Ni an ye "sugunɛbilenni" daɲɛw mɛn, an caman bɛ siran o yɔrɔnin bɛɛ la, tiɲɛ tɛ? Nka fɛn min nafa ka bon kosɛbɛ aw ka kan ka min dɔn, o ye ko kuru minnu bɛ bɔ kunsɛmɛ na, olu bɛɛ tɛ kansɛri ye. Tumu suguya dɔw fana bɛ yen minnu tɛ kansɛri ye, o kɔrɔ ye ko u tɛ jɛnsɛn farikolo yɔrɔ wɛrɛw la, nka u bɛ se ka bonya ka taa a fɛ ka taamasiɲɛ dɔw lase mɔgɔ ma. Dɔgɔtɔrɔw b’o wele ko ‘tumu ɲumanw’. O la bi, an ka kuma nin kunkolodimi ninnu kan minnu tɛ kansɛri ye.
Min nafa ka bon, o ye ko hali ni o kurukuru ninnu tɛ kansɛri ye, u man kan ka ban. Sabula, hali ni a man ca kosɛbɛ, o dɔw bɛ se ka wuli kɔfɛ ka kɛ kansɛri ye. O la, a nafa ka bon ka to ka taa dɔgɔtɔrɔso la tuma bɛɛ ani ka sɛgɛsɛgɛli wajibiyalenw kɛ.
Meninjiyɔmu suguya min ka teli ka kɛ, o ye
Nin ye kunsɛmɛnasumaya suguya ye min ka teli ka kɛ. A bɛ kɛ kunsɛmɛnasumaya bɛɛ tila sabanan ɲɔgɔn ye. U bɛ Kɛ an ka kùnkolo ni kɔkolo lamini lakananifɛnw na, minnu bɛ Weele ko meninges (sɔgɔsɔgɔninjɛ).
Musow ka teli ka nin kuru suguya in sɔrɔ ka tɛmɛ cɛw kan siɲɛ fila. Nin fɛn ninnu fana bɛ se ka dɔ fara farati kan:
- Ni a bɛ kɛ ni fiɲɛ ye min ka bon kosɛbɛ.
- Ni bangekɔlɔsi banaw bɛ aw la i n’a fɔ `(Neurofibromatose type 1 (NF1))` walima `(type 2 (NF2))`.
A ka ca a la, o kurukuru ninnu tɛ taamasiɲɛw jira fo n’u ka bon. Ni kuru bɛ bonya, a taamasiɲɛw i n’a fɔ:
- Kunkolodimi
- Kɔnɔboli
- Dusukunnata walima fɔɔnɔ
- Mɔgɔya bɛ Changé ani hakili ɲagami
- Yeli gɛlɛyaw
- Kuma gɛlɛya
- Mɛnbaliya walima mankan bɛ tulo la
- Farikolo fanga dɔgɔyali
Schwannoma (sɔgɔsɔgɔninjɛ) .
O kurukuru ninnu tɔgɔ dara u bɛ bɔ farikolokisɛ suguya min na: Schwann selilɛriw, minnu bɛ farikolokisɛw lamini.
Nin suguya in suguya min ka teli ka kɛ, o bɛ wele ko vestibular schwannoma. Aw ka dɔgɔtɔrɔ bɛ se fana k’o wele ko acoustic neuroma. O bɛ nɔ bila nɛrɛ la min bɛ bɔ an tulo kɔnɔna na ka taa a bila kunsɛmɛ na ani ka farikolo balansi kɔlɔsi.
Bana min bɛ sɔrɔ cɛya la min bɛ wele ko `(NF2)`, olu ka teli ka nin kuru ninnu sɔrɔ. Yan fana, musow bɛ faratiba la.
A taamasiɲɛ kunbabaw:
- Lamɛnni dɛsɛ
- Mankan min bɛ mankan walima mankan dɔ mɛn tulo la
- Dimi bɛ mɔgɔ la
- Dumuni munumunu gɛlɛya
- Balance gɛlɛyaw
Pituitaire adenoma (tumu min bɛ sɔrɔ ɲɛgɛnɛsira la min bɛ ɔrimɔniw kɔlɔsi) .
O kurukuru ninnu bɛ sɔrɔ ɲɛgɛnɛsira la, min bɛ sɔrɔ kunsɛmɛ da la. O glande in ye hormones (hormones) dilanyɔrɔba ye ani ka gland wɛrɛw kɔlɔsi an farikolo la.
Ninnu fana ye kuru suguya dɔw ye minnu ka teli ka sɔrɔ. Baliku duuru o duuru, kelen ɲɔgɔn bɛ se ka kɛ ni pituitaire kuru fitiniw ye kosɛbɛ. Nka o fanba tɛ bonya abada walima ka gɛlɛyaw lase mɔgɔ ma.
Bana min bɛ sɔrɔ cɛya la ``Multiple Endocrine Neoplasia type 1 (MEN1)`` bɛ mɔgɔ minnu na, olu ka bana ninnu sɔrɔli farati ka bon.
Pituitaire kuru dɔw bɛ ɔrimɔni (hormones) dilan. Olu bɛ wele ko ‘tumu baarakɛtaw’. A taamasiɲɛw bɛ bɔ ni kuru bɛ ɔrimɔni bɔ, ani ni o kɛra, ɔrimɔni jumɛnw.
- Prolactin hormone : Musow bɛ se ka kalolabɔ kɛ cogo la min tɛ kɛ tuma bɛɛ walima koli tɛ kɛ. Cɛw bɛ se ka sinji bonya.
- ACTH hormone : O bɛ kɛ sababu ye ka bana dɔ taamasiɲɛw jira min bɛ wele ko ``Cushing ka bana''. Misali la, farikolo girinya, joginni nɔgɔya, ani barikantanya.
- TSH ɔrimɔni : A bɛ sɔgɔsɔgɔninjɛ taamasiɲɛw jira minnu bɛ baara kɛ kojugu (Hyperthyroïdie), i n’a fɔ farikolo girinya dɔgɔyali, dimi, ani sumaya kojugu.
Taamasiɲɛ wɛrɛ minnu ka teli ka ye:
- Kunkolodimi
- Yeli bɔnɛni walima yeli fila
- Cɛnimusoko nege bɛ dɔgɔya
- Bangekɔlɔsi
- Taamacogo bɛ Changé
- Kisɛya sɔrɔli kun tɛ
Tumu suguya wɛrɛw minnu tɛ kansɛri ye
Numu suguya damadɔ wɛrɛw bɛ yen.
Ɲɛgɛnɛsiraw (Hémangioblastoma).
Olu bɛ yiriwa joli siraw la. U bɛ se ka sɔrɔ kunsɛmɛ na, kɔkolo la walima ɲɛkisɛ ɲɛkisɛ la. U bɛ ye mɔgɔw la minnu ka bana bɛ sɔrɔ cɛya la min bɛ wele ko ``Von Hippel-Lindau syndrome.`` A taamasiɲɛw bɛ se ka kɛ farikolo yɔrɔw sɔgɔsɔgɔli ye, fanga dɔgɔyali, kungolodimi, kɔnɔboli, ani taama gɛlɛya.
Kungolo ni farinjiyɔmu
Olu bɛ daminɛ farikolokisɛw la minnu bɛ kunsɛmɛ da la, pituitaire gland kɛrɛfɛ. U bɛ se ka kɛ foroko gɛlɛnw ye walima minnu falen don ji la (cysts). U ka teli ka kɛ denmisɛnniw na minnu si bɛ san 5 ni san 14 cɛ ani balikuw minnu si tɛmɛna san 45. U bɛ se ka taamasiɲɛw bila mɔgɔ la i n’a fɔ fasa, minnɔgɔ kojugu, denmisɛnniw ka bonyabaliya, ani yelikɛcogo caman.
Glioma (Gliome) (Gliome) (Gliome).
Olu bɛ bɔ glial cellules la minnu bɛ nerve cellules dɛmɛ kunsɛmɛ ni kɔkolo la. U tilalen dòn kàlanso damadɔw la. Kalanso fɔlɔ ni filanan tɛ kansɛri ye, wa u bɛ bonya dɔɔni dɔɔni. Kalanso 3nan ni 4nan ye kurukuruw ye minnu bɛ juguya, minnu bɛ bonya joona.
| Glioma Grade (Glioma) hakɛ | Ɲɛfɔli nɔgɔman |
|---|---|
| Kalanso 1nan | Kɔnɔnatumuw bɛ i n’a fɔ selilu gansanw. U bɛ bonya dɔɔni dɔɔni kosɛbɛ. |
| Kalanso 2nan | Fɛn misɛnninw bɛ kɛ farikolokisɛw la. Furakɛli kɔfɛ, a bɛ se ka segin ka kɛ kuru ye min ka bon. |
| Kalanso 3nan | Kansɛri jugumanba min kɔnɔ, farikolokisɛw bɛ tila joona. |
| Kalanso 4nan | Kɔnɔnatumuw tɛ i n’a fɔ farikolokisɛ nɔgɔmanw fewu. O ye kansɛri ye min ka jugu kosɛbɛ ani a bɛ jɛnsɛn joona. |
Dɔgɔtɔrɔw bɛ a dɔn cogo di ni o kurukuruw bɛ yen?
Aw ka dɔgɔtɔrɔ bɛna aw ɲininka fɔlɔ aw ka bana taamasiɲɛw la, i n’a fɔ kungolodimi ni kirinni. O kɔ, walasa ka bana sɛgɛsɛgɛli dafalen kɛ, u bɛ se ka nin sɛgɛsɛgɛli ninnu dɔ la kelen walima caman kɛ:
- CT Scan: O ye fɛɛrɛ ye min bɛ kɛ ni X-ray barikamaw ye walasa ka hakili ja caman dilan.
- MRI Scan: O ye fɛɛrɛ ye min bɛ kɛ ni magɛnni barikamaw ni arajo fiɲɛw ye walasa ka hakili ja jɛlenba dilan.
- Biopsie : Farikolo yɔrɔ fitininba dɔ bɛ bɔ tumu na ka a lajɛ ni mikroskɔpu ye walasa ka a dɔn ni kansɛribanakisɛw bɛ yen.
- Lumbar Puncture / Spinal Tap : Nin sɛgɛsɛgɛli in bɛ kɛ walasa ka a lajɛ ni farikolokisɛw tɛ kɔkolo la.
- Joli ni sugunɛ sɛgɛsɛgɛli : Olu bɛ dɛmɛ ka ɔrimɔni walima fɛn wɛrɛw ɲini minnu bɛ bɔ farikolo la tumu fɛ.
O furakɛcogo jumɛnw bɛ yen?
Furakɛli kɛcogo bɛ bɔ kuru suguya, a bonya ani a sigiyɔrɔ la.
- Tumu misɛnniw: Furakɛli si tɛ se ka kɛ. Tuma caman na, aw ka dɔgɔtɔrɔ bɛna CT walima MRI sɛgɛsɛgɛli kɛ walasa ka a lajɛ ni kuru bɛ ka bonya.
- Tumu belebelebaw : Opereli bɔli ye furaba ye. Operelikɛla bɛna a ɲini ka kuru caman bɔ a la ni a bɛ se ka kɛ.
- Furakɛli min bɛ kɛ ni fiɲɛ ye:Nin ye fɛɛrɛ ye min bɛ kɛ ni rezow ye minnu fanga ka bon walasa ka kuruw dɔgɔya. Nin furakɛli in bɛ kɛ tumuw la minnu tɛ se ka bɔ pewu opereli fɛ walima minnu seginna opereli kɔfɛ. Stereotactic Radiosurgery ye kɛnɛyaji furakɛli suguya kɛrɛnkɛrɛnnen ye min bɛ kuru laɲini k’a ɲɛsin a yɛrɛ ma, ka tiɲɛni dɔgɔya lamini farikolo yɔrɔ kɛnɛmanw na.
Aw ka dɔgɔtɔrɔ bɛna aw dɛmɛ ka furakɛli fɛɛrɛ ɲuman sugandi aw ye, ka baro kɛ aw ka sugandiliw bɛɛ kan ni aw ye. O la sa, kana desizɔn si ta i yɛrɛ ma. Aw bɛ baro kɛ u kan ni aw ka dɔgɔtɔrɔ ye tuma bɛɛ.
Take-Home cikan
- Aw kana siran ni aw ye "sɔgɔsɔgɔninjɛ" daɲɛ mɛn. Tumu minnu bɛ bɔ kunsɛmɛ na, olu bɛɛ tɛ kansɛri ye. Tumu suguya caman bɛ yen minnu tɛ kansɛri ye.
- Hali ni a ye kuru ye min tɛ kansɛri ye, ni a bonya bɛ bonya, a bɛ se ka taamasiɲɛw lase mɔgɔ ma i n’a fɔ kungolodimi, yeli gɛlɛya, ani ɲɛnamini.
- Ni taamasiɲɛ dɔw bɛ aw la minnu tɛ deli ka kɛ, minnu bɛ to sen na, aw ye aw jija ka taa dɔgɔtɔrɔso la walasa ka laadilikan sɔrɔ.
- Aw ka dɔgɔtɔrɔ bɛna a latigɛ ni furakɛli ka kan ka kɛ walima ni a man kan ka kɛ ani ni fura min ka kan ka kɛ. O la, a nafa ka bon kosɛbɛ ka tugu dɔgɔtɔrɔ ka laadilikanw kɔ.











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