Ðe nèsena le ɖokuiwò me ɣeaɖewoɣi abe ɖe nèle
gbɔgbɔm ne èle atrakpui liam alo zɔ mɔ kpui aɖea? Alo ɖe nèsena le ɖokuiwò me be ɖeɖi mete ye ŋu abe tsã ene o, eye fifia ɖeɖi tea ŋuwò ŋutɔ ne èle dɔ suewo wɔm gɔ̃ hã? Susu ɖeka si ta nu siawo nadzɔ ɖo ate ŋu anye tɔtrɔ si ava wò lãkusiwo me. Enyo, Pulmonary Fibrosis, si nye dɔléle si nana lãkusiwo sesẽna vivivi eye wònana gbɔgbɔ sesẽna, ye nye nusi ŋu míaƒo nu tsoe egbea.
Nuka tututue nye Aklã ƒe Dɔléle?
Kpuie ko la, Pulmonary Fibrosis nye lãkusi si le wò lãkusi me ƒe
abi kple eƒe ƒoƒo . Bu eŋu abe abi si le ŋutigbalẽ ŋu ne èxɔ abi ene, nu ma tɔgbe dzɔna le lãkusi me. Esia le aɖuɖɔtoedɔlélewo ƒe ƒuƒoƒo aɖe si woyɔna be interstitial lung disease me. Nusi dzɔna le afisia enye be yakotoku suetɔ kekeake siwo le míaƒe lãkusiwo me, teƒe siwo oxygen gena ɖe eme ne míele gbɔgbɔm la, míeyɔa wo be `(alveoli)`, eye lãkusi siwo ƒo xlã `(alveoli)` mawo la gblẽna. Azɔ kpɔ ɖa, lãkusiwo le abe ƒumebɔbɔ ene. Wogbɔa ya ne míegbɔ ya, eye wotsia ne míegbɔ ya. Gake ne nɔnɔme sia (Pulmonary Fibrosis) do mo ɖa la, lãkusi siwo le lãkusiwo me la
sesẽna eye wosesẽna, eyata womete ŋu ƒoa ya alo ƒoa ƒu nyuie abe tsã ene o. Ɣemaɣie gbɔgbɔ va sesẽna, eye nègbɔa
ya . Gbesiagbedɔ siwo nɔ bɔbɔe tsã gɔ̃ hã ate ŋu ase le eɖokui me fifia be ɖeɖi tea yewo ŋutɔ.
Nu vevitɔe nye be nɔnɔme sia si woyɔna be (Pulmonary Fibrosis) nɔa anyi ɖaa , si fia be esesẽna be woadae keŋkeŋ. Azɔ hã, ate ŋu agblẽ ɖe edzi vivivi le ɣeyiɣi aɖe megbe (vivivivi la, ate ŋu agblẽ ɖe edzi) . Míeyɔa ema be `(progressive pulmonary fibrosis)`.
Ðe lãkusiwo ate ŋu asẽ le susu manɔmeea? Nukae Nye Idiopathic Pulmonary Fibrosis ƒe Dɔléle?
Ẽ, ɣeaɖewoɣi la,
womekpɔa nusi gbɔ lãkusidɔ sia tsona o . Emae nye nusi míeyɔna be `(Idiopathic Pulmonary Fibrosis)` na dɔléle mawo tɔgbe. Nya "idiopathic" gɔmee nye "si womenya nusi gbɔ wòtso o." Zi geɖe la, dɔnɔ akpa gãtɔ siwo ŋu (Pulmonary Fibrosis) le la ƒe `(Idiopathic Pulmonary Fibrosis)` nɔnɔme sia nɔa wo ŋu.
Aleke nàwɔ anya ne aklãdɔléle le ŋuwò? Nukawoe nye dzesiawo?
Dɔléle sia ƒe dzesiwo ate ŋu ato vovo vie tso ame ɖeka gbɔ yi bubu gbɔ, gake dzesi aɖewo li siwo bɔ:
- Yagbɔgbɔ kpui : Yagbɔgbɔ sesẽ, vevietɔ le kamedede bɔbɔe me alo le kamedede vɔ megbe, dɔ aɖe wɔwɔ, alo le ewuwu vɔ megbe.
- Gbɔgbɔ kpui siwo me goglo o: Gbɔgbɔ kabakaba, suesuesuewo, abe ɖe màte ŋu ayɔ wò akɔta o ene.
- Persistent dry cough : Kɔdzi si meɖea ʋuʋudedi o eye meɖina le ɣeyiɣi aɖe megbe o.
- Ðeɖi te eŋu le susu aɖeke manɔmee (Ðeɖiteameŋu: Ðeɖiteameŋu ƒe seselelãme ɣesiaɣi, ne èdɔ alɔ̃ nyuie alo mèwɔa dɔ geɖe o gɔ̃ hã.
- Kpekpeme dzi ɖeɖe kpɔtɔ si womeɖe o : Kpekpeme dzi ɖeɖe kpɔtɔ nuɖuɖumadzroame manɔmee ko.
- Asibidɛ siwo wotsɔ ga ƒo ɖe wo nɔewo ŋu : Ame aɖewo ƒe asibidɛwo kple afɔbidɛwo ate ŋu avuvu eye woalolo, anɔ abe kpẽ ene.
- Ŋutilã ƒe amadede ƒe tɔtrɔ (Cyanosis): Ne oxygen mesɔ gbɔ le ʋua me o la, nuyiwo, ŋkuwo ƒo xlãe, kple asibidɛwo ate ŋu atrɔ azu blɔ, aŋutiɖiɖi, alo ɣie.
Ne dzesi siawo dometɔ ɖeka alo esi wu nenema le ŋuwò la,
anyo wu be nàdi atikewɔlawo ƒe aɖaŋuɖoɖo. Nukatae esia (Pulmonary Fibrosis) dzɔna? Nukawoe gbɔ wòtsona?
Eŋutinunyalawo xɔe se be aklã me fibrosis dzɔna ne lãkusia gblẽ alo dɔdzẽ le eŋu, eye dɔa mehaya nyuie o. Esia fia be ne lãkusiwo dze agbagba be yewoada gbe le wo ɖokui ŋu la, nane gblẽna eye abi ƒe lãkusiwo dzɔna. Nu tɔxɛ geɖewo li siwo ate ŋu ana esia nadzɔ:
- Kadodo ƒe dɔlélewo : Ne dɔlélewo abe Rheumatoid Arthritis (RA), Lupus, alo Scleroderma ene le ŋuwò la, esiawo ate ŋu agblẽ nu le wò lãkusiwo hã ŋu .
- Nutoa me ƒe nɔnɔme: Ke kple atike aɖewo zazã ɣeyiɣi didi ate ŋu agblẽ nu le lãkusi ŋu. Kpɔɖeŋu aɖewoe nye asbestos, silica, kple beryllium. Aklãdɔléle si nu sẽ akpa, si nye aŋɔ, dɔlékui, xeviwo ƒe fu, alo dander aɖewo ƒe nulɔdɔ hã ate ŋu ahe nɔnɔme sia vɛ.
- Granulomatous dɔlélewo: Nɔnɔmewo abe sarcoidosis alo Langerhans cell histiocytosis ene.
- Atike alo atike aɖewo: Atike aɖewo abe amiodarone na dzidɔ, nitrofurantoin na aɖuɖɔtoedɔléle, methotrexate na kansa kple ƒunukpeƒetetedɔ, kple keklẽŋusẽ ƒe atikewɔwɔ na kansa hã ate ŋu agblẽ nu le lãkusi ŋu.
- Sigaretnono: Sigaretnono gblẽa nu le ame ƒe lãkusi ŋu ŋutɔ. Enye nu vevi aɖe si hea Aklãdɔléle hã vɛ.
Gake abe alesi míegblɔe va yi ene la,
le go geɖe me la, womate ŋu ake ɖe nusi koŋ gbɔ wòtso ŋu o.Amekawoe le afɔku gã me be woaxɔ Aklãdɔléle?
Tsɔ kpe ɖe susu siwo míeyɔ ɖe etame ŋu la, ame bubu aɖewo hã le afɔku me vie be woaxɔ dɔléle sia:
- Le amesiwo xɔ wu ƒe 65 gome.
- Le ŋutsuwo gome la, esɔ gbɔ wu nyɔnuwo.
- Ne Aklãdɔléle le ƒomea me la, domenyiŋusẽfianu ate ŋu akpɔ ŋusẽ ɖe ame dzi.
- Le amesiwo ŋu domenyiŋusẽfianu ƒe nɔnɔme aɖewo (DNA ƒe tɔtrɔ) siwo hea dɔlélewo vɛ gome. Le kpɔɖeŋu me, ƒumeŋuɖui ƒe dɔléle aɖe si mebɔ kura o si woyɔna be dyskeratosis congenita.
Kuxi bubu kawoe ate ŋu ado mo ɖa le Aklã ƒe Dɔléle ta?
Ne lãkusiwo gblẽ la, mete ŋu tsɔa oxygen yia ŋutilãa ƒe akpa mamlɛa nyuie o. Esia nana míaƒe dzi wɔa dɔ sesĩe wu. Esia ate ŋu ahe kuxi vovovowo vɛ:
- Oxygen ƒe agbɔsɔsɔ si dzi ɖe kpɔtɔ le ʋu me (hypoxemia) kple oxygen ƒe anyimanɔmanɔ na lãmenugbagbeviwo (hypoxia).
- Aklã me ʋusɔgbɔdɔ.
- Aɖuɖɔtoe si mu.
- Aɖuɖɔtoedɔléle enuenu.
- Yagbɔgbɔ ƒe dɔmawɔmawɔ nyuie keŋkeŋ.
- Dzi ƒe dɔmawɔmawɔ nyuie.
Esia tae wòle vevie be nàyi ɖɔkta gbɔ enumake eye nàdi atike ne dzesiwo le ŋuwò.
Aleke nèwɔna kpɔa aklãdɔléle si nye aklãdɔ? Dodokpɔ kawoe wowɔna?
Dodokpɔ geɖe hiã be woatsɔ aɖo kpe edzi be wokpɔ aklãdɔ le aklã me. Wò ɖɔkta aɖo to wò lãkusiwo gbã ahabia wò dzesiwo. Emegbe woawɔ dodokpɔwo akpɔ alesi wò lãkusiwo le dɔ wɔm nyuie. Woalé ŋku ɖe dzi alo lãkusi ƒe dɔléle bubu siwo ate ŋu anɔ wò dzesiwo hem vɛ hã ŋu. Dodokpɔ siwo bɔ wue nye:
- Akɔta ƒe X-ray: Kpɔ alesi lãkusiwo le le goawo katã me ɖa.
- High-resolution CT (HRCT) scan: Esia ate ŋu aɖe abi si le lãkusia ŋu afia nyuie ŋutɔ.
- Aklã ƒe dɔwɔwɔ dodokpɔ (PFT): Esiawo dzidzea alesi nàte ŋu agbɔ ya nyuie ahado goe, kple ya agbɔsɔsɔme si wò lãkusi ate ŋu alé ɖe te.
- Ʋudodokpɔ: Dodokpɔwo abe ʋukawo me ʋu ƒe gas ene be woatsɔ akpɔ oxygen ƒe agbɔsɔsɔ le ʋua me, eye woatsɔ akpɔ dɔléle bubuwo hã.
- Bronchoscopy: Dodokpɔ si me wotsɔa fotoɖemɔ̃ sue aɖe si ŋu mɔ̃ aɖe bla ɖe eŋu la toa ŋɔti alo nu me be wòalé ŋku ɖe lãkusia me. Woate ŋu axɔ lãmenugbagbeviwo ƒe kpɔɖeŋu (biopsy) hã le ɣeyiɣi sia me.
- Biopsy: Woɖea lãkusi sue aɖe tso lãkusi me hedoa eŋu le nusuekpɔmɔ̃ me.
Ɣeaɖewoɣi la, wò ɖɔkta ate ŋu aɖo aɖaŋu hã be nàwɔ echocardiogram atsɔ akpɔe ɖa be dzidɔ hã le ŋuwò hã.
Ðe woate ŋu ada Aklã ƒe Dɔlélea keŋkeŋa? Dɔdamɔnu kawoe li?
Nublanuitɔe la,
fifia la, womekpɔ atike aɖeke na aklãdɔléle o. Gake mègatsi dzi o. Atikewɔwɔ siwo li fifia ate ŋu akpe ɖe ŋuwò
nàɖu dzesiawo dzi, ana dɔlélea nayi edzi blewu, eye wòana wò agbenɔnɔ nanyo ɖe edzi . Dɔdamɔnu vevi siwo wozãnae nye:
- Atike siwo tsia lãkusi nu: Atikewo abe Nintedanib (OFEV®) alo Pirfenidone (Esbriet®) kpena ɖe ame ŋu be abi ƒe abi le lãkusi me dzi ɖena kpɔtɔna eye wòléa lãkusi ƒe dɔwɔwɔ ta.
- Corticosteroids: Wozãa esiawo ɣeaɖewoɣi tsɔ ɖea abi si le lãkusiwo me dzi kpɔtɔna.
- Oxygen zazã: Ne wò ʋu alo lãkusiwo mele oxygen si sɔ xɔm o la, wò ɖɔkta ate ŋu agblɔ na wò be nàno oxygen kpeɖeŋutɔ. Wotoa aɖuɖɔtoe alo motsyɔnu dzi naa esia.
- Aklã ƒe ɖɔɖɔɖo: Esia bia be nàwɔ gbɔgbɔ ƒe kamedede tɔxɛwo kple kamedede siwo akpe ɖe ŋuwò nàdo ŋusẽ wò aklã eye wòana gbɔgbɔ nanɔ bɔbɔe.
- Aɖuɖɔtoe dodo: Woate ŋu abu dɔnɔ aɖewo siwo ŋu Pulmonary Fibrosis le ŋu be woado aklã na wo ne dɔlélea nu sẽ.
- Dɔdamɔnu dodokpɔwo: Ne ètsɔ ɖe le eme la, àte ŋu akpɔ gome le numekuku siwo wowɔ tso atike yeyewo kple atikewɔmɔnu yeyewo ŋu hã me. Bia wò ɖɔkta tso esia ŋu.
Gakpe ɖe eŋu la, ne dɔléle bubu aɖe li si le Aklãdɔléle hem vɛ (e.g., `(autoimmune disease)`), ahiã be woadae, alo ne nɔnɔme aɖewo li siwo nana lãkusia ƒe ʋuʋu gagblẽ ɖe edzi (e.g., `(GERD)` - dɔgbo ƒe fuɖename), ahiã be nàno atike hã ɖe ema ta.
Ne Pulmonary Fibrosis le ŋunye la, aleke wòle be malé be na ɖokuinye?
(Pulmonary Fibrosis)
Ate ŋu asesẽ vie na amesi ŋu aklãdɔ le be wòawɔ avu kple dɔlékuiwo ahahaya. Eyata ele vevie ŋutɔ be nàklɔ asi enuenu kple adzalẽ kple tsi, ana nusiwo ƒo xlã wò nanɔ dzadzɛ, eye nànɔ adzɔge tso teƒe siwo amewo sɔ gbɔ ɖo alesi nàte ŋui (vevietɔ le dzamezã kple vuvɔŋɔli kple COVID dɔvɔ̃ɣi). Azɔ hã,
ele vevie be nàxɔ atike siwo wò ɖɔkta kafu na wò. Atike siawo kpena ɖe ame ŋu be woakpɔ ame ta tso dɔlélewo abe aklãdɔ, dzamezã, RSV, kple COVID me.
Ɣekaɣie wòle be makpɔ ɖɔkta?
Ne gbɔgbɔ sesẽ na wò alo ɖeɖi tea ŋuwò bɔbɔe wu tsã la,
yi ɖɔkta gbɔ enumake. Elabena
ne ède dzesi nɔnɔme siawo hedze wo dada gɔme kaba la, àte ŋu aɖe dɔlélea ƒe ŋgɔyiyi dzi akpɔtɔ.Ne kadodoŋusẽdɔ alo granulomatous dɔléle le ŋuwò xoxo la, ƒo nu kple wò ɖɔkta tso mɔ siwo dzi nàto aɖe aklãdɔléle si ate ŋu axɔ wò dzi akpɔtɔ ŋu.
Ɣekaɣie wòhiã be nàyi Atikewɔwɔ Kpata ƒe Dɔwɔƒe (ETU) ?
Ne dzesi siwo gbɔna dometɔ aɖe do mo ɖa la,
ƒo ka na 911 alo yi xɔ si me wokpɔa dɔnɔwo gbɔ kpata le si te ɖe ŋuwò enumake:- Yagbɔgbɔ sesẽna zi ɖeka kpata.
- Akɔtave sesẽ.
- Tɔtɔ alo susu ƒe nɔnɔme si trɔ.
- Ŋutilã, nuyi, alo asibidɛ ƒe amadede si trɔna blɔ.
Nukae wòle be mabia nye ɖɔkta?
Aɖe vi na wò be nàbia nya siawo ne èyi ɖɔkta gbɔ:
- "Ðɔkta, nukae na nye lãkusiwo le sesẽm alea?"
- "Atikewɔwɔ ƒe tiatia kawoe le asinye?"
- "Aleke wòle be mazã atike siawo?"
- "Ɣekaɣie wòle be mava ɖɔkta gbɔ le etsɔme?"
- "Ðe medze na lãkusi dodo na amea?"
Ele vevie ŋutɔ be nàbia nya siawo tɔgbe eye nàse wò nɔnɔmea gɔme nyuie wu.
Ðe woate ŋu axe mɔ ɖe Aklã ƒe Dɔléle nua?
Míate ŋu axe mɔ ɖe nusiwo hea aklãdɔléle vɛ dometɔ geɖe nu o. Gake nu aɖewo li míate ŋu awɔ atsɔ aɖe nusiwo nutome ƒe nɔnɔmewo gblẽna le lãkusiwo ŋu dzi akpɔtɔ:
- Te ɖa le nusiwo gblẽa nu le lãkusi ŋu (e.g. asbestos, ga ƒe ke, atikewo) gbɔ alesi nàte ŋui. Ne ele be nàwɔ dɔ kple nu mawo tɔgbe godoo la, ke zã yagbɔgbɔmɔ̃ tɔxɛ aɖe.
- Te ɖa le nusiwo ate ŋu ana nulɔdɔ nanɔ ame ŋu ɣeyiɣi didi ŋu (e.g., gbe, nukuwo, xeviwo ƒe aɖuɖɔ, fuwo, kple yaƒoƒomɔ̃ aɖewo). Zã yagbɔgbɔmɔ̃ ne èle dɔ wɔm kple esiawo.
- Ne ènoa atama la, dzudzɔ enumake, alo mègadze egɔme gbeɖe o.
Ne Pulmonary Fibrosis le ŋunye la, nukae wòle be makpɔ mɔ na?
Aɖuɖɔtoe ƒe abi sia
nɔa anyi ɖaa kloe (negbe le go siwo mebɔ o me ko, ne atike aɖe gbɔe wòtso eye wòlée kaba). Ne dɔléle bubu aɖe le ŋuwò la, nɔnɔme ma dzi ɖuɖu ate ŋu akpe ɖe ŋuwò nàɖe nu bubu siwo agblẽ le wò lãkusiwo ŋu dzi akpɔtɔ. Ne womete ŋu ke ɖe nusi gbɔ wòtso ŋu o la, wò ɖɔkta adze agbagba ada wò dzesiwo esime wòle agbagba dzem be yeaxe mɔ ɖe nusiwo agblẽ le ŋuwò nu.
Esesẽna na ɖɔktawo be woagblɔ alesi tututu aklãdɔlélea ayi ŋgɔe. Le ame aɖewo gome la, dzesiawo ate ŋu adze vivivi le ƒe aɖewo megbe. Le ame bubuwo gome la, dɔlélea ate ŋu ayi ŋgɔ kabakaba eye wòasẽ ɖe edzi le ɣleti ʋɛ aɖewo megbe.
Ɣeyiɣi didi kae nàte ŋu anɔ agbe kple Aklãdɔléle?
Zi geɖe la, amesi si dɔléle si bɔ wu, ``Idiopathic Pulmonary Fibrosis,'' nɔa agbe le mama dedie nu nyea ƒe etɔ̃ va ɖo atɔ̃. Gake
esi wowɔ ŋgɔyiyi le atikewɔwɔ me nyitsɔ laa ta la, amesiwo ŋu Aklã ƒe Dɔléle le ƒe agbenɔƒe dzi ɖe edzi vie. Eyata mègatsi dzi o.
Ðe Aklã ƒe Dɔléle ƒe afɔɖeɖe aɖewo lia?
"Stage" ɖoɖo aɖeke meli si dzi dziɖuɖua da asi ɖo na aklã me ʋu ƒe sisi o. Gake ɖɔkta aɖewo ate ŋu anɔ te ɖe wò dzesiwo, aɖuɖɔtoedɔ dodokpɔ me tsonu, kple foto siwo nèwɔ nu atsɔ ada dɔlélea ɖe hatsotso si nye “si mesẽ o,” “si mesẽ o,” “esẽ ŋutɔ,” alo “si nu sẽ ŋutɔ.”
Ƒe nenie Aklã ƒe Dɔléle dzea egɔme zi geɖe?
Zi geɖe la
, amesiwo xɔ wu ƒe 65 ŋue wokpɔa aklãdɔléle le. Mlɔeba la, nusiwo dzi wòle be woaɖo ŋkui (Take-Home Message) .
Ne èva nya be Aklã ƒe Dɔléle le ŋuwò la, ate ŋu atrɔ wò agbenɔnɔ. Ate ŋu anye nusi agbɔ eme eye kakaɖedzi mele etsɔme ŋu o. Le ɣeyiɣi siawo tɔgbe me
la, kpekpeɖeŋunaɖoɖo aɖe ƒe amesinɔnɔ tso wò lɔlɔ̃tɔwo, ƒomea, kple ame bubu siwo ŋu nɔnɔme ma ke le gbɔ ate ŋu anye nusi ŋu asixɔxɔ gã aɖe le. Nu vevitɔe nye be ame sia ame si ŋu aklãdɔ le la to vovo. Ame aɖeke mate ŋu agblɔ alesi tututu wò etsɔme anɔ o. Dɔdamɔnu siwo li fifia ate ŋu akpe ɖe ŋuwò nàɖe dɔlélea ƒe ŋgɔyiyi blewu, aɖu dzesiwo dzi, eye wòana wò agbenɔnɔ nanyo ɖe edzi. Eyata, gblɔ nyateƒe na wò ɖɔkta le nusi nàkpɔ mɔ na kple nusi nàte ŋu awɔ tso wò nɔnɔmea ŋu. Ele vevie hã be nànɔ susu nyuiwo me.
Aklã ƒe Ʋuʋu, Aklã ƒe Ʋuʋu, Yagbɔgbɔ sesẽ, Kɔdzi Kuku, Aklãdɔ, Yagbɔgbɔdɔ, Idiopathic Aklã ƒe Ʋuʋu, Aklã ƒe Abi
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