Yu dɔn yɛri bɔt wan sik we nɔ kin apin so ɔltɛm we kin mek di blɔd vesel dɛn smɔl na di bren? (Moyamoya Disease) Mek wi tok abaut dis!

Yu dɔn ɛva gɛt ed we de at wantɛm wantɛm ɔ yu dɔn fil lɛk se yu nɔ gɛt wan say na yu bɔdi? Sɔntɛnde, rizin kin de biɛn dɛn tin ya we yu nɔ kin ivin imajin. Tide wi go tɔk bɔt wan rare bɔt rili impɔtant mɛdikal kɔndishɔn. Dɛn kɔl am Moyamoya Sik . Di nem de saund likl strenj, no bi so? Lɛ wi si wetin i bi.

Wetin na Moyamoya Sik?

Fɔ tɔk am simpul wan, Moyamoya Disease na wan sik wae de afɛkt di blɔd vesel dɛm na yu bren. Fɔ tɔk di kɔrɛkt tin, na sik we de mek pɔsin in bɛlɛ . Di men blɔd vesel dɛn we de gi blɔd to yu bren na di carotid arteries , we de kɔmɔt na di sayd dɛn na yu nɛk to yu bren. Insay dis sik, wan ɔ ɔl tu pan dɛn at ya kin smɔl smɔl ɔ kin blok ɔltogɛda. I kin afɛkt bak di sɛribra at , we de gi blɔd to di fɔs ɛn midul pat na yu bren.

Tink bɔt dis, na lɛk tu-tɛd pat pan di frɔnt pat na wi bren na dɛn men blɔd vesel dɛn ya de gi blɔd ɛn ɔksijɛn. So wetin kin apin we dɛn tin ya smɔl? Di blɔd ɛn ɔksijɛn we di bren nid kin go dɔŋ. I tan lɛk se we wata paip klos, di wata we de flɔ kin go dɔŋ.

Naw wi bɔdi rili wɔndaful. We wan big blɔd vesel blok lɛk dis, di bren kin tray fɔ mek di blɔd we nɔ de bay we i de mek nyu smɔl smɔl blɔd vesel dɛn. Bɔt dɛn nyu blɔd vesel ya nɔ strɔng lɛk di men blɔd vesel dɛn. Bɔku tɛm dɛn kin wik ɛn dɛn kin smɔl . I tan lɛk se dɛn dɔn blok wan big rod ɛn dɛn de divayt motoka dɛn tru smɔl smɔl sayd rod dɛn. Dɛn smɔl smɔl blɔd vesel ya nɔ go ebul fɔ gi di bren inof blɔd. Dɔn bak, sɔntɛnde dɛn wik blɔd vesel dɛn ya kin bɔs. Dis kin mek yu bren blɔd ɛn strok .

Wetin di nem "Moyamoya" min?

"Moyamoya" na wan Japan wɔd. I min "wan plume of smoke" ɔ "lɛk wan puff of smoke." Na di fɔs dɔktɔ dɛn na Jepan bin kam fɔ no dis sik. We dɛn du spɛshal skan fɔ di blɔd vesel dɛn, we dɛn kɔl angiogram , dɛn si se di smɔl smɔl blɔd vesel dɛn we dɛn jɔs dɔn mek, kɔba lɛk smok, ɔ smok we de kɔmɔt. Na dat mek dɛn gi dis sik di nem "Moyamoya sik." Yu nɔ tink se dat na wɔndaful nem?

Aw Moyamoya Sik nɔ kin bɔku?

Dis na rili sik we nɔ kin apin so ɔltɛm. Dɛn kin si am mɔ na Jepan. Dɛn se na avrej fayv pipul dɛn de pan ɛvri ɔndrɛd tawzin we gɛt dis sik. Ivin na kɔntri lɛk Amɛrika, nɔto 5,000 pipul dɛn we gɛt dis sik. So wi kin tek am se dis nɔ kin apin so ɔltɛm na Sri Lanka bak. Bɔt wan wan tɛm, dɛn kin ripɔt dɛn kayn sik pipul dɛn de.

Wetin na di sayn dɛm fɔ Moyamoya Disease?

De sayn dɛm fɔ dis sik kin kam wae di blɔd de go dɔŋ na di bren. Bɔrku tɛm, de fɔs tɛm wae yu kin no de sik naWe strok apin, ɔ we sɔm transiɛnt ischemic atak (TIA) dɛn de . Sɔntɛnde, dɔktɔ dɛn kin kɔl dɛn TIA ya "mini-stroke". Dis min se di blɔd we de go na di bren kin stɔp fɔ sɔm tɛm ɛn afta dat i kin kam bak. Bɔt dis na wɔnin.

Ɔda sayn dɛn kin bi:

• Ɛmoraji na di bren: Dis kin kam bikɔs di wik smɔl blɔd vesel dɛn we wi bin dɔn tɔk bɔt kin bɔs.
• Ed we de at: Bɔku tɛm, sɔm tɛm dɛn kin gɛt bad bad ed pen.
• Di delay we dɛn de divɛlɔp: Ɛspɛshali if yɔŋ pikin dɛn gɛt dis sik, dɛn divɛlɔpmɛnt kin slo pas ɔda pikin dɛn.
• Aneurism: Na bulge we tan lɛk balɔ na wan pat pan blɔd vesel. Dɛn tin ya kin bɔs.
• Muvmɛnt we yu nɔ want: Fɔ shek tin dɛn lɛk limb dɛn we yu nɔ ebul fɔ kɔntrol.
• Prɔblɛm wit di tin dɛn we pɔsin kin ebul fɔ no: Fɔ ɛgzampul, i nɔ kin izi fɔ lan, mɛmba, ɛn fɔ pe atɛnshɔn.
• Prɔblɛm dɛn we pɔsin kin gɛt we i de fil: I kin chenj di we aw i de si, we i de yɛri, we i de smɛl, we i de tɔch, ɛn we i de te.
• Seizures: Kɔndishɔn dɛn we tan lɛk seizure.

Yu kin gɛt wan ɔr mɔr pan dɛn sik ya. Nɔto ɔlman go ɛkspiriɛns dɛn di sem we.

Wetin kin mek pɔsin gɛt Moyamoya Sik?

Infakt, di wan dɛn we de stɔdi bɔt dis nɔ dɔn ebul fɔ no yet di rayt tin we kin mek pɔsin gɛt dis sik. Bɔt dɛn dɔn si se i gɛt jɛnɛtik inflɔwɛns, ɛn sɔntɛnde i kin bi wan sik we dɛn kin gɛt bikɔs ɔf ɔda rizin dɛn. Dɛn stil de du risach bɔt di jin dɛm we kin pas dis sik frɔm mama ɛn papa to pikin dɛm. Dɛn kin sɔprayz bak se sɔm tin dɛn lɛk inflamɛns ɔ infɛkshɔn na di bɔdi kin mek i apin.

Sɔmtɛm, dɛn Moyamoya simptom ya kin apin wit ɔda mɛdikal kɔndishɔn. Dɛn kɔl dis Moyamoya sindrom ɔ Moyamoya fenomen. Fɔ ɛgzampul:

• Sindrom we gɛt di sik we dɛn kɔl Down syndrome
• Graves’ disease ( wan sik we gɛt fɔ du wit di tayroyd gland) .
• Nyurofibromatosis tayp 1 (jɛnɛtik kɔndishɔn) .
• Siklɔs sik ( wan sik we de na blɔd) .
• Atɛrosklɛrosis (fat we de na di blɔd vesel) .

Pipul wae gɛt ɔda sik lɛk dis kin gɛt sɔm kayn sik wae de kam wit Moyamoya.

Na Moyamoya Disease na jenɛtik?

Yes, risechar dεm dכn fכnd RNF213di mכtεshכn, כ chenj dεm na wan jin we dεn kכl RNF213 kin bi rispansabl fכ sכm kes dεm fכ fibromyalgia. dεn tink se wan protin we dis jin de mek, RNF213, de involv fכ divεlכpmεnt fכ di bכdi vεsul dεm.

Na lɛk 15% pan di pipul dɛm na Jepan wae gɛt Moyamoya sik gɛt famili mɛmba wae gɛt dis sik, wae sho se dɛn gɛt dis sik. Bɔt di rayt we aw dɛn kin gɛt di prɔpati dɛn we dɛn gɛt, stil nɔ klia.

Udat kin gɛt di sik we dɛn kɔl Moyamoya?

As wi bin dɔn tɔk, dis na sik we nɔ kin apin so ɔltɛm. Pan ɔl we di sik we dɛn kɔl moyamoya, we dɛn kin gɛt bikɔs ɔf di tin dɛn we dɛn kin gɛt, kin bɔku pan pipul dɛn na Jepan, naw dɛn de ripɔt am to ɔda etnik grup dɛn bak.

Pan ɔl we sayɛnsman dɛn stil nɔ ɔndastand di rayt tin we kin mek dɛn gɛt dis sik, uman dɛn kin gɛt dis sik lɛk tu tɛm pas man dɛn.

Moyamoya sik kin kam pan ɛni ej. Bɔt pikin dɛn we ol bitwin 5 ɛn 10 ia ɛn big pipul dɛn we ol bitwin 30 ɛn 50 ia kin gɛt dis sik.

Wetin na de prɔblɛm wae kin kam wit dis sik?

If dɛn nɔ trit moyamoya sik fayn, difrɛn prɔblɛm dɛn kin apin. Dɛn tin ya na:

• Paralayz we pɔsin kin gɛt
• Prɔblɛm dɛn we pɔsin kin gɛt we i de si
• Prɔblɛm dɛn we pɔsin kin gɛt we i de tɔk
• Dizayd we de mek pɔsin muv
• Di bren we de pwɛl ɔltɛm

Dis na wae mek e fayn fɔ no ɛn trit de sik kwik kwik wan.

Aw yu go no if yu gɛt Moyamoya Disease?

If yu gɛt sayn dɛm fɔ moyamoya sik, dɔktɔ go chɛk yu ɛn aks yu bɔt yu sayn dɛm. Dɔn, if dɛn tink se pɔsin gɛt moyamoya sik, dɛn kin ɔda fɔ du tɛst lɛk:

• Sɛribra atɛriografi: Insay dis tɛst, dɛn kin put wan smɔl tiub we dɛn kɔl kateshɔn insay wan at we de na yu an ɔ yu leg. Dɔn dɛn kin put wan spɛshal wata we gɛt ayodin (kɔntrast day) insay di blɔd tru di kateshɔn. Dɔn dɛn kin tek ɛkstrem rayt fɔ si aw di wata de muv tru di blɔd vesel dɛn. Dis kin mek yu si aw di blɔd vesel dɛn smɔl ɛn aw di blɔd de flɔ.
• Magnetic Resonance Angiography (MRA): Dis na tɛst we nɔ de mek yu fil pen ɛn yu kin yuz magnɛtik fil, redio wev, ɛn kɔmpyuta fɔ luk yu blɔd vesel dɛn.
• Magnetic Resonance Imaging (MRI): Dis na wan we we fiba MRA. I kin tek pikchɔ fɔ di insay pat na yu bɔdi ɛn i kin ebul fɔ no aw di sik kin du to yu bren.

Na dɛn tɛst ya kin mek dɔktɔ dɛn no klia wan if yu gɛt Moyamoya sik ɔ yu nɔ gɛt am.

Wetin na di stej dɛm fɔ Moyamoya Disease?

Moyamoya sik na sik we de go bifo.Wan sik we dɛn kɔl sik. Dat min se if dɛn nɔ trit di sik, i go wɔs smɔl smɔl. Dɔktɔ dɛn kin yuz wan klas we dɛn kɔl "Suzuki stej" fɔ tɔk bɔt aw di sik kin tranga. Dɛn kin yuz di infɔmeshɔn we dɛn kin gɛt frɔm di MRA skan fɔ no us stej pan di sik yu de pan.Dɛn Suzuki stej ya, insay simpul wɔd dɛn, na dɛn wan ya:

• Stej 1: na di insay pat nɔmɔ na di karotid at de smɔl ɔ blok.
• Stej 2: כl di apikal branch dεm na di karotid at dεn dכn bigin fכ tכn. dεn "smoky" bכdi vεsεl dεm (di sכm sכm wan dεm we lεk smok) de bכku fכ si na di angiogram.
• Stej 3: di bכdi vεsul dεm de klia wan na di angiogram. Yu kin si klia wan se "smok plume" apin.
• Stej 4: Di blɔd vesel dɛn na di bren kin bigin fɔ stɔp smɔl smɔl. insay dεn ples, כda bכdi vεsεl dεm (transdural kolataral vεsul dεm) de bigin fכ fכm.
• Stej 5: Di nɔmba fɔ di blɔd vesel dɛn de go dɔŋ mɔ, ɛn mɔ ɔda blɔd vesel dɛn de divɛlɔp.
• Stej 6: Di blɔd vesel dɛm na di bren dɔn lɛf smɔl fɔ lɛ i nɔ de igen. di karotid atεri de sכmtεm sכmtεm כ blכk.

We dɔktɔ dɛn ɔndastand dɛn stej ya kɔrɛkt wan, dat kin ɛp fɔ plan di tritmɛnt.

Wetin na di tritmɛnt fɔ Moyamoya Disease?

We dɛn de trit moyamoya sik, di men gol na fɔ kɔntrol di sik ɛn tray fɔ mek di sik nɔ wɔs. Fɔ dis, yu dɔktɔ kin gi yu sɔm mɛrɛsin dɛn:

• Aspirin: Aspirin de ɛp fɔ mek blɔd nɔ klɔt ɔ ridyus na dɛn smɔl smɔl blɔd vesel dɛn we dɛn jɔs dɔn mek.
• Antiseizure medications: Dɛn kin gi dɛn tin ya fɔ mek yu nɔ gɛt epileptic seizure (convulsions) we kin kam wit epilepsy.
• Anticoagulants: Dɛn tin ya na tin dɛn we de mek blɔd tan. Dɛn kin ɛp fɔ mek blɔd nɔ klot. Bɔt dɛn mɛrɛsin ya gɛt prɔblɛm, dat na if blɔd de kɔmɔt, i kin at fɔ lɛ dɛn stɔp am. So, dɔktɔ dɛn kin tek tɛm gi dɛn tin ya, na spɛshal kes dɛn nɔmɔ.
• Calcium channel blockers: Dɛn tin ya kin ɛp fɔ ridyus ed pen we maygren kin kam wit. Bɔt dɛn mɛrɛsin ya kin mek yu blɔd prɛshɔn go dɔŋ bak, ɛn dis kin mek yu gɛt strok. So, na spɛshal kes dɛn nɔmɔ dɛn kin yuz dɛn.

Bɔt mɛmba se dɛn mɛrɛsin ya nɔ go ebul fɔ stɔp di blɔd vesel dɛn we de smɔl. So, de sik kin wɔs smɔl smɔl. If dis apin, yu dɔktɔ go tɛl yu fɔ du baypas ɔpreshɔn . Dis ɔpreshɔn we dɛn du:

• fכ mek nyu bכdi we de yuz hεlty at dεm na di sכl, baypas di at we dεn blכk.
• Fɔ ridayrɛkt di blɔd flɔ to di pat dɛn na di bren we di sik afɛkt.
• Fɔ opin di blɔd vesel dɛn we dɔn smɔl.

Yu dɔktɔ go ɛksplen to yu ditayli us ɔpreshɔn we go fayn fɔ yu, di sayd ɛfɛkt dɛn we i go gɛt, ɛn di prɔblɛm dɛn we kin apin.

Yu tink se dɛn kin ebul fɔ avɔyd Moyamoya Sik?

No we nɔ de we dɛn dɔn pruv fɔ mek dɛn nɔ gɛt Moyamoya syndrome, we na bikɔs ɔf di jɛnɛtiks. Bɔt dɛn kin ridyus di risk fɔ gɛt Moyamoya sindrom bay we dɛn kɔntrol di tin dɛn we gɛt fɔ du wit di blɔd vesel ɛn ridyus di risk fɔ gɛt atherosclerosis .

Dɔn bak, if yu gɛt Moyamoya sik, if yu tek di mɛrɛsin we yu dɔktɔ gi yu di rayt we ɛn lɛk aw dɛn tɛl yu fɔ tek, dat kin ɛp fɔ kɔntrol yu sik dɛn ɛn mek yu nɔ gɛt prɔblɛm dɛn.

Wetin pɔsin we gɛt dis sik kin ɛkspɛkt?

Fɔ bɔku pipul dɛn, Moyamoya sik kin wɔs smɔl smɔl as tɛm de go. As di blɔd vesel dɛn de smɔl, dɛn kin ivin gɛt strok . If dɛn nɔ trit am, Moyamoya sik kin mek pɔsin gɛt bad bad nyurolɔjik damej, strok, ɛn ivin day.

Bɔt sɔm pipul dɛn kin kɔntinyu fɔ de stebul fɔ lɔng lɔng tɛm ɛn dɛn nɔ kin gɛt ɛni sayn. We di sik bigin fɔ sho, di dɔktɔ kin tɛl yu fɔ du ɔpreshɔn.

Wetin na de layf fɔ pɔrsin wae gɛt Moyamoya Disease?

If dɛn no di sik kwik kwik wan ɛn bigin fɔ trit am kwik, pipul dɛn we gɛt Moyamoya sik kin liv nɔmal layf.

Bɔt if dɛn nɔ trit dis sik, i kin kil pɔsin. Na dat mek fɔ no di sik kwik kwik wan ɛn fɔ trit am rili impɔtant.

Ustɛm pɔrsin wae gɛt Moyamoya Disease fɔ go to dɔktɔ kwik kwik wan?

If yu si ɛni sayn fɔ se yu gɛt strok , yu fɔ go to dɔktɔ wantɛm wantɛm . Taym na di men tin na ya.

Di American Stroke Association de yuz wan akɔdin we dɛn kɔl FAST fɔ mek i izi fɔ pipul dɛn fɔ mɛmba. Lɛ wi luk wetin i min insay Sinhala:

• F - Fes droop: Wan sayd na yu fes de fil numb? If yu tray fɔ smayl, yu tink se wan say na yu fes kin drɔp?
• A - Arm wik: Yu kin es ɔl tu yu an? Yu tink se wan an kin drɔp dɔŋ?
• S - Difikulti fɔ tɔk: Yu tɔk slɔ? Ɔ i de sloslo? Yu kin ripit wan simpul sɛntɛns?
• T - Taym fɔ kɔl imejensi savis: If yu si ɛni wan pan dɛn sayn ya fɔ strok, kɔl 911 wantɛm wantɛm ɛn gɛt ambulans, ɔ go na ɔspitul wantɛm wantɛm. Taym na di men tin!

Ɔda sayn dɛm wae de sho se yu gɛt strok kin bi wae yu bigin fɔ gɛt:

• Kɔnfyus
• Wan say na di bɔdi we nɔ gɛt bɛtɛ trɛnk
• Prɔblɛm dɛn we pɔsin kin gɛt we i de si
• I nɔ izi fɔ waka
• Rili bad bad ed pen

Moyamoya Disease na wan sik wae nɔr kin bɔrku wae kin mek yu gɛt strok ɛn blɔd kɔmɔt na yu bren. Pan ɔl we di wan dɛn we de stɔdi bɔt dis nɔ no yet di rayt tin we kin mek i apin, i kin apin mɔ pan pipul dɛn na Jepan. If yu gɛt ɛni wan pan di sayn dɛm fɔ Moyamoya, go to dɔktɔ wantɛm wantɛm. Fɔ no ɛn trit Moyamoya Sik kwik kwik wan kin bi di difrɛns bitwin layf ɛn day. I impɔtant bak fɔ no di sayn dɛm we de sho se pɔsin gɛt strok ɛn tek akshɔn kwik kwik wan if i apin.

Sɔma (Mɛsej we dɛn kin tek go na os) .

So, a op se yu dɔn gɛt sɔm ɔndastandin naw bɔt di Moyamoya Sik we wi tɔk bɔt tide. Na sɔm impɔtant tin dɛn we yu fɔ mɛmba:

• Dis na sik we nɔ kin apin so ɔltɛm we kin mek di blɔd vesel dɛn na di bren smɔl.
• Sɔm kayn sik lɛk strok , ed pen , ɛn sik kin kam.
• I rili impɔtant fɔ no ɛn trit di sik kwik kwik wan.
• Di tritmɛnt inklud mɛrɛsin ɛn if nid de , baypas ɔpreshɔn .
• If yu no di sayn dɛm fɔ strok (FAST) kin sev yu layf.

If yu ɔ pɔsin we yu sabi gɛt dɛn sik ya, duya go to dɔktɔ. Nɔ wɔri, sɔlv de fɔ ɔltin. Di tin we impɔtant pas ɔl na fɔ du sɔntin kwik kwik wan.

` Moyamoya, bren sik, strok, blɔd vesel, nyurolɔjik sik, jenɛtik sik, ed pen