Omusaayi gw’omutima gwo gukyusiddwa? Ka tuyige ku PAPVR (Partial Anomalous Pulmonary Venous Return)!

Oluusi owulira ng’okooye? Osanga obuzibu okussa ng’olinnye amadaala? Oba obuusabuusa katono enkulaakulana y’omwana wo omuto? Wayinza okubaawo ensonga eziwerako eziviirako ebintu bino. Naye oluusi ekivaako kino kiyinza okuba enkyukakyuka entono mu mutima gye tuzaalibwa nayo. Leero tugenda kwogera ku mbeera ng’eno, ekwatagana n’entambula y’omusaayi mu mutima, naye nga si ya bulijjo nnyo. Kino kiyitibwa PAPVR, ekitegeeza (Partial Anomalous Pulmonary Venous Return).

Omanyi PAPVR (Partial Anomalous Pulmonary Venous Return) kye ki?

Mu ngeri ennyangu, PAPVR bulwadde bwa mutima obuzaalibwa nabwo . Ekibaawo mu kino kiri nti waliwo obuzibu obutonotono ku ngeri omusaayi ogulongooseddwa, ogulimu omukka oguyitibwa oxygen okuva mu mawuggwe gaffe gye gudda mu mutima. Mu budde obwabulijjo, omusaayi guno gwonna ogulimu omukka gwa oxygen gugenda ku ludda olwa kkono olw’omutima. Olwo, oludda olwa kkono olw’omutima lupampagira omusaayi ogwo okutuuka ku mubiri gwonna.

Naye mu muntu alina PAPVR, akatono ku musaayi guno ogulimu omukka gwa oxygen oguva mu mawuggwe gwe gugenda ku ludda olwa ddyo olw’omutima . Omanyi oludda olwa ddyo olw’omutima mu budde obutuufu lufuna omusaayi ogubadde guweddewo omubiri, nga gulimu omukka gwa oxygen omutono. Kale omusaayi ogumu ogulimu omukka gwa oxygen bwe gugenda mu kkubo erikyamu, omuwendo gw’omusaayi ogujja ku ludda olwa ddyo olw’omutima gweyongera. Kiki ekibaawo olwo? Oludda olwa ddyo olw’omutima lulina okukola n’omusaayi guno ogw’enjawulo, ekitegeeza nti gulina okukola ennyo . Omugugu guno ogw’enjawulo guyinza okuzimba ku mutima okumala ekiseera, era guyinza n’okukosa obulamu bwaffe okutwalira awamu.

Naye PAPVR tekosa buli muntu mu ngeri y’emu. Kisinziira ku bungi bw’omusaayi ogukyusibwa. Abantu abamu bayinza okuba n‟embeera etali ya maanyi nnyo, era bayinza obutafuna bubonero bwonna obulamu bwabwe bwonna. Naye singa obubonero bubaawo oba ebizibu ebirala ne bibaawo, abasawo baffe basobola okuddukanya obulungi embeera eno. Emirundi egisinga, okulongoosa kuyinza okujjanjaba obulungi PAPVR n’okukuyamba okubeera n’obulamu obuwanvu era obulungi.

Eno y’engeri eya bulijjo omusaayi gye gukulukuta mu mutima gwaffe, n’engeri gye gukyuka nga tulina PAPVR.

Okutegeera enkola ya PAPVR ku ntambula y’omusaayi, ka tusooke tulabe engeri omusaayi gye gutambulamu mu butonde wakati w’omutima gwaffe n’amawuggwe. Kilowoozeeko ng’olugendo olutono.

1. Ekisooka, omusaayi gw’omubiri ogukozesebwa, ogutaliimu mukka gwa oxygen gukulukuta okuyita mu misuwa eminene ebiri (omusuwa ogw’okungulu n’omusuwa ogwa wansi) ne guyingira mu kisenge ekya waggulu (omusuwa ogwa ddyo) ku ludda olwa ddyo olw’omutima.

2. Olwo, omusaayi guno ogutaliimu oxygen guva mu kisenge ekya waggulu ekya ddyo okudda mu kisenge ekya wansi ekya ddyo (`(right ventricle)`).

3. Omusaayi guno gusimbulwa okuva mu kisenge ekya wansi ku ddyo okutuuka mu mawuggwe , nga kino kiyambibwako emisuwa gy’amawuggwe. Mu mawuggwe, omusaayi guno guddamu okuteekebwamu omukka gwa oxygen, nga gulinga aguweereddwa obulamu obupya.

4. Omusaayi omupya ogulimu omukka gwa oxygen kati gudda mu mutima nga guyita mu misuwa egiwerako (emisuwa gy’amawuggwe) okuva mu mawuggwe, butereevu mu kisenge ekya waggulu ekya kkono eky’omutima.(`(omusuwa gwa kkono)`).

5. Omusaayi guno ogulimu omukka gwa oxygen okuva mu kisenge ekya waggulu ku kkono gugenda mu kisenge ekya wansi ku kkono (`(left ventricle)`).

6. N’ekisembayo, omusaayi guno ogulimu omukka gwa oxygen okuva mu kisenge ekya wansi ku ludda olwa kkono gusaasaanyizibwa mu mubiri gwonna nga guyita mu musuwa ogusinga obunene (the aorta).

Olaba mu budde obwabulijjo omusaayi ogulimu oxygen omutono gubeera mu bisenge ebiri ku ddyo, ate omusaayi ogulimu oxygen omungi gubeera mu bisenge ebiri ku kkono. Tebatabula.

Naye ne PAPVR, enkola eno tekola bulungi. PAPVR ereeta enkola y’omusaayi okutambula mu mutima mu ngeri etaali ya bulijjo, eyitibwa cardiac shunt okuva ku kkono okudda ku ddyo. "Partially anomalous" kitegeeza nti ekitundu kyokka eky'omusaayi ogulimu oxygen okuva mu mawuggwe tekituuka ku mutima mu ngeri eya bulijjo.

Kino kiri bwe kityo kubanga omusuwa gwo gumu oba okusingawo ogw’amawuggwe gukuba omusaayi ogulimu omukka gwa oxygen mu kisenge ekya waggulu ku ludda olwa ddyo, mu kifo ky’okuguyingiza mu kisenge ekya waggulu ku ludda olwa kkono. Kiki ekibaawo olwo? Omusaayi ogutaliimu mukka gwa oxygen mu kisenge kyo ekya waggulu ku ludda olwa ddyo gutabulwa n’omusaayi ogulimu oxygen. Kale, omusaayi guno ogutabuliddwa gusindikibwa mu kisenge ekya wansi ku ludda olwa ddyo, mu mawuggwe.

Kino kirina ebizibu bibiri:

• Ekisooka kiri nti omusaayi ogumu ogulimu omukka gwa oxygen gudda mu ngeri y’emu mu ngeri gye gwajja, kwe kugamba, mu mawuggwe mu ngeri eteetaagisa .
• Ekyokubiri, omusaayi ekisenge kyo ekya wansi ekya ddyo gwe gulina okugutwala mu mawuggwe gwe gweyongera . Omulimu guno ogw’enjawulo guyinza okukuteeka akazito ku mutima okumala ekiseera.

Endwadde z’omutima endala zisobola okubaawo ne PAPVR?

Abantu abamu bayinza okuba ne PAPVR yokka, nga tebalina bulwadde bwa mutima bulala. Kino kiyitibwa "isolated PAPVR". Kyokka, abantu bangi abalina PAPVR bayinza n’okuba n’ebintu ebirala ebitali bya bulijjo, gamba ng’ekituli wakati w’ebisenge bibiri ebya waggulu eby’omutima . Kino kiyitibwa ekizibu ky’omubiri ekiyitibwa Atrial Septal Defect (ASD).

Si bulijjo nnyo, PAPVR eyinza okukwatagana n’okukula obubi kw’amawuggwe aga ddyo n’omusuwa ogutwala omusaayi mu mawuggwe (`(Scimitar syndrome)`).

PAPVR etatera kubaawo etya?

Abanoonyereza bateebereza nti abantu nga 4 ku 7 ku buli 1,000 balina PAPVR. Kyokka omuwendo guno guyinza okuba nga gusingako nnyo, kubanga abantu abamu bayinza obutafuna bubonero bwonna era bayinza obutazuulibwa nti balina embeera eno.

Bubonero ki obwa PAPVR?

Singa omuwendo gw’omusaayi ogugenda ku ludda olukyamu (oguyitibwa `shunting`) guba mutono, PAPVR tetera kuleeta bubonero. Naye, `shunting` eno bwe yeeyongera, oyinza okulaba obubonero. Abaana abato bayinza okuba n’obubonero singa baba n’embeera eno wamu n’embeera endala ez’omutima. Wabula abantu abasinga obungi abalina PAPVR batandika okufuna obubonero nga bali mu myaka gyabwe egy’obukulu 20 oba 30 .

Obubonero mu baana abato:

• Okulwawo kw’enkulaakulana.
• Okukoowa amangu ng’okola dduyiro oba ng’ozannya.
• Obulwadde bw’okussa obutera okubaawo (e.g., okuzibikira mu kifuba).
• Okussa obubi.
• Obuzibu mu kugejja.

Obubonero mu bantu abakulu:

• Okukaluubirirwa okussa.
• Okuwulira nga okooye buli kiseera (`(Fatigue)`).
• Okuwulira omutima nga gukuba mu ngeri etaali ya bulijjo (`(Heart pulpitations)`).
• Obulumi mu kifuba (`(Obulumi mu kifuba)`).
• Omutima gweyongera.
• Obulwadde bw’okussa obutera okubaawo.

Lwaki PAPVR eno ebaawo?

Okufaananako n’endwadde endala ez’omutima ezizaalibwa, PAPVR ebaawo ng’omutima tegukola bulungi mu kiseera ky’okukula kw’omwana ali mu lubuto . Mu budde obwabulijjo, mu wiiki ezisooka ez’olubuto, emisuwa ena egy’amawuggwe gikolebwa okuva mu musuwa gw’amawuggwe ogwa bulijjo. Emisuwa gino gikwatagana n’ekisenge ekya waggulu ekya kkono eky’omutima gw’omwana ali mu lubuto. Naye singa wabaawo enkyukakyuka yonna mu nkola eno, omusuwa gw’amawuggwe gusobola okuyungibwa ku kisenge ekya waggulu ekya ddyo mu kifo ky’ekisenge ekya waggulu ekya kkono, oba ku misuwa emirala egy’okumpi (nga superior vena cava oba left brachiocephalic vein). Wano PAPVR w’ebaawo.

Bizibu ki ebiyinza okuva mu PAPVR?

Shunts okuva ku kkono okudda ku ddyo ezibadde zirekeddwa okumala ebbanga nga tezijjanjabiddwa zisobola okudda emabega ne ziviirako embeera ey’amaanyi eyitibwa Eisenmenger syndrome. N’olwekyo, kikulu okugenda amangu ew’abasawo amagezi bw’oba ​​olina obubonero.

Omanya otya oba olina PAPVR?

Abasawo bazuula PAPVR nga bakeberebwa omubiri n'okukeberebwa ebirala eby'enjawulo . Nga akukebera, omusawo wo ajja kuwuliriza omutima gwo ng’akozesa ekyuma ekiwuliriza. Abantu abamu abalina PAPVR bayinza okuwulira eddoboozi ly’omutima eritali lya bulijjo (okwemulugunya kw’omutima). Kino bwe kiba kiteeberezebwa, omusawo ajja kulagira okwongera okukeberebwa.

Emyaka PAPVR gy’ezuulibwa gyawukana okusinziira ku muntu. Kiyinza okuzuulibwa mu buwere, oba okuzuulibwa ng’omuntu akuze ekikeerezi. Osobola okuba ne PAPVR, naye nga tolina bubonero bwonna, kale oyinza obutagimanya obulamu bwo bwonna. Oluusi, embeera eno ezuulibwa mu butanwa mu kiseera ky’okukebera okukolebwa ku kintu ekirala.

Bigezo ki ebikolebwa?

Ebigezo ebiyamba okuzuula PAPVR bye bino:

• Echocardiogram (Echocardiogram) - naddala okukebera omutima okuyita mu nnywanto (TEE). Kino kikuba ekifaananyi ky’omutima mu ultrasound.
• MRI y’omutima (MRI y’omutima).
• Okukebera omutima mu kompyuta (CT).

PAPVR yeetaaga okulongoosebwa?

Abaana n’abantu abakulu abamu beetaaga okulongoosebwa okuddaabiriza PAPVR okutereeza ekkubo omusaayi gye guyita mu mutima. Abaana abazuulibwa nga balina PAPVR batera okwetaaga okulongoosebwa okusinga abantu abakulu. Kino kiri bwe kityo kubanga batera okuba ne PAPVR wamu n’embeera z’omutima endala ezeetaaga okulongoosebwa.

Abasawo bagamba nti omuntu alongoosebwe.Bwe kiba kyetaagisa nnyo okumalawo obubonero oba okuziyiza ebizibu ebiyinza okubaawo mu biseera eby’omu maaso. Ggwe oba omwana wo muyinza okwetaaga okulongoosebwa singa PAPVR ereeta okukyusakyusa okw’amaanyi okuva ku kkono okudda ku ddyo. Kino kitegeeza nti omusaayi omunene ogulina okuba nga gugenda mu mubiri gudda ku ludda olwa ddyo olw’omutima n’amawuggwe. Kino kiyinza okuleeta obubonero obutanyuma n’ebizibu nga puleesa y’amawuggwe (PAH) oba omutima okulemererwa. Omusawo wo ajja kukozesa okukebera ebifaananyi okuzuula obunene bw’okusiba kuno.

Okulongoosa emirundi mingi kusobola okujjanjaba obulungi PAPVR. Kikulu okwogera n’omusawo wo ku bikwata ku kulongoosebwa kwo n’ebyo by’osuubira.

Enkola y’okulongoosa eyinza okwawukana okusinziira ku nkula y’omutima gwo n’emisuwa gy’amawuggwe. Okutwalira awamu, abasawo abalongoosa baluubirira okukyusa ekkubo ly’okutambula kw’omusaayi omusaayi ogulimu omukka gwa oxygen ne gukulukuta mu bisenge ebya kkono eby’omutima.

Kyokka, abantu abasinga obungi tebajja kwetaaga kulongoosebwa . Singa PAPVR yo eba nnyangu, omusawo ajja kulondoola embeera yo. Bw’ofuna obubonero oba ng’olaga obubonero bw’ebizibu, omusawo ayinza okukuwa amagezi okulongoosebwa mu kiseera ekyo.

PAPVR esobola okuziyizibwa?

Ebyembi, tewali ngeri yonna gye tuyinza kuziyiza PAPVR. Kintu kyetuzaalibwa nakyo. Wabula bw’oba ​​oteekateeka okufuna olubuto, yogerako n’omusawo wo ku ngeri gy’oyinza okukendeeza ku bulabe bw’okuzaala omwana alina obuzibu ku mutima. Wano waliwo obukodyo:

• Weewale ddala omwenge, ebiragalalagala, ebintu ebikolebwa mu taaba, n’okunywa sigala.
• Weetabe mu nteekateeka zonna nga tonnazaala n’omusawo wo.
• Kola n‟omusawo wo okuddukanya embeera endala zonna ez‟obulamu ezikusibukako z‟oyinza okuba nazo (e.g., ssukaali, puleesa).

Omuntu alina PAPVR asobola okubeera n’obulamu obwa bulijjo?

Kisoboka ddala okubeera obulamu obuwanvu, obulungi nga okozesa PAPVR. Abantu bangi bawangaala emyaka nga tebalina bubonero bwonna oba ebizibu. N’abo abeetaaga okulongoosebwa ebiseera ebisinga bafuna ebirungi. Kyokka ebivaamu bisobola okwawukana okusinziira ku bulwadde bw’omutima obulala oba embeera omuntu z’alina. Kale kirungi okwogera n’omusawo wo ku by’osuubira okusinziira ku mbeera yo ssekinnoomu.

Bw’oba ​​olina PAPVR, weerabirira otya? / Omwana wo olabirira otya?

Okubeera n’obulwadde bw’omutima obuzaaliranwa kiyinza okukuleetera okunyigirizibwa ebiseera ebimu. Kikulu okujjukira okutwala ebintu olunaku lumu ku lumu. Wano waliwo amagezi aga bulijjo g’osobola okugoberera:

• Noonya obujjanjabi okuva ew’omusawo w’omutima mukugu mu bulwadde bw’omutima obuzaalibwa mu bantu abakulu. Ajja kulondoola embeera yo ng’ayita mu kukeberebwa buli kiseera n’okukeberebwa.
• Buuza omusawo wo ebika bya dduyiro ebikusaanira. Nga muli wamu, musobola okukola enteekateeka y’okukola dduyiro.
• Goberera emmere eyamba omutima (e.g., Endya ya Mediterranean).
• Eddagala lyonna limira ddala nga omusawo bw’akulagidde.
• Weewale okunywa sigala n’ebintu byonna ebikolebwa mu taaba. Buuza omusawo wo oba weetaaga okuyambibwa okulekera awo okunywa sigala.

Omwana wo bw’aba alina PAPVR, buuza omusawo we engeri gy’ayinza okumulabirira obulungi. Omwana wo ayinza okwetaaga okugoberera ebiragiro eby’enjawulo ku kukola dduyiro oba emirimu emirala naddala ng’alina n’embeera endala ez’omutima ze yazaalibwa.

Ddi lwe weetaaga okulaba omusawo?

Laba omusawo wo nga bwe wategese. Okugoberera buli kiseera n‟okukebera ebifaananyi kikulu okulondoola embeera ya PAPVR yo n‟okuddukanya ebizibu.

Kuba essimu y’omusawo mu bwangu singa ggwe oba omwana wo mufuna ekimu ku bino wammanga:

• Singa obubonero obupya bulabika oba obubonero obuliwo bukyuka.
• Singa wabaawo ebizibu ebiva mu ddagala lino.
• Bwoba olina ekibuuzo kyonna oba ekikweraliikiriza.

Mu mbeera ki gy’olina okugenda mu kitongole ekikola ku by’obujjanjabi obw’amangu (ETU) ?

Singa ggwe oba omwana wo olaga obubonero buno bwonna, kuba 911 oba ennamba y’amangu mu kitundu kyo mu bwangu:

• Omutima ogukuba amangu ennyo (okukuba 100-150 buli ddakiika) ate nga tegukendeera.
• Okubulwa amagezi n’okuzirika.
• Obuzibu bw’okussa obuyitiridde mu bikwatagana ne dduyiro ne/oba obutagenda ne bwe buwummudde.
• Obulumi obw’amangu era obw’amaanyi mu kifuba.
• Omutwe ogw’amangu era ogw’amaanyi.
• Okunafuwa oba okuziyira mu mikono oba amagulu mu bwangu.

Ebibuuzo ebikulu by’olina okubuuza omusawo wo

Yogerako n’omusawo wo ku mbeera gy’olimu n’ebyo by’osuubira mu biseera eby’omu maaso. Bino bye bimu ku bibuuzo by’oyinza okubuuza:

Bw’oba ​​olina PAPVR:

• Embeera yange ya maanyi etya?
• Nkyukakyuka ki mu bulamu bwe nneetaaga okukola?
• Nnaaba nneetaaga okulongoosebwa?
• Migaso ki n’akabi akali mu kulongoosebwa?
• Ebiseera byange eby’omu maaso binaaba bitya?

Omwana wo bw’aba alina PAPVR, buuza omusawo we:

• Embeera y’omwana wange ya maanyi etya?
• Omwana wange alina endwadde endala yonna ey’omutima gy’azaalibwa?
• Omwana wange anaakyetaaga okulongoosebwa oba obujjanjabi obulala?
• Nnyinza ntya okulabirira omwana wange awaka?
• Alina obukwakkulizo bwonna ku mirimu?
• Bikozesebwa ki ebiriwo okuyamba omwana wange okutegeera kino mu ngeri etuukana n’emyaka gye?

Njawulo ki eri wakati wa PAPVR ne TAPVR?

PAPVR ya njawulo ku mbeera eyitibwa ``Total Anomalous Pulmonary Venous Return (TAPVR)``. Mu muntu alina TAPVR, emisuwa gyonna mu mawuggwe giyungibwa ku mutima mu ngeri etali ya bulijjo. TAPVR mbeera ya maanyi nnyo okusinga ebika bya PAPVR ebisinga obungi, era ebiseera ebisinga yeetaaga obujjanjabi obw’amangu nga wayiseewo akaseera katono ng’amaze okuzaalibwa. Wabula PAPVR ne TAPVR zombi zifaanagana mu ngeri nti zitaataaganya engeri eya bulijjo omusaayi gye guyitamu mu mutima.

N’ekisembayo, jjukira ebintu bino:

PAPVR eyinza obutakosa bulamu bwo n’akatono. Oba, kiyinza okuleeta obubonero oba ebizibu ebyetaagisa okujjanjabibwa. Wabula kya bulijjo okuwulira ng’olina situleesi oba okweraliikirira ku PAPVR. Omwana wo bw’aba alina PAPVR, era kya bulijjo ggwe okufaayo ku bulamu bwe. Enneewulira zino za bulijjo nnyo, era toziwulira bubi.

Buulira omusawo wo ebikweraliikiriza. Buuza ku bintu ebiyinza okukuyamba ggwe n’ab’omu maka go. Okuyiga ebisingawo ku bulwadde bw’omutima obuzaalibwa – oba bukosa ggwe, omwana wo, oba omuntu wo – kiyinza okukuyamba okuddukanya obulungi embeera yo. Okwogera n’omubuulirizi era kiyinza okukuyamba okuteeka ebirowoozo byo mu mbeera ennungi. Mu lugendo luno, tolwawo kubuuza musawo wo ku bibuuzo byonna oba ebikweraliikiriza by’oyinza okuba nabyo. Toli wekka.

` PAPVR, obulwadde bw’omutima, endwadde ezizaalibwa, amawuggwe, okutambula kw’omusaayi, okulongoosa omutima, obulwadde bw’omutima obuzaalibwa, emisuwa gy’amawuggwe, okulongoosa omutima