Ðe nètsi dzi ɖe viwò sue ƒe mo ƒe nɔnɔme ŋua? Mina míaƒo nu tso Binder Syndrome ŋu!

Esi wodzi viwò sue la, ɖe nède dzesi tɔtrɔ sue aɖewo le woƒe mo ƒe nɔnɔme ŋua? Ɣeaɖewoɣi la, woƒe ŋɔti ate ŋu adze abe ɖe wòle gbadzaa vie ene, alo woƒe nuyi si le etame la manɔ teƒe nyuitɔ o. Enye nusi sɔ be vidada alo vifofo navɔ̃ vie ne wokpɔ nane si le abe esia ene. Gake megatsi dzi o, egbea míele nu ƒom tso nɔnɔme aɖe si ɖea dzesi mawo tɔgbe fiana, gake mebɔ boo o, si woyɔna be Binder Syndrome ŋu.

Nukae nye Binder Syndrome? Kpuie ko la,...

Binder syndrome nye dɔléle si mebɔ o , si wodzina, si dzɔna le vidzidzi me. Edzena le eŋu be ƒu siwo le mo titina, vevietɔ ŋɔti kple aɖu si le etame, metsina nyuie o. Eɖi ale si wometu xɔ ƒe gli aɖewo nyuie o. Esia ate ŋu ana vidzĩa ƒe mo nato vovo vie.

Bu eŋu kpɔ, ƒu siwo le ete tae míaƒe ŋɔti kple nuyi si le etame la ƒe nɔnɔme le. Eyata ne ƒu mawo dzudzɔ tsitsi la, woƒe dzedzeme trɔna. Gbɔgbɔ ate ŋu asesẽ na ɖevi aɖewo le nɔnɔme sia ta, eye nuɖuɖu hã ate ŋu asesẽ na wo, vevietɔ ne wole no nam . Gake nya nyuiae nye be, atike aɖe li na esia. Zi geɖe la, ne ɖevia tsi vie, si fia be ne woɖo ƒewuiwo me (zi geɖe la, exɔ tso ƒe 15-19) la, woate ŋu agbugbɔ ƒu siawo aɖo wo nɔewo ŋu eye woate ŋu agbugbɔ mo ƒe dzedzeme aɖo to mo kple aɖu ƒe dɔwɔwɔ (`maxillofacial surgery`) .

Ðe ŋkɔ bubuwo li na Binder Syndromea?

Ẽ, ɣeaɖewoɣi ɖɔktawo zãa ŋkɔ bubuwo na dɔléle sia. Enyo be nànya elabena ɖewohĩ àse ŋkɔ siawo hã:

• Binder phenotype - Esia nye ŋkɔ bubu na Binder syndrome.
• Binder ƒomevi nasomaxillary dysplasia
• Maxillonosal ƒe dɔmawɔmawɔ nyuie
• Nasomaxillary hypoplasia ƒe dɔléle

Togbɔ be ŋkɔ siawo adze nu sesẽ vie hã la, gɔmesese ɖeka koe wo katã le.

Aleke gbegbee nɔnɔme sia bɔe be Binder Syndrome?

Le nyateƒe me la, esia nye nɔnɔme si mebɔ kura o . Nyatakaka aɖewo ɖee fia be nɔnɔme sia dzɔna le vidzĩ yeye siwo mede ɖeka le 10,000 ɖesiaɖe me o . Eyata esia megavɔ̃ o. Gake, togbɔ be mebɔ o hã la, ele vevie be nànyae.

Nukae nye Binder Syndrome ƒe dzesiwo?

Nu vevitɔ si ɖe dzesi le nɔnɔme sia ŋue nye mo titina ƒe tsitsi ƒe anyimanɔmanɔ . Esia awɔe be ɖevia ƒe mo ate ŋu aɖe tɔtrɔ siawo afia:

• Noa va nɔa gbadzaa, eye nuyi si le etame la va nɔa gbadzaa . Ate ŋu adze abe ɖe ŋɔti la nyrɔ ɖe eme ene.
• Aɖu si le ete la dona ɖe ŋgɔ.Edze abe alea ene. Dzedzeme sia dzɔna elabena aɖu si le etame la yia eme eye aɖu si le ete la dona ɖe ŋgɔ.
• Aɖu siwo le etame kple esiwo le ete la mewɔ ɖeka nyuie o (`malocclusion`) . Esia ate ŋu ana wòasesẽ ne èle nu ɖum hele nu ƒom.
• ŋɔtiawo xɔa dzogoe etɔ̃ alo dzinuvi ƒe nɔnɔme .

Esiawoe nye dzesi siwo bɔ wu. Gake tsɔ kpe ɖe eŋu la, àte ŋu akpɔ dzesi siwo gbɔna hã le nɔnɔme siwo mebɔ o me :

• Aɖu si me mã .
• Dzi ƒe gbɔdzɔgbɔdzɔ siwo wodzina .
• Tosese ƒe kuxi .
• Susu ƒe nuwɔametɔnyenye .
• Aklã ƒe dɔmawɔmawɔ nyuie .
• Strabismus alo ŋku siwo wotso .

Menye ɖeviwo katãe akpɔ dzesi siawo katã o. Ðewohĩ dzesi veviwo koe anɔ ɖevi aɖewo ŋu.

Nukatae Binder Syndrome dzɔna? Nukawoe gbɔ wòtsona?

Ne míagblɔe tututu la, eŋutinunyalawo mekpɔ nya nusi tututu hea esia vɛ haɖe o . Zi geɖe la, ɖeviwo va xɔa nɔnɔme sia le susu aɖeke manɔmee.

Gake esi wònye be dɔléle sia le ɖevi geɖe ŋu le ƒome aɖewo me ta la, wosusui be domenyiŋusẽfianu ate ŋu anɔ anyi, si fia be domenyiŋusẽfianu ƒe ŋusẽkpɔɖeamedzi aɖe ate ŋu anɔ anyi . Gake womeɖo kpe esia dzi keŋkeŋ haɖe o.

Tsɔ kpe ɖe eŋu la, numekulawo xɔe se be nu geɖe siwo le nutoa me hã ate ŋu awɔ akpa aɖe. Nu mawo dometɔ aɖewoe nye:

• Vidadawo ƒe ahanono le fufɔɣi.
• Atike aɖewo zazã le fufɔɣi. Kpɔɖeŋu aɖewoe nye phenytoin si tsia asrãdɔ nu (Dilantin®, Phenytek®) kple warfarin si nana ʋu mekɔna o (Coumadin®, Jantoven®). (Ele be woano atike siawo le atikewɔlawo ƒe dzikpɔkpɔ te ne ehiã, gake ele be woakpɔ egbɔ etɔxɛe le fufɔɣi.)
• Vitamin K ƒe anyimanɔmanɔ le fufɔɣi.
• Nuveviwɔame le ta alo mo ŋu le vidzidzi me.

Esiawoe nye afɔku siwo wokpɔ fifia.

Aleke ɖɔktawo wɔa dea dzesi Binder Syndrome?

Ðɔktawo kea ɖi nɔnɔme sia gbã ne wolé ŋku ɖe vidzĩa ƒe mo ƒe dzedzeme ŋu . Emegbe be woaɖo kpe ɖikeke ma dzi alo agbee la, wowɔa dodokpɔ tɔxɛ siwo ate ŋu akpɔ mo ƒe ƒu ƒe wɔwɔme nyuie . Woyɔa esiawo be:

• CT-dɔdamɔnu siwo wozãna
• MRI Scan (`MRI`) .
• Ultrasound ƒe fotoɖeɖe (`ultrasounds`) .

To fotoɖeɖe siawo dzi la, míate ŋu ade dzesi tsitsi ƒe gbɔdzɔgbɔdzɔ ɖesiaɖe si le mo ƒe ƒuwo me pɛpɛpɛ.

Nukawoe nye Binder Syndrome ƒe atikewo?

Atikewɔwɔ na esia toa vovo tso ɖevi ɖesiaɖe gbɔ, eye wònɔa te ɖe dzesiawo ƒe sesẽ hã dzi.Eto vovo. Atikewɔwɔmɔnu vevi eve li:

1. Aɖuɖɔtoewo dzi kpɔkpɔ:

• Esia bia be woatsɔ ka (`braces`) ade nu me be aɖu kple aɖuwo nasɔ nyuie .
• Ɣeaɖewoɣi la, ne dzesiawo mesẽ akpa o la, aɖudɔdada sia ɖeɖe ate ŋu asu.
• Le go bubuwo me la, ahiã be woawɔ atike sia do ŋgɔ na amekoko alo le amekoko vɔ megbe.

2. Amekoko:

• Esiae nye atikewɔwɔmɔnu vevitɔ. Tagbɔdɔdala (ɖɔkta si bi ɖe tagbɔ kple mo me) ye wɔa dɔ siawo.
• Le esia me la, wozãa ƒu, ƒunukpeƒetetedɔ, alo nusiwo wotsɔ lãgbalẽ wɔe siwo woɖe tso ɖevia ŋutɔ ƒe ŋutilã me tsɔ trɔa asi le ŋɔti ƒe nɔnɔme ŋu . Wogayɔa esia be rhinoplasty .
• Azɔ hã, woate ŋu awɔ amekoko ƒomevi aɖe si woyɔna be Le Fort I alo II osteotomy be wòana aɖu si le etame la naɖo teƒe nyuitɔ. Esiawo nye amekoko siwo sesẽ vie, gake ɖɔkta bibiwo ate ŋu awɔ wo dzidzedzetɔe.
• Zi geɖe la, ɖɔktawo ɖoa aɖaŋu be woalala va se ɖe esime ɖevia ƒe mo ƒe ƒuwo nadzudzɔ tsitsi keŋkeŋ hafi awɔ dɔ sia, eye zi geɖe la , exɔa ƒe 15 va ɖo ƒe 19. Esia le alea elabena ne wowɔe do ŋgɔ na ema la, kuxiwo ate ŋu ado mo ɖa ne ƒuawo yi edzi le tsitsim.

Vevietɔ: Menye ɖeviwo katãe ahiã atikewɔwɔ evea siaa o. Ðewohĩ atikewɔwɔ ɖeka koe ahiã ɖevi aɖewo. Atikewɔlawo ƒe ƒuƒoƒoa atso nya me le esia ŋu ne wodo ɖevia kpɔ vɔ.

Ðe woate ŋu axe mɔ ɖe nɔnɔme sia si woyɔna be Binder Syndrome nua?

Esi womenya nusi tututu gbɔ esia tso o ta la, womate ŋu aka ɖe edzi be woate ŋu axe mɔ ɖe enu keŋkeŋ o .

Gake ne èfɔ fu la, àte ŋu aɖe afɔku si le eme be nàxɔ dɔléle sia dzi akpɔtɔ va ɖo afi aɖe ne èɖe wò nutome ƒe nɔnɔme aɖewo siwo ŋu míeƒo nu tsoe va yi la dzi ɖeɖe kpɔtɔ . Àte ŋu aƒo nu tso esia ŋu kple wò ɖɔkta:

• Atikewo ƒe dedienɔnɔ le fufɔɣi , vevietɔ phenytoin kple warfarin (mègano atike aɖeke o negbe ɖe ɖɔkta ŋlɔe na wò hafi, eye ne woŋlɔe na wò la, ƒo nu tso eŋu na wò ɖɔkta).
• Ku ɖe vitamin ƒe anyimanɔmanɔ ŋu, vevietɔ vitamin K ƒe anyimanɔmanɔ . Ele vevie ŋutɔ be nunyiame nyuitɔ nasu ame si le fufɔɣi.

Nukae nye mɔkpɔkpɔ na ɖevi si ŋu Binder Syndrome le?

Esiae nye nya nyuitɔ kekeake. Mɔkpɔkpɔ nyui aɖe le nɔnɔme sia ŋu le goawo katã me .

Ðevi akpa gãtɔ mehiã be woawɔ atike bubu aɖeke na wo le woƒe aɖuɖɔtoewo ɖeɖe vɔ megbe o. Woate ŋu agbɔ ya nyuie, aɖu nu nyuie, eye woƒe mo ƒe dzedzeme nyona ɖe edzi le amekoko vɔ megbe.Ate ŋu adzɔ. Eyata naneke meli si ŋu nàtsi dzi ɖo o, gake nu vevitɔ kekeakee nye be nàdi atikewɔlawo ƒe aɖaŋuɖoɖo kaba ale si nàte ŋui.

Nya kawoe wòle be mabia nye ɖɔkta?

Ne èkpɔe be Binder Syndrome le ye alo viwò ŋu la, àte ŋu abia nya siawo tɔgbe wò ɖɔkta. Esiawo akpe ɖe ŋuwò nàse nɔnɔmea gɔme:

• "Ðɔkta, nukae ate ŋu anye nusi gbɔ vinyea ƒe nɔnɔmea tso wu? "
• " Dodokpɔ kawoe wowɔna be woatsɔ anya Binder Syndrome ƒe nɔnɔme sia pɛpɛpɛ? "
• " Nukae nye atikewɔmɔnu siwo woate ŋu azã na esia? Nukae nyo na vinyea?"
• " Mɔnukpɔkpɔ kawoe li be woagahiã atikewɔwɔ ake le agbe me? "
• "Ne vi bubu le asinye la, mɔnukpɔkpɔ kawoe li be eya hã naxɔ nɔnɔme sia? "

Tsɔ kpe ɖe biabia siawo ŋu la, bia wò ɖɔkta nusianu si le susu me na wò.

Nɔnɔme bubu kawoe ƒe dzesiwo sɔ kple Binder Syndrome tɔ?

Nɔnɔme bubu geɖewo li siwo gblẽa nu le mo ƒe ƒu ƒe tsitsi ŋu eye wodzena abe Binder ƒe dɔlélea ene. Ðɔktawo hã tsia dzi ɖe nusiawo ŋu. Kpɔɖeŋu aɖewoe nye:

• Acrodysostosis ƒe dɔléle
• Apert ƒe dɔlélea
• Chondrodysplasia punctata, si nye lãkusi ƒe ƒomevi (CDPR) .
• Fetal warfarin syndrome (nɔnɔme si dona tso warfarin zazã le fufɔɣi) .
• Keutel ƒe dɔlélea
• Stickler ƒe dɔlélea

Ðeko nànya ŋkɔ siawo. Ðɔktawoe anya nɔnɔme si tututu le viwòa ŋu.

Mlɔeba la, nusiwo dzi wòle be woaɖo ŋkui (Take-Home Message) .

Enyo, eyata mina míaƒo nu tso nusi ŋu míeƒo nu tsoe ŋu kpuie:

• Binder Syndrome nye dɔléle si mebɔ kura o, si wodzina .
• Esia nana be ƒu ƒe tsitsi le mo titina dzi ɖena kpɔtɔna, vevietɔ ŋɔti kple aɖu si le etame . Esia wɔnɛ be nɔnɔme aɖewo abe ŋɔti gbadza kple aɖu si le ete si do ɖe gota ene dona.
• Womenya nusi tututu gbɔ esia tso o , gake domenyiŋusẽfianu kple nutoa me ƒe nɔnɔmewo ate ŋu awɔ akpa aɖe.
• Woate ŋu ada nɔnɔme sia dzidzedzetɔe to aɖuɖɔɖɔɖɔdɔ kple/alo amekoko me .
• Ðevi geɖe ƒe dɔwɔwɔ nyo ŋutɔ le atikewɔwɔ vɔ megbe eye woate ŋu anɔ agbe si sɔ.

Ne dzimaɖitsitsi alo dzimaɖitsitsi aɖe le viwòa ƒe mo ƒe dzedzeme ŋu la, taflatse yi ɖɔkta bibi gbɔ kaba ale si nàte ŋui . Nu vevitɔ kekeakee nye be menye be nàtsi dzodzodzoe o, ke boŋ be nàxɔ nyatakaka kple mɔfiame nyuitɔ. Ðɔktawo li be yewoakpe ɖe ŋuwò.

Mele mɔ kpɔm be nyatakaka sia aɖe vi na wò. Mele lãmesẽ nyui dim na wò kple wò ƒomea!

` Binder Syndrome, Binder Syndrome, mo ƒe dɔmawɔmawɔ nyuie, dɔléle siwo wodzina, ɖeviwo ƒe lãmesẽ, maxillofacial dɔwɔwɔ, tagbɔ kple mo ƒe dɔwɔwɔ