Ke emi nei kāu hana koko? E kamaʻilio kākou e pili ana i kēia maʻi weliweli i kapa ʻia ʻo Aplastic Anemia!

Ke luhi nei hoʻi ʻoe a luhi hoʻi i nā manawa a pau? Ke paʻakikī nei ʻoe e hanu ma hope o ka hana ʻana i kahi mea liʻiliʻi? A i ʻole loaʻa iā ʻoe nā palapū a me ke koko ma nā wahi a pau o kou kino? I kekahi manawa, ʻaʻole paha mākou e nānā nui i kēia mau mea ma ke ʻano he mau mea maʻamau. Eia nō naʻe, i kekahi manawa aia kekahi mea koʻikoʻi i hūnā ʻia ma hope o kēia mau hōʻailona. ʻO ka Anemia Aplastic kekahi o nā maʻi kakaikahi, ʻo ia hoʻi, ʻaʻole i ʻike pinepine ʻia, akā hiki ke lilo i maʻi weliweli loa. No laila i kēia lā e kamaʻilio mākou e pili ana i kēia me ka kikoʻī a me ka maʻalahi, i hiki iā ʻoe ke loaʻa kahi ʻike maikaʻi aʻe i kēia.

I ka ʻōlelo maʻalahi, he aha ka anemia aplastic?

I nā huaʻōlelo maʻalahi, ʻo ka anemia aplastic ka wā e hana pono ʻole ai ka iwi iwi i loko o ko kākou kino. ʻIke ʻoe, ʻo ka ʻāpana o ko kākou mau iwi i kapa ʻia ʻo ka iwi iwi ka mea e hana ai i nā hunaola koko ʻulaʻula, nā hunaola koko keʻokeʻo, a me nā platelets e pono ai ko kākou kino. No laila, loaʻa ka anemia aplastic i ka wā ʻaʻole hiki i ka iwi iwi ke hana pono i kēia mau hunaola.

Ua like ia me kahi hale hana koko e pani koke ana. He aha ka mea e hana ʻia a laila? Nalowale ke kino i nā hunaola koko e pono ai. Hoʻonui kēia i ka pilikia o nā maʻi koʻikoʻi , hoʻolilo i mea paʻakikī ke hoʻōki i ke kahe ʻana o ke koko, a hiki ke alakaʻi i nā pilikia ʻē aʻe e like me ka maʻi puʻuwai. Aia nā lāʻau lapaʻau e kāohi i nā hōʻailona. Eia naʻe, ʻo ke ala wale nō e ho'ōla loa ai ma o ka hoʻoili ʻana i nā cell kumu .

Pehea ka maʻamau o kēia ʻano? Pono anei mākou e makaʻu pēlā?

ʻOiaʻiʻo, he mea laha ʻole kēia maʻi i kapa ʻia ʻo Aplastic Anemia. ʻO ia hoʻi, ʻaʻole ia he maʻi e hoʻopilikia i nā kānaka a pau. No ka laʻana, ma ʻAmelika Hui Pū ʻIa, ma waena o 300 a me 900 mau kānaka wale nō i ʻike ʻia me kēia maʻi i kēlā me kēia makahiki. Ma ʻEulopa, ua ʻōlelo nā noiʻi e hoʻopilikia kēia ʻano ma kahi o ʻelua mau kānaka i hoʻokahi miliona.

ʻOiai hiki ke hoʻopilikia i kekahi o kēlā me kēia makahiki, ʻoi aku ka maʻamau i nā poʻe ma waena o 15 a me 25 mau makahiki a me nā poʻe ma luna o 60 mau makahiki. No laila, mai hopohopo nui e pili ana i ka luhi mau a me ka noʻonoʻo inā loaʻa iā ʻoe kēia maʻi. Eia nō naʻe, he mea nui e makaʻala i nā hōʻailona.

He aha nā hōʻailona o ka Anemia Aplastic?

ʻAʻole ʻike ʻia nā hōʻailona o kēia maʻi i ka manawa hoʻokahi. I ka manawa pinepine, ʻike mālie ʻia kēia mau hōʻailona i nā pule a i ʻole nā ​​mahina. No laila, ʻaʻole paha ʻoe e ʻike i ka ʻokoʻa i ka wā mua. Eia nō naʻe, hiki i kekahi poʻe ke loaʻa koke nā hōʻailona koʻikoʻi. E nānā e ʻike inā loaʻa iā ʻoe kekahi o kēia mau hōʻailona:

• ʻOi aku ka pinepine o ka loaʻa ʻana o nā maʻi viral (e like me ke anu a me ka maʻi palū), a lōʻihi ka manawa e ho'ōla ai ma mua o ka maʻamau.
• Ka manaʻo mau o ka luhi nui a me ka luhi.
• ʻIke ʻia nā palapū ma ke kino holoʻokoʻa, a i ʻole he ʻeha liʻiliʻi e lōʻihi ka manawa e hoʻōki ai ke kahe ʻana o ke koko.
• Ke paʻakikī nei ka hanu ʻana (dyspnea), ʻoiai hoʻi i ka hana ʻana i nā hana liʻiliʻi.
• ʻIke ʻia aku ua ʻoi aku ka keʻokeʻo o ka ʻili ma mua o ka maʻamau.
• Pōʻaiʻī.
• ʻEha poʻo.
• Kuni.

E hoʻomanaʻo, hiki ke hana ʻia kekahi o kēia mau hōʻailona e nā maʻi ʻē aʻe, ʻaʻole koʻikoʻi. No ka laʻana, he mea maʻamau ka luhi a me ke kuni ke loaʻa iā ʻoe ke anu. No laila, mai hopohopo inā loaʻa iā ʻoe kekahi a ʻelua paha o kēia mau hōʻailona a manaʻo ʻoe he anemia aplastic kou. Eia nō naʻe, inā ua maʻi ʻoe no nā pule a ke manaʻo mau nei ʻoe i ka luhi hiki ʻole ke hoʻomanawanui, ʻoi aku ka maikaʻi o ke ʻike ʻana i ke kauka no ka ʻōlelo aʻo.

No ke aha e kū mai ai ka anemia aplastic? He aha nā kumu?

ʻO ka ʻoiaʻiʻo, ʻaʻole maopopo i nā loea ke kumu e loaʻa ai i kekahi poʻe ka anemia aplastic. Akā pinepine ia no ka mea ʻo kā mākou ʻōnaehana pale ponoʻī - ka ʻōnaehana e pale ai iā mākou mai ka maʻi - e kuhihewa iā mākou a hoʻouka i ko mākou iwi iwi ponoʻī, e luku ana i nā hunaola kumu ma laila. ʻO kēia mau hunaola kumu nā mea e hana i nā hunaola koko hou.

Ma waho aʻe o kēia, hiki i kekahi mau kumu ʻē aʻe ke hoʻopilikia i kēia:

Kekahi mau kūlana olakino:

• ʻO nā maʻi autoimmune , e like me lupus, he mau maʻi ia e hoʻouka ai kā mākou ʻōnaehana pale i ko mākou kino ponoʻī.
• ʻO kekahi mau maʻi viral, no ka laʻana, nā virus e like me ka Epstein-Barr virus, cytomegalovirus (CMV), parvovirus B19 , a me ka human immunodeficiency virus (HIV) .
• ʻO ka paroxysmal nocturnal hemoglobinuria kahi maʻi i loaʻa kahi e haki koke ai nā hunaola koko ʻulaʻula.
• ʻO ka hāpai ʻana i kekahi manawa ke kumu o kēia, akā he mea kakaikahi loa ia.

Nā kūlana e hiki mai ana mai nā hanauna mai:

I kekahi poʻe, hiki ke pili ka anemia aplastic me nā syndromes bone marrow failure i hoʻoilina ʻia. Ua kapa ʻia kēia mau mea ʻo 'inherited bone marrow failure syndromes'. Eia kekahi mau laʻana:

• ʻO ka maʻi anemia Fanconi
• ʻO ka maʻi dyskeratosis congenita
• ʻO ka maʻi Shwachman-Diamond
• ʻO ka anemia Diamond-Blackfan
• ʻO ka maʻi Pearson

ʻO kekahi mau lāʻau lapaʻau:

Hoʻonui pū kekahi mau lāʻau lapaʻau i ka pilikia o kēia ʻano.

• ʻO kekahi mau lāʻau lapaʻau no nā maʻi autoimmune.
• ʻO ka radiation a me ka chemotherapy no ke kanesa. Ma muli o ka ikaika loa o kēia mau lāʻau lapaʻau, hiki iā lākou ke hōʻino i ka iwi iwi.

Eia kekahi, ʻo ka hoʻohana lōʻihi ʻana i kekahi mau kemika i kapa ʻia ʻo carcinogens , e like me ka arsenic a me ka benzene , hiki ke hoʻonui i kēia pilikia.

He aha nā pilikia e hiki ai i kēia ke hana?

Hiki i kekahi kanaka me ka anemia aplastic ke loaʻa i nā pilikia e like me kēia, a hiki i kekahi o ia mau mea ke hoʻoweliweli i ke ola:

• Anemia: ʻO ke ʻano kēia o ka emi ʻana o ka nui o ke koko i loko o ke kino. Hiki i kēia ke hana i nā mea e like me ka luhi nui a me ka paʻakikī o ka hanu ʻana.
• Nā maʻi koʻikoʻi: I ka emi ʻana o nā hunaola koko keʻokeʻo, emi iho ka hiki ke pale aku i nā maʻi.
• Ke kahe koko nui: Ma muli o ka emi ʻana o nā platelets, ua lōʻihi ka manawa no ke koko e hoʻopili ai.
• ʻO ka hemahema o ka manawa o ka puʻuwai (arrhythmia) a i ʻole ka hāʻule ʻana o ka puʻuwai.
• ʻO ka Myelodysplastic syndrome kahi ʻano e ulu ai nā pūnaewele i loko o ka iwi iwi i ke ʻano ʻē.

Pehea e ʻike ʻia ai ka Anemia Aplastic?

Hoʻoponopono nā kauka i kēia maʻi ma ka nānā ʻana iā ʻoe, ka hana ʻana i nā hoʻokolohua koko, a i kekahi manawa ka hoʻāʻo ʻana i ka genetic. Hiki i kēia mau hoʻokolohua ke komo pū me:

• Helu koko piha (CBC) me ka ʻokoʻa: Ke ana kēia i ka helu o nā keena koko ʻulaʻula, nā ʻano keena koko keʻokeʻo ʻelima, a me nā platelets i loko o kou koko.
• ʻO ka palaki koko peripheral: Lawe ʻia kahi hāpana koko a nānā ʻia ma lalo o kahi microscope e nānā i ke ʻano a me ke ʻano o nā hunaola koko a me nā platelets.
• Helu Reticulocyte: Ke ana kēia i ka helu o nā hunaola koko ʻulaʻula hou i hana ʻia (reticulocytes).
• ʻO ka ʻume ʻana o ka iwi iwi a me ka biopsy iwi iwi: Ma kēia, lawe ʻia kahi hāpana liʻiliʻi o ka iwi iwi, maʻamau mai ka iwi ʻūhā, ma lalo o ka anesthesia. A laila e nānā ʻia ma lalo o kahi microscope e ʻike pono i ke ʻano o ka iwi iwi. ʻO kēia ka hoʻāʻo nui e hōʻoia i ka hōʻailona.

He aha nā lāʻau lapaʻau?

ʻOkoʻa nā koho lapaʻau ma muli o kou kūlana. No ka laʻana, loaʻa i kekahi poʻe ka anemia aplastic ma muli o nā lāʻau lapaʻau kanesa a i ʻole nā ​​​​lāʻau lapaʻau no nā maʻi autoimmune. I kēlā mau hihia, hiki i nā kauka ke hoʻāʻo e hoʻololi i kēlā mau lāʻau lapaʻau.

Inā haʻahaʻa ka helu o kou mau cell koko ma mua o ka maʻamau akā ʻaʻohe ou hōʻailona nui, e ʻōlelo paha kāu kauka he anemia aplastic moderate kou. I kēia hihia, e nānā mau ana kāu kauka i kou olakino a me nā helu koko. Ma kēia ʻano, hiki iā ʻoe ke hana koke inā ʻike ʻia kou kūlana e ʻoi aku ka ʻino.

ʻO nā lāʻau lapaʻau no nā hihia koʻikoʻi o ka anemia aplastic:

• Nā Immunosuppressants: Hana kēia mau lāʻau lapaʻau ma ke kāohi ʻana i ka hana o kāu ʻōnaehana pale a me ke kāohi ʻana iā ia mai ka hoʻouka ʻana i kou iwi iwi. ʻO nā hiʻohiʻona o kēia mau lāʻau lapaʻau e komo pū me ka antithymocyte globulin injection (Atgam®) a me ka cyclosporine (Sandimmune®) .
• Nā hoʻoili koko:ʻO kēia ke komo ʻana i ka hoʻololi ʻana i nā hunaola koko ʻulaʻula a me nā platelets i hoʻopau ʻia. ʻAʻole kēia e ho'ōla i ka maʻi, akā kōkua ia i ka hōʻoluʻolu ʻana i nā hōʻailona.
• Nā lāʻau lapaʻau: ʻO ka poʻe me ka anemia aplastic e piʻi aʻe ka pilikia o ka loaʻa ʻana o nā maʻi bacteria. No laila, hāʻawi ʻia nā lāʻau lapaʻau e mālama i nā maʻi.
• ʻO ka hoʻoili ʻana o nā cell kumu allogeneic: ʻO kēia ke ʻano lapaʻau nui no kēia maʻi. Ma kēia kaʻina hana, ua hoʻoili ʻia nā cell kumu olakino mai kahi mea hāʻawi olakino (pinepine he lālā ʻohana a i ʻole kahi mea hāʻawi i kūlike) i loko o ka iwi iwi i hōʻino ʻia o ka mea maʻi. Ma hope o kēia, hoʻomaka nā cell koko olakino hou e hana.

He aha nā hopena ʻaoʻao o ka lāʻau lapaʻau?

ʻOkoʻa nā hopena ʻaoʻao ma muli o ka lāʻau lapaʻau:

• ʻO ka maʻi Graft-versus-host: He pilikia kēia e hiki ke hana i ka wā o ka hoʻoili ʻana o nā cell stem allogeneic . ʻO ke ʻano kēia, hana nā cell i hoʻoili ʻia i ke kino o ka mea maʻi.
• Hoʻonui nā lāʻau immunosuppressant i ka pilikia o ka maʻi.
• Hoʻonui ʻia ka nui o ka hao i loko o ke kino ma muli o ke kahe koko pinepine ʻana (hemochromatosis / iron overload).

Hiki ke pale ʻia kēia?

ʻO ka mea pōʻino, ʻaʻohe ala i ʻike ʻia e pale aku ai i ka anemia aplastic i kēia manawa.

Hiki ke ho'ōla loa ʻia?

ʻAe, i kekahi mau hihia, hiki i kahi hoʻoili ʻana o nā cell kumu allogeneic holomua ke ho'ōla loa i kēia maʻi. Ma keʻano laulā, ʻoi aku ka nui o nā keiki a me nā poʻe ma lalo o 40 mau makahiki e holomua me kēia lāʻau lapaʻau ma mua o nā pākeke.

He aha nā kūlana e ola ai?

Pili maoli kēia i nā mea he nui. Kou mau makahiki, ka lāʻau lapaʻau āu e loaʻa ai, ke koʻikoʻi o kou maʻi, a pēlā aku. Ua hōʻike kekahi noiʻi ma ka laulā, 96% o ka poʻe i ola ma hope o ka hoʻoili ʻana i nā cell stem. Ua ʻike pū ka noiʻi like he 100% o nā keiki a me nā pākeke ma lalo o 40 mau makahiki i ola i ʻelima mau makahiki ma hope o ka lāʻau lapaʻau.

Eia nō naʻe, ua hoʻokumu ʻia kēia mau helu helu ma nā ʻike o kahi hui nui o ka poʻe. ʻAʻole paha lākou e hoʻopilikia iā ʻoe ma ke ʻano like. Inā he mau nīnau kāu e pili ana i kēia, ʻoi aku ka maikaʻi o ke kamaʻilio ʻana me kāu kauka. Hiki iā ia ke hāʻawi i ka ʻike i kūpono i kou kūlana.

Inā loaʻa iaʻu ka Aplastic Anemia, pehea wau e mālama ai iaʻu iho?

Inā loaʻa iā ʻoe kēia maʻi, he mea nui e mālama pono iā ʻoe iho. He mea nui e hahai pololei i ka hoʻolālā lapaʻau a kāu kauka a e makaʻala i kāu mau hōʻailona. Hiki iā ʻoe ke hana i kēia mau mea:

• E hōʻalo i nā hana e hiki ai ke hōʻeha hou aku. ʻOi aku kou pilikia o ke kahe ʻana o ke koko. No laila, ʻoi aku ka maikaʻi o ka noho mamao ʻana mai nā haʻuki e like me ka rugby, hockey, a me ka wrestling.
• E mālama iā ʻoe iho mai nā maʻi a me nā germs.ʻOi aku ka nui o kou loaʻa ʻana i nā maʻi. E nīnau i kāu kauka e pili ana i nā lāʻau pale kūpono iā ʻoe. E holoi pinepine i kou mau lima a e noho mamao aku mai ka poʻe maʻi (e like me ka poʻe me ke anu, ka maʻi palū, a i ʻole ka ʻōpū ʻeha).
• E hoʻomaha pono. ʻOiai ʻo ka anemia kahi pilikia o kēia, hiki iā ʻoe ke manaʻo luhi loa a pōkole ka hanu. He mea paʻakikī paha ke hana i nā hana o kēlā me kēia lā. No laila, e hoʻomaha a hiamoe maikaʻi i ka wā e pono ai, ʻaʻole i ka wā hiki iā ʻoe.
• E ʻai i ka meaʻai olakino. ʻO kahi meaʻai kaulike e komo pū ana me nā ʻiʻo momona, nā mea kanu, nā huaʻai, a me nā palaoa piha e kōkua i ka hoʻonui ʻana i kou pae ikehu. Inā hiki iā ʻoe ke loaʻa ka ʻōlelo aʻoaʻo mai kahi meaʻai loea, hiki iā ʻoe ke aʻo pehea e loaʻa ai ka hapa nui o nā meaʻai āu e ʻai ai.
• E hoʻoikaika kino. Hiki i ka hoʻoikaika kino māmā ke kōkua i ka hōʻemi ʻana i ke kaumaha. Eia nō naʻe, e kamaʻilio me kāu kauka ma mua o ka hoʻomaka ʻana i kahi hana hoʻoikaika kino hou.

Āhea ʻoe e ʻike ai i ke kauka?

E kāhea koke aku i kāu kauka i kēia hihia:

• Inā loaʻa iā ʻoe ke kuni he 38 kekelē Celsius (100.4 kekelē Fahrenheit) a ʻoi aku paha .
• Inā e ʻoi aku ka ʻino o kou mau hōʻailona.

He aha nā nīnau e pono iaʻu e nīnau aku i ke kauka?

Inā loaʻa iā ʻoe ka anemia aplastic, makemake paha ʻoe e nīnau i kāu kauka i kēia mau nīnau:

• He aha ke kumu kūpono loa o koʻu maʻi?
• He koʻikoʻi anei koʻu kūlana?
• He aha nā lāʻau lapaʻau āu e paipai nei?
• He aha nā hopena ʻaoʻao o ka lāʻau lapaʻau?
• ʻAʻohe oʻu hōʻailona. Pono anei au i ka lāʻau lapaʻau?
• He mau hōʻailona koʻu. He aha kaʻu mau koho lapaʻau?

He maʻi kanesa anei ka Anemia Aplastic?

ʻAʻole. ʻAʻole ka maʻi kanesa ka anemia aplastic. Eia nō naʻe, aia kekahi poʻe me ka anemia aplastic i ka pilikia o ka hoʻomohala ʻana i kahi ʻano maʻi koko i kapa ʻia ʻo leukemia .

He maʻi koko kakaikahi akā koʻikoʻi ka anemia aplastic. Hana pinepine ia i ka wā e hoʻouka ai kāu ʻōnaehana pale i kou iwi ponoʻī, e kāohi ana iā ia mai ka hana ʻana i nā hunaola koko a me nā platelets e pono ai kou kino. Nui nā kumu hiki, no laila e hopohopo a makaʻu paha ʻoe no ia mea. Eia naʻe, ʻoiai ʻaʻole hiki i nā kauka ke loaʻa kahi kumu kikoʻī, hiki ke mālama ʻia ke ʻano a i kekahi manawa hoʻōla ʻia. Inā loaʻa iā ʻoe ka anemia aplastic, e wehewehe kāu kauka i nā koho lapaʻau kūpono iā ʻoe a me ko lākou mau hopena ʻaoʻao. No laila, e wiwo ʻole a e hahai i ka ʻōlelo aʻo a kāu kauka.

He Leka Lawe-Home mai iā Mākou

Hiki ke hopohopo ka Anemia Aplastic ke lohe ʻoe i ka inoa. No ka mea, he maʻi koʻikoʻi ia. Akā e hoʻomanaʻo, aia kahi lāʻau lapaʻau no ia mea. Inā ʻike mua ʻoe i nā hōʻailona, ​​e ʻimi i ke aʻo lapaʻau, a hoʻomaka i ka lāʻau lapaʻau, hiki iā ʻoe ke kāohi i kēia maʻi, a hoʻōla iā ia.

ʻO ka mea nui loa, inā loaʻa iā ʻoe ka luhi i wehewehe ʻole ʻia, ka maʻi pinepine, a i ʻole ke kahe koko ʻē, mai hoʻowahāwahā wale iā ia a ʻike i ke kauka no ka nānā ʻana. ʻO ka wā mua āu e ʻike ai, ʻo ka nui o ka kūleʻa o ka lāʻau lapaʻau. ʻAʻole ʻoe hoʻokahi, a aia nā kauka, ka ʻohana, a me nā hoaaloha ma laila e kōkua iā ʻoe ma kēia huakaʻi.

ʻAnemia Aplastic, Anemia Aplastic, Anemia, Iwi ʻōpū, Nā Maʻi Koko, Hoʻoili Kelepona Kumu, ʻŌnaehana Palekana