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Puas yog koj tus me nyuam lub plawv aorta nyob rau lwm qhov chaw? Cia peb kawm txog qhov '(Overriding Aorta)' no!

Puas yog koj tus me nyuam lub plawv aorta nyob rau lwm qhov chaw? Cia peb kawm txog qhov '(Overriding Aorta)' no!

Qee zaum peb cov menyuam yaus los rau hauv ntiaj teb no nrog kev hloov pauv me me hauv lawv lub siab. Nws yog ib qho ib txwm muaj rau koj, ua ib tug niam lossis ib tug txiv, yuav ntshai thiab txhawj xeeb heev thaum koj hnov ​​​​​​ib yam dab tsi zoo li ntawd. Tab sis tsis txhob txhawj, vim hnub no peb yuav tham txog ib qho mob hu ua "Overriding Aorta", uas yog ib qho kab mob plawv yug los. Peb yuav tham txog ntau yam hauv cov lus yooj yim, xws li qhov no yog dab tsi, vim li cas nws tshwm sim, cov tsos mob yog dab tsi, thiab kev kho mob yog dab tsi. Yog tias koj nkag siab cov no kom raug, nws yuav muab zog ntau rau koj los muab kev kho mob zoo tshaj plaws rau koj tus menyuam.

Qhov no yog dab tsi (Overriding Aorta)? Cia peb nkag siab yooj yim, puas yog?

Zoo, cia peb xub saib seb qhov '(Overriding Aorta)' no yog dab tsi. Hais yooj yim xwb, qhov no yog ib txoj hlab ntshav loj hauv peb tus menyuam lub plawv, lub aorta, uas nyob rau qhov chaw txawv me ntsis ntawm qhov chaw uas nws yuav tsum nyob.

Tam sim no saib seb, hauv lub plawv uas ib txwm noj qab nyob zoo, cov hlab ntsha loj no '(Aorta)' nyob rau sab laug ntawm lub plawv, uas yog, txuas nrog lub plawv sab laug. Koj puas paub dab tsi? Qhov ntawd yog qhov uas cov ntshav uas muaj oxygen ntau thiab huv si los ntawm lub ntsws tuaj yeem faib mus thoob plaws lub cev. Qhov ntawd yog nws txoj haujlwm tseem ceeb.

Tiam sis nyob rau hauv rooj plaub ntawm `(Overriding Aorta)`, lub aorta no nyob saum phab ntsa ntawm sab laug thiab sab xis ventricle ntawm lub plawv (qhov no hu ua `Ventricular Septum`), lossis saum ib lub qhov hauv phab ntsa ntawd (`Ventricular Septal Defect` lossis VSD). Xav txog, qhov tshwm sim ntawm no zoo li teeb tsa lub twj tso dej rau lub tank tsis raug.

Vim li no muaj dab tsi tshwm sim? Sab xis ntawm lub plawv muaj cov pa oxygen tsawg dua, uas txhais tau tias nws siv tag lawm, cov ntshav me ntsis "qias neeg". Vim yog lub qhov ('VSD') thiab lub aorta nyob rau qhov chaw tsis raug, qee cov ntshav uas tsis muaj pa oxygen no nkag mus rau hauv aorta thiab sib xyaw nrog cov ntshav uas ncig thoob plaws lub cev. Qhov no txhais tau tias cov pa oxygen hauv cov ntshav uas mus txog ntau qhov ntawm lub cev ntawm tus menyuam raug txo qis. Qhov no yog qhov teeb meem tseem ceeb.

Qhov kev sib raug zoo ntawm qhov no thiab tus mob hu ua '(Tetralogy of Fallot)' yog dab tsi?

Kev kov yeej Aorta tsis yog ib qho mob uas feem ntau tshwm sim ib leeg xwb. Nws yog ib qho ntawm plaub yam tseem ceeb ntawm tus kab mob plawv uas muaj txij thaum yug los hu ua Tetralogy of Fallot . "Tetralogy" txhais tau tias plaub. Yog li, hauv tus mob no, plaub qhov teeb meem plawv loj pom ua ke:

1. `(Kev Hloov Pauv Aorta)`: Lub aorta uas peb nyuam qhuav tham txog nyob rau hauv qhov chaw tsis yog lawm.

2. Qhov tsis zoo ntawm lub plawv sab laug thiab sab xis (VSD): Ib lub qhov hauv phab ntsa ntawm ob chav sab laug thiab sab xis ntawm lub plawv. Qhov no ua rau cov ntshav uas muaj oxygen ntau sib xyaw nrog cov ntshav uas tsis muaj oxygen ntau.

3. Mob Plawv Qaug: Cov hlab ntsha hauv lub ntsws, uas nqa cov ntshav uas muaj oxygen los ntawm sab xis ntawm lub plawv mus rau lub ntsws, raug thaiv lossis nws lub qhov ntswg, uas tsis qhib kom zoo, ua rau cov ntshav mus rau lub ntsws tsawg dua.

4. Phab ntsa ntawm lub plawv sab xis ua tuab ('Right Ventricular Hypertrophy'):Vim tias cov hlab ntsha hauv lub ntsws raug thaiv, lub plawv sab xis yuav tsum ua haujlwm hnyav dua los nqus cov ntshav. Ib yam li cov leeg nqaij loj dua thaum koj tawm dag zog, cov phab ntsa ntawm lub plawv sab no yuav tuab zuj zus.

Xav txog seb, zoo li tsis muaj phab ntsa ntawm thaj chaw haus luam yeeb thiab thaj chaw tsis haus luam yeeb hauv tsev noj mov. Tom qab ntawd cov pa luam yeeb yooj yim txav mus los ntawm ib qho chaw mus rau lwm qhov, thiab tsis muaj leej twg xis nyob. Qhov ntawd yog qhov tshwm sim hauv qhov xwm txheej '(Tetralogy of Fallot)' no. Cov ntshav uas muaj cov pa oxygen tsawg thiab cov ntshav uas muaj cov pa oxygen ntau sib xyaw ua ke.

Leej twg raug kev txom nyem tshaj plaws los ntawm tus mob no (Overriding Aorta)?

Tus mob no, hu ua "Tetralogy of Fallot", uas suav nrog "Overriding Aorta," feem ntau pom muaj nyob rau hauv cov menyuam tub ntau dua li cov menyuam ntxhais.

Tsis tas li ntawd xwb, cov menyuam mos uas muaj qee yam kev tsis zoo ntawm cov chromosomal, xws li Down syndrome, yuav muaj feem ntau dua rau kev mob Tetralogy of Fallot. Qhov teeb meem plawv no kuj tseem tuaj yeem pom nrog lwm yam mob tsis tshua muaj, xws li Apert syndrome thiab Williams syndrome.

Qhov teeb meem no feem ntau tshwm sim li cas?

Lawv hais tias muaj li ntawm ib tug ntawm txhua 100 tus menyuam mos uas yug los hauv ntiaj teb no yuav muaj qee yam teeb meem plawv txij thaum yug los. Thaum koj saib nws li ntawd, muaj li ntawm 10% ntawm cov menyuam mos uas muaj teeb meem plawv, uas yog, kwv yees li ntawm ib tug ntawm 3,000 tus menyuam mos, yuav muaj tus mob hu ua '(Tetralogy of Fallot)', uas suav nrog '(Overriding Aorta)'. Yog li, qhov no tsis yog ib qho uas pom ntau, tab sis nws yog ib qho mob uas cov kws kho mob feem ntau pom.

Cov tsos mob ntawm tus mob no yog dab tsi?

Tsis yog txhua tus menyuam mos uas muaj tus kab mob Tetralogy of Fallot muaj cov tsos mob zoo ib yam. Tej zaum yuav muaj cov tsos mob me me xwb, tiam sis lwm tus yuav muaj cov tsos mob hnyav heev. Qhov xwm txheej ntawm cov tsos mob no feem ntau nyob ntawm seb cov hlab ntsha hauv lub ntsws raug thaiv ntau npaum li cas. Uas yog, cov ntshav mus rau lub ntsws ntau npaum li cas. Yog tias tsis kho, cov tsos mob no yuav maj mam zuj zus tuaj.

Cov tsos mob me me

Qee tus menyuam mos yuav muaj cov tsos mob me me xws li cov no:

  • Xim tawv nqaij xiav ('Cyanosis'): Xim xiav no pom tseeb tshwj xeeb hauv cov cheeb tsam xws li daim di ncauj, tus nplaig, thiab cov rau tes. Qhov no yog vim muaj kev txo qis ntawm cov pa oxygen hauv cov ntshav.
  • Xav tias nkees sai: Koj tus menyuam yuav zoo li nkees sai tom qab ua si lossis pub niam mis.
  • Ua tsis taus pa: Tej zaum koj yuav ua tsis taus pa, tshwj xeeb tshaj yog thaum koj ua ub ua no.
  • Teeb meem kev noj mov thiab qhov hnyav nce: Tus me nyuam yuav tsis noj mov zoo thiab yuav tsis hnyav nce.

Cov tsos mob hnyav thiab `(Tet Spells)`

Qee zaum, cov pa oxygen ntawm tus menyuam poob qis tam sim ntawd, ua rau "Tet spells".Muaj ib qho mob txaus ntshai hu ua tet spell uas yuav tshwm sim tau. Qhov no yuav tshwm sim sai sai, kav ntev li ob peb feeb mus txog ob peb teev. Xav txog ib tug me nyuam mos uas tab tom ua si thiab mam li hloov xiav thiab ua pa nyuaj.

Cov tsos mob hnyav xws li cov no tuaj yeem pom thaum lub sijhawm Tet:

  • Daim tawv nqaij mam li hloov xiav tsaus.
  • Xav tias nkees heev, zoo li koj lub cev tsis muaj zog lawm.
  • Tej zaum yuav tsaus muag.
  • Qaug dab peg.
  • Ua pa nyuaj, ua pa sai.
  • Tus me nyuam yuav pib quaj tam sim ntawd thiab tom qab ntawd tuag.

Tom qab ua "tej lus qhuab qhia Tet" zoo li no, tus me nyuam yuav tsaug zog ntev heev. Cov "tej lus qhuab qhia Tet" no yog ib qho mob uas yuav tsum tau kho mob sai sai.

Vim li cas cov mob zoo li "Overriding Aorta" tshwm sim?

Qhov tseeb, feem ntau, nws nyuaj rau nrhiav qhov laj thawj tshwj xeeb rau cov teeb meem zoo li no thaum lub plawv ntawm tus menyuam mos loj hlob hauv plab. Qhov ntawd yog, qhov ua rau tsis meej ('tsis paub yog vim li cas'). Txawm li cas los xij, nws tau pom tias kwv yees li 25% ntawm cov menyuam mos uas muaj tus mob no '(Tetralogy of Fallot)' (uas suav nrog '(Overriding Aorta)') muaj qee qhov teeb meem yug los lossis teeb meem hauv lwm qhov ntawm lawv lub cev .

Cov kws kho mob kuaj mob li cas (Overriding Aorta)?

Thaum koj tus menyuam yug los, cov kws kho mob thiab cov kws tu mob hauv tsev kho mob yuav kuaj xyuas tus menyuam txoj kev noj qab haus huv. Tib lub sijhawm, lawv yuav ua tib zoo saib xyuas txhua yam teeb meem hauv lub plawv.

  • Kev ntsuas pa oxygen hauv cov ntshav: Muaj ib lub cuab yeej me me uas muab tso rau ntawm tus menyuam txhais tes lossis ceg kom ntsuas tau qhov oxygen hauv cov ntshav. Cov pa oxygen tsawg tuaj yeem yog ib qho cim qhia tias muaj kab mob plawv. Qhov no yog ib qho kev kuaj yooj yim thiab tsis mob.
  • Lub Plawv Qw: Thaum tus kws kho mob mloog tus menyuam lub plawv nrog lub stethoscope, yog tias muaj mob zoo li "Overriding Aorta", lub suab sib txawv, hu ua "lub plawv qwm" , yuav hnov ​​ntxiv rau lub plawv dhia ib txwm. Txawm li cas los xij, tsis yog txhua lub suab qwm yog qhov txaus ntshai, tab sis hauv qhov no, nws yog ib qho cim tseem ceeb.

Cov kev ntsuam xyuas kom paub tseeb

Yog tias muaj cov tsos mob saum toj no, cov kws kho mob yuav xaj kom kuaj xws li cov no los paub meej tias muaj mob thiab txiav txim siab qhov xwm txheej ntawm qhov teeb meem plawv:

  • Echocardiogram (Echo): Qhov no zoo li kev ntsuas ultrasound ntawm lub plawv. Nws tuaj yeem pom txhua yam meej meej los ntawm cov qauv ntawm lub plawv, kev ua haujlwm ntawm cov valves, txoj kev ntshav ntws, qhov loj ntawm VSD, thiab qhov chaw ntawm aorta. Qhov no yog qhov kev kuaj tseem ceeb los kuaj mob Tetralogy of Fallot.
  • Kev kuaj hluav taws xob ntawm lub plawv (ECG/EKG): Qhov no sau cov haujlwm hluav taws xob ntawm lub plawv. Nws tuaj yeem ntes tau tej yam xws li cov chav plawv loj thiab teeb meem ntawm lub plawv dhia.
  • X-ray hauv siab:Qhov no tuaj yeem muab ib lub tswv yim ntawm tej yam xws li qhov loj thiab cov duab ntawm lub plawv thiab seb cov ntshav mus rau lub ntsws puas tsawg dhau lossis ntau dhau.
  • Kev thaij duab Computed Tomography (CT) lossis MRI ntawm lub plawv: Qee zaum, cov kev kuaj no yuav ua yog tias xav tau cov ntaub ntawv ntxaws ntxiv txog lub plawv thiab cov hlab ntsha loj.
  • Kev Siv Txoj Hlab Ntswg Rau Lub Plawv: Hauv qhov no, ib lub raj nyias nyias (catheter) raug xa mus rau lub plawv los ntawm cov hlab ntsha hauv tus menyuam lub qhov ncauj lossis caj npab, qhov twg ntsuas qhov siab hauv lub plawv, ntsuas cov pa oxygen, thiab qee zaum txhaj tshuaj zas thiab thaij duab X-ray. Qhov no pab tau zoo heev rau kev soj ntsuam qhov mob ntawm lub plawv ua ntej phais.
  • Kev kuaj ntshav: Cov no pab xyuas tej yam xws li qib oxygen hauv cov ntshav thiab qhov ntau ntawm cov qe ntshav liab (Hemoglobin).

Yuav kho tus mob "(Overriding Aorta)" no li cas?

Txoj kev kho mob zoo tshaj plaws thiab tsuas yog kho mus tas li rau tus mob no (Tetralogy of Fallot) yog phais kom kho tag nrho plaub qhov tsis zoo hauv lub plawv. Feem ntau qhov no yog phais qhib lub plawv .

  • Lub Sijhawm Phais: Feem ntau, cov kws kho mob pom zoo kom ua qhov kev phais no ua ntej tus menyuam muaj 6 lub hlis, lossis hauv thawj xyoo . Muaj tej lub sijhawm uas yuav ua tau ua ntej dua rau qee tus menyuam, nyob ntawm tus menyuam tus mob.
  • Muaj dab tsi tshwm sim thaum lub sijhawm phais?: Tus kws phais yuav kaw lub qhov hauv phab ntsa ntawm cov hlab ntsha hauv lub plawv (VSD) nrog ib daim ntaub tshwj xeeb. Nws kuj tshem tawm qhov txhaws hauv cov hlab ntsha hauv lub ntsws thiab lub valve, ua rau cov ntshav ntws tau zoo. Thaum cov no raug kho, qhov teeb meem ntawm cov hlab ntsha aorta uas hla dhau thiab qhov tuab ntawm cov hlab ntsha sab xis tau daws teeb meem.
  • Kev Tshem Tawm Ib Ntus: Qee tus menyuam mos me heev, lossis lawv cov hlab ntsha hauv lub ntsws me heev, yog li nws yuav nyuaj rau ua qhov kev phais tag nrho tam sim ntawd. Hauv cov xwm txheej zoo li no, tus kws phais yuav muab ib qho kev tshem tawm ib ntus. Qhov no suav nrog kev rho ib ceg ntawm tus menyuam lub aorta lossis lwm cov hlab ntsha loj thiab txuas nws mus rau cov hlab ntsha hauv lub ntsws. Qhov no ua rau cov ntshav ntau ntxiv mus rau hauv lub ntsws, muab kev pab kom txog thaum tus menyuam loj me ntsis thiab tuaj yeem ua tiav tag nrho kev phais.

Cov kws kho mob tau ua qhov kev phais plawv qhib no los kho Tetralogy of Fallot txij li xyoo 1950, yog li nws yog ib qho kev phais mob uas tau tsim muaj zoo hauv kev kho mob.

Cov hom tshuaj siv

Ntxiv rau kev phais mob, qee cov tshuaj kuj siv los tswj cov tsos mob thiab tiv thaiv cov teeb meem:

  • Cov tshuaj Beta-blocker (piv txwv li Propranolol): Cov no pab tiv thaiv cov kab mob Tet txaus ntshai kom tsis txhob tshwm sim thiab txo qhov hnyav yog tias lawv tshwm sim.
  • Cov tshuaj diuretics: Cov no pab txo cov kua dej tsis tsim nyog hauv lub cev thiab txo qhov siab ntawm lub plawv (hauv cov mob xws li lub plawv tsis ua haujlwm).
  • `(Tshuaj tua kab mob)` (Tshuaj tua kab mob):Cov menyuam mos uas muaj hom kab mob plawv no muaj feem yuav kis tau kab mob rau sab hauv ntawm lub plawv ('Infective Endocarditis'), tshwj xeeb tshaj yog thaum lub sijhawm kho mob xws li rho hniav. Yog li ntawd, cov tshuaj no yog muab los tiv thaiv cov kab mob no.

Puas muaj teeb meem dab tsi nrog kev kho mob?

Txawm tias qhov kev phais mob ua tiav los xij, qee qhov teeb meem yuav tshwm sim raws sijhawm.

  • Thaum kho Tetralogy of Fallot, cov kws phais ua rau lub qhov ntswg ntawm lub ntsws yoog tau me ntsis, yog li ntawd ntau tus neeg yuav muaj cov ntshav me ntsis ntws rov qab los ntawm lub qhov ntswg ntawd (pulmonary regurgitation).
  • Qhov no ua rau muaj kev pheej hmoo ntawm kev muaj teeb meem plawv dhia (arrhythmias).
  • Raws li lub sijhawm dhau mus, qhov xau ntawm lub plawv no yuav nce ntxiv, ua rau sab xis ntawm lub plawv ntxhov siab ntxiv, ua rau qhov ntawd loj zuj zus, thiab tuaj yeem ua rau lub plawv tsis ua haujlwm.
  • Xyoo tom qab phais lawm, tej yam xws li lub plawv aorta loj (aortic root dilatation) lossis lub tricuspid valve xau tuaj yeem tshwm sim. Yog tias qhov no tshwm sim, koj yuav xav tau kev phais ntxiv lossis lwm yam kev kho mob. Yog vim li ntawd nws thiaj li tseem ceeb uas yuav tsum tau mus kuaj xyuas tsis tu ncua.

Yuav ua li cas thiaj tswj tau cov tsos mob ntawm tus menyuam kom txog thaum phais?

Txog thaum phais tiav, cov kws kho mob yuav ua cov hauv qab no los tswj cov tsos mob ntawm tus menyuam thiab muab kev nplij siab rau tus menyuam:

  • Yog tias tsim nyog, muab cov tshuaj kho mob plawv (piv txwv li, beta-blockers).
  • Xyuas kom tus me nyuam tau txais dej thiab khoom noj txaus.
  • Xyuas cov ntshav hemoglobin tsis tu ncua thiab, yog tias tsim nyog, muab cov kua txiv uas muaj hlau (kom tiv thaiv kev mob ntshav tsis txaus).
  • Tsis txhob ua tej yam uas ua rau tus menyuam nyuaj siab heev, xws li quaj ntev ntev.
  • Yog tias muaj "kev ua koob tsheej tet," tuav tus menyuam lub hauv caug ze rau nws lub hauv siab (qhov "kev sawv ntawm lub hauv caug thiab lub hauv siab") yuav pab tau. Koj tus kws kho mob yuav qhia koj yuav ua li cas.

Puas yuav txo tau qhov kev pheej hmoo ntawm qhov no?

Txawm hais tias feem ntau tsis paub meej tias yog dab tsi ua rau muaj kab mob plawv rau cov menyuam mos, cov kws tshawb fawb ntseeg tias leej niam txoj kev noj qab haus huv thiab kev ua neej thaum cev xeeb tub tuaj yeem cuam tshuam rau nws. Cov yam hauv qab no tuaj yeem ua rau muaj kev pheej hmoo ntawm tus menyuam yaus uas muaj kab mob plawv:

  • Muaj kab mob plawv txij thaum yug los rau hauv niam, txiv, lossis lwm tus neeg hauv tsev neeg.
  • Niam haus luam yeeb thaum cev xeeb tub.
  • Thaum cev xeeb tub, leej niam muaj tus kab mob hu ua "Rubella" (German measles).
  • Niam muaj tus kab mob ntshav qab zib uas tsis tswj tau.
  • Noj qee yam tshuaj (piv txwv li, qee yam tshuaj qaug dab peg) thaum peb lub hlis thawj zaug ntawm cev xeeb tub.
  • Niam haus dej cawv.
  • Kev tsis txaus noj haus thaum cev xeeb tub.
  • Niam muaj hnub nyoog tshaj 40 xyoo thaum cev xeeb tub.

Yog li ntawd, txhawm rau txo qhov kev pheej hmoo no hauv kev cev xeeb tub yav tom ntej, nws yog ib qho tseem ceeb heev uas yuav tsum saib xyuas koj txoj kev noj qab haus huv ua ntej cev xeeb tub, tswj cov mob uas twb muaj lawm (xws li ntshav qab zib), tsis txhob haus luam yeeb thiab haus cawv kiag li, thiab tsis txhob noj tshuaj yam tsis tau kev pom zoo los ntawm koj tus kws kho mob. Yog tias leej twg hauv koj tsev neeg muaj kab mob plawv, nws tseem yog ib qho zoo kom nrhiav kev qhia los ntawm tus kws pab tswv yim txog caj ces.

Tus menyuam uas muaj '(Overriding Aorta)' yuav xav tau lub neej yav tom ntej zoo li cas?

Qhov no yuav zoo li ntshai rau koj, tab sis qhov tseeb yog, feem ntau cov menyuam mos mus ua neej zoo li qub, noj qab nyob zoo tom qab phais.

  • Ntau tshaj 90% ntawm cov menyuam mos uas tau phais mob Tetralogy of Fallot (uas suav nrog Overriding Aorta) loj hlob zoo thiab ua neej nyob zoo li qub. Lawv mus kawm ntawv, ua si, ua haujlwm, thiab muaj tsev neeg. Ib txhia nyob kaj siab lug txog thaum lawv muaj hnub nyoog 70 thiab 80 xyoo.
  • Txawm li cas los xij, yog tias tsis phais, qhov mob no yuav txaus ntshai heev. Yog tias qhov ntawd tshwm sim, cov tsos mob yuav hnyav zuj zus tuaj, ua rau koj lub neej luv dua. Tej zaum koj yuav tsis nyob txog 20 xyoo.

Yog li ntawd, qhov tseem ceeb tshaj plaws yog muab kev kho mob kom raug rau lub sijhawm zoo.

Yuav saib xyuas tus menyuam li cas tom qab phais?

Thaum koj coj koj tus menyuam los tsev tom qab phais lawm, koj muaj lub luag haujlwm loj heev.

  • Mus ntsib kws kho mob plawv tsis tu ncua: Koj tus menyuam yuav tsum tau mus ntsib kws kho mob plawv tsis tu ncua. Thaum xub thawj tej zaum yuav mus ntsib ntau zaus dua, thiab tom qab ntawd yuav mus ntsib ntau zaus dua. Tsis txhob hla cov no.
  • Tiv thaiv kab mob ua pa: Cov menyuam yaus uas tau phais plawv zoo li no tuaj yeem kis kab mob ua pa, uas tuaj yeem ua rau muaj teeb meem sai sai. Yog li ntawd, khaws koj tus menyuam kom deb ntawm cov neeg mob khaub thuas thiab kub taub hau. Yog tias muaj kab mob zoo li no tshwm sim, nrhiav kev kho mob tam sim ntawd.
  • Tshuaj tua kab mob: Cov kws kho mob yuav pom zoo kom siv tshuaj tua kab mob ua ntej qee qhov kev kho hniav lossis lwm yam kev phais me me kom tiv thaiv kev kis kab mob plawv (endocarditis). Nug koj tus kws kho mob txog qhov no.
  • Kev Noj Haus thiab Kev Loj Hlob: Saib xyuas koj tus menyuam txoj kev noj haus thiab kev loj hlob.
  • Tej Yam Ua Si: Thaum koj tus me nyuam loj hlob tuaj, nrog koj tus kws kho mob tham txog tej yam ua si thiab kev ua si uas nws ua tau. Feem ntau, nws ua tau txhua yam li qub.

Thaum peb laus zuj zus, tej zaum yuav muaj teeb meem plawv tshiab tshwm sim, yog li nws tseem ceeb heev uas yuav tsum tau mus kuaj mob plawv ntxiv mus txog thaum peb laus zuj zus.

Kuv yuav tsum mus ntsib kws kho mob thaum twg?

Yog koj tus menyuam muaj ib qho ntawm cov tsos mob no, mus ntsib kws kho mob lossis coj nws mus rau tsev kho mob tam sim ntawd:

  • Yog tias muaj cov tsos mob tshiab tshwm sim.
  • Yog tias koj daim tawv nqaij, daim di ncauj, thiab tus nplaig zoo li tig xiav.
  • Yog koj ua pa nyuaj.
  • Yog koj tsis kam haus mis los yog noj zaub mov.
  • Yog koj zoo li nkees sai sai.

Kuv yuav tsum mus rau chav kho mob ceev (ER) thaum twg?

Yog tias koj tus menyuam muaj "Tet spell" hnyav heev, uas txhais tau tias lawv hloov xiav tam sim ntawd, ua pa nyuaj, lossis yuav tsaus muag, hu rau 911 tam sim ntawd lossis coj lawv mus rau chav kho mob ceev ntawm lub tsev kho mob ze tshaj plaws. Nyob ntawd, lawv tuaj yeem tau txais oxygen thiab / lossis tshuaj xws li "Morphine" los tswj tus mob.

Kuv yuav tsum nug kuv tus kws kho mob li cas?

Thaum lub sijhawm zoo li no, tej zaum koj yuav muaj ntau lo lus nug hauv koj lub siab. Tsis txhob ntshai nug koj tus kws kho mob txog cov no:

  • Kuv puas yuav tsum txwv kuv tus menyuam txoj kev ua si lossis lwm yam kev ua ub no?
  • Kuv tus menyuam yuav tsum tuaj kuaj mob ntau npaum li cas?
  • Puas yuav tsum tau phais kuv tus menyuam ntxiv? Yog tias tau, yuav tsum tau phais thaum twg?
  • Yuav muaj teeb meem dab tsi tshwm sim mus ntev? Yuav ua li cas thiaj tiv thaiv tau?
  • Yuav tsum muab cov tshuaj twg rau tus menyuam? Yuav tsum muab ntev npaum li cas? Puas muaj cov kev mob tshwm sim?

Cov yam tseem ceeb tshaj plaws uas peb xav coj los tsev los ntawm zaj dab neeg no yog

Zoo, peb tau tham ntau txog Overriding Aorta thiab Tetralogy of Fallot. Tej zaum koj yuav xav tias muaj kev nyuaj siab heev tam sim no. Tab sis, nco ntsoov cov no:

  • Kev hla dhau Aorta yog ib qho teeb meem plawv uas muaj txij thaum yug los hu ua Tetralogy of Fallot. Qhov no yog thaum tus menyuam lub aorta tsis sib luag, ua rau cov ntshav tsis muaj oxygen txaus ntws thoob plaws lub cev.
  • Cov tsos mob yuav muaj xws li daim tawv nqaij xiav, qaug zog sai, ua pa nyuaj, thiab "Tet spells" txaus ntshai.
  • Qhov mob no kho tau zoo los ntawm kev phais. Cov kws phais tau ua qhov kev phais no tau zoo heev rau ntau xyoo lawm.
  • Tom qab phais lawm, ntau tus menyuam mos muaj lub neej noj qab nyob zoo thiab zoo li qub.
  • Kev kuaj mob tsis tu ncua thiab ua raws li cov lus qhia kho mob yog qhov tseem ceeb tshaj plaws. Koj tsis yog tib tug hauv txoj kev no. Muaj cov kws kho mob, cov kws tu mob, thiab cov neeg ua haujlwm kho mob uas muaj peev xwm los pab thiab coj koj thiab koj tus menyuam. Yog li ntawd, cia li ua siab loj.

Yog koj tus menyuam mos tseem tos kev phais, nco ntsoov nug tus kws kho mob thiab cov neeg ua haujlwm saib xyuas menyuam txog tej yam koj ua tau los pab koj tus menyuam thaum lub sijhawm phais, thiab yuav ua li cas yog tias muaj "tet spell". Qhov kev paub ntawd yuav pab tau koj zoo heev.


` hla lub aorta, tetralogy of fallot, qhov tsis zoo ntawm lub plawv txij thaum yug los, qhov tsis zoo ntawm lub ventricular septal, cyanosis, tet spells, phais plawv qhib, kab mob plawv, cov menyuam yug los tsis zoo, tus menyuam xiav, tetralogy of fallot, phais plawv, kab mob plawv menyuam yaus

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.

Ntxiv koj cov lus

Thov xam: 1 + 4 =
Puas yog koj tus me nyuam lub plawv aorta nyob rau lwm qhov chaw? Cia peb kawm txog qhov '(Overriding Aorta)' no!

Puas yog koj tus me nyuam lub plawv aorta nyob rau lwm qhov chaw? Cia peb kawm txog qhov '(Overriding Aorta)' no!

Qee zaum peb cov menyuam yaus los rau hauv ntiaj teb no nrog kev hloov pauv me me hauv lawv lub siab. Nws yog ib qho ib txwm muaj rau koj, ua ib tug niam lossis ib tug txiv, yuav ntshai thiab txhawj xeeb heev thaum koj hnov ​​​​​​ib yam dab tsi zoo li ntawd. Tab sis tsis txhob txhawj, vim hnub no peb yuav tham txog ib qho mob hu ua "Overriding Aorta", uas yog ib qho kab mob plawv yug los. Peb yuav tham txog ntau yam hauv cov lus yooj yim, xws li qhov no yog dab tsi, vim li cas nws tshwm sim, cov tsos mob yog dab tsi, thiab kev kho mob yog dab tsi. Yog tias koj nkag siab cov no kom raug, nws yuav muab zog ntau rau koj los muab kev kho mob zoo tshaj plaws rau koj tus menyuam.

Qhov no yog dab tsi (Overriding Aorta)? Cia peb nkag siab yooj yim, puas yog?

Zoo, cia peb xub saib seb qhov '(Overriding Aorta)' no yog dab tsi. Hais yooj yim xwb, qhov no yog ib txoj hlab ntshav loj hauv peb tus menyuam lub plawv, lub aorta, uas nyob rau qhov chaw txawv me ntsis ntawm qhov chaw uas nws yuav tsum nyob.

Tam sim no saib seb, hauv lub plawv uas ib txwm noj qab nyob zoo, cov hlab ntsha loj no '(Aorta)' nyob rau sab laug ntawm lub plawv, uas yog, txuas nrog lub plawv sab laug. Koj puas paub dab tsi? Qhov ntawd yog qhov uas cov ntshav uas muaj oxygen ntau thiab huv si los ntawm lub ntsws tuaj yeem faib mus thoob plaws lub cev. Qhov ntawd yog nws txoj haujlwm tseem ceeb.

Tiam sis nyob rau hauv rooj plaub ntawm `(Overriding Aorta)`, lub aorta no nyob saum phab ntsa ntawm sab laug thiab sab xis ventricle ntawm lub plawv (qhov no hu ua `Ventricular Septum`), lossis saum ib lub qhov hauv phab ntsa ntawd (`Ventricular Septal Defect` lossis VSD). Xav txog, qhov tshwm sim ntawm no zoo li teeb tsa lub twj tso dej rau lub tank tsis raug.

Vim li no muaj dab tsi tshwm sim? Sab xis ntawm lub plawv muaj cov pa oxygen tsawg dua, uas txhais tau tias nws siv tag lawm, cov ntshav me ntsis "qias neeg". Vim yog lub qhov ('VSD') thiab lub aorta nyob rau qhov chaw tsis raug, qee cov ntshav uas tsis muaj pa oxygen no nkag mus rau hauv aorta thiab sib xyaw nrog cov ntshav uas ncig thoob plaws lub cev. Qhov no txhais tau tias cov pa oxygen hauv cov ntshav uas mus txog ntau qhov ntawm lub cev ntawm tus menyuam raug txo qis. Qhov no yog qhov teeb meem tseem ceeb.

Qhov kev sib raug zoo ntawm qhov no thiab tus mob hu ua '(Tetralogy of Fallot)' yog dab tsi?

Kev kov yeej Aorta tsis yog ib qho mob uas feem ntau tshwm sim ib leeg xwb. Nws yog ib qho ntawm plaub yam tseem ceeb ntawm tus kab mob plawv uas muaj txij thaum yug los hu ua Tetralogy of Fallot . "Tetralogy" txhais tau tias plaub. Yog li, hauv tus mob no, plaub qhov teeb meem plawv loj pom ua ke:

1. `(Kev Hloov Pauv Aorta)`: Lub aorta uas peb nyuam qhuav tham txog nyob rau hauv qhov chaw tsis yog lawm.

2. Qhov tsis zoo ntawm lub plawv sab laug thiab sab xis (VSD): Ib lub qhov hauv phab ntsa ntawm ob chav sab laug thiab sab xis ntawm lub plawv. Qhov no ua rau cov ntshav uas muaj oxygen ntau sib xyaw nrog cov ntshav uas tsis muaj oxygen ntau.

3. Mob Plawv Qaug: Cov hlab ntsha hauv lub ntsws, uas nqa cov ntshav uas muaj oxygen los ntawm sab xis ntawm lub plawv mus rau lub ntsws, raug thaiv lossis nws lub qhov ntswg, uas tsis qhib kom zoo, ua rau cov ntshav mus rau lub ntsws tsawg dua.

4. Phab ntsa ntawm lub plawv sab xis ua tuab ('Right Ventricular Hypertrophy'):Vim tias cov hlab ntsha hauv lub ntsws raug thaiv, lub plawv sab xis yuav tsum ua haujlwm hnyav dua los nqus cov ntshav. Ib yam li cov leeg nqaij loj dua thaum koj tawm dag zog, cov phab ntsa ntawm lub plawv sab no yuav tuab zuj zus.

Xav txog seb, zoo li tsis muaj phab ntsa ntawm thaj chaw haus luam yeeb thiab thaj chaw tsis haus luam yeeb hauv tsev noj mov. Tom qab ntawd cov pa luam yeeb yooj yim txav mus los ntawm ib qho chaw mus rau lwm qhov, thiab tsis muaj leej twg xis nyob. Qhov ntawd yog qhov tshwm sim hauv qhov xwm txheej '(Tetralogy of Fallot)' no. Cov ntshav uas muaj cov pa oxygen tsawg thiab cov ntshav uas muaj cov pa oxygen ntau sib xyaw ua ke.

Leej twg raug kev txom nyem tshaj plaws los ntawm tus mob no (Overriding Aorta)?

Tus mob no, hu ua "Tetralogy of Fallot", uas suav nrog "Overriding Aorta," feem ntau pom muaj nyob rau hauv cov menyuam tub ntau dua li cov menyuam ntxhais.

Tsis tas li ntawd xwb, cov menyuam mos uas muaj qee yam kev tsis zoo ntawm cov chromosomal, xws li Down syndrome, yuav muaj feem ntau dua rau kev mob Tetralogy of Fallot. Qhov teeb meem plawv no kuj tseem tuaj yeem pom nrog lwm yam mob tsis tshua muaj, xws li Apert syndrome thiab Williams syndrome.

Qhov teeb meem no feem ntau tshwm sim li cas?

Lawv hais tias muaj li ntawm ib tug ntawm txhua 100 tus menyuam mos uas yug los hauv ntiaj teb no yuav muaj qee yam teeb meem plawv txij thaum yug los. Thaum koj saib nws li ntawd, muaj li ntawm 10% ntawm cov menyuam mos uas muaj teeb meem plawv, uas yog, kwv yees li ntawm ib tug ntawm 3,000 tus menyuam mos, yuav muaj tus mob hu ua '(Tetralogy of Fallot)', uas suav nrog '(Overriding Aorta)'. Yog li, qhov no tsis yog ib qho uas pom ntau, tab sis nws yog ib qho mob uas cov kws kho mob feem ntau pom.

Cov tsos mob ntawm tus mob no yog dab tsi?

Tsis yog txhua tus menyuam mos uas muaj tus kab mob Tetralogy of Fallot muaj cov tsos mob zoo ib yam. Tej zaum yuav muaj cov tsos mob me me xwb, tiam sis lwm tus yuav muaj cov tsos mob hnyav heev. Qhov xwm txheej ntawm cov tsos mob no feem ntau nyob ntawm seb cov hlab ntsha hauv lub ntsws raug thaiv ntau npaum li cas. Uas yog, cov ntshav mus rau lub ntsws ntau npaum li cas. Yog tias tsis kho, cov tsos mob no yuav maj mam zuj zus tuaj.

Cov tsos mob me me

Qee tus menyuam mos yuav muaj cov tsos mob me me xws li cov no:

  • Xim tawv nqaij xiav ('Cyanosis'): Xim xiav no pom tseeb tshwj xeeb hauv cov cheeb tsam xws li daim di ncauj, tus nplaig, thiab cov rau tes. Qhov no yog vim muaj kev txo qis ntawm cov pa oxygen hauv cov ntshav.
  • Xav tias nkees sai: Koj tus menyuam yuav zoo li nkees sai tom qab ua si lossis pub niam mis.
  • Ua tsis taus pa: Tej zaum koj yuav ua tsis taus pa, tshwj xeeb tshaj yog thaum koj ua ub ua no.
  • Teeb meem kev noj mov thiab qhov hnyav nce: Tus me nyuam yuav tsis noj mov zoo thiab yuav tsis hnyav nce.

Cov tsos mob hnyav thiab `(Tet Spells)`

Qee zaum, cov pa oxygen ntawm tus menyuam poob qis tam sim ntawd, ua rau "Tet spells".Muaj ib qho mob txaus ntshai hu ua tet spell uas yuav tshwm sim tau. Qhov no yuav tshwm sim sai sai, kav ntev li ob peb feeb mus txog ob peb teev. Xav txog ib tug me nyuam mos uas tab tom ua si thiab mam li hloov xiav thiab ua pa nyuaj.

Cov tsos mob hnyav xws li cov no tuaj yeem pom thaum lub sijhawm Tet:

  • Daim tawv nqaij mam li hloov xiav tsaus.
  • Xav tias nkees heev, zoo li koj lub cev tsis muaj zog lawm.
  • Tej zaum yuav tsaus muag.
  • Qaug dab peg.
  • Ua pa nyuaj, ua pa sai.
  • Tus me nyuam yuav pib quaj tam sim ntawd thiab tom qab ntawd tuag.

Tom qab ua "tej lus qhuab qhia Tet" zoo li no, tus me nyuam yuav tsaug zog ntev heev. Cov "tej lus qhuab qhia Tet" no yog ib qho mob uas yuav tsum tau kho mob sai sai.

Vim li cas cov mob zoo li "Overriding Aorta" tshwm sim?

Qhov tseeb, feem ntau, nws nyuaj rau nrhiav qhov laj thawj tshwj xeeb rau cov teeb meem zoo li no thaum lub plawv ntawm tus menyuam mos loj hlob hauv plab. Qhov ntawd yog, qhov ua rau tsis meej ('tsis paub yog vim li cas'). Txawm li cas los xij, nws tau pom tias kwv yees li 25% ntawm cov menyuam mos uas muaj tus mob no '(Tetralogy of Fallot)' (uas suav nrog '(Overriding Aorta)') muaj qee qhov teeb meem yug los lossis teeb meem hauv lwm qhov ntawm lawv lub cev .

Cov kws kho mob kuaj mob li cas (Overriding Aorta)?

Thaum koj tus menyuam yug los, cov kws kho mob thiab cov kws tu mob hauv tsev kho mob yuav kuaj xyuas tus menyuam txoj kev noj qab haus huv. Tib lub sijhawm, lawv yuav ua tib zoo saib xyuas txhua yam teeb meem hauv lub plawv.

  • Kev ntsuas pa oxygen hauv cov ntshav: Muaj ib lub cuab yeej me me uas muab tso rau ntawm tus menyuam txhais tes lossis ceg kom ntsuas tau qhov oxygen hauv cov ntshav. Cov pa oxygen tsawg tuaj yeem yog ib qho cim qhia tias muaj kab mob plawv. Qhov no yog ib qho kev kuaj yooj yim thiab tsis mob.
  • Lub Plawv Qw: Thaum tus kws kho mob mloog tus menyuam lub plawv nrog lub stethoscope, yog tias muaj mob zoo li "Overriding Aorta", lub suab sib txawv, hu ua "lub plawv qwm" , yuav hnov ​​ntxiv rau lub plawv dhia ib txwm. Txawm li cas los xij, tsis yog txhua lub suab qwm yog qhov txaus ntshai, tab sis hauv qhov no, nws yog ib qho cim tseem ceeb.

Cov kev ntsuam xyuas kom paub tseeb

Yog tias muaj cov tsos mob saum toj no, cov kws kho mob yuav xaj kom kuaj xws li cov no los paub meej tias muaj mob thiab txiav txim siab qhov xwm txheej ntawm qhov teeb meem plawv:

  • Echocardiogram (Echo): Qhov no zoo li kev ntsuas ultrasound ntawm lub plawv. Nws tuaj yeem pom txhua yam meej meej los ntawm cov qauv ntawm lub plawv, kev ua haujlwm ntawm cov valves, txoj kev ntshav ntws, qhov loj ntawm VSD, thiab qhov chaw ntawm aorta. Qhov no yog qhov kev kuaj tseem ceeb los kuaj mob Tetralogy of Fallot.
  • Kev kuaj hluav taws xob ntawm lub plawv (ECG/EKG): Qhov no sau cov haujlwm hluav taws xob ntawm lub plawv. Nws tuaj yeem ntes tau tej yam xws li cov chav plawv loj thiab teeb meem ntawm lub plawv dhia.
  • X-ray hauv siab:Qhov no tuaj yeem muab ib lub tswv yim ntawm tej yam xws li qhov loj thiab cov duab ntawm lub plawv thiab seb cov ntshav mus rau lub ntsws puas tsawg dhau lossis ntau dhau.
  • Kev thaij duab Computed Tomography (CT) lossis MRI ntawm lub plawv: Qee zaum, cov kev kuaj no yuav ua yog tias xav tau cov ntaub ntawv ntxaws ntxiv txog lub plawv thiab cov hlab ntsha loj.
  • Kev Siv Txoj Hlab Ntswg Rau Lub Plawv: Hauv qhov no, ib lub raj nyias nyias (catheter) raug xa mus rau lub plawv los ntawm cov hlab ntsha hauv tus menyuam lub qhov ncauj lossis caj npab, qhov twg ntsuas qhov siab hauv lub plawv, ntsuas cov pa oxygen, thiab qee zaum txhaj tshuaj zas thiab thaij duab X-ray. Qhov no pab tau zoo heev rau kev soj ntsuam qhov mob ntawm lub plawv ua ntej phais.
  • Kev kuaj ntshav: Cov no pab xyuas tej yam xws li qib oxygen hauv cov ntshav thiab qhov ntau ntawm cov qe ntshav liab (Hemoglobin).

Yuav kho tus mob "(Overriding Aorta)" no li cas?

Txoj kev kho mob zoo tshaj plaws thiab tsuas yog kho mus tas li rau tus mob no (Tetralogy of Fallot) yog phais kom kho tag nrho plaub qhov tsis zoo hauv lub plawv. Feem ntau qhov no yog phais qhib lub plawv .

  • Lub Sijhawm Phais: Feem ntau, cov kws kho mob pom zoo kom ua qhov kev phais no ua ntej tus menyuam muaj 6 lub hlis, lossis hauv thawj xyoo . Muaj tej lub sijhawm uas yuav ua tau ua ntej dua rau qee tus menyuam, nyob ntawm tus menyuam tus mob.
  • Muaj dab tsi tshwm sim thaum lub sijhawm phais?: Tus kws phais yuav kaw lub qhov hauv phab ntsa ntawm cov hlab ntsha hauv lub plawv (VSD) nrog ib daim ntaub tshwj xeeb. Nws kuj tshem tawm qhov txhaws hauv cov hlab ntsha hauv lub ntsws thiab lub valve, ua rau cov ntshav ntws tau zoo. Thaum cov no raug kho, qhov teeb meem ntawm cov hlab ntsha aorta uas hla dhau thiab qhov tuab ntawm cov hlab ntsha sab xis tau daws teeb meem.
  • Kev Tshem Tawm Ib Ntus: Qee tus menyuam mos me heev, lossis lawv cov hlab ntsha hauv lub ntsws me heev, yog li nws yuav nyuaj rau ua qhov kev phais tag nrho tam sim ntawd. Hauv cov xwm txheej zoo li no, tus kws phais yuav muab ib qho kev tshem tawm ib ntus. Qhov no suav nrog kev rho ib ceg ntawm tus menyuam lub aorta lossis lwm cov hlab ntsha loj thiab txuas nws mus rau cov hlab ntsha hauv lub ntsws. Qhov no ua rau cov ntshav ntau ntxiv mus rau hauv lub ntsws, muab kev pab kom txog thaum tus menyuam loj me ntsis thiab tuaj yeem ua tiav tag nrho kev phais.

Cov kws kho mob tau ua qhov kev phais plawv qhib no los kho Tetralogy of Fallot txij li xyoo 1950, yog li nws yog ib qho kev phais mob uas tau tsim muaj zoo hauv kev kho mob.

Cov hom tshuaj siv

Ntxiv rau kev phais mob, qee cov tshuaj kuj siv los tswj cov tsos mob thiab tiv thaiv cov teeb meem:

  • Cov tshuaj Beta-blocker (piv txwv li Propranolol): Cov no pab tiv thaiv cov kab mob Tet txaus ntshai kom tsis txhob tshwm sim thiab txo qhov hnyav yog tias lawv tshwm sim.
  • Cov tshuaj diuretics: Cov no pab txo cov kua dej tsis tsim nyog hauv lub cev thiab txo qhov siab ntawm lub plawv (hauv cov mob xws li lub plawv tsis ua haujlwm).
  • `(Tshuaj tua kab mob)` (Tshuaj tua kab mob):Cov menyuam mos uas muaj hom kab mob plawv no muaj feem yuav kis tau kab mob rau sab hauv ntawm lub plawv ('Infective Endocarditis'), tshwj xeeb tshaj yog thaum lub sijhawm kho mob xws li rho hniav. Yog li ntawd, cov tshuaj no yog muab los tiv thaiv cov kab mob no.

Puas muaj teeb meem dab tsi nrog kev kho mob?

Txawm tias qhov kev phais mob ua tiav los xij, qee qhov teeb meem yuav tshwm sim raws sijhawm.

  • Thaum kho Tetralogy of Fallot, cov kws phais ua rau lub qhov ntswg ntawm lub ntsws yoog tau me ntsis, yog li ntawd ntau tus neeg yuav muaj cov ntshav me ntsis ntws rov qab los ntawm lub qhov ntswg ntawd (pulmonary regurgitation).
  • Qhov no ua rau muaj kev pheej hmoo ntawm kev muaj teeb meem plawv dhia (arrhythmias).
  • Raws li lub sijhawm dhau mus, qhov xau ntawm lub plawv no yuav nce ntxiv, ua rau sab xis ntawm lub plawv ntxhov siab ntxiv, ua rau qhov ntawd loj zuj zus, thiab tuaj yeem ua rau lub plawv tsis ua haujlwm.
  • Xyoo tom qab phais lawm, tej yam xws li lub plawv aorta loj (aortic root dilatation) lossis lub tricuspid valve xau tuaj yeem tshwm sim. Yog tias qhov no tshwm sim, koj yuav xav tau kev phais ntxiv lossis lwm yam kev kho mob. Yog vim li ntawd nws thiaj li tseem ceeb uas yuav tsum tau mus kuaj xyuas tsis tu ncua.

Yuav ua li cas thiaj tswj tau cov tsos mob ntawm tus menyuam kom txog thaum phais?

Txog thaum phais tiav, cov kws kho mob yuav ua cov hauv qab no los tswj cov tsos mob ntawm tus menyuam thiab muab kev nplij siab rau tus menyuam:

  • Yog tias tsim nyog, muab cov tshuaj kho mob plawv (piv txwv li, beta-blockers).
  • Xyuas kom tus me nyuam tau txais dej thiab khoom noj txaus.
  • Xyuas cov ntshav hemoglobin tsis tu ncua thiab, yog tias tsim nyog, muab cov kua txiv uas muaj hlau (kom tiv thaiv kev mob ntshav tsis txaus).
  • Tsis txhob ua tej yam uas ua rau tus menyuam nyuaj siab heev, xws li quaj ntev ntev.
  • Yog tias muaj "kev ua koob tsheej tet," tuav tus menyuam lub hauv caug ze rau nws lub hauv siab (qhov "kev sawv ntawm lub hauv caug thiab lub hauv siab") yuav pab tau. Koj tus kws kho mob yuav qhia koj yuav ua li cas.

Puas yuav txo tau qhov kev pheej hmoo ntawm qhov no?

Txawm hais tias feem ntau tsis paub meej tias yog dab tsi ua rau muaj kab mob plawv rau cov menyuam mos, cov kws tshawb fawb ntseeg tias leej niam txoj kev noj qab haus huv thiab kev ua neej thaum cev xeeb tub tuaj yeem cuam tshuam rau nws. Cov yam hauv qab no tuaj yeem ua rau muaj kev pheej hmoo ntawm tus menyuam yaus uas muaj kab mob plawv:

  • Muaj kab mob plawv txij thaum yug los rau hauv niam, txiv, lossis lwm tus neeg hauv tsev neeg.
  • Niam haus luam yeeb thaum cev xeeb tub.
  • Thaum cev xeeb tub, leej niam muaj tus kab mob hu ua "Rubella" (German measles).
  • Niam muaj tus kab mob ntshav qab zib uas tsis tswj tau.
  • Noj qee yam tshuaj (piv txwv li, qee yam tshuaj qaug dab peg) thaum peb lub hlis thawj zaug ntawm cev xeeb tub.
  • Niam haus dej cawv.
  • Kev tsis txaus noj haus thaum cev xeeb tub.
  • Niam muaj hnub nyoog tshaj 40 xyoo thaum cev xeeb tub.

Yog li ntawd, txhawm rau txo qhov kev pheej hmoo no hauv kev cev xeeb tub yav tom ntej, nws yog ib qho tseem ceeb heev uas yuav tsum saib xyuas koj txoj kev noj qab haus huv ua ntej cev xeeb tub, tswj cov mob uas twb muaj lawm (xws li ntshav qab zib), tsis txhob haus luam yeeb thiab haus cawv kiag li, thiab tsis txhob noj tshuaj yam tsis tau kev pom zoo los ntawm koj tus kws kho mob. Yog tias leej twg hauv koj tsev neeg muaj kab mob plawv, nws tseem yog ib qho zoo kom nrhiav kev qhia los ntawm tus kws pab tswv yim txog caj ces.

Tus menyuam uas muaj '(Overriding Aorta)' yuav xav tau lub neej yav tom ntej zoo li cas?

Qhov no yuav zoo li ntshai rau koj, tab sis qhov tseeb yog, feem ntau cov menyuam mos mus ua neej zoo li qub, noj qab nyob zoo tom qab phais.

  • Ntau tshaj 90% ntawm cov menyuam mos uas tau phais mob Tetralogy of Fallot (uas suav nrog Overriding Aorta) loj hlob zoo thiab ua neej nyob zoo li qub. Lawv mus kawm ntawv, ua si, ua haujlwm, thiab muaj tsev neeg. Ib txhia nyob kaj siab lug txog thaum lawv muaj hnub nyoog 70 thiab 80 xyoo.
  • Txawm li cas los xij, yog tias tsis phais, qhov mob no yuav txaus ntshai heev. Yog tias qhov ntawd tshwm sim, cov tsos mob yuav hnyav zuj zus tuaj, ua rau koj lub neej luv dua. Tej zaum koj yuav tsis nyob txog 20 xyoo.

Yog li ntawd, qhov tseem ceeb tshaj plaws yog muab kev kho mob kom raug rau lub sijhawm zoo.

Yuav saib xyuas tus menyuam li cas tom qab phais?

Thaum koj coj koj tus menyuam los tsev tom qab phais lawm, koj muaj lub luag haujlwm loj heev.

  • Mus ntsib kws kho mob plawv tsis tu ncua: Koj tus menyuam yuav tsum tau mus ntsib kws kho mob plawv tsis tu ncua. Thaum xub thawj tej zaum yuav mus ntsib ntau zaus dua, thiab tom qab ntawd yuav mus ntsib ntau zaus dua. Tsis txhob hla cov no.
  • Tiv thaiv kab mob ua pa: Cov menyuam yaus uas tau phais plawv zoo li no tuaj yeem kis kab mob ua pa, uas tuaj yeem ua rau muaj teeb meem sai sai. Yog li ntawd, khaws koj tus menyuam kom deb ntawm cov neeg mob khaub thuas thiab kub taub hau. Yog tias muaj kab mob zoo li no tshwm sim, nrhiav kev kho mob tam sim ntawd.
  • Tshuaj tua kab mob: Cov kws kho mob yuav pom zoo kom siv tshuaj tua kab mob ua ntej qee qhov kev kho hniav lossis lwm yam kev phais me me kom tiv thaiv kev kis kab mob plawv (endocarditis). Nug koj tus kws kho mob txog qhov no.
  • Kev Noj Haus thiab Kev Loj Hlob: Saib xyuas koj tus menyuam txoj kev noj haus thiab kev loj hlob.
  • Tej Yam Ua Si: Thaum koj tus me nyuam loj hlob tuaj, nrog koj tus kws kho mob tham txog tej yam ua si thiab kev ua si uas nws ua tau. Feem ntau, nws ua tau txhua yam li qub.

Thaum peb laus zuj zus, tej zaum yuav muaj teeb meem plawv tshiab tshwm sim, yog li nws tseem ceeb heev uas yuav tsum tau mus kuaj mob plawv ntxiv mus txog thaum peb laus zuj zus.

Kuv yuav tsum mus ntsib kws kho mob thaum twg?

Yog koj tus menyuam muaj ib qho ntawm cov tsos mob no, mus ntsib kws kho mob lossis coj nws mus rau tsev kho mob tam sim ntawd:

  • Yog tias muaj cov tsos mob tshiab tshwm sim.
  • Yog tias koj daim tawv nqaij, daim di ncauj, thiab tus nplaig zoo li tig xiav.
  • Yog koj ua pa nyuaj.
  • Yog koj tsis kam haus mis los yog noj zaub mov.
  • Yog koj zoo li nkees sai sai.

Kuv yuav tsum mus rau chav kho mob ceev (ER) thaum twg?

Yog tias koj tus menyuam muaj "Tet spell" hnyav heev, uas txhais tau tias lawv hloov xiav tam sim ntawd, ua pa nyuaj, lossis yuav tsaus muag, hu rau 911 tam sim ntawd lossis coj lawv mus rau chav kho mob ceev ntawm lub tsev kho mob ze tshaj plaws. Nyob ntawd, lawv tuaj yeem tau txais oxygen thiab / lossis tshuaj xws li "Morphine" los tswj tus mob.

Kuv yuav tsum nug kuv tus kws kho mob li cas?

Thaum lub sijhawm zoo li no, tej zaum koj yuav muaj ntau lo lus nug hauv koj lub siab. Tsis txhob ntshai nug koj tus kws kho mob txog cov no:

  • Kuv puas yuav tsum txwv kuv tus menyuam txoj kev ua si lossis lwm yam kev ua ub no?
  • Kuv tus menyuam yuav tsum tuaj kuaj mob ntau npaum li cas?
  • Puas yuav tsum tau phais kuv tus menyuam ntxiv? Yog tias tau, yuav tsum tau phais thaum twg?
  • Yuav muaj teeb meem dab tsi tshwm sim mus ntev? Yuav ua li cas thiaj tiv thaiv tau?
  • Yuav tsum muab cov tshuaj twg rau tus menyuam? Yuav tsum muab ntev npaum li cas? Puas muaj cov kev mob tshwm sim?

Cov yam tseem ceeb tshaj plaws uas peb xav coj los tsev los ntawm zaj dab neeg no yog

Zoo, peb tau tham ntau txog Overriding Aorta thiab Tetralogy of Fallot. Tej zaum koj yuav xav tias muaj kev nyuaj siab heev tam sim no. Tab sis, nco ntsoov cov no:

  • Kev hla dhau Aorta yog ib qho teeb meem plawv uas muaj txij thaum yug los hu ua Tetralogy of Fallot. Qhov no yog thaum tus menyuam lub aorta tsis sib luag, ua rau cov ntshav tsis muaj oxygen txaus ntws thoob plaws lub cev.
  • Cov tsos mob yuav muaj xws li daim tawv nqaij xiav, qaug zog sai, ua pa nyuaj, thiab "Tet spells" txaus ntshai.
  • Qhov mob no kho tau zoo los ntawm kev phais. Cov kws phais tau ua qhov kev phais no tau zoo heev rau ntau xyoo lawm.
  • Tom qab phais lawm, ntau tus menyuam mos muaj lub neej noj qab nyob zoo thiab zoo li qub.
  • Kev kuaj mob tsis tu ncua thiab ua raws li cov lus qhia kho mob yog qhov tseem ceeb tshaj plaws. Koj tsis yog tib tug hauv txoj kev no. Muaj cov kws kho mob, cov kws tu mob, thiab cov neeg ua haujlwm kho mob uas muaj peev xwm los pab thiab coj koj thiab koj tus menyuam. Yog li ntawd, cia li ua siab loj.

Yog koj tus menyuam mos tseem tos kev phais, nco ntsoov nug tus kws kho mob thiab cov neeg ua haujlwm saib xyuas menyuam txog tej yam koj ua tau los pab koj tus menyuam thaum lub sijhawm phais, thiab yuav ua li cas yog tias muaj "tet spell". Qhov kev paub ntawd yuav pab tau koj zoo heev.


` hla lub aorta, tetralogy of fallot, qhov tsis zoo ntawm lub plawv txij thaum yug los, qhov tsis zoo ntawm lub ventricular septal, cyanosis, tet spells, phais plawv qhib, kab mob plawv, cov menyuam yug los tsis zoo, tus menyuam xiav, tetralogy of fallot, phais plawv, kab mob plawv menyuam yaus

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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