Ke hoʻopilikia nei kēia mumū kakaikahi i kou puʻuwai? E aʻo kākou e pili ana i ka Cardiac Sarcoidosis!

Ke luhi wale nei ʻoe i kekahi manawa? A i ʻole he ʻeha iki kou umauma a paʻakikī paha ka hanu ʻana? Manaʻo paha ʻoe he mau mea maʻamau kēia. Eia nō naʻe, he mau maʻi kakaikahi loa kēia e hoʻopilikia ai i ka puʻuwai. ʻO Cardiac Sarcoidosis kekahi maʻi like, he mea paʻakikī iki ia, akā inā ʻike pono ʻia ʻoe, hiki ke mālama ʻia. I kēia lā, e kamaʻilio mākou e pili ana i kēia ma ke ʻano maʻalahi e hiki ai iā ʻoe ke hoʻomaopopo.

He aha ka Cardiac Sarcoidosis?

I ka ʻōlelo maʻalahi, ʻo Sarcoidosis kahi maʻi mumū laha ʻole e kū mai ana i loko o ko mākou kino. I loko o kēia, hōʻiliʻili nā hunaola mumū liʻiliʻi a hana i nā puʻupuʻu (granulomas) ma nā ʻano kino like ʻole o ke kino, ʻoi aku hoʻi ma nā wahi e like me nā māmā, nā lymph node, ka ʻili, a me nā maka. Hiki i kēia mau puʻupuʻu ke hoʻopilikia i ka hana maʻamau o kēlā mau ʻano.

I kēia manawa, inā hoʻopilikia kēia maʻi sarcoidosis i ka puʻuwai, ʻo ia ka mea a mākou e kapa nei he cardiac sarcoidosis . He mea kakaikahi loa kēia i waena o nā poʻe maʻi sarcoidosis. Eia nō naʻe, i ka wā e hoʻopilikia ʻia ai ka puʻuwai ma kēia ʻano, hiki ke hana ʻia nā ʻōpala i loko o ka ʻiʻo puʻuwai a ma nā ala e hele ai nā hōʻailona uila i loko o ka puʻuwai. E noʻonoʻo iā ia e like me kahi ʻōpala ma ka ʻili ma hope o kahi ʻeha. Hiki i kēia mau ʻōpala ke hana i nā ʻano puʻuwai maʻamau ʻole a me nā pilikia me ka puʻuwai.

Pehea ka maʻamau o kēia ʻano?

ʻAʻole maʻamau ka maʻi sarcoidosis cardiac. Ma ka honua holoʻokoʻa, ʻike pinepine nā kauka i ka 2% a 5% wale nō o ka poʻe me ka sarcoidosis ma nā wahi ʻē aʻe o ke kino he maʻi ma ka puʻuwai. Eia nō naʻe, hōʻike kekahi mau noiʻi ma nā ʻāina e like me ʻAmelika Hui Pū ʻIa, 20% a 30% o ka poʻe me ka sarcoidosis paha he maʻi ma ka puʻuwai, akā ʻaʻole paha e ʻike ʻia.

ʻOi aku ka maʻamau o kēia ʻano ma nā ʻāina e like me Iapana, kahi i loaʻa ai i ka hapalua o ka poʻe me ka sarcoidosis ka maʻi i loko o ko lākou puʻuwai. Eia nō naʻe, he mea kakaikahi ka sarcoidosis cardiac i hoʻohālikelike ʻia me ka sarcoidosis e hoʻopilikia ana i nā ʻōpū ʻē aʻe.

ʻO kekahi mea nui e hoʻomaopopo ai, ʻo ka hapakolu o ka poʻe me ka sarcoidosis cardiac ʻaʻole hōʻike i nā hōʻailona o ka sarcoidosis ma nā wahi ʻē aʻe o ke kino. ʻO ke ʻano kēia , ʻo kou puʻuwai paha ke kino mua i hoʻopilikia ʻia e ka maʻi.

He aha nā hōʻailona o kēia maʻi?

Hiki ke ʻokoʻa nā hōʻailona o ka Cardiac Sarcoidosis mai kēlā kanaka a kēia kanaka. ʻAʻole paha i loaʻa i kekahi poʻe kekahi mau hōʻailona. Eia nō naʻe, aia kekahi mau hōʻailona maʻamau:

• ʻEha umauma: Hiki ke manaʻo ʻia e like me ka ʻūmiʻi ʻana a i ʻole ka ʻūmiʻi ʻana.
• Pōkole o ka hanu:E manaʻo paha ʻoe ua pōkole ka hanu, inā paha he luhi iki ʻoe a i ʻole e hoʻomaha wale ana.
• Nāwaliwali a poniuniu paha: Hiki iā ʻoe ke nalowale koke ka ʻike a hāʻule.
• Luhi: Manaʻo mau i ka luhi, me ka nānā ʻole i nā mea āu e hana ai.
• ʻŪhū: Aia paha he ʻūhū maloʻo mau.
• Ka pehu ʻana i kou mau wāwae: Hiki i nā wahi e like me ka kuʻekuʻe wāwae ke pehu.
• Nā puʻuwai puʻuwai kūpono ʻole / Nā palpitations o ka puʻuwai: Hiki ke piʻi koke, emi, a manaʻo paha e like me ka hala ʻana o kahi kuʻi ʻana o ka puʻuwai.

Inā loaʻa iā ʻoe kekahi a ʻoi aku paha o kēia mau hōʻailona, ​​​​mai hoʻowahāwahā iā lākou. ʻOi aku ka maikaʻi o ka ʻimi ʻana i ke aʻo lapaʻau.

No ke aha e kū mai ai ka Cardiac Sarcoidosis?

ʻO kaʻoiaʻiʻo, ʻaʻole i loaʻa i nā kauka kahi kumu kikoʻī no kēia maʻi. Eia nō naʻe, manaʻoʻiʻo nā kānaka noiʻi he kuleana ko kekahi poʻe e pili ana i ke ʻano hoʻoilina a me nā mea pili i ke kaiapuni. ʻO ia hoʻi, hiki i ke kino o kekahi poʻe ke pane i kahi mea i loko o ke kaiapuni (no ka laʻana, he bacteria, he virus, a he lepo paha) e hoʻoulu ai i kēia maʻi mumū. Eia naʻe, aia nō kēia i loko o ke kahua noiʻi.

Pehea e ʻike ʻia ai kēia maʻi?

Inā kānalua ʻoe he cardiac sarcoidosis kou, e hana mua kāu kauka i kahi hoʻokolokolo kino. A laila e nīnau lākou e pili ana i kou mōʻaukala olakino . ʻO ia hoʻi nā mea e like me kou mau maʻi ma mua a inā paha ua loaʻa i kekahi o kou ʻohana nā kūlana like.

Eia kekahi, e kauoha ʻia nā hoʻokolohua like ʻole e nānā i nā puʻuwai puʻuwai kūpono ʻole. E nānā ke kauka no nā hōʻailona o ka sarcoidosis ma nā wahi ʻē aʻe o kou kino, a no nā hōʻike o nā hōʻailona like i loko o kou puʻuwai.

He aha nā hoʻokolohua diagnostics?

Aia kekahi mau hoʻokolohua e hōʻoia pololei i kēia maʻi:

• Electrocardiogram (EKG/ECG): Hoʻopaʻa kēia i ka hana uila o kou puʻuwai ma ke ʻano he ʻano. Hiki iā ia ke ʻike i nā ʻano ʻē i loko o kou puʻuwai.
• Echocardiogram: Ua like kēia me ke scan o ka puʻuwai. Hoʻohana ia i nā nalu kani e nānā i ke ʻano a me ka nui o ka puʻuwai, pehea e hana ai nā keʻena a me nā valve o ka puʻuwai, a me nā mea hou aku. I kekahi manawa hana ʻia kahi echo transthoracic.
• Nānā Holter: He mea liʻiliʻi kēia āu e ʻaʻahu ai no 24 a 48 mau hola. Kōkua ia i ka hoʻopaʻa mau ʻana i ka hana o kou puʻuwai ʻoiai ʻoe e hana ana i kāu mau hana o kēlā me kēia lā.
• ʻO ka Tomography Hoʻokuʻu Positron (PET scan):He scan kūikawā kēia. He mea pono loa ia i ka ʻike ʻana i nā wahi o ka mumū a me nā ʻōpala ma ka puʻuwai.
• MRI o ka Puʻuwai (Cardiac Magnetic Resonance Imaging): Hoʻohana kēia i nā kahua magnetic a me nā nalu lekiō e hana i nā kiʻi kikoʻī o ka puʻuwai. Hiki i kēia ke kōkua i ka ʻike maopopo ʻana i ka pōʻino a me ka ʻeha i ka ʻiʻo o ka puʻuwai.

ʻIke pinepine ʻia ka Sarcoidosis ma nā wahi ʻē aʻe o ke kino ma ka lawe ʻana i kahi biopsy (kahi laʻana liʻiliʻi o ka ʻiʻo a nānā iā ia ma lalo o kahi microscope). Eia naʻe, ʻaʻole kēia i maʻamau i ka puʻuwai, no ka mea, he paʻakikī ke kiʻi i kahi laʻana mai kahi kikoʻī o ka puʻuwai kahi o ka pilikia.

Kōkua pū kēia mau hoʻāʻo kiʻi i nā kauka e hoʻoholo i nā pae o ka sarcoidosis cardiac. Hiki iā ia ke ʻano mai ka ʻoluʻolu a i ka koʻikoʻi. Hiki iā ia ke holomua ma o nā pae mua, nā pae holomua, a me nā pae hana, e alakaʻi ana i ka hōʻino ʻana o ka myocardial a me ka fibrosis.

He aha nā lāʻau lapaʻau?

ʻO ka nūhou maikaʻi, aia nā lāʻau lapaʻau no ka sarcoidosis cardiac. E koho kāu kauka i ka lāʻau lapaʻau kūpono loa no kou kūlana. Eia kekahi o nā lāʻau lapaʻau i hoʻohana pinepine ʻia:

• Nā lāʻau Corticosteroid: Hana kēia ma ka hōʻemi ʻana i ka mumū i loko o ke kino. ʻO Prednisolone kahi lāʻau i kuhikuhi pinepine ʻia i kēia hui.
• Nā immunosuppressants ʻē aʻe: I kekahi manawa, inā ʻaʻole lawa nā corticosteroids wale nō, a inā koʻikoʻi loa ko lākou mau hopena ʻaoʻao, hiki ke hāʻawi ʻia nā lāʻau lapaʻau ʻē aʻe e kāohi i ka ʻōnaehana pale o ke kino mai ka lilo ʻana i overactive.
• Nā lāʻau anti-arrhythmic: Inā ʻaʻole kūpono ka puʻuwai, aia nā lāʻau lapaʻau kūikawā e kaohi iā ia.
• Pacemaker: Inā paʻi wikiwiki ka puʻuwai, ua hoʻokomo ʻia kēia mea liʻiliʻi i loko o ka puʻuwai e mālama iā ia ma kahi wikiwiki maʻamau.
• ʻO ka Implantable Cardioverter Defibrillator (ICD): Hoʻokomo ʻia kēia mea hana ke loaʻa kahi pilikia o nā arrhythmias weliweli e hoʻoweliweli ana i ke ola. I kēlā mau manawa, hāʻawi ia i kahi haʻalulu uila liʻiliʻi i ka puʻuwai e hoʻihoʻi i ka rhythm maʻamau.
• ʻO ka hoʻopau ʻana o ka catheter: He lāʻau lapaʻau kēia no nā puʻuwai puʻuwai kūpono ʻole. Loaʻa a luku ʻia nā wahi o ka puʻuwai e hoʻoulu ai i nā hōʻailona uila kūpono ʻole me ka hoʻohana ʻana i kahi catheter.

He mea kākaʻikahi loa, inā lilo ka maʻi i mea koʻikoʻi loa a hiki i ka hāʻule ʻana o ka puʻuwai , pono paha kahi hoʻoili puʻuwai .

He aha nā lāʻau lapaʻau a me nā lāʻau lapaʻau i hoʻohana pinepine ʻia?

Hoʻomaka pinepine nā kauka me kahi mahele nui o ka corticosteroid i kapa ʻia ʻo prednisone (ʻo nā inoa inoa e komo pū ana me Sterapred® a i ʻole Rayos®). Lawe ʻia kēia no kekahi mau mahina. A laila hoʻemi mālie ʻia ka mahele. Inā ʻike ʻia a mālama ʻia ka maʻi i ka wā mua, hiki i kēia mau lāʻau lapaʻau ke kāohi nui i nā hōʻailona.

Aia kekahi mau hopena ʻaoʻao o ka lāʻau lapaʻau?

Hiki i nā lāʻau Corticosteroid e like me Prednisone ke hana i kekahi mau hopena ʻaoʻao ke hoʻohana ʻia no ka manawa lōʻihi. ʻO ia ke kumu e nānā mau ai kāu kauka iā ʻoe. ʻO nā hopena ʻaoʻao maʻamau:

• Osteoporosis: Ka nāwaliwali o nā iwi.
• Nā maʻi: Hiki ke piʻi aʻe ka pilikia o ka loaʻa ʻana o nā maʻi i ka wā e emi ai ka palekana o ke kino.
• Ke koko kiʻekiʻe.
• Ke kō koko kiʻekiʻe.
• Nā loli o ka naʻau.
• ʻAʻole hiki ke hiamoe.

ʻOiai ua holomua mua ka mālama ʻana me ka catheter ablation, hiki i kekahi poʻe, ʻoiai ka poʻe me ka ventricular tachycardia (kahi puʻuwai wikiwiki e hoʻomaka ana ma nā keʻena haʻahaʻa o ka puʻuwai), ke loaʻa hou ʻana a hiki i ka 86% o nā hihia.

ʻO ka pilikia o ka sarcoidosis cardiac e hoʻi hou ana ma hope o ka hoʻoili ʻana o ka puʻuwai he emi iho ia ma mua o 10%.

He maʻi koʻikoʻi anei ka Cardiac Sarcoidosis?

E loli kēia ma muli o kou kūlana. Loaʻa nā hopena maikaʻi loa inā ʻike mua ʻia ka maʻi a hoʻomaka koke ʻia ka mālama ʻana. Inā hoʻopaneʻe ʻia ka mālama ʻana, hiki i ke kūlana ke lilo i mea koʻikoʻi.

Inā loaʻa iā ʻoe nā kūlana e like me ke koko kiʻekiʻe o ka pulmonary ( ka hoʻonui ʻia o ke kaomi i loko o nā aʻa e lawe ana i ke koko i nā māmā) a i ʻole kahi aneurysm ventricular (ka nāwaliwali o ka paia o kekahi o nā keʻena haʻahaʻa o ka puʻuwai e pehu ana e like me ka pōpō), ʻaʻole paha e maikaʻi ka prognosis.

Pehea ka lōʻihi e hiki ai iā ʻoe ke ola me kēia maʻi?

Inā hoʻomaka mua ʻia ka lāʻau lapaʻau, nui ka poʻe e ola maikaʻi.

Ua ʻike ʻia nā noiʻi ma waena o 83% a me 93% o ka poʻe e noho ana me ka sarcoidosis cardiac e ola mau ana ma hope o 10 mau makahiki.

ʻO ka nui o ke ola ma hope o ka hoʻoili puʻuwai he 80% a ʻoi aku paha i hoʻokahi a me ʻelima mau makahiki.

E hoʻomanaʻo, ʻoiai ke hōʻike nei kēia mau helu helu i nā kūlana maʻamau, hiki ke ʻokoʻa kou kūlana pilikino. No laila e kamaʻilio me kāu kauka e loaʻa ai kahi ʻike maopopo o kou kūlana.

Hiki i ka Cardiac Sarcoidosis ke make?

ʻAe, hiki i ka sarcoidosis cardiac ke make no kekahi poʻe. Kiʻekiʻe ka pilikia o ka make, ʻoiai inā ʻaʻole e hoʻomaʻamaʻa pono ka ventricle hema o kou puʻuwai i ke koko.

ʻO ka make koke ʻana o ka puʻuwai ka mea pinepine i hoʻokumu ʻia e nā arrhythmias ventricular (nā puʻuwai kūpono ʻole i loko o nā keʻena haʻahaʻa o ka puʻuwai). Inā ʻoe i ka pilikia, hiki i kāu kauka ke ʻōlelo aku e hoʻokomo ʻia kahi mea ICD.

Pehea lā wau e mālama ai iaʻu iho?

No ka mea hiki i kēia kūlana ke lilo i mea ʻino i loko o kahi manawa pōkole, he mea nui e lawe i ka lāʻau lapaʻau e like me ke kuhikuhi ʻana a kāu kauka. Pono paha ʻoe e lawe i kahi lāʻau lapaʻau e like me Prednisone a hiki i hoʻokahi makahiki. Inā loaʻa iā ʻoe kekahi mau hopena ʻaoʻao mai ka lāʻau lapaʻau, e haʻi i kāu kauka. Akā, mai ho'ōki i ka lawe ʻana i ka lāʻau lapaʻau me ka ʻole o ka ʻōlelo aʻoaʻo lapaʻau.

Āhea wau e ʻike ai i ke kauka?

Pono ʻoe e hana hou i nā hoʻokolohua kiʻi ma kahi o hoʻokahi mahina a ʻeono paha mahina ma hope o kou hoʻomaka ʻana e lawe i nā steroids (e.g., prednisone). Kōkua kēia i kāu kauka e hoʻoholo i ka maikaʻi o ka hana ʻana o ka lāʻau lapaʻau a me ka nui o ka lāʻau e pono ai e hana i ka wā e hiki mai ana.

ʻOiai ma hope o ka hoʻōki ʻia ʻana o nā steroids a i ʻole ka hoʻemi ʻia ʻana o ka nui, pono ʻoe e hoʻomau i nā nānā ʻana me kāu kauka no ʻekolu mau makahiki ma ka liʻiliʻi. ʻO kēia no ka mea hiki ke hoʻi hou mai ka sarcoidosis cardiac. Ma kahi o 40% o ka poʻe e loaʻa hou mai ka maʻi ma kēia ʻano.

Āhea wau e hele ai i ka Emergency Treatment Unit (ETU) ?

Inā ʻike koke ʻoe i kekahi o kēia mau hōʻailona , ​​e hele koke i ka lumi pilikia o ka haukapila kokoke loa a kāhea aku paha i ka 1990:

• ʻEha umauma me ka paʻakikī o ka hanu ʻana
• Nā palpitations hoʻomau
• Pōʻino a/a i ʻole ka nawaliwali

He mau hōʻailona paha kēia o kahi maʻi puʻuwai weliweli.

He aha nā nīnau e pono iaʻu e nīnau aku i ke kauka?

Mai poina e nīnau i kēia mau nīnau ke ʻike ʻoe i ke kauka:

• Hiki iaʻu ke kāohi i kēia kūlana me ka lāʻau lapaʻau wale nō?
• Pehea koʻu manaʻo, ʻoiai ke kūlana o kēia manawa?
• Pehea ka maikaʻi o ka hana ʻana o koʻu ventricle hema?
• ʻEhia ka lōʻihi e pono ai iaʻu e lawe i ka lāʻau lapaʻau?
• He aha nā hoʻololi o ke ʻano o ka nohona e hiki iaʻu ke hana?

ʻO ka mea hope loa, nā mea e hoʻomanaʻo ai (Leka Lawe-Home)

He huaʻōlelo weliweli iki ka Cardiac Sarcoidosis, akā he mea nui loa ia e ʻike.

Hiki ke hoʻokō ʻia nā hopena maikaʻi loa inā ʻike mua ʻia kēia maʻi a hoʻomaka koke ka lāʻau.

No laila, inā loaʻa iā ʻoe kēia mau hōʻailona, ​​mai hoʻowahāwahā iā lākou a e ʻimi i ke aʻo lapaʻau. E lawe i ka lāʻau lapaʻau a kāu kauka i kuhikuhi ai me ka pololei, i ka manawa kūpono. E kamaʻilio me kāu kauka e pili ana i nā hopena ʻaoʻao. E hele i nā nānā lapaʻau i ka manawa kūpono. Inā hana pololei ʻoe i kēia mau mea, hiki iā ʻoe ke ola maikaʻi me kēia maʻi. ʻAʻole ʻoe hoʻokahi, a aia nā kauka ma laila e kōkua iā ʻoe.

ʻO ka maʻi puʻuwai, sarcoidosis, ka mumū o ka puʻuwai, ka hanu pōkole, ka ʻeha o ka umauma, ka puʻuwai kūpono ʻole, nā corticosteroids