Ua manaʻo paha ʻoe ua paʻa ke apo āu e ʻaʻahu mau nei i kou manamana lima? A i ʻole ua lilo ka nui o kou kāmaʻa, ʻoiai ka laulā, i ʻoi aku ka nui ma mua o ka maʻamau? Me ia mau loli liʻiliʻi, ke manaʻo nei ʻoe e loli mālie ana ke ʻano o kou helehelena? ʻAʻole paha ʻoe e hoʻolohe nui i kēia mau mea. Akā hiki i kēia ke lilo i mau hōʻailona o kahi maʻi kakaʻikahi akā hopohopo i kapa ʻia ʻo Acromegaly. E kamaʻilio wale kākou e pili ana i kēia i kēia lā.
I ka ʻōlelo maʻalahi, he aha ka Acromegaly?
He maʻi kakaikahi akā koʻikoʻi ka Acromegaly e kū mai ana i ka wā e nui loa ai ka hormone ulu (GH) o kou kino. Hana ʻia kēia hormone e ka pituitary gland, kahi gland nui e like me ka pī ma ke kumu o kou lolo. Eia nō naʻe, i ka acromegaly, hana nui ʻia kēia hormone ma muli o kahi puʻupuʻu i loko o ka pituitary gland a i ʻole ma kahi ʻē aʻe o ke kino.
He mea nui ka Hormone Ulu no nā keiki e ulu a kiʻekiʻe a ulu. Akā i ka wā e lilo ai kākou i poʻe mākua, ma hope o ka pani ʻana o nā papa ulu i loko o ko kākou mau iwi, ʻaʻole e hoʻonui hou kēia hormone i ko kākou kiʻekiʻe. Akā, pono nō hoʻi i ko kākou kino makua kēia hormone. ʻO ia ke mālama i ke ʻano olakino o ko kākou mau iwi, ka cartilage, a me nā ʻōpū, e hoʻokō pono i ka metabolism, a e mālama i nā pae kō koko ma ka pae kūpono.
Eia nō naʻe, inā piʻi nui ka hormone ulu i loko o ke kino o ka pākeke, hiki ke loaʻa nā pilikia he nui, e like me nā loli ʻano ʻole i ke ʻano o nā iwi, ka hoʻonui ʻia ʻana o nā ʻōpū, a me ka hoʻonui ʻia o ke kō koko (hyperglycemia).
He aha ka ʻokoʻa ma waena o ka acromegaly a me ka gigantism?
Hoʻokumu ʻia kēia mau kūlana ʻelua e ka piʻi ʻana o ka Growth Hormone (GH). Aia ka ʻokoʻa ma ka hui makahiki i hoʻopilikia ʻia.
- Gigantism: Hana ʻia kēia i nā keiki. ʻO ke ʻano kēia inā piʻi ka hormone GH ma mua o ka wā ʻōpio, ma mua o ka pani ʻana o nā papa ulu o nā iwi, ulu nui kēlā mau keiki. He ʻano kakaikahi kēia ma mua o ka acromegaly.
- Acromegaly: Hana ʻia kēia i nā pākeke. E like me ka mea i ʻōlelo ʻia ma mua, ma hope o ka pani ʻana o nā papa ulu, piʻi aʻe ka GH, akā ma kahi o ia mea, loli ke ʻano o nā iwi ma nā lima, nā wāwae, a me ke alo a lilo i mea nui.
ʻO wai ka mea e loaʻa ana i ka acromegaly? Pehea ka maʻamau?
He maʻi laha ʻole ka Acromegaly. Wahi a nā helu helu, ma waena o 3 a me 14 mau kānaka mai loko mai o 100,000 i ʻike ʻia me kēia maʻi. ʻOiai hiki ke ulu aʻe i kēlā me kēia makahiki ma hope o ka wā ʻōpio, ʻike pinepine ʻia ka maʻi i ka wā waena, ʻo ia hoʻi, ma waena o 40 a me 50 mau makahiki.
Pehea ka hopena o kēia kūlana i ke kino?
Ke piʻi ka Hormone Ulu (GH), hōʻailona ia i ko kākou akepaʻa e hana i kahi hormone ʻē aʻe. Ua kapa ʻia ʻo ia ʻo 'Insulin-like Growth Factor 1 (IGF-1)'. ʻO kēia hormone i kapa ʻia ʻo IGF-1 ka mea e hoʻoulu ai i ko kākou mau iwi a me nā ʻiʻo, a hoʻomalu pū i ke kō koko a me nā lipids. No laila, ke piʻi ka GH, piʻi nui pū ka IGF-1. ʻO ka hopena, hiki ke loaʻa nā maʻi koʻikoʻi e like me ka Type 2 Diabetes, High Blood Pressure, a me ka maʻi puʻuwai .
I ka ʻōlelo maʻalahi, ʻoiai hoʻomaka ka pilikia me GH, ʻo ka nui o nā mea e hōʻino ai i ke kino e hana ʻia ma o ka piʻi ʻana o ka hormone IGF-1.
He aha nā hōʻailona o ka acromegaly?
ʻIke mālie loa nā hōʻailona o ka acromegaly, i nā makahiki he nui. No laila hiki ke paʻakikī iki ke ʻike i nā pae mua. Hiki paha iā ʻoe ke ʻike i nā loli i kou helehelena inā ʻoe e nānā i kahi kiʻi kahiko o ʻoe iho.
Hōʻike maopopo ka papa ma lalo nei i kēia mau hōʻailona.
| Nā loli o waho i ke kino | Nā hōʻailona ʻē aʻe a me nā ʻeha ʻole |
|---|---|
| Ka hoʻonui ʻia ʻana o nā lima a me nā wāwae (paʻa nā apo, hoʻololi ka nui o nā kāmaʻa) | ʻEha ke poʻo (ʻoi aku hoʻi inā nui ka puʻupuʻu) |
| Nā loli i ke ʻano o ka helehelena (ka puka ʻana o ka ʻauwae a me ka lae) | ʻEha hui |
| Ka hoʻonui ʻia ʻana o nā lehelehe, ka ihu, a me ke alelo | Nā loli o ka ʻike (e like me ka ʻike maka pōwehiwehi) |
| Ka hou nui a me ka ʻili ʻaila | ʻO ka maneʻo o nā lima (Carpal Tunnel Syndrome) |
| Ka hohonu ʻana, ka palahalaha o ka leo | Ka hanu ʻana a me ka apnea hiamoe |
| Hoʻonui ʻia ka hanana o nā hōʻailona ʻili | ʻEha hope a me nā pilikia o ke kuamoʻo |
Inā loaʻa iā ʻoe kekahi a ʻoi aku paha o kēia mau hōʻailona, he mea nui loa e ʻike koke i kāu kauka a kamaʻilio e pili ana i kēia.
Pehea e ʻike ʻia ai ka acromegaly?
Ke ʻike ʻoe i ke kauka, e hoʻolohe pono ʻo ia i kāu mau hōʻailona, e hana i kahi hoʻokolokolo kino, a laila e kauoha i kekahi mau hoʻokolohua e hōʻoia i ka hōʻailona.
- Nā hoʻāʻo koko: ʻO kēia ka mea nui loa. Ke ana lākou i nā pae o GH a me IGF-1 i loko o kou koko.
- Nā Hoʻāʻo Kiʻi: Inā hōʻoia nā hoʻāʻo koko ua kiʻekiʻe nā pae GH, hiki ke kauoha ʻia kahi scan MRI e nānā i kahi puʻupuʻu pituitary.
Inā ua hōʻoia ʻia ka maʻi, hiki ke hana ʻia nā hoʻokolohua hou aʻe e ʻike ai inā ua hoʻopilikia i nā ʻāpana ʻē aʻe o ke kino.
- ʻO kahi echocardiogram e nānā i ka hana o ka puʻuwai.
- He hana hiamoe e ʻike ai inā e hanu ana ʻoe i ka wā e hiamoe ana.
- Colonoscopy no ka nānā ʻana i ke olakino o ka colon.
- ʻO kahi kiʻi X-ray a i ʻole DEXA e nānā i ke olakino o ka iwi.
He aha nā lāʻau lapaʻau no ka acromegaly?
Aia kekahi mau koho lapaʻau no ka acromegaly. Na kāu kauka e hoʻoholo i ka lāʻau lapaʻau kūpono loa iā ʻoe ma muli o kou kūlana, ka nui a me kahi o ka puʻupuʻu.
1. ʻO ke ʻoki kino: ʻO kēia ka lāʻau lapaʻau nui no ka hapa nui o nā kānaka. ʻO ke kaʻina hana maʻamau i kapa ʻia ʻo Transsphenoidal Surgery . Pili kēia i ka wehe ʻana i ka puʻupuʻu pituitary ma o ka ihu. Inā wehe loa ʻia ka puʻupuʻu, aia kahi manawa kūpono e ho'ōla loa ʻia ka maʻi.
2. Lāʻau lapaʻau: Inā ʻaʻole hiki i ke ʻoki kino ke wehe loa i ka puʻupuʻu, a inā pono e hoʻēmi i ka puʻupuʻu ma mua o ke ʻoki kino, hoʻohana ʻia nā lāʻau lapaʻau. Hoʻomalu kēia mau lāʻau lapaʻau i nā pae GH o ke kino. Pono paha kekahi poʻe e lawe i ka lāʻau lapaʻau no ka wā lōʻihi.
3. Lapaʻau Radiation: Hoʻohana ʻia kēia lāʻau lapaʻau e luku i nā ʻāpana i koe o ka puʻupuʻu ke hiki ʻole i ke ʻoki kino a me ka lāʻau lapaʻau ke kāohi i ka maʻi.
He aha nā pilikia e hiki mai ana inā ʻaʻole mālama ʻia?
Inā ʻaʻole mālama ʻia, hiki i ka acromegaly ke alakaʻi i nā pilikia olakino koʻikoʻi i ka hala ʻana o ka manawa. ʻO kēia ka ʻaoʻao weliweli loa o ka maʻi.
- ʻAno 2 Diabetes
- Ke koko kiʻekiʻe (Hypertension)
- ʻO ka maʻi puʻuwai, ʻoi aku ka cardiomyopathy
- ʻO ka ʻāʻī o ke kino
- Nā polyp o ka kolona - Hiki i kēia ke lilo i ka maʻi kanesa ma hope aku.
- Ka hāʻule ʻana o ke kino
No laila, he mea nui loa e ʻike koke i ke kauka inā loaʻa iā ʻoe nā hōʻailona a e hahai i ka lāʻau i kuhikuhi ʻia inā ʻike ʻia ka maʻi. Inā kāohi ʻia nā pae GH me ka lāʻau lapaʻau, hiki ke hoʻemi nui ʻia ka pilikia o kēia mau pilikia.
Leka Lawe-Home
- ʻO ka Acromegaly kahi maʻi i hoʻokumu ʻia e ka hana nui ʻana o ka hormone ulu (GH) i loko o ke kino o ka pākeke.
- ʻIke lohi loa nā hōʻailona o kēia (e like me nā lima nui, nā wāwae, a me ka maka). No laila e makaʻala i nā loli i kou kino.
- Hoʻokumu pinepine ʻia kēia e kahi puʻupuʻu ʻaʻole maʻi kanesa i loko o ka gland pituitary.
- Inā kānalua ʻoe he mau hōʻailona kēia, e ʻike koke i kāu kauka .
- Aia nā lāʻau lapaʻau kūpono e like me ke ʻoki kino a me ka lāʻau lapaʻau. Me ka lāʻau lapaʻau kūpono, hiki iā ʻoe ke pale aku i nā pilikia koʻikoʻi e like me ka maʻi diabetes a me ka maʻi puʻuwai a ola i kahi ola olakino a maʻamau.











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