Ua ʻike anei ʻoe i kekahi e hoʻomaka koke ana e ʻai i nā mea ʻaʻole ia he meaʻai, a i ʻole e loli koke kā lākou ʻano moekolohe, a i ʻole ʻaʻole lākou e ʻike i kā lākou poʻe aloha? He mau hōʻailona kakaikahi loa kēia, akā hiki iā lākou ke loaʻa ka hopena nui i ke ola o ke kanaka. I kēia lā e kamaʻilio mākou e pili ana i kahi ʻano ʻē, akā he mea nui loa ke ʻano o ka maʻi.
I ka ʻōlelo maʻalahi, he maʻi lolo laha ʻole ʻo Klüver-Bucy Syndrome (KBS). ʻO nā hōʻailona nui ka nalowale o ka hoʻomanaʻo a me nā loli nui o ke ʻano. Hiki i kekahi poʻe ke hoʻomohala i ka makemake e ʻai i nā mea ʻaʻole meaʻai, e like me nā ʻāpana plastik a me ka lepo. Hiki i kekahi ke loaʻa i kahi makemake moe kolohe kiʻekiʻe loa. I nā hihia koʻikoʻi, hiki iā ia ke alakaʻi i nā hopu ʻana a i ʻole ka dementia.
I kēia manawa, e nānā kākou pehea e hana ai kēia. ʻElua ʻāpana o ko kākou lolo i kapa ʻia ʻo nā lobes temporal , e like me nā ʻaoʻao o ko kākou pepeiao. Kōkua kēia mau lobes temporal iā kākou e hana i nā hoʻomanaʻo hou, e kāohi i kā kākou ʻai ʻana a me nā ʻano moekolohe, a e hana i ka ʻike mai ko kākou mau manaʻo a me nā ʻike. E noʻonoʻo e pili ana i ia mea, ke aʻo ʻoe i kahi mea hou, ke ʻike ʻoe i ka meaʻai a makemake ʻoe e ʻai, a i ʻole ke manaʻo ʻoe i ke aloha a i ʻole ka huhū no kekahi, ke hana nei kēia mau lobes temporal. Hana ʻia ʻo Klüver-Bucy Syndrome (KBS) i ka wā e hōʻino ʻia ai nā lobes temporal ʻelua o ka lolo. Hoʻomaka pinepine kēia mau hōʻailona ma hope o kahi ʻeha o ka lolo a i ʻole kekahi ʻano olakino ʻē aʻe e hōʻino ana i nā lobes temporal ʻelua. Hiki iā ia ke hoʻopilikia i nā kānaka o kēlā me kēia makahiki, ʻoiai nā keiki ʻōpio loa.
Akā, hoʻokahi mea e hoʻomanaʻo ai, ʻaʻohe lāʻau lapaʻau piha no kēia maʻi KBS. Eia nō naʻe, hiki ke kāohi ʻia nā hōʻailona me ka lāʻau kūpono . No laila, he mea nui loa ka ʻike mua ʻana i ka maʻi.
He aha nā hōʻailona o ka maʻi ʻo Klüver-Bucy (KBS)?
Hiki i ka Klüver-Bucy Syndrome (KBS) ke hana i nā ʻano hōʻailona like ʻole. Hoʻololi ka nui o nā hōʻailona i ke ʻano o kou noʻonoʻo ʻana i ka meaʻai a i ʻole ke ʻano o kou manaʻo e pili ana i ke kau ʻana i nā mea i loko o kou waha. Eia kekahi mau laʻana:
- ʻAi nui ʻana a laila luaʻi (bulimia nervosa) .
- Makemake pinepine e ʻai, ʻai kāohi ʻole ʻia (hyperphagia) .
- Hoʻoikaika pinepine ʻia e puhi a inu paha i ka waiʻona.
- ʻO ka makemake e ʻai i nā mea hiki ʻole ke ʻai ʻia, e like me ka lepo, nā pōhaku, a i ʻole nā lau (pica) . He mea weliweli loa kēia, ʻeā? E noʻonoʻo i kahi keiki liʻiliʻi e hoʻāʻo nei e ʻai i kahi mea pāʻani.
- Ke hoʻokomo pinepine ʻana i nā mea i loko o ka waha, a i ʻole ka palu ʻana i nā mea me ke kūpono ʻole (hyperorality) .
Loaʻa i ka poʻe me ka Klüver-Bucy Syndrome (KBS) ka 'hypersexuality'He mea maʻamau nō hoʻi ke ʻano i kapa ʻia ʻo hypersexuality. ʻO ia hoʻi, he makemake nui ko lākou i ka moekolohe. Manaʻo lākou i ka pono e moe pinepine a ʻoi aku paha ma mua o ka maʻamau. Hiki i kahi keiki ʻōpio me KBS ke hana i nā mea e like me ka hoʻopā ʻana i ko lākou mau ʻōpū, hamo iā lākou, a i ʻole e hoʻoneʻe i ko lākou mau ʻūhā i mua a i hope. Inā ʻike mākou i kahi mea e like me kēia, he mea nui iā mākou ma ke ʻano he mau mākua ke hopohopo ʻole a ʻimi i ke aʻo lapaʻau.
Aia kekahi mau hōʻailona ʻē aʻe o ka Klüver-Bucy Syndrome (KBS), e hoʻopilikia ana i ka hana o ko mākou lolo (hana cognitive). ʻO ia hoʻi, nā mea e like me ka noʻonoʻo a me ka hoʻomanaʻo. Hiki paha iā ʻoe ke ʻike i nā mea e like me:
- Ka nalowale o ka hoʻomanaʻo (amnesia) .
- Ka maʻi ʻōpū .
- Ka hoʻohuli ʻia.
- ʻO ka hiki ʻole ke manaʻo i nā manaʻo e like me ka huhū a me ka makaʻu. E noʻonoʻo, inā ʻike ʻoe i kahi mea weliweli, ʻaʻole ʻoe e manaʻo i ka makaʻu.
- ʻO ka agnosia ʻike maka ka hiki ʻole ke ʻike i nā poʻe kamaʻāina a i ʻole nā mea kamaʻāina, ʻoiai inā kamaʻāina lākou iā ʻoe. Ua like ia me ka ʻike ʻana i kekahi o kou ʻohana ponoʻī a ke noʻonoʻo nei, "ʻO wai kēia?"
- Nā ʻōʻili.
No ke aha i loaʻa ai ka maʻi ʻo Klüver-Bucy (KBS)?
ʻO ke kumu nui o ka Klüver-Bucy Syndrome (KBS), e like me kaʻu i ʻōlelo ai ma mua, ʻo ia ka hōʻino ʻia ʻana o nā ʻāpana ʻelua o ko kākou lolo i kapa ʻia ʻo 'temporal lobes'. Kāhea nā kauka i kēia ʻo 'bilateral temporal lobe damage' . ʻO ia hoʻi, ka hōʻino ʻia ʻana o nā lobes temporal ʻākau a me ka hema o ka lolo. ʻOi aku hoʻi, inā ua hōʻino ʻia ka ʻāpana o kēia mau lobes temporal i kapa ʻia ʻo 'hippocampus' , e pili ana i ka hoʻomanaʻo, a me ka ʻāpana o kēia mau lobes temporal i kapa ʻia ʻo 'amygdala', e pili ana i ka kaohi ʻana i nā manaʻo, ʻoi aku ka kiʻekiʻe o ka manawa e loaʻa ai ʻo KBS.
Aia kekahi mau kumu nui no kēia pōʻino:
- ʻEha lolo traumatic (TBI): E noʻonoʻo i kahi ʻeha poʻo nui i loko o kahi ulia kaʻa.
- Hahau: Hana ʻia e ke kahe koko i ka lolo.
- Nā maʻi e hoʻopilikia ana i ka lolo:
- ʻO ka maʻi lolo (encephalitis) i hoʻokumu ʻia e ka maʻi herpes simplex.
- ʻO ka maʻi puʻupuʻu e hoʻopilikia ana i ka lolo.
- Nā maʻi o ka lolo a me nā meninges, e like me ka meningoencephalitis .
- Nā kūlana olakino ʻē aʻe:
- ʻO ka maʻi o Alzheimer .
- ʻO ka maʻi o Huntington .
- ʻO ka maʻi o Pick .
- ʻO ka maʻi o Whipple .
I kekahi manawa hoʻohana nā kauka i nā inoa ʻē aʻe no Klüver-Bucy Syndrome (KBS), ma muli o ke kumu. Eia kekahi laʻana:
- Ma muli o ka hōʻino ʻia ʻana o nā lobes temporal ʻelua (Bilateral temporal lobe disorder) .
- Ma hope o ka maʻi lolo (Post-encephalitic Klüver-Bucy syndrome) .
- Ma hope o ka ʻeha o ka lolo (Post-traumatic Klüver-Bucy syndrome) .
He aha nā pilikia e hiki mai ana o ka Klüver-Bucy Syndrome (KBS)?
Hiki i ke kanaka me ka Klüver-Bucy Syndrome (KBS) ke hoʻowalewale ʻia e hana i nā mea a lākou e hana ʻole ai. Hiki i kekahi o kēia mau hana ke lilo i mea weliweli loa . E nānā kākou i kekahi mau laʻana:
- ʻO ke kūlana 'pica' aʻu i ʻōlelo ai ma mua ke kumu e kau ai nā kānaka a ʻai i nā mea pono ʻole lākou e ʻai. Hoʻokomo kēia iā lākou i ka pilikia o ka lāʻau make a i ʻole nā pilikia weliweli ʻē aʻe mai ka ʻai ʻana i nā mea pono ʻole lākou e ʻai . E noʻonoʻo wale i ke ʻano o nā pilikia e kū mai inā ʻoe e ʻai i kahi mea e like me ka pila a i ʻole kahi ʻāpana pena.
- ʻO nā maʻi ʻai e like me ka bulimia nervosa hiki ke hōʻeha i ke kino a hiki ke hoʻoweliweli i ke ola.
- Hiki i ka moekolohe nui ke alakaʻi i ka moekolohe palekana ʻole a i ʻole ka hana antisocial. Hiki i kēia ke alakaʻi i nā maʻi i laha ma ke kolohe a i ʻole nā pilikia pilikanaka ʻē aʻe.
No laila, inā ʻike ʻoe i kēia mau hōʻailona i loko o kekahi āu i ʻike ai, ʻo ka mea maikaʻi loa e hana ai, ʻaʻole ia e hilahila a makaʻu paha, akā e ʻimi koke i ke kōkua lapaʻau. A laila hiki iā ʻoe ke pale aku i ia mau pilikia weliweli.
Pehea e ʻike ʻia ai ka maʻi ʻo Klüver-Bucy (KBS)?
E ʻike paha ʻoe i nā loli hou a ʻano ʻē i kāu ʻano ponoʻī, a i ʻole i ke ʻano o kāu keiki. A i ʻole, ke hele ʻoe e ʻike i ke kauka, e ʻike paha ke kauka i kekahi o kēia mau hōʻailona.
Inā ʻike ʻoe i kahi makemake hou a ʻokoʻa paha a i ʻole kahi loli o ke ʻano, mai hilahila a makaʻu paha e haʻi i kāu kauka . ʻO ka mea nui loa, ʻo ia ke kamaʻilio me kāu kauka e pili ana i kāu mea e ʻike nei. ʻO ka wikiwiki o kou kamaʻilio ʻana me ke kauka, ʻo ka nui o kou pale ʻana i nā pilikia weliweli.
E hana ke kauka i kahi hoʻokolokolo kino e hoʻoholo ai inā loaʻa iā ʻoe ʻo Klüver-Bucy Syndrome (KBS), a hiki iā ia ke kauoha i kekahi mau hoʻokolohua ʻē aʻe. ʻO kekahi o kēia mau mea:
- Nā hoʻāʻo koko.
- ʻO ke kiʻi CT .
- Hoʻāʻo EEG (Electroencephalogram - EEG) - Ke ana kēia i ka hana uila o ka lolo.
- ʻO ke kiʻi MRI (MRI) .
He aha nā lāʻau lapaʻau no ka Klüver-Bucy Syndrome (KBS)?
E ʻōlelo aku kāu kauka i nā lāʻau lapaʻau e hiki ke kōkua i ka kaohi ʻana i nā hōʻailona āu e ʻike nei. ʻOkoʻa ke ʻano o ka lāʻau lapaʻau āu e pono ai mai kēlā kanaka a i kēia kanaka. Ma muli o nā hōʻailona āu e loaʻa ai a me ke koʻikoʻi o lākou.
ʻO nā lāʻau lapaʻau no ka Klüver-Bucy Syndrome (KBS) e komo pū paha me:
- Nā lāʻau hoʻēmi kaumaha .
- Nā lāʻau antipsychotic .
- Nā lāʻau lapaʻau antiseizure .
- Inā loaʻa kēia maʻi i kahi maʻi viral, ua kuhikuhi ʻia nā lāʻau antiviral .
- Nā lāʻau lapaʻau e like me Carbamazepine a i ʻole Leuprolide e kāohi i nā pilikia o ka moekolohe.
- Nā mea hoʻopaʻa manaʻo .
- Inā makemake ʻoe i ke kōkua me nā hana o kēlā me kēia lā, e noʻonoʻo i nā lāʻau lapaʻau e like me ka occupational therapy .
Hiki i kāu kauka ke kōkua iā ʻoe e ʻike i nā koho lapaʻau maikaʻi loa e hōʻemi i ka hopena o nā hōʻailona KBS i kou ola o kēlā me kēia lā. ʻAʻohe lāʻau lapaʻau no ka Klüver-Bucy Syndrome (KBS) , ʻoiai ʻaʻole hiki ke hoʻohuli ʻia ka pōʻino i ka lolo e hoʻokumu ai. Eia nō naʻe, hiki iā ʻoe ke loaʻa ke kōkua e hoʻokele i kāu mau hōʻailona a ola i kahi ola maʻamau.
Inā loaʻa iaʻu ʻo Klüver-Bucy Syndrome (KBS), he aha kaʻu e manaʻo ai?
Pono ʻoe e manaʻo e mālama i nā hōʻailona o Klüver-Bucy Syndrome (KBS) no ka manawa lōʻihi, malia paha no ke koena o kou ola .
ʻO ka nui o ka hopena o KBS iā ʻoe e pili ana i kekahi mau kumu:
- He aha ke kumu o kēia kūlana?
- Ke koʻikoʻi o ka pōʻino i ka lolo.
- ʻEhia ke kōkua āu e loaʻa ai i ka kaohi ʻana i kāu mau hōʻailona mai nā lāʻau lapaʻau a me nā lāʻau lapaʻau ʻē aʻe.
E kōkua kāu kauka iā ʻoe e hoʻonohonoho i nā pahuhopu a me nā mea i manaʻo ʻia.
Āhea wau e ʻike ai i ke kauka?
Inā loaʻa iā ʻoe kekahi mau hōʻailona hou a i ʻole nā loli i kāu mau hōʻailona, e kamaʻilio koke me kāu kauka . Inā manaʻo ʻoe ua nalowale kou mana a kānalua paha i kāu mea e hana nei, e haʻi i kāu kauka. Hiki paha iā lākou ke hoʻololi i kāu hoʻolālā lapaʻau.
Makemake paha ʻoe e ʻike i kahi loea olakino noʻonoʻo , e like me ke kauka noʻonoʻo a i ʻole ke kākāʻōlelo. Hiki iā lākou ke kōkua iā ʻoe e kamaʻilio ma o kou mau manaʻo a me nā manaʻo a kōkua iā ʻoe e hoʻomaopopo iā lākou. Hiki iā lākou ke kōkua iā ʻoe e ʻimi i nā ala e hoʻokele ai i nā hōʻailona e like me ka pica a me ka hypersexuality ma ke ʻano palekana a olakino hoʻi.
He aha nā nīnau e pono iaʻu e nīnau aku i kaʻu kauka?
Hiki iā ʻoe ke nīnau i ke kauka i nā nīnau e like me kēia:
- He aha ke kumu i loaʻa ai iaʻu ka Klüver-Bucy Syndrome (KBS)?
- He aha nā lāʻau lapaʻau maikaʻi loa noʻu? Pehea e hoʻohana ai ia mau mea?
- ʻEhia pinepine e pono ai iaʻu e ʻike i ke kauka a loaʻa nā hoʻokolohua?
- Aia kekahi mau hōʻailona a i ʻole nā loli e pono iaʻu e makaʻala nui?
ʻO ka mea hope loa, he aha e hoʻomanaʻo ai
Hiki i ka Klüver-Bucy Syndrome (KBS) ke hoʻoikaika iā ʻoe e noʻonoʻo a hana i nā mea āu e noʻonoʻo ʻole ai a hana paha. Akā e hoʻomanaʻo, ʻo ʻoe nō ʻoe . Inā ʻike ʻoe i kēia mau loli i kāu ʻano a i ʻole kou noʻonoʻo ʻana, he mea nui e ʻike koke i ke kauka.
Hiki i kāu kauka ke kōkua iā ʻoe e hoʻomaopopo i ke kumu o kēia mau loli i kāu ʻano, a kōkua iā ʻoe e hoʻokele i kēia mau hōʻailona a manaʻo hou e like me ʻoe iho. Mai manaʻo mehameha, a mai makaʻu e noi i ke kōkua.
ʻO ka maʻi Klüver-Bucy, nā maʻi lolo, nā loli o ke ʻano, ka nalowale o ka hoʻomanaʻo, ka lobe temporal, pica, ka moekolohe nui











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