Ua noʻonoʻo paha ʻoe i ka mea e hiki mai ana inā pau ka hana pono ʻana o nā keʻena liʻiliʻi i loko o kou puʻuwai? I kekahi manawa, lilo ko kākou mau ʻiʻo puʻuwai i mea paʻakikī a ʻaʻole hiki ke hoʻopiha pono i ke koko. ʻO ia ka manawa e hiki ai iā kākou ke hoʻomohala i ka mea a kākou e kamaʻilio ai: restrictive cardiomyopathy. Mai hopohopo, e mālama kākou i ka maʻalahi.
He aha ka Cardiomyopathy Restrictive?
I ka ʻōlelo maʻalahi, he ʻano kēia e pili ana i ka ʻiʻo puʻuwai. ʻO nā ʻiʻo i loko o nā keʻena ʻelua ma lalo o ko kākou puʻuwai, i kapa ʻia ʻo nā ventricles , lilo i ʻoʻoleʻa. ʻAʻole ia e like me kahi kaula laholio e hoʻihoʻi ana i kona wahi ke kīkoʻo ʻoe, akā ʻaʻole e pelu pono nā ʻiʻo. ʻO ke ʻano kēia, ʻaʻole lawa ka lumi o kēia mau keʻena e hoʻopiha pono ai me ke koko. Ke hana ʻia kēia, e pilikia ke kahe ʻana o ke koko ma o ka puʻuwai.
Aia kekahi mau inoa ʻē aʻe no kēia, a i kekahi manawa hoʻohana paha nā kauka i kēia mau inoa:
- ʻO ka cardiomyopathy hoʻopaʻa idiopathic
- ʻO ka cardiomyopathy infiltrative (maʻi ʻiʻo puʻuwai i hoʻokumu ʻia e ke komo ʻana o nā mea ʻē aʻe i loko o ka ʻiʻo)
ʻO wai ka mea i loaʻa pinepine i kēia maʻi? Pehea ka maʻamau?
ʻOiai hiki i kekahi ke loaʻa i kēia maʻi, ʻo ia hoʻi, ʻoi aku ka maʻamau i kekahi poʻe ma muli o kekahi mau maʻi kumu. No ka laʻana, ʻoi aku ka maʻamau o ka maʻi ʻo "Sarcoidosis" (hiki ke hana i ka maʻi "(Restrictive Cardiomyopathy)") i nā wahine o kekahi mau lāhui.
He maʻi maʻamau ka Cardiomyopathy. Hoʻopilikia ia ma kahi o 1 i loko o 500 mau kānaka. Eia nō naʻe, ʻo kēia ʻano cardiomyopathy ka mea kakaikahi loa . He 5% ia o nā hihia āpau o ka cardiomyopathy. No laila, he mea kēia i lohe pinepine ʻole ʻia, akā he mea pono ke ʻike.
Pehea ka hopena o ka cardiomyopathy restrictive i ka puʻuwai?
He ʻōkana kupaianaha ko kākou puʻuwai. He ʻehā ona keʻena, i hana ʻia me nā ʻiʻo. Hoʻopuka kēia mau keʻena i ke koko ma o ka ʻaelike ʻana. Ua kapa ʻia nā keʻena ʻelua o luna he 'Atria' , a ua kapa ʻia nā keʻena ʻelua o lalo he 'Ventricles' .
ʻO ka mea e hana ʻia ma kēia kūlana `(Restrictive Cardiomyopathy)` ʻo ia ka lilo ʻana o nā ʻiʻo o nā keʻena haʻahaʻa (`Ventricles`) i mea paʻakikī a nalowale ko lākou elasticity. A laila ʻaʻole hiki i kēlā mau keʻena ke hoʻopiha piha me ke koko. E noʻonoʻo e like me ka hoʻopiha ʻana i kahi pōpō, inā ʻaʻole i hoʻopiha pono ʻia ka pōpō, e paʻa wale ia i kahi ea liʻiliʻi. ʻO ia ka mea e hana ʻia ma ʻaneʻi. Hoʻopilikia kēia i ke kaʻina holoʻokoʻa o ke kahe ʻana o ke koko ma o ka puʻuwai.
He aha nā hōʻailona? Hiki ke ʻike koke ʻia?
I kekahi manawa ʻaʻohe hōʻailona , ʻoiai i nā pae mua. Akā i ka holomua ʻana o ka maʻi, hiki ke loaʻa ka hāʻule ʻana o ka puʻuwai.Hoʻomaka ka ʻike ʻia ʻana o nā hōʻailona like me nā hōʻailona o ka maʻi palū. Eia kekahi o kēlā mau hōʻailona:
- ʻŌpū piha a nausea paha.
- ʻEha umauma (hiki ke loaʻa i ka wā hoʻomaha a i ka wā hoʻoikaika kino paha).
- Ka poniuniu a i ʻole ka māʻule ʻana.
- Ka pehu ʻana o nā wāwae a me nā wāwae ('Edema').
- Luhi mau ka manaʻo ('Fatigue').
- Ke manaʻo nei i kahi puʻuwai puʻuwai ʻē aʻe ('Heart palpitations').
- Paʻakikī ka hanu ʻana (Dyspnea), i kekahi manawa me ka hoʻoikaika māmā.
- Piʻi koke ke kaumaha.
He mea nui: Inā loaʻa iā ʻoe kekahi a ʻoi aku paha o kēia mau hōʻailona, mai manaʻo he 'Restrictive Cardiomyopathy' ia. Eia nō naʻe, ʻoi aku ka maikaʻi o ke kipa ʻana i ke kauka no ka ʻōlelo aʻo.
No ke aha i kū ai kēia kūlana? He aha nā kumu?
Aia kekahi mau kumu nui o ka cardiomyopathy restrictive. ʻO ia hoʻi, hiki ke hana ʻia e nā kūlana olakino ʻē aʻe.
- ʻAmyloidosis : ʻO kēia ka wā e waiho ʻia ai kahi protein i loko o ka ʻiʻo o ka puʻuwai.
- Nā maʻi pili pili : Nā maʻi e hoʻopilikia ana i nā ʻiʻo like ʻole o ke kino.
- Hemochromatosis (hao nui) : Ka hōʻiliʻili nui ʻana o ka hao i loko o ke kino.
- ʻO Sarcoidosis : ʻO ka hoʻokumu ʻia ʻana o nā puʻupuʻu liʻiliʻi o nā cell i kapa ʻia he granulomas ma nā ʻano ʻāpana like ʻole o ke kino.
Eia kekahi, aia kahi hiki ke hana ʻia kēia ʻano ma hope o kekahi mau lāʻau lapaʻau no ka maʻi kanesa:
- Kemoterapia
- Hoʻōla radiation
Pehea e ʻike pololei ai nā kauka i kēia maʻi? (Diagnosis)
Ke hele ʻoe e ʻike i ke kauka, e nīnau mua ʻo ia iā ʻoe e pili ana i kāu mau hōʻailona, e hana i kahi hoʻokolokolo kino, e hoʻolohe i kou puʻuwai, a e nānā i kou koko.
A laila, no ka hōʻoia ʻana i ka maʻi a me ka ʻike ʻana inā e hana pono ana nā keʻena puʻuwai (ventricles), hana ʻia kahi echocardiogram (heart scan). Hiki i kēia ke nānā i nā mea e like me ka hana o ka puʻuwai a me ka mānoanoa o nā ʻiʻo.
Hiki i kāu kauka ke paipai i kekahi mau hoʻokolohua ʻē aʻe e nānā i nā kūlana kumu ʻē aʻe e hiki ai ke hoʻoulu i ka Restrictive Cardiomyopathy. ʻO kēia mau mea:
- Nā hoʻāʻo koko a me ka mimi.
- X-ray umauma.
- ʻO ke kiʻi ʻana o ka puʻuwai (ʻO ke kiʻi ʻana o ka CT scan o ka puʻuwai).
- Hoʻāʻo hoʻoluhi kino.
- MRI o ka puʻuwai.
- Nānā PET o ka puʻuwai.
- Ke kālai ʻana o ka puʻuwai ʻākau.
- ʻO ka biopsy myocardial - ʻO kēia ka lawe ʻana i kahi hāpana liʻiliʻi o ka ʻiʻo puʻuwai a hoʻāʻo iā ia.
- Ka hoʻāʻo ʻana i ka hoʻoilina.
Aia kekahi lāʻau lapaʻau? Pehea e mālama ʻia ai?
ʻO ka mea pōʻino, ʻo kēia ʻano, i kapa ʻia ʻo 'Restrictive Cardiomyopathy', he mea kūikawā ia no kēia ʻano.ʻAʻohe lāʻau lapaʻau i kēia manawa. Eia nō naʻe, hiki i nā kauka ke mālama i ke kumu kumu a kaohi i nā hōʻailona.
Inā loaʻa iā ʻoe nā hōʻailona e pili ana i ka hāʻule ʻana o ka puʻuwai, hiki i kāu kauka ke ʻōlelo i nā lāʻau lapaʻau penei:
- ʻO Corticosteroids (nā lāʻau lapaʻau ʻano steroid) inā loaʻa iā ʻoe ka sarcoidosis.
- ʻO nā diuretics (nā lāʻau lapaʻau e hoʻonui ai i ka mimi) e hōʻemi i ke kahe nui o ke koko i loko o ke kino.
- Nā lāʻau lapaʻau e mālama ai i nā ʻano ʻino o ka puʻuwai (e like me 'Antiarrhythmics', 'Beta-blockers' a i ʻole 'Calcium channel blockers').
- ʻO ka phlebotomy therapeutic kahi lāʻau lapaʻau no ka poʻe me ka hemochromatosis (iron overload).
- Nā lāʻau lapaʻau kūikawā no kekahi mau ʻano `(Amyloidosis)`.
Pono paha kekahi poʻe i kahi ʻoki hoʻoili puʻuwai ke lilo ka maʻi i mea koʻikoʻi. Hiki ke kuhikuhi ʻia lākou no ka mālama palliative e kāohi i nā hōʻailona a mālama i kahi ola maikaʻi.
He aha nā pilikia e hiki mai ana o kēia maʻi?
Hiki ke loaʻa kekahi mau pilikia ʻē aʻe ma muli o ka 'Restrictive Cardiomyopathy'. Eia kēia mau mea:
- ʻArrhythmia o ka puʻuwai : He puʻuwai kūpono ʻole.
- Ka hāʻule ʻana o ka puʻuwai : ʻAʻole hiki i ka puʻuwai ke pamu i ke koko kūpono i ke kino.
- ʻO nā ʻūpā koko a me ka hahau ʻana ('Thromboembolism' a i ʻole 'Stroke') : Hiki i kahi ʻūpā koko ke hana i ka hahau ʻana.
He aha kā mākou e hana ai e hōʻemi i ka pilikia?
ʻO kēia kūlana, ʻo "Restrictive Cardiomyopathy," ʻo ia hoʻi, pono kou puʻuwai e hana ikaika e pamu i ke koko. No laila, he mea nui e kamaʻilio me kāu kauka e pili ana i kāu mea hiki ke hana e hōʻemi i ka ukana hana ma kou puʻuwai.
ʻOiai he paʻakikī ke pale aku i nā kūlana olakino kumu e hoʻoulu ai i ka Restrictive Cardiomyopathy, hiki iā ʻoe ke hana i kēia mau mea e mālama ai i kou puʻuwai olakino:
- E kāohi i kou koko .
- E mālama i ke kaumaha olakino .
- E hōʻemi i ke kaumaha .
He aha kāu e manaʻo ai i ka wā e noho ai me kēia maʻi?
He maʻi paʻakikī ka Restrictive Cardiomyopathy, no laila he mea nui e kamaʻilio pinepine me kāu kauka e pili ana i nā hana e hiki ai iā ʻoe ke hana e mālama i ke olakino o kou puʻuwai.
ʻOkoʻa ka lōʻihi o kou ola ʻana me kēia maʻi mai kēlā kanaka a kēia kanaka. E wehewehe kāu kauka iā ʻoe a me kou ʻohana pehea e holomua ai ka maʻi a me nā mea e manaʻo ʻia.
Pehea e mālama ai iaʻu iho? (Mālama ponoʻī)
ʻO ka mea nui loa, ʻo ia ke hahai pono i nā kuhikuhi a kāu kauka a lawe i nā lāʻau lapaʻau āpau i kuhikuhi ʻia i ka manawa kūpono. Eia kekahi, hiki i kāu kauka ke haʻi aku iā ʻoe e hana i nā hoʻololi i ke ʻano o ka nohona e like me:
- He ʻai olakino haʻahaʻa i ka paʻakai (sodium-controlled)E lawe.
- Hoʻoikaika kino (e like me ka ʻōlelo a kāu kauka).
Āhea ʻoe e ʻimi koke ai i ke aʻo lapaʻau?
Inā manaʻo ʻoe e ʻoi aku ka ʻino o nā hōʻailona o ka hāʻule ʻana o kou puʻuwai, a inā paha e loaʻa iā ʻoe nā hōʻailona hou, e kāhea koke aku i kāu kauka .
Eia kekahi, i ka wā e loaʻa ai kahi pilikia e like me kēia, e hele koke i ka haukapila (inā ma Sri Lanka, e kelepona i kahi helu pilikia e like me 1990):
- Inā loaʻa iā ʻoe ka ʻeha nui o ka umauma .
- Inā ʻoe e hiolo .
- Inā loaʻa koke iā ʻoe ka pilikia nui o ka hanu ʻana .
E hoʻomanaʻo: He ʻōkana koʻikoʻi ka puʻuwai i ko kākou ola, no laila he mea nui loa ka mālama ʻana iā ia.
Leka Lawe-Home
ʻAe, eia kekahi mau mea maʻalahi e hoʻomanaʻo e pili ana i ka `(Restrictive Cardiomyopathy)` a mākou i kamaʻilio ai:
- ʻO ka mea e hana ʻia ana ma kēia, ʻo ia ka lilo ʻana o nā ʻiʻo i loko o nā keʻena haʻahaʻa (ventricles) o ka puʻuwai i ʻoʻoleʻa a nalowale ko lākou palupalu .
- No laila, ʻaʻole hiki i kēlā mau hunaola ke hoʻopiha pono i ke koko .
- A laila, pono ka puʻuwai e hana ikaika e pamu i ke koko i ke kino, kahi e hiki ai ke hana i ka "Puʻuwai hāʻule".
- ʻOiai ʻaʻohe lāʻau lapaʻau kūikawā no kēia, mālama ʻia ia ma ka mālama ʻana i ke kumu kumu a me ka kaohi ʻana i nā hōʻailona .
- Inā he mau nīnau a kānalua paha kāu e pili ana i kēia, mai makaʻu e kamaʻilio me kāu kauka .
Ke makemake nei iā ʻoe i ke olakino maikaʻi!
ʻO ka Cardiomyopathy Restrictive, maʻi puʻuwai, maʻi ʻiʻo puʻuwai, pōkole o ka hanu, ʻeha umauma, hōʻeha puʻuwai, lapaʻau











💬 Comments (0)
ʻAʻohe manaʻo i kau ʻia. Hoʻohui i kāu manaʻo ma ʻaneʻi no ka manawa mua.
Hoʻohui i kāu manaʻo