Ke manaʻo nei ʻoe i kekahi manawa i nā ʻeha kino i wehewehe ʻole ʻia? Ke mae nei kou mau lālā? A i ʻole ke manaʻo nei ʻoe e kolo wale ana kou ʻili? ʻO kekahi o nā kumu o kēia mau mea he maʻi i kapa ʻia ʻo hypoparathyroidism, a mākou e kamaʻilio nei i kēia lā. Mai hopohopo, ʻoiai he maʻi kakaikahi kēia, hiki ke hoʻomalu ʻia inā ʻike ʻia a mālama pono ʻia. E kamaʻilio kākou e pili ana i kēia me nā kikoʻī.
He aha ka Hypoparathyroidism?
I ka ʻōlelo maʻalahi, ʻo ka hypoparathyroidism ka wā e hana ai kou koko i ka liʻiliʻi a i ʻole ka ʻole o ka Parathyroid Hormone (PTH). He mea nui kēia hormone no ka hoʻoponopono ʻana i nā pae o ka calcium a me ka phosphorus i loko o kou kino. No laila, ke haʻahaʻa kāu mau pae PTH, hāʻule kāu mau pae calcium koko - kapa mākou i kēia hypocalcemia - a piʻi aʻe kāu mau pae phosphorus koko.
He maʻi mau kēia maʻi pinepine, ʻo ia hoʻi hiki ke mau i ke ola holoʻokoʻa. Eia nō naʻe, i kekahi mau hihia, hiki nō hoʻi ke hoʻomaikaʻi no kekahi manawa.
No laila he aha kēia mau kelepa parathyroid?
E noʻonoʻo, ma ke alo o ko kākou ʻāʻī, ma ke ʻano o ka pulelehua, aia ka Thyroid Gland. Ma hope o kēlā Thyroid Gland, aia nā ʻehā kelepa, ʻo ka nui maʻamau e like me ka nui o kahi pī liʻiliʻi. Ua kapa ʻia kēia mau mea he Parathyroid Glands . He ʻāpana kēia o ka Endocrine System, ka mea e hana ana i nā hormones i loko o ko kākou kino.
I kekahi manawa hiki ke loaʻa kēia mau kelepa ʻehā ma kahi ʻē aʻe o ka ʻāʻī, ka umauma, a i ʻole ma ka esophagus. Ua kapa ʻia kēia mau mea he ectopic parathyroid glands .
ʻO ka hana nui a kēia mau kelepa parathyroid ka hana ʻana i ka hormone parathyroid (PTH). ʻO kēia PTH ka mea e mālama ai i ka pae calcium i loko o ko kākou koko ma ka pae kūpono.
- Inā emi ka PTH: E emi ana ka calcium i loko o ke koko (Hypocalcemia).
- Inā piʻi ka PTH: Piʻi ka calcium i loko o ke koko (Hypercalcemia).
ʻAʻole wale kēlā, akā kōkua pū kēia hormone PTH i ka kaohi ʻana i nā pae o ka phosphorus a me ka wikamina D i loko o ke koko a me nā iwi.
He aha ka kalipuna? He aha kāna hana no ko kākou kino?
He mineral koʻikoʻi ka kalipuna no ko kākou kino. Ua ʻike anei ʻoe ʻo ka hapa nui o ka kalipuna i loko o ko kākou kino e mālama ʻia ana i loko o ko kākou mau iwi? Eia nō naʻe, pono nō hoʻi e loaʻa kahi nui o ka kalipuna i loko o ke koko.
E nānā kākou i kekahi mau mea koʻikoʻi ʻē aʻe ma mua o ka calcium i loko o ke koko:
- Kōkua ia i ka hana o kā mākou ʻōnaehana nerve .
- Kōkua ia i nā ʻiʻo e ʻūmiʻi a hoʻomaha . ʻO kēia ka mea e hiki ai iā mākou ke hoʻoneʻe i ko mākou mau lālā a hele.
- Ke loaʻa iā mākou kahi ʻeha a kahe ke koko, kōkua ia i ke kāpili ʻana o ke koko .
- He mea nui i ko kākou puʻuwai e hana pono .
I kēia manawa ua maopopo iā ʻoe pehea e hiki ai i ka hypocalcemia (ka haʻahaʻa o ke kalaka koko) ma muli o ka hypoparathyroidism ke hoʻopilikia i nā mea he nui. Pono pū ka kalaka e hoʻoikaika i nā iwi. Akā, ʻo ka hypocalcemia ka emi ʻana o ka kalaka i loko o ke koko, ʻaʻole ka emi ʻana o ka kalaka i loko o nā iwi.
Hiki i ka hypoparathyroidism ke hoʻoulu i ka electrolyte imbalance?
ʻAe, ʻoiaʻiʻo nō. ʻO ka Calcium a me ka Phosphorus ʻelua ʻano o nā electrolytes . ʻO nā electrolytes he mau minelala nona ka hoʻouka uila i loko o ko kākou kino a hāʻawi i nā hana koʻikoʻi he nui. I ka hypoparathyroidism, emi ka calcium i loko o ke koko a piʻi ka phosphorus, e hana ana i kahi kaulike ʻole o ka electrolyte. He mea nui loa ia e hoʻoponopono i kēia.
Aia kekahi mea hou aʻe. ʻO ka Magnesium kekahi electrolyte koʻikoʻi. Inā emi ka pae o ka magnesium i loko o ke koko (Hypomagnesemia) , hiki iā ia ke lilo i kumu o ka hypoparathyroidism. No ka mea, he mea nui ka magnesium no ka hana pono ʻana o nā kelepa parathyroid.
He aha ka ʻokoʻa ma waena o ka Hypoparathyroidism a me ka Hyperparathyroidism?
Ua like iki kēia mau inoa ʻelua, no laila hiki ke huikau. I ka lāʻau lapaʻau, ʻo ka prefix "Hypo" ʻo ia hoʻi "emi" a i ʻole "ʻaʻole lawa." ʻO ka prefix "Hyper" ʻo ia hoʻi "ʻoi aku" a i ʻole "kiʻekiʻe."
- Hypoparathyroidism: ʻAʻole hana nā kelepa parathyroid i ka nui o ka hormone parathyroid (PTH), kahi e hoʻohaʻahaʻa ai i nā pae calcium i loko o ke koko.
- Hyperparathyroidism: Hoʻopuka nā kelepa parathyroid i ka nui o ka PTH, kahi e hoʻonui ai i ka calcium i loko o ke koko.
Maʻalahi, ʻeā?
ʻO wai ka mea e loaʻa ana i kēia maʻi i kapa ʻia ʻo hypoparathyroidism?
Hiki i kēia ke hana i nā pākeke a me nā keiki ʻōpio. Akā e like me ka mea i ʻōlelo ʻia ma mua, he ʻano laha ʻole kēia.
- I nā pākeke: Hoʻokumu pinepine ʻia kēia e ka hōʻino ulia pōpilikia i nā kelepa parathyroid i ka wā o ke ʻoki ʻāʻī - no ka laʻana, ke ʻoki thyroid.
- No nā keiki: Hoʻokumu pinepine ʻia kēia e kahi maʻi genetic i kapa ʻia ʻo DiGeorge Syndrome i nā keiki.
ʻOiai ma kahi ʻāina e like me ʻAmelika, ua ʻōlelo ʻia ua hoʻopilikia kēia kūlana i ka emi ma mua o ʻelua haneli tausani kānaka. No laila, ma ko mākou ʻāina, hiki ke emi iki aku.
He aha nā kumu nui o ka hypoparathyroidism?
Aia kekahi mau kumu no kēia.
- ʻO ka hōʻino ʻana i nā kelepa parathyroid: ʻO kēia ke kumu maʻamau. Ma kahi o 75 pakeneka (75%) oLoaʻa i nā maʻi kēia ʻano ke hōʻino ʻia nā glands i ka wā o ke ʻoki ʻana ma ka ʻāʻī a i ʻole ke kelepa thyroid. I kekahi manawa, hiki ke loaʻa kēia ʻano i nā makahiki ma hope o ke ʻoki ʻana. Akā ʻo ka hapa nui, hoʻomaka koke ia ma hope o ke ʻoki ʻana. ʻO ka Hypoparathyroidism e hana ʻia ma kēia ʻano he manawa pōkole wale nō, akā i kekahi poʻe hiki ke mau loa. ʻAʻole paha e hōʻino ka radiation therapy i kēia mau glands.
- Nā kūlana hoʻoilina: ʻOi aku ma mua o ʻumi pakeneka (10%) o nā hihia i hoʻokumu ʻia e nā kūlana hoʻoilina. ʻO ka mea maʻamau o kēia mau mea ʻo DiGeorge Syndrome . He kūlana hoʻoilina chromosomal kēia. ʻAʻohe o nā kelepa parathyroid o nā pēpē i hānau ʻia me kēia maʻi. No laila, no ka mea ʻaʻole lākou e hana i ka PTH, loaʻa iā lākou ka hypoparathyroidism mau loa. Ma kahi o 60% o nā keiki me ka hypoparathyroidism ua ʻōlelo ʻia he DiGeorge Syndrome. Hiki ke hoʻokumu ʻia e nā syndromes genetic ʻē aʻe e pili ana i ka kuli a me nā maʻi puʻupaʻa.
- Nā Maʻi Autoimmune: I kekahi manawa, hoʻouka hewa kā mākou ʻōnaehana pale ponoʻī i nā kelepa parathyroid. ʻO ka maʻi polyglandular autoimmune Type 1 kekahi o ia mau maʻi. Hoʻoulu kēia i ka hypoparathyroidism mau. Hiki ke hana ʻia e nā kūlana i kapa ʻia ʻo ka maʻi Addison a me ka anemia pernicious .
- Nā Maʻi Komo: I kekahi mau kūlana maʻi, hiki i nā mea e like me ka hao (e like me ka hemochromatosis) a me ke keleawe (e like me ka maʻi o Wilson) ke hōʻiliʻili i loko o nā kelepa parathyroid. Eia kekahi, hiki i kekahi mau metastases kanesa ke hoʻopilikia i ka hana o kēia mau kelepa, e hana ana i ka hypoparathyroidism.
- Nā Pae Magnesium Haʻahaʻa: E like me ka mea i ʻōlelo ʻia ma mua, he mea nui ka magnesium no nā kelepa parathyroid e hana pono. ʻO nā pae haʻahaʻa o ka magnesium i loko o ke koko (hypomagnesemia) hiki ke alakaʻi i ka hypoparathyroidism. Ua kapa ʻia kēia he hypoparathyroidism hana . Hoʻopau pinepine ʻia kēia kūlana ke hoʻihoʻi ʻia nā pae magnesium.
He aha nā hōʻailona o ka hypoparathyroidism?
I ka manawa pinepine, lohi loa ka ulu ʻana o kēia maʻi. No laila, hiki ke maʻalahi loa nā hōʻailona. ʻAʻole ʻike kekahi poʻe ua loaʻa iā lākou ke ʻano no nā makahiki.
Eia nā hōʻailona i ʻike ʻia ma ke ʻano laulā:
- Ke ʻūlū nei ma nā lehelehe, nā manamana lima, a me nā manamana wāwae.
- ʻŌpū ʻiʻo.Ke hoʻomanaʻo nei ʻoe i kekahi manawa he lauoho ma kou mau wāwae i ka pō? Nā mea e like me ia, akā inā hana pinepine ia, he hōʻailona paha ia o kēia nele i ka calcium.
- Nā ʻūmiʻi ʻiʻo (Tetany).
- ʻEha ʻōpū.
- ʻO ka "Brain fog" kahi kūlana kahi e paʻakikī ai iā ʻoe ke noʻonoʻo pono a manaʻo iki i ka huikau.
- Nā ʻano like ʻole o ka puʻuwai (Arrhythmia).
- Nā kui palupalu.
- Lauoho maloʻo a me ka ʻili maloʻo a unahi.
- ʻO ke ʻano o nā cataracts.
- Ka nāwaliwali o ka enamel niho i nā keiki.
Pehea e ʻike ai nā kauka i kēia maʻi?
Hoʻomaopopo pinepine ʻia a hōʻoia ʻia ka Hypoparathyroidism ke hōʻike nā hoʻokolohua he haʻahaʻa ka nui o ka calcium koko a me ka parathyroid hormone (PTH) o ke kanaka.
Ma muli o ka maʻalea loa o nā hōʻailona, ʻike pinepine nā kauka i kēia kūlana "ma ke ʻano ulia." ʻO ia hoʻi, hoʻomaka wale lākou e ʻimi iā ia ke ʻike lākou i ka calcium haʻahaʻa i loko o ke koko i ka wā o kahi hoʻāʻo koko maʻamau no kekahi kūlana ʻē aʻe.
Inā ua hōʻoia ʻia kahi kanaka he haʻahaʻa ka hormone PTH a me nā pae calcium i loko o ko lākou koko i ʻelua manawa i loko o ʻeono mahina, ua manaʻo ʻia he hypoparathyroidism mau loa .
He aha nā ʻano hoʻokolohua i hana ʻia no kēia?
Inā loaʻa iā ʻoe kēia mau hōʻailona, e hana kāu kauka i kahi hoʻokolokolo kino a nīnau e pili ana i kāu mau hōʻailona, ka mōʻaukala olakino ʻohana, a me nā lāʻau lapaʻau āu e lawe ai.
Eia kekahi, hiki ke hana ʻia hoʻokahi a ʻoi aku paha o nā hoʻokolohua aʻe:
- Hoʻāʻo koko no ka hormone parathyroid (PTH).
- Hoʻāʻo koko kalsiuma.
- Hoʻāʻo koko phosphorus.
- Hoʻāʻo koko magnesium.
- He hoʻāʻo mimi 24-hola: Ke ana kēia i ka nui o ka calcium i hoʻokuʻu ʻia i loko o ka mimi.
I kekahi manawa, hiki i kāu kauka ke kauoha i nā hoʻokolohua hou aʻe e nānā i nā hopena ʻaoʻao koʻikoʻi e hiki ke hana ʻia e kēia ʻano. Eia kekahi laʻana:
- Electrocardiogram (ECG a i ʻole EKG): Nānā i nā ʻano hewa o ka puʻuwai.
- ʻO ke kiʻi ʻikepili i helu ʻia (CT): Nānā i nā waihona calcium i loko o ka lolo (Brain Calcifications).
Pehea e mālama ʻia ai kēia?
ʻO ka pahuhopu nui o ka mālama ʻana no ka hypoparathyroidism ʻo ia ka hōʻemi ʻana i nā hōʻailona a hoʻihoʻi i nā pae o ka calcium a me nā minela ʻē aʻe i loko o kou kino i nā pae kūpono.
Hiki ke hana i kēia mau mea ma ke ʻano he lāʻau lapaʻau:
- Ke hāʻawi nei i nā mea hoʻopihapiha Calcium Carbonate a me Vitamin D:Pono ka nui o ka poʻe me ka hypoparathyroidism e lawe i nā pila calcium a me ka wikamina D a i ʻole nā wai no ke koena o ko lākou ola. ʻO kēia ka laina nui a me ka laina mua o ka lāʻau lapaʻau no kēia maʻi. He mea nui ka wikamina D no ko mākou kino e omo pono i ka calcium. No laila, inā loaʻa iā ʻoe ka hypoparathyroidism, pono ʻoe e lawe i kēia mau mea hoʻohui ʻelua.
- ʻO ka ʻai kiʻekiʻe i ka calcium a haʻahaʻa i ka phosphorus: Hiki i kāu kauka ke aʻo aku iā ʻoe e ʻai i nā meaʻai waiwai i ka calcium (waiū, tīhi, yogurt, nā mea kanu ʻōmaʻomaʻo) a hōʻemi i nā meaʻai kiʻekiʻe i ka phosphorus (nā ʻiʻo i hana ʻia, nā mea inu e like me ka cola). Eia nō naʻe, no ka mea he paʻakikī ke loaʻa ka calcium lawa mai ka meaʻai wale nō, pono paha ka lawe ʻana i nā mea hoʻohui.
- Nā inikini hormone parathyroid (PTH): Inā ʻaʻole hiki i nā mea hoʻopihapiha calcium a me ka vitamin D wale nō ke kaohi i kou kūlana, hiki i kāu kauka ke hoʻoholo e hāʻawi iā ʻoe i nā inikini hormone parathyroid (PTH).
Aia kekahi mau hopena ʻaoʻao o ka lāʻau lapaʻau?
ʻAe, i kekahi manawa inā kiʻekiʻe loa ka nui o ka wikamina D a me ka calcium i hāʻawi ʻia ma ke ʻano he lāʻau lapaʻau, hiki i ka pae calcium i loko o ke koko ke lilo i kiʻekiʻe loa. Ua kapa ʻia kēia he hypercalcemia . He mea ʻino nō hoʻi kēia i ke kino. No laila, pono ʻoe e loaʻa i nā hoʻāʻo koko maʻamau e ʻike ai inā e hana pono ana kāu lāʻau lapaʻau a pololei kāu pae calcium.
He liʻiliʻi loa ka pilikia o ka loaʻa ʻana o kahi ʻano maʻi ʻaʻai iwi i kapa ʻia ʻo osteosarcoma me ka hoʻohana lōʻihi ʻana i nā inikini hormone parathyroid (PTH). No laila, ʻōlelo nā kauka i kēia inikini i nā hihia koʻikoʻi loa, i ka wā ʻaʻole i holomua nā lāʻau ʻē aʻe.
He aha nā kumu pilikia no kēia maʻi?
Aia kekahi mau kumu e hoʻonui ai i ka pilikia o ka hoʻomohala ʻana i ka hypoparathyroidism:
- Ma hope o ka hana ʻana i ke ʻoki ʻāʻī a i ʻole ka thyroid.
- Ka moʻolelo ʻohana o nā maʻi kelepa parathyroid.
- Loaʻa kekahi mau maʻi autoimmune e hoʻopilikia i ka ʻōnaehana endocrine, e like me ka maʻi ʻo Addison.
He aha ka wānana o kēia kūlana?
Ma keʻano laulā, maikaʻi ka nānā ʻana no ka hypoparathyroidism, ʻoiai inā ʻike mua ʻia ke ʻano a hoʻomaka ʻia ka mālama kūpono.
Eia nō naʻe, inā hoʻoulu kēia ʻano i nā mea e like me ke cataracts, nā calcifications o ka lolo, a me nā loli niho, he paʻakikī ke hoʻohuli. No laila he mea nui ka ʻike mua ʻana.
Pehea ka lōʻihi o kēia kūlana?
ʻO ka hapa nui o ka manawa, he maʻi mau ka hypoparathyroidism, ʻo ia hoʻi he ola ia. Eia nō naʻe, hiki i ka hypoparathyroidism ke lilo i mea manawa pōkole ma muli o kekahi mau kumu (e.g., nele i ka magnesium, manawa pōkole ma hope o ke ʻoki ʻana).
He aha nā pilikia e hiki ke kū mai mai kēia?
Inā ʻaʻole mālama pono ʻia ka hypoparathyroidism, hiki ke loaʻa nā pilikia lōʻihi like ʻole:
- Nā pilikia hana puʻupaʻa.
- Nā pōhaku puʻupaʻa.
- Nā katarata.
- Nā waihona calcium ma nā wahi like ʻole o ka lolo.
ʻO kēia kūlana, ʻoi aku hoʻi i nā keiki, hiki ke hana i nā pilikia e like me:
- Ka ulu maikaʻi ʻole.
- Nā pilikia niho.
- Ka lohi o ka ulu ʻana o ka noʻonoʻo.
He mea nui loa ia e hoʻomaopopo inā e emi koke a koʻikoʻi ka pae calcium i loko o ke koko (Acute Hypocalcemia), inā ʻaʻole e mālama koke ʻia, hiki iā ia ke alakaʻi i nā kūlana hoʻoweliweli ola e like me nā hopu ʻana a me ka paʻakikī o ka hanu ʻana ma muli o nā spasms laryngeal . Inā ʻike ʻoe i kēia mau hōʻailona (e laʻa me ka ʻūlū nui o nā ʻiʻo, nā convulsions), pono ʻoe e hele koke i ka haukapila kokoke loa.
Āhea ʻoe e ʻike ai i ke kauka?
- Inā loaʻa iā ʻoe nā hōʻailona āu e manaʻo ai he hypoparathyroidism paha, e ʻike pono i ke kauka.
- Inā ua ʻike mua ʻia ʻoe me ka hypoparathyroidism, pono ʻoe e nānā i kou pae calcium koko i nā manawa maʻamau e like me ke kuhikuhi a kāu kauka e hōʻoia i ka loaʻa ʻana o ka lāʻau kūpono.
- E like me ka mea i ʻōlelo ʻia ma mua, inā ʻike ʻoe i nā hōʻailona o ka hypocalcemia koʻikoʻi, e like me ka ʻūlū koke ʻana o nā ʻiʻo a i ʻole nā hōʻailona hopu , e hele koke i ka haukapila kokoke loa.
Nā mea nui e pono ai ʻoe e hoʻomanaʻo (Leka Lawe-Home)
He maʻi laha ʻole ka Hypoparathyroidism, akā hiki ke mālama ʻia a mālama ʻia . Hiki i nā hōʻailona ke maʻalahi a paʻakikī ke ʻike. No laila, he mea nui e haʻi i kāu kauka inā he mau kumu pilikia kou no kēia maʻi (no ka laʻana, inā ua hana ʻia ʻoe i ke ʻoki ʻāʻī a inā paha he maʻi parathyroid kekahi o kou ʻohana).
Hiki i kekahi mau hoʻāʻo koko maʻalahi ke nānā i kāu hormone parathyroid (PTH) a me nā pae calcium. Inā ʻike mua ʻoe i kēia kūlana, hiki iā ʻoe ke hoʻomaka i ka lāʻau kūpono, pale i nā pilikia, a ola i kahi ola olakino. No laila, mai hopohopo, akā e makaʻala i kēia. Inā he mau hopohopo kāu, mai kānalua e kamaʻilio me kāu kauka.
ʻO ka Hypoparathyroidism, Hypoparathyroidism, Nā ʻōpū parathyroid, ka hormone parathyroid, PTH, Calcium, Hypocalcemia, Phosphorus, Vitamin D, Electrolytes, Nā hōʻailona, lāʻau lapaʻau











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