Obulwadde bwa Eisenmenger Syndrome kye ki? Tukyogerako mu bujjuvu?

Wali owuliddeko nti obulema obumu obw’omutima obuzaalibwa nabwo busobola okukuviirako embeera ez’amaanyi ng’okuludde? Embeera emu ng’eyo enzibu ye Eisenmenger syndrome. Erinnya lino liyinza okuba nga lipya gy’oli naye kikulu okulimanya naddala ng’omuntu mu maka go alina obulwadde bw’omutima obuzaaliranwa. Ka twogere ku nsonga eno mu bujjuvu katono, kubanga okuzuula amangu n’okutegeera embeera eno kikulu nnyo.

Ddala Obulwadde bwa Eisenmenger Syndrome kye ki?

Mu ngeri ennyangu, Eisenmenger Syndrome mbeera ebaawo ng’omusaayi mungi gukulukuta mu misuwa (emisuwa) egitambuza omusaayi okuva ku mutima gwo okutuuka mu mawuggwe go. Kilowoozeeko ng’amazzi agakulukuta amangu mu ttaapu. Kino kivaamu puleesa mu misuwa gy’amawuggwe go ne ku ludda olwa ddyo olw’omutima gwo, embeera eyitibwa Pulmonary Hypertension . Kiba ng’okugezaako okusika amazzi amangi okuyita mu payipu entono, ekivaamu puleesa nnyingi munda mu payipu.

Okugatta ku ekyo, omusaayi gutandika okukulukuta mu ngeri etasaana wakati w’oludda olwa kkono ne ddyo olw’omutima (`blood shunting`). Kino kitegeeza nti olw’okuyungibwa okutali kwa bulijjo (nga ekituli ekibeerawo ng’omwana azaalibwa), omusaayi okuva ku ludda olwa kkono olw’omutima (ogulimu omukka gwa oxygen) gukulukuta ne gugenda ku ludda olwa ddyo (mu oxygen omutono). Ekiseera bwe kigenda kiyitawo, embeera eno nayo esobola okukyusibwa, ekitegeeza nti omusaayi ogulimu omukka omutono gukulukuta okuva ku ludda olwa ddyo okudda ku kkono.

Embeera eno eyitibwa Eisenmenger syndrome, etera okubaawo ng’ekizibu ekimu oba ebisingawo ku mutima ebizaalibwa nga tebijjanjabiddwa oba nga tebizuuliddwa . Singa embeera eno ewangaala, esobola okuleeta amawuggwe okwonooneka enkalakkalira n’ebizibu ebirala ebiyinza okutta omuntu. Eno y’ensonga lwaki eno mbeera eyeetaaga okufaayo ennyo.

Ani asinga okulwala embeera eno?

Eisenmenger syndrome mbeera etera okubaawo mu baana n’abavubuka abakulu abazaalibwa n’obulwadde bwa Ventricular Septal Defect (VSD), ekituli mu bbugwe wakati w’ebisenge bibiri ebya wansi eby’omutima (ventricles za kkono ne ddyo).

Ate era, obulwadde bwa Eisenmenger buyinza okubaawo ng’obulema obulala obumu obw’omutima obuzaalibwa tebujjanjabiddwa bulungi. Wano waliwo ebyokulabirako ebitonotono:

• Obulema mu mwala gw’omusuwa gw’omubiri (atrioventricular canal).
• Obulema mu bitundu by’omubiri ebiyitibwa atrial septal
• Obulwadde bw’omutima obuyitibwa Cyanotic heart disease (omubiri mwe gufuuka bbululu) .
• Patent ductus arteriosus (omusuwa ogulina okuggalwa oluvannyuma lw’okuzaalibwa) .
• Tetralogy of Fallot (okugatta ebizibu by’omutima bina) .
• Omusuwa gw’omugongo `(Truncus arteriosus)`

Ekirala kiri nti, obulwadde bwa Down syndrome.Abaana abalina obulwadde bwa Down syndrome nabo balina emikisa mingi egy’okufuna obulwadde bw’omutima obuzaalibwa. N’ekyavaamu, era bayinza okuba nga batera okukwatibwa obulwadde bwa Eisenmenger. Mu butuufu, ebibalo biraga nti wakati wa 25% ne 50% ku bantu abakulu abalina obulwadde bwa Eisenmenger nabo balina obulwadde bwa Down syndrome.

Obulwadde bwa Eisenmenger butera kwenkana wa?

Ekirungi, obulwadde bwa Eisenmenger embeera etali ya bulijjo nnyo . Bukwata wakati wa 1% ne 6% ku bantu abakulu abazaalibwa n’obulemu ku mutima. Kyokka wadde nga tekitera kubaawo, kikulu okukimanya olw’obukulu bwakyo.

Kiki ekivaako obulwadde bwa Eisenmenger?

Okusobola okutegeera obulungi ensonga lwaki kino kibaawo, olina okuba n’endowooza entonotono ku ngeri omusaayi gye gukulukuta mu mutima gwaffe. Kuba akafaananyi ng’omutima gwaffe gulinga ennyumba erimu ebisenge bina.

Entambula y’omusaayi mu mutima omulamu ebaawo bweti:

1. Right atrium: Omusaayi gw’omubiri ogukozesebwa, ogutaliimu mukka gwa oxygen gusooka kujja ne gukuŋŋaanyizibwa wano. Olwo omusaayi guno gusindikibwa mu kisenge kya ddyo.

2. Right ventricle: Wano omusaayi ogutaliimu mukka gwa oxygen we gusindikibwa mu mawuggwe okufuna oxygen omupya.

3. Left atrium: Omusaayi omuyonjo ogubadde guteekeddwamu omukka gwa oxygen mu mawuggwe gudda ku mutima wano. Olwo omusaayi guno ne gusindikibwa mu kisenge kya kkono.

4. Left ventricle: Eno ye ppampu enkulu ey’omutima. Wano omusaayi ogulimu omukka gwa oxygen we gusaasaanyizibwa mu mubiri gwonna.

Kati teebereza nti waliwo ekikyamu mu nsengeka y’omutima, gamba ng’ekituli mu bbugwe wakati w’omusuwa ogwa ddyo n’ogwa kkono (VSD). Kiki ekibaawo olwo? Omusaayi ogulimu oxygen omungi (ku ludda olwa kkono) n’omusaayi ogutaliimu oxygen (ku ludda olwa ddyo) bitandika okutabula wamu. N’ekyavaamu, omusaayi omungi gukulukuta ne gugenda mu mawuggwe. Kino kye kivaako puleesa y’amawuggwe eyogeddwako waggulu. Ekirala, omusaayi ogulimu omukka gwa oxygen ogwetaaga okugenda mu mubiri gwonna gukendeera. Kino kye kizibu ekikulu eky’obulwadde bwa Eisenmenger syndrome.

Bubonero ki obulaga obulwadde bwa Eisenmenger syndrome?

Obubonero bw’obulwadde bwa Eisenmenger syndrome busobola okwawukana okusinziira ku muntu. Zisinziira ku kika ky’obulema bw’omutima n’ebitundu ebikoseddwa. Ebiseera ebisinga, obubonero buno tebulabika omulundi gumu. Zitera okutandika okulabika mu myaka gy’obuvubuka oba nga bukyali bato. Olwo, obubonero bweyongera mpolampola.

Buno bwe bumu ku bubonero obusinga okulabibwa:

• Obulumi mu kifuba oba okunyiga (Angina) .
• Omutima gukuba mu ngeri etali ya bulijjo (Arrhythmias) - Kino kitegeeza nti omutima gukuba mu ngeri ez’enjawulo mu kifo ky’okukuba mu ngeri emu.
• Okugaziwa kw’enkomerero z’enjala n’okukoona kw’emisumaali (Clubbing) - ng’ensonga y’omuggo gw’engooma.
• Okusesema omusaayi.
• Olususu okukyuka langi ya bbululu oba enzirugavu (Cyanosis) - Kino kiva ku bungi bwa oxygen mu musaayi okukendeera.
• Okuziyira oba okuzirika.
• Okuzimba amagulu, enkizi, ebigere oba olubuto (edema).
• Okuwulira ng’omutima gwo gukuba mangu, okuwulira eddoboozi ly’ekifuba nga kikuba (heart pulpitations).
• Obukoowu obuyitiridde n’obutaba na maanyi (Lethargy).
• Dyspnea - Okukaluubirirwa okussa ne bw’oba ​​ofubye katono.

Bw’oba ​​olina obubonero buno obumu oba obusingawo, kikulu nnyo okugenda mu basawo amagezi amangu ddala.

Bizibu ki ebiyinza okuva mu bulwadde bwa Eisenmenger?

Ebyembi, obulwadde bwa Eisenmenger si bulwadde obusigala mu kifo kimu. Kiyinza okuvaako ebizibu eby’enjawulo mu bulamu. Ebimu ku byo bye bino:

• Okuvaamu omusaayi mu bwongo.
• Okuzimba ku bwongo olw’okukwatibwa yinfekisoni.
• Omusaayi obutamala ku bwongo (Cerebral vascular insufficiency).
• Gaasi.
• Omutima okulwala.
• Omutima okulemererwa.
• Yinfekisoni z’omutima, okugeza, endocarditis.
• Okuzimba omusaayi (Hyperviscosity syndrome).
• Okulemererwa kw’ekibumba.
• Ebizibu ebiva mu lubuto (kino kya bulabe nnyo).
• Storoko.
• Okufa okw’amangu.

Bw’otunuulira ebizibu bino, olaba embeera eno bw’eri ey’amaanyi, nedda? Eno y’ensonga lwaki kino tulina okukissaako essira mu ngeri ey’enjawulo.

Obulwadde bwa Eisenmenger buzuulibwa butya?

Omusawo ajja kutera okunoonya obubonero bw’obulwadde bwa Eisenmenger syndrome ng’akebera omubiri. Ng’ekyokulabirako, oba olususu lwo lwa bbululu, oba engalo zo zikubiddwa emiggo, era oba owulira amaloboozi agatali ga bulijjo ng’owuliriza omutima gwo.

Oluvannyuma, omusawo ayinza okulagira okukeberebwa ekimu oba ebisingawo ku bino wammanga okukakasa nti omuntu azuuliddwa:

• Okukebera omukka gwa oxygen mu musaayi.
• Cardiac catheterization: Kino kizingiramu okuyingiza akatuli akatono mu mutima okupima puleesa n’okukebera ensengekera yaago.
• X-ray y’ekifuba.
• Okubala omusaayi mu bujjuvu (CBC).
• Echocardiogram (Echocardiogram - echo): Eno ye scan y’omutima mu ddoboozi ery’omwanguka. Kisobola okutunuulira ebisenge by’omutima, obuuma obuyitibwa valve, n’engeri omusaayi gye gutambulamu.
• Electrocardiogram (EKG/ECG): Kino kikebera amasannyalaze g’omutima.
• Okukeberebwa kw’omutima okwa MRI.
• Okukebera enkola y’amawuggwe.

Omusawo asobola okuzuula obulungi obulwadde buno ng’asinziira ku mawulire agafunibwa mu kukeberebwa kuno.

Obulwadde bwa Eisenmenger bujjanjabwa butya?

Ekigendererwa ekikulu eky’okujjanjaba obulwadde bwa Eisenmenger kwe kufuga obubonero n’okuziyiza okwongera okwonooneka kw’omutima oba amawuggwe.

Bino wammanga bisobola okukozesebwa ng’obujjanjabi:

• Eddagala eritta obuwuka: Liziyiza obuwuka obuleeta endwadde mu mutima n’amawuggwe.
• Anticoagulants: Kikendeeza ku kutondebwa kw’omusaayi mu misuwa.
• Eddagala erifulumya amazzi (empeke z’amazzi): Kikendeeza ku mazzi ag’enjawulo agakuŋŋaana mu mubiri.
• Dual endothelin receptor antagonists: Zino ddagala lya njawulo eriweebwa okukendeeza puleesa mu mawuggwe.
• Ebirungo ebiyamba ekyuma: Okujjanjaba okukendeeza ku musaayi oguva ku bbula ly’ekyuma.
• Oxygen ow’okugatta: Kwanguyiza okussa n’okwongera ku oxygen mu musaayi.

Ekikulu kiri nti obulwadde bwa Eisenmenger bwe bumala okukula, kitera okulwawo okulongoosa okuddaabiriza ekizibu ky’omutima ekizaalibwa, kubanga mu kiseera ekyo okwonooneka kw’amawuggwe kwaba kwakolebwa dda.

Kyokka abantu abamu abalina obubonero obw’amaanyi ennyo n’ebitundu by’omubiri ebyonooneddwa ennyo bayinza okwetaaga okusimbibwa omutima oba amawuggwe. Naye eyo nayo nkola nzibu nnyo era ya bulabe.

Obulwadde bwa Eisenmenger busobola okuziyizibwa?

Yee, engeri yokka ey’okuziyiza obulwadde bwa Eisenmenger kwe kuzuula obulema bw’omutima obuzaalibwa nga bukyali, nga bukyali, n’okubujjanjaba obulungi, era bwe kiba kyetaagisa, okulongoosebwa. Singa obulema buno buzuulibwa ne bujjanjabwa mu buto, emikisa mingi egy’okuziyiza embeera ey’amaanyi nga Eisenmenger syndrome.

Abantu abalina obulwadde bwa Eisenmenger syndrome bawangaala ki?

Abantu abalina obulwadde bwa Eisenmenger bayinza okuba n’obulamu obutono okusinga abantu bonna. Kino kiva ku bizibu ebijja n’embeera eno. Kyokka abantu abamu babeera mu myaka egy’omu makkati. Ebbanga lye basobola okuwangaala kisinziira ku bintu gamba ng’obuzibu bw’obubonero bwabwe, engeri y’obulema bw’omutima obuzaaliranwa, n’engeri gye bikwatamu obujjanjabi. N’olwekyo kikulu okugoberera amagezi g’omusawo n’okufaayo ku bulamu bwo.

Bwemba nnina obulwadde bwa Eisenmenger, nsobola okufuna olubuto?

Kino kibuuzo kikulu nnyo. Olubuto lwa bulabe nnyo eri omuntu alina obulwadde bwa Eisenmenger. Kiyinza okuvaako obulabe obw’amaanyi ng’omutima okulemererwa, omusaayi okuzimba, n’okufa okw’amangu. Bw’oba ​​olina embeera eno era ng’olowooza ku ky’okufuna olubuto, mazima ddala wandibadde olaba omukugu mu mbeera z’omutima oguzaalibwa mu bantu abakulu (`(omukugu mu mbeera z’omutima oguzaalibwa mu bantu abakulu)`) okukubaganya ebirowoozo ku bulabe buno. Ajja kuba asobola okukuwa amagezi agasinga obulungi.

Nnyinza ntya okwerabirira nga nnina obulwadde bwa Eisenmenger?

Bw’oba ​​olina obulwadde bwa Eisenmenger syndrome, waliwo ebintu ebiwerako by’oyinza okukola okukendeeza ku bulabe bw’okufuna ebizibu. Okugoberera emitendera gino kijja kukuyamba okutumbula obulamu bwo n’omutindo gw’obulamu bwo.

Ebintu by'olina okukola:

• Lya emmere erimu sodium: Okulya omunnyo omungi kiyinza okuvaako amazzi okusigala mu musaayi n’okwongera ku puleesa.
• Funa eddagala erigema ettuufu: Weekuume ku yinfekisoni nga ekifuba ne ssennyiga.
• Nywa amazzi mangi era toleka mubiri gwo kuggwaamu mazzi (`(Staying hydrated)`) : Naye mu bungi bwokka obuwabuddwa omusawo.
• Goberera ddala eddagala lyonna n’obujjanjabi obulala obukuweereddwa omusawo w’omutima. Tosubwa ddoozi emu.
• Mumira eddagala eritta obuwuka nga tonnaba kujjanjaba mannyo oba kulongoosebwa: Kino kiyinza okuyamba okuziyiza endwadde z’omutima. Buuza omusawo wo ku nsonga eno.

Ebintu by’otolina kukola:

• Weewale okugenda mu bifo ebiri waggulu ennyo waggulu w’obugulumivu bw’ennyanja (`(High altitudes)`): Obuzibu mu kussa buyinza okweyongera olw’obutaba na mukka gwa oxygen ku buwanvu.
• Weewale okukozesa ssauna, ebisenge ebifuuwa omukka oba bbaafu ezibuguma: Bino biyinza okuvaako puleesa okukka amangu.
• Weewale ddala okunywa sigala oba okukozesa ebintu ebikolebwa mu taaba.
• Weewale dduyiro ow’amaanyi: Kola dduyiro omutono yekka ku mutendera omusawo gw’akkirizza.

Obubaka Obutwala Awaka

Eisenmenger syndrome mbeera nga puleesa mu misuwa gy’amawuggwe n’oludda olwa ddyo olw’omutima. Ebiseera ebisinga kiva ku bulema bw’omutima obuzaalibwa nabwo obutajjanjabiddwa. Obubonero butera okutandika okulabika mu myaka gy’obutiini oba mu myaka emito. Obubonero buno mulimu olususu lwa bbululu (cyanosis), okussa obubi ng’okola dduyiro, n’omutima obutakuba bulungi.

Obujjanjabi bw’embeera eno okusinga bugendereddwamu okumalawo obubonero n’okukendeeza ku kwonooneka kw’omutima n’amawuggwe. Kikeeredde nnyo okuwonya embeera eno ng’olongooseddwa. N’olwekyo, kirungi okuzuula n’okujjanjaba obulema bw’omutima obuzaalibwa nga bukyali.

Bw’oba ​​olina ekibuuzo ekirala kyonna ku nsonga eno, totya kwogera na musawo wo. Bajja kukuyamba.

` Eisenmenger syndrome, obulwadde bw’omutima, puleesa y’amawuggwe, cyanosis, obulema bw’omutima obuzaalibwa, obuzibu mu kussa, obulamu bw’omutima