Yu dɔn ɛva tink bɔt aw wi bren wɔndaful ɛn kɔmpleks? Dis smɔl ɔgan de kɔntrol ɛnitin we wi de tink bɔt, ɛnitin we wi de muv, ɛn ɛnitin we wi de mɛmba. So, di bren nid fɔ kɔntinyu fɔ flɔ blɔd we nɔ go ambɔg am ɛn we de gi ɔksijɛn ɛn tin dɛn we go mek i gɛt tin fɔ it. Bɔt imajin wetin go apin if di men at we de kɛr blɔd go na di bren, blok? Tide wi go tɔk bɔt wan pan dɛn kayn sik ya we nɔ kin bɔku, bɔt we rili impɔtant fɔ no bɔt. Dat na Moyamoya Sik.
Fɔ tɔk am simpul wan, wetin na Moyamoya?
Strɔk na sik we kin ambɔg di blɔd vesel dɛn na wi bren. We wi de tɔk bɔt mɛrɛsin, na sik we de ambɔg di bɛlɛ. Tu men blɔd vesel dɛn de na wi nɛk we de kɛr blɔd go na di bren, we dɛn kɔl di carotid arteries. We pɔsin gɛt strok, wan ɔ sɔm tɛm dɛn ɔl tu pan dɛn men at dɛn ya kin smɔl smɔl ɛn blok. I kin afɛkt wan ɔda impɔtant at bak na di bren, we na di sɛribra at. Dis na di men blɔd vesel dɛn we de gi blɔd to di fɔs pat dɛn na wi bren.
Imajin se di men wata paip we de briŋ wata kam na yu os dɔn blok. Wetin kin apin da tɛm de? Wata nɔ de. So, i de tray fɔ gɛt wata frɔm di smɔl smɔl paip dɛn we de insay di os. Wi bren na di sem. We di men blɔd vesel dɔn blok, di bren kin mek bɔku nyu smɔl smɔl blɔd vesel dɛn fɔ mek di blɔd vesel dɛn we nɔ de. Dɛn tin ya tan lɛk sayd rod dɛn. Bɔt di prɔblɛm na dat, dɛn nyu blɔd vesel ya kin rili wik ɛn dɛn kin tan lɛk tin. So, dɛn nɔ kin ebul fɔ gi dɛn blɔd ɛn bak wan men vein. Sɔntɛnde, dɛn wik vein dɛn ya kin bɔs. If na so i bi, Moyamoya Disease kin mek bak blɔd kɔmɔt insay di bren (Brain hemorrhage). Dɔn bak, siriɔs tin lɛk strok kin apin bikɔs di bren nɔ kin gɛt inof blɔd.
Wetin mek dɛn kɔl dis "Moyamoya"?
"Moyamoya" na wan Japan wɔd. I min "lɛk smok we de blo." We di dɔktɔ dɛn na Jepan we bin fɔs kam fɔ no dis sik bin du wan angiogram fɔ di blɔd vesel dɛn na di bren, dɛn si se di nɛtwɔk we gɛt smɔl smɔl blɔd vesel dɛn we dɛn jɔs dɔn mek, tan lɛk smok we de kɔmɔt. Na dat mek dɛn gi dis sik di nem "Moyamoya."
Wetin na di sayn dɛm fɔ moyamoya sik?
Di men sayn dɛm fɔ dis sik na bikɔs di blɔd we de go na di bren nɔ de go. Sɔmtɛm dɛn kin no di sik fɔs afta dɛn dɔn gɛt strok ɔ sɔm transient ischemic attack (TIA) dɛn. sכmtεm dεn kin kכl dεn sכm sכm strכk ya "mini-strok." Dis min se di sayn dɛm fɔ strok kin kam ɛn go fɔ sɔm tɛm.
Lɛ wi luk sɔm pan de kɔmɔn sayn dɛm wae wi kin si pan dis sik.
| Di sayn we de sho se di sik de | Wan simpul ɛksplen |
|---|---|
| Strɔk ɔ mini-strok (TIA) . | Sɔm sayn dɛm lɛk wae yu gɛt wan say na yu bɔdi nɔr de fil fayn, yu nɔr kin ebul fɔ tɔk, ɛn yu kin drɔp wan say na yu fes. Dɛn simptom ya kin dɔn afta sɔm tɛm na TIA. |
| Ɛmoraji na di bren | Blɔd we de kɔmɔt na di bren kin apin we wan wik ɛn smɔl blɔd vesel bɔs. Dis kin mek yu ed at bad bad wan. |
| Ed de at | Bɔku tɛm, sɔm tɛm dɛn de, i kin at bad bad wan. |
| Di sik dɛn we kin mek pɔsin sik | Di we aw tin kin apin we tan lɛk fit. |
| Muvmɛnt dɛn we dɛn nɔ ebul fɔ kɔntrol | Di pat dɛn na di bɔdi lɛk di an ɛn fut dɛn, de muf we pɔsin nɔ ebul fɔ kɔntrol. |
| Divɛlɔpmɛnt dilɛys | If dis sik afɛkt yɔŋ pikin dɛn, mɔ, dɛn kin gɛt dilɛys pan dɛn divɛlɔpmɛnt ɛn lan. |
| Prɔblɛm dɛn we pɔsin kin gɛt we i de fil | Prɔblɛm fɔ si, yɛri, smɛl, tɔch, ɔ teist. |
Wetin kin mek pɔsin gɛt Moyamoya sik?
Fɔ tɔk tru, dɛn nɔ dɔn no yet di rayt tin we kin mek pɔsin gɛt dis sik.. Bɔt di wan dɛn we de stɔdi bɔt dis biliv se sɔntin de we gɛt fɔ du wit dis. Dat min se, dɛn kin pas am to jɛnɛreshɔn dɛn. Bikɔs dis sik kin bɔku mɔ pan pipul dɛn na Jepan, dɛn dɔn si se sɔm kɔnekshɔn de pan dɛn jin. naw dεn dכn no se chenj dεm na wan jin we dεn kכl `RNF213` kin kכntribyut to dis.
Sɔmtɛm, dis Moyamoya fenomen kin apin wit ɔda mɛdikal kɔndishɔn. Dɔn wi kin kɔl am Moyamoya sindrom. Fɔ ɛgzampul:
- Sindrom we gɛt di sik we dɛn kɔl Down syndrome
- Grevs in sik
- Nyurofibromatosis tayp 1
- Siklɔs sik sik
- Atɛrosklɛrosis we kin mek pɔsin gɛt at
Pɔsin wae gɛt sik lɛk wae de pan de risk fɔ gɛt wan sik wae dɛn kɔl Moyamoya.
Udat kin gɛt dis sik pas ɔlman?
Moyamoya na wan sik we nɔ kin bɔku . Dɛn nɔ kin ripɔt am bɔku tɛm na kɔntri dɛn lɛk Sri Lanka. Bɔt i impɔtant fɔ no bɔt dis sik.
- Dis sik kin kam pan ɛni ej, bɔt i kin kam pan pikin dɛn we ol bitwin 5 ɛn 10 ia ɛn big pipul dɛn we ol bitwin 30 ɛn 50 ia .
- Pan ɔl we wi nɔ no di rayt tin we kin mek dɛn gɛt dis sik, uman dɛn kin gɛt dis sik lɛk tu tɛm pas man dɛn.
- Dɛn kin si dis sik pan pipul dɛm na Jepan ɛn ɔda kɔntri dɛm na Is Eshia.
Aw yu kin no dis sik kɔrɛkt wan?
If yu gɛt di sayn dɛm wae wi bin dɔn tɔk bɔt, yu dɔktɔ go fɔs chɛk yu ɛn aks yu bɔt yu sik dɛm. Dɔn, if pɔsin we dɛn tink se gɛt moyamoya sik, dɛn go se dɛn fɔ du sɔm spɛshal tɛst fɔ no if i gɛt am.
| Tɛst | Wetin yu de du wit dis? |
|---|---|
| Sεribral atεriografi | Dis na di bɛst tɛst fɔ no dis sik. Insay dis tɛst, dɛn kin put smɔl tiub (kateta) insay wan at we de na di an ɔ leg, ɛn dɛn kin put spɛshal day insay di blɔd vesel dɛn tru am. Dɔn dɛn kin tek ɛkstrem rayt fɔ si aw di blɔd vesel dɛn tan ɛn aw di blɔd de flɔ fayn fayn wan. |
| MRA Skan (Magnetik Rɛsɔnans Angiografi) . | Dis na tɛst we nɔ gɛt pen we dɛn kin yuz magnɛtik fil ɛn redio wev fɔ tek ditayli pikchɔ dɛn bɔt di blɔd vesel dɛn na di bren. |
| MRI skan (Magnetik Rizɔnans Imej) . | Dɛn kin yuz wan we we fiba MRA fɔ chɛk di kɔndishɔn na di bren tisu. Dis kin ɛp fɔ no if ɛnitin dɔn pwɛl di bren bikɔs di blɔd nɔ de flɔ. |
Yu tink se tritmɛnt de fɔ moyamoya sik?
Yɛs, tritmɛnt dɛn de fɔ mɛn dis sik. Tu men gol dɛn de fɔ tritmɛnt. Wan pan dɛn na fɔ kɔntrol di sayn dɛn we pɔsin kin gɛt. Di ɔda wan na fɔ mek di blɔd flɔ fayn fayn wan na di bren ɛn fɔ mek i nɔ gɛt siriɔs prɔblɛm lɛk strok.
1. Tritmɛnt wit mɛrɛsin
Di dɔktɔ kin gi am difrɛn mɛrɛsin dɛn fɔ di pɔsin we sik.
- Aspirin: Dis mɛrɛsin de ɛp fɔ mek blɔd nɔ klɔt ɛn i de mek blɔd flɔ tru dɛn smɔl smɔl blɔd vesel dɛn de.
- Antiseizure medications: If di sik de mek yu gɛt epileptic seizure, dɛn kin gi dɛn mɛrɛsin ya fɔ kɔntrol am.
- Anticoagulants: Pan ɔl we dɛn tin ya kin ɛp fɔ mek blɔd nɔ klɔt, dɔktɔ dɛn kin jɔs tɛl dɛn fɔ du tin dɛn we rili spɛshal bikɔs i kin mek blɔd kɔmɔt.
- Calcium channel blockers: Dɛn tin ya kin ɛp fɔ ridyus di sayn dɛm lɛk ed we de at. Bɔt dɛn kin mek yu blɔd prɛshɔn go dɔŋ bak, we kin mek yu gɛt strok, so yu fɔ tek tɛm yuz dɛn.
Di tin we impɔtant pas ɔl na dat , mɛrɛsin nɔ kin ebul fɔ stɔp di blɔd vesel dɛn we de tan , so di sik kin wɔs smɔl smɔl.
2. Ɔspitul tritmɛnt (Bypass Surgery) .
If dɛn nɔ ebul fɔ kɔntrol di sik wit mɛrɛsin, ɛn if i de wɔs smɔl smɔl, di dɔktɔ kin tɛl yu fɔ du ɔpreshɔn. Dɛn kɔl dis baypas ɔpreshɔn.
Fɔ tɔk am simpul wan, dis min se dɛn fɔ mek nyu rod fɔ mek blɔd go na di bren, ɛn pas wan blɔd vesel we dɔn blok. Dis min se yu fɔ tek wan wɛlbɔdi at we kin gi blɔd to di skel ɛn kɔnɛkt am to wan blɔd vesel na di bren. I tan lɛk se yu de bil nyu flay ova fɔ baypas wan bizi rod. Dis ɔpreshɔn kin mek di blɔd we kin rich na di bren bɔku, ɛn dis kin mek pɔsin nɔ gɛt strok bad bad wan.
Yu dɔktɔ go ɛksplen to yu ditayli us ɔpreshɔn we bɛtɛ fɔ yu, ɛn wetin na di bɛnifit ɛn bad tin dɛn we i gɛt.
Ustɛm fɔ go to dɔktɔ fɔ ɛp yu kwik kwik wan? Stroke simptom dɛm (FAST) .
I rili impɔtant fɔ mek pɔsin we gɛt Moyamoya sik no bɔt di sayn dɛn we pɔsin kin gɛt we i gɛt strok . Di kwik we dɛn de gi di tritmɛnt, na di mɔ dɛn nɔ go ebul fɔ mek di bren nɔ pwɛl. Dɛn kin yuz di akɔdin FAST fɔ ɛp yu fɔ mɛmba di sayn dɛm wae de sho se yu gɛt strok.
| Stroke Simptom (FAST) - Akt Wantɛm wantɛm! | |
|---|---|
| F - Fes we yu de du | Yu tink se wan say na yu fes kin fil lɛk se yu nɔ gɛt bɛtɛ trɛnk? Yu tink se wan say na yu fes kin shek shek we yu de smayl? |
| A - Arm dɛn | Yu kin es yu tu an? Yu tink se wan an kin fɔdɔm? |
| S - Tɔk we yu de tɔk | Yu tink se di tɔk kin kɔnfyus? Yu kin tɔk smɔl smɔl? Yu tink se i at fɔ tɔk simpul sɛnt? |
| T - Taym | If yu gɛt ɛni wan pan dɛn sik ya, nɔ de te. Go na ɔspitul in Imejɛnsi Dipatmɛnt (ETU) wantɛm wantɛm ɔ kɔl ambulans. Taym na di men tin! |
Apat frɔm dɛn tin ya, di sayn dɛm lɛk fɔ kɔnfyus wantɛm wantɛm , fɔ mek yu nɔ fil fayn na yu bɔdi, yu nɔ de si fayn, yu nɔ go ebul fɔ waka, ɔ yu ed de at bad bad wan we yu nɔ go ebul fɔ bia, kin bi sayn dɛm bak we de sho se yu gɛt strok.
We yu de liv wit dis sik, if dɛn no di sik kwik kwik wan ɛn trit am fayn, bɔku pipul dɛn kin liv nɔmal layf. If dɛn nɔ trit di sik, i kin rili bad ɛn i kin ivin kil am. So, e fayn fɔ no bɔt de sik ɛn fala di dɔktɔ in instrɔkshɔn dɛn gud gud wan.
Mɛsej we dɛn kin kɛr go na os
- Moyamoya sik na wan sik we nɔ kin apin so ɔltɛm we di men at we de gi blɔd to di bren kin smɔl smɔl ɛn blok.
- Dis kin mek di blɔd we de go na di bren nɔ de go dɔŋ, ɛn dis kin mek i gɛt siriɔs tin dɛn lɛk strok ɔ blɔd we de kɔmɔt na di bren.
- Di men sayn dɛm na wae yu kin gɛt lɛk wae yu gɛt strok, yu ed kin at, ɛn yu kin gɛt sik wae de mɛk yu nɔr de fil fayn.
- Dɛn kin ebul fɔ mɛn di sik fayn fayn wan bay we dɛn no am kwik kwik wan ɛn trit am wit mɛrɛsin ɔ ɔpreshɔn.
- If yu ɔ pɔrsin wae yu sabi de gɛt sayn dɛm fɔ strok (FAST), yu fɔ go na ɔspitul in Imejɛnsi Dipatmɛnt (ETU) wantɛm wantɛm. We yu west tɛm, dat kin mek yu bren pwɛl mɔ ɛn mɔ.
- If yu gɛt ɛni dawt ɔ kwɛstyɔn bɔt dis, tɔk to yu dɔktɔ fɔ advays.











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