Ke manaʻo nei ʻoe i kekahi manawa ua pōwehiwehi iki kou ʻike? A i ʻole ua lilo koke nā mea i maopopo i ka wā ma mua i mea ʻole? He mea maʻamau ke makaʻu iki i ka wā e hana ʻia ai kekahi mea e like me kēia. Akā inā ʻike ʻoe i ke ʻano i kapa ʻia ʻo `(Ectopia Lentis)` a mākou e kamaʻilio nei i kēia lā, e hiki iā ʻoe ke hoʻomaopopo pono i ka mea e hana ai me ka ʻole o ka hopohopo i kēlā mau manawa.
He aha ka `(Ectopia Lentis)`? E hoʻomaopopo maʻalahi kākou
I ka ʻōlelo maʻalahi, ʻo `(Ectopia Lentis)` ʻo ia hoʻi ua neʻe iki ka lens i loko o ko kākou maka mai kahi e pono ai, ʻo ia hoʻi, ua neʻe. E noʻonoʻo e like me ka `lens` i loko o kāu kāmela, aia kahi lens i loko o ko kākou maka. Hoʻopili kēia lens i ka mālamalama e komo i loko o ka maka a hoʻouna iā ia i ko kākou lolo ma ke ʻano he kiʻi maopopo. No laila, inā ʻaʻole kēia lens ma kahi kūpono, hoʻomaka nā mea a kākou e ʻike ai e lilo i mea palalulu.
Aia kēia aniani maka ma hope o ka haumāna o ko kākou maka. I kekahi manawa, hiki i ka aniani ke neʻe ma kēia ʻano ma ka maka hoʻokahi wale nō. Kāhea mākou iā ia he "isolated ectopia lentis". A i ʻole, hiki ke loaʻa ma nā maka ʻelua i ka manawa like, ʻo ia hoʻi ka "bilateral ectopia lentis".
Inā ʻike ʻoe i kekahi mau loli i kou mau maka a i ʻole ka ʻike ʻana, ʻoi aku ka maikaʻi o ka ʻike koke ʻana i kahi kauka maka. A laila hiki iā lākou ke hoʻoholo i ke kumu a paipai i ka lāʻau kūpono.
He aha nā hopena o ka `(Ectopia Lentis)` i ke kino?
E like me kā mākou i ʻōlelo ai ma mua, ua like ke aniani o loko o ka maka me ke aniani o ke kāmela. ʻO ia ka mea e hiki ai iā ʻoe ke ʻike maopopo i nā mea i mua ou. No laila, i ke ʻano o `(Ectopia Lentis)`, ʻaʻole kēia aniani ma kahi e pono ai, no laila e lilo kou ʻike i mea pōwehiwehi a maopopo ʻole. Hiki i kēia ke kumu i loaʻa iā ʻoe kahi maʻi i kapa ʻia ʻo `(refractive error)`, ʻo ia hoʻi kahi kīnā ʻike.
ʻO ke ʻano o ka neʻe ʻana o ka lens i kekahi ʻaoʻao e hoʻoholo ai i ka hopena o ka ʻike. Inā hānau ʻia ʻoe me ka `(Ectopia Lentis)`, hiki i ka lens ke neʻe i kekahi ʻaoʻao i kou wā ʻelemakule. Inā hana ʻia kēia ʻano e kahi ulia pōpilikia (trauma), hiki ke waiho ʻia ʻoe me ka ʻike ʻole i ka maka i hoʻopilikia ʻia.
ʻO ka mea nui loa, ʻo ka poʻe me ka `(Ectopia Lentis)` ʻoi aku ka nui o ka loaʻa ʻana o nā maʻi pili maka ʻē aʻe.
I waena o lākou, ke lawe nei kēia mau mea i kahi wahi koʻikoʻi:
- `(Glaucoma)` (Glaucoma)
- `(Nā Cataract)` (Nā Cataract)
- `(Ka hemo ʻana o ka Retinal)` (Ka hemo ʻana o ka Retinal)
ʻO ia ke kumu he mea nui e ʻimi koke i ke kōkua lapaʻau.
ʻO wai ka mea i kūpono loa e loaʻa i ka `(Ectopia Lentis)`?
ʻOiaʻiʻo, hiki i kekahi ke loaʻa i kahi maʻi i kapa ʻia ʻo `(Ectopia Lentis)`. Eia nō naʻe, ua ʻike nā kauka he ʻoi aku ka nui o ka loaʻa ʻana o ia mea i nā kāne ma mua o nā wahine.
Hiki i kekahi ke loaʻa i ka ʻeha maka mai kahi ulia, ʻeā? ʻOi aku ka maʻalahi o nā keiki ʻōpio a me nā ʻōpio i nā ʻeha maka i ka wā e pāʻani ana a i ʻole e hana ana i nā hana ʻē aʻe. E noʻonoʻo i ka pā ʻia ʻana e ka pōpō i ka wā e pāʻani ana i ka cricket, a i ʻole ka hāʻule ʻana i ka wā e holo ana a lele ana.Nā mea e like me ia. Eia kekahi, ʻoi aku ke kiʻekiʻe o kēia pilikia no ka poʻe e pāʻani ana i nā haʻuki koʻikoʻi e like me ka pôpeku a me ka hockey.
Akā, ʻaʻole kēia he maʻi maʻamau loa. Wahi a nā kuhi lapaʻau, ʻaʻole i hoʻopilikia kēia maʻi i ka ʻumi no kēlā me kēia haneli tausani o ka heluna kanaka o ka honua.
He aha nā hōʻailona o ka `(Ectopia Lentis)`?
Eia nā hōʻailona i ʻike pinepine ʻia:
- ʻIke makapō: ʻO kēia ka hōʻailona nui a maʻamau.
- Myopia: ʻIke kokoke: ʻIke maopopo ʻia nā mea kokoke, akā ua pōwehiwehi nā mea mamao.
- Astigmatism: Ma kēia ʻano, ʻaʻole i kau ʻia ka mālamalama e komo ana i ka maka ma kahi hoʻokahi, no laila e ʻike ʻia paha ka ʻike i ke ʻano ʻē a me ka pōwehiwehi.
- ʻUlaʻula o nā maka
- ʻEha maka
- `(Diplopia)` (ʻike pālua): ʻIke ʻana i hoʻokahi mea me he mea lā ʻelua.
Inā loaʻa iā ʻoe kekahi a ʻoi aku paha o kēia mau hōʻailona, e ʻike pono i kahi ophthalmologist.
No ke aha e hana ʻia ai kēia? Nā kumu nui o ka `(Ectopia Lentis)`
Aia kekahi mau kumu nui o ka `(Ectopia Lentis)`.
1. Nā ʻeha maka
ʻO nā pōʻino i ka maka, e like me nā hahau nui, hiki ke hoʻoneʻe i ka lens i loko o ka maka mai kona kūlana mua. Eia kekahi laʻana:
- Nā ulia haʻuki (ʻoi aku ka paʻi ʻia e ka pōpō, nā kuʻi ʻana)
- Nā ulia kaʻa
- Hāʻule (e like me ka hāʻule ʻana mai kahi kiʻekiʻe, ka paheʻe ʻana, a pēlā aku)
2. Nā maʻi hoʻoilina
ʻO nā maʻi genetic nā kūlana i hoʻokumu ʻia e kahi mutation genetic a i ʻole kahi loli i ka nui o nā mea genetic i loko o kā mākou mau genes. Hoʻoilina mākou i kēia mau genes mai ko mākou mau mākua. No laila, hiki i kekahi mau maʻi genetic ke hoʻonui i ka pilikia o ka hoʻomohala ʻana iā Ectopia Lentis. ʻO kekahi o nā kūlana genetic nui:
- ʻO ka maʻi Marfan
- ʻO ka maʻi Weill-Marchesani
- ʻAniridia
- `(Homocystinuria)`
- ʻO ka maʻi Ehlers-Danlos
- ʻO ka maʻi ʻo Pierre Robin
- ʻO ka Retinitis pigmentosa
- `(Maʻi Refsum)`
- ʻO ka maʻi Axenfeld-Rieger
- `(ʻIli pupillary paʻa)`
He mea paʻakikī paha kēia mau inoa, akā ʻo kēia nā huaʻōlelo lapaʻau. Inā he kānalua kou e pili ana i kahi maʻi e like me kēia, ʻoi aku ka maikaʻi o ke kamaʻilio ʻana me ke kauka.
3. Nā kūlana olakino ʻē aʻe e pili ana i nā maka
ʻO kekahi kūlana olakino e hōʻino ana i nā maka a i ʻole nā ʻiʻo maka e hiki ke hana i ka `(Ectopia Lentis)`. Eia kekahi mau laʻana:
- `(Pseudoexfoliation syndrome)`
- `(Hyperinsulinemia)` (nā pae insulin kiʻekiʻe)
- `(Syphilis)` (Syphilis)
- Ka maʻi ʻaʻai maka
Pehea e ʻike ai i ka `(Ectopia Lentis)`? (Diagnosis)
Hiki i ke kauka maka ke ʻike maopopo inā loaʻa iā ʻoe kēia maʻi. E nānā pono ʻo ia i kou mau maka, ʻo ia hoʻi e nānā i loko o kou mau maka. E hana pū ʻo ia i kahi 'hoʻāʻo ʻike maka' e ʻike i ka maikaʻi o kou ʻike.
Eia kekahi, e nānā pono ke kauka i kēia mau ʻāpana o kou maka:
- ʻO Cornea (ka ʻāpana moakaka o ke alo o ka maka)
- `(Retina)` (Retina)
- Kaomi maka
I kekahi manawa, pono paha nā hoʻāʻo koko e hoʻoholo ai inā he genetic ke kumu o Ectopia Lentis. Hiki i kāu kauka ke kauoha i nā hoʻokolohua e nānā i nā kūlana genetic e hoʻopilikia i kāu ʻōnaehana musculoskeletal, e like me kou mau iwi, nā ʻiʻo, nā ligaments, a me nā tendons.
He aha nā lāʻau lapaʻau no ka `(Ectopia Lentis)`?
ʻO ka lāʻau no ka `(Ectopia Lentis)` e pili ana i ke kumu.
Pono ka poʻe he nui e komo i nā aniani maka a i ʻole nā aniani hoʻopili e hoʻomaikaʻi i ko lākou ʻike. Na kāu kauka maka e haʻi iā ʻoe i ka mea maikaʻi loa iā ʻoe.
Inā ua hana ʻia ʻo Ectopia Lentis e kahi ulia a i ʻole kahi maʻi hoʻoilina, pono e mālama ʻia kēlā kumu kumu.
ʻO ke ʻoki kino ʻana (Ectopia Lentis)
I kekahi mau hihia, ʻoiai inā he mau pilikia maka ʻē aʻe e like me ka glaucoma a i ʻole ka retinal detachment e hoʻopilikia pū ana i kou mau maka, pono paha ke ʻoki ʻana e hoʻoponopono i ke kūlana. Hana ʻia kēia ʻano ʻoki e ke kauka maka (Ophthalmologist). E haʻi aku ʻo ia iā ʻoe i ke ʻano o ke ʻoki āu e pono ai a me ka lōʻihi o ka manawa e hoʻōla ai.
Aia kekahi ala e pale aku ai i ka `(Ectopia Lentis)`?
ʻO ke kūlana `(Ectopia Lentis)` i hoʻokumu pinepine ʻia e nā kumu hoʻoilina a me nā ulia pōpilikia i hiki ʻole iā mākou ke kāohi. No laila, he paʻakikī ke pale loa aku.
Eia nō naʻe, inā ʻoe e pilikia ana i ka hoʻoili ʻana i nā maʻi genetic, e kamaʻilio me kāu kauka e pili ana i ia mea. Hiki paha i ke aʻo ʻana i nā genetic ke kōkua iā ʻoe e ʻike pehea e pili ai kēia mau maʻi i kou ʻohana.
ʻO ka mea nui loa, ʻo ia ke komo ʻana i nā lako pale i ka wā e hana ana i ka hana a i ʻole e pāʻani ana i nā haʻuki e hiki ke hoʻoweliweli i nā maka. ʻO ka hoʻohana ʻana i nā mea e like me ka mahiole a me nā aniani palekana hiki ke pale aku i nā ulia he nui.
ʻEhia pinepine e pono ai iaʻu e nānā i koʻu mau maka?
Ma ka nānā mau ʻana i kou mau maka a me kou ʻike maka, hiki i ke kauka maka ke ʻike i nā pilikia i ka wā mua. ʻOkoʻa ka awelika o ka manawa ma waena o nā hoʻokolohua maka ma muli o kou makahiki:
- Nā keiki ʻōpio: E nānā ʻia kou mau maka e ke kauka lapaʻau keiki i kēlā me kēia kipa ʻana i ke keiki olakino a hiki i ko lākou hoʻomaka ʻana i ke kula, a laila hoʻokahi manawa i hoʻokahi a ʻelua paha makahiki ma hope o kēlā.
- Nā mākua ma lalo o 40 mau makahiki: I kēlā me kēia ʻelima a ʻumi makahiki.
- Nā pākeke ma waena o 40 a me 54 mau makahiki: I kēlā me kēia ʻelua a ʻehā mau makahiki.
- Nā pākeke ma waena o 55 a me 64 mau makahiki: I kēlā me kēia makahiki a i ʻole i kēlā me kēia ʻekolu makahiki.
- Nā mākua he 65 mau makahiki a ʻoi: Hoʻokahi manawa i kēlā me kēia makahiki a ʻelua paha makahiki.
Inā ʻoe e kau ana i nā aniani maka, nā aniani hoʻopili, a i ʻole nā mea kōkua ʻike maka ʻē aʻe, pono paha ʻoe e nānā pinepine i kou mau maka. Pono nō hoʻi ka poʻe me ka maʻi diabetes, kekahi mau maʻi maka, a i ʻole kahi mōʻaukala ʻohana o nā maʻi maka e nānā pinepine ʻia ko lākou mau maka. E nīnau i kāu kauka maka i ka pinepine o kou nānā ʻana i kou mau maka.
He aha ke ʻano o ka wā e hiki mai ana e hiki i kekahi me `(Ectopia Lentis)` ke manaʻo?
Pehea e hoʻopilikia ai ʻo Ectopia Lentis iā ʻoe i ka wā e hiki mai ana ma muli o kekahi mau kumu:
- Ka mamao i neʻe ai kāu aniani.
- Pehea ka nui o ka hopena i kou ʻike.
- He aha ke kumu o ka `(Ectopia Lentis)`?
- kou mau makahiki.
- ʻO nā kūlana olakino a i ʻole nā ʻeha ʻē aʻe āu i loaʻa ai.
Na kāu kauka a kauka maka paha e haʻi iā ʻoe i ka lōʻihi o ka manawa e hoʻōla ai a me ka nui o ka ʻike hiki iā ʻoe ke hoʻihoʻi.
Āhea wau e ʻike ai i ke kauka?
E ʻike i ke kauka maka i ka wā e ʻike ai ʻoe i kekahi mau loli i kou ʻike - ʻoiai inā e lilo koke ia i mea ʻino . ʻOiai inā ʻaʻole ʻo Ectopia Lentis, inā he ʻike pohihihi hou kāu a i ʻole kahi manaʻo ʻaʻole hiki i kou mau maka ke nānā pono, he mea nui e nānā koke i kou mau maka.
Inā loaʻa iā ʻoe kahi ʻeha nui o kou maka, a inā nalowale koke kou ʻike ma kekahi a i ʻole nā maka ʻelua, e hele koke i ka keʻena pilikia o ka haukapila.
He aha nā nīnau āu e nīnau ai i kāu kauka?
- He aha ke kumu e loaʻa ai iaʻu ka `(Ectopia Lentis)`?
- He aha nā hoʻokolohua e pono ai iaʻu e hana?
- E pono anei iaʻu nā aniani maka a i ʻole nā aniani hoʻopili? Inā pēlā, ʻoi aku ka maikaʻi o nā aniani maka a i ʻole nā aniani hoʻopili noʻu?
- E pono anei iaʻu ke ʻoki kino?
- Pono anei au e ʻimi i ke aʻoaʻo genetic e ʻike ai inā paha e pilikia ana kaʻu mau keiki i ka loaʻa ʻana o kēia mau kūlana genetic?
He ʻelua mau mea ʻokoʻa anei ʻo `(Ectopia Lentis)` a me `(Lens Subluxation)`?
ʻO `(Ectopia Lentis)` a me `(Lens Subluxation)` ʻelua mau inoa i hoʻohana ʻia no ke kūlana like. Hiki i kāu kauka maka ke ʻōlelo he `subluxation` kāu lens i hoʻopilikia ʻia. Pili kēia i ke kekelē i neʻe ai ka lens mai kona kūlana maʻamau.
ʻO ka mea hope loa, leka lawe i ka home
ʻOiai ke kumu o Ectopia Lentis, inā neʻe ka lens i loko o kou maka i waho o kona wahi, lilo kou ʻike i mea pōwehiwehi a paʻakikī. ʻO ka mea pōmaikaʻi, hiki i ka hapa nui o ka poʻe ke ʻike maopopo hou me nā aniani a i ʻole nā lens hoʻopili.
Inā he ulia a he maʻi hoʻoilina paha ke kumu o ka `(Ectopia Lentis)`, pono paha nā lāʻau lapaʻau ʻē aʻe ma waho aʻe o nā aniani. Inā ʻike ʻoe i kekahi mau loli liʻiliʻi i kou ʻike, a i ʻole manaʻo ʻoe ʻaʻole "ʻoi e like me ka wā ma mua," mai hoʻowahāwahā iā ia. E ʻike i kahi kauka maka i ka wā hikiwawe loa a e nānā iā ia. ʻO ia ka mea maikaʻi loa hiki iā ʻoe ke hana no kou mau maka.
`ʻEctopia Lentis, aniani o ka maka, ʻike maka pōwehiwehi, maʻi maka, maʻi hoʻoilina, ulia maka, kauka maka











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