Loaʻa iā ʻoe i kekahi manawa nā palapū ma kou kino? A i ʻole he lōʻihi ka manawa e pau ai ke kahe ʻana o ke koko ma hope o kahi ʻoki liʻiliʻi? Malia paha e kahe mau ana kou mau ʻāʻī? I kekahi manawa hiki i kēia ke lilo i hōʻailona o kahi pilikia me nā platelets, kahi ʻano cell liʻiliʻi i loko o ko kākou koko. I kēia lā, e kamaʻilio mākou e pili ana i ke ʻano o kēia mau maʻi platelet.
He aha kēia mau maʻi platelet?
I ka ʻōlelo maʻalahi, ʻo nā maʻi platelet he mau kūlana e hoʻopilikia ai i ka helu o nā platelets i loko o kou koko a i ʻole ke ʻano o kā lākou hana. ʻAe, i kēia manawa ke noʻonoʻo nei paha ʻoe, "He aha kēia mau platelets?" E wehewehe pū kākou i kēlā.
He aha nā platelets?
E noʻonoʻo he ʻeha liʻiliʻi kou. Pau ke kahe ʻana o ke koko ma hope o kekahi manawa, ʻeā? ʻĀ, kōkua kēia mau platelets i kēlā. He mau ʻāpana liʻiliʻi loa nā platelets (e like me nā ʻāpana o nā cell) i loko o ko kākou koko. Hana ʻia lākou i loko o ko kākou iwi iwi. Ke loaʻa kahi ʻeha, hui pū kēia mau platelets, sila i ka ʻeha a hoʻōki i ke kahe ʻana o ke koko. Ua like ia me ka plaster kūlohelohe i loko o ko kākou kino! Hoʻopili lākou a hana i kahi clot koko. ʻO kēia ke kaʻina hana nui e hoʻōki ai i ke kahe ʻana o ke koko.
No laila he aha nā maʻi platelet?
No laila, he hewa ka maʻi platelet me kēia mau platelet. ʻO ia hoʻi, he haʻahaʻa a kiʻekiʻe paha kāu helu platelet, a inā paha he nui kūpono kāu o nā platelet, ʻaʻole paha lākou e hana pono. I kēlā me kēia ʻano, hiki iā ia ke hoʻoulu i nā pilikia kahe koko.
He aha nā ʻano nui o nā maʻi platelet?
ʻEkolu mau ʻano nui o nā maʻi platelet:
1. Thrombocytosis: ʻO ke ʻano kēia, ʻoi aku ka nui o nā platelets i loko o kou koko ma mua o ka maʻamau .
2. Thrombocytopenia: ʻO kēia ka manawa e haʻahaʻa loa ai ka helu o nā platelets i loko o kou koko ma mua o ka maʻamau .
3. Ka hana pono ʻole o ka platelet: Maanei, ʻoiai he maʻamau ka helu platelet i loko o kou koko, ʻaʻole lākou e hana pono. Ua like ia me ka loaʻa ʻana o ʻehā mau huila ma ke kaʻa, akā ua palahalaha kekahi o lākou.
ʻO ka hapa nui o ka manawa, ʻaʻole koʻikoʻi nā hōʻailona o kēia mau maʻi platelet. ʻAʻole paha e hōʻike kekahi poʻe i kekahi mau hōʻailona. Eia nō naʻe, i kekahi mau hihia, ʻoiai inā haʻahaʻa nā platelet a hana pono ʻole paha, aia paha ka nui o ka pilikia o ke kahe ʻana o ke koko. Eia kekahi, inā kiʻekiʻe loa ka helu platelet, aia paha ka nui o ka pilikia o ka hoʻokumu ʻana o nā clots koko (kahi clot koko weliweli) .
Hiki i kāu kauka ke wehewehe i kēia mau pilikia a ʻōlelo aku i nā lāʻau lapaʻau e pono ai e pili ana i kou kūlana.
He aha kēia mau hōʻailona?
ʻO kekahi o nā hōʻailona e ʻike ʻia i nā maʻi platelet:
- Nā hōʻailona o ke kahe koko ma lalo o ka ʻili:
- ʻIke wale ʻia nā palapū ma nā wahi o ke kino. I kekahi manawa ua kapa ʻia kēia he purpura.
- ʻIke ʻia nā kiko ʻulaʻula liʻiliʻi e like me ke kiko kui (petechiae) ma ka ʻili. ʻO kēia mau wahi ʻaʻole maneʻo a ʻaʻole e lilo i keʻokeʻo ma o lākou iho.
- Loaʻa i nā wāhine ke kahe nui o ke koko i ka wā o ka menstruation (ʻoi aku ka lōʻihi ma mua o ka maʻamau, kahe nui ke koko).
- Ka kahe pinepine ʻana o ke koko ihu.
- Ke kahe koko ʻana o nā ʻāʻī i ka wā e palaki ai i kou mau niho.
- ʻO ke koko i loko o kou noho (hiki ke lilo i ʻeleʻele) a i ʻole ke koko i loko o kou mimi (hiki ke lilo i ʻulaʻula/poni).
- Manaʻo nāwaliwali, poniuniu, a maule paha (ʻoi aku hoʻi i ka wā e kahe ai ke koko).
- I kekahi manawa hiki ke hana ʻia nā ʻūpā koko kūpono ʻole (ʻoi aku hoʻi i nā hihia o ka helu platelet kiʻekiʻe).
Inā loaʻa iā ʻoe kekahi a ʻoi aku paha o kēia mau hōʻailona, ʻoi aku ka maikaʻi o ka ʻimi ʻana i ke kōkua lapaʻau.
No ke aha lā kēia e hana nei? He aha nā kumu?
Hiki ke loaʻa nā maʻi platelet no nā kumu like ʻole. I kekahi manawa, hiki ke hana ʻia e kekahi maʻi ʻē aʻe āu e loaʻa ai a i ʻole kahi lāʻau lapaʻau āu e lawe ai. I kekahi manawa, hiki ke hana ʻia e kahi maʻi genetic āu e hoʻoilina ai mai kou mau mākua mai.
Nā kumu o nā platelets kiʻekiʻe
ʻElua mau kumu nui no ka hoʻonui ʻana o nā platelet:
- ʻO ka thrombocythemia koʻikoʻi: He ʻano laha ʻole kēia kahi e hana ai kou iwi iwi i nā platelets he nui aʻe ma mua o ka mea e pono ai ma muli o ka hoʻololi ʻana o ka genetic.
- ʻO ka thrombocytosis reactive: ʻO kēia ke ʻano maʻamau. Hana ʻia ia i ka wā e hana ai ke kino i nā platelets he nui i ka pane ʻana i kekahi kūlana ʻē aʻe. Eia kekahi laʻana:
- ʻAʻai anemia nele i ka hao.
- Nā kūlana mumū i loko o ke kino (e.g. ke kanesa, nā maʻi).
- Nā ʻeha.
- Kekahi mau lāʻau lapaʻau.
Nā kumu o nā platelets haʻahaʻa
Aia paha kekahi mau kumu e emi ai ka helu platelet:
- ʻAʻole hana ke kino i nā platelets lawa: Hiki paha kēia ma muli o kahi pilikia me ka iwi iwi.
- ʻO ka luku ʻia ʻana o nā platelet ma muli o kahi maʻi: No ka laʻana, i loko o nā `(Nā maʻi Autoimmune)` (nā maʻi o ka ʻōnaehana pale), hoʻopau ka ʻōnaehana pale ponoʻī o ke kino i kāna mau platelet ponoʻī. ʻO ia ʻano maʻi ka `(Immune thrombocytopenia - ITP)`.
- Mālama ka spleen i nā platelets hou aʻe: ʻO ka maʻamau, mālama ka spleen i kahi hapakolu o kā mākou mau platelets. Eia nō naʻe, i kekahi mau maʻi, piʻi kēia nui.
- Nā kumu ʻē aʻe:
- ʻAʻai koko (i hana ʻia e ka hoʻopiha ʻana o ka iwi me nā hunaola kanesa).
- ʻO kekahi mau maʻi koko, no ka laʻana `(Thrombotic thrombocytopenic purpura - TPP)` a me `(Disseminated intravascular coagulation - DIC)`.
- Nā maʻi koʻikoʻi.
- Kekahi mau lāʻau lapaʻau a me nā lāʻau lapaʻau no ke kanesa (Chemotherapy, Radiation therapy).
Nā kumu o ka hana ʻole o ka platelet
I kekahi manawa, ʻoiai inā maʻamau ka helu platelet, aia paha kekahi pilikia me kā lākou hana. Aia kekahi mau kumu no kēia:
- Nā kūlana hānau (genetic): He mea kākaʻikahi loa kēia. Nā laʻana: `(Bernard Soulier syndrome)`, `(Glanzman thrombasthenia)`, `(Von Willebrand disease)` (ka mea e hoʻopilikia ai i ka hana platelet a me nā mea ʻē aʻe e pili ana i ke kāpili ʻana o ke koko), `(Wiskott-Aldrich syndrome)`.
- Nā kūlana i loaʻa: ʻO nā maʻi e like me ka hāʻule ʻana o ka puʻupaʻa, ka maʻi ate, a me ka lupus e hiki ke hoʻopili i ke ʻano o ka hana ʻana o nā platelets.
- Nā lāʻau lapaʻau: Hiki i kekahi mau lāʻau lapaʻau, ʻoiai nā SSRI antidepressants a me nā NSAID, ke hoʻopilikia i ka hana platelet. ʻO ka ʻoiaʻiʻo, ʻo ka hana ʻole o ka platelet i hoʻoulu ʻia e ka lāʻau lapaʻau ke kumu maʻamau.
ʻO wai ka mea i ʻoi aku ka nui o ka pilikia o ka hoʻomohala ʻana i kēia mau mea?
Aia kekahi mau kumu e hoʻonui ai i ka pilikia o ka hoʻomohala ʻana i kahi maʻi platelet:
- Makahiki: Hiki ke ʻike pinepine ʻia kekahi mau maʻi platelet i kekahi mau hui makahiki.
- Kāne: ʻOiai hiki i kekahi ke loaʻa iā ia, ʻoi aku ka nui o nā wahine e ʻike i nā hōʻailona i ka wā o ke kahe koko, e like me ka menstruation a me ka hānau keiki ʻana.
- Moʻolelo ʻohana: Hiki ke hoʻoili ʻia kekahi mau maʻi platelet genetic mai kēlā hanauna a kēia hanauna.
- Nā kūlana olakino ʻē aʻe: Nui nā maʻi, e like me nā maʻi autoimmune, nā maʻi, nā maʻi puʻupaʻa a me ke ake, a me ke kanesa, hiki ke hana i nā pilikia platelet.
- Nā lāʻau lapaʻau no ke kanesa: Hiki i ka chemotherapy a me ka radiation therapy ke hōʻemi i ka helu platelet.
- Nā lāʻau lapaʻau: Hiki i nā antibiotics a me kekahi mau lāʻau lapaʻau no ka maʻi epilepsy ke hoʻopilikia i nā platelets.
- ʻAno nohona: ʻO ka inu nui ʻana i ka waiʻona a me ka hoʻohana ʻana i nā huahana paka e hiki ke hoʻopilikia i ka hana ʻana o nā platelet.
He aha nā pilikia e hiki ke kū mai mai kēia maʻi?
Inā ʻaʻole mālama pono ʻia nā maʻi platelet, hiki ke loaʻa kekahi mau pilikia:
- Ke kahe koko: ʻOiai kahi ʻeha liʻiliʻi hiki ke hoʻoulu i ka nui o ke kahe koko.
- Ke kahe koko nui o ke koko i nā wahine (Menorrhagia).
- Ke kahe koko ʻana o ka ʻōpū.
- I nā kūlana e like me ka 'thrombocytosis koʻikoʻi', hiki ke loaʻa nā kūlana weliweli e like me ke koko i loko o nā aa koko o nā wāwae (deep vein thrombosis) a i ʻole nā koko koko i loko o nā māmā (pulmonary embolism) .
- ʻO ka pilikia o ka hōʻeha puʻuwai a i ʻole ka hahau ʻana (ʻoi aku hoʻi inā maʻalahi ke ʻano o nā ʻūpā koko).
Akā, e hoʻomanaʻo,Ma ka hana pū ʻana me ke kauka a me ka hahai ʻana i kahi hoʻolālā lapaʻau kūpono, hiki ke pale ʻia kēia mau pilikia he nui.
Pehea ʻoe e ʻike ai i kēia? (Diagnosis)
Inā loaʻa iā ʻoe nā hōʻailona o ka maʻi platelet, e hana mua ke kauka i kahi hoʻokolokolo kino. E nīnau lākou e pili ana i kāu mau hōʻailona, nā lāʻau lapaʻau āu e lawe ai, a inā paha ua loaʻa i kekahi o kou ʻohana nā pilikia like. E lawe pū lākou i kahi mōʻaukala lapaʻau. A laila, e hana lākou i kekahi mau hoʻokolohua koko e nānā i kāu mau platelet.
ʻO nā hoʻāʻo koko nui:
- Helu koko piha (CBC): Ke ana kēia i ka helu o nā hunaola koko ʻulaʻula, nā hunaola koko keʻokeʻo, a me nā platelets i loko o kou koko.
- ʻO ka palaki koko peripheral (PBS): Ma kēia hoʻokolohua, lawe ʻia kahi kulu o kāu hāpana koko a nānā ʻia ma lalo o kahi microscope e ʻike inā he maʻamau ke ʻano o nā platelets a inā he mau loli i ko lākou ʻano a i ʻole ka nui.
- Nā hoʻāʻo hana platelet: Nānā kēia mau hoʻāʻo i ka maikaʻi o kāu mau platelets e hana ai i nā ʻūpū koko a inā e hana pono ana lākou.
Inā hōʻoia kēia mau hoʻokolohua he maʻi platelet kou, pono paha ʻoe e loaʻa nā hoʻokolohua hou aʻe e ʻike ai i ke kumu o ia mea. Eia kekahi laʻana:
- ʻO ka biopsy iwi iwi: Ma kēia, lawe ʻia kahi hāpana liʻiliʻi o ka iwi iwi a nānā ʻia no nā ʻano ʻē (nā hōʻailona o ka maʻi koko a i ʻole ke kanesa).
- Hoʻāʻo genetic: ʻOiai ʻo kekahi mau maʻi platelet i hoʻokumu ʻia e nā kumu genetic, ke nānā nei kēia hoʻāʻo i nā mutations genetic e pili ana me lākou.
He aha nā lāʻau lapaʻau?
ʻO ka mālama ʻana no nā maʻi platelet e pili ana i ke kumu. He manawa pōkole kekahi mau kūlana a hoʻopau ʻia ke pau ke kumu. Eia nō naʻe, inā loaʻa iā ʻoe kahi maʻi platelet mau loa (lōʻihi), pono ʻoe e ʻike i kahi hematologist a loaʻa ka lāʻau lapaʻau e mālama pono i kāu mau pae platelet.
Hiki ke hana i kēia mau mea ma ke ʻano he lāʻau lapaʻau:
- Ke kali makaʻala: Inā ʻaʻole koʻikoʻi kāu mau hōʻailona, ʻaʻole paha ʻoe e pono koke i ka lāʻau lapaʻau. Akā, e nānā kāu kauka i kāu mau pae platelet me nā hoʻāʻo koko maʻamau.
- Nā lāʻau lapaʻau: Inā kiʻekiʻe loa kou helu platelet, inā paha ma muli o kahi kūlana e like me ka 'essential thrombocytosis' a i ʻole kekahi maʻi koko ʻē aʻe (e like me ka '(myeloproliferative disease)'), hiki ke hāʻawi ʻia iā ʻoe ka lāʻau lapaʻau e hoʻohaʻahaʻa iā ia. Pēlā nō, inā haʻahaʻa kou helu platelet, hiki ke hāʻawi ʻia iā ʻoe ka lāʻau lapaʻau e hoʻonui i kā lākou hana ʻana a i ʻole e hōʻemi i ko lākou luku ʻia.
- Ka hoʻopau ʻana o nā platelet: Hana kākaʻikahi ʻia kēia. ʻO ke kaʻina hana i kapa ʻia ʻo apheresis e wehe i nā platelet keu mai ke koko.
- Ka hoʻoili ʻana o ka platelet:Inā haʻahaʻa loa ka helu o kāu platelet (ʻoi aku hoʻi inā e kahe ana ke koko), hiki ke hāʻawi ʻia nā platelets iā ʻoe ma waho.
- Lapaʻau plasma / hoʻololi plasma: Pono paha kēia lāʻau lapaʻau i nā hihia o nā maʻi e like me TPP. Pili kēia i ka hoʻololi ʻana i ka ʻāpana koko i nalowale i kapa ʻia ʻo (ADAMTS13).
Pehea ʻoe e noho ai me kēia maʻi? Pehea ʻoe e mālama ai iā ʻoe iho?
E hilinaʻi kou ʻike i ke ʻano o ka maʻi platelet āu e loaʻa ai a me ke kumu. I ka hapanui o nā hihia, e hoʻi hou kāu helu platelet i ka maʻamau ke mālama ʻia ke kumu. A i ʻole, ʻaʻole paha e hoʻoweliweli kou kūlana i ke ola a hiki i kou loaʻa ʻana o kahi ʻeha. I kēlā hihia, pono ʻoe e hana i nā hana e hōʻemi i ka pilikia o ka ʻeha. Inā ʻoe e loaʻa ana i kahi mea e like me ke ʻoki ʻana, pono kāu hui lapaʻau e mālama pono e pale i ke kahe ʻana o ke koko.
I nā hihia koʻikoʻi, pono paha ʻoe e hoʻomau i ka lawe ʻana i ka lāʻau lapaʻau, e hana i nā lāʻau lapaʻau maʻamau, a e hana i nā hoʻokolohua e hōʻoia i loaʻa iā ʻoe nā platelets olakino i loko o kou kino.
Inā pono ʻoe e noho me kahi maʻi platelet, ʻo ka mea maikaʻi loa hiki iā ʻoe ke hana, ʻo ia ke hoʻomaopopo pono i ke ʻano e hōʻemi ai i kou pilikia o ke kahe ʻana o ke koko a i ʻole nā ʻū koko weliweli. He mea nui e ʻike i kēia mau mea:
- Nā hana e pale aku ai: Hiki i kekahi mau maʻi platelet ke hoʻoulu i ke kahe koko nui inā ʻeha ʻoe. No laila, pono e pale ʻia nā hana e kiʻekiʻe ka pilikia o ka hōʻeha (e laʻa, nā haʻuki pili).
- Pehea e mālama ai i kahi ʻeha: Inā he pilikia o ke kahe ʻana o ke koko, he mea nui e ʻike pehea e kaomi ai i kahi ʻeha e hoʻōki ai i ke kahe ʻana o ke koko. Hiki i kāu kauka ke aʻo iā ʻoe pehea e hana ai i kēia.
- Nā lāʻau lapaʻau e lawe ai (a ʻaʻole e lawe): Pono paha ʻoe e hoʻomau i ka lawe ʻana i nā lāʻau lapaʻau e mālama i kahi maʻi platelet. Pono paha ʻoe e pale i kekahi mau lāʻau lapaʻau (e like me NSAID e like me ka aspirin) e hoʻopilikia i ka hana platelet a hoʻonui i ka pilikia o ke kahe ʻana o ke koko.
- Nā mea hoʻohui e pale aku ai: Hiki i kekahi mau mea hoʻohui ke hoʻonui i ka pilikia o ke kahe koko i nā poʻe me nā maʻi platelet. E nīnau i kāu kauka he aha kēia mau mea.
- Pehea e kamaʻilio ai me kāu mau kauka: Inā ʻoe e hoʻolālā ana e loaʻa kekahi mea e hiki ai ke hoʻokahe koko, inā he hana liʻiliʻi e like me ka unuhi ʻana i ka niho a i ʻole kahi ʻoki kino nui, pono ʻoe e hoʻomaopopo i kāu mau kauka e pili ana i ia mea.
E ʻimi i ka ʻōlelo aʻo no kēia mau mea a pau mai kāu hematologist a i ʻole ke kauka e mālama nei i kou kūlana.
Āhea ʻoe e ʻike ai i ke kauka?
Inā ʻike ʻoe i nā hōʻailona o kahi maʻi platelet, e like me ka ʻeha mau ʻana me ke kumu ʻole (ʻoi aku ka nui o nā ʻeha ma mua o kahi ʻāpana ʻelima rupee āu e hoʻomanaʻo ʻole ai) , e ʻike i ke kauka.
Inā loaʻa iā ʻoe nā hōʻailona o ke kahe koko nui (e laʻa me ke kahe koko ʻole e pau, ka poniuniu nui, ka nalowale o ka ʻike) a i ʻole nā hōʻailona o ke koko i hoʻopaʻa ʻia (e laʻa me ka ʻeha o ka umauma, ka paʻakikī o ka hanu ʻana, ka paʻakikī o ka ʻōlelo ʻana, ka mae ʻana o ka lima a i ʻole ka wāwae - he mau hōʻailona paha kēia o ka "stroke" a i ʻole ka "hōʻeha puʻuwai"), e hele koke i kahi lumi pilikia.
He aha nā nīnau āu e nīnau ai i ke kauka?
Ke ʻike ʻoe i ke kauka, mai kānalua e nīnau i nā nīnau e like me kēia:
- Pehea ke koʻikoʻi o koʻu kūlana?
- Hiki ke ho'ōla loa ʻia kēia?
- He aha nā ʻano lāʻau lapaʻau e kōkua iaʻu?
- ʻEhia pinepine e pono ai iaʻu e nānā i ka nui o kaʻu platelet?
- He aha kaʻu e hana ai e pale aku ai i ke kahe koko weliweli a i ʻole nā ʻūpā koko?
He leka hope loa e lawe ʻia i ka home
Nui nā mea e hiki ke hoʻopilikia i nā platelets, a hiki i kekahi mau lāʻau lapaʻau. No laila, mai manaʻo ʻoe i ka mea ʻino loa ke ʻike ʻoe he ʻano ʻē kāu helu platelet. Eia nō naʻe, he mea nui e ʻike pono i ke kumu o ka pilikia. A laila wale nō ʻoe e ʻike pono ai i kāu mea e hana nei.
Inā manaʻo ʻoe he mau hōʻailona kou o kahi maʻi platelet, e ʻike i ke kauka. Hiki iā ia ke kuhikuhi i nā lāʻau lapaʻau e kōkua i ka hoʻihoʻi ʻana i kāu mau pae platelet i ka maʻamau a i ʻole e hoʻokele i kou kūlana. ʻO ke ala maikaʻi loa e noho olakino ai, ʻo ia ke wehe, e nīnau i nā nīnau, a e loaʻa ka hoʻomaopopo maikaʻi i kou kūlana.
nā maʻi platelet, nā platelet, ke kahe ʻana o ke koko, ke kāpili ʻana o ke koko, ka thrombocytopenia, ka thrombocytosis, ka hana pono ʻole o ka platelet, ka lāʻau lapaʻau Sinhala, nā maʻi koko











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