Ke ʻū mau nei a ʻūmiʻi paha kou mau ʻiʻo? He maʻi laha ʻole paha kēia i kapa ʻia ʻo Isaacs' Syndrome?

Ke manaʻo nei ʻoe i kekahi manawa e like me ka ʻūlū wale ʻana o kou mau ʻiʻo, a i ʻole e wili koke ana kou mau ʻiʻo a ʻūmiʻi? He mea maʻamau kēia mau hōʻailona i waena o nā pākeke. ʻO ka hapa nui o ka manawa, ʻaʻole lākou he mea koʻikoʻi. Eia naʻe, he mea kakaikahi loa, hiki i kēia mau hōʻailona ke lilo i hōʻailona o kahi maʻi neurological koʻikoʻi. ʻO kekahi maʻi kakaikahi a mākou e kamaʻilio ai i kēia lā ʻo ia ka maʻi ʻo Isaacs.

He aha ka Isaacs' Syndrome? E hoʻomaopopo maʻalahi kākou!

ʻAe, e nānā kākou i ke ʻano o kēia. He maʻi neuromuscular kakaʻikahi loa ka maʻi ʻo Isaacs. ʻO ka mea e hana ʻia ma kēia, ʻo ia ka hoʻoulu nui ʻia ʻana o nā aʻalolo i loko o ka ʻōnaehana aʻalolo peripheral o ko kākou kino. E noʻonoʻo e like me ke kuapo uila e hoʻā a pio mau ʻia, hoʻāla ʻia hoʻi ko kākou mau aʻalolo me ka pono ʻole. Hoʻomaka kēia i nā ʻiʻo e hana aunoa, me ka ʻole o kā mākou kaohi.

Hoʻomaʻamaʻa pinepine ke kanaka me kēia maʻi i nā ʻūmiʻi ʻiʻo, nā ʻūmiʻi, a me ka ʻūmiʻi. I kekahi manawa hiki i kēia ke hoʻopilikia i kā mākou ʻōnaehana nerve autonomic. Hiki i kēia ke hana i nā mea e like me ka hoʻonui ʻia o ka hou ʻana a me nā loli i ka helu o ka puʻuwai.

Ua kapa ʻia hoʻi kēia:

• ʻO ka maʻi hana fiber muscle hoʻomau
• ʻO ka maʻi ʻo Isaacs-Mertens
• ʻO ka neuromyotonia
• ʻO ka maʻi squander Quantal

Pehea ka maʻamau o ka Isaacs' Syndrome?

ʻO ka ʻoiaʻiʻo, he maʻi laha loa kēia. ʻAʻole hiki i nā kānaka ʻepekema ke ʻōlelo pololei i ka nui o ka poʻe i loaʻa iā ia, no ka mea, a hiki i kēia manawa, he mau haneli wale nō nā hihia i hōʻike ʻia ma ka honua holoʻokoʻa.

Eia nō naʻe, e like me ka mea i ʻōlelo ʻia ma mua, ʻo ka ʻūlū ʻana o nā ʻiʻo a me ka ʻūlū ʻana o nā ʻiʻo (i kekahi manawa i kapa ʻia ʻo fasciculations ) he mea maʻamau loa ia i nā pākeke. ʻAʻole lākou he mea weliweli. No laila, mai makaʻu e manaʻo he maʻi neurological koʻikoʻi ʻo Isaacs' syndrome no ka mea he hoʻokahi kāu. He nui ka poʻe i loaʻa kēia mau hōʻailona no nā kumu ʻē aʻe a maʻalahi hoʻi.

ʻO wai ka mea hiki ke loaʻa i ka Isaacs' Syndrome?

Hoʻomaka pinepine ka maʻi ʻo Isaacs ma waena o nā makahiki 15 a me 60. Eia nō naʻe, ua hōʻike ʻia ke ʻano i nā poʻe ʻōpio, i kekahi manawa ʻoiai nā pēpē.

Hiki ke pili kēia maʻi me kekahi mau maʻi olakino ʻē aʻe. ʻO ke ʻano kēia, ʻoi aku ka nui o ka loaʻa ʻana o ia maʻi i ka poʻe me kēlā mau maʻi. Eia kekahi mau laʻana:

• Ka maʻi ʻaʻai
• Maʻi Celiac
• ʻO ka polyneuropathy demyelinating inflammatory mau loa (CIDP) - He maʻi aʻalolo kēia.
• ʻO ka maʻi Guillain-Barré
• ʻO ka maʻi o Hashimoto
• Lupus
• ʻO ka maʻi ʻaʻai
• ʻO ka neuropathy peripheral
• ʻO ka ʻāʻī rheumatoid
• Thymoma - He maʻi ʻaʻai kēia e ulu ana i loko o ka ʻōpū thymus.
• Ka nele o ka wikamina B12

He aha nā kumu o kēia ʻano i kapa ʻia ʻo neuromyotonia?

Hiki i ʻelua mau kumu nui no kēia:

1. Loaʻa: He maʻi autoimmune kēia. I ka ʻōlelo maʻalahi, hoʻomaka ka ʻōnaehana pale o ko mākou kino e hoʻouka i kā mākou mau hunaola olakino ponoʻī me he mea lā he poʻe komo hewa lākou. Ma kahi o 50% o ka poʻe me ka maʻi ʻo Isaacs he mau antibodies e hoʻouka i nā kahawai e ʻae ai i ka electrolyte potassium e komo a haʻalele i ko mākou mau aʻalolo. Hoʻopilikia kēia neʻe ʻana o ka potassium i ka hana aʻalolo. Ke hōʻino ʻia kēia mau kahawai, hoʻoulu nui ʻia nā aʻalolo.

2. Kūlana hoʻoilina: He ʻano hoʻoilina kēia. ʻO ia hoʻi, ua hoʻoilina ʻia mai nā mākua a i nā keiki.

He aha nā hōʻailona o ka Isaacs' Syndrome?

ʻO ka maʻamau, mau kēia mau hōʻailona i ka lā a hiki ke loaʻa i ka wā e hiamoe ana. ʻO ka hapa nui, ʻike nui ʻia nā hōʻailona o ka ʻeha ʻiʻo ma nā lima a me nā wāwae. Eia nō naʻe, hiki iā ia ke hoʻopilikia i nā ʻāpana ʻē aʻe o ke kino.

Eia kekahi o nā hōʻailona nui:

• Ataxia: ʻO ke ʻano kēia o ka nalowale ʻana o ke kaulike a me ka hoʻonohonoho ʻana o ke kino i ka wā e hele ana a neʻe paha. Hiki iā ʻoe ke luliluli e like me ka mea ʻona.
• Ka manawa e pono ai e wehe i kahi puʻupuʻu: Ke paʻa kahi puʻupuʻu, lōʻihi ka manawa e hoʻi ai i ka maʻamau.
• Ka hou nui ʻana (hyperhidrosis): Ka hou nui ʻana me ke kumu ʻole.
• Nā loli i ka helu o ka puʻuwai: Hiki ke wikiwiki a lohi paha ka puʻuwai.
• Luhi a me ka hiamoe ʻole: Manaʻo luhi mau i nā manawa a pau a ʻaʻole hiki ke hiamoe i ka pō.
• ʻŌwili ʻana o ka ʻiʻo, ʻūmiʻi ʻana, ʻūmiʻi ʻana, a nāwaliwali ʻana: Hoʻonui mālie kēia mau mea i ka hala ʻana o ka manawa.
• ʻO Myokymia: He manaʻo kēia o nā ʻiʻo e hoʻomau nei i ka ʻūlū ʻana, ka ʻūlū ʻana, a i ʻole ka ʻūlū ʻana. Ua wehewehe kekahi poʻe iā ia me he "e like me nā ilo e kolo ana ma lalo o ka ʻili."
• Paʻakikī ke ʻōlelo a hanu paha inā pilikia nā tonsils ma ka puʻu.

E noʻonoʻo, ʻoiai ʻoe e kū mālie ana, e ʻoni mau ana kahi puʻu ʻiʻo i loko o kou lima a i ʻole kou wāwae, me he mea lā e ʻoni ana kekahi mea i loko. Pehea ka hoʻonāukiuki inā ʻaʻole e pau kēia ʻoiai ʻoe e hiamoe ana i ka pō? ʻO ia ke ʻano o ka myokymia.

Pehea e ʻike ʻia ai ka maʻi ʻo Isaacs?

Hiki i kāu kauka ke kauoha i kekahi mau hoʻokolohua e hōʻoia i ka maʻi ʻo Isaacs a kāpae i nā kūlana ʻē aʻe. ʻO kekahi o kēia mau mea:

• Nā hoʻāʻo koko: Kōkua kēia i ka ʻike ʻana i nā ʻano antibodies kikoʻī i loko o ke koko o ka hapalua o ka poʻe me ka maʻi ʻo Isaacs.
• Nā haʻawina hoʻoili aʻalolo a me nā electromyograms (EMG): Ana kēia mau hoʻokolohua i ke ʻano o ka hana ʻana o kou mau ʻiʻo a me nā aʻalolo, e like me ka mea uila e nānā ana i ke au i loko o kahi uea.
• Nā haʻawina kiʻi e like me ka CT scan a i ʻole MRI scan: Hiki i kēia ke nānā i loko o ke kino e ʻike inā he mau pilikia ʻē aʻe.

I kekahi manawa, hiki ke huikau ʻia ka maʻi ʻo Isaacs me nā kūlana ʻē aʻe e like me ka stiff person syndrome , rippling muscle syndrome , a i ʻole cramp-fasciculation syndrome, no laila he mea nui ka loaʻa ʻana o ka ʻike pololei.

Pehea e mālama ʻia ai ka Isaacs' Syndrome?

ʻAʻohe lāʻau lapaʻau no kēia maʻi i kēia manawa. ʻO ke kumu nui o ka lāʻau lapaʻau ʻana, ʻo ia ke kāohi ʻana i kou mau hōʻailona a kōkua iā ʻoe e hana maikaʻi loa.

Inā pili ka maʻi ʻo Isaacs me kahi maʻi autoimmune ʻē aʻe a i ʻole ka maʻi ʻino, he mea nui hoʻi e mālama i ke kūlana kumu.

Hiki i kāu kauka ke ʻōlelo i kēia mau lāʻau lapaʻau no ka maʻi ʻo Isaacs:

• Nā lāʻau lapaʻau anticonvulsant: No ka laʻana, nā lāʻau lapaʻau e like me phenytoin a me carbamazepine. Hoʻemi kēia i nā ʻūmiʻi ʻiʻo, nā haʻalulu, a me ka ʻeha.
• Nā lāʻau lapaʻau immunosuppressive: Hana nā lāʻau lapaʻau e like me ka azathioprine a me methotrexate ma ke kaohi ʻana i ka ʻōnaehana pale mai ka hana kūpono ʻole.
• ʻO ka immunoglobulin intravenous (IVIG): Pili kēia i ka hāʻawi ʻana i kahi hopena e loaʻa ana nā antibodies mai nā mea hāʻawi olakino i loko o ke kino ma o kahi aa koko.
• ʻO nā corticosteroids waha: No ka laʻana, prednisolone.
• Hoʻololi plasma:He ʻano hana kēia no ke kānana ʻana i nā mea ʻawahia a me kēlā mau antibodies ʻino mai ke koko o ka poʻe i loaʻa nā antibodies kūpono ʻole.

Hiki ke pale ʻia ka Isaacs' Syndrome?

ʻOiai ʻaʻole maopopo loa i nā kānaka ʻepekema ke kumu o kēia, ʻaʻohe ala e pale aku ai i kēia manawa.

He aha ka manaʻolana no nā poʻe me ka neuromyotonia?

ʻOkoʻa ke ʻano o ka nānā ʻana no kekahi me ka maʻi ʻo Isaacs. Aia ia i ke koʻikoʻi o ka maʻi, ke kumu kumu, pehea ka holomua o ka mālama ʻana, a me nā kūlana olakino ʻē aʻe e pili ana.

ʻOi aku ka ʻino o nā hōʻailona neuromyotonia i ka hala ʻana o ka manawa. Hiki iā lākou ke kaupalena nui i ka neʻe ʻana a hoʻopilikia i nā hana o kēlā me kēia lā.

ʻO ke ʻano kēia, ʻo ka mea i ʻike mua ʻia he ʻūmiʻi ʻiʻo liʻiliʻi hiki ke lilo i mea koʻikoʻi loa a hiki ʻole ke hele. No laila, he mea nui e ʻike mua i ka maʻi a hoʻomaka i ka lāʻau lapaʻau.

ʻOiai ʻaʻohe lāʻau lapaʻau piha i kēia manawa, ʻaʻole maʻamau ka make o kēia maʻi.

He aha kaʻu e hana ai e ola maikaʻi ai me ka Isaacs' Syndrome?

Hiki ke paʻakikī ke noho me kēia ʻano, akā ua loaʻa i kekahi poʻe ka holomua i ka hoʻokele ʻana i nā hopena kino a me ka noʻonoʻo ma o ka hana ʻana i kēia mau mea:

• Ke kākoʻo nei i nā poʻe me nā maʻi neuromuscular: ke komo ʻana i nā papahana hoʻomaopopo a me ke aʻo ʻana i nā poʻe ʻē aʻe e pili ana i kēia.
• Ke hele ʻana i nā hālāwai kūkā: Hiki iā ʻoe ke aʻo i nā hoʻolālā e pono ai e hoʻoponopono i kēia kūlana ma ka noʻonoʻo.
• Ke pili ʻana me nā poʻe ʻē aʻe i kahi kūlana like: ʻOi loa aku ma o ka pāpili kaiapili. He ikaika nui ia e manaʻo ai ʻaʻole ʻoe hoʻokahi.
• Ke noʻonoʻo nei.
• Ke hoʻomaʻamaʻa nei i ka yoga.
• Ke hele wāwae nei: He mea nui e noho ikaika kino e like me ka hiki.

He aha hou aʻe kaʻu e hiki ai ke nīnau aku i kaʻu kauka e pili ana i ka Isaacs' Syndrome?

Inā ua ʻike ʻia ʻoe me ka neuromyotonia a i ʻole ka maʻi ʻo Isaacs, e nīnau pono i kāu kauka i kēia mau nīnau:

• No ke aha i loaʻa ai iaʻu ka maʻi ʻo Isaacs?
• He mau pilikia olakino ʻē aʻe koʻu e pili ana i kēia?
• Pehea lā mākou e ʻike pono ai ʻo Isaacs' syndrome kēia a ʻaʻole he maʻi neuromuscular ʻē aʻe e like me ALS (Amyotrophic Lateral Sclerosis)?
• He aha nā wahi o koʻu kino e hoʻopilikia ʻia e kēia?
• He aha nā lāʻau lapaʻau āu e paipai nei?
• Ua kūpono anei au no kekahi mau hoʻokolohua lapaʻau?
• E kōkua mai anei ka hoʻōla kino a i ʻole ka hoʻōla hana iaʻu?
• Hiki iā ʻoe ke kuhikuhi iaʻu i kahi kākā'ōlelo a i ʻole hui kākoʻo e kōkua iaʻu e hoʻoponopono i kēia kūlana?
• Pono anei kekahi o koʻu ʻohana e hoʻāʻo ʻia no ka maʻi ʻo Isaacs?

ʻO ka mea hope loa, nā mea e hoʻomanaʻo ai (Leka Lawe-Home)

He maʻi neuromuscular kakaʻikahi ka maʻi ʻo Isaacs e hoʻoulu ai i nā aʻalolo a me nā ʻiʻo e lilo i mea hana nui. Inā ua ʻike ʻia ʻoe me kēia maʻi, mai hopohopo, akā e kamaʻilio me kāu kauka. Hiki iā ia ke nānā i nā kūlana pili ʻē aʻe a kōkua iā ʻoe e hoʻokele i nā hōʻailona e like me ka ʻūlū ʻana o nā ʻiʻo a me ka ʻoʻoleʻa. E hoʻomanaʻo, me ka mālama kūpono a me ke kākoʻo, hiki iā ʻoe ke ola i kahi ola maikaʻi me kēia maʻi.

ʻO ka maʻi ʻo Isaacs , neuromyotonia, ʻeha ʻiʻo, ʻūlū ʻana o nā ʻiʻo, maʻi neurological