Wali obaddeko n’olubuto oluzibu, okuwulira ng’ojjudde oba okuziyira obutasalako? Oluusi tulowooza nti bino bintu bya bulijjo, naye mu mbeera ezitatera kubaawo, wayinza okubaawo ensonga endala emabega w’obubonero buno. Leero tugenda kwogera ku mbeera ya kookolo etali ya bulijjo nnyo, naye nga nkulu nnyo. Eyo mbeera eyitibwa `Pseudomyxoma Peritonei`, era gye tuyita `(PMP)` mu bufunze.
Obulwadde bwa Pseudomyxoma Peritonei (PMP) kye ki?
Mu ngeri ennyangu, `Pseudomyxoma Peritonei` kika kya kookolo ekitali kya bulijjo nnyo. Ekibaawo mu kino kiri nti munda mu lubuto lwo, kwe kugamba, olubuto n’ebitundu ebikyetoolodde (`(peritoneal cavity)`) bijjudde obutoffaali bwa kookolo. Obutoffaali buno obwa kookolo bukola ekintu ekinene ekiringa jelly, ekiwunya ekiyitibwa ``mucin`` . Teebereza, kiringa munda mu lubuto lwo olujjudde jelly! Eno y'ensonga lwaki abantu abamu era obulwadde buno babuyita ``jelly belly.``
Erinnya "Pseudomyxoma Peritonei" litegeeza ekintu nga "ekizimba eky'obulimba eky'omu lubuto." Kino abasawo bakiyita "ekizimba eky'obulimba" kubanga tekifaananako kookolo omulala atandikira mu kifo kimu n'asaasaana. Mu butuufu kitandikira ku kizimba ekitono ekiyitibwa ``polyp'' ekikolebwa mu appendix yo, appendix .
Polyp eno bw’eva mu appendix, obutoffaali bwa kookolo obukola ekintu ekyo ekiringa jelly gye njogeddeko butandika okusaasaana mu lubuto lwonna. Ekiseera bwe kigenda kiyitawo, kino kiyinza okukosa enkola yo ey’okugaaya emmere.
Bubonero ki bwe tufuna nga tufunye PMP?
Obubonero bwa PMP butera okujja mu bwangu ennyo. Oyinza obutaziraba mu kusooka, oba oyinza okulowooza nti kintu kya bulijjo, gamba ng’okuziyira oba obutagaaya mmere. Naye obubonero buno bwe busigala oba ne bweyongera, olina okweraliikirira.
Bino bye bimu ku bubonero obukulu obulaga nti obulwadde buno:
- Okugaziwa kw’olubuto: Olubuto lulabika nga luzimba era nga lugaziye.
- Obulumi mu lubuto: Ekintu kino ekiringa jelly mu lubuto kiyinza okuwulira ng’obutabeera bulungi oba okulumwa okutwalira awamu.
- Okuziyira: Okuzimba kuyinza okuziba ekyenda ekinene ne kizibuwalira okuyisa omusulo.
- Okukaluubirirwa okufuna embuto: Okusingira ddala ku bakyala, kiyinza okuba ekizibu okufunyisa omwana olubuto olw’okunyigirizibwa okuva ku nnabaana ono ajjudde jelly oba okuzimba ebitundu by’okuzaala.
- Hernias: Puleesa yeeyongera munda mu lubuto kiyinza okuvaako ekimu ku bitundu byo okusika okufuluma nga kiyita mu binywa. Mu basajja, okusannyalala kw’omumwa gwa nnabaana kabonero akatera okukwatibwa PMP.
- Emmere tewooma.
- Ekikeeto.
Oluusi, omusawo ayinza okukwata embeera eno eya `PMP` nga bukyali mu kiseera ky'okukeberebwa kwo okwa buli mwaka oba ng'akukebera embeera endala. Naye abantu abasinga bakizuula ng’ebizibu by’olubuto bikyaliwo ne byeyongera.
Lwaki PMP eno ebaawo? Ensonga eri etya?
Mu butuufu, abakugu n’okutuusa kati tebamanyi bulungi lujegere ki olutuusa ku PMP. Naye bakimanyi nti kitandikira ku kikula ekitono ekiyitibwa polyp mu appendix. Okuva awo, obutoffaali bwa kookolo obukola mucin okutambula ne buyingira mu lubuto.
Jjukira, `PMP` bulwadde obutatera nnyo nnyo . Bukwata abantu nga omu ku bana mu bukadde buli mwaka. Kale totya mu ngeri eteetaagisa ng’owulira ku nsonga eno.
Abasawo bazuula batya oba balina PMP?
Bw’ogenda okulaba omusawo, bajja kukubuuza ku bubonero bwo. Omaze bbanga ki ng’ozirina, era oba zeeyongera okusajjuka? Olwo bajja kukola okukebera omubiri. Bagenda kulagira n’okukeberebwa omusaayi n’okukeberebwa ebifaananyi.
Okukebera omusaayi
Omusawo ayinza okulagira okubala omusaayi mu bujjuvu (CBC). Era bayinza okulagira okukeberebwa omusaayi okunoonya obubonero bw’ekizimba. Bino bintu ebiyinza okulaga nti olina kookolo mu mubiri gwo.
Ebigezo by’okukuba ebifaananyi
Okukebera kuyinza okukolebwa okulaba oba ebitundu by'olubuto byo bigaziye, bijjudde amazzi (ascites), oba nga bikuŋŋaanye mucin, nga "jelly belly":
- Okukebera eddoboozi mu lubuto.
- Okukebera CT.
- Okukebera MRI.
Okugatta ku ekyo, omusawo ayinza okukukebera empiso, nga kino kizingiramu okuggya akatundu akatono ak’amazzi oba ebitundu by’omubiri okuva munda mu lubuto lwo. Omukugu mu by’endwadde mu by’obujjanjabi ajja kwekenneenya sampuli ng’akozesa microscope (cytology). Oluusi oyinza okukolebwako laparoscopy okutunula munda mu lubuto lwo n’okutwala sampuli z’ebitundu by’omubiri.
Bujjanjabi ki obuweebwa PMP? Kisobola okuwona?
Obujjanjabi businziira ku bintu bingi, omuli embeera yo n’obulamu bwo okutwalira awamu. Mu mbeera ezimu, abasawo basobola okujjanjaba n’okuwonya obulwadde bwa Pseudomyxoma Peritonei.
Ebiseera ebisinga, obujjanjabi buno buzingiramu okulongoosebwa. Kino kizingiramu okuggyawo ebitundu byonna ebirimu obutoffaali bwa kookolo. Oyinza n’okuweebwa eddagala eriweweeza ku bulwadde (intraperitoneal chemotherapy) ng’olongooseddwa. Naye omusawo alongoosa kino ajja kukikola singa okulongoosa asobola okuggyawo kookolo yenna oba ebisinga obungi oba mucin. Okusalawo okwo kukolebwa mu kiseera ky’okulongoosebwa.
Waliwo ebika by’okulongoosa eby’enjawulo okujjanjaba PMP.
Ng’ekyokulabirako, bw’oba olina mucin mu kyenda kyo ekitono oba mu kyenda ekinene, omusawo ajja kukusala ekyenda . Waliwo n’ebika by’okulongoosa ebirala ebiggyamu ebitundu by’omubiri ebitongole:
- Cholecystectomy: Okuggyamu ekibumba kyo.
- Okuggyamu nnabaana n’okusalako salpingo-oophorectomy ku njuyi zombi : Okuggyamu enseke zo, enkwaso, ne nnabaana.
- Liver capsulectomy: Okuggyawo ekitundu ku ngulu w’ekibumba kyo.
- Omenectomy: Okuggyawo amasavu mu maaso g’olubuto .
- Peritonectomy : Okuggyawo oluwuzi oluli mu layini munda mu lubuto lwo n’ekisambi (peritoneum).
- Splenectomy : Okuggyamu enseke yo.
Bizibu ki ebiyinza okubaawo nga balongooseddwa?
Bw’oba olongooseddwa okuggyamu ebitundu by’omubiri, bulijjo wabaawo omukisa gw’ebizibu ng’okuvaamu omusaayi omungi , okukwatibwa yinfekisoni, oba okukulukuta kw’omubiri (nastomotic leak) . Okulongoosa okunene era kuyinza okuleeta ebizibu ebiyinza okutta omuntu. Kigambibwa nti abalwadde nga kimu ku bibiri ku buli kikumi (1-2%) bafa oluvannyuma lw’okulongoosebwa ennyo. N’olwekyo, kikulu okuteesa ku bino byonna n’omusawo wo.
Waliwo obujjanjabi obulala obutaliimu kulongoosa?
Oluusi omusawo ayinza okukuwa amagezi ku bujjanjabi obulala obutali bwa kulongoosa, gamba nga:
- Okulondoola okukola : Bw’oba olina PMP ey’omutendera ogusooka, oba enkola ey’obukambwe ennyo, era omusawo wo alowooza nti obulabe bw’okulongoosebwa businga obulabe bw’obulwadde, omusawo ayinza okukuwa amagezi okulondoola okukola. Kino kizingiramu omusawo wo okulondoola obulamu bwo buli kiseera. Bayinza okukola okukebera ebifaananyi n’okukebera omusaayi okulaba oba PMP esaasaana.
- Palliative care : Bw’oba tosobola kulongoosebwa, omusawo ayinza okukuwa amagezi ku bujjanjabi nga chemotherapy oba radiation therapy obuyinza okufuga embeera ya PMP n’okukendeeza ku bubonero.
Mu kiseera kino abasawo era banoonyereza ku kusimbuliza ekyenda ekitono ng’obujjanjabi eri abantu abalina PMP mu kyenda ekitono.
Omuntu alina PMP ayinza okusuubira ebiseera eby’omu maaso eby’engeri ki?
Mu mbeera ezimu, okulongoosa okuggyawo obutoffaali bwa kookolo bwonna mu lubuto kiyinza okuyamba okufuga obulwadde okumala ebbanga eddene . Obujjanjabi obulala busobola okukuyamba okubeera n’obulwadde buno okumala ebbanga eddene.
Nga twogera ku ``survival rate``, ekisinga obukulu okujjukira nti buno bulwadde bwa bbula nnyo. Kino kitegeeza nti abantu batono nnyo ababufuna. Abanoonyereza bayiga bye bamanyi ku nsonga eno okuva mu bibinja by’abantu ebitono ennyo. Bwoba olina obulwadde buno, kirungi okubuuza omusawo wo ku kunoonyereza kuno okwa ``survival rate`` n'engeri gye bukosaamu embeera yo.
Nze nneerabirira ntya? (Okwefaako) .
Bw’oba olongooseddwa okuggyamu obutoffaali bwa kookolo oba okuggyamu ebitundu ebimu, kikulu okujjukira nti omubiri gwo gwetaaga obudde n’okuwummula okusobola okuwona. Okugeza singa olongoosebwa okuggyamu enseke, omusawo ajja kukunnyonnyola engeri kino gye kinaakukwatako.
Bw’oba olonze obujjanjabi obw’okukkakkanya obulumi, oyinza okubeera ng’olina okugenda mu bujjanjabi bwa kookolo nga chemotherapy n’obujjanjabi obw’amasannyalaze obulamu bwo bwonna. Kikulu okusigala ng’oli mugumu n’okugoberera n’obwegendereza ebiragiro by’omusawo.
Nsaana okulaba omusawo ku ssaawa mmeka?
Bwoba olina `PMP`, olina okutegeeza omusawo wo mu mbeera zino wammanga:
- Singa ebizibu bibaawo oluvannyuma lw’okujjanjabwa. Okugeza, singa wabaawo omusaayi oguyitiridde okuvaamu oluvannyuma lw’okulongoosebwa, oba singa wabaawo obubonero obulaga nti waliwo obuwuka mu kiwundu ekyalongoosebwa.
- Singa ebizibu ebiva mu bujjanjabi biba bibi okusinga bwe wali osuubira.
- Singa wabaawo obubonero bwa `Pseudomyxoma Peritonei` okuddamu okulabika oluvannyuma lw'okulongoosebwa.
N’ekisembayo, obubaka obusinga obukulu (Take-Home Message) .
Pseudomyxoma Peritonei (PMP) bulwadde obutatera kulabika nnyo era busomooza. Abakugu n’okutuusa kati tebamanyi bulungi lwaki kikulaakulana. Oyinza okumala ebbanga nga olina n’otolaba nkyukakyuka yonna ya maanyi mu mubiri gwo. Obubonero bwe bulabika, buyinza okuba obwangu ng’okuziyira oba okuzimba.
Kale, kiyinza okukuwuniikiriza okukimanya nti obubonero bwo buva ku bulwadde obutatera kulabika bwe butyo. Kiyinza okukuzitoowerera okutegeezebwa nti obujjanjabi bujja kuzingiramu okulongoosebwa okuggyamu ekitundu kimu oba ebisingawo mu lubuto lwo. Kiyinza okuba ekizibu okutegeera bino byonna omulundi gumu.
Naye teweeraliikiriranga. Abasawo bo bakitegeera nti oyinza okuba n’ebibuuzo bingi – mpozzi n’ebibuuzo bye bimu emirundi egiwerako. Nga bw’oyiga ku bujjanjabi bwo n’okulowooza ku mitendera gyo egiddako, baagala okuwulira buli kimu ekikuli mu birowoozo. Eyo ddembe lyo. Okubeera mu mbeera ennungi ey’obwongo nakyo kiyamba nnyo mu bujjanjabi.
` Pseudomyxoma Peritonei, PMP, kookolo, ekituli mu lubuto, mucin, olubuto lwa jelly, appendix, okulongoosa











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