Mí katã míenya be ʋu si le míaƒe ŋutilã me mele abe tsi ene o, ke boŋ enye tsi si ƒe ʋeʋẽ lilili aɖe. Gake bu eŋu kpɔ, nukae adzɔ ne ʋu sia va le ɣie wu alesi wòle dzɔdzɔmee sã, abe aŋɔ ɣi ene? Eva sesẽna na ʋu ɣi sia be wòato ʋuka nyui siwo le míaƒe ŋutilã katã me la me. Ele abe anyikpe ɣi aɖe si ge ɖe pɔmpi me ene. To mɔ sia dzi la, ʋua ƒoa ke abe koklozi ene, eye ʋu ƒe sisi le ŋutilãa me gblẽna, si nye nusi míeyɔna be Hyperviscosity Syndrome le atikewɔwɔ me. Esia menye nu sue aɖe ko o, ke ɣeaɖewoɣi la, enyea nɔnɔme si me afɔku le ŋutɔ, si dea ame ƒe agbe afɔku me. Mina míaƒo nu tso esia ŋu bɔbɔe, le mɔ si gɔme nàte ŋu ase nu.
Nukatae ʋua yɔ zi ɖeka alea gbegbe ɖo?
Nu gbãtɔ si gɔme wòle be míase enye be Hyperviscosity Syndrome menye dɔléle le eɖokui si o. Enye nɔnɔme bubu si gbɔ wòtso ƒe dzesi. Abe alesi ko kɔdzi nye dzamezã alo aklãdɔ ƒe dzesi ene. Lãmenugbagbevi alo protein ƒomevi vovovo siwo le ʋua me ƒe agbɔsɔsɔ fũ koŋ gbɔe ʋu ƒe ƒoƒo tsona.
Kpuie ko la, ne ʋumenugbagbevi dzĩwo, ʋumenugbagbevi ɣiwo, ʋumenugbagbevi dzĩwo, alo serum protein siwo le ʋua me ƒe xexlẽme dzi ɖe edzi le mɔ si mesɔ o nu la, ʋua me sẽna.
Tabla si le ete la yɔ atikewɔwɔ me nɔnɔme vevi aɖewo siwo ate ŋu ahe dɔléle sia vɛ.
| Nɔnɔme siwo ate ŋu ana ʋu natsi | Numeɖeɖe bɔbɔe aɖe |
|---|---|
| Waldenström ƒe dɔléle si nye Macroglobulinemia (WB) . | Esiae nye nusi gbɔ wòtsona wu be eƒe lãme nasẽ akpa. Esia nye ʋumenugbagbeviɣidɔ ƒomevi aɖe si dzɔna le ƒumeŋuɖui kple ʋukawo me. Protein si mesɔ o ƒe dzidziɖedzi fũ akpa, si nana ʋua ƒoa ƒu gbɔe wòtsona. |
| Multiple Myeloma ƒe dɔléle | Esia hã nye kansa ƒomevi aɖe si gblẽa nu le ʋumenugbagbevi dzĩwo ŋu. Protein siwo mesɔ o siwo kansadɔlékuiawo wɔna la nana ʋua tsina. |
| Lãmenugbagbevi geɖe ƒe ʋumenugbagbeviɣidɔ Rubra Vera | Esia nye ƒumeŋuɖui ƒe dɔléle. Le nɔnɔme sia me la, wowɔa ʋumenugbagbevi dzĩwo le mɔ si dzi womate ŋu aɖu o nu. Ne ʋumenugbagbevi dzĩwo ƒe xexlẽme le dzidzim ɖe edzi la, ʋua ƒe ʋeʋẽ hã dzina ɖe edzi ŋutɔ. |
| Ʋumenugbagbeviɣidɔ | Le ʋumenugbagbeviɣidɔ, si nye ʋumenugbagbeviɣidɔ me la, ʋumenugbagbevi ɣiwo ƒe dzidziɖedzi fũ akpa. Ðewohĩ lãmenugbagbevi siawo ƒe nɔnɔme mesɔ o. Esia ate ŋu ana ʋukawo naxe eye ʋua natsi. |
| Kadodo ƒe lãmekawo ƒe dɔlélewo | Ʋu ƒe sisi ate ŋu adzɔ ɣeaɖewoɣi le dɔlélewo abe ƒunukpeƒetetedɔ ene me, gake esia mebɔ kura o. |
| Nu bubu siwo mebɔ o siwo gbɔ wòtsona | Nu bubu geɖewo hã ate ŋu atsoe, abe cryoglobulinaemia (dɔléle si nana ʋukawo me vuvu), hypoxia si nɔa anyi didi (oxygen ƒe anyimanɔmanɔ atraɖii), kple kansa dada aɖewo (Retinoic acid therapy). |
Aleke nèsena le ɖokuiwò me ne wò ʋu le ƒoƒom? Nukawoe nye dzesiawo?
Bu eŋu kpɔ, míaƒe ŋutilã ƒe ŋutinu ɖesiaɖe, tso ahɔhɔ̃a dzi va ɖo míaƒe asibidɛwo ƒe nugbɔ dzi la, ʋu tsɔna, eye wòtsɔa ɔksidzin kple nunyiamewo. Eyata ne woxe ʋu ƒe sisi sia la, ŋutinu mawo mekpɔa nusi hiã o. Esia tae dzesiawo dzena ɖo. Dzesi siawo ate ŋu ato vovo tso ame ɖeka gbɔ yi bubu gbɔ, eye woate ŋu ato vovo le dɔléle gbãtɔ si na ʋua ƒo ƒu hã nu.
Esiawo nye dzesi siwo wokpɔna zi geɖe la dometɔ aɖewo:
Dzesi siwo gblẽa nu le ahɔhɔ̃ kple lãmekawo ŋu
Ʋu ƒe sisi ƒe gbegblẽ ate ŋu akpɔ ŋusẽ ɖe ahɔhɔ̃a dzi wu.
- Taɖuame sesẽ kple taɖuame
- Nukpɔkpɔ ƒe kuxiwo: nukpɔkpɔ si me kɔ o, nukpɔkpɔ zi eve, ɣeaɖewoɣi la, nukpɔkpɔ ƒe bu kpata
- Tosese ƒe kuxiwo: tosese dzi ɖe kpɔtɔ alo megabu o
- Ʋuʋudedi
- Ðeɖiteameŋu si gbɔ eme kple alɔ̃dɔdɔ (Lethargy) .
Dzesi siwo do ƒome kple ʋudodo
Ne ʋu le ƒoƒom la, ʋua ƒe sisi dzi ɖuɖu vivivi la me gblẽna, si ate ŋu ana ʋu nado le ame si le vome.
- Nuveviwɔame bɔbɔe
- Ʋu si dona le lãkusi me (ŋɔti me ʋu, aɖuɖɔtoe) .
- Ʋudodo bubu siwo mebɔ o (e.g., ʋu le aɖuɖɔ me) .
Dzesi sesẽ bubuwo
Esiawo ɖee fia be ŋutilãa ƒe ŋutinu veviwo le gbegblẽm.
- Ʋusɔgbɔdɔ (Hypertension) .
- Dzi ƒe dɔmawɔmawɔ nyuie: akɔtave, gbɔgbɔtsixetsixe
- Ayiku ƒe dɔmawɔmawɔ nyuie
- Ʋu ƒe sisi (Thrombosis) .
- Dɔlékui sesẽ (Sepsis) .
Ne dzesi siawo dometɔ ɖeka alo esi wu nenema le wò alo ame aɖe si nènya ŋu la, ele vevie ŋutɔ be nàyi ɖɔkta gbɔ enumake eye màhe ɖe megbe o.
Aleke woawɔ ada nɔnɔme sia si me afɔku le?
Hyperviscosity Syndrome nye atikewɔwɔ kpata elabena ne womewɔ atike nɛ o la, ate ŋu ana ɔksidzin nawu ŋutinu veviwo abe ahɔhɔ̃, dzi, kple ayiku ene, si ana woagblẽ nu le wo ŋu tegbee alo ado kpo nu gɔ̃ hã. Eyata atikewɔwɔ kaba hiã vevie.
Zi geɖe la, atikewɔwɔ ƒe ɖoɖoa nyea ɖoɖo eve.
1. Atikewɔwɔ enumake, si anɔ anyi ɣeyiɣi kpui aɖe
Afɔɖeɖe gbãtɔe nye be woaɖu dzesiawo dzi eye woaɖe ʋua ƒe ʋeʋẽ dzi akpɔtɔ kaba. Atike siwo wozãna wu na esia dometɔ ɖekae nye Plasmapheresis .
Plasmapheresis nye nusi sɔ kple ʋukɔklɔ. Woɖea wò ʋu sue aɖe le wò ŋutilã me, toa mɔ̃ tɔxɛ aɖe me, eye woɖea ʋumenugbagbevi dzĩ si me protein bubu siwo nana wò ʋu ƒoa ƒu le la ɖe vovo heɖenɛ ɖa. Emegbe wotsakaa ʋumenugbagbevi dzĩ kple ɣi siwo le lãmesẽ me la kple tsi si woatsɔ aɖo eteƒe eye wogbugbɔna vaa wò ŋutilã me.
Esia ate ŋu aɖe ʋu ƒe sisi dzi akpɔtɔ kaba eye wòatɔ te ŋutinuwo ƒe gbegblẽ. Gake wò atikewɔlawo ƒe ƒuƒoƒoa ŋutɔe atso nya me nenye be atikewɔwɔ sia sɔ na amesiame kple nenye be ehiã.
2. Atikewɔwɔ ɣeyiɣi didi (dɔléle si gbɔ wòtso la dada) .
Ne woɖe ʋua ƒe ʋeʋẽ dzi kpɔtɔ vɔ la, nu vevitɔ si kplɔe ɖoe nye be woada dɔléle gbãtɔ si hee vɛ . Elabena ne womeda dɔléle ma o la, ʋua ate ŋu aƒo ake.
- Ne kansa abe Multiple Myeloma alo Leukemia , gbɔe wòtso la, wowɔa atike siwo tsia kansa nu abe atikewɔmɔnu ene .
- Ne nusi gbɔ wòtsoe nye polycythaemia , la, wowɔa atike be woaɖe ʋumenugbagbevi dzĩ siwo sɔ gbɔ wu la ɖa alo be woaɖe woƒe wɔwɔme dzi akpɔtɔ.
- Ne enye atikewɔwɔ ƒe nɔnɔme bubu la, ɖɔktawo aɖo aɖaŋu na wo be woawɔ atike aɖewo koŋ nɛ.
Le esia ta la, ɖɔktawo ƒe ƒuƒoƒo aɖe, siwo dome ʋumenugbagbeviɣidɔdalawo, kansadɔdalawo, kple ayikuŋutinunyalawo hã le, aƒo ƒu awɔ atikewɔwɔ ƒe ɖoɖo nyuitɔ kekeake na wò.
Gbedasi si Wotsɔ Yi Aƒeme
- Hyperviscosity Syndrome nye nɔnɔme si me ʋua va ƒoa ke abe akɔɖumi ene, si xea mɔ na ʋu ƒe sisi le ŋutilãa me.
- Esia menye dɔléle si to vovo o. Enye dɔléle sesẽ bubu, abe ʋumekansa ene, ƒe dzesi .
- Mègaŋe aɖaba ƒu dzesiwo abe taɖuame sesẽ, ŋku ƒe tɔtrɔ, ʋu si mebɔ o, alo ɖeɖiteameŋu si gbɔ eme ene dzi o.
- Esia nye atikewɔwɔ me nudzɔdzɔ kpata aɖe . Kpɔ wò ɖɔkta ne ènya de dzesi dɔlélea ƒe dzesiwo ko. Ne ehiã la, yi kɔdzi aɖe ƒe Atikewɔwɔ Kpata ƒe Dɔwɔƒe (ETU) enumake.
- Dɔdamɔnua lɔ afɔɖeɖe siwo woawɔ enumake atsɔ aɖe ʋu ƒe ʋeʋẽ dzi akpɔtɔ (abe plasmapheresis ene) kple dɔléle si gbɔ wòtso la dada siaa ɖe eme.











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