Ke ʻike koke nei ʻoe i nā pehu ma kou ʻili e ʻānai ana? He Bullous Pemphigoid paha kēia!

Ua loaʻa koke anei iā ʻoe kahi ʻulaʻula ma kou ʻili i ʻike ʻole ʻia ma mua, a me ka ʻūlū, i kekahi manawa he wai piha i nā pehu? Makemake paha ʻoe e ʻike e pili ana i kahi maʻi i kapa ʻia ʻo bullous pemphigoid. He maʻi ʻili kakaikahi ia, akā he mea pono ke makaʻala. E kamaʻilio kākou e pili ana i ia mea ma ke ʻano maʻalahi hiki iā ʻoe ke hoʻomaopopo.

He aha ka Bullous Pemphigoid? He aha ke ʻano o ia maʻi?

I ka ʻōlelo maʻalahi, ʻo Bullous Pemphigoid kahi maʻi ʻili kakaʻikahi e hoʻoulu ai i nā ʻulaʻula, nā ʻūlū ma ka ʻili o ka ʻili, e like me ka eczema. I kekahi manawa, hiki i kēia mau ʻūlū ke ulu a lilo i mau pehu piha i ka wai. E noʻonoʻo e like me ka nahu ʻana o ka makika, me nā pehu nui e ʻūlū nui ana.

Hiki ke ʻike ʻia kēia mau pehu ma kahi liʻiliʻi o ke kino, a i ʻole hiki iā lākou ke pālahalaha ma ke kino holoʻokoʻa. ʻIke pinepine ʻia lākou ma nā wahi e pelu ai ka ʻili. No ka laʻana, ma lalo o nā armpits (axilla), ma ka ʻūhā, a i ʻole ma ka ʻōpū. Hiki i kekahi poʻe ke loaʻa i kēia mau pehu ma nā wahi e like me loko o ka waha, ke alelo, ka ʻāʻī, ka esophagus, a i ʻole nā ​​maka.

I kēia manawa, ke noʻonoʻo nei paha ʻoe, "No ke aha lā kēia e hana nei?" He maʻi autoimmune ka bullous pemphigoid. ʻO ke ʻano kēia, ʻo ka ʻōnaehana pale o ko mākou kino, ka mea i manaʻo ʻia e pale iā mākou, e hoʻouka hewa ana i nā ʻiʻo ma lalo o ko mākou ʻili ponoʻī. Ua like ia me ko mākou pūʻali koa ponoʻī e hoʻouka ana i ko mākou ʻāina ponoʻī.

ʻO wai ka mea e loaʻa pinepine ai kēia? Pehea ka maʻamau?

ʻO ka bullous pemphigoid kahi maʻi i ʻike nui ʻia i ka poʻe ma luna o 60 mau makahiki. Eia nō naʻe, hiki ke loaʻa i ka poʻe ʻōpio. ʻOiai he mea maʻamau ia ma nā ʻāina Komohana, ʻaʻole ia he mea maʻamau ma nā ʻāina ʻĀsia, ʻo ia hoʻi, ma ko mākou ʻāpana o ka honua.

Hiki i kēia ke hana i nā kāne a me nā wahine, me ka nānā ʻole i ke kāne.

Aia kekahi pilina me nā maʻi neurological?

ʻAe, ua ʻike ʻia ka poʻe me kekahi mau maʻi neurological e ʻoi aku ka nui o ka loaʻa ʻana o ka bullous pemphigoid. ʻO kēia mau mea:

• Dementia
• ka maʻi o Parkinson
• Hahau
• ʻEpilepsy
• ʻO ka sclerosis lehulehu

ʻAʻole kēia manaʻo e loaʻa i nā kānaka a pau me kēia mau kūlana ka bullous pemphigoid. Eia nō naʻe, wahi a nā kauka aia paha kahi pilina.

He mea maʻamau loa ia a ua hōʻike ʻia ka nui o ka maʻi ma waena o 2.4 a me 23 i kēlā me kēia miliona i ka heluna kanaka. Eia nō naʻe, ma waena o ka poʻe he 80 a ʻoi paha ka makahiki, aia ka nui ma waena o 190 a me 312 i kēlā me kēia miliona . ʻO ke ʻano kēia, ʻoi aku ka nui o ka loaʻa ʻana i ia mea i kou wā ʻelemakule.

He mea weliweli anei ka bullous pemphigoid? Hiki iā ia ke hoʻoweliweli i ke ola?

He mea weliweli iki paha kēia iā ʻoe. Akā eia ka ʻoiaʻiʻo: kāuHiki i ka bullous pemphigoid ke hoʻoweliweli i ke ola inā ʻaʻole maikaʻi kou olakino a inā ʻaʻole ʻoe e mālama pono iā ia, ʻoiai inā haki kou mau pehu a lilo i maʻi. ʻO ia ke kumu e ʻōlelo aku ai mākou e ʻike koke i ke kauka inā ʻike ʻoe i kekahi mea ʻē.

He aha nā hōʻailona? Pehea ʻoe e ʻike ai?

ʻO nā hōʻailona nui o ka bullous pemphigoid ka ʻike ʻia ʻana o nā ʻeha ʻulaʻula he nui e like me ka eczema (welts) a i ʻole nā ​​​​​​pehu i piha i ka wai (bullae) . ʻIke pinepine ʻia kēia mau mea ma:

• I loko o nā lima
• Ma nā wāwae
• Ma ka ʻāpana ʻōpū
• Ma ka ʻāpana ʻūhā
• I loko o ka waha

Hoʻokumu pinepine ʻia kēia mau pehu ma nā ʻāpana o ka ʻili, ma nā ʻāpana o ka ʻili. ʻO ka hapa nui o ka manawa, ʻaʻole lākou he ʻeha , akā inā haki lākou, hiki iā lākou ke lilo i ʻeha a ʻeha, a hiki ke lilo i mau ʻōpū.

Hiki ke moakāka a koko iki paha ke wai i loko o ka pehu. Hiki ke maʻamau ka ʻili a puni ka pehu a i ʻole ua loli ke kala (ʻulaʻula, poni, ʻeleʻele, a i ʻole he ʻeleʻele iki ke kala ma mua o kou ʻili).

ʻO ka nūhou maikaʻi, ʻaʻole paha e hoʻoulu kēia ʻulaʻula a me nā pehu i ka ʻeha.

No ke aha e ulu ai ka bullous pemphigoid? He aha nā kumu?

E like me kā mākou i ʻōlelo ai ma mua, ʻo ka bullous pemphigoid kahi maʻi i hoʻokumu ʻia e kahi hana hewa i loko o ka ʻōnaehana pale. Eia nō naʻe, ʻaʻole i loaʻa i nā kauka a me nā mea noiʻi kahi kumu paʻa no ke kumu e pane ai kā mākou ʻōnaehana pale i kēia ʻano.

Hiki i kekahi mau lāʻau lapaʻau ke hoʻoulu a hoʻonui paha i kēia kūlana. No ka laʻana, ʻo ka lāʻau maʻi diabetes ʻo alogliptin. Hiki i ke kukui Ultraviolet (UV) a me ka radiation ionizing mai ka lā ke hoʻoulu a hoʻonui paha i kēia kūlana.

Hiki i kekahi mau meaʻai a me nā mea inu ke hoʻonui i kēia?

He nīnau kēia a ka poʻe he nui e nīnau ai. ʻO ka ʻoiaʻiʻo, ʻaʻohe hōʻike ʻepekema maopopo a nā kauka e hōʻoia ai he pilina ma waena o ka meaʻai a me ka bullous pemphigoid. Wahi a kekahi poʻe ua hoʻomaikaʻi ʻia ko lākou mau hōʻailona i ka wā i hōʻoki ai lākou i kekahi mau meaʻai mai kā lākou ʻai. Eia naʻe, ʻaʻohe hōʻike ikaika e hōʻoia i kēia.

Inā loaʻa iā ʻoe ka bullous pemphigoid, e kamaʻilio me kāu kauka e pili ana i ka hiki ke kōkua i ka hoʻopau ʻana i kekahi mau meaʻai a me nā mea inu. Hiki iā ia ke haʻi iā ʻoe e mālama i kahi puke moʻolelo meaʻai . A laila hiki iā ʻoe ke ʻike inā hoʻonui kekahi mau meaʻai i kāu mau hōʻailona. Inā ʻike ʻoe e hana lākou, hiki iā ʻoe ke hoʻopau mālie i kēlā mau meaʻai a ʻike inā kōkua kēlā.

He maʻi lele anei kēia?

ʻAʻole, ʻaʻole laha ka bullous pemphigoid. ʻAʻole hiki ke laha i kekahi kanaka ma o ka pili ʻana o ka ʻili a i ka ʻili. No laila, mai hopohopo no ia mea.

Pehea e ʻike pololei ai ke kauka i kēia?

Ke hele ʻoe e ʻike i ke kauka, e nānā mua ʻo ia i nā wahi i hoʻopilikia ʻia o kou ʻili. A laila e nīnau lākou iā ʻoe i kekahi mau nīnau. Eia kekahi laʻana:

• "I ka manawa hea i hoʻomaka ai kēia mau hōʻailona?"
• "He ʻōpala a koko paha kou i loko o kou mau pehu?"
• "Ua loaʻa iā ʻoe ke kuni?"
• "Ua hoʻomaka anei ʻoe i kekahi mau lāʻau lapaʻau hou?"

Ma hope o ka nīnau ʻana i nā nīnau e like me kēia, hiki mai ke kauka i kahi hopena maʻamau e pili ana i nā pane āu e hāʻawi ai.

He aha nā hoʻokolohua e hana ʻia nei no kēia?

No ka hōʻoia ʻana i ka hōʻailona, ​​​​hiki i kāu kauka ke ʻōlelo iā ʻoe e hana i kēia mau hoʻokolohua:

• Hoʻāʻo koko: Hoʻohana ʻia kahi nila liʻiliʻi e lawe i kahi hāpana koko mai kahi aʻa koko i kou lima a hoʻouna aku i kahi hale hana no ka hoʻāʻo ʻana.
• ʻO ka biopsy ʻili: Pili kēia i ka lawe ʻana i kahi ʻāpana liʻiliʻi o kou ʻili a hoʻouna aku i kahi keʻena hoʻokolohua no ka hoʻāʻo ʻana. ʻO kēia wale nō ke ala e hōʻoia ai i ke kumu pololei o ke kūlana.

He aha nā lāʻau lapaʻau maikaʻi loa?

I nā hihia ʻoluʻolu o ka bullous pemphigoid, ʻo ka lāʻau maikaʻi loa ka hoʻopili ʻana i nā kirīmi corticosteroid a i ʻole nā ​​​​​​mea ʻaila pololei i nā wahi i hoʻopilikia ʻia.

Eia nō naʻe, i nā hihia kaulike a koʻikoʻi paha , hiki i kāu kauka ke hāʻawi iā ʻoe i nā pila corticosteroid waha, e like me ka prednisone , me ka hoʻohui ʻana i ka kirīmi corticosteroid. Hiki iā lākou ke hāʻawi iā ʻoe i nā mea hana immunomodulatory ʻē aʻe e hiki ke kōkua i ka hōʻemi ʻana i ka hoʻohana ʻana i nā steroids. No ka laʻana, nā lāʻau lapaʻau e like me dapsone, mycophenolate mofetil, azathioprine, methotrexate, a i ʻole chlorambucil.

Inā ʻaʻole hiki iā ʻoe ke lawe i nā corticosteroids a i ʻole nā ​​​​lāʻau lapaʻau ʻē aʻe e hoʻopau ana i ka pale ʻana, hiki i kāu kauka ke kuhikuhi i nā papa i kapa ʻia ʻo tetracycline a i ʻole doxycycline .

I kekahi manawa, inā ʻaʻole hiki i kēia mau lāʻau lapaʻau ke kāohi i ka maʻi (nā hihia paʻakikī), hiki i ke kauka ke ʻōlelo aku i nā lāʻau lapaʻau e like me Rituximab a i ʻole IVIG infusion (kahi wai i hāʻawi ʻia i loko o kahi aʻa) .

ʻO ka mea nui loa, mai hoʻohana i kekahi lāʻau lapaʻau me ka ʻole o ke kūkākūkā ʻana me ke kauka. ʻO ia ka mea nāna e hoʻoholo i ka lāʻau kūpono loa no kou kūlana.

Aia kekahi mau lāʻau lapaʻau e hiki ke hana ma ka home?

ʻAʻohe lāʻau lapaʻau home kikoʻī no ka bullous pemphigoid. Eia nō naʻe, aia kekahi mau mea hiki iā ʻoe ke hana e kōkua i ka hōʻemi ʻana i kāu mau hōʻailona a hāʻawi i kahi hōʻoluʻolu.

No nā pehu ma ka ʻili:

• E ʻaʻahu i nā lole palupalu a ākea i hana ʻia mai nā olonā kūlohelohe (e like me ka pulupulu).
• Mai noho lōʻihi i ka lā. Inā ʻoe e hele i waho, e kau i ka pale lā.
• E mālama i kou mau ʻeha a i ʻole nā ​​ʻeha ma ka holoi ʻana iā lākou me ke kopa antibacterial a me ka wai. Ma hope o kāu hana ʻana i kēia, e hoʻopili i kahi kirīmi antiseptic i nā ʻeha a uhi iā lākou me kahi kāʻei nonadhesive. Hiki i kēia ke kōkua i ka pale ʻana i ka maʻi.
• Inā he bullous pemphigoid kou ma kou mau wāwae, e pale i ke kū ʻana a i ʻole ka hele ʻana no ka manawa lōʻihi.
• E hoʻopili i ka moisturizer, kirīmi, ʻaila niu, a i ʻole ka pata shea e mālama i kou ʻili i ka maʻū.

Inā he mau ʻeha waha kou:

Inā he mau ʻeha pemphigoid bullous i loko o kou waha, hiki i kēia mau ʻōlelo aʻoaʻo ke kōkua iā ʻoe e pale i nā pilikia meaʻai a hoʻemi i kekahi o kāu mau hōʻailona:

• E ʻai i nā meaʻai palaka, e like me nā sopa, nā meaʻai i kuʻi ʻia, nā puddings, a me ka applesauce.
• I ka ʻai ʻana i nā meaʻai wela, e kali a hōʻalili ma mua o ka ʻai ʻana.
• E pale i ka ʻai ʻana i nā meaʻai ʻoi a palupalu (e like me nā ʻuala palai, nā meaʻai liʻiliʻi, nā ʻuala palai, nā ʻuala palai, nā huaʻai maka, a me nā mea ʻai māmā).
• Mai ʻai i nā meaʻai ʻakika loa (e.g., chili, salsa, limes, tōmato).
• E pale i ka inu ʻana i ka waiʻona.

ʻEhia ka manawa e ʻoi aku ai koʻu maikaʻi ke hoʻomaka wau i ka lāʻau lapaʻau?

Pono ʻoe e hoʻomaka e ʻoluʻolu i loko o kekahi mau lā o ka hoʻomaka ʻana o ka lāʻau lapaʻau. Eia nō naʻe, hiki ke ʻokoʻa kēia mai kēlā kanaka a kēia kanaka.

Aia kekahi ala e pale aku ai i kēia mai ka hana ʻana?

ʻO ka mea pōʻino, ʻaʻole ʻike nā kauka a me nā mea noiʻi i kahi ala e pale aku ai i ka ulu ʻana o ka bullous pemphigoid.

He aha ka mea e hiki mai ana inā loaʻa iaʻu kēia maʻi? He aha ka mea e hiki mai ana i ka wā e hiki mai ana?

ʻO ka maʻamau, e hoʻōla hou ka bullous pemphigoid iā ia iho i loko o ʻelima mau makahiki. Pane maikaʻi ia i ka lāʻau lapaʻau. Eia nō naʻe, i kekahi manawa hiki i ka maʻi ke hoʻāla a i kekahi manawa hiki ke hoʻomaha. I ka wā o ka hoʻomaha ʻana, hiki paha iā ʻoe ke hoʻōki i ka lāʻau lapaʻau (me ka ʻōlelo aʻo a kāu kauka).

Inā pahū a loaʻa ka maʻi i kou mau pehu, aia ʻoe i ka pilikia o ka loaʻa ʻana o kahi maʻi weliweli i ke ola i kapa ʻia ʻo sepsis . No laila, he mea nui loa ka mālama ʻana i kou mau pehu.

He aha nā manawa kūpono loa e ʻike ai i ke kauka?

Inā loaʻa iā ʻoe nā pehu i wehewehe ʻole ʻia , e ʻike koke i ke kauka. E like me ka mea i ʻōlelo ʻia ma mua, ʻoi aku ka maikaʻi o ka loaʻa ʻana o kahi hōʻailona a me ka lāʻau lapaʻau i ka wā hikiwawe.

Nā nīnau koʻikoʻi e nīnau aku i kāu kauka

Ke hele ʻoe e ʻike i ke kauka, he mea kōkua paha ka nīnau ʻana i kēia mau nīnau:

• "Pehea lā ʻoe e ʻōlelo ai he bullous pemphigoid koʻu?"
• "Inā ʻaʻohe oʻu bullous pemphigoid, he aha nā maʻi ʻili ʻē aʻe e loaʻa iaʻu?"
• "Pehea e hiki ai iaʻu ke mālama i kaʻu mau hōʻailona?"
• "He aha nā lāʻau lapaʻau āu e ʻōlelo mai nei noʻu?"
• "He mau hopena ʻaoʻao anei kēlā mau lāʻau lapaʻau?"
• "He aha hou aʻe kaʻu e hana ai e hoʻomaikaʻi ai i koʻu mau hōʻailona?"
• "Pehea ka lōʻihi o koʻu loaʻa ʻana i kēia maʻi bullous pemphigoid?"
• "Pono anei au e ʻike i ke kauka ʻili a i ʻole kekahi loea ʻē aʻe?"

He aha ka ʻokoʻa ma waena o ka Pemphigus Vulgaris a me ka Bullous Pemphigoid?

He mau maʻi ʻelua e hoʻoulu ai i nā pehu ma ka ʻili ma muli o ka hana hewa ʻana o ka ʻōnaehana pale. Loaʻa i ka Pemphigus vulgaris nā hōʻailona like me ka bullous pemphigoid. Eia nō naʻe, hoʻomaka pinepine ka pemphigus vulgaris i loko o nā membrane mucous i loko o ka waha. He kakaikahi ka poʻe e hoʻomohala i nā pehu ma ka ʻili. Eia kekahi, ʻoi aku ka palupalu o nā pehu ma ka pemphigus vulgaris ma mua o nā mea ma ka bullous pemphigoid.

Ke ʻike ʻia nā pehu pemphigus vulgaris, he mau ʻino pinepine ia, ʻaʻole nā ​​pehu i haki ʻole e like me ka bullous pemphigoid. Inā loaʻa iā ʻoe ka pemphigus vulgaris, e hoʻokaʻawale maʻalahi nā papa luna o kou ʻili mai nā papa lalo me kahi kaomi iki a i ʻole ka hamo ʻana (ua kapa ʻia kēia ʻo ka hōʻailona Nikolsky) .

ʻOiai ʻo ka hapa nui o nā kānaka me ka bullous pemphigoid he mau hopena ʻili, ʻo ka hapakolu wale nō (33%) o lākou e hoʻomohala i nā pehu ma ka waha .

ʻO ka mea hope loa, leka lawe i ka home

ʻAe, ua kamaʻilio nui mākou e pili ana i ka bullous pemphigoid. Eia kekahi o nā mea nui e hoʻomanaʻo:

• He maʻi laha ʻole ka bullous pemphigoid i loko o ka ʻōnaehana pale e hoʻoulu ai i nā pehu a i ʻole nā ​​​​ʻeha ma ka ʻili.
• ʻAʻole kēia he mea laha.
• ʻIke pinepine ʻia ia i nā poʻe ʻelemakule, akā hiki nō hoʻi ke hana i nā poʻe ʻōpio.
• Inā pehu a ʻānai paha kou ʻili me ke kumu ʻole, e ʻike koke i ke kauka.
• Me ka mālama pono ʻana, hiki ke kaohi maikaʻi ʻia kēia, a i ka hala ʻana o ka manawa, aia kahi hiki ke hoʻōla piha ʻia.
• Hiki i nā pehu ke lilo i mea weliweli inā loaʻa iā lākou ka maʻi, no laila he mea nui loa ia e mālama iā lākou i ka maʻemaʻe.

Inā loaʻa iā ʻoe kēia mau hōʻailona, ​​mai hopohopo. Ma ka hahai ʻana i nā ʻōlelo aʻoaʻo lapaʻau, hiki iā ʻoe ke ho'ōla koke.

ʻO Bullous Pemphigoid, Nā maʻi ʻili, Nā pehu wai, Nā pehu ʻāʻī, Nā maʻi Autoimmune, Nā maʻi ʻili, Maʻi Autoimmune, Nā pehu ʻili