Ðe wò ɖɔkta gblɔ na wò be nàwɔ G6PD dodokpɔa? Alo ɖe nèle dodokpɔ sia me dzrom le esi wò vi suea xɔ aɖuɖɔtoe eye madzo o ta? Ðewohĩ ɖeko nèse nya G6PD teti koe nye ema. Enye nusi sɔ be nàvɔ̃ vie elabena ŋkɔa wɔ nuku vie. Gake mègavɔ̃ naneke o. Egbea, míaƒo nu tso G6PD dodokpɔ sia kple G6PD ƒe anyimanɔmanɔ si henɛ vɛ ŋu le mɔ bɔbɔe aɖe ŋutɔ si gɔme nàte ŋu ase nu.
Mina míakpɔe ɖa gbã, nukae nye G6PD?
Enyo, mina míadze egɔme kple kpɔɖeŋu bɔbɔe aɖe ŋutɔ. Tsɔe be ʋumenugbagbevi dzĩ siwo le wò ŋutilã me le abe aƒe suewo ene. Le aƒe siawo me la, dɔ vevi si nye oxygen tsɔtsɔ yi teƒe bubuwo yia edzi. Fifia, ehiã be ‘dzɔla’ nanɔ anyi si akpɔ aƒe siawo ta, be woalé wo sesĩe. Eyata, dɔwɔla tɔxɛ aɖe li si woyɔna be G6PD si kpɔa míaƒe aƒewo ta si woyɔna be ʋumenugbagbevi dzĩwo eye wòkpena ɖe wo ŋu be woanɔ lãmesẽ me.
Le atikewɔwɔ me la, G6PD ye nye ŋkɔ kpui si wotsɔ na enzyme si nye glucose-6-phosphate dehydrogenase . Enzyme nye protein si kpena ɖe míaƒe ŋutilã ŋu wòwɔa atike vovovowo ƒe dɔwɔwɔ nyuie. Dɔ vevitɔ si G6PD enzyme sia wɔnae nye be wòakpɔ míaƒe ʋumenugbagbevi dzĩwo ta tso atike aɖewo (siwo woyɔna be reactive oxygen species) siwo ate ŋu agblẽ nu le wo ŋu la si me.
Eyata ne dzɔla sia, alo enzyme si woyɔna be G6PD, mele ame ƒe ŋutilã me o la, míeyɔnae be G6PD ƒe anyimanɔmanɔ . Esia nye domenyiŋusẽfianu, si fia be enye domenyinu. Ame si ŋu dɔmawɔmawɔ nyuie sia le la ƒe ʋumenugbagbevi dzĩwo ƒe xexlẽme gbɔdzɔna vie. Ele abe aƒe si me dzɔla aɖeke mele o ene. Emegbe ne wodo go nu aɖewo la, ʋumenugbagbevi dzĩ siawo tea gbagbã eye wogblẽna kabakaba. Ne ŋutilãa mete ŋu wɔ ʋumenugbagbevi dzĩ yeyewo o eye xoxoawo tsrɔ̃ kabakaba la, nɔnɔme aɖe si woyɔna be ʋusɔgbɔdɔ dzɔna. Ne ʋumenugbagbevi dzĩwo gblẽ alea la, míeyɔnɛ be ʋusɔgbɔdɔ si me ʋu sina tona .
Eyata ɣekaɣie wòle be nàwɔ G6PD dodokpɔ?
Zi geɖe la, amesiwo ŋu G6PD ƒe anyimanɔmanɔ meɖea dzesi aɖeke fiana o. Wonɔa agbe si sɔ. Gake ne wodo go ‘nu aɖewo siwo ʋãa wo’ ko hafi ʋusɔgbɔdɔ si me ʋu sina tona ƒe nɔnɔme si ŋu míeƒo nu tsoe va yi la dzɔna eye dzesiawo dzena.
Azɔ mina míakpɔ nusiwo nye nusiwo ʋãa ame siawo ɖa.
| Nusiwo hea dɔlélea vɛ siwo hea dzesiwo vɛ | Numeɖeɖe bɔbɔe aɖe tso esia ŋu |
|---|---|
| Dɔlékui aɖewo | Nuteɖeamedzi si le ŋutilãa me si dɔlékuiwo alo dɔlékuiwo hena vɛ ate ŋu ana ʋumenugbagbevi dzĩwo nagbã kabakaba. |
| Fava-gbewo | Esiae nye nusi hea nɔnɔme sia vɛ wu. Ame aɖewo ate ŋu adze dzesiwo gɔme ne woɖu fava-ku alo woƒe aŋɔ gɔ̃ hã gbɔgbɔ. Wogayɔa esia be ‘favism’. |
| Atike aɖewo | Gake menye atikewo katãe ate ŋu ana nɔnɔmea nagblẽ ɖe edzi o, abe dɔlékuiwutike aɖewo, asrãtikewo, kple atike siwo me steroid mele o siwo tsia dɔdzẽ nu (NSAID) ene. Eyata ne G6PD ƒe dɔmawɔmawɔ nyuie le ŋuwò la, ele vevie be nàgblɔe na wò ɖɔkta hafi ano atike aɖeke. |
Eyata ne èdo go nusi aʋã wò nenema la, àte ŋu adze ʋusɔgbɔdɔ si me ʋu sina tona ƒe dzesiwo afia. Ɣemaɣie ɖɔkta ate ŋu ado susu ɖa be woawɔ G6PD dodokpɔ. Kpɔe ɖa be dzesi siawo ɖi nusi nènya nyuie hã.
| Dzesi si dzena | Nukae esia fia? |
|---|---|
| Alɔ̃madɔmadɔ kpata (syncope) . | Ne ahɔhɔ̃a mexɔ ɔksidzin si sɔ o la, manyamanya ate ŋu adzɔ. |
| Sese le eɖokui me be ɖeɖi te ye ŋu ŋutɔ (Ðɖiteameŋu) . | Ne ʋumenugbagbevi dzĩ siwo tsɔa ɔksidzin yia ŋutilã bliboa me dzi ɖe kpɔtɔ la, ɖewohĩ ɖeɖi te ŋuwò akpa be yeate ŋu awɔ dɔ siwo sɔ gɔ̃ hã. |
| Sese le ɖokuiwò me be yeƒe dzi le ƒoƒom sesĩe | Ele be dzia nawɔ dɔ sesĩe wu be wòakɔ ʋua kabakaba eye wòana ɔksidzin si ŋutilãa hiã. |
| Yagbɔgbɔ sesẽ (gbɔgbɔtsixetsixe) . | Ne oxygen ƒe agbɔsɔsɔ si le ʋua me dzi ɖe kpɔtɔ la, gbɔgbɔtsixe tsi ƒowò eye nàse le ɖokuiwò me be yegbɔdzɔ. |
| Aɖuɖɔ dzĩ alo aŋutiɖiɖi | Ne ʋumenugbagbevi dzĩ gbogbo aɖewo gblẽ la, wo me nuwo dona le aɖuɖɔ me, si wɔnɛ be aɖuɖɔa ƒe amadede trɔna. |
| Ŋutilã si ƒe ŋutigbalẽ le ɣie | Ne ʋu ƒe agbɔsɔsɔ dzi ɖe kpɔtɔ la, ŋutigbalẽa ƒe amadede meganɔa pink o eye wòzua ɣie. |
| Ŋutilã kple ŋku ƒe ɣie (jaundice) . | Ne ʋumenugbagbevi dzĩwo gblẽ la, nu ɣi aɖe si woyɔna be bilirubin ƒoa ƒu ɖe ŋutilãa me. Esiae nana ŋku ƒe ŋutigbalẽ kple ɣiwo zua ɣie. |
Nukatae wowɔa G6PD dodokpɔ na vidzĩ suewo?
Jaundice bɔ ɖe vidzĩ siwo wodzi yeyee me ŋutɔ. Zi geɖe la, adzo le eɖokui si le ŋkeke ʋɛ aɖewo va ɖo kwasiɖa eve megbe. Gake ne vidzĩ aɖewo xɔ ʋusɔgbɔdɔ wu kwasiɖa eve eye womete ŋu ke ɖe nusi gbɔ wòtso si me kɔ o ŋu la, wò ɖɔkta ate ŋu aɖo aɖaŋu be woado G6PD kpɔ.
Tsɔ kpe ɖe eŋu la, ne ènya be G6PD ƒe dɔmawɔmawɔ nyuie le wò ƒomea me la, anyo be nàwɔ dodokpɔ sia le vidzĩa dzidzi vɔ megbe. To mɔ sia dzi la, àte ŋu anya esia do ŋgɔ eye nàwɔ afɔɖeɖewo.
Aleke gbegbee G6PD ƒe anyimanɔmanɔ bɔe?
Le nyateƒe me la, esia nye domenyiŋusẽfianu ƒe nɔnɔme si bɔ ŋutɔ le xexeame. Woxɔe se be dɔléle sia le ame miliɔn 400 kple edzivɔ ŋu le xexeame katã. Gake abe alesi míegblɔe va yi ene la, ame siawo ƒe akpa gãtɔ makpɔ dzesi aɖeke le woƒe agbemeŋkekewo katã me o.
G6PD ƒe anyimanɔmanɔ ƒe dzesiwo bɔ ɖe ŋutsuwo me wu nyɔnuwo, eye wòbɔ ɖe amesiwo tso Asia, Afrika, alo Mediterraneatɔwo dome.
Aleke wowɔa G6PD dodokpɔae?
Esia nye ʋudodokpɔ si le bɔbɔe ŋutɔ, si wowɔna edziedzi. Naneke meli si woavɔ̃ na le mɔ aɖeke nu o. Exɔa ɣeyiɣi si mede aɖabaƒoƒo atɔ̃ o.
- Wodea aŋe sue aɖe ʋuka aɖe si le dɔnɔ aɖe ƒe alɔnu me eye woɖea ʋu.
- Emegbe woɖea aŋea ɖa eye wotsɔa aŋɔ sue aɖe ƒoa eŋu.
Ame aɖewo vɔ̃na vie ɖe aŋenuwo ŋu (woyɔa esia be trypanophobia). Ne vɔvɔ̃ sia le ŋuwò la, gblɔe na dɔnɔdzikpɔla si ɖea wò ʋu. Woakpe ɖe ŋuwò. Àte ŋu aɖe ŋku ɖa, agbɔ ya blewu, alo xɔ̃wò alo ƒometɔ aɖe nanɔ gbɔwò le ʋuɖeɖea me.
Alesi woawɔ dodokpɔ sia na vidzĩwo
Esi wònye be esesẽna be woaxɔ ʋu tso vidzĩ ƒe alɔnu ta la, woɖea ʋu tso woƒe afɔkpodzi. Wozãa aŋe sue aɖe tsɔ toa teƒe sue aɖe le afɔkpodzia ŋu nyuie ŋutɔ eye woƒoa ʋu ʋɛ aɖewo nu ƒu. Emegbe woblaa aŋe sue aɖe ɖe teƒea. Vidzĩa ate ŋu ase veve vie, gake esia nu ayi kaba. Ðewohĩ abi aɖe anɔ anyi vie, gake esia ahaya le ŋkeke ɖeka alo eve megbe.
Ðe wòhiã be madzra ɖo hafi adoe kpɔa?
Esia nye nya vevi aɖe ŋutɔ. Ẽ, nu aɖewo li siwo ŋu wòle be míaɖɔ ŋu ɖo.
- Gblɔ atike siwo katã nènona (vitamin kple kpeɖeŋutɔtikewo hã le eme) na wò ɖɔkta.
- Atike kple nuɖuɖu aɖewo ate ŋu akpɔ ŋusẽ ɖe dodokpɔ sia me tsonu dzi. Eyata wò ɖɔkta ate ŋu agblɔ na wò be nàƒo asa na fava-ku ɖuɖu alo nàdzudzɔ atike aɖewo siwo me sulfa le nono ŋkeke ʋɛ aɖewo.
- Zi geɖe la, mehiã be woatsi nu dɔ hafi dodokpɔ sia nava o.
Nu vevi aɖee nye esi: Ne ʋusɔgbɔdɔ ƒe dzesi siwo le dɔ wɔm (e.g., ʋusɔgbɔdɔ, ɖeɖiteameŋu) le ŋuwò le gbesigbe nèwɔ wò dodokpɔa la, wò ɖɔkta ate ŋu ahe dodokpɔa ɖe megbe vaseɖe ŋkeke bubu. Esia le alea elabena kaka dzesiawo nadze le ŋuwò la, ʋumenugbagbevi dzĩ siwo me G6PD mele o la tsrɔ̃na zi geɖe. Ema gblẽa lãmenugbagbevi siwo le lãmesẽ me ko ɖe wò ʋu me. Ne èwɔ dodokpɔ ɣemaɣi la, àte ŋu akpɔ alakpanya si gblɔ be wò G6PD ƒe agbɔsɔsɔme sɔ.
Ðe afɔku aɖewo le dodokpɔ sia mea?
Esia nye dodokpɔ si me afɔku mele boo o. Abe ʋudodokpɔ bubu ɖesiaɖe ene la, .
- Abi sue aɖe si me wotsɔ aŋea de.
- Abi sue aɖe si wotsɔ ƒoe
- Ƒã ŋutɔ, ʋu alo dɔlékuiwo ƒe dodo
Nu mawo tɔgbe ate ŋu adzɔ, gake zi geɖe la, esiawo hayana keŋkeŋ le ŋkeke ɖeka alo eve me.
Nukae dodokpɔa ƒe nyatakakaa gblɔ?
Ne wò nyatakaka ɖee fia be wò G6PD ƒe agbɔsɔsɔ le sue la, efia be G6PD ƒe gbɔdzɔgbɔdzɔ le ŋuwò. Gake mefia be ʋusɔgbɔdɔ si me ʋu sina tona le ame ŋu le ŋuwò godoo o. Ame geɖe nɔa agbe dzesi aɖeke manɔmee. Nu vevitɔe nye be nànɔ adzɔge tso nusiwo hea dɔlélea ƒe dzesiwo vɛ gbɔ.
Nyɔnu aɖewo ƒe G6PD ƒe agbɔsɔsɔ ate ŋu aɖiɖi vie wu alesi wòle dzɔdzɔmee. Esia fia be wonye ‘tsɔla’ na G6PD ƒe anyimanɔmanɔ. Kpuie ko la, domenyiŋusẽfianu si naa G6PD ƒe anyimanɔmanɔ kple domenyiŋusẽfianu si le lãmesẽ me siaa le woƒe domenyiŋusẽfianuwo me. Zi geɖe la, dzesi aɖeke menɔa ame siawo ŋu o. Gake woate ŋu atsɔ domenyiŋusẽfianua ana wo viwo.
Ɣekaɣie wòle be makpɔ ɖɔkta?
Ame geɖe siwo ŋu G6PD ƒe anyimanɔmanɔ le nɔa agbe dzidzedzetɔe nusiwo hea dɔlélea vɛ manɔmee. Gake ne ʋusɔgbɔdɔ si me ʋu sina tona ƒe dzesiwo dze ŋuwò, eye dzesi mawo dometɔ aɖewoe nye:
- Ne esẽ akpa be nàwɔ wò gbesiagbedɔwo
- Ne exɔ wu gaƒoƒo 24-48
Kpɔ wò ɖɔkta enumake. Le dɔléle sesẽwo me la, ahiã be woaxɔ wò ɖe kɔdzi be woawɔ atike na wò. Le nɔnɔme kpata sia tɔgbe me la, ele be nàyi kɔdzi si te ɖe ŋuwò ƒe Dɔwɔƒe si Kpɔa Nudzɔdzɔ Kpatawo Gbɔ (ETU).
Gbedasi si Wotsɔ Yi Aƒeme
- G6PD nye enzyme vevi aɖe si kpɔa míaƒe ʋumenugbagbevi dzĩwo ta.
- Enzyme sia ƒe anyimanɔmanɔ (G6PD ƒe anyimanɔmanɔ) nye domenyiŋusẽfianu ƒe nɔnɔme.
- Dɔléle sia le ame geɖe ŋu gake womeɖea dzesi aɖeke fiana o.
- Ne wodo go nusiwo hea dɔlélea abe fava beans, atike aɖewo, kple dɔlékuiwo ene la, ate ŋu ana ʋumenugbagbevi dzĩwo nagbã, si ana ʋusɔgbɔdɔ si nana ʋu sina toa ʋu me nava.
- G6PD dodokpɔ nye ʋudodokpɔ bɔbɔe aɖe si wowɔna tsɔ dea dzesi nɔnɔme sia.
- Ne G6PD ƒe anyimanɔmanɔ le ŋuwò la, nu vevitɔe nye be nànya nusiwo nye nusiwo hea wò dɔléle vɛ eye nàƒo asa na wo.
- Vevietɔ wu: Ne G6PD ƒe dɔmawɔmawɔ nyuie le ŋuwò la, kpɔ egbɔ be yena wò ɖɔkta nanya hafi aŋlɔ atike yeye ɖesiaɖe na wò.

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