Omutima gw’omwana wo omuto ogwa ddyo tegukula bulungi? (Obulwadde bw’omutima ogwa ddyo obuyitibwa Hypoplastic)

Watya singa omwana wo omuto yazaalibwa n’ekizibu ky’omutima? Teebereza engeri ekyo gye kyandibadde kimenya omutima. Abalongo abamu bazaalibwa ng’oludda olwa ddyo olw’omutima terukula bulungi. Kino abasawo bakiyita Hypoplastic Right Heart Syndrome. Kino kikendeeza ku mukka gwa oxygen omwana gw’afuna. Ka twogere ku nsonga eno mu bujjuvu, nedda?

Obulwadde bw’omutima ogwa ddyo obuyitibwa Hypoplastic Right Heart Syndrome kye ki?

Mu ngeri ennyangu, obulwadde bw’omutima ogwa Hypoplastic Right Heart Syndrome bulwadde bwa mutima obutatera kulabika ng’abaana abamu bazaalibwa nabwo . Ekibaawo mu kino kwe kuba nti ebitundu ebimu ku ludda olwa ddyo olw’omutima gw’omwana tebikula mu bujjuvu. Kilowoozeeko ng’aka ppampu entono. Oludda olwa ddyo olw’omutima lwe luggya omusaayi ogutaliimu mukka gwa oxygen mu mubiri ne gugusindika mu mawuggwe okufuna omukka gwa oxygen. Kale, singa oludda luno olwa ddyo terukulaakulana bulungi, terujja kukola mulimu gwalwo bulungi.

Mu mbeera eno, ebitundu by’omutima bino wammanga biyinza okukosebwa:

• Tricuspid valve: Kino kiringa ekikomera wakati w’omusuwa ogwa ddyo n’omusuwa ogwa ddyo ogw’omutima. Bwe kitakola bulungi, kiremesa omusaayi okutambula.
• Pulmonary valve: Eno ye valve omusuwa gw’amawuggwe ogutambuza omusaayi okuva mu ventricle eya ddyo okutuuka mu mawuggwe we gutandikira.
• Right ventricle: Kino kye kisenge ekikulu eky’okupampagira omusaayi ku ludda olwa ddyo olw’omutima. Singa efuuka entono, ejja kupampagira omusaayi mutono.
• Omusuwa gw’amawuggwe: Guno gwe musuwa omunene ogutwala omusaayi okuva mu kisenge kya ddyo okutuuka mu mawuggwe.

Okusinziira ku ngeri embeera eno gy’eri ey’amaanyi oba etali ya maanyi, emirimu gy’ebitundu bino eby’omutima giyinza okukendeera oba okweyongera.

Oluusi, abalongo abalina HRHS nabo basobola okuba n’embeera endala ez’omutima. Okugeza nga:

• Atrial septal defect (ASD): Ekituli mu bbugwe wakati w’ebisenge bibiri ebya waggulu (atria) eby’omutima.
• Ventricular septal defect (VSD): Ekituli mu bbugwe wakati w’ebisenge bibiri ebya wansi (ventricles) eby’omutima.
• Atrioventricular canal defect: Ekituli ekinene wakati mu mutima wamu n’ebizibu ebirala ebiwerako.

Embeera eno ya maanyi etya?

Obulwadde bw’omutima ogwa ddyo obuyitibwa Hypoplastic right heart syndrome (HRHS) buyinza okuba obw’amaanyi eri abantu abamu okusinga abalala . Abantu abalina embeera ez’amaanyi, gamba ng’omukka gwa oxygen omutono ennyo , beetaaga okujjanjabibwa mu bwangu . Kyokka, abantu abamu bayinza obutabufuna nga bwa maanyi, nga balina obuzibu obutonotono. Abantu ng’abo bayinza obutazuulibwa okutuusa nga bakuze.

Embeera eno ya bulijjo etya?

Eno mbeera ya bbula nnyo ddala.Abanoonyereza bateebereza nti abantu abatakka wansi wa 50,000 mu Amerika balina HRHS. Tekitera kubaawo okusinga Hypoplastic Left Heart Syndrome, embeera ng’oludda olwa kkono olw’omutima terukula bulungi.

Bubonero ki obw’obulwadde bw’omutima ogwa ddyo obuyitibwa hypoplastic right heart syndrome (HRHS)?

Wammanga bwe bubonero bw’embeera eno:

• Okukyuka langi ya bbululu mu lususu lw’emikono n’ebigere. Kino kiyitibwa cyanosis . Kitegeeza nti omubiri tegufuna mukka gwa oxygen gumala.
• Okukaluubirirwa okussa. Kino kiyitibwa obuzibu bw'okussa .
• Okussa amangu. Kino kiyitibwa tachypnea .
• Omwana aba tanywa bulungi mata.
• Okukoowa amangu, okuwulira otulo buli kiseera.

Omwana wo bw’aba alina obubonero buno obumu oba obusingawo, kirungi okugenda ew’omusawo mu bwangu.

Kiki ekivaako kino?

Mu butuufu, ekituufu ekivaako obulwadde bw’omutima ogwa ddyo obuyitibwa hypoplastic right heart syndrome (HRHS) tekinnazuulibwa .

Wabula abanoonyereza balowooza nti obuzaale buyinza okwenyigira mu nsonga eno , kubanga abantu abawerako mu maka ge gamu bategeezeddwa nti balina HRHS nga bazaalibwa. N’olwekyo, kyetaagisa okwongera okunoonyereza.

Bizibu ki ebirala bino bye biyinza okuleeta?

Obulwadde bw’omutima ogwa ddyo obuyitibwa Hypoplastic Right Heart Syndrome (HRHS) buyinza okuleeta ebizibu nga:

• Omukka gwa oxygen omutono mu mubiri. Kino kiyitibwa hypoxemia .
• Omutima okulemererwa ku ludda olwa ddyo.
• Omutima okukuba obutasalako. Kino kiyitibwa arrhythmia .

Ku myaka emito, ne ku abo abatakosebwa nnyo HRHS, okuvaamu embuto kuyinza okubaawo olw’omukka gwa oxygen omutono mu mubiri.

Obulwadde buno buzuulibwa butya?

Oluusi, omusawo asobola okuzuula HRHS ng’omwana akyali mu lubuto (okukula kw’omwana mu lubuto) . Bakozesa ‘ultrasound scan’ okulaba omutima gw’omwana. Bw’oba ​​oyagala okutunula obulungi, osobola n’okukola fetal echocardiogram . Ebigezo bino byombi tebiyingira mu mubiri.

Bikebe ki ebikolebwa ng’omwana amaze okuzaalibwa?

Oluvannyuma lw’okuzaalibwa omwana, okukebera kuno okutali kwa kuyingirira kuyinza okukolebwa okuzuula oba omwana alina HRHS:

• Pulse oximeter (pulse ox): Kino kyuma kitono ekiringa clip ekipima oxygen levels nga bagikwata ku ngalo oba ku kutu.
• Electrocardiogram (EKG/ECG): Okukebera okupima amasannyalaze g’omutima.
• Echocardiogram (Echocardiogram - echo): Kino kigezo ekikozesa amaloboozi, agafaananako n’amaloboozi aga ultrasound, okukuba ebifaananyi by’omutima. Kiyinza okulaga ensengekera y’omutima, engeri obusuwa gye bukolamu, n’engeri omusaayi gye gutambulamu.
• Heart MRI (Magnetic Resonance Imaging): Ekozesa amaanyi ga magineeti n’amayengo ga leediyo okufulumya ebifaananyi ebikwata ku mutima mu bujjuvu.

Bujjanjabi ki obukolebwa ku kino?

Obulwadde bw’omutima ogwa ddyo obuyitibwa Hypoplastic Right Heart Syndrome (HRHS) busobola okujjanjabwa n’eddagala, okukozesa enkola ezitayingirira nnyo, oba okulongoosebwa . Ekigendererwa ekikulu eky’obujjanjabi buno bwonna kwe kuyamba amawuggwe g’omwana okufuna omusaayi n’omukka ogumala .

Eddagala

• Prostaglandin ekozesebwa okuyamba okukuuma ductus arteriosus y’omwana nga nzigule. Ductus arteriosus eno ye tube omwana gy’akozesa okufuna omusaayi ogulimu omukka gwa oxygen okuva ku maama ng’ali mu lubuto. Omwana bw’atandika okussa ng’ayita mu mawuggwe ng’amaze okuzaalibwa, ttanka eno etera okuggalwa mu nnaku ntono. Wabula mu mwana alina HRHS, olw’okuba oludda olwa ddyo olw’omutima terukola bulungi, okukuuma ttanka eno nga nzigule kiyamba omusaayi okutambula okutuuka mu mawuggwe.

Enkola ezitayingirira nnyo

• Omusawo asobola okukozesa ekyuma ekigonvu ekiyitibwa catheter okuyingiza stent (akatundu akatono akalinga akatimba ak’ekyuma) mu ductus arteriosus y’omwana. Kino kikuuma omukutu nga guggule era kisobozesa omusaayi okutambula obulungi okutuuka mu mawuggwe.
• Ekirala kwe kutomera vvaalu y'amawuggwe . Mu kino, ekituli kiyisibwa mu musuwa gw’omusaayi ne kiyingira mu vvaalu y’amawuggwe etagguka bulungi, ne kivaamu ekituli mu vvaalu. Kino kisobozesa omusaayi okukulukuta mu musuwa gw’amawuggwe. Abasawo abamu era bakozesa enkola eyitibwa ablation ku kino.

Okuloongoosa

Emisango egy’amaanyi egya HRHS gyetaaga okulongoosebwa okusobola okujjanjaba. Bino bitera okukolebwa mu mitendera egiwerako.

• Blalock-Taussig-Thomas (BTT) shunt: Eno ekozesebwa okuzzaawo omusaayi mu mawuggwe g’omwana alina HRHS. Ekozesa olugoye olukoleddwa mu ngeri ey’ekikugu okukola akakwate wakati w’omusuwa oguyitibwa subclavian artery (omusuwa oguli mu ggumba ly’omu bulago) n’omusuwa gw’amawuggwe.
• Oluvannyuma lw’emyezi oba emyaka mitono, omusawo alongoosa ayinza okukola enkola ya Glenn ne/oba enkola ya Fontan . Buli emu ku nkola zino ekola ekkubo eppya omusaayi okutambula okwetooloola ekitundu kya ddyo ekiyitibwa ventricle ekitali kikola bulungi. Mu budde obwabulijjo, ekitundu kya ddyo ekiyitibwa ventricle kipampa omusaayi mu musuwa gw’amawuggwe.

Enkola za Glenn ne Fontan zisobozesa omusaayi okukulukuta butereevu okuva mu musuwa omunene ne guyingira mu musuwa gw’amawuggwe, gye guva ne gugenda mu mawuggwe okulonda omukka gwa oxygen.

Waliwo ebizibu byonna ebiva mu bujjanjabi?

Nga bwe kiri ku kulongoosa kwonna, waliwo ebizibu ebiyinza okuva mu bujjanjabi buno. Ebizibu ebiyinza okuvaamu biyinza okwawukana okusinziira ku bujjanjabi. Okugeza nga:

• Stent eyinza okutambula okuva mu kifo we yali.
• Okulongoosa obusimu obuyitibwa BTT shunt kuyinza okuleetera emisuwa okufunda oba okwonoona obusimu.
• Okukutuka kwa vvaalu y’amawuggwe kuyinza okuvaako omutima okukuba obutasalako (arrhythmia) oba okwonoona omusuwa.
• Okulongoosa okunene kuyinza okuvaako puleesa, okufulumya amazzi mu nnyindo, omutima okusiba, obulwadde bw’ensigo oba ekibumba, oba omutima obutakuba bulungi.

Naye teweeraliikiriranga. Abasawo bajja kukutegeeza ku bino byonna era bakole emitendera egyetaagisa.

Kitwala bbanga ki okuwona?

Ebiseera by’okuwona byawukana okusinziira ku bujjanjabi. Okulongoosa okunene kwe kusinga okutwala ekiseera ekiwanvu. Omwana wo ayinza okumala ennaku eziwera mu ddwaaliro, oboolyawo okusukka wiiki emu. Bajja kwetaaga okulondoolebwa ennyo nga bamaze okudda eka.

Kiki kye nsuubira singa omwana wange aba mu mbeera eno?

Olw’omukka gwa oxygen omutono nga bakyali bato, abantu abalina obulwadde bw’omutima ogwa ddyo (HRHS) bayinza okufuna okusoomoozebwa nga:

• Ensonga z’olulimi.
• Ensonga z’okujjukira.
• Okwongera ku bulabe bw’okulwala omutima, ekibumba oba ekibumba mu myaka egy’obukulu.
• Obuzibu mu muudu oba obuzibu mu kweraliikirira.
• Okukaluubirirwa okuteekateeka ekintu oba okugonjoola ekizibu.

Naye, waliwo abakugu okuyamba ku bino byonna. Kale teweeraliikiriranga.

Embeera eno etegeeza ki?

Si kya bulijjo nnyo abantu abalina obulwadde bw’omutima ogwa ddyo obuyitibwa severe hypoplastic right heart syndrome (HRHS) okuwangaala okutuuka mu bukulu nga tebalongooseddwa . Wabula abantu abalina HRHS etali ya maanyi nnyo bayinza n’obutamanya nti balina embeera eno okutuusa nga bakuze.

Olabirira otya omwana alina HRHS?

Obulabirizi omwana wo bw'anaaba yeetaaga bujja kusinziira ku mbeera ye ey'amaanyi . Singa yalongoosebwa amangu ddala ng’amaze okuzaalibwa, ajja kwetaaga okulondoolebwa ennyo ng’amaze okutuuka awaka. Omusawo oba omuzaalisa ajja kukuwa amagezi amalungi ku ngeri y’okulabirira omwana wo.

Ddi lwe weetaaga okulaba omusawo?

Omwana eyalongoosebwa ajja kwetaaga okulaba omusawo okugenda okumugoberera . Bajja kukubuulira by’olina okwegendereza n’ebyo by’olina okubuulira omusawo amangu ago singa olaba ekintu kyonna. Bw’oba ​​olina ekibuuzo kyonna oba ekikweraliikiriza ku mbeera y’omwana wo, kuba essimu y’omusawo amangu ago.

Omwana wo bw’aba n’obuzibu mu kuyiga oba okutereeza enneewulira ze, oyinza n’okufuna abakugu abalala abasobola okuyamba mu bintu ebyo. Omusawo wo ajja kukuwa obulagirizi obwetaagisa.

Bibuuzo ki bye nnina okubuuza omusawo?

Bino bye bimu ku bibuuzo by’oyinza okubuuza omusawo w’omwana wo:

• Omwana wange yeetaaga okulongoosebwa?
• Olina okulongoosebwa amangu wa?
• Okulongoosebwa kumeka okujja okwetaagisa, era kujja kukolebwa ddi?
• Endowooza etya eri omwana wange alina embeera eno entongole?

Ntegedde engeri gye kizibu okumanya nti omwana wo alina obulwadde bw’omutima. Kyokka abaana abazaalibwa leero balina obujjanjabi obwali tebufunibwa milembe egyayita. Ggwe muntu asinga amaanyi gw’osobola okubeera eri omwana wo mu kiseera kino. Manya ebikwata ku HRHS. Buuza omusawo wo ku kintu kyonna ekitali kitegeerekeka bulungi. Yogerako n’omusawo wo asalewo ekisinga obulungi eri omwana wo.

N’ekisembayo, jjukira kino (Obubaka bw’Okutwala Awaka)

Obulwadde bw’omutima ogwa ddyo obuyitibwa Hypoplastic Right Heart Syndrome (HRHS) bulwadde obutatera kulabika ng’abaana bazaalibwa nabwo, ng’oludda olwa ddyo olw’omutima terukula bulungi. Kino kikendeeza ku bungi bwa oxygen omubiri gwe gufuna. Okuzuula amangu obulwadde n’obujjanjabi obutuufu (eddagala, okulongoosebwa okutonotono, oba okulongoosebwa okunene) kiyinza okulongoosa obulamu bw’omwana . Mu mbeera ng’eno, kikulu nnyo ggwe ng’omuzadde okutegeezebwa n’okukolera awamu n’abasawo bo. Jjukira nti toli wekka. Osobola okufuna obuyambi bwe weetaaga.

` Hypoplastic Right Heart Syndrome, HRHS, Obulwadde bw’omutima mu baana abawere, Obulema mu mutima obuzaalibwa, Cyanosis, Obuzibu mu kussa, Okulongoosebwa omutima