Ke ʻeha mau nei ka ʻōpū o kāu pēpē? E aʻo kākou e pili ana i kēia (Autoimmune Enteropathy)?

Ke kahe mau nei anei ka ʻōpala o kāu keiki liʻiliʻi? ʻAʻole anei he mea ʻino ke hana ʻia no ʻelua a ʻekolu paha lā? I kekahi manawa, ma ke ʻano he mau mākua, hopohopo iki mākou ke ʻike mākou i nā mea e like me kēia? ʻOiai he pēpē hānau hou ia, hopohopo nui mākou i kēlā me kēia loli liʻiliʻi iā ia. No laila, i kēia lā e kamaʻilio mākou e pili ana i kahi maʻi kakaikahi loa e hōʻike ana i nā hōʻailona like.

He aha ka "Autoimmune Enteropathy"? E hoʻomaopopo maʻalahi kākou, ʻeā?

I ka ʻōlelo maʻalahi, ʻo `(Autoimmune Enteropathy)` he maʻi kakaikahi kahi e hoʻouka hewa ai ka ʻōnaehana pale ponoʻī o ko mākou kino, ʻo ia hoʻi, ka ʻōnaehana pale, i ko mākou mau ʻōpū ponoʻī . E noʻonoʻo i ka mea e hana ʻia ma ʻaneʻi, inā hoʻouka ka pūʻali koa i manaʻo ʻia e pale i ko mākou ʻāina, i kahi wahi koʻikoʻi ma ko mākou ʻāina ponoʻī. ʻO ka maʻamau, hoʻopilikia kēia i nā keiki ʻōpio. Akā hiki nō hoʻi ke ulu i nā pākeke i kēlā me kēia manawa.

Ke loaʻa i nā pēpē kēia maʻi, he wai ko lākou ʻōpala a hoʻomau. ʻAʻole e pau kēia maʻi kahe ma hope o ʻelua a ʻekolu paha lā. Hoʻomaka kēia mau hōʻailona e ʻike ʻia ma waena o ʻelua a ʻehā pule ma hope o ka hānau ʻana o ka pēpē.

He aha ka mea e hana ʻia ke hōʻino ka ʻōnaehana pale i nā ʻōpū ma kēia ʻano? ʻAʻole hiki i ke kino ke omo i nā meaʻai mai ka waiū umauma a i ʻole ka waiū waiū a ka pēpē e inu ai. Akā, hoʻokuʻu ʻia kēlā mau meaʻai a pau mai ke kino ma ke ʻano he maʻi kahe. Hiki i kēia ke hoʻomaloʻo i ka pēpē, ʻo ia hoʻi, nele lākou i ka wai. Eia kekahi, ʻaʻole paha e loaʻa ke kaumaha o ka pēpē e like me ka mea i manaʻo ʻia.

Inā ʻoe e lawe i kāu pēpē no nā nānā pēpē maikaʻi mau, hiki i ke kauka lapaʻau ke ʻike i nā pilikia me ka ulu ʻana a i ʻole ke olakino o kāu pēpē. Eia nō naʻe, inā ʻike ʻoe i kekahi mau loli i ka ʻōpala o kāu pēpē, mai hoʻokaʻulua i ka haʻi ʻana i ke kauka.

ʻO kēia kūlana, i kapa ʻia ʻo "Autoimmune Enteropathy," ua mālama ʻia me nā lāʻau lapaʻau e hōʻemi a hoʻōki paha i ka ʻōnaehana pale mai ka hoʻouka ʻana i nā ʻōpū.

Pehea ka maʻamau o kēia maʻi?

He maʻi laha ʻole ka Autoimmune Enteropathy. Wahi a nā loea, inā ʻoe e nānā a puni ka honua, ma kahi o hoʻokahi i loko o kēlā me kēia haneli tausani pēpē e loaʻa i kēia maʻi. ʻOiai hiki i nā pākeke ke loaʻa i kēia maʻi, ʻoi aku ka liʻiliʻi o ia ma mua o nā pēpē. No laila, mai makaʻu pono ʻole ma hope o ka lohe ʻana i kēia.

He aha nā hōʻailona o ka `(Autoimmune Enteropathy)`?

ʻO ka hōʻailona nui , ka neʻe mau ʻana o ka ʻōpū wai (diarrhea) ma kahi o nā ʻōpala palupalu e hele mau ai nā pēpē hānau hou a me nā keiki ʻōpio.

ʻO kekahi hōʻailona ʻē aʻe, ʻo ia ka incontinence (ʻaʻole mimi). Pono kahi pēpē hānau hou e loaʻa ma ka liʻiliʻi he ʻelima a ʻeono mau diaper pulu i ka lā. ʻO ka emi ʻana o nā diaper pulu ma mua o kēlā he hōʻailona paha ia ua maloʻo kāu pēpē.

E noʻonoʻo, ʻo ka maʻamau, he ʻōpala ka pēpē i nā manawa he nui i ka lā, a he mānoanoa iki a he kala kona. Akā i kēia hihia, he wai wale nō ka ʻōpala. A he ʻoluʻolu ʻole paha ka pēpē a uē.

He aha ke kumu o ka `(Autoimmune Enteropathy)`?

ʻAʻole ʻike ka poʻe loea i ke kumu kikoʻī. ʻO ka hapa pinepine, loaʻa i nā pēpē me ka autoimmune enteropathy kahi immunodeficiency mua e hōʻino ana i ka villi i loko o ko lākou ʻōpū liʻiliʻi.

Ua ʻike anei ʻoe i ke ʻano o kēia mau `(villi)`? ʻO ia nā mea liʻiliʻi e like me ka lauoho e hoʻopuni ana i nā paia o ka ʻōpū liʻiliʻi o kāu pēpē. Ua like lākou me nā olonā ma luna o kahi kāpeti liʻiliʻi. ʻO kā lākou hana nui, ʻo ia ke omo i nā meaʻai mai ka meaʻai a kāu pēpē e ʻai ai (waiū umauma a i ʻole ka waiū waiū) a hoʻouna i kēlā mau meaʻai i ke kahe koko o kāu pēpē. No laila, i ka wā e hōʻino ʻia ai kēia mau `(villi)`, ʻaʻole hiki nā meaʻai i ke kino.

He aha nā pilikia e hiki mai ana o kēia maʻi?

Hiki i ka Autoimmune Enteropathy ke hana i nā pilikia like ʻole. ʻO kekahi o lākou:

• Ka maloʻo ʻana o ka wai: Ke emi nei ka nui o ka wai i loko o ke kino ma muli o ka luaʻi mau ʻana. He mea weliweli loa kēia no nā pēpē ʻōpio.
• Hypoproteinemia: Haʻahaʻa ka pae protein i loko o ke koko ma muli o ka ʻole o ka komo ʻana o nā meaolaola.
• Nā maʻi pinepine: Ma muli o ka hana hewa ʻana o ka ʻōnaehana pale a me ka nele i nā meaʻai, ʻoi aku ka nui o ka maʻi o nā pēpē.
• Malabsorption: ʻO kēia ka pilikia nui. Ma muli o ka hōʻino ʻia o nā ʻōpū, ʻaʻohe meaʻai i komo i loko o ke kino.

Hiki i kēia mau pilikia ke hoʻoulu i ka ulu maikaʻi ʻole o ka pēpē, e emi ke kaumaha, a maʻi mau i nā manawa a pau.

Pehea e ʻike ai nā kauka i ka Autoimmune Enteropathy?

E nīnau aku kāu kauka keiki iā ʻoe e pili ana i nā hōʻailona o kāu pēpē a hana i kahi hoʻokolokolo kino. A laila e kauoha paha lākou i nā hoʻokolohua e like me:

• Nā hoʻāʻo koko: No ka ʻike ʻana i kekahi mau ʻano ʻē aʻe i loko o ka ʻōnaehana pale.
• Flow Cytometry: He ʻano kēia no ka nānā ʻana i nā laʻana o nā pūnaewele ʻōnaehana pale me ka hoʻohana ʻana i nā kukuna laser kūikawā.

Eia kekahi, hiki i kāu kauka ke kuhikuhi iā ʻoe i kahi gastroenterologist, nāna e hana i nā hoʻokolohua e like me ka biopsy ʻōpū liʻiliʻi . Hiki i kāu pediatrician ke kuhikuhi iā ʻoe i kahi loea i nā maʻi autoimmune.

Pehea e mālama ʻia ai ka `(Autoimmune Enteropathy)`?

Inā ua ʻike ʻia kāu pēpē me kēia maʻi, e hāʻawi ʻia paha iā ia nā wai a me ka meaʻai ma ke ʻano intravenous (ma o kahi aʻa - ``IV``) . ʻO ke ʻano kēia o ka hāʻawi ʻana iā lākou i ka saline, no ka mea, ʻaʻole hiki i ke kino ke omo i kekahi mea i hāʻawi ʻia ma ka waha.

Eia kekahi, hāʻawi ʻia nā lāʻau lapaʻau e kaupalena i ka hoʻouka ʻana o ka ʻōnaehana pale ma ka ʻōpū liʻiliʻi o ka pēpē. ʻO nā lāʻau lapaʻau kikoʻī:

• Nā Corticosteroids:He ʻano lāʻau lapaʻau ikaika kēia e hoʻemi ana i ka hana o ka ʻōnaehana pale.
• Nā Immunomodulators: ʻO kēia nā lāʻau lapaʻau e kōkua i ka hōʻemi ʻana i ka pōʻino ma o ka hoʻololi ʻana i ka hana o ka ʻōnaehana pale.

I kekahi mau hihia, inā ʻaʻole i loaʻa nā hopena i makemake ʻia i kēia mau lāʻau lapaʻau, hiki i nā kauka ke hoʻohana i nā lāʻau lapaʻau paʻakikī, e like me ka hoʻoili ʻana i nā cell stem . Eia nō naʻe, pili nui kēia i ke kūlana o ka pēpē.

He aha kaʻu e manaʻo ai inā loaʻa i kaʻu pēpē ka `(Autoimmune Enteropathy)`?

ʻAʻole like nā pēpē a pau, no laila e ʻokoʻa nā mea āu e manaʻo ai ma muli o ko lākou kūlana. I kekahi mau hihia, hiki i nā lāʻau lapaʻau e pale ana i ka ʻōpū liʻiliʻi o ka pēpē mai nā hoʻouka ʻana o ka ʻōnaehana pale ke kōkua i ko lākou kino e omo i nā meaʻai.

Eia nō naʻe, he pilikia ko nā pēpē me kēia maʻi me ko lākou ʻōnaehana pale. Inā loaʻa kēia maʻi i kāu pēpē, pono paha lākou i nā ʻano lapaʻau like ʻole a me ka mālama olakino lōʻihi . No ka laʻana, hiki i ke kauka o kāu pēpē ke paipai i kahi hoʻoili cell stem.

I nā manawa e like me kēia, he mea nui e hilinaʻi i kāu mau kauka a hahai i kā lākou ʻōlelo aʻo. Eia kekahi, e nīnau i kāu kauka i nā nīnau a hopohopo paha āu e loaʻa ai.

Āhea wau e hoʻokaʻaʻike aku ai i ke kauka pediatric o kaʻu pēpē?

Inā ua ʻike ʻia kāu pēpē me ka Autoimmune Enteropathy, a ʻike ʻoe i kekahi mau loli i ke alapine o ka mimi ʻana a me ka defecation - no ka laʻana, ka emi ʻana o ka nui o nā diapers pulu - pono ʻoe e hoʻokaʻaʻike koke aku i ke kauka pediatric o kāu pēpē. He mea weliweli loa ka maloʻo ʻana o ka wai no nā pēpē ʻōpio. Eia kekahi, inā piʻi ka maʻi diarrhea a i ʻole e loaʻa i kāu pēpē nā hōʻailona ʻē aʻe, e like me ke kuni, e ʻimi koke i ke kōkua lapaʻau.

He aha nā nīnau e pono iaʻu e nīnau aku i ke kauka pediatric o kaʻu pēpē?

No ka mea, he maʻi laha ʻole ka Autoimmune Enteropathy, ʻaʻole paha ʻoe i ʻike nui e pili ana i ia mea. No laila, eia kekahi mau nīnau hiki iā ʻoe ke nīnau i kāu kauka:

• Ua ʻike anei ʻoe i ke kumu i loaʻa ai kēia maʻi i kaʻu pēpē? (ʻAʻole paha mākou i ʻike i ke kumu pololei, akā he mea maikaʻi ke ʻike.)
• He aha ke ʻano o ka lāʻau lapaʻau e pono ai kaʻu pēpē?
• He aha nā hopena ʻaoʻao o kēia mau lāʻau lapaʻau? Pehea e mālama ʻia ai?
• Pehea ka lōʻihi e pono ai kaʻu pēpē i ka lāʻau lapaʻau?
• He aha kekahi mau mea e pono iaʻu e makaʻala nui ai i ka wā e mālama ai i kaʻu pēpē ma ka home?
• Hiki i kēia kūlana ke hoʻopilikia i ka ulu ʻana o ka pēpē i ka wā e hiki mai ana?

Ma waho aʻe o kēia mau nīnau, mai makaʻu e kamaʻilio me kāu kauka e pili ana i nā mea a pau ma kou manaʻo.

Pehea ka maʻamau o ka Autoimmune Enteropathy i nā pākeke?

He mea kākaʻikahi loa i nā pākeke ke loaʻa i ka "Autoimmune Enteropathy".Eia nō naʻe, he mea paʻakikī ke ʻōlelo pololei i ka nui. Ua hōʻike nā kauka ma kekahi haukapila i loko o 16 mau makahiki, he 13 wale nō kānaka i ʻike ʻia me ka Autoimmune Enteropathy. Loaʻa iā lākou āpau he 13 kekahi maʻi autoimmune ʻē aʻe.

ʻO ka mea hope loa, he leka iki i nā mākuahine a me nā mākua kāne

Inā he pēpē liʻiliʻi kāu, he mea maʻamau ke hopohopo inā i kekahi lā e palupalu ka ʻōpala o kāu pēpē ma mua o ka maʻamau, a inā ʻaʻole lākou e mimi pinepine. Mai hopohopo i nā manawa e like me kēia.

ʻO ka maʻi kahe i kekahi manawa a i ʻole ka emi iki o ka mimi ʻana i kekahi lā, ʻaʻole ia he kumu e hopohopo ai. ʻO ka mea paha, ʻo kēia mau loli liʻiliʻi i ka ʻōnaehana hoʻoheheʻe o kāu pēpē ʻaʻole ia he hōʻailona o kahi maʻi koʻikoʻi e like me ka "Autoimmune Enteropathy". Eia nō naʻe, inā ʻaʻole e hoʻomaikaʻi ka loli o ka ʻōpala a i ʻole ka mimi o kāu pēpē ma hope o kekahi mau lā, he manaʻo maikaʻi ke kamaʻilio ʻana me kāu kauka pediatric. E hāʻawi kēlā iā ʻoe i ka maluhia o ka noʻonoʻo. E hoʻomanaʻo, he mea naʻauao mau ka ʻimi ʻana i ka ʻōlelo aʻoaʻo lapaʻau.

Nā mea nui e hoʻomanaʻo (Leka Lawe-Home)

• He maʻi laha ʻole ka Autoimmune Enteropathy kahi e hoʻouka ai ka ʻōnaehana pale ponoʻī o ke kino i nā ʻōpū.
• ʻO ka hōʻailona nui ka maʻi kahe mau me ka wai, ʻoi aku hoʻi i nā keiki ʻōpio.
• Hiki i kēia ke alakaʻi i nā pilikia e like me ka komo maikaʻi ʻole o nā meaʻai, ka dehydration, a me ka pohō kaumaha.
• Pono paha ke ʻano o ka hōʻoia ʻana i nā hoʻāʻo koko, Flow Cytometry, a me ka Biopsy ʻōpū liʻiliʻi paha.
• Hoʻokomo ʻia ka lāʻau lapaʻau i ka meaʻai intravenous a me nā lāʻau lapaʻau e kaohi ana i ka ʻōnaehana pale kino ('Corticosteroids', 'Immunomodulators').
• Inā hoʻomau ka ʻike ʻana o ka ʻōpala a i ʻole ka mimi o kāu pēpē i nā loli maʻamau ʻole, e ʻike koke i kahi kauka keiki. Mai hopohopo, a e hahai i nā ʻōlelo aʻoaʻo lapaʻau kūpono.

ʻO ka enteropathy autoimmune, ka ʻeha o ka ʻōpū, ka pehu ʻana, ka maʻi kahe, nā maʻi kamaliʻi, ka ʻōnaehana pale, nā hemahema meaʻai