Ke manaʻo nei ʻoe i kekahi manawa ua luhi a palaualelo paha ʻoe no ke kumu ʻole? Ke nānā aku nei kou ʻili i ka melemele? A i ʻole ʻaʻole e nalowale ka jaundice o kāu pēpē hānau hou ma hope o ʻelua pule? ʻO ke kumu o kēia mau mea, he hemahema paha ia o kahi enzyme i kapa ʻia ʻo G6PD i loko o kou kino. Mai hopohopo, he maʻi maʻamau loa kēia. I kēia lā, e kamaʻilio maʻalahi a maopopo mākou e pili ana i ke ʻano o G6PD, nā mea e hana ʻia ke haʻahaʻa, a me ka hoʻāʻo G6PD.
He aha wale nō ka G6PD?
E noʻonoʻo i nā hunaola koko ʻulaʻula i loko o ko kākou kino e like me nā koa e hana ana. Aia kekahi 'kiaʻi' e pale ana i kēia mau koa mai nā mea ʻino like ʻole. ʻO kēlā kiaʻi he enzyme i kapa ʻia ʻo G6PD.
I ka ʻōlelo maʻalahi, ʻo G6PD (Glucose-6-Phosphate Dehydrogenase) kahi enzyme koʻikoʻi loa e pale ana i kā mākou mau cell, ʻoiai nā cell koko ʻulaʻula i loko o ko mākou koko, mai nā kemika ʻino. Hoʻopuka ko mākou kino i nā mea ʻino (i kapa ʻia ʻo 'Free Radicals' a i ʻole 'Reactive Oxygen Species' ) i hana ʻia i ka wā hana maʻamau. Hana ka enzyme G6PD i kēia ma ka pale ʻana i kēia mau mea ʻino mai ka hōʻiliʻili ʻana a me ka hōʻino ʻana i nā cell.
He aha ka mea e hana ai ke haʻahaʻa ka G6PD?
I kēia manawa, e noʻonoʻo i ka mea e hana ʻia inā haʻahaʻa kēlā 'mea pale' (G6PD) i loko o ke kino? A laila hele mai kēlā mau mea ʻino a hoʻomaka e luku i kā mākou mau hunaola koko ʻulaʻula. ʻO kēia kaʻina hana o ka haki ʻana o nā hunaola koko ʻulaʻula ma mua o ka hiki ke hana ʻia ua kapa ʻia ʻo hemolysis .
Ke nalowale ʻoe i ka nui o nā hunaola koko ʻulaʻula ma kēia ʻano, ʻaʻole loaʻa i kou kino ka oxygen e pono ai. ʻO ia ka mea a mākou e kapa nei he anemia, a ʻoi aku ka pololei, he anemia hemolytic . ʻO ia ke kumu e luhi ai ʻoe, nāwaliwali, a mae wale hoʻi i nā manawa a pau.
Pehea e kū mai ai ka hemahema o ka G6PD?
He maʻi hoʻoilina hoʻoilina ka hemahema o ka G6PD. ʻO ia hoʻi, he mea ia āu e hoʻoilina ai mai kou mau mākua mai. Ke loaʻa kahi mutation i loko o ka gene e kuhikuhi ana iā ʻoe e hana i ka enzyme G6PD, e emi ana ka nui o kēia enzyme i hana ʻia i loko o ke kino.
Akā, ʻo ka mea nui ma ʻaneʻi, ʻaʻole e loaʻa i nā kānaka a pau me ka hemahema o ka G6PD nā hōʻailona. Noho ka nui o ka poʻe i ke ola maʻamau me ka ʻole o nā pilikia. Eia nō naʻe, hiki i kekahi mau mea o waho (kapa mākou i kēia mau 'mea hoʻoulu') ke hoʻoulu i nā hōʻailona e ʻike koke ʻia.
Nā mea hoʻonāukiuki e hoʻoulu ai i nā hōʻailona G6PD
ʻO kēia mau mea hoʻonāukiuki ke kumu o ke kino e hoʻonui koke i ka nui o kēlā mau 'radical free' ʻino a mākou i kamaʻilio ai. ʻAʻole hiki i ke kanaka me ka hemahema G6PD ke kāohi i kēia mau mea ʻino e hoʻonui nei. ʻO ia ka manawa e hoʻomaka ai nā hunaola koko ʻulaʻula e haki, a ʻike ʻia nā hōʻailona.
| ʻAno Hoʻāla | Wehewehena |
|---|---|
| Kekahi mau meaʻai | ʻO nā pī Fava ma ke ʻano kūikawā. Hiki ke hoʻāla ʻia nā hōʻailona ma ka ʻai ʻana iā lākou a i ʻole ka hanu ʻana i kā lākou pollen. Ua kapa ʻia kēia maʻi ʻo 'Favism'. |
| Kekahi mau lāʻau lapaʻau | ʻO kekahi mau lāʻau ʻeha e like me Aspirin, Acetaminophen (Paracetamol), kekahi mau lāʻau Sulfa, kekahi mau antibiotics a me nā lāʻau malaria nā mea nui. Mai lawe i kekahi lāʻau me ka ʻole o ke aʻo ʻana a ke kauka. |
| Nā maʻi viral a me bacteria | ʻO kēlā me kēia maʻi, mai ke anu maʻamau a i nā maʻi koʻikoʻi, hiki ke hoʻoulu i nā hōʻailona G6PD. |
ʻOi aku ka maʻamau o ka hemahema o G6PD i nā kāne ma mua o nā wahine, a ʻoi aku ka maʻamau i nā poʻe o ʻApelika, ʻAsia, a me ke Kaiwaenahonua.
ʻO wai ka mea e pono ai ke hana i ka hoʻāʻo G6PD?
Hiki i kāu kauka ke ʻōlelo aku i kahi hoʻāʻo G6PD (kahi hoʻāʻo koko maʻalahi), ʻoiai inā loaʻa iā ʻoe kekahi o kēia mau hōʻailona:
- Ka luhi a me ka nāwaliwali i wehewehe ʻole ʻia
- ʻIli keʻokeʻo
- Paʻakikī ka hanu ʻana a i ʻole ka wheezing
- Nā palpitations o ka puʻuwai
- Melemele o ka ʻili a me nā maka (jaundice)
- Mimi ʻeleʻele (kala kola)
- ʻEha kua a ʻeha paha
- Ke kūlana o ka huikau o kēia manawa
E mālama pono i nā pēpē hānau hou.
He mea maʻamau no kahi pēpē hānau hou ke loaʻa ka jaundice. Akā inā mau ia no ʻelua pule a ʻoi aku , a lilo ka mimi o ke pēpē i ʻeleʻele, a maeʻele ka ʻōpala, manaʻo paha ke kauka he hemahema G6PD a hana i kēia hoʻāʻo.
Pehea e hoʻomaopopo ai i ka hōʻike hoʻāʻo?
Hiki ke ʻokoʻa iki nā hopena o ka hoʻāʻo G6PD mai kēlā me kēia keʻena hoʻokolohua, no laila hiki i kāu kauka ke hāʻawi iā ʻoe i ka ʻike pololei loa . Eia nō naʻe, ma ke ʻano laulā, aia ʻekolu ʻano hopena.
- Maʻamau: Loaʻa iā ʻoe ka nui o ka enzyme G6PD i loko o kou kino. ʻAʻohe ou hemahema G6PD.
- Ka hemahema kūpono: Aia nā pae enzyme ma waena o 10% a me 60% o ka maʻamau. ʻIke pinepine kēia poʻe i nā hōʻailona ke loaʻa iā lākou kahi maʻi a i ʻole e lawe ana i kahi hopena lāʻau maikaʻi ʻole.
- Ka hemahema nui: Aia ka enzyme ma lalo o 10% o nā pae maʻamau. Loaʻa paha i kēia poʻe ka anemia mau a i ʻole nā hōʻailona pinepine.
Ka mālama ʻana a me ka hoʻokele ʻana i ka hemahema o G6PD
ʻAʻole hiki ke ho'ōla loa ʻia ka hemahema o ka G6PD, no ka mea, he maʻi hoʻoilina ia. Eia nō naʻe, inā mālama pono ʻia, hiki iā ʻoe ke ola i kahi ola olakino me ka ʻole o nā pilikia .
ʻO ka mea maikaʻi loa e hana ai, ʻo ia ke pale aku i nā 'mea hoʻoulu' e hoʻoulu ai i nā hōʻailona. ʻO kēia ka lāʻau lapaʻau nui.
Pono ʻoe:
- E pale loa i ka ʻai ʻana i nā pī fava.
- Mai lawe i nā lāʻau ʻeha e like me Aspirin a me Acetaminophen (Paracetamol) me ka ʻae ʻole ʻia e kāu kauka.
- E hoʻomaopopo i kāu kauka he hemahema kou o ka G6PD ma mua o ke kau ʻana i kekahi lāʻau lapaʻau .
- E ʻimi koke i ke kōkua lapaʻau inā loaʻa iā ʻoe kekahi maʻi.
Inā ʻoluʻolu kou mau hōʻailona, hiki i kāu kauka ke kuhikuhi i nā pila folic acid a me ka hao. Inā koʻikoʻi kou anemia, pono paha ʻoe e lawe ʻia i ka haukapila a hāʻawi ʻia i kahi hoʻoili koko a i ʻole ka lāʻau oxygen.
E hoʻomanaʻo ʻaʻole e kōkua nā antioxidants e like me ka Vitamin E i kēia kūlana.
Leka Lawe-Home
- ʻO ka hemahema o ka G6PD kahi maʻi hoʻoilina maʻamau i hoʻoili ʻia mai nā hanauna a ʻaʻohe mea e makaʻu ai.
- ʻAʻohe hōʻailona iki o ka nui o ka poʻe. Hōʻike ʻia nā hōʻailona ke loaʻa iā lākou nā 'mea hoʻonāukiuki' e like me nā pīni fava, kekahi mau lāʻau lapaʻau, a i ʻole nā maʻi.
- ʻO ka hoʻokele nui, ʻo ia ka pale ʻana i kēia mau mea hoʻonāukiuki.
- Inā loaʻa iā ʻoe ka hemahema o ka G6PD, he mea nui e hoʻomaopopo i kekahi kauka ma mua o ka ʻimi ʻana i ka lāʻau lapaʻau.
- Inā ʻike ʻoe i nā hōʻailona e like me ka luhi nui koke, ka melemele o ka ʻili, a i ʻole ka mimi ʻeleʻele, e ʻike koke i kāu kauka.











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