Thaum tus kws kho mob qhia rau koj tias koj tus me nyuam muaj mob plawv hu ua "Shone's Complex," koj yuav xav tsis thoob, ntshai, thiab tsis meej pem . Nws yog ib qho uas tshwm sim ntau heev. Tej zaum koj yuav tsis tau hnov txog lub npe no ua ntej. "Tus kab mob no yog dab tsi? Yuav muaj dab tsi tshwm sim rau kuv tus menyuam?" Tej zaum koj yuav muaj ntau lo lus nug hauv koj lub siab. Tsis txhob txhawj. Cia peb tham txog qhov no yooj yim thiab meej. Shone's Complex yog dab tsi? Cia peb nkag siab meej tias nws ua li cas rau tus menyuam.
Hais yooj yim xwb, qhov Shone's Complex no yog dab tsi?
Kab mob Shone's Complex yog ib yam kab mob plawv uas muaj txij thaum yug los . Qhov uas tshwm sim hauv qhov no yog tias muaj kev thaiv ntau dua ib qho chaw hauv txoj kev ntshav mus rau sab laug ntawm peb tus menyuam lub plawv. Xav txog, sab laug ntawm peb lub plawv yog qhov uas coj cov ntshav huv thiab muaj oxygen ntau los ntawm lub ntsws thiab thawb nws mus rau tag nrho lub cev. Ib yam li lub tshuab dej. Tam sim no yuav ua li cas yog tias muaj kev thaiv lossis mob hauv txoj kev ntshav no? Nws nyuaj rau lub plawv nqus ntshav, thiab nws nyuaj rau thawb ntshav mus rau lub cev. Qhov ntawd yog qhov tshwm sim hauv Shone's Complex.
Tus mob no hu ua Shone's Complex, raws li tus kws kho mob uas tau piav qhia txog nws thawj zaug. Txawm hais tias nws tau txheeb xyuas plaub qhov teeb meem plawv uas cuam tshuam nrog nws, cov kws kho mob tam sim no tau pom tias muaj ntau qhov teeb meem ntxiv cuam tshuam.
Cov teeb meem plawv twg tuaj yeem cuam tshuam nrog Shone's Complex?
Yuav kom kuaj tau tias muaj tus kab mob Shone's Complex, tus menyuam mos yuav tsum muaj tsawg kawg yog ob ntawm yim yam teeb meem plawv uas peb yuav tham txog hauv qab no. Cia peb saib seb lawv yog dab tsi. Tej lo lus yuav zoo li nyuaj me ntsis, tab sis kuv yuav piav qhia yooj yim.
| Kev puas tsuaj ntawm lub plawv | Hauv lus yooj yim, yuav ua li cas nrog qhov no? |
|---|---|
| Lub plawv triad | Muaj ib daim nyias nyias ntxiv nyob rau hauv lub plawv sab laug sab saud (lub plawv sab laug). Qhov no faib lub plawv ua ob ntu, tiv thaiv cov ntshav kom tsis txhob ntws mus rau hauv lub plawv sab laug. |
| Lub nplhaib supravalvular mitral | Muaj ib lub voj ntawm cov nqaij mos uas loj hlob nyob rau saum lub mitral valve hauv lub plawv. Qhov no ua rau qhov qhib uas lub valve qhib los ntawm, ua rau cov ntshav ntws tsis tau zoo. |
| Lub mitral valve ntawm lub parachute | Feem ntau, muaj ob lub leeg nqaij (cov leeg nqaij papillary) uas pab lub mitral valve qhib thiab kaw. Hauv qhov teeb meem no, tsuas muaj ib qho xwb. Zoo li tag nrho cov hlua ntawm lub parachute tau sib sau ua ke hauv ib qho chaw. Qhov no tuaj yeem ua rau lub valve nqaim lossis ntshav ntws rov qab. |
| Sab laug ventricle hypoplastic | "Hypoplastic" txhais tau tias tsis tau tsim kho kom zoo. Hauv qhov no, lub plawv sab laug, lub chamber tseem ceeb ntawm lub plawv, tsis tau tsim kho kom zoo. Nws me me. Yog li nws tsis tuaj yeem tso ntshav kom zoo. |
| Kev mob hlab ntsha hauv qab aortic stenosis | Cov nqaij ntxiv sib sau ua ke hauv qab lub plawv aorta, uas thawb cov ntshav mus rau hauv lub plawv aorta, ua rau thaj chaw nqaim. Qhov nqaim no ua rau lub plawv nyuaj rau thawb cov ntshav. |
| Bicuspid aortic valve | Feem ntau, lub plawv aortic valve muaj peb daim. Tab sis cov menyuam mos uas muaj qhov tsis zoo no tsuas muaj ob daim xwb. Qhov no tuaj yeem ua rau lub plawv nqaim lossis ntshav tawm. |
| Lub aortic valve me me annulus | Lub nplhaib muaj zog (annulus) nyob ib puag ncig lub hauv paus ntawm lub aortic valve yuav me dua li qub, yog li ntawd cov ntshav uas tuaj yeem hla lub valve mus rau hauv aorta thiaj li txo qis. |
| Kev coarctation ntawm lub aorta | Qhov nqaim ntawm lub aorta, uas yog cov hlab ntsha tseem ceeb uas nqa ntshav mus rau lub cev, ua rau lub plawv ua haujlwm hnyav dua los tso ntshav hla thaj chaw nqaim ntawd. |
Qhov tseem ceeb yog tias yog muaj ob lossis ntau dua ntawm yim qhov teeb meem no, nws yog qhov uas cov kws kho mob hu ua Shone's Complex. Feem ntau, muaj ib qho kev thaiv thaum nkag mus thiab ib qho kev thaiv thaum tawm mus.
Yog tias kuv tus menyuam muaj tus mob no, cov tsos mob yuav zoo li cas?
Yog tias muaj mob hnyav, tej zaum yuav muaj ib txhia menyuam mos uas muaj mob no pib tshwm sim sai sai tom qab yug los . Qhov no yog vim lub plawv ntawm tus menyuam tsis muaj peev xwm tso ntshav txaus rau lub cev. Txawm li cas los xij, qee zaum, cov tsos mob tuaj yeem tshwm sim thaum yau lossis txawm tias thaum hluas.
Nrhiav cov cim no hauv koj tus menyuam:
- Nyuaj siab nce phaus: Tsis nce phaus kom raug.
- Xav tias nkees thaum haus mis nyuj: Tom qab haus mis nyuj, koj pib tawm hws thiab ua pa nyuaj.
- Cov zis tso tawm tsawg dua: Tso zis tsawg dua li qub.
- Lub plawv dhia tsis muaj zog: Lub plawv dhia tsis muaj zog heev, tshwj xeeb tshaj yog ntawm tes thiab taw.
- Qhov sib txawv ntawm cov ntshav siab ntawm caj npab thiab ceg: Cov ntshav siab hauv caj npab siab dua li ntawm ob txhais ceg.
- Kev sib sau ua ke ntawm cov kua qaub lactic hauv cov ntshav.
Yog tias koj tus menyuam muaj ib lossis ntau yam ntawm cov tsos mob no, nws yog ib qho tseem ceeb heev uas yuav tsum nrog koj tus kws kho mob tham sai li sai tau.
Vim li cas qhov no thiaj tshwm sim rau kuv tus menyuam? Dab tsi yog qhov ua rau qhov no?
Tam sim no tej zaum koj yuav xav tias, "Vim li cas qhov no thiaj tshwm sim rau kuv tus menyuam? Puas yog kuv qhov txhaum?" Qhov tseeb, cov kws kho mob tseem tsis tau pom qhov ua rau qhov no. Feem ntau, nws tshwm sim tsis tu ncua. Peb tseem tsis tau muaj cov ntaub ntawv txaus los hais qhov tseeb tias nws yog caj ces lossis ib puag ncig.
Txawm hais tias qee qhov kev tshawb fawb qhia tias nws yuav yog los ntawm noob caj noob ces los xij, txoj kev uas nws kis mus rau hauv tsev neeg yog qhov nyuaj heev. Yog li ntawd, yuav tsum tau tshawb fawb ntxiv kom nkag siab qhov no tag nrho.
Yog li ntawd, thov nco ntsoov, qhov no tsis yog koj qhov txhaum. Peb tsis muaj hwj chim tswj hwm tej no.
Tej yam teeb meem uas yuav tshwm sim ntawm tus mob no yog dab tsi?
Kab mob Shone's Complex ua rau muaj qee yam teeb meem, yog vim li cas kev kho mob sai thiab kev saib xyuas mus sij hawm ntev yog qhov tseem ceeb.
- Kab mob ntshav siab hauv lub ntsws: Kev nce siab tsis zoo hauv cov hlab ntsha uas nqa ntshav mus rau lub ntsws.
- Lub plawv dhia tsis zoo: Lub plawv dhia tsis sib xws.
- Mob plawv tsis ua haujlwm: Ib qho mob uas lub plawv tsis tuaj yeem tso ntshav txaus rau lub cev.
Cov kws kho mob nrhiav tau qhov no li cas?
Cov kws kho mob siv ntau yam kev kuaj mob los kuaj mob no.
- Kev kuaj lub plawv hauv plab menyuam: Qhov no yog kev tshuaj ntsuam tshwj xeeb uas ua thaum tus menyuam tseem nyob hauv plab. Nws tuaj yeem kuaj pom cov teeb meem plawv ua ntej tus menyuam yug los.
- Kev kuaj plawv los ntawm lub qhov ntswg (Transthoracic echocardiogram - TTE): Kev kuaj lub plawv los ntawm lub tshuab ultrasound tom qab tus menyuam yug los. Qhov kev kuaj no feem ntau yog siv los kuaj mob Shone's Complex.
- Kev kuaj mob plawv CT lossis MRI: Feem ntau tsis yog ua rau txhua tus, tab sis qee zaum, cov kev kuaj no tuaj yeem pab muab cov ntaub ntawv ntxaws ntxiv txog cov qauv ntawm lub plawv.
Feem ntau, tus kab mob no raug kuaj pom ua ntej lossis tom qab yug los. Txawm li cas los xij, qee zaum tus kab mob no raug kuaj pom thawj zaug thaum yau lossis thaum hluas, thaum cov tsos mob tsis hnyav heev. Hauv cov xwm txheej zoo li no, tus kws kho mob yuav xa mus kuaj ntxiv vim muaj lub suab txawv txawv (lub suab nrov nrov) hnov thaum mloog lub plawv.
Cov kev kho mob rau qhov no yog dab tsi?
Tib txoj kev kho mob Shone's Complex yog phais xwb . Tam sim no tsis muaj tshuaj kho tau qhov mob no. Txawm li cas los xij, tus kws kho mob yuav sau ntawv kom tswj tau cov tsos mob ntawm tus menyuam thiab txhawb nqa lub plawv ua haujlwm kom txog thaum phais.
Tsis muaj kev phais tshwj xeeb rau qhov no. Hloov chaw, cov kws kho mob yuav txiav txim siab seb yuav tsum tau phais dab tsi raws li qhov teeb meem ntawm koj tus menyuam lub plawv thiab seb lub plawv ua haujlwm zoo li cas.
Koj tus menyuam yuav xav tau ib lossis ntau qhov kev phais mob hauv qab no:
- Tshem tawm cov ntaub so ntswg ntxiv uas nyob ib puag ncig lub mitral valve.
- Kev kho lub mitral valve.
- Kev hloov pauv ntawm lub mitral valve (qhov no tsis tshua muaj ntau).
- Tshem tawm cov ntaub so ntswg ntau dhau hauv qab lub aortic valve.
- Kev nthuav dav ntawm lub aortic valve.
- Kho ib feem ntawm lub aorta uas nqaim lawm.
Kev phais mob
Qee zaum cov kws kho mob ua qhov no ua ntu zus . Yog li ntawd, lawv tsis ua qhov phais tag nrho ib zaug. Lawv ua ob ntu, sib cais los ntawm ib lub sijhawm. Piv txwv li, thawj qhov kev phais tshem tawm qhov txhaws ntawm txoj kev uas cov ntshav ntws tawm ntawm lub plawv. Tom qab ntawd, qhov kev phais thib ob tshem tawm qhov txhaws ntawm txoj kev uas cov ntshav ntws mus rau hauv lub plawv. Koj tus kws kho mob yuav piav qhia rau koj paub meej tias koj tus menyuam yuav tsum tau phais pes tsawg zaus thiab thaum twg lawv ua tau zoo tshaj plaws.
Lub neej yav tom ntej thiab kev kwv yees ntawm tus menyuam yog dab tsi?
Lub neej yav tom ntej thiab kev noj qab haus huv ntawm tus menyuam nyob ntawm ntau yam:
- Qhov Hnyav ntawm tus kab mob: Qhov teeb meem ntawm lub plawv hnyav npaum li cas.
- Kev kho mob sai: Kev kho mob pib sai npaum li cas.
- Teeb Meem: Seb puas yuav muaj lwm yam teeb meem tshwm sim.
- Rov qab muaj teeb meem dua: Cov teeb meem plawv uas tau kho ua ntej puas yuav rov qab muaj dua raws sijhawm?
Piv txwv li, tej yam xws li coarctation ntawm lub aorta tuaj yeem rov tshwm sim dua. Yog li, thaum koj tus menyuam loj hlob tuaj, yuav tsum tau phais ntau dua. Koj tus kws kho mob yuav muab cov ntaub ntawv ntxiv rau koj txog qhov no nyob ntawm seb koj tus menyuam mob li cas.
Muaj ntau txoj kev tshawb fawb tau qhia tias tus nqi ciaj sia ntev tom qab phais mob yog ntau dua 75%, txog li 20 xyoo . Qhov ntawd txhais tau tias peb ntawm plaub tus menyuam mos muaj sia nyob zoo thiab noj qab nyob zoo tom qab kev kho mob.
Tej zaum koj yuav muaj ib txhiab lo lus nug hauv koj lub siab tom qab hnov txog koj tus menyuam qhov kev kuaj mob. Qhov ntawd yog ib txwm muaj. Sau cov lus nug uas koj xav rau hauv phau ntawv sau. Thaum koj mus ntsib kws kho mob, nug txhua tus. Pab neeg kho mob ntawm koj tus menyuam yuav piav qhia txhua yam no rau koj thiab qhia koj txog yam koj yuav tsum ua tom ntej.
Cov Lus Qhia Txog Kev Coj Mus Tsev
- Shone's Complex yog ib yam kab mob plawv uas tsis tshua muaj txij thaum yug los uas ua rau cov ntshav ntws mus rau sab laug ntawm lub plawv raug thaiv.
- Yuav kom kuaj tau tus kab mob no, ib tug me nyuam yuav tsum muaj tsawg kawg yog 2 ntawm 8 qhov teeb meem tshwj xeeb ntawm lub plawv.
- Txoj kev kho mob no tsuas yog phais xwb. Feem ntau kev phais yeej ua tau zoo.
- Tom qab phais lawm, tus me nyuam yuav tsum tau mus ntsib kws kho mob plawv tas mus li. Tsis txhob ncua ib qho ntawm cov sijhawm teem tseg no.
- Qhov tseem ceeb tshaj plaws yog qhov xwm txheej no tsis yog koj qhov txhaum lossis koj tus khub qhov txhaum. Tsis txhob txhawj txog nws.











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