He mea kupanaha anei kekahi e pili ana i kou mau kīʻaha koko? E aʻo kākou e pili ana i kēia mau mea (Vascular Malformations)?

Aia kekahi mau wahi o kou ʻili i loli ke kala, e like me nā puʻupuʻu liʻiliʻi, a i kekahi manawa ʻeha? A i ʻole he wahi ʻē ma kou kino i hānau ʻia ai kāu pēpē, akā me he mea lā e ulu nui ana? He mau mea maʻalahi paha kēia. Eia naʻe, i kekahi manawa he mau hōʻailona kēia o kahi kūlana ʻē i kapa ʻia ʻo Vascular Malformations , ʻo ia hoʻi nā ʻano ʻē i loko o nā kīʻaha koko, a i ʻole, nā kīʻaha koko. No laila, mai hopohopo. E kamaʻilio kākou e pili ana i kēia me nā kikoʻī a me ka maʻalahi i kēia lā.

He aha nā malformations vascular? I ka ʻōlelo maʻalahi...

ʻO nā malformations vascular he mau mea ʻē aʻe a i ʻole nā ​​loli i loko o nā kīʻaha koko i loko o ko kākou kino. He mea hānau pinepine kēia. Eia nō naʻe, i kekahi manawa e ʻike ʻia lākou i ka wā kamaliʻi, ʻōpio, a i ʻole ka wā makua.

E noʻonoʻo i ka ʻōnaehana aʻa koko e holo ana ma loko o ko kākou kino e like me kahi pūnaewele o nā alanui. I kekahi manawa, i ke kūkulu ʻia ʻana o kēia mau alanui, hiki ke loaʻa nā hemahema liʻiliʻi a me nā pilina hewa. Pēlā nō hoʻi ka mea e hana ʻia ma ʻaneʻi.

Hiki i kēia mau malformations vascular ke loaʻa ma nā wahi āpau o kou kino, mai kou poʻo a i kou mau manamana wāwae. I kekahi manawa ʻike ʻia lākou ma ke ʻano he puʻupuʻu palupalu , ʻeha , pehu , a i ʻole ka hoʻololi ʻana o ka ʻili . ʻIke ʻia kekahi ma ka maka, ka ʻāʻī, kokoke i ka lolo, a i ʻole ke kaula kuamoʻo. ʻIke ʻia kekahi e like me nā māka hānau a i ʻole nā ​​​​kiko ʻulaʻula.

He mea kākaʻikahi loa, hiki iā lākou ke hoʻi hou ma hope o kahi trauma a i ʻole kekahi hanana ʻē aʻe, a i ʻole i ka wā makua. Inā hōʻeha lākou, hoʻopilikia i ka ʻike, hoʻopilikia i nā hana o kēlā me kēia lā, kahe ke koko, a i ʻole ke kumu o nā pilikia ʻē aʻe, pono e mālama ʻia kēia mau malformations vascular.

Ma hea ma ke kino e loaʻa pinepine ai kēia mau mea?

ʻO ke ʻano o ka huaʻōlelo "vascular" ʻo ia hoʻi "pili i nā kīʻaha koko." No laila hiki i kēia kūlana ke hoʻopilikia i kekahi kīʻaha koko i loko o kā mākou ʻōnaehana hoʻopuni koko. Hiki iā ia ke hoʻopilikia i nā kīʻaha lymphatic i loko o kā mākou ʻōnaehana lymphatic.

ʻO nā ʻano o nā kīʻaha koko e hiki ke hoʻopilikia ʻia:

• Nā aʻa a me nā arterioles - ʻO kēia nā kīʻaha koko e lawe i ke koko i piha i ka oxygen mai ka puʻuwai i nā ʻōpū ʻē aʻe.
• Nā Capillaries - He pūnaewele o nā kīʻaha koko maikaʻi loa.
• Nā aa koko a me nā venule - ʻO kēia nā mea e hoʻihoʻi i ke koko i hoʻohana ʻia mai nā ʻōpū i ka puʻuwai.
• Nā kahawai lymphatic- Hoʻoili kēia i ka wai lymph i loko o ke kino.

He aha nā ʻano nui o nā malformations vascular?

Hiki i kēia mau kūlana ke ʻike ʻia i kekahi manawa ma ke ʻano he mau māka hānau ma ka ʻili o kahi pēpē. A i ʻole, e like me ka mea i ʻōlelo ʻia ma mua, hiki iā lākou ke ulu ma nā wahi āpau o ke kino, me ka lolo a me ke kaula iwi kuamoʻo. Hoʻoholo nā kauka i ke ʻano ma muli o ke ʻano o ke kīʻaha koko i hoʻopilikia ʻia.

Eia kekahi o nā ʻano i ʻike pinepine ʻia:

• ʻO ka maʻi ʻaʻai: ʻO kēia ke ʻano maʻamau. E like me ka inoa e hōʻike nei, ulu ia i loko o kahi aʻa. ʻO nā aʻa nā kīʻaha koko i loko o ko mākou kino e lawe ana i ke koko nele i ka oxygen i ka puʻuwai. Hiki ke like kēia me kahi puʻupuʻu polū, a i kekahi manawa he ʻeha ke hoʻopā.
• ʻO ka maʻi Arteriovenous (AVM): He hui ʻano ʻē kēia o nā aʻa a me nā veins. ʻO ka maʻamau, pau nā aʻa i nā capillaries, a laila hoʻomaka nā veins. Akā i loko o kahi AVM, kahe pololei ke koko mai nā aʻa i loko o nā veins, ma o kahi puʻupuʻu ʻano ʻē o nā kahawai i kapa ʻia he nidus . Hiki i kēia kūlana AVM ke hoʻopilikia i ka lolo a i ʻole ke kaula spinal.
• ʻO ka telangiectasia capillary: He wahi liʻiliʻi kēia o ka hoʻonui ʻia ʻana o nā capillaries i loko o ka lolo. ʻO ka hapa nui o ka manawa, ʻaʻole ia he pilikia. Eia naʻe, he mea kakaikahi loa, hiki iā lākou ke hoʻoulu i ke kahe koko , ʻo ia hoʻi ke kahe koko.
• Nā malformations Cavernous: Ma kēia ʻano, ua paʻa pono nā capillaries i loko o ka lolo, e hana ana i nā "caverns" lōʻihi. Ke kahe mālie nei ke koko ma o kēia mau ana.
• Nā malformations lymphatic: Ma kēia, lilo nā ducts lymphatic i hoʻonui ʻia a hana i nā cysts piha i ka wai. ʻIke pinepine ʻia kēia mau mea ma nā ʻiʻo palupalu e like me ka maka, ka ʻāʻī, a me nā ʻāpana axillary.

He aha ka ʻokoʻa ma waena o nā hemangioma a me nā malformations vascular?

Hoʻokumu ʻia nā mea ʻelua e nā ʻano ʻē o ke koko. Hiki ke ʻike ʻia nā mea ʻelua e like me nā kiko, e like me nā māka hānau. Akā, aia nā ʻokoʻa maopopo ma waena o nā mea ʻelua.

• Hemangioma: He mau puʻupuʻu vascular ʻaʻole cancerous (benign). Hoʻokumu ʻia lākou i ka wā e hui pū ai nā kīʻaha koko ma lalo o ka ʻili. ʻO ke ʻano i kapa ʻia ʻo "strawberry hemangiomas" e ʻike pinepine ʻia ma hope o ka hānau ʻana o kahi pēpē. Ulu koke lākou i nā mahina ʻeono mua o ka pēpē. Eia nō naʻe, ʻaʻole pinepine kēia mau puʻupuʻu e hoʻopilikia a hele pinepine iā lākou iho me ka ʻole o ka mālama ʻana. Inā nui ka hemangioma, hoʻopilikia i kekahi mau hana, hoʻoulu i ka ʻeha, a i ʻole ke kumu o nā pilikia ʻē aʻe, hiki ke kāohi ʻia me ka lāʻau lapaʻau e hoʻemi koke ai. ʻAʻole pono pinepine ke ʻoki ʻana.

• Nā ʻano kīnā o ke koko:He mau mea kēia e kū nei i ka wā hānau, akā ʻaʻole paha e ʻike ʻia a hiki i ka wā kamaliʻi a i ʻole ka wā makua. Ulu mālie lākou. Eia kekahi, hiki iā lākou ke pālahalaha hohonu i loko o nā ʻiʻo a me nā hale a puni a hoʻoulu i nā pilikia. Pono pinepine ka mālama ʻana i nā malformations vascular.

I ka ʻōlelo maʻalahi: He puʻupuʻu maikaʻi ʻole ʻo Hemangioma e nalo pinepine ana iā ia iho. Eia nō naʻe, ʻo nā malformations vascular he mau kūlana mau e hiki ke ulu a hoʻoulu i nā pilikia. No laila he mea nui e hoʻokaʻawale ma waena o nā mea ʻelua.

He aha nā malformations vascular kahe lohi a me ke kahe wikiwiki?

Hāʻule ka nui o nā malformations vascular i loko o ka māhele "kahe lohi" . ʻO ke ʻano kēia, neʻe mālie loa ke koko ma o nā kīʻaha koko i hoʻopilikia ʻia. ʻO nā hiʻohiʻona o kēia he venous, lymphatic, a i ʻole nā ​​​​malformations ʻelua (venolymphatic).

Eia nō naʻe, ʻo ka AVM (Arteriovenous malformation) he "fast-flow" vascular malformation. Ma kēia, kahe ke koko mai nā aʻa i nā veins ma ka wikiwiki kiʻekiʻe, maʻamau ma o kahi kīʻaha koko ʻē i kapa ʻia ʻo nidus . Ke hele wikiwiki ke koko i loko o kahi AVM nui, pono ka puʻuwai e hana ikaika. Hoʻonui kēia i ka pilikia o ka hāʻule ʻana o ka puʻuwai .

Pehea ka maʻamau o kēia mau mea?

He mau maʻi laha ʻole nā ​​maʻi vascular. Loaʻa lākou ma kahi o 1% o nā hānau ʻana āpau. Ma waena o kēia mau mea, ʻo nā malformations venous, ke ʻano maʻamau, e hoʻopilikia ana i hoʻokahi i kēlā me kēia 5,000 a 10,000 mau kānaka.

He aha ke kumu o nā malformations vascular?

ʻO ka hapa pinepine, ua hoʻokumu ʻia kēia e kahi ʻano ʻē i ka ulu ʻana o nā kīʻaha koko a me/a i ʻole nā ​​​​kahawai lymphatic ʻoiai e ulu ana ka fetus i loko o ka ʻōpū o ka makuahine (i loko o ka utero). ʻO ke ʻano kēia he mea maʻamau lākou i hānau ʻia .

ʻOi aku ka liʻiliʻi o ka pohō ʻana i nā kīʻaha koko i ka wā o kahi ʻeha, ʻaʻole paha e ʻike ʻia a lilo i malformation vascular i ka hala ʻana o ka manawa. Hiki ke ʻike ʻia nā malformations venous no ka manawa mua ma hope o kahi ulia a i ʻole ma muli o nā loli hormonal i ka wā ʻōpio a i ʻole ka hāpai ʻana .

I kahi hihia kakaikahi loa, hoʻoilina kekahi poʻe i nā hoʻololi genetic e hoʻonui ai i ka pilikia o ka loaʻa ʻana o nā malformations vascular. Ke aʻo hou nei nā kānaka noiʻi e pili ana i kēia mau kumu genetic.

ʻO wai ka mea i ʻoi aku ka nui o ka pilikia o ka hoʻomohala ʻana i kēia mau mea?

Hoʻoilina kekahi poʻe i nā loli genetic e hiki ke hoʻonui i ka pilikia o nā malformations vascular. ʻO kekahi o kēia mau kūlana:

• ʻO ka maʻi polū bleb nevus: Hoʻopilikia kēia i nā venous malformations i loko o kou ʻōpū a me ka ʻōnaehana digestive. Hiki iā ia ke hana i nā ʻeha polū ʻeleʻele, ʻulaʻula, a ʻeleʻele paha ma kou ʻili.
• ʻO ka maʻi CLOVES (ka ulu nui ʻana o ka lipomatous congenital, nā malformations vascular, nā nevi epidermal a me nā deformities spine): ʻO kēia ke kumu o ka hoʻokumu ʻana o nā AVM i loko o kou kaula spinal. Hiki iā ia ke hana i ka scoliosis ( curvature o ka spine), ka ulu ʻana o nā ʻiʻo momona, a me kahi ʻulaʻula ʻeleʻele.
• ʻO ka telangiectasia hemorrhagic hereditary (i ʻike ʻia hoʻi ʻo Osler-Weber-Rendu syndrome): ʻO kēia ke kumu o nā tangles abnormal, a i ʻole AVMs, i loko o nā capillaries liʻiliʻi.
• ʻO ka maʻi Klippel-Trenaunay (KTS): Hoʻoulu kēia i nā māka hānau ʻulaʻula-poni i kapa ʻia ʻo "port-wine stains", ka ulu ʻana o ka iwi a i ʻole nā ​​​​ʻiʻo, a me nā malformations e pili ana i nā veins a i ʻole nā ​​​​kahawai lymphatic.
• ʻO ka maʻi Parkes Weber: ʻO kēia ke kumu o ka hoʻokumu ʻana o nā AVM i kou mau lima a i ʻole kou mau wāwae.

Inā loaʻa iā ʻoe nā maʻi genetic e like me kēia, he mea nui e ʻike iā lākou.

He aha nā hōʻailona o nā malformations vascular?

Pili nā hōʻailona i ke ʻano o ka malformation. ʻO kahi malformation vascular e hoʻopilikia ai i kou ʻili e like paha me kahi hōʻailona hānau ʻulaʻula, polū, poni, ʻeleʻele, a ʻeleʻele paha i hāpai ʻia . Hiki i kēia mau kiko ke pehu, kahe ke koko, a ʻeha paha.

Inā he AVM kou i loko o kou lolo , ʻaʻole paha ʻoe e loaʻa i kekahi mau hōʻailona a hiki i ke kahe ʻana o ke koko. Inā kahe ke koko o ka lolo AVM, hiki iā ʻoe ke loaʻa i nā ʻeha poʻo, nā hopu ʻana, a i ʻole ka lolo ma kekahi ʻaoʻao o kou kino .

Hiki i nā malformations venous ke hoʻoulu i ka ʻeha, ka pehu ʻana, nā pilikia o ke koko, a me ka hōʻino ʻana i nā ʻōkana.

Pehea ʻoe e ʻike ai i kēia mau mea? Pehea e ʻike ai ke kauka i kēia?

Ma muli o ka ʻole o nā malformations vascular i nā hōʻailona i nā manawa a pau, ʻike pinepine nā kauka i ke kūlana ke hana nei lākou i nā hoʻokolohua no kekahi pilikia ʻē aʻe.

Hoʻohana nā kauka i nā hoʻokolohua kiʻi kūikawā e nānā i ke kahe koko a ʻike i nā malformations vascular. ʻO kēia mau hoʻokolohua:

• ʻO ke ultrasound , i kapa ʻia hoʻi he ultrasound vascular .
• MRI (Magnetic Resonance Imaging) , nona pū kekahi hoʻokolohua i kapa ʻia ʻo MR Angiogram (MRA) .
• ʻO ka scan CT (Computed Tomography scan), nona pū kekahi hoʻokolohua i kapa ʻia ʻo CT angiogram .
• ʻAngiogram a me/a i ʻole venogram .
• Nā kukuna X-ray maʻamau.

Hiki i kēia mau hoʻokolohua ke ʻike maopopo i ke kūlana o nā kīʻaha koko ma ia wahi, ke ʻano o ke kahe ʻana o ke koko, a inā he ʻano haiki a hoʻonui paha i ka ʻano ʻē.

He aha ka lāʻau lapaʻau no kēia?

ʻO ka pahuhopu nui o ka mālama ʻana i nā malformations vascular ka hōʻemi ʻana i nā hōʻailona a me nā pilikia e hiki mai ana. ʻO nā malformations i hana ʻole i kekahi pilikia ʻaʻole pono paha ka mālama ʻana a hiki ke ʻike wale ʻia i ka hala ʻana o ka manawa.

Aia ka lāʻau lapaʻau i ke ʻano o ke kīʻaha koko i hoʻopilikia ʻia. ʻO ka pinepine, pili kēia mau lāʻau lapaʻau i ka pani ʻana a i ʻole ka wehe ʻana i ke kīʻaha koko i hoʻopilikia ʻia ma ke ʻoki ʻana. Hiki ke mālama ʻia nā malformations he nui me ka hoʻohana ʻana i nā ʻano hana minimally invasive . Hiki i nā kauka ke hoʻohana i nā ʻano e like me:

• Sclerotherapy: Ma kēia, ua hoʻokomo ʻia kahi lāʻau lapaʻau kūikawā i loko o ke kīʻaha koko i hoʻopilikia ʻia, ka mea e hoʻēmi ai a pani ai ke kīʻaha koko.
• ʻO ka hoʻopili ʻana o ka catheter: Ma kēia kaʻina hana, ua hoʻokomo ʻia kahi paipu liʻiliʻi (catheter) ma o kahi kīʻaha koko a ua hoʻopaʻa ʻia ke kīʻaha koko ʻē aʻe mai loko mai.
• Nā lāʻau lapaʻau Laser: Hoʻohana ʻia kēia no kekahi mau malformations ʻili.
• Lapaʻau radiation (radiosurgery): Hoʻohana ʻia kēia no kekahi mau malformations hohonu a paʻakikī ke hana.

I kekahi manawa, hiki i kāu kauka ke ʻōlelo aku i kahi biopsy , ʻo ia hoʻi ka lawe ʻana i kahi ʻāpana o ka ʻiʻo no ka hoʻokolokolo ʻana. Hiki i kēia ke kōkua i ka hōʻoia ʻana i ka maʻi a/a i ʻole ka loaʻa ʻana o ka ʻiʻo no ka hoʻāʻo ʻana i ka genetic .

No ka mea he paʻakikī a he kakaikahi nā malformations vascular, ʻoi aku ka maikaʻi o ka mālama ʻana iā lākou me kahi hui e pili ana i nā loea he nui .

Hiki i kēia mau mea ke hoʻomaka hou ma hope o ka mālama ʻana?

ʻAe, hiki i nā malformations vascular ke hoʻi hou ma hope o ka mālama ʻana. No laila, pono paha ʻoe e loaʻa nā kipa hahai maʻamau a me nā hoʻokolohua e ʻike mua i nā malformations e hana hou ana.

Aia kekahi ala e pale ai i kēia mau mea mai ka hoʻokumu ʻana?

He mea hānau pinepine nā malformations vascular, ʻo ia hoʻi, ʻaʻohe ala e pale aku ai iā lākou.

Eia nō naʻe, inā loaʻa i kekahi o kou ʻohana kahi maʻi genetic e hoʻoulu ai i nā malformations vascular, pono paha ʻoe e ʻike i kahi kākāʻōlelo genetic.Hiki i kēia loea ke wehewehe iā ʻoe i nā koho i loaʻa e hōʻemi i ka pilikia o ka hoʻoili ʻana i kēia maʻi i kāu mau keiki.

He aha nā pilikia e hiki ke kū mai ma muli o kēia mau malformations vascular?

ʻAʻole pilikia kekahi mau ʻano kīnā a hiki ke ʻike wale ʻia. Eia nō naʻe, i nā manawa he nui, hiki iā lākou ke hōʻeha a me ka pehu .

Hiki i kekahi mau ʻano kīnā ke hōʻeha, a i ʻole ke komo ʻana o nā ʻiʻo, nā hono, a i ʻole nā ​​aʻalolo, hiki ke hoʻopilikia i ka hoʻoikaika kino, nā haʻuki, ka hana, a i ʻole nā ​​​​hana o kēlā me kēia lā .

Hiki i nā ʻano malformations nui a kiʻekiʻe ke alakaʻi i ka hāʻule ʻana o ka puʻuwai .

ʻO nā ʻano kīnā o ke koko i loko o nā ʻōkana paʻa e like me ke akepaʻa, nā puʻupaʻa, a i ʻole ka uterus hiki ke hana i ka hana pono ʻole o ke kino a me nā pilikia ʻē aʻe.

Hiki i kekahi mau malformations vascular, e like me nā AVM i loko o ka lolo a i ʻole ke kaula spinal, ke hōʻemi i ka nui o ke koko oxygenated e hiki aku i ka lolo. Hiki i kēia ke alakaʻi i nā pilikia e hoʻoweliweli i ke ola, e like me:

• Aneurysms ( nāwaliwali o ka paia o ke kīʻaha koko a me ka pehu ʻana e like me ka pōpō)
• Ke kahe koko ʻana o loko o ke poʻo
• Nā hahau

He aha ka wā e hiki mai ana no ka poʻe me kēia maʻi? Pehea ka hopena o kēia i ko lākou ola?

ʻO nā malformations vascular, e like me nā māka hānau, hiki ke hoʻopilikia i ke ʻano o ke kanaka a me ka hilinaʻi iā ia iho. Hiki i kēia ke alakaʻi i nā kūlana noʻonoʻo e like me ke kaumaha a me ka hopohopo . Eia nō naʻe, nui o kēia mau malformations e pane maikaʻi i ka mālama ʻana.

ʻO nā malformations koʻikoʻi, e like me nā AVM i loko o ka lolo, hiki ke hoʻoweliweli i ke ola inā hoʻomaka lākou e kahe ke koko.

Akā, ʻo ka mea nui loa, hiki ke mālama ʻia ka hapa nui o nā malformations a pane maikaʻi i ka lāʻau. No laila, he mea nui e ʻimi i ka ʻōlelo aʻoaʻo lapaʻau kūpono me ka hopohopo ʻole.

He aha kāu e nīnau ai i kāu kauka?

Inā he kānalua kou e pili ana i kēia maʻi, a inā paha ua ʻike ʻia ʻoe me ia, hiki iā ʻoe ke nīnau i kāu kauka i kēia mau nīnau:

• Pehea i loaʻa ai iaʻu kēia malformation vascular? (He aha ke kumu?)
• He aha ke ʻano o ka maʻi vascular i loaʻa iaʻu?
• He aha ka lāʻau lapaʻau maikaʻi loa noʻu?
• He aha nā pilikia a i ʻole nā ​​hopena ʻaoʻao e hiki mai ana o ka lāʻau lapaʻau?
• Pono anei au e hopohopo e pili ana i nā hōʻailona o nā pilikia? He aha kēlā mau hōʻailona?

E nīnau i kēia mau nīnau a e loaʻa iā ʻoe kahi ʻike maopopo o kou kūlana.

ʻO ka mea hope loa, nā mea nui e hoʻomanaʻo (Leka Lawe-Home)

ʻAe, e nānā wale kākou i nā kumu nui e pono ai ʻoe e hoʻomanaʻo mai nā mea a mākou i kamaʻilio ai.

• ʻO nā malformations vascular he mau ʻano ʻē o nā kīʻaha koko, ʻike pinepine ʻia i ka wā hānau.
• Hiki i kēia ke ʻike ʻia ma nā wahi a pau o ke kino , hōʻike i nā ʻōuli like ʻole, a i kekahi manawa ʻaʻole hōʻike iki i nā ʻōuli.
• He ʻelua mau mea like ʻole nā ​​Hemangiomas a me nā Vascular Malformations. He mea nui e ʻike i ka ʻokoʻa ma waena o nā mea ʻelua.
• Aia nā ʻano lapaʻau like ʻole no kēia maʻi. Na kāu kauka e hoʻoholo i ka lāʻau lapaʻau maikaʻi loa no kou maʻi.
• Hiki i kekahi mau ʻano koʻikoʻi, ʻoiai nā AVM i ka lolo, ke hana i nā pilikia, no laila he mea nui ka nānā pono ʻana i ke kauka.
• Inā loaʻa iā ʻoe a i kāu keiki paha kekahi o kēia mau hōʻailona, ​​mai hopohopo a e ʻimi i ke kauka no ka ʻōlelo aʻo.

E hoʻomanaʻo, ʻaʻole ʻoe hoʻokahi i ka wā e hana nei me kēia maʻi. Me ka ʻike kūpono a me ke kākoʻo lapaʻau, hiki ke mālama maikaʻi ʻia kēia maʻi.

Nā ʻano ʻino o ke koko, nā ʻano ʻē o ke koko, nā māka hānau, nā AVM, nā ʻano ʻino o ke koko, nā pilikia o ke koko, nā maʻi hānau