ʻIke ʻoe he ʻelua puʻupaʻa ko kākou a pau, hoʻokahi ma kēlā me kēia ʻaoʻao o ko kākou iwi kuamoʻo? Ua like kēia me nā kānana ʻelua i loko o ko kākou kino. ʻO kā lākou hana nui, ʻo ia ka hoʻomaʻemaʻe ʻana i ke koko a wehe i nā mea ʻōpala e like me ka mimi. Eia naʻe, ua hānau ʻia kekahi poʻe me ʻelua puʻupaʻa ʻaʻole i kaʻawale, akā ua pili ma lalo, e like me ka lio. ʻO ia ke kumu i kapa ʻia ai lākou ʻo "Horseshoe Kidney" i ka lāʻau lapaʻau. Mai makaʻu i kou lohe ʻana i kēia inoa. ʻAʻole kēia he mea weliweli e like me kou manaʻo. Akā, he mea nui loa ia iā ʻoe e makaʻala i kēia.
I ka ʻōlelo maʻalahi, he aha kēia Lio Holo Lio?
He kūlana kēia i loaʻa i ka wā hānau. I ka lāʻau lapaʻau, kapa mākou i kēia mau mea he "congenital anomaly." I ka ʻōlelo maʻalahi, he mea ia e hana ʻia ana i ka wā e ulu ana ke pēpē i loko o ka ʻōpū.
E noʻonoʻo i kēia ʻano. Ke ulu mua nei kahi pēpē i loko o ka ʻōpū, hana ʻia nā puʻupaʻa mua ʻelua ma lalo loa o ka ʻōpū, ma ka ʻāpana pelvic. A laila, i ka ulu ʻana o ke pēpē, neʻe mālie kēia mau puʻupaʻa ʻelua i luna a i ko lākou mau wahi kūpono ma nā ʻaoʻao ʻelua o ke kuamoʻo.
Eia nō naʻe, he mea ʻokoʻa ka mea e hana ʻia i kekahi me ke ʻano o ka Horseshoe Kidney. I ka piʻi ʻana o nā puʻupaʻa ʻelua, hui pū ko lākou mau wēlau haʻahaʻa. E like me ka leka "U". Ke hui pū lākou e like me kēia, ʻaʻole hiki iā lākou ke piʻi pololei. No laila, ʻo ka puʻupaʻa i hui pū ʻia aia ma kahi haʻahaʻa iki ma mua o ka maʻamau, ma ke alo o ka ʻōpū. Ua kapa ʻia hoʻi kēia he renal fusion .
He koʻikoʻi anei kēia kūlana? He mea anei kaʻu e hopohopo ai?
ʻO kēia ka pilikia nui loa i loaʻa i nā kānaka he nui. ʻO kaʻoiaʻiʻo, ʻo ka hapa nui o ka poʻe me Horseshoe Kidney ʻaʻole lākou e ʻike i nā pilikia olakino koʻikoʻi. He nui ka poʻe me kēia maʻi e ola maʻamau a hana me ka ʻole o nā pilikia.
ʻO ka mea nui, ʻaʻole maʻamau ka hopena o ka Horseshoe Kidney i kou ola. Hiki iā ʻoe ke ola i kahi ola lōʻihi a olakino e like me nā poʻe ʻē aʻe.
Eia nō naʻe, aia kekahi mea liʻiliʻi e pono ai kākou e makaʻala. ʻOi aku ka nui o ka pilikia o ka poʻe me kēia maʻi i ka loaʻa ʻana o ka maʻi ʻaʻai puʻupaʻa ma mua o ka heluna kanaka maʻamau. I kēia manawa, mai hopohopo ke lohe ʻoe i kēia. ʻAʻole kēia manaʻo e loaʻa i nā kānaka a pau ka maʻi ʻaʻai, akā ʻo ia hoʻi "ʻoi aku ka kiʻekiʻe o ka pilikia." ʻO ia ke kumu he mea nui e loaʻa nā hoʻokolohua maʻamau e like me ka ʻōlelo a kāu kauka. Inā ʻike mua ʻia, he maʻi hiki ke ho'ōla ʻia ka maʻi ʻaʻai puʻupaʻa.
ʻAʻole maʻamau loa kēia ʻano. Hoʻopilikia ia ma kahi o 1 i loko o 500 mau kānaka. ʻOi aku ka maʻamau o ia i nā kāne ma mua o nā wahine.
Aia kekahi mau pilikia ʻē aʻe e pili ana me ka Horseshoe Kidney?
ʻAe. I kekahi manawa hiki ke loaʻa ka puʻupaʻa Horseshoe ma kāna iho. Eia nō naʻe, i kekahi mau hihia, ʻike ʻia ia me nā kūlana genetic a chromosomal ʻē aʻe. He mea maikaʻi ke makaʻala i kēia.
| Māhele maʻi | Nā kūlana olakino pili paha |
|---|---|
| Nā kūlana chromosomal |
|
| Nā kūlana genetic ʻē aʻe (nā kūlana Nonchromosomal) |
He aha nā hōʻailona o kēia maʻi?
Eia ka mea kupaianaha. ʻO ka hapa nui o ka poʻe me Horseshoe Kidney, ʻaʻole lākou e ʻike i kekahi mau hōʻailona i ko lākou ola. ʻO ka hapa nui o ka manawa, ʻike ʻia ke kūlana ma ka hanana i ka wā o ka scan no kekahi mea ʻē aʻe.
Eia nō naʻe, hiki i kekahi poʻe ke loaʻa nā hōʻailona. Inā loaʻa, ʻo nā hōʻailona maʻamau:
| Hōʻailona | He wehewehe maʻalahi |
|---|---|
| Nā maʻi ʻōpū mimi pinepine (UTIs) | Hiki i nā maʻi ʻaʻai mimi (UTI) ke hōʻike pinepine me nā hōʻailona e like me ke kuni, ka ʻeha (dysuria) , a me ke kuni i ka wā e mimi ai. |
| Nā pōhaku puʻupaʻa | Hiki i nā hōʻailona ke komo pū me ka ʻeha o ka ʻōpū, ka ʻeha o ke kua i lalo, ke koko i loko o ka mimi (hematuria) , a me ka ʻeha i ka wā e mimi ai. |
| Ka luaʻi a me ka luaʻi | Hiki i kekahi poʻe ke loaʻa i ka nausea a me ka luaʻi ma muli o ka hana ʻino o nā puʻupaʻa. |
No ke aha lā kēia e hana nei?
ʻAʻole maopopo i nā kauka a me nā mea noiʻi ke kumu o kēia. Ma muli wale nō ia o kahi loli i ke ʻano o ka hana ʻana o nā genes i ka wā e ulu ana ke pēpē i loko o ka ʻōpū.
Ke ʻike ʻia kahi pēpē hānau hou me ka Horseshoe Kidney, pinepine nā mākua e noʻonoʻo inā ua hana hewa lākou i ka wā hāpai. ʻAʻohe hewa o ia mea. ʻAʻole kēia kou hewa. He mea kēia e hana pinepine ʻia i kekahi manawa, a ʻaʻole mākou i ʻike i ke kumu. No laila, mai hopohopo no ia mea.
He aha nā pilikia e hiki ai i kēia ke hana?
ʻOiai inā ʻaʻohe hōʻailona, ʻo ka loaʻa ʻana o kahi Horseshoe Kidney e kau iā ʻoe i kahi pilikia kiʻekiʻe iki o ka hoʻomohala ʻana i kekahi mau pilikia.
- ʻO ka pilikia maʻamau: He kūlana kēia i kapa ʻia ʻo ka ureteropelvic junction (UPJ) obstruction . I ka ʻōlelo maʻalahi, he poloka ia ma ka hoʻomaka ʻana o ka ureter, ka ʻōmole e lawe ana i ka mimi mai ka puʻupaʻa a i ka ʻōpū mimi. Hiki i ke ʻano o ka puʻupaʻa ke ālai i ke kahe o ka mimi. Loaʻa kēia kūlana ma kahi o hoʻokahi hapakolu (33%) o ka poʻe me ka puʻupaʻa lio.
- Nā pilikia ʻē aʻe:
- ʻO ka reflux Vesicoureteral (VUR): Ke kahe hope ʻana o ka mimi mai ka ʻōpū mimi i loko o nā puʻupaʻa.
- Hydronephrosis: Ka pehu ʻana o ka puʻupaʻa ma muli o ka mimi ʻole e kahe pono ana.
- ʻO ka maʻi puʻupaʻa Polycystic (PKD): Ke kūkulu ʻia ʻana o nā cysts piha i ka wai i loko o nā puʻupaʻa.
- ʻO ke koko kiʻekiʻe Renovascular: Ke koko kiʻekiʻe i hoʻokumu ʻia e ka haiki ʻana o nā kīʻaha koko e hoʻolako koko i nā puʻupaʻa.
- Ka maʻi ʻaʻai puʻupaʻa: E like me ka mea i ʻōlelo ʻia ma mua, ʻoi aku ke kiʻekiʻe o ka pilikia.
No laila, inā loaʻa iā ʻoe ka Horseshoe Kidney, he mea naʻauao ke makaʻala i nā hōʻailona o ka maʻi ʻaʻai puʻupaʻa.
- Koko i loko o ka mimi
- Ke manaʻo nei i kahi puʻupuʻu ʻē a i ʻole ka pehu ʻana i loko o ka ʻōpū
- ʻO ka ʻeha maʻamau e hele mai ana mai ka ʻaoʻao o ka ʻaoʻao haʻahaʻa
Inā ʻike ʻoe i kekahi mea e like me kēia, e ʻike koke i kāu kauka.
Pehea e ʻike ai i kēia maʻi?
E like me ka mea i ʻōlelo ʻia ma mua, ʻike pinepine ʻia kēia ma ka manawa kūpono. Eia nō naʻe, inā loaʻa iā ʻoe nā hōʻailona e pili ana i kou mau puʻupaʻa, e nānā kāu kauka iā ʻoe. Eia kekahi, hiki iā lākou ke hana i nā hoʻokolohua e like me kēia.
- Urinalysis: Nānā i ke koko a i ʻole ka maʻi i loko o ka mimi.
- Nā hoʻāʻo koko: Nā hoʻāʻo e ʻike ai i ka hana maikaʻi o nā puʻupaʻa.
- Ka helu kānana glomerular i manaʻo ʻia (eGFR)
- Hoʻāʻo ʻia ka naikokene urea koko (BUN)
- Hoʻāʻo hoʻomaʻemaʻe Creatinine
- Nā Hoʻāʻo Kiʻi (Scans): Kōkua kēia i ka hoʻoholo pololei ʻana i ke ʻano, ke kūlana, a me ka hana o nā puʻupaʻa.
- ʻO ke ultrasound o nā puʻupaʻa: ʻO ka hoʻāʻo i hana pinepine ʻia, ʻaʻohe ʻeha.
- Voiding cystourethrogram (VCUG): He hoʻāʻo X-ray kūikawā e nānā ai no ka reflux urinary (VUR).
- ʻO ke kiʻi Radionuclide: He hoʻāʻo e ʻike ai i ka hana maikaʻi ʻana o nā puʻupaʻa a me ka maikaʻi o kā lākou hana ʻana i ka mimi.
- ʻO nā hoʻokolohua kikoʻī hou aku e like me ka MRI scan (Magnetic resonance imaging): a me CT scan (Computed tomography scan) .
He mea pono anei ka lāʻau lapaʻau? He aha ka mea hiki ke hana ʻia?
Aia nō ia i kou loaʻa ʻana o nā hōʻailona a i ʻole.
ʻAʻole hiki ke "ho'ōla" a hoʻopau ʻia paha ke kuniʻo o Horseshoe no ka mea he ʻāpana ia o ke kino i loaʻa i ka wā hānau. No laila, inā ʻaʻohe hōʻailona, ʻaʻole pono ʻoe i kekahi lāʻau lapaʻau.
Eia nō naʻe, inā he mau hōʻailona a pilikia paha kou, hiki ke mālama ʻia.
- No nā maʻi ʻaʻai mimi (UTIs): E hāʻawi kāu kauka iā ʻoe i nā lāʻau antibiotic .
- No nā pōhaku puʻupaʻa a i ʻole nā mea ālai: I kekahi manawa, pono paha ke ʻoki ʻana e wehe i nā pōhaku puʻupaʻa a i ʻole e maʻalahi ai ke kahe ʻana o ka mimi.
ʻO ka maʻamau, ʻaʻole hoʻāʻo nā kauka e hoʻokaʻawale a wehe paha i kahi puʻupaʻa lio (nephrectomy) ma ke ʻoki ʻana no ka mea ʻaʻole ia he maʻi kanesa, a nui ka poʻe e noho me ia me ka pilikia ʻole.
Pehea lā e hiki ai iaʻu ke noho maluhia me kēia maʻi?
ʻAʻole paʻakikī ka noho ʻana me kēia. Eia nō naʻe, pono mākou e hana i kekahi mau hana palekana. ʻOiai aia ka puʻupaʻa Horseshoe ma mua o ka ʻōpū ma mua o ka puʻupaʻa maʻamau,ʻOi aku ka kiʻekiʻe o ka manawa kūpono o ka hōʻeha kino.
No laila, e makaʻala i kēia mau mea:
1. E komo i kahi kūpeʻe lima makaʻala lapaʻau: E mālama i kahi kūpeʻe lima a kāleka paha e hōʻike ana he maʻi puʻupaʻa kou. I ka wā o kahi pilikia, e kōkua ia i nā kauka e mālama nei a me nā lawelawe pilikia e ʻike e pili ana i kou kūlana.
2. E hōʻalo i nā haʻuki pili: He mea nui loa kēia no nā keiki. ʻO nā haʻuki e pili pono ana i ka pili ʻana, e like me ka rugby, ka pôpeku, karate, a me ka mokomoko, hiki ke hōʻino i nā puʻupaʻa.
3. E ʻaʻahu i ke kāʻei pale: Inā ʻoe (a i ʻole kāu keiki) e komo ana i kahi haʻuki a hana paha e hiki ai ke hōʻino i nā puʻupaʻa, e ʻaʻahu i kahi pale pale kūikawā e uhi ana i ka ʻōpū (pale puʻupaʻa a pale puʻupaʻa paha) .
ʻOi aku ka maikaʻi o ka launa pū ʻana me kāu kauka a loaʻa nā nānā kino a me nā scans maʻamau e like me kāna e ʻōlelo ai.
Leka Lawe-Home
- He maʻi hānau ʻia ka puʻupaʻa lio kahi e hui pū ʻia ai nā puʻupaʻa ʻelua ma lalo. ʻAʻole kēia he mea weliweli e like me kou manaʻo.
- ʻAʻole ʻike ka nui o ka poʻe i kekahi mau hōʻailona a ola i nā ola maʻamau a olakino.
- Hiki i kekahi poʻe ke loaʻa i nā pilikia e like me nā maʻi ʻaʻai mimi pinepine (UTIs) a i ʻole nā pōhaku puʻupaʻa. Aia nā lāʻau lapaʻau maikaʻi no kēia mau mea.
- Hiki i kēia ʻano ke hōʻino maʻalahi i nā puʻupaʻa. No laila, he mea nui loa e pale i nā haʻuki e pili ana i ke kino a e noho palekana.
- Inā he mau nīnau kāu, hopohopo, a kānalua paha e pili ana i kēia, a inā ʻike ʻoe i nā hōʻailona e like me ka ʻeha o ka ʻōpū a i ʻole nā maʻi mimi, ʻo ka mea maikaʻi loa e hana ai, ʻo ia ke kamaʻilio me kāu kauka e pili ana i ia mea.











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