Omwana wo alina ekizimba ku mutima? Ka tuyige ku bulwadde bwa Cardiac Rhabdomyoma!

Nga maama oba taata, bw’olowooza ku bulamu bw’omwana wo omuto, n’ekintu ekitono ennyo kiwulira nga kinene, nedda? Naddala omusawo bw'agamba nti, "Waliwo ekintu ng'ekizimba ekitono mu mutima gw'omwana wo," kiyinza okukumenya omutima. Naye teweeraliikiriranga . Leero tugenda kwogera ku mbeera gy’owulira mu biseera nga bino, naye ng’ebiseera ebisinga si ya bulabe. Oyo ye Cardiac Rhabdomyoma .

Obulwadde bwa Cardiac Rhabdomyoma kye ki?

Mu ngeri ennyangu, cardiac rhabdomyoma kizimba ekitali kya kookolo, ekikula mu binywa by’omutima gw’omwana wo . Bino biba bitono nnyo. Naye, ekyewuunyisa, ze kika ky’ekizimba ky’omutima ekisinga okukula mu mutendera gw’omwana ali mu lubuto, kwe kugamba, ng’omwana akyali mu lubuto lwa maama (`olubuto`). Ebiseera ebisinga, obulwadde buno obuyitibwa cardiac rhabdomyomas bulabika ng’omwana akyali mu lubuto oba mu mwaka ogusooka ogw’obulamu bwe.

Ebizimba bino biva mu binywa by’omutima byennyini. Eky’enjawulo kiri nti ebiseera ebisinga tezirabibwa zokka, wabula mu bibinja . Kino kye kyawula ku fibromas, ekika ekirala eky’ekizimba ekitali kya bulabe ekikula mu mutima. Kubanga fibromas nazo zisibuka mu binywa by’omutima byennyini, naye zisituka ng’ekizimba kimu, so si mu bikunta.

Ekikulu nti cardiac rhabdomyomas si za bulabe oba kookolo . Kino kitegeeza nti tezisaasaana mu bitundu by’omubiri ebirala. Engeri yokka gye ziyinza okuba ez’akabi, bwe zitaataaganya enkola y’omutima gw’omwana wo eya bulijjo. Naye ekyo tekitera kubaawo nnyo. Ebiseera ebisinga ebizimba bino bikendeera ne bigenda ku bwabyo ne bitaleeta buzibu bwa maanyi.

Ebizimba bino bisobola okukula ku ludda olwa ddyo oba olwa kkono olw’omutima gw’omwana. Zisinga kusangibwa mu bisenge ebya wansi eby'omutima , omusuwa ogwa ddyo oba omusuwa ogwa kkono . Oluusi era zisobola okukula mu bisenge eby’okungulu eby’omutima, atria , oba mu bbugwe eyawula ebisenge ebyo byombi. Enkula y’ebizimba eyinza okwawukana okuva ku milimita ntono okutuuka ku sentimita eziwerako. Zirabika nga za kyenvu oba enjeru eriiso.

Cardiac rhabdomyoma kizimba ekitali kya kookolo, nga kikola mu bikunta mu binywa by’omutima.

Ani asinga okukulaakulanya kino?

Abalongo n’abaana abalina embeera y’obuzaale eyitibwa tuberous sclerosis bali mu bulabe obw’okufuna obulwadde bwa cardiac rhabdomyomas. Mu butuufu, abaana nga 8 ku buli 10 abalina obulwadde bwa cardiac rhabdomyomas nabo balina obulwadde bwa tuberous sclerosis. Obulwadde bwa Tuberous sclerosis nayo mbeera ya buzaale etali ya bulijjo nnyo. Ng’ekyokulabirako, kikwata abaana nga 1 ku buli 6,000 abaakazaalibwa mu Amerika.

Okunoonyereza tekuzudde bujulizi bwonna bulaga nti ekikula ky’omuntu, eggwanga oba ekika kikosa okubeerawo kw’embeera eno.

Embeera eno ya bulijjo etya?

Cardiac rhabdomyomas kye kika ky’ekizimba ky’omutima ekisinga okubeera mu baana abawere n’abaana abato. Kyokka, okutwalira awamu, ebizimba by’omutima tebitera nnyo ne kiba nti ebizimba by’omutima bitwalibwa ng’ebitono . Ebizimba ebitandikira mu mutima gwennyini (ebiyitibwa `primary cardiac tumors`) bikosa abantu abatakka wansi wa muntu omu ku buli 2,000.

Lwaki obulwadde bwa cardiac rhabdomyoma bubaawo?

Kirowoozebwa nti obulwadde bwa cardiac rhabdomyomas buva ku nkyukakyuka mu buzaale ezibaawo nga tannazaalibwa . Enkyukakyuka zino mu buzaale era zireeta embeera eyitibwa tuberous sclerosis. Abantu abalina obulwadde bwa tuberous sclerosis balina enkyukakyuka mu buzaale bwa `TSC1` oba `TSC2`. Omulimu omukulu ogw’obuzaale buno obubiri kwe kufuga okutondebwa kw’ebizimba mu mubiri. Kale, abaana bangi abalina cardiac rhabdomyomas nabo balina tuberous sclerosis.

Wabula abaana abamu basobola okufuna obulwadde bwa cardiac rhabdomyoma nga tebalina bulwadde bwa tuberous sclerosis. Mu mbeera ng’ezo, ekituufu ekivaako ekizimba kino tekinnazuulibwa .

Kino kintu ekiva mu kuzaalibwa? Kiba kya nsikirano?

Obulwadde bwa Cardiac rhabdomyoma butera kuba bwa kuzaalibwa . N’olwekyo, kitwalibwa ng’ekizaalibwa. Kyokka, si kye kimu n’eky’obusika . Singa embeera eba ya nsikirano, esobola okuyisibwa okuyita mu buzaale bw’amaka.

Obulwadde bwa Cardiac rhabdomyoma buyinza okuba obw’obuzaale, naye si bwa bulijjo. Kino kiri bwe kityo kubanga embeera y’obuzaale eyitibwa tuberous sclerosis, ekwatagana n’ekizimba kino, etera okubaawo mu ngeri ey’okwekolako, nga tewali kakwate konna ka nsikirano.

Omuzadde alina obulwadde bwa tuberous sclerosis alina emikisa 50% okubuyisa mu mwana we. Wabula "obusika" buno bulabibwa mu nga kimu kya kusatu kyokka ku balwadde ba tuberous sclerosis. Mu mbeera endala ezisinga obungi, enkyukakyuka mu buzaale ebaawo omulundi ogusooka mu mwana eyaakazuulibwa , nga talina byafaayo bya maka. Kino kitegeeza nti cardiac rhabdomyoma oluusi esobola okulabika nga bwe kisuubirwa, ate oluusi ng’ekintu ekibaawo mu ngeri ey’ekifuulannenge awatali bubonero bwonna bulabula.

Kino kiyinza okuwulikika ng’ekizibu, naye jjukira nti obuzaale kitundu kyokka ku mboozi eyo. Bw’oba ​​olina ekibuuzo kyonna oba ekikweraliikiriza ku bulwadde bwa cardiac rhabdomyoma oba tuberous sclerosis, kakasa nti oyogera n’omusawo wo . Teesa ku byafaayo by’amaka go n’engeri gye biyinza okukukwatako oba omwana wo.

Bubonero ki obulaga kino?

Ebiseera ebisinga, obulwadde bwa cardiac rhabdomyoma tereeta bubonero bwonna.. Wabula si bulijjo nnyo, singa ekizimba oba ekibinja ky’ebizimba kifuuka kinene, kiyinza okuleeta obuzibu munda mu mutima gw’omwana ne kireeta obubonero. Ng’ekyokulabirako, ebizimba ebinene bisobola okuziyiza omusaayi okutambula oba okutaataaganya ennyimba z’omutima. Singa kino kibaawo ng’oli lubuto, kiyinza okuba eky’obulabe ennyo eri omwana ali mu lubuto. Kiyinza okuvaako omutima okulemererwa oba embeera ey'amaanyi eyitibwa hydrops .

Omusawo wo ajja kutera okukebera ebizibu eby’ekika kino ng’oli lubuto ng’akebera ebifaananyi.

Singa ebizimba bino mu baana abawere n’abato tebigenda ku bwabyo ne bisigala, oba bwe bikula, biyinza okuvaako omutima okulemererwa oba omutima okukuba obutasalako (arrhythmias). Kino nakyo tekitera kubaawo nnyo. Naye omusawo w’omwana wo ajja kulondoola embeera eno alabe oba waliwo obuzibu bwonna obubaawo.

Omwana wo bw’alaga obubonero bwonna ku buno wammanga, kuba ku ssimu ya 1990 mu bwangu, oba mutwale mu ddwaaliro erikuli okumpi:

• Enkyukakyuka mu nnyimba z’omutima.
• Omutima okukuba amangu ( tachycardia ).
• Okukaluubirirwa okussa oba okussa obubi naddala ng’ogalamidde ( dyspnea ).
• Obulumi mu kifuba oba okunyiga ekiwona ng’otudde.
• Okukolola.
• Okuziyira oba okuzirika.
• Okuwulira ng’okooye oba nga munafu.
• Okuzimba mu magulu, enkizi oba mu lubuto.

Kino okitegeera otya?

Obulwadde bwa Cardiac rhabdomyoma buzuulibwa nga bayita mu kukeberebwa ebifaananyi . Ebigezo bino osobola okubikola ng’oli lubuto oba ng’omwana amaze okuzaalibwa.

Okukebera okuzuula obulwadde bwa cardiac rhabdomyoma

Ekizimba kino kitera okusooka okuzuulibwa mu kiseera ky’okukebera eddoboozi nga tonnazaala ng’oli lubuto. Ekizimba kino kitandika okulabika ku ultrasound wakati wa wiiki 20 ne 30 ng’oli lubuto. Era kiyinza okuzuulibwa nga bakozesa sikaani ey'enjawulo eyitibwa fetal echocardiogram . Kino nakyo kika kya ultrasound, naye mu ngeri ey’enjawulo kinoonya obuzibu bwonna ku mutima ng’omwana ali mu lubuto akula mu lubuto.

Ebigezo ebikozesebwa okuzuula n’okwekenneenya obulwadde bwa cardiac rhabdomyoma ng’omwana amaze okuzaalibwa mulimu:

• Okukebera omutima mu byuma (EKG/ECG) .
• Okukebera omutima (echo) .
• Okukuba ebifaananyi mu ngeri ya magineeti (MRI) .

Omwana wo ayinza okwetaaga okwekebejjebwa buli kiseera, gamba nga EKG oba echo. Omusawo ajja kulondoola ebizimba okulaba oba bikendeera ku bwabyo . Ebizimba byonna ebitagenda ku bwabyo bijja kwetaaga okujjanjabibwa.

Cardiac rhabdomyoma etera okukyamulwa nti tuberous sclerosis.Kiyinza okuba akabonero akasooka ak’obulwadde buno. N’olwekyo, kiyinza okwetaagisa okwongera okukeberebwa okulaba oba omwana alina obubonero bw’obulwadde bwa tuberous sclerosis mu bitundu by’omubiri ebirala.

Singa omwana wo azuulibwa ng’alina obulwadde bwa tuberous sclerosis, yogerako n’omusawo wo ku kukebera obuzaale . Oluusi abazadde bayinza okuba n’embeera eno mu ngeri etali ya maanyi nnyo ne batazuulibwako. Kale, omusawo wo ayinza okwagala okulaba oba ggwe oba munno mulina enkyukakyuka y’obuzaale ereeta obulwadde buno.

Obujjanjabi bwe buruwa?

Amawulire amalungi gali nti cardiac rhabdomyomas zitera okukendeera ne zibula ku bwazo , kale tekyetaagisa bujjanjabi . Emirundi egisinga ebizimba bino biba bituuse ku bunene bwabyo obusingako omwana w’azaalibwa. Oluvannyuma lw’ekyo, ebizimba bikendeera ku bwabyo , nga tebireese buzibu bwonna.

Wabula si bulijjo nnyo, ebizimba bino bitaataaganya enkola y’omutima ne byetaaga okujjanjabibwa. Oluusi kino kiyinza okubaawo ng’oli lubuto. Mu mbeera ng’ezo, maama ayinza okwetaaga okumira eddagala okukendeeza ku kizimba.

Oluusi obuzibu buyinza okubaawo ng’omwana amaze okuzaalibwa. Singa ekizimba oba ekikuta tekigenda ku bwakyo , oba bwe kikula, kiyinza okutaataaganya enkola y’omutima gw’omwana. Kino kiyinza okuvaako omutima okulemererwa oba omutima okukuba obutasalako (arrhythmia).

Bwe kiba bwe kityo, omwana wo ayinza okwetaaga eddagala nga lino:

• Ebiziyiza enziyiza y’okukyusa angiotensin (ACE).
• Eddagala erifulumya amazzi (lino ddagala eriggya amazzi agasukkiridde mu mubiri) .
• Eddagala eriweweeza ku kutambula kw’omusaayi

Omusawo wo ajja kuteesa naawe ku ngeri y’obujjanjabi era akuyambe okulonda enteekateeka esinga obulungi eri omwana wo. Okulongoosa tekitera kwetaagisa .

Endowooza etya eri abo abalina embeera eno? (Endowooza)

Abantu abasinga abalina obulwadde bwa cardiac rhabdomyoma tebeetaaga bujjanjabi . Kyokka singa baba n’embeera endala, gamba nga tuberous sclerosis, kiyinza okukosa obulamu bwabwe obw’omu maaso.

Omwana wo bw’aba alina obulwadde bw’akafuba, ajja kwetaaga okwekebejjebwa buli kiseera n’okukeberebwa abasawo . Ku bantu abamu, embeera eno teba nnyo, era eyinza obutategeerekese. Ku balala, kiyinza okuleeta ebizibu eby’amaanyi era ne kikosa nnyo omutindo gw’obulamu. Omusawo wo ajja kwogera naawe ku byetaago by’omwana wo ebitongole eby’obujjanjabi n’engeri gy’agenda okuteeberezaamu. Nga muli wamu, musobola okukola enteekateeka esinga obulungi ey’okulabirira omwana wo.

Kiki kye nsaana okubuuza omusawo?

Yogerako n’omusawo wo ku mbeera y’omwana wo n’engeri gy’atunuuliramu. Bw’oba ​​ozuuliddwa ng’olina obulwadde bwa cardiac rhabdomyoma ng’oli lubuto, oyinza obutamanya w’otandikira. Kirabika omusawo wo ajja kukunnyonnyola ebintu bingi nga tonnaba na kubuuza bibuuzo. Kyokka, kiyinza okuyamba okubuuza ebibuuzo nga bino okufuna ebisingawo:

• Tuyinza tutya okulondoola obulwadde bwa rhabdomyoma bw’omwana wange?
• Omwana wange anaakyetaaga eddagala oba okulongoosebwa?
• Omwana wange alina obulwadde bwa tuberous sclerosis?
• Obulwadde bw’akafuba bunaakwata butya omwana wange?
• Nkole okukeberebwa obuzaale ku bulwadde bwa tuberous sclerosis?
• Osobola okunkwataganya n’ekibiina ekiyamba abantu abalina obulwadde bwa tuberous sclerosis?

Okuzuula nti omwana wo alina obulwadde buno kiyinza okukutiisa n’okusinga ggwe kennyini okubufuna. Naye ng’olina amawulire amatuufu n’ebintu ebituufu, osobola okuyamba omwana wo okuddukanya embeera eyo n’okutereera . Omwana wo bw’aba alina obulwadde bwa cardiac rhabdomyoma, yogerako n’omusawo wo okumanya ebisingawo. Omusawo ayinza okukuwa amagezi okukozesa enkola eyitibwa "okulinda n'obwegendereza," erimu okukuuma eriiso ku bizimba n'okulaba oba bigenda ku bwabyo . Emirundi mingi, enkola eno yokka yeetaagibwa. Kyokka bwe kiba kyetaagisa obujjanjabi, omusawo ajja kukutegeeza.

Mu bufunze (Obubaka Obutwala Awaka)

Maama ne Taata abaagalwa, Wadde ng’erinnya Cardiac Rhabdomyoma liyinza okuwulikika ng’ertiisa, jjukira nti litera okuba ekizimba ekitali kya kookolo . Businga kubeera mu baana abawere, era butera okugenda ku bwayo nga tewali bujjanjabi bwonna .

Ekisinga obukulu kwe kusigala nga mukkakkamu, okugoberera amagezi g’abasawo, n’okuwuliziganya n’omusawo buli kiseera ku mbeera y’omwana wo. Beera mumanyi embeera ezikwatagana nga tuberous sclerosis, era ofune okukeberebwa okwetaagisa n’okugoberera.

Nga twagaliza omwana wo okuwona amangu!

` Cardiac Rhabdomyoma, Cardiac Rhabdomyoma, Ebizimba by’omutima, Obulwadde bw’omutima mu baana abawere, Tuberous Sclerosis, Tuberous Sclerosis, Obulwadde bw’omutima mu lubuto