Koj puas muaj teeb meem o, mob, thiab mob hauv qab koj daim tawv nqaij? Cia peb tham txog Eosinophilic Fasciitis!

Koj puas tau muaj ib zaug twg uas koj xav tias muaj ib lub pob, o, lossis mob hauv qab daim tawv nqaij ntawm koj txhais caj npab lossis ceg? Tej zaum nws tshwm sim tom qab ua si zoo. Koj puas tau muaj ib yam dab tsi zoo li no? Yog li, ntawm no yog ib qho mob uas tsis tshua paub uas tej zaum yuav tseem ceeb rau koj.

Eosinophilic Fasciitis yog dab tsi?

Hais yooj yim xwb, Eosinophilic Fasciitis yog ib yam mob uas cov nqaij uas npog peb cov leeg thiab cov nqaij hauv qab peb daim tawv nqaij - peb hu nws ua fascia hauv kev kho mob - mam li o, tuab, thiab nruj. Xav txog nws zoo li lub mesh uas tuav peb daim tawv nqaij thiab cov leeg ua ke thiab pab lawv txav mus los, ib yam li lub mesh uas peb muab tso rau hauv lub thawv ntawm peb lub tsheb thaum peb mus yuav khoom.

Qhov no yog ib hom kab mob autoimmune . Qhov no txhais tau hais tias peb lub cev tiv thaiv kab mob, lub cev tiv thaiv kab mob, pib tawm tsam cov khoom noj qab haus huv ntawm peb lub cev tsis raug. Nws zoo li tawm tsam peb tsev neeg thaum lawv xav tias lawv raug nyiag.

Yog tias tsis kuaj pom thiab kho thaum ntxov, nws tuaj yeem ua rau daim tawv nqaij hloov pauv mus tas li thiab poob qhov kev txav mus los ntawm cov pob qij txha . Yog li ntawd, nws yog ib qho tseem ceeb heev uas yuav tsum nrhiav kev pab kho mob sai li sai tau thaum cov tsos mob tshwm sim.

Qhov xwm txheej no cuam tshuam li cas rau feem ntau? Nws cuam tshuam rau leej twg?

Kab mob Eosinophilic Fasciitis tuaj yeem cuam tshuam rau fascia txhua qhov chaw ntawm lub cev, tab sis feem ntau nws cuam tshuam rau tes thiab taw . Rau ntau tus neeg, cov tsos mob, xws li mob lossis o, yuav tshwm sim thawj zaug tom qab kev tawm dag zog hnyav lossis ua haujlwm uas yuav tsum sawv ntsug thoob plaws hnub.

Cov tsos mob no, xws li mob nqaij thiab o, yuav zoo ib yam li lwm yam kab mob uas tshwm sim, yog li nws tseem ceeb heev uas yuav tsum mus ntsib kws kho mob tam sim ntawd yog tias koj pom muaj kev hloov pauv tshiab lossis mob hauv koj daim tawv nqaij, cov leeg, lossis cov pob qij txha. Tej zaum koj kuj yuav tsum mus ntsib kws kho mob rheumatologist, tus kws kho mob uas tshwj xeeb hauv cov pob qij txha thiab lwm yam kab mob o.

Tam sim no tsis muaj tshuaj kho tau tus kab mob no. Txawm li cas los xij, qhov xov xwm zoo yog tias rau feem ntau ntawm cov neeg, cov tsos mob yuav ploj mus hauv ob peb xyoos, uas txhais tau tias tus kab mob yuav "zam txim", lossis lub sijhawm pw tsaug zog. Txawm li cas los xij, qee tus neeg yuav rov qab muaj cov tsos mob dua.

Qhov Sib Txawv Ntawm Eosinophilic Fasciitis thiab Scleroderma

Thaum tham txog ob yam kab mob no, qee tus neeg yuav tsis nkag siab tias lawv yog lwm yam kab mob hu ua 'Scleroderma'. 'Eosinophilic Fasciitis' thiab 'Scleroderma' yog ob yam kab mob 'autoimmune' uas tsis tshua muaj. Tsis tas li ntawd, ob yam kab mob no, cov nqaij ntawm lub cev yuav tuab thiab tawv.

Yog li ntawd, qhov txawv yog dab tsi? Qhov txawv yog nyob rau hauv cov hom nqaij uas raug kev txom nyem.

• Hauv Eosinophilic Fasciitis, raws li peb tau tham ua ntej, lub fascia, uas yog ib daim ntaub nyias nyias thiab ywj pheej hauv qab daim tawv nqaij, raug cuam tshuam. Raws li lub sijhawm dhau mus, lub fascia no tuab thiab nthuav dav, ua rau nws nyuaj rau txav qhov chaw raug mob.
• Tiam sis hauv 'Scleroderma', lub cev tiv thaiv kab mob ua rau lwm cov hlwb tsim cov protein hu ua 'collagen' ntau dua (ib yam dab tsi uas muab zog rau peb daim tawv nqaij thiab cov nqaij). Cov collagen ntau dhau no tau tso rau hauv daim tawv nqaij thiab cov kab mob sab hauv, ua rau lawv tuab thiab tawv, zoo li ib qho caws pliav qub. Tiam sis es tsis txhob kho qhov txhab, cov collagen ntau dhau no kuj tuaj yeem ua rau cov nqaij noj qab haus huv puas tsuaj.

Eosinophilic Fasciitis thiab COVID-19

Cov neeg uas muaj cov kab mob autoimmune xws li Eosinophilic Fasciitis raug suav hais tias muaj feem yuav kis tus kab mob COVID-19 ntau dua li cov pej xeem feem ntau.

Cov kws tshaj lij tseem tsis tau paub meej tias cov neeg uas muaj tus mob no puas yuav muaj cov tsos mob hnyav dua los ntawm COVID-19. Yog li ntawd, nws yog qhov zoo tshaj plaws los ua raws li cov lus qhia ntawm cov tub ceev xwm saib xyuas kev noj qab haus huv, xws li Lub Chaw Tswj thiab Tiv Thaiv Kab Mob (CDC), los tiv thaiv koj tus kheej ntawm kev kis kab mob.

Leej twg yuav muaj feem kis tau tus kab mob no tshaj?

Kab mob Eosinophilic Fasciitis tuaj yeem cuam tshuam rau txhua tus neeg, tab sis feem ntau nws cuam tshuam rau cov neeg hnub nyoog ntawm 30 thiab 60 xyoo.

Tsis tas li ntawd xwb, cov neeg uas muaj tej yam mob nkeeg ntev yuav muaj feem mob no ntau dua. Ib txhia ntawm cov mob no suav nrog:

• Aplastic anemia (aplastic anemia - ib qho anemia uas cov qe ntshav tsim tsawg dua)
• Hemolytic anemia (anemia uas cov qe ntshav liab tawg sai sai)
• Lymphoma (mob qog nqaij hlav ntawm lub cev lymphatic)
• Kab mob Leukemia (mob qog ntshav ntawm cov qe ntshav)
• Qee hom kab mob "Thyroid"

Qhov no feem ntau tshwm sim li cas?

Kab mob Eosinophilic Fasciitis yog ib yam kab mob tsis tshua muaj . Txog tam sim no, tsuas muaj ob peb tug neeg mob xwb, kwv yees li 300 tus, tau tshaj tawm hauv cov ntawv xov xwm tshawb fawb thoob ntiaj teb. Txawm li cas los xij, tej zaum vim tsis tau kuaj mob lossis tsis tau tshaj tawm txaus, tus lej ntawm cov neeg mob yuav ntau dua.

Kab mob Eosinophilic Fasciitis cuam tshuam li cas rau kuv lub cev?

Zoo li peb tau tham ua ntej lawm, qhov mob no yog tshwm sim los ntawm kev o ntawm lub fascia, uas yog ib daim ntaub nyias nyias thiab yoog tau hauv qab daim tawv nqaij. Cov txheej fascia no npog thiab tiv thaiv peb cov leeg thiab qee cov kab mob sab hauv. Nws kuj tuav daim tawv nqaij thiab cov leeg kom ruaj khov thiab txhawb nqa lawv thaum lawv txav mus los.

Xav txog nws, qhov fascia no pab kom peb ob txhais ceg yoog tau, tab sis tsis yog tsuas yog dai rau hauv av xwb. Tab sis rau ib tus neeg uas muaj 'Eosinophilic Fasciitis', daim nyias nyias fascia no yuav o, maj mam tuab, thiab tawv. Thaum kawg, qhov o no ua rau nws nyuaj rau txav daim tawv nqaij thiab cov leeg nyob ib puag ncig nws. Yog tias tsis kho, qhov fascia no tuaj yeem daig rau hauv ib qho chaw thiab nruj. Qhov no qee zaum hu ua 'contracture'. Ntawd yog, ib qho mob uas ib qho pob qij txha tsis tuaj yeem ncab lossis khoov.

Es tsis txhob ua kom cov fascia ywj pheej li qub, cov qhov ntawm lub cev uas raug mob yuav mob lossis nyuaj rau txav mus los.

Cov feem ntawm lub cev uas feem ntau cuam tshuam yog:

• Tes (tshwj xeeb tshaj yog lub xib teg, uas yog, sab hauv ntawm tes)
• Ob txhais ceg (tshwj xeeb tshaj yog pem hauv ntej, txoj cai ntawm pob txha duav)
• Cov pob qij txha lossis thaj chaw ib puag ncig

Txawm hais tias tsis tshua muaj los xij, qhov mob no kuj tseem tuaj yeem cuam tshuam rau daim tawv nqaij ntawm lub ntsej muag, hauv siab, thiab plab.

Ib txhia neeg mob uas muaj tus kab mob Eosinophilic Fasciitis kuj tseem yuav mob pob qij txha zoo ib yam li mob Rheumatoid Arthritis. Yog tias qhov mob pob qij txha no tsis raug tswj, cov pob txha mos hauv cov pob qij txha yuav raug puas tsuaj, ua rau mob pob qij txha mus sij hawm ntev.

Tsis tas li ntawd xwb, yog tias tus kab mob no cuam tshuam rau lub fascia hauv koj txhais tes lossis dab teg, qhov o tuaj yeem ua rau cov hlab ntsha median, ib qho ntawm cov hlab ntsha tseem ceeb hauv tes, raug nias, ua rau muaj mob hu ua Carpal Tunnel Syndrome (mob loog, mob, thiab tsis muaj zog hauv tes).

Qhov tseem ceeb yog tias Eosinophilic Fasciitis yog ib yam mob uas tuaj yeem hloov pauv thiab loj hlob sai heev. Koj tuaj yeem pib pom cov teebmeem pom tseeb hauv lub sijhawm luv luv, zoo li ob peb lub lis piam. Yog li ntawd, yog tias koj pom muaj cov tsos mob lossis kev hloov pauv hauv koj lub cev, mus ntsib kws kho mob tam sim ntawd.

Cov tsos mob ntawm Eosinophilic Fasciitis yog dab tsi?

Yog li, koj yuav tsum paub tias muaj tus kab mob no li cas ? Nov yog qee cov tsos mob tseem ceeb:

• Mob nqaij .
• Tawv nqaij mos.
• O los yog o .
• Cov tsos mob ntawm 'Carpal Tunnel Syndrome' (xws li loog, mob, tsis muaj zog hauv tes).
• Mob pob qij txha (mob pob qij txha - o ntawm pob qij txha, mob, mob tawv nqaij thaum sawv ntxov).
• Cov tawv nqaij zoo li tuab dua thiab nruj dua li qub.
• Hauv qee qhov chaw, daim tawv nqaij zoo li puckered thiab ntxhib, zoo li daim tawv txiv kab ntxwv ('puckered skin' lossis "peau d'orange" appearance).

Vim li cas ho ua li no?

Yog hais qhov tseeb, cov kws tshaj lij tseem tsis tau paub tseeb tias yog vim li cas Eosinophilic Fasciitis thiaj li tshwm sim. Ib yam li ntau yam kab mob autoimmune, nws tuaj yeem tshwm sim sai sai, qee zaum tsis muaj laj thawj pom tseeb.

Txawm li cas los xij, qee qhov kev tshawb fawb tau pom tias cov kab mob autoimmune no tuaj yeem "ua rau" los ntawm qee yam. Ntawd yog, tus kab mob tuaj yeem tshwm sim vim yog lwm yam. Piv txwv li:

• Qee hom kev kis kab mob .
• Qee qhov kev ua xua .
• Siv qee yam tshuaj .
• Siv qee yam tshuaj .

Ib txhia neeg uas muaj tus kab mob Eosinophilic Fasciitis hais tias lawv cov tsos mob thawj zaug tshwm sim tom qab ua si nawv hnyav , xws li khiav, tsa hnyav, lossis tawm dag zog, lossis thaum ua haujlwm uas yuav tsum tau siv zog ntau ntawm lawv txhais tes lossis ceg.

Nws yog ib lub tswv yim zoo los tham nrog koj tus kws kho mob txog koj cov yam ntxwv uas ua rau muaj tus kab mob autoimmune zoo li no.

Cov kws kho mob kuaj mob li cas? (Kev kuaj mob)

Yog tias koj muaj cov tsos mob no, tus kws kho mob yuav ua ntau qhov kev kuaj mob kom paub seb koj puas muaj Eosinophilic Fasciitis:

1. Kev kuaj mob ntawm daim tawv nqaij ntawm lub plab: Kev kuaj mob yog thaum koj tus kws kho mob coj ib qho qauv me me ntawm koj cov ntaub so ntswg thiab xa mus rau chav kuaj mob kom saib nws hauv qab lub tshuab tsom iav. Qhov no suav nrog kev coj ib daim me me ntawm daim tawv nqaij uas raug mob thiab daim tawv nqaij ntawm lub plab hauv qab nws thiab kuaj xyuas nws. Feem ntau, qhov no yog txoj hauv kev ntseeg siab tshaj plaws los kuaj mob.

2. Kev kuaj ntshav: Yog tias koj muaj Eosinophilic Fasciitis, tej zaum koj yuav muaj cov qe ntshav dawb hu ua Eosinophils ntau hauv koj cov ntshav (uas yog qhov chaw uas tus kab mob tau txais nws lub npe). Txawm li cas los xij, kev kuaj ntshav ib leeg tsis tuaj yeem lees paub tus kab mob. Feem ntau, yuav tsum tau kuaj nqaij.

3. Kev kuaj duab: Cov kev kuaj xws li MRI (Magnetic Resonance Imaging) tuaj yeem pab txheeb xyuas qhov o ntawm lub cev, tshwj xeeb tshaj yog nyob rau hauv fascia thiab cov nqaij nyob ib puag ncig. Txawm li cas los xij, zoo li kev kuaj ntshav, lawv tsis meej npaum li kev kuaj nqaij los kuaj mob.

Kev Kho Mob Rau Eosinophilic Fasciitis

Tsis tshua muaj tej yam tshwm sim uas yuav ploj mus nws tus kheej yam tsis tau kev kho mob. Tiam sis feem ntau, cov kws kho mob kho Eosinophilic Fasciitis nrog ib hom tshuaj hu ua corticosteroids . Cov no yog ib hom tshuaj steroid.

Cov tshuaj Corticosteroids ua haujlwm los ntawm kev txo qhov o ntawm lub cev thiab tiv thaiv lub cev tiv thaiv kab mob uas ua haujlwm ntau dhau. Prednisone yog cov tshuaj corticosteroid uas feem ntau siv.

Koj tus kws kho mob kuj tseem yuav sau ntawv rau lwm yam kev kho mob ntxiv rau corticosteroids, xws li:

• Cov Tshuaj NSAIDs: Cov tshuaj uas tsis yog steroidal anti-inflammatory drugs (NSAIDs) muaj nyob rau ntawm lub tsev muag tshuaj - piv txwv li, ibuprofen thiab diclofenac - tuaj yeem txo cov tsos mob xws li mob thiab o. Txawm li cas los xij, yog tias koj twb noj cov tshuaj 'corticosteroids' lawm, nrog koj tus kws kho mob tham ua ntej noj cov tshuaj 'NSAIDs'. Tsis txhob noj cov tshuaj 'NSAIDs' ntau tshaj 10 hnub ib zaug yam tsis tau kev pom zoo los ntawm koj tus kws kho mob.
• Cov tshuaj tiv thaiv kab mob: Nyob ntawm seb koj tus mob hnyav npaum li cas, koj tus kws kho mob yuav sau ntawv rau lwm cov tshuaj (piv txwv li, Methotrexate) uas tiv thaiv lub cev tiv thaiv kab mob uas ua rau Eosinophilic Fasciitis.
• Kev Kho Mob Lub Cev: Kev kho mob lub cev tuaj yeem pab ncab thiab ua kom koj cov fascia xoob thaum nws nruj, thiab pab tswj kev txav mus los ntawm cov pob qij txha. Koj tus kws kho mob lossis tus kws kho mob lub cev yuav qhia koj cov kev tawm dag zog thiab kev ncab uas tsim nyog rau koj cov tsos mob.
• Kev kho lwm yam mob: Koj yuav xis nyob dua los ntawm kev kho cov tsos mob ntawm lwm yam mob, xws li carpal tunnel syndrome lossis mob pob qij txha.
• Phais Mob: Yog tias koj tus kab mob Eosinophilic Fasciitis hnyav txaus ua rau mob, tej zaum koj yuav tsum tau phais kom tshem tawm lossis tshem tawm ib feem ntawm koj lub fascia (fascial release). Qhov no feem ntau yog qhov kawg.

Yuav tswj cov tsos mob li cas?

• Nws yog ib qho tseem ceeb heev uas yuav tsum noj tshuaj raws nraim li tus kws kho mob hais, rau lub sijhawm uas tau sau tseg.
• Yog koj tus kws kho mob lossis tus kws kho lub cev muab kev ncab lossis lwm yam kev tawm dag zog rau koj, ua lawv ntau zaus li lawv qhia koj kom pab ncab cov fascia uas raug mob. Txawm hais tias qhov no yuav nyuaj, nws tuaj yeem pab tau yog tias koj txuas ntxiv ua lawv.
• Yog koj muaj mob Carpal Tunnel Syndrome, tej zaum koj yuav tsum hnav ib lub brace los pab kom koj lub dab teg nyob ruaj khov thaum koj pw tsaug zog. Siv nws raws li koj tus kws kho mob qhia.

Kuv yuav zoo dua sai npaum li cas tom qab kho tas?

Qhov mob Eosinophilic Fasciitis uas ua rau mob yuav tsum pib ploj mus hauv ob peb teev tom qab noj thawj koob tshuaj corticosteroids. Qhov kev pab no yuav yog ib ntus xwb, thiab cov tsos mob yuav rov qab los thaum cov tshuaj tas sij hawm. Yog li ntawd, nws yog ib qho tseem ceeb uas yuav tsum noj cov tshuaj kom tag nrho raws li koj tus kws kho mob tau sau tseg.

Puas tiv thaiv tau tus kab mob Eosinophilic Fasciitis?

Tu siab kawg li, tsis muaj ib txoj kev tshwj xeeb los tiv thaiv tus kab mob no. Cov kws tshaj lij tsis paub meej tias dab tsi ua rau muaj cov kab mob autoimmune lossis lawv ua rau muaj li cas, yog li lawv tsis tuaj yeem hais thaum twg lossis vim li cas koj thiaj yuav muaj tus kab mob no.

Ib tug neeg uas muaj tus kab mob no yuav tsum xav li cas?

Yog tias koj raug kuaj pom tias muaj Eosinophilic Fasciitis, koj yuav tsum xav tias yuav tswj tau koj cov tsos mob ib ntus. Yog tias koj pom muaj kev hloov pauv hauv koj cov tsos mob, tshwj xeeb tshaj yog tias lawv hnyav zuj zus, nrog koj tus kws kho mob tham tam sim ntawd.

Zoo li peb tau hais ua ntej lawm, tsis muaj tshuaj kho qhov no. Muaj coob tus neeg nyob nrog nws tau ob peb xyoos, tom qab ntawd cov tsos mob ploj mus (mus rau 'kev zam txim'). Ib txhia neeg yeej tsis tau rov qab mob dua, tab sis lwm tus yuav muaj cov tsos mob rov qab los tom qab ('rov tshwm sim').

Koj puas yuav mus tsis tau haujlwm lossis mus kawm ntawv?

Yog tias koj ua tau koj txoj haujlwm lossis ua haujlwm hauv tsev kawm ntawv yam tsis muaj kev ntxhov siab ntau dhau rau koj cov fascia uas raug mob, koj yuav tsum rov qab mus ua haujlwm lossis kawm ntawv kom txog thaum koj zoo los ntawm Eosinophilic Fasciitis. Txawm li cas los xij, koj tus kws kho mob yuav qhia koj txog yam koj yuav tsum tsis txhob ua kom txog thaum koj zoo. Nws yog ib qho tseem ceeb uas yuav tsum ua raws li cov lus qhia no.

Nco ntsoov nrog koj tus kws kho mob tham thiab tau txais kev tso cai ua ntej rov pib ua cov kev ua ub ua no hnyav xws li khiav, tsa cov hnyav, lossis tawm dag zog.

Thaum twg koj yuav tsum mus ntsib kws kho mob?

• Yog tias koj pom muaj cov tsos mob tshiab hauv koj txhais tes, taw, lossis pob qij txha - tshwj xeeb tshaj yog tias koj muaj mob lossis o uas tsis ploj mus tom qab ob peb hnub so - mus ntsib kws kho mob tam sim ntawd.
• Yog tias koj twb tau kuaj pom tias muaj Eosinophilic Fasciitis lawm, qhia rau koj tus kws kho mob tam sim ntawd yog tias koj cov tsos mob hnyav zuj zus, lossis yog tias koj pom ib feem ntawm koj lub cev tawv lossis loog.

Thaum twg koj yuav tsum mus rau Chav Kho Mob Thaum Muaj Xwm Ceev (ETU) ?

Yog tias koj cia li tsis txav tau lossis siv ib feem ntawm koj lub cev tau, lossis yog tias koj mob heev, mus rau chav kho mob ceev uas nyob ze tshaj plaws tam sim ntawd .

Koj yuav tsum nug tus kws kho mob li cas?

Thaum koj mus ntsib kws kho mob, koj tuaj yeem nug cov lus nug zoo li no:

• Kuv puas muaj mob Eosinophilic Fasciitis, los yog nws puas yog lwm yam?
• Kuv cov tsos mob yuav hnyav zuj zus sai npaum li cas?
• Kuv xav tau kev kho mob hom twg? Kuv yuav tsum tau kho mob ntev npaum li cas?
• Kuv puas yuav tsum tau phais?
• Thaum twg kuv mam li rov qab ua ub ua no tau li qub?
• Qhov xwm txheej no cuam tshuam li cas rau kuv lub neej txhua hnub?

Qee yam tseem ceeb tshaj plaws uas peb yuav tsum nco ntsoov los ntawm zaj dab neeg no yog

Kab mob Eosinophilic fasciitis yog ib yam mob uas tsis tshua muaj tab sis loj heev uas tuaj yeem cuam tshuam rau koj sai sai. Yog tias koj pom qhov mob tshiab, o, lossis nruj hauv koj txhais tes lossis taw, tshwj xeeb tshaj yog tias nws tsis ploj mus hauv ob peb hnub, tsis txhob ncua mus ntsib kws kho mob. Vim tias qhov mob no tuaj yeem tshwm sim sai heev , qhov sai dua koj tau kuaj xyuas koj cov tsos mob, qhov sai dua koj tus kws kho mob tuaj yeem nrhiav tau qhov ua rau thiab pib kho mob tsim nyog.

Koj tus kws kho mob yuav ntxiv cov tshuaj corticosteroids thiab lwm yam kev kho mob yog tias xav tau los pab tswj koj cov tsos mob. Tsis txhob ntshai, tab sis yuav tsum paub txog koj cov tsos mob thiab ua raws li koj tus kws kho mob cov lus qhia kom zoo. Xav kom koj zoo sai sai!

` Eosinophilic Fasciitis, Eosinophilic Fasciitis, Cov Kab Mob Tawv Nqaij, Fascia, Mob Pob Qij Txha, Mob Nqaij, Cov Kab Mob Autoimmune