Manaʻo paha ʻoe i kekahi manawa he ʻeha kou ʻōpū a i ʻole he manaʻo piha me ke kumu ʻole? Manaʻo pinepine mākou he pilikia kinoea a he pilikia hoʻoheheʻe liʻiliʻi paha, ʻeā? Akā i kekahi manawa, aia paha kekahi kūlana ma hope o kēia ʻaʻole mākou e kamaʻilio nui e pili ana a he inoa ʻē iki kona. I kēia lā e kamaʻilio mākou e pili ana i kekahi kūlana kakaʻikahi akā koʻikoʻi loa e ʻike ai. ʻO ia ka Sclerosing Mesenteritis.
I ka ʻōlelo maʻalahi, he aha ka Sclerosing Mesenteritis?
He mea weliweli paha kēia inoa, akā e wāwahi kākou a hoʻomaopopo maʻalahi.
E noʻonoʻo ʻaʻole e lana wale ana nā ʻōpū i loko o ko kākou ʻōpū ma ʻō a ma ʻaneʻi, ʻeā? Aia kahi membrane e kōkua ana e mālama iā lākou i ke ʻano a ma kahi hoʻokahi. I ka pololei, ua hoʻopili ʻia ko kākou mau ʻōpū i ka paia hope o ka ʻōpū e kēia membrane. I ka lāʻau lapaʻau, kapa mākou i kēia membrane ʻo ka mesentery . Aia kekahi papa o ka momona (ʻiʻo adipose) i loko o kēia mesentery.
I kēia manawa, e nānā, ʻo "Mesenteritis" e pili ana i ka mumū o ka mesentery. ʻO ia hoʻi ke ʻano o ka pehu ʻana. ʻO ka huaʻōlelo "sclerosing" ʻo ia hoʻi kahi mea e mānoanoa ana, a i ʻole ka hoʻokumu ʻana o nā ʻiʻo ʻeha a mānoanoa. E like me ka wā e loaʻa ai kahi ʻeha ma ko mākou ʻili, ma hope o kona ho'ōla ʻana, mānoanoa iki ka ʻili a koe kahi ʻeha. ʻO kēia ka mea a mākou e kapa nei he fibrosis .
ʻO ka Sclerosing Mesenteritis kahi kūlana e mānoanoa mālie ai ka mesentery, ka membrane e paʻa ana i ko kākou ʻōpū, a hana i nā ʻiʻo ʻeha ma muli o ka mumū lōʻihi.
Ke mānoanoa ka mesentery ma kēia ʻano, hiki ke ʻano like me kahi puʻupuʻu ma kahi scan. No laila he mea nui e ʻike pono i ke ʻano o ia mea.
He maʻi mau anei kēia?
ʻAe, ʻoiaʻiʻo nō. No ka mea, no ka loaʻa ʻana o ka ʻōpala āu i ʻōlelo ai a hiki i ke kahua o ka sclerosis, pono e hoʻomau ka mumū no ka manawa lōʻihi. ʻAʻole hana ʻia kēia i ka manawa hoʻokahi. Aia kekahi mau pae i kēia.
1. ʻO ka mea mua, hoʻomaka ka ʻiʻo momona i loko o ka mesentery e wāwahi mālie.
2. A laila, hōʻea nā ʻano pūnaewele like ʻole i kēlā wahi a hoʻomaka e hōʻuluʻulu.
3. Hoʻomaka ka hana ʻana o nā ʻiʻo ʻeha i ka hopena.
No laila, he maʻi lōʻihi a holomua ka Sclerosing Mesenteritis. Akā, hoʻokahi mea maikaʻi e ʻōlelo ai ma ʻaneʻi. ʻAʻole ia e lilo i mea ʻino mau. I ka hapanui o nā hihia, hiki ke hoʻomaikaʻi iā ia iho, me ka ʻole o ka lāʻau lapaʻau. No laila, mai makaʻu e lohe i ka inoa.
Ua kapa ʻia anei kēia he Mesenteric Panniculitis?
Ua lohe paha ʻoe i kēia inoa. Mesenteric PanniculitisPili ia i ka mumū o ka ʻiʻo momona (panniculus) ma ka mesentery. I ka ʻōlelo maʻalahi, manaʻo ka nui o nā kauka he maʻi like nā kūlana ʻelua. No ka mea, ʻaʻohe kumu kikoʻī no nā mea ʻelua, he mau mumū idiopathic lākou.
Eia nō naʻe, manaʻo kekahi mau kauka e hoʻohana ʻia ka inoa ʻo Sclerosing Mesenteritis no ke kahua ʻoi aku ka ʻino a me ka ʻeha o ka maʻi. ʻO Mesenteric Panniculitis e pili ana i ke kahua mua o ka mumū, ma mua o ka hoʻomaka ʻana o ka ʻeha e hana. Eia nō naʻe, ua manaʻo ʻia kēia mau mea ʻelua he mau kahua like ʻole o ka maʻi like.
ʻO wai ka mea i loaʻa pinepine i kēia maʻi?
ʻO ka mea mua, he maʻi laha ʻole ka Sclerosing Mesenteritis. Hoʻopilikia ia i kahi poʻe liʻiliʻi loa, ma kahi o 0.6% o ka heluna kanaka. No laila, mai makaʻu nui iā ia.
Wahi a nā ʻikepili i loaʻa, ʻike pinepine ʻia kēia maʻi ma:
- Ma waena o nā kānaka ma luna o 50 mau makahiki .
- Inā loaʻa i kekahi o ka ʻohana nā maʻi autoimmune .
- Wahi a kekahi mau noiʻi, ma kahi o 60% o ka poʻe i ʻike ʻia me kēia maʻi i loaʻa a i loaʻa paha i nā maʻi kanesa ʻē aʻe. Ua hōʻike ʻia e pili ana i kahi ʻano maʻi kanesa i kapa ʻia ʻo lymphoma .
| ʻAno | Wehewehena |
|---|---|
| Kakaikahi | He kūlana maʻamau ʻole ia. |
| Makahiki i hoʻopilikia ʻia | Hoʻopilikia pinepine ia i nā kānaka ma luna o 50 mau makahiki. |
| Nā Hoʻokaʻaʻike ʻē aʻe | Hōʻike i nā loulou me nā maʻi autoimmune a me kekahi mau maʻi kanesa (ʻoi aku ka lymphoma). |
No laila, he maʻi ʻaʻai anei kēia? He nīnau e hopohopo nei i nā poʻe he nui!
ʻAʻole. ʻAʻole maʻi kanesa ka Sclerosing Mesenteritis.
ʻO kēia ka mea nui loa āu e hoʻomanaʻo ai. ʻAʻole kēia he maʻi kanesa. Eia nō naʻe, hiki ke pili pū me ke kanesa a i kekahi manawa e like me ke kanesa ma nā scans. E hoʻomaopopo kākou i kēlā.
ʻO nā hunaola kanesa kahi ʻano hunaola e hiki ke māhelehele, ulu, a laha me ke kāohi ʻole ʻia ma ke kino holoʻokoʻa. Eia nō naʻe, ʻaʻole māhelehele a laha ka ʻiʻo ʻeha i hana ʻia ma ka sclerosing mesenteritis ma kēia ʻano. Eia nō naʻe, i ka wā e hōʻiliʻili ai a mānoanoa ka ʻiʻo ʻeha, hiki ke like me ka puʻupuʻu ma kahi scan. Eia kekahi, hiki i kēia mau hōʻailona ke like me kekahi mau hōʻailona kanesa.
No kēia mau kumu, pono i ke kauka ke hana i kekahi mau hoʻokolohua e hoʻokaʻawale pololei ma waena o kēia mau kūlana ʻelua.
He aha nā hōʻailona o kēia maʻi?
ʻO ka mea kupanaha ma ʻaneʻi, ʻaʻohe o ka poʻe he nui i loaʻa i kekahi mau hōʻailona . ʻIke pinepine ʻia ia i ka wā o kahi scan i hana ʻia no kekahi kumu ʻē aʻe.
Eia nō naʻe, inā loaʻa nā hōʻailona, ʻo ka mea maʻamau:
- ʻEha ʻōpū: He manaʻo mau o ka ʻeha iki a i ʻole ka ʻoluʻolu ʻole i loko o ka ʻōpū.
- Pehu: Manaʻo o ka pehu a me ka pehu.
- Ka maʻi kahe a i ʻole ke kuni: Hiki ke ʻike ʻia kēia mau hōʻailona inā koʻikoʻi ka mumū.
- Ke manaʻo nei i kahi puʻu i loko o ka ʻōpū: I kekahi manawa, ke manaʻo ʻoe i ka ʻōpū mai waho mai, hiki i ka ʻāpana mānoanoa ke manaʻo e like me kahi puʻu.
- Ka luaʻi, ka luaʻi ʻana, a me ka pohō kaumaha: He mea kākaʻikahi loa, hiki i kēia ʻiʻo mānoanoa ke ālai i ka ʻōpū liʻiliʻi. ʻO kēia ka manawa e ʻike ʻia ai nā hōʻailona e like me ka luaʻi ʻana, ka luaʻi ʻana, a me ka pohō kaumaha.
No ke aha e loaʻa ai kēia ʻano maʻi? He aha ke kumu?
ʻO kaʻoiaʻiʻo, ʻaʻole i loaʻa ke kumu kikoʻī o kēia , akā ʻo ka manaʻo nui o nā kauka he maʻi autoimmune paha ia.
I ka ʻōlelo maʻalahi, ʻo ka hana a ko kākou ʻōnaehana pale kino, ʻo ia ke kaua aku i nā germs e hoʻoulu ai i nā maʻi. Akā i loko o kahi maʻi autoimmune, hoʻomaka hewa ko kākou ʻōnaehana pale kino ponoʻī e hoʻouka i ko kākou mau ʻiʻo olakino ponoʻī. Hoʻoulu kēia hoʻouka i ka mumū mau loa.
He nui ka poʻe i loaʻa i ka sclerosing mesenteritis he moʻolelo ʻohana o nā maʻi autoimmune ʻē aʻe. Ua manaʻoʻiʻo ʻia hoʻi hiki ke hoʻoulu ʻia ke ʻano e ke kaumaha kino, e like me ke ʻoki kino, ka maʻi, a i ʻole ke kanesa.
Pehea e ʻike ai ke kauka i kēia maʻi? (Diagnosis)
Ma hope o ka hoʻolohe ʻana i kāu mau hōʻailona, inā kānalua ke kauka i kēia maʻi, e kuhikuhi ʻo ia iā ʻoe no kekahi mau hoʻokolohua.
1. Nā scan (kiʻi)
- ʻO ke scan Ultrasound: He hoʻāʻo wikiwiki a maʻalahi kēia e hiki ke hana ʻia e ʻike i nā hōʻailona mua.
- CT scan a i ʻole MRI scan: He mau hoʻokolohua koʻikoʻi kēia. Hiki i kēia mau scan ke hōʻike i nā mea e like me ka mānoanoa o ka mesentery a me nā ʻiʻo scar me ka maopopo loa.
- ʻIke PET: I kekahi manawa he mea paʻakikī ke ʻike mai kahi ʻike CT a MRI paha inā he Sclerosing Mesenteritis a i ʻole ke kanesa. I ia mau hihia, hiki i kahi ʻike PET ke kōkua. Maanei, ua hoʻokomo ʻia kahi mea radioactive i loko o ke kino. ʻOiai ʻoi aku ka omo ʻana o nā hunaola kanesa i kēia mea ma mua o nā hunaola maʻamau, hiki ke ʻike maopopo ʻia inā he kanesa.
2. Biopsy
Inā ʻaʻole i maopopo nā hoʻokolohua i luna, ʻo ka hoʻokolohua hope loa he biopsy. Ma kēia, lawe ʻia kahi ʻāpana liʻiliʻi loa o ka ʻiʻo mai ka ʻāpana mānoanoa o ka mesentery a nānā ʻia ma lalo o kahi microscope. Lawe pinepine ʻia kēia laʻana ʻiʻo ma ke komo ʻana i kahi nila lahilahi ma o ka ʻōpū. I kekahi poʻe, pono paha e lawe ʻia kēia laʻana ma o kahi hana liʻiliʻi, e like me ka laparoscopy.
He aha nā lāʻau lapaʻau no kēia?
ʻO ka nūhou maikaʻi, ʻaʻole pono ka hapa nui o ka poʻe i kekahi lāʻau lapaʻau . Hoʻopau pinepine kēia maʻi iā ia iho. Inā ʻaʻohe ou hōʻailona, a i ʻole ke ʻike nei ʻoe i ka ʻoluʻolu iki wale nō, e ʻōlelo paha kāu kauka ʻaʻole ʻoe e lawe i kekahi lāʻau lapaʻau a kali wale.
Eia nō naʻe, inā hoʻomau nā hōʻailona a hoʻopilikia paha i kou ola o kēlā me kēia lā, aia kekahi mau lāʻau lapaʻau e kuhikuhi ai kāu kauka.
- ʻO nā Corticosteroids: No ka laʻana, ʻo Prednisone. Hoʻomalu kēia i ka mumū i loko o ke kino.
- Nā lāʻau pale kino: No ka laʻana, azathioprine. Hana kēia mau mea ma ka hōʻemi ʻana i ka hana o ka ʻōnaehana pale kino e hana hewa ana.
- Hoʻōla Hormonal: Hoʻohana ʻia nā lāʻau lapaʻau e like me Tamoxifen i kekahi manawa.
ʻO ka mea nui loa, ʻo ia ka mea e hoʻoholo wale ʻia ai kēia lāʻau e ke kauka nāna ʻoe e nānā. Mai hoʻōla ponoʻī ma muli o ka lohe.
Hiki ke hoʻomalu ʻia kēia kūlana me ka meaʻai a me ka mea inu?
ʻO ka hahai ʻana i kahi papaʻai anti-inflammatory hiki ke kōkua i ka hōʻemi ʻana i ka mumū i loko o ke kino, ʻoi aku hoʻi i ka ʻōnaehana hoʻoheheʻe. ʻAʻole paha kēia e ho'ōla loa i ka Sclerosing Mesenteritis , akā hiki iā ia ke kōkua i ka kaohi ʻana i nā hōʻailona i kekahi ʻano.
I ka ʻōlelo maʻalahi, ʻo ka papaʻai anti-inflammatory:
- Ke hoʻoikaika nei i nā meaʻai hou a kūlohelohe (nā meaʻai holoʻokoʻa) ma kahi o nā meaʻai i hoʻopili ʻia a hana ʻia.
- ʻAi ʻana i nā meaʻai hou aku i loaʻa nā momona olakino, unsaturated (e.g., omega-3).
- E hoʻohui i nā mea kanu hou, nā huaʻai, a me nā mea kanu i kāu meaʻai.
He mea maikaʻi ke kamaʻilio me kāu kauka e pili ana i kēia a, inā pono, e ʻimi i ka ʻōlelo aʻo a ke kauka meaʻai.
Leka Lawe-Home
- He maʻi mumū laha ʻole ka Sclerosing Mesenteritis e kū mai ana ma ka mesentery, ka membrane e hoʻopaʻa pū ana i nā ʻōpū. Hiki i kēia ke hoʻomānoanoa i nā ʻiʻo a me ka ʻeha.
- ʻAʻole kēia he maʻi kanesa , akā hiki ke nānā aku e like me kahi puʻupuʻu ma nā kiʻi a pili pū me ka maʻi kanesa.
- ʻAʻole ʻike ka nui o ka poʻe i kekahi mau hōʻailona. Hiki i nā hōʻailona ke komo pū me ka ʻeha o ka ʻōpū a me ka pehu ʻana.
- I ka manawa pinepine , hoʻōla wale kēia maʻi me ka ʻole o ka lāʻau lapaʻau . Inā pono, e kuhikuhi ke kauka i ka lāʻau lapaʻau.
- Inā ua lōʻihi kou ʻike ʻana i kēia mau hōʻailona, mai makaʻu a hopohopo paha no ia mea, akā e ʻike i ke kauka kūpono a e kiʻi i nā ʻōlelo aʻoaʻo a me nā hoʻokolohua e pono ai.











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