu. 7. Awiei koraa no, wɔde mogya kɔkɔɔ kronkron yi a efi benkum so ahurututu no mu fa nipadua no ntini kɛse (aorta) no mu kɔ nipadua no nyinaa mu. Eyi ne ɔkwan a yɛn akwaa ahorow no nya mframa pa a ehia na ama wɔatumi atra ase no.

Mfomso anan a ɛba wɔ Tetralogy of Fallot (The "Tetralogy") mu no .

Wɔ akokoaa a ɔwɔ Tetralogy of Fallot koma mu no, sintɔ atitiriw anan na ɛsakra ɔkwan a ɛfata a yɛaka ho asɛm no.

Dɛn na ɛde tebea yi ba?

Wonnya nhuu nea ɛde eyi ba ankasa. Ɛyɛ dɛmdi a ɛba bere a koma no afã horow no reyɛ ayɛ ntɛm wɔ akokoaa no nyin mu wɔ awotwaa no mu no. Ɛnyɛ wo mfomso, na saa ara nso na ɛnyɛ biribi a woyɛe wɔ nyinsɛn mu. Enti nte afobu nka wɔ ho.

So wo ba no nso wɔ saa sɛnkyerɛnne ahorow yi?

Mmofra dodow no ara a wɔwɔ Tetralogy of Fallot no da sɛnkyerɛnne ahorow adi wɔ wɔn nkwa afe a edi kan no mu.

• Nsu a ɛyɛ bruu (Cyanosis): .Eyi ne sɛnkyerɛnne titiriw no. Akokoaa no anofafa, ne tɛkrɛma, ne honam ani, ne ne nnadewa nya kɔla a ɛyɛ bruu anaa kɔkɔɔ.
• "Tet Spells / Hypercyanosis": Eyi yɛ ade a ɛho hia yiye. Sɛ akokoaa su, ɔnom nufusu, ɔbɔ mmɔden sɛ ɔbɛkɔ tiafi, anaa ɔsɔre anɔpa a, ebia ne kɔla yɛ bruu a emu dɔ mpofirim, ɛbɛyɛ den sɛ ɔbɛhome, na ne ho atɔ no kɛse. Ɛtɔ mmere bi mpo a, ebia wɔn adwene bɛyera. Saa tebea yi tumi di simma kakraa bi kosi nnɔnhwerew pii.
• Ɔhome a ɛyɛ den : Akokoaa no brɛ ntɛmntɛm na ɔda bere a watu mmirika akɔ akyirikyiri na wadi agoru kakra no.
• Squatting: Sɛ abofra ketewa a ɔretu mmirika brɛ esiane agodie nti a, ɔbɛtra ase mpofirim a wɔatwe wɔn nkotodwe akɔ ne moma so (squatting). Eyi ma mogya dodow a ɛkɔ wɔn ahurututu mu no yɛ kɛse a wonnim, na ɛma ɛyɛ mmerɛw sɛ wɔbɛhome .
• Onyin a entumi nyɛ adwuma yiye: Ebia akokoaa no mu duru , ne nyin, ne ne nyin bɛyɛ brɛoo asen mmofra afoforo.

Bere bɛn na ɛsɛ sɛ wohwehwɛ aduruyɛ mu afotu?

Mma wo ba no ayaresabea a ɔwɔ ɔsram biara no nmpa wo ti so. Oduruyɛfo no betumi ahu saa tebea horow yi bere a ɔreyɛ wo ba no mu nhwehwɛmu no. Sɛ wowɔ sɛnkyerɛnne ahorow a edidi so yi mu biara a, kɔ oduruyɛfo nkyɛn ntɛm ara.

• Sɛ akokoaa no were ne n’ano dan bruu a.
• Sɛ ɛyɛ den ma wo sɛ wobɛhome a .
• Sɛ wobrɛ bere a worenom nufu anaa woresu a.
• Sɛ wote nka sɛ wo nyin rekɔ fam a.

Sɛ ntɛmpɛ a edidi so yi si a, fa onipa no kɔ ayaresabea Emergency Department (ETU) a ɛbɛn wo no ntɛm ara:

• Tet Nkɔmhyɛ
• Ɛyɛ den yiye sɛ wobɛhome.
• Akisikuru a ɛma obi ho kyere no
• Nnipa a wɔtotɔ piti
• Ɔbrɛ anaa mmerɛwyɛ dodo

Ɔkwan bɛn so na wohu yare no? (Nsɔhwɛ ne Nhwehwɛmu a Wɔyɛ) .

Wo duruyɛfo bɛhwɛ akokoaa no mu, atie sɛnea koma bɔ, na sɛ adwenem naayɛ bi wɔ hɔ a, ɔde wo bɛkɔ akɔyɛ nhwehwɛmu mpɛn pii.

• Chest X-ray: Eyi hwɛ sɛnea koma no te. Wɔ Tetralogy of Fallot mu no, koma no betumi ayɛ te sɛ "boot-shaped" efisɛ ventricle nifa no ayɛ kɛse.
• Electrocardiogram ( ECG ): Sɔhwɛ a ɛyaw nnim a ɛkyerɛ sɛnea koma no mu anyinam ahoɔden yɛ adwuma.
• Echocardiogram (Echo) a wɔde kyerɛw nsɛm: .Eyi ne sɔhwɛ a ɛho hia na ɛyɛ pɛpɛɛpɛ sen biara. Ɛte sɛ scan. Etumi hu biribiara a ɛwɔ koma no mu pefee, te sɛ adan, valve, ntokuru ( VSD ), ne narrowing (PS).
• Koma mu Catheterization: Wɔ tebea horow bi mu no, wɔyɛ nhwehwɛmu yi ansa na wɔayɛ oprehyɛn de ahu koma no nhyɛso ne oxygen dodow, na wɔahwɛ sɛnea ntini no te yiye. Wɔ sɔhwɛ yi mu no, wɔde afiri ketewaa bi fa ntini bi a ɛwɔ asen no mu kɔ koma no mu.

Dɛn ne ayaresa ahorow no?

Ayaresa biako pɛ a ɛtra hɔ daa a wɔde sa Tetralogy of Fallot ne oprehyɛn .

Sɛ wonya "Tet Spell" a, dɛn na woyɛ?

Sɛ wo ba no dan bruu kɛse mpofirim a, ɛho hia yiye sɛ wo bo dwo . 1. Fa akokoaa no to n’akyi, na twe nkotodwe no kɔ ne moma so (gyinabea a efi kotodwe so kɔ ne koko so) . 2. Fa akokoaa no kɔ ayaresabea ntɛm ara. Wɔ ayaresabea hɔ no, wɔbɛma akokoaa no oxygen ne nnuru te sɛ propranolol a ɔde bedi "tet spells" so.

Sɛɛgyiri

Bere a wɔbɛyɛ oprehyɛn no gyina sɛnea akokoaa no yare no ho sɛnkyerɛnne no mu yɛ den so. Wɔtaa yɛ oprehyɛn wɔ nkwa mfe abien a edi kan no mu.

• Palliative Surgery (Blalock-Taussig shunt): Nkokoaa binom sua koraa anaasɛ wɔyɛ mmerɛw na ebia wontumi nnyina oprehyɛn no nyinaa ano. Wɔ tebea horow a ɛtete saa mu no, wɔyɛ nkitahodi ketewaa bi a ɛte sɛ afiri bi a ɛda ntini bi a ɛwɔ nipadua no mu ne ntini bi a ɛwɔ ahurututu mu ntam ma mogya dodow a ɛkɔ ahurututu no mu no yɛ kɛse. Eyi betumi aboa akokoaa no ma wayɛ kɛse kakra na wanya ahoɔden.
• Oprehyɛn a Wɔde Siesie Nnipa Nyinaa: Wɔ eyi mu no, wɔde aduru bi to tokuru a ɛwɔ koma no mu (VSD) no mu, na wɔtrɛw ɔkwan a ɛyɛ teateaa a ɛkɔ ahurututu no mu (PS) no mu. Wɔ oprehyɛn yi akyi no, mogya a ɛkɔ koma no mu no san kɔ sɛnea na ɛte kan no.

Esiane sɛ nnuruyɛ mu mfiridwuma anya nkɔso nnɛ nti, oprehyɛn yi di yiye paa.

Oprehyɛn akyi...

Wɔ oprehyɛn a edi mu akyi no, mmofra dodow no ara tumi tra ase sɛnea ɛsɛ a wonni sɛnkyerɛnne anaa anohyeto biara. Wobetumi akɔ sukuu, adi agoru, ayɛ adwuma daakye, na wɔaware. Nanso, wɔ oprehyɛn akyi mpo no, ɛho hia sɛ wo ne oduruyɛfo di wɔn akyi daa wɔ wɔn nkwa nna nyinaa mu. Ɛtɔ mmere bi a, nsakrae a ɛba koma no mu (arrhythmias) betumi aba, enti ɛho hia sɛ wɔkɔhwɛ wɔn daa. tetralogy of fallot, komayare, mmofra ayaresa, akokoaa bruu, cyanosis, tet spells, awo mu dɛmdi, koma mu dɛmdi a wɔde awo obi, koma mu tokuru, VSD