Ua noʻonoʻo paha ʻoe i ke ʻano o ke kīʻaha koko nui loa a koʻikoʻi loa i loko o ko kākou kino? ʻO ia ka aorta, a i ʻole aorta . Ua like ia me ke alaloa nui i loko o ko kākou kino. Holo ia mai ka puʻuwai a hiki i ka ʻōpū. ʻO ia ka mea e lawe ana i ke koko maʻemaʻe a waiwai i ka oxygen i hoʻopuka ʻia e ka puʻuwai i ke kino holoʻokoʻa. No laila, inā hewa kekahi mea me kēia aorta, hiki iā ia ke hoʻopilikia i ke kino holoʻokoʻa. ʻO ia ka hui o nā maʻi e hoʻopilikia ana i ka aorta, a mākou e kapa nei he Aortopathy .
He aha ka Aortopathy? E hoʻomaopopo maʻalahi kākou.
I ka ʻōlelo maʻalahi, ʻo ka aortopathy kahi hōʻiliʻili o nā kūlana e hoʻonāwaliwali a hōʻino paha i nā paia o kou aorta. I kēia manawa e noʻonoʻo, e hoʻopuka pololei ana kou puʻuwai i ke koko i loko o kēia aorta i kēlā me kēia manawa e paʻi ai. No laila, pono e ikaika loa kēia mau paia o ke aʻa e kū i kēlā kaomi. Akā, he aha ka mea e hana ai inā nāwaliwali kēia mau paia? Hiki iā lākou ke haki a ʻokiʻoki paha. He mea weliweli loa kēia. ʻO ke ʻano o ka aortopathy āu e loaʻa ai e hoʻopilikia i ka aorta i kekahi ʻano ʻē aʻe.
He aha nā ʻano nui o ka aortopathy?
Aia nā ʻano like ʻole o ka aortopathy. E kamaʻilio kākou e pili ana i kekahi o nā mea nui.
ʻO ka Aneurysm Aortic ʻōpū (AAA)
ʻO kēia ka manawa e nāwaliwali ai ka paia o kou aorta, ka mea e holo ana ma kou ʻōpū, a puka i waho e like me ka pōpō. Kāhea pū mākou i kēia he aneurysm . Hoʻopilikia pinepine kēia ʻano i ka poʻe ma luna o 65, nā mea puhi paka, a i ʻole ka poʻe me nā kumu pilikia ʻē aʻe no ka maʻi puʻuwai. He mea weliweli kēia "(AAA)" no ka mea hiki ke pahū koke a hoʻoulu i ke kahe koko e hoʻoweliweli i ke ola.
ʻO ka Aneurysm Aortic Thoracic (TAA)
He nāwaliwali a hoʻonui paha kēia o ka ʻāpana o ka aorta e holo ana ma ka umauma. ʻAʻole like ka maʻamau o ke kūlana `(TAA)` me `(AAA)`. Eia nō naʻe, ʻoi aku ka nui o ka holo ʻana i loko o nā ʻohana, ʻo ia hoʻi, hiki ke hoʻoili ʻia ma o nā hanauna. E like me `(AAA)`, ʻo ka pilikia nui o `(TAA)` ʻo ia ka haki ʻana.
ʻO ke kūlana weliweli i kapa ʻia ʻo Aortic Dissection
He mea paʻakikī iki kēia. ʻO ka mea e hana ʻia ma ʻaneʻi, ʻo ia ka haehae ʻana o ka papa o loko o ka paia o ka aorta. Hana ʻia kēia ma kahi nāwaliwali o ka paia o ka aorta. I kekahi manawa, e like me ka mea i ʻōlelo ʻia ma mua, hiki ke hana ʻia ma kahi o kahi aneurysm. Eia nō naʻe, hiki nō hoʻi ke hana me ka ʻole o kahi aneurysm. ʻElua ʻano nui o kēia. ʻO ka dissection ʻano A he haehae ia ma ka ʻāpana o ka aorta kokoke loa i ka puʻuwai (ʻo ia hoʻi, ma mua o ke ā aortic). ʻO ka dissection ʻano B he haehae ia ma hope o ke ā aortic, ma ka umauma a i ʻole ka ʻōpū. ʻO kēia "(Aortic Dissection)" he kūlana hoʻoweliweli ola e pono ai ka ʻike koke ʻana a me ka mālama ʻana .
E aʻo kākou e pili ana i ka Familial Aortopathy?
ʻO ka Familial Aortopathy kahi maʻi genetic e holo i loko o nā ʻohana.ʻO ka familial aortopathy kahi maʻi o nā aʻa nui e pili ana me ka mōʻaukala ʻohana o ka maʻi aortic. Loaʻa i kēia poʻe kahi ʻano gene e hoʻonui ai iā lākou i ka loaʻa ʻana o ka maʻi aortic. ʻO ka hapa pinepine, hoʻopilikia kēia aortopathy hoʻoilina i nā aʻa nui i loko o ka umauma, ʻoi aku hoʻi ke aʻa aortic a i ʻole ka aorta piʻi.
Aia kekahi mau ʻāpana nui ʻelua i kēia:
He aha ka Syndromic Aortopathy?
Kāhea pū mākou i kēia ʻo `(Syndromic hereditary thoracic aortic disease)`. I ka ʻōlelo maʻalahi, loaʻa iā ʻoe kahi maʻi genetic e hoʻopilikia i kou aorta a hoʻoulu i nā loli ʻē aʻe i kou kino. ʻO kekahi mau syndromes e alakaʻi ai i ka maʻi aortic:
- ʻO ka maʻi Loeys-Dietz
- ʻO ka maʻi Marfan
- ʻO ka maʻi Turner
- ʻO ka maʻi ʻo Vascular Ehlers-Danlos
E makaʻala hoʻi kākou i ka Aortopathy Non-syndromic
Ua kapa ʻia kēia ʻo "Non-syndromic heritable thoracic aortic disease." Maanei, ʻaʻohe ou ʻano genetic syndrome kikoʻī, akā he ʻano gene kou e hoʻonui ai i kou pilikia o ka loaʻa ʻana o ka maʻi aortic. Ua hoʻopili nā kānaka ʻepekema ma mua o 50 mau mutations genetic i kēia aortopathy. ʻO kekahi o nā genes i hoʻopili ikaika ʻia:
- ʻO `ACTA2` (ʻO kēia ka mea i ʻike pinepine ʻia)
- ʻO FOXE3
- ʻO LOX
- `MYH11`
- ʻO MYLK
E hoʻomanaʻo, inā ua loaʻa i kekahi o kou ʻohana kahi aneurysm a i ʻole ka dissection o ka aorta, e kamaʻilio me kāu kauka e pili ana i ka hoʻāʻo genetic . Inā ua ʻike ʻia ʻoe me ka maʻi aortic, pono paha ʻoe e hana i ka hoʻāʻo genetic e ʻike inā aia kekahi mau lālā ʻē aʻe o kou ʻohana i ka pilikia.
He aha ka Bicuspid Aortopathy?
Ua kapa ʻia hoʻi kēia ʻo `(Bicuspid valve-associated aortopathy)`. ʻO ke ʻano kēia, me ka stenosis aortic, loaʻa iā ʻoe kahi maʻi puʻuwai hānau i kapa ʻia ʻo Bicuspid Aortic Valve (BAV) . ʻO kēia `(BAV)` kahi maʻi puʻuwai hānau maʻamau, e pili ana i kahi o hoʻokahi i loko o 50 mau pēpē.
I kēia manawa, ʻo kāu valve aortic kekahi o nā "puka" ʻehā e kāohi ana i ke kahe o ke koko i loko o kou puʻuwai. Hoʻokele ia i ke kahe o ke koko mai ka ventricle hema, ke keʻena pamu nui o ka puʻuwai, i loko o ka aorta. ʻEkolu mau leaflet o kahi valve aortic olakino e wehe a pani ana e kāohi i ke kahe o ke koko. Eia nō naʻe, ʻelua wale nō leaflet o kahi valve aortic bicuspid. ʻAʻole paha kēia e hoʻopilikia nui no kekahi manawa, akā hiki ke hoʻopilikia i ka hala ʻana o ka manawa.
Inā loaʻa iā ʻoe ka bicuspid aortopathy, ʻelua mau leaflet o kāu valve aortic, a ʻoi aku ka laulā o kou aorta ma mua o ka maʻamau (dilated). I ka poʻe me ka bicuspid aorta, ʻike pinepine ʻia ka dilation ma ke aʻa aortic a i ʻole ka aorta ascending. ʻO kēia nā ʻāpana o ka aorta kokoke loa i ka puʻuwai.
Nā pilikia o ka Bicuspid Aortopathy
ʻAʻole paha he pilikia nui ka aorta i hoʻonui iki ʻia. Eia nō naʻe, inā lilo ia i mea nui loa, hiki ke ulu kahi aneurysm. Hoʻokomo kēia aneurysm i ke kaomi hou aʻe ma nā paia o ka aorta, hiki ke kumu i ka haki ʻana a i ʻole ka dissection. ʻO ka poʻe me ka bicuspid aortopathy he ʻeiwa manawa ka nui o ka loaʻa ʻana o ka dissection aortic ma mua o ka poʻe me ka ʻole o ke ʻano.
Pehea ka maʻamau o kēia aortopathy?
ʻOkoʻa ia ma muli o ke ʻano o ka maʻi. ʻO ka aortic aneurysm (AAA) ke ʻano maʻamau o ka aortopathy, a ʻo ia hoʻi ke ʻano maʻamau o ka aneurysm. Ma ʻAmelika Hui Pū ʻIa wale nō, ma kahi o 200,000 mau kānaka i ʻike ʻia me ka AAA i kēlā me kēia makahiki. Ma ka honua holoʻokoʻa, ma kahi o 47,000 mau kānaka e make i kēlā me kēia makahiki mai nā ʻano aortopathy āpau.
He aha nā hōʻailona o ka Aortopathy? Mai hoʻowahāwahā i kēia mau mea!
ʻAʻohe hōʻailona o ka Aortopathy. ʻO ia ka mea weliweli loa. ʻO ia ke kumu he mea nui e loaʻa nā nānā lapaʻau maʻamau inā he mau kumu pilikia kou.
Aia kekahi mau hōʻailona e ʻike ʻia i ka wā e kokoke ana e haki kahi aneurysm. ʻO nā hōʻailona hōʻailona e ʻike ʻia ma mua o kona haki ʻana:
- Manaʻo piha ʻoiai ma hope o ka ʻai iki ʻana.
- ʻEha mau ma ke kua, ka puʻupuʻu, ka ʻūhā, ka wāwae, a i ʻole ka ʻōpū.
- Ke manaʻo nei i ka puʻuwai o ka naʻau ma kahi ʻōpū.
- Paʻakikī ka hanu ʻana.
ʻO ka haki ʻana o ka aneurysm a me ka dissection aortic he mau pilikia hoʻoweliweli i ke ola! Inā loaʻa iā ʻoe nā hōʻailona aʻe , e kāhea koke i ka 1990 no kahi ambulance, a i ʻole e hele i ka lumi pilikia haukapila kokoke loa:
- Ka hoʻomaka koke ʻana o ka ʻeha nui o ka ʻōpū.
- He ʻeha koke, ʻoi, a nui hoʻi ma ka umauma a i ʻole ke kua o luna. Hiki i kēia ke manaʻo e like me ka haehae ʻia ʻana mai loko mai, e like me ka pahi e hou ana, a i ʻole e like me ke hou ʻia ʻana.
- ʻIli pipili a i ʻole ka hou nui.
- Ka huikau.
- Ka poniuniu a i ʻole ka māʻule ʻana.
- Piʻi ka helu o ka puʻuwai.
- Ka luaʻi a me ka luaʻi.
- Paʻakikī ka hanu ʻana.
- Paʻakikī i ka ʻōlelo ʻana.
- Ka nalowale ʻana o ka ʻike.
- Ka nāwaliwali a i ʻole ka maneʻo ma kekahi ʻaoʻao o ke kino.
He aha nā kumu o ka Aortopathy?
Aia kekahi mau kumu o ka aortopathy. Loaʻa kekahi i ka wā hānau, aʻo kekahi e ulu aʻe ma hope o ke ola.
- ʻIke Hoʻoilina: E like me ka mea i ʻōlelo ʻia ma mua, hiki i nā maʻi hoʻoilina a me nā ʻano like ʻole o ka gene ke kumu i ka maʻi aortic. Hoʻoilina pinepine ʻia ka aortopathy familial ma ke ʻano autosomal dominant. ʻO ke ʻano kēia inā loaʻa i kekahi makua ka gene, loaʻa i kā lāua keiki he 50% ka manawa e hoʻoilina ai.
- ʻO ka maʻi puʻuwai hānau: Pili kēia mau mea me ka aortopathy. ʻAʻole kēia manaʻo ua hoʻokumu ʻia ka aortopathy e ka maʻi puʻuwai hānau, akā ʻike pinepine ʻia nā mea ʻelua. Nā laʻana: `Bicuspid aortic valve`, `Coarctation of the aorta`, `Pulmonary atresia with ventricular septal defect (VSD)`, `Tetralogy of Fallot`, `d-Transposition of the great arteries`, `Truncus arteriosus`. Hiki nō hoʻi ke hana ʻia ka Aortopathy ma hope o nā ʻoki ʻana no kekahi mau maʻi puʻuwai hānau. Nā laʻana: `Arterial switch (ASO) operation`, `Atrial baffle (Mustard/Senning) operation`, `The staged Norwood, Glenn and Fontan surgeries`.
- Atherosclerosis: ʻO kēia ka hōʻiliʻili ʻana o nā waihona momona (plaque) i loko o nā aʻa, e hoʻohaiki mālie ana iā lākou. ʻO Atherosclerosis o ka aorta ke kumu nui o ka aortopathy ma hope o ke ola.
ʻO wai ka mea i ʻoi aku ka nui o ka pilikia o ka hoʻomohala ʻana i ka aortopathy?
Aia kekahi mau kumu pilikia e hiki ke kōkua i ka ulu ʻana o ka aortopathy:
- Ka puhipaka a me ka hoʻohana ʻana i ka paka: He kumu pilikia nui kēia. ʻO ka hapa nui o nā aneurysms e kū mai ana i ka poʻe puhipaka a i ʻole i puhipaka ma mua.
- Ke koko kiʻekiʻe (Hypertension): Hiki i kēia kūlana ke hoʻonāwaliwali i nā paia o nā aʻa i ka hala ʻana o ka manawa.
- Ka ʻelemakule: Hoʻonui ʻia ka pilikia o ka hoʻomohala ʻana i kahi aneurysm ma hope o 65 mau makahiki.
- Moʻolelo ʻohana: Inā ua loaʻa i kahi lālā o ka ʻohana piliola kahi aneurysm a dissection paha, ua piʻi aʻe kou pilikia.
- ʻO ke kolamu kiʻekiʻe a i ʻole nā triglycerides kiʻekiʻe: ʻO ka hoʻonui ʻia o nā pae o nā momona (lipids) i loko o ke koko e hoʻonui ai i ka pilikia o nā waihona momona i loko o nā aʻa.
- Nā maʻi Autoimmune: ʻO nā maʻi Autoimmune e like me 'Giant cell arteritis' a me 'Takayasu arteritis' hiki ke hoʻoulu i ka mumū i loko o nā paia o nā aʻa nui, e hoʻonāwaliwali ana iā lākou.
- Maʻi: I kekahi manawa, hiki i nā maʻi e like me ka syphilis, a i ʻole nā maʻi bacteria o ka paia o nā aʻa nui, ke hoʻonāwaliwali iā ia.
Pehea e ʻike ai i ka aortopathy?
ʻAʻohe hōʻailona a hōʻailona hoʻi o nā aneurysms a me nā dissections, no laila ʻaʻole paha e ʻike ʻia a hiki i ka wā e loaʻa ai nā pilikia koʻikoʻi. Eia nō naʻe, inā he mau mea pilikia kou, e nānā kāu kauka i kāu aorta no nā hōʻailona o ka maʻi.
ʻO nā ʻano hana i hoʻohana ʻia no ka ʻike ʻana i ka aortopathy:
- Hoʻokolohua kino: E nānā kāu kauka i nā ʻano āpau o kou olakino. E loiloi pū ʻo ia i kāu mau kumu pilikia no ka maʻi puʻuwai. E komo pū kēia me ka nīnau ʻana e pili ana i kou mōʻaukala olakino, nā kumu nohona (e like me ka puhipaka), a me ka mōʻaukala ʻohana.
- Hoʻāʻo ʻana i ka genetic: Hiki i kāu kauka ke ʻōlelo aku i ka hoʻāʻo genetic. E hōʻike kēia inā he mau hoʻololi genetic kou e pili ana i ka maʻi coronary artery.
- Nā hoʻāʻo kiʻi: Hiki i kāu kauka ke kauoha i kēia mau hoʻāʻo e nānā i ka nui a me ke olakino o kou aorta. Ana kēia mau hoʻāʻo i ke anawaena o kou aorta a ʻike inā ʻoi aku ka laulā ma mua o ka maʻamau.
He aha nā hoʻokolohua i hoʻohana ʻia e ʻike ai i ka aortopathy?
- ʻO ke kiʻi ʻana o ka tomography i helu ʻia (CT)
- ʻO ke kiʻi hoʻohālikelike makeneka (MRI)
- ʻO ka transthoracic echocardiogram (TTE) (kahi scan o ka puʻuwai)
- ʻO ka Transesophageal echocardiogram (TEE) (kahi scan puʻuwai i hana ʻia ma o ka esophagus)
- ʻO ka ultrasound ʻōpū (kahi scan ultrasound o ka ʻōpū)
Loaʻa i kēlā me kēia hoʻāʻo kona mau pono a me nā hemahema. E wehewehe kāu kauka i ka hoʻāʻo āu e pono ai a me ke kumu. Hiki i kāu kauka ke hoʻohana i hoʻokahi a ʻoi aku paha o kēia mau hoʻāʻo e nānā i kāu aorta i ka hala ʻana o ka manawa. Pono paha ʻoe e kiʻi i kēia mau kiʻi i nā manawa maʻamau (no ka laʻana, hoʻokahi manawa i ka makahiki). ʻO ka pinepine o kou pono ʻana i kēia mau hoʻāʻo e pili ana i kāu mau mea pilikia a me ke olakino o kou aorta i kēia manawa.
He aha nā lāʻau lapaʻau no ka Aortopathy?
Aia ka lāʻau lapaʻau i kou kūlana kikoʻī a me kou pilikia o nā pilikia. E hoʻopili kāu kauka i kāu lāʻau lapaʻau i kou kūlana a me nā pono. ʻO nā koho lapaʻau e pili ana i nā hoʻololi ʻana i ke ʻano o ka nohona, nā lāʻau lapaʻau, nā kaʻina hana lapaʻau, a me ke ʻoki kino.
E hoʻomaka kākou me nā hoʻololi ʻana i ke ʻano o ka nohona!
Hiki i nā hoʻololi ʻana i ke ʻano o ka nohona ke kōkua i ka hoʻolohi ʻana i ka holomua o kekahi ʻano maʻi aortic a hōʻemi i ka pilikia o ka pahū ʻana o kahi aneurysm. Inā loaʻa iā ʻoe ka maʻi aortic, he mea nui e hana i kēia mau mea:
- E pale i ka waiʻona.
- E pale i ka puhipaka a me nā huahana paka a pau.
- E ʻai i ka meaʻai olakino no ka puʻuwai.
- E hoʻoikaika kino mau (e like me ke kuhikuhi a kāu kauka).
- E mālama i ke kaumaha olakino nou.
- E kāohi i nā mea pilikia o ka maʻi puʻuwai e like me ke koko kiʻekiʻe a me ka cholesterol kiʻekiʻe.
Inā pono, aia kekahi mau lāʻau lapaʻau e like me kēia.
Hiki i kāu kauka ke kuhikuhi i ka lāʻau lapaʻau e kōkua i ka hoʻohaʻahaʻa ʻana i kou koko. Hoʻemi nā lāʻau lapaʻau koko i ke kaomi o ke koko i nā paia o kou mau aʻa. Hiki i kēia ke hōʻemi i ka pilikia o ka haki ʻana a i ʻole ka dissection o kahi aneurysm aʻa nui. ʻO nā ʻano lāʻau lapaʻau āu e lawe ai:
- ʻO nā mea hoʻopaʻa i ka enzyme hoʻololi angiotensin (ACE)
- ʻO nā mea pale i ka mea loaʻa Angiotensin (ARBs)
- Nā mea pale Beta
- Nā mea pale i ke kahawai calcium
- Diuretics (nā lāʻau lapaʻau e hoʻonui ai i ka mimi)
Nā ʻoki kino a me nā kaʻina hana lapaʻau ʻē aʻe
Pono kekahi poʻe i ka lāʻau lapaʻau a i ʻole ke ʻoki ʻana no ka aortopathy. ʻO kēia mau mea:
- ʻO ke ʻoki ʻana o ka aneurysm (ʻoki wehe kuʻuna)
- ʻO ke ʻoki hoʻololi aʻa aortic
- Hoʻoponopono ʻana i ka aneurysm endovascular (EVAR) - He hana kēia e hoʻokomo ʻia ai kahi paipu ma o kahi ʻoki liʻiliʻi.
- Hoʻoponopono ʻana i ka aneurysm endovascular Thoracic (TEVAR) - He ʻano hana like kēia no ke aʻa thoracic.
He aha kā mākou e hana ai e hōʻemi i ka pilikia o ka aortopathy?
Hiki iā ʻoe ke hōʻemi i kou pilikia o ka loaʻa ʻana o ka aortopathy ma o ka lawe ʻana i kahi nohona olakino puʻuwai. Eia kekahi mau ʻōlelo aʻoaʻo:
- E pale i nā lāʻau lapaʻau: ʻAʻole maikaʻi ka paka, nā lāʻau lapaʻau, a me ka waiʻona no kou puʻuwai. ʻOiaʻiʻo, hiki iā lākou ke hōʻino i kou puʻuwai a me nā kīʻaha koko. E hoʻōki loa i ka puhipaka a me nā lāʻau lapaʻau. I ka wā e pili ana i ka waiʻona, e ʻike pono i ke ʻano o ka 'inu' a kaupalena i ka nui. Paipai nā kauka ʻaʻole e inu nā wahine ma mua o hoʻokahi 'inu' i ka lā a ʻaʻole e inu nā kāne ma mua o ʻelua 'inu' i ka lā.
- E ʻai i ka meaʻai olakino no ka puʻuwai: ʻO kēia ka ʻai ʻana i nā meaʻai haʻahaʻa i ka momona saturated, trans fat, sodium (paʻakai), a me ke kō. E hōʻemi i nā kalapona i hoʻomaʻemaʻe ʻia (e like me ka berena keʻokeʻo) a ʻai i nā palaoa piha (e like me ka berena palaoa piha, ka laiki ʻeleʻele). Eia kekahi, e makaʻala i ka hopena o ka meaʻai i kāu mau pae cholesterol.
- Hoʻoikaika Kino: ʻAʻohe ala hoʻokahi e kūpono i nā mea āpau no ka hoʻoikaika kino. E hana i kāu mea e makemake ai. Eia kekahi, e hahai i ka ʻōlelo aʻo a kāu kauka e pili ana i ka hoʻoikaika kino palekana nou. ʻŌlelo pinepine nā kauka he 150 mau minuke o ka hoʻoikaika kino ikaika i kēlā me kēia pule. Hiki i kēia ke komo pū me ka hele wāwae wikiwiki, ke kaʻa paikikala, a i ʻole ka ʻauʻau ʻana.
- E hoʻokele i ke kaumaha: ʻAʻole ia he mea maʻalahi e like me ka mea i lohe ʻia. Akā, he mea nui e hoʻāʻo e aʻo i nā ala hou e kōkua iā ʻoe e hoʻoponopono i ke kaumaha i kou ola o kēlā me kēia lā. Eia kekahi, e kamaʻilio me kou ʻohana a me nā hoaaloha e pili ana i nā ʻano hana e pono ai no lākou.
He aha ka manaʻo no kekahi me ka Aortopathy? (Outlook)
ʻO ke kanaka maikaʻi loa e nīnau ai e pili ana i kou wā e hiki mai ana, ʻo ia kāu kauka. E noʻonoʻo ʻo ia i nā kumu he nui, no ka laʻana:
- Kou kūlana olakino kūikawā.
- ʻO ka wikiwiki o ka holomua ʻana o kou maʻi.
- Kou makahiki a me kou kāne.
- Nā mea pilikia o kou maʻi puʻuwai.
- Kou mōʻaukala lapaʻau ʻohana.
- Kou mōʻaukala lapaʻau holoʻokoʻa.
E kamaʻilio me kāu kauka e pili ana i nā mea e manaʻo ai i ka wā e hiki mai ana.
Inā loaʻa iaʻu ka Aortopathy, pehea wau e mālama ai iaʻu iho?
E hāʻawi kāu kauka iā ʻoe i nā alakaʻi no ka mālama ponoʻī. E hahai pono i kēlā mau alakaʻi, a e nīnau i kāu kauka inā he mau nīnau kāu. Pono ʻoe e hana i kēia mau mea:
- E hōʻalo i ka hoʻoikaika kino a i ʻole nā haʻuki pili.
- E hōʻemi a hoʻōki loa paha i ka inu ʻana i ka waiʻona.
- E hoʻololi i kāu meaʻai.
- E ho'ōki i ka puhipaka a i ʻole ka hoʻohana ʻana i nā huahana paka.
- E lawe i kāu lāʻau lapaʻau e like me ke kauoha.
ʻO ka hāpai ʻana a me ka Aortopathy
Hiki ke hoʻoweliweli ka hāpai ʻana inā loaʻa iā ʻoe ka maʻi ʻaʻa coronary. E kamaʻilio me kāu kauka ma mua o kou hoʻolālā ʻana e hāpai e hōʻoia i ka palekana nou. Pono paha ʻoe i ka mālama kūikawā i ka wā hāpai (e like me nā hoʻokolohua kiʻi pinepine) e hōʻemi i kou pilikia o nā pilikia. E pale i nā lāʻau lapaʻau i palekana ʻole i ka wā hāpai. Pono paha kāu kauka e hoʻololi i kāu mau lāʻau lapaʻau.
I ka manawa hea e pono ai iaʻu ke ʻike i ke kauka?
E ʻike i kāu kauka no nā hoʻokolohua makahiki, a e hele i nā hālāwai hoʻomaʻamaʻa āpau. E haʻi aku kāu kauka iā ʻoe i ka pinepine o kou hele ʻana mai no nā hoʻokolohua.
Inā ua ʻike ʻia ʻoe me ka maʻi puʻuwai hānau i kou wā kamaliʻi, aia paha he kauka puʻuwai pediatric kāu nāna i mālama i kou kūlana. Akā, ma hope o kou piha ʻana i 18 mau makahiki, ʻaʻole paha ʻoe i loaʻa i kahi loea hou. Hōʻike ka noiʻi he nui ka poʻe e huikau ana i ka wā e hoʻololi ai lākou mai ka mālama pediatric i ka mālama makua. Inā ua mālama ʻia ʻoe no ka maʻi puʻuwai hānau i kou wā kamaliʻi, he mea nui e hoʻomau i ka hana ʻana me kahi kauka puʻuwai i kou wā makua. He ʻoiaʻiʻo kēia ʻoiai inā ʻaʻole ʻoe e manaʻo i kekahi pilikia. E aʻo aku kāu kauka puʻuwai iā ʻoe e pili ana i kou pilikia no ka aortopathy a me nā kūlana ʻē aʻe i kou wā ʻelemakule.
ʻO ka mea hope loa, nā mea nui e hoʻomanaʻo (Leka Lawe-Home)
He maʻi koʻikoʻi ka Aortopathy hiki ke hoʻoweliweli i ke ola inā ʻaʻole i ʻike ʻia a mālama ʻia. Inā ua loaʻa i kekahi o kou ʻohana kahi aneurysm a i ʻole ka dissection o ka aorta, e kamaʻilio me kāu kauka e pili ana i kou pilikia. ʻOi aku ka nui o ka pilikia o kekahi poʻe ma muli o nā kūlana genetic, nā maʻi puʻuwai hānau, a i ʻole nā kumu nohona e like me ka puhipaka. ʻO ka noho ʻana i kahi nohona olakino puʻuwai hiki ke hōʻemi i kou pilikia o ka aortopathy a hoʻoikaika i kou kino holoʻokoʻa.E mālama pono i kou puʻuwai, no ka mea, ʻo ia ka puʻuwai o kou ola!
👩🏽⚕️ Nā nīnau hou aku (FAQs)
💬 He maʻi puʻuwai anei ka Aortopathy?
ʻAʻole no ka puʻuwai, he maʻi kēia o ke 'kīʻaha koko nui loa' e puka mai ana mai ka puʻuwai. Hāʻawi ʻia kēia inoa i kekahi maʻi e kū mai ana ma ke kīʻaha koko nui a nui loa (Aorta) e lawe ana i ke koko mai ko kākou puʻuwai a i ke kino holoʻokoʻa. ʻO ka mea pinepine, ʻo ka mea e hana ʻia, ʻo ia ka lahilahi a nāwaliwali o nā paia o kēia kīʻaha koko.
💬 He aha ka mea e hana ai ke nāwaliwali kēia aa koko?
Ke nāwaliwali kēia, ʻaʻole hiki i ke aʻa ke kū i ke kaomi o ke koko i hoʻopuehu ʻia e ka puʻuwai, a hoʻomaka ke aʻa e puʻupuʻu e like me ka pōpō (Aortic aneurysm). Inā hoʻomau ia i ka ulu ʻana e like me kēia, pohā koke ke aʻa me ka ʻole o ka ʻōlelo aʻo mua (Aortic dissection / Rupture). A laila make ka mea maʻi i loko o nā minuke.
💬 Hiki iā ʻoe ke ʻike i kēia ma mua o kona pahū ʻana?
ʻO ka hapa nui o ka manawa, ʻaʻole manaʻo ka mea maʻi i kekahi ʻeha a ʻoluʻolu ʻole paha mai kēia hoʻonui ʻia ʻana o ke aʻa (he maʻi leo ʻole). ʻOiai he mea hoʻoilina pinepine kēia (genetic - e like me Marfan syndrome), inā he aorta pohā ko kekahi o ka ʻohana, he mea nui e loaʻa i nā poʻe ʻē aʻe kahi Echocardiogram a i ʻole CT scan e nānā i kēia a lawe i ke ʻoki kino e pono ai a i ʻole ka lāʻau lapaʻau koko.
ʻAortopathy , Aorta, Maʻi Puʻuwai, Aneurysm, Aortic Dissection, Nā Maʻi Genetic, ʻEha Umauma, Koko Kiʻekiʻe, Puhipaka, Ola Kino Puʻuwai











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