Ua haʻi aku paha kāu kauka iā ʻoe he maʻi paha kou i kapa ʻia ʻo myopathy. He mea maʻamau ka nui o nā nīnau e hiki mai ana i kou manaʻo ke lohe ʻoe i kēlā. He aha maoli ka myopathy? He mea anei e makaʻu ai? Aia kekahi lāʻau lapaʻau no ia mea? E kamaʻilio kākou e pili ana i ia mea me ka maʻalahi a me ka maopopo.
I ka ʻōlelo maʻalahi, he aha ka myopathy?
ʻO ka myopathy kahi inoa maʻamau i hāʻawi ʻia i kahi hui o nā maʻi e hoʻopilikia i nā ʻiʻo iwi o ko mākou kino. Hoʻopōʻino kēia mau maʻi a hoʻonāwaliwali i nā olonā ʻiʻo i loko o ko mākou mau ʻiʻo. Hiki ke loaʻa kēia ʻano ma ka wā hānau a i ʻole e ulu aʻe ma hope o ke ola.
I kēia manawa, ke noʻonoʻo nei paha ʻoe i ke ʻano o nā ʻiʻo iwi. He mea maʻalahi loa ia. ʻO lākou nā ʻiʻo i hoʻopili ʻia i ko kākou iwi a hiki iā kākou ke hoʻomalu a neʻe e like me ko kākou makemake. E noʻonoʻo, ke hāpai ʻoe i kou lima, kūlou i kou wāwae, hele, kamaʻilio... kōkua kēia mau ʻiʻo iwi i kēia mau mea a pau. ʻO ka nui o nā ʻiʻo i loko o ko kākou kino no kēia ʻano. No laila, i ka wā e loaʻa ai kahi myopathy, hiki ke paʻakikī ka hana ʻana i kēia mau hana o kēlā me kēia lā.
He aha nā ʻano nui o nā myopathy?
Hiki ke hoʻokaʻawale ʻia nā myopathies i ʻelua mau māhele nui: hoʻoilina a loaʻa. E nānā kākou i kēia mau ʻano ma ke kaʻawale.
| ʻAno o ka myopathy | He wehewehe maʻalahi |
|---|---|
| 1. Nā Myopathies i hoʻoilina ʻia Nā ʻano i hoʻoilina ʻia mai nā mākua mai ma o ka hoʻololi ʻana o ka genetics. | |
| Nā Myopathies hānau | ʻIke pinepine ʻia kēia mau mea ma ke ʻano he mau hōʻailona i kahi pēpē ʻōpiopio a keiki paha. Hiki ke lohi nā mākau neʻe e like me ke kolo ʻana a me ka hele wāwae. Hoʻopilikia pinepine ʻia nā ʻiʻo iwi āpau o ke kino, a ʻaʻole e ʻoi aku ka ʻino o ke kūlana i ka hala ʻana o ka manawa. |
| Nā Myopathies Mitochondrial | Hoʻokumu ʻia ia e nā hemahema i loko o ka mitochondria, nā "hale mana" o kā mākou mau cell e hana i ka ikehu. Ma waho aʻe o ka nāwaliwali o nā ʻiʻo, hiki iā ia ke hoʻopilikia i ka puʻuwai, ka lolo, a me ka ʻōnaehana hoʻoheheʻe. ʻO nā laʻana e komo pū me Kearns-Sayre syndrome , MELAS , a me MERRF . |
| Nā Dystrophies Muscular | I kēia mau hihia, e piʻi mālie ana ka nāwaliwali o nā ʻiʻo i ka hala ʻana o ka manawa. Hoʻokumu ʻia kēia ʻano ma muli o ka haki ʻana o nā ʻiʻo ma muli o nā hemahema i loko o nā protein e kākoʻo ana i nā ʻiʻo. |
| Nā Myopathies Metabolic | He kūlana kēia kahi e nāwaliwali koke ai nā ʻiʻo i ka wā o ka hoʻoikaika kino a i ʻole ke kaumaha o nā ʻiʻo. Hoʻokumu ʻia kēia kūlana e nā hemahema i loko o nā genes e hana ana i kekahi mau enzymes. |
| 2. Nā Myopathies i loaʻa Nā ʻano e kū mai ana ma hope o ke ola ma muli o nā kumu o waho. | |
| ʻO ka Myopathy Autoimmune/Inflammatory | Hoʻokumu ʻia ia e kahi pilikia me kā mākou ʻōnaehana pale ponoʻī e hoʻouka ana i nā ʻiʻo. |
| ʻO ka Myopathy ʻawahia | Hiki ke hana ʻia e kekahi mau mea ʻawahia (e like me ka waiʻona nui) a i ʻole kekahi mau lāʻau lapaʻau. |
| ʻO ka Myopathy Endocrine | Hoʻokumu ʻia lākou e nā pilikia me ka ʻōnaehana endocrine, ka mea e kaohi ana i nā hormones i loko o ko mākou kino. Hiki ke hoʻokumu ʻia kēia mau mea e nā maʻi o ka thyroid gland a i ʻole nā gland adrenal. |
| ʻO ka Myopathy maʻi | Ka nāwaliwali o nā ʻiʻo ma muli o kahi maʻi viral, bacteria, parasitic, a fungal paha. |
| ʻO ka Myopathy Maʻi Koʻikoʻi ma ka Hale Mālama Koʻikoʻi | Hiki ke hana ʻia i ka wā o ka mālama ʻia ʻana ma kahi keʻena mālama koʻikoʻi (ICU). Ua manaʻo ʻia ua hana ʻia ma muli o ke kūlana like no ka manawa lōʻihi. Hoʻopilikia nui ia i nā ʻiʻo e kōkua ana i ka hanu ʻana. |
He aha nā hōʻailona maʻamau o ka myopathy?
ʻO ka hōʻailona nui i maʻa mau i nā ʻano myopathy āpau, ʻo ia ka nāwaliwali o nā ʻiʻo . ʻIke pinepine ʻia kēia ma nā lima o luna, nā poʻohiwi, a me nā ʻūhā. Eia kekahi, nā hōʻailona e like me:
- ʻO nā ʻūpā a me ke koʻikoʻi o nā ʻiʻo
- Nā ʻūmiʻi ʻiʻo
- Ikehu haʻahaʻa
- Manaʻo koke i ka luhi ma hope o ka hana ʻana i nā hana liʻiliʻi
Ma muli o kēia nāwaliwali o nā ʻiʻo, ʻoiai nā hana maʻalahi o kēlā me kēia lā e like me ke komo ʻana i ke kapa, ka ʻauʻau ʻana, ka hamo ʻana i kou lauoho, ka piʻi ʻana i nā alapiʻi, a me ke ala ʻana mai kahi moe hiki ke lilo i mea paʻakikī.
Loaʻa i kekahi mau ʻano myopathy nā hōʻailona kikoʻī. No ka laʻana, i nā dystrophies muscular, piʻi mālie ka nāwaliwali o nā ʻiʻo . Hoʻomaka pinepine kēia nāwaliwali ma ka maka, nā pūhaka, a me nā poʻohiwi.
Pehea e ʻike ʻia ai ka myopathy?
No ka mea, he nui nā maʻi e hoʻopilikia ana i nā aʻalolo a me nā ʻiʻo i loko o ko kākou kino, pono kekahi mau hoʻokolohua e ʻike pololei i ka myopathy. Hiki i kāu kauka ke paipai i hoʻokahi a ʻoi aku paha o kēia mau hoʻokolohua.
| Inoa o ka hoʻāʻo | I ka ʻōlelo maʻalahi... |
|---|---|
| Hoʻāʻo Genetic | Hoʻohana lākou i kahi hāpana koko a lawai paha e nānā inā he kīnā i kāu mau genes. |
| Hoʻāʻo Genetic Biochemical | Ua hoʻāʻo ʻia ke koko, ka mimi, a i ʻole ka wai o ka iwi kuamoʻo e nānā i nā ʻano ʻē o ka enzyme. |
| CT Scan (Tomography Kamepiula) | Lawe ʻia kekahi mau kukuna X e hana i kahi kiʻi 3D piha o nā iwi, nā kīʻaha koko, a me nā ʻiʻo palupalu. |
| ʻO ke kī ʻana o ka lumbar | Hoʻokomo ʻia kahi nila liʻiliʻi ma waena o ʻelua vertebrae ma ke kua haʻahaʻa a lawe ʻia ka wai cerebrospinal (CSF) a hoʻāʻo ʻia. |
| ʻIke MRI (Kiʻi Resonance Magnetic) | Hoʻohana ʻia kahi kahua magnetic ikaika a me nā nalu lekiō e kiʻi i nā kiʻi kikoʻī o nā ʻōpū, nā ʻiʻo, a me ka iwi. |
| Biopsy o ke aʻalolo a me nā ʻiʻo | No ka hoʻāʻo ʻana, ua wehe ʻia kahi ʻāpana liʻiliʻi o ka ʻiʻo mai ke ʻiʻo a i ʻole ke aʻalolo pili a hoʻouna ʻia i ka hale hana. |
| Nā Haʻawina Hoʻoili Aʻalolo | Hoʻopili ʻia nā electrodes i ka ʻili, e hoʻoulu ana i nā aʻalolo a ana i ka wikiwiki o ka hele ʻana o nā hōʻailona uila ma o lākou. Kōkua kēia i ka hoʻoholo ʻana inā he pilikia me nā aʻalolo. |
| ʻElectromyography (EMG) | Hoʻokomo ʻia nā electrodes liʻiliʻi i loko o nā ʻiʻo a ana ʻia ka hana uila i ka wā e ʻaelike a neʻe ai nā ʻiʻo. Hiki i kēia ke kōkua i ka hoʻoholo ʻana inā aia ka pilikia i loko o nā ʻiʻo ponoʻī. |
He aha nā lāʻau lapaʻau no ka myopathy?
ʻO ke ʻano o ka mālama ʻana no ka myopathy e pili wale ana i ke ʻano o ka myopathy āu e loaʻa ai.
ʻAʻohe lāʻau lapaʻau no ka hapa nui o nā myopathies hoʻoilina . Eia nō naʻe, hiki ke mālama ʻia nā hōʻailona a hiki ke maʻalahi ke ola ma o nā lāʻau lapaʻau e like me ka hoʻōla kino . Hiki ke mālama ʻia kekahi mau ʻano, e like me ka Duchenne muscular dystrophy a me ka maʻi Pompe, me ka lāʻau lapaʻau.
Hoʻōla pinepine ʻia nā myopathies i loaʻa ma ka mālama ʻana i ke kumu kumu . No ka laʻana, mālama ʻia ka myopathy endocrine ma ka hoʻopaʻa ʻana i nā pae hormone. Ma muli o ke koʻikoʻi o ke kūlana, pono paha ka lāʻau lapaʻau kino i kēia mau hihia.
ʻO ka mea nui loa, na kāu kauka e hoʻoholo i ka hoʻolālā lapaʻau maikaʻi loa no kou kūlana, no laila e wehe a ʻoiaʻiʻo me ia e pili ana i kekahi mea.
Leka Lawe-Home
- ʻAʻole ka maʻi myopathy he maʻi neurological, akā he maʻi e hoʻopilikia ai i nā ʻiʻo .
- Nui nā ʻano o kēia; ʻike ʻia kekahi i ka wā hānau, a ʻo kekahi e ulu aʻe ma hope o ke ola.
- ʻO ka hōʻailona nui, ʻo ia ka nāwaliwali o nā ʻiʻo, hiki ke hoʻolilo i nā mea e like me ka hele wāwae a me ka hāpai ʻana i mea paʻakikī.
- Pono paha nā hoʻokolohua like ʻole, e like me nā hoʻokolohua koko, nā scan, a me nā biopsies, e ʻike pololei i ka maʻi.
- Aia ka lāʻau lapaʻau i ke ʻano o ka myopathy āu e loaʻa ai, no laila e nīnau mau i kāu kauka no ka ʻōlelo aʻoaʻo kūpono.
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