Oluusi tuwulira nti, ‘Oh, omwana wange alina ekizibu ky’omutima ekitono, kyazaalibwa n’okwemulugunya kw’omutima’? Oba, omuvubuka bw’afuna obuzibu mu kussa oba ng’alumizibwa mu kifuba, abasawo bagamba nti, ‘Waliwo obuzibu obutono ku vvaalu y’omutima.’ Bw’etyo bwe tugenda okwogera ku mbeera y’omutima etali ya bulijjo nnyo, naye nga nkulu nnyo okumanya.
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Valiva eno ey’omusuwa gw’omusuwa ogw’ekipapula kimu (Unicuspid Aortic Valve) kye ki?
Mu ngeri ennyangu, vvaalu y’omusuwa gw’omusaayi mu mutima gwo erina akapapula kamu kokka mu kifo ky’obusatu bwe butera okuba nabwo. Ekigambo "unicuspid" kitegeeza "olupapula olumu." Kilowoozeeko ng’oluggi oluliko kkufulu emu yokka mu kifo ky’ebiri.
Obupapula buno bulinga enzigi entonotono. Zigguka ne ziggalawo okusobozesa omusaayi omuyonjo ogulimu omukka gwa oxygen okuyita okuva mu kisenge kya kkono eky’omutima - ekisenge ekya kkono wansi w’omutima - okutuuka mu aorta . Olwo omusuwa oguyitibwa aorta gukuba omusaayi mu mubiri gwonna. Kale, omuwendo gw’obupapula mu vvaalu eno bwe gukendeera, wayinza okubaawo obuziyiza obutonotono okutambula kw’omusaayi.
Abantu abamu abalina embeera eno, Unicuspid Aortic Valve, nabo bayinza okuba n’ebizibu ebirala eby’omutima. Okugeza nga:
- Aortopathy : Kino kitegeeza obunafu mu bisenge by’omusuwa.
- Ventricular Septal Defect (VSD) : Ekituli mu bbugwe wakati w’ebisenge bibiri ebya wansi eby’omutima.
- Patent Ductus Arteriosus (PDA) : Omusuwa ogwalina okuggalwa oluvannyuma lw’okuzaalibwa gusigala nga guggule.
- Coronary Artery Anomalies : Enkyukakyuka ezimu mu misuwa egigabira omutima omusaayi.
Eno mbeera ya bbula nnyo. Kikwata ebitundu nga 0.02% ku bantu bonna. Ekirala, kisinga kubeera mu basajja.
Waliwo ebika bya kino?
Yee, waliwo ebika bibiri ebikulu ebya Unicuspid Aortic Valve''. Enjawulo wakati w'ebika bino ebibiri kye bbanga ebipapula ebibiri (ebipapula) we bikwatagana ne bbugwe wa vvaalu, ekiyitibwa Commissure'' . Kino osobola okukitegeera bw’otyo. Kuba akafaananyi ng’emimwa gyo ginyweredde ku maaso go enkalakkalira, naye nga gisobola okukwatagana ne gyawukana, nedda? Ekyo kye kitegeeza Commissure''.
Ebika bino ebibiri bye bino:
1. Ekika kya Acommissural: Kino kye kika ekisinga okuba eky’amaanyi . Mu mbeera eno, tewali commissure, kwe kugamba, tewali gap. Era tekikwatagana na aorta. Ebipapula byonna binyweredde wamu, kumpi nga biweerezeddwa wamu. Omusaayi gukulukuta mu kinnya ekitono kyokka, ng’ekituli kya ppini.
2. Ekika kya Unicommissural:Kino tekiba kya maanyi nnyo okusinga ekirala, era nakyo kye kika ekisinga okubeerawo . Kirina Commissure emu, kwe kugamba, ekituli kimu. Era kiyungibwa ku aorta. Valiva ey’ekika kino bw’eggulwawo, eringa layini. Abantu abamu bagigeraageranya ku kamwa k’ekyennyanja.
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Singa omuntu omukulu aba n’embeera eno (Unicuspid Aortic Valve), obubonero obutera okulabibwa bwe buno:
- Okussa obubi : Bw’oba okooye katono, oyinza okuwulira ng’ogenda okuzirika ng’olinnya amadaala.
- Okuziyira : Bw’oyimirira mu bwangu, oyinza okuwulira ng’oziyira.
- Angina : Kino kiba kuwulira obulumi oba okunyiga mu kifuba. Ku bantu abamu, kino kiyinza okusaasaana mu bbwa, mu bulago oba n’emikono.
- Okuzirika/okuzirika : Okuzirika mu bwangu.
Abaana abato abalina embeera eno batera okufuna embeera ng’omutima okulemererwa ku ludda olwa kkono . Era batera okugejja ng’abaana abalala ab’emyaka gyabwe, ekitegeeza nti bagejja kitono nnyo.
Ekika kya Acommissural ekyayogeddwako emabegako, nga kino kye kika eky'amaanyi, kiraga obubonero mu baana abato ennyo . Naye abo abalina ekika kya Unicommissural bayinza obutalaga bubonero bwonna okutuusa nga bawezezza emyaka 20 oba 30, kwe kugamba okutuusa nga batuuse mu myaka emito.
Lwaki kino kigenda mu maaso? Ensonga eri etya?
Embeera eno eyitibwa Unicuspid Aortic Valve'', ebaawo ng'ebipapula ebisatu ebirina okutondebwa mu budde obutuufu bitandika okukula ng'omwana akyali mu lubuto, olwo mu kifo ky'okwawukana, ne bikwatagana ne bifuuka kimu. Kino kibaawo nga omwana tannazaalibwa na kuzaalibwa .
Wadde ng'abanoonyereza tebannaba kukikakasa mu butuufu, bateebereza nti eno eyinza okuba embeera ey'obusika.'' Ekyo kitegeeza nti wayinza okubaawo enkola y'obuzaale.
Kino kiyinza okuleeta bizibu ki?
Omuntu alina unicuspid aortic valve ayinza okufuna ebizibu eby’enjawulo okumala ekiseera. Ebikulu bye bino:
- Aortic valve stenosis : Kino kibaawo nga valve tegguka bulungi, ekiziyiza omusaayi okutambula. Kino kireetera omutima okukola ennyo okukuba omusaayi.
- Aortic valve regurgitation : Valiva teggalawo bulungi, ekivaako omusaayi ogumu ogusindikiddwa okukulukuta okudda mu mutima.
- Infective Endocarditis : Yinfekisoni y’omubiri gw’omutima naddala mu bitundu by’omubiri ebiyitibwa valves. Abantu abalina valve ezitali za bulijjo bali mu bulabe bwa maanyi.
- Okwongera ku bulabe bw’okusalako omusuwa : Eno mbeera ya mangu era ya maanyi ng’ekisenge ky’omusuwa kikutuka okuva munda.
Ekikulu: Kikulu nnyo okuzuula n’okujjanjaba obulwadde buno mu budde, ng’ebizibu bino tebinnabaawo.
Kino okisanga otya?
Bw’ogenda okulaba omusawo, ajja kuwuliriza omutima gwo ng’akozesa ekyuma ekiwuliriza ng’okeberebwa omubiri gwo . Singa omusawo awulira eddoboozi ly’omutima eritali lya bulijjo (heart murmur) okumpi n’omusuwa gwo, ayinza okuteebereza kino. Oluvannyuma, ayinza okukuwa amagezi okukeberebwa ebirala.
Bigezo ki ebikolebwa?
Ebigezo ebikulu ebikolebwa okukakasa obulungi nti waliwo embeera eno eya Unicuspid Aortic Valve'' bye bino:
- Transthoracic Echocardiogram (TTE) : Kino kiringa okukebera omutima mu ddoboozi ery’omwanguka. Kikolebwa ku ngulu w’ekifuba. Kisobola bulungi okwekenneenya enkula y’omutima n’enkola ya vvaalu zaagwo.
- Transesophageal Echocardiogram (TEE) : Kino nakyo kifaananyi kya mutima. Wabula akatundu akatono kayingizibwa mu mumiro era omutima ne gutunuulirwa nga guyita mu nnywanto. Kino kiyinza okuvaamu ebifaananyi ebitegeerekeka obulungi okusinga TTE.
- Cardiac Computed Tomography (CT) scan : Kino kiyinza okufulumya ebifaananyi ebisalasala mu 3D eby’omutima n’omusuwa gw’omusaayi.
- Heart MRI (Magnetic Resonance Imaging) : Kino era kisobola okuwa ebikwata ku nsengeka n’enkola y’omutima mu bujjuvu.
Kijjanjabwa kitya?
Obujjanjabi bwa kino bwawukana okusinziira ku myaka n’obuzibu bw’obubonero.
Obujjanjabi obutera okukozesebwa abaana abato bwe buno:
- Surgical Valvotomy : Kino kizingiramu okulongoosa okusala ebitundu bya valve ebisibye wamu n’okukola obupapula obupya.
- Valvuloplasty : Kino kizingiramu okukozesa ekintu nga bbaatule okuggulawo vvaalu.
- Commissurotomy : Okulongoosa okwawula ebitundu ebiyitibwa Commissures'' ebikowe by'amaaso we bikwatagana.
- Ross Procedure : Eno okulongoosa okusingako katono. Ebisingawo ku nsonga eno tujja kwogera oluvannyuma.
Ku bantu abakulu , okulongoosa kitera okwetaagisa okuddaabiriza vvaalu y’omusuwa (Unicuspid Aortic Valve repair) oba okugikyusa ne vvaalu empya (okukyusa) .
Waliwo ebizibu/ebizibu ebiva mu bujjanjabi?
Nga bwe kiri ku kulongoosa kwonna, waliwo ebizibu ebiyinza okuva mu bujjanjabi buno. Naye bino si buli muntu nti ajja kubifuna. Tofaayo, omusawo ajja kukumanyisa bulungi ku bino.
Ebimu ku bizibu ebitera okubaawo ebiyinza okubaawo bye bino:
- Ekirwadde
- Okuzimba omusaayi
- Okuvaamu omusaayi oguyitiridde (Bleeding) .
- Endocarditis (obulwadde bwa valve) .
- Obuzibu ku patch ekozesebwa mu kuddaabiriza valve.
- Complete Heart Block : Okutaataaganyizibwa kw’okutambuza obubonero bw’amasannyalaze bw’omutima.
- Omutima okulwala
- Omusaayi nga gukulukuta okuva ku vvaalu okudda ku ludda olukyamu.
- Ennyimba z’Omutima ezitali za bulijjo
Kitwala bbanga ki okuwona?
Kino kijja kwawukana okusinziira ku kika ky’enkola gye walina. Kiyinza okutwala wonna okuva ku wiiki emu okutuuka ku myezi egiwerako okuwona. Omusawo ajja kukubuulira ddala ebbanga ly’olina okuwummulamu ne ddi lw’osobola okuddamu okukola emirimu gya bulijjo.
Obulamu bunaaba butya ng’embeera eno ebaawo?
Bw’oba olina Unicuspid Aortic Valve, kirabika ojja kwetaaga okulongoosebwa . Mu butuufu, kiyinza okwetaagisa okuddaabiriza oba okukyusibwa vvaalu yo emirundi egisukka mu gumu mu bulamu bwo. Oyinza n’okuba n’ebizibu ebirala eby’omutima. Era oyinza okwetaaga okugenda mu maaso n’okumira eddagala erikendeeza omusaayi (anticoagulants) ng’omaze okulongoosebwa okusinziira ku kika kya vvaalu gy’olina.
Naye era kisaana okugambibwa nti kino Unicuspid Aortic Valve'' si kintu ekijja okutereera mu ngeri ey'otoma . Embeera eno esigala y’emu okutuusa lw’olongoosebwa okugitereeza.
Waliwo amawulire amalungi. Okunoonyereza okumu kwazuula nti abantu 97% abalongoosebwa omusuwa gw'omusaayi olw'embeera eyitibwa Unicuspid Aortic Valve'' baali bakyali balamu oluvannyuma lw'emyaka 10 .
Wabula era waliwo endowooza nti omuntu atali wansi w’emyaka 65 bw’aweebwa ekyuma ekiyitibwa prosthetic aortic valve olw’embeera eno, kiyinza okukendeeza ku bulamu bw’omuntu emyaka egisukka mu 10. Eno y’ensonga lwaki abanoonyereza bagamba nti Enkola ya Ross esinga ku bavubuka, abakola ennyo. Mu nkola eno eya Ross procedure, okwata valve yo ey'amawuggwe n'ogisimbuliza mu kifo awali valve y'omusuwa omulwadde. Olwo, ekintu ekiyitibwa pulmonary homograft okuva mu muntu omugenzi kisimbibwa mu kifo awaali vvaalu y’amawuggwe eyaggyibwamu. Wadde kino kizibu katono, kigambibwa nti ebyavaamu birungi.
Kiki ky’oyagala okukola ku ludda lwo?
Oluvannyuma lw’okulongoosebwa, olina okugoberera ebiragiro by’omusawo wo n’obwegendereza ku ngeri y’okulabirira ebitundu byo ebisaliddwa/ebisaliddwa . Era ajja kukubuulira ebbanga ly’olina okuwummulamu ne ddi lw’osobola okutandika okuvuga n’emirimu emirala egya buli lunaku.
Tewerabira: Kikulu nnyo okumira eddagala lyo mu budde, ng’omusawo bw’akulagidde, n’okugenda mu ddwaaliro ku nnaku eziteekeddwawo.
Oluusi olowooza nti, "Oh, sinnakula kufuna bulwadde bwa mutima," naye ng'okyalina obulumi mu kifuba n'okukaluubirirwa okussa.Bw’oba olina ekimu ku bino wammanga, kakasa nti olaba omusawo. Oluvannyuma lw’okulongoosebwa Unicuspid Aortic Valve, ojja kusigala ng’olina enteekateeka z’okugoberera n’omusawo wo. Singa ekizibu (nga yinfekisoni) kibaawo oluvannyuma lw’okulongoosebwa, oyinza okwetaaga obujjanjabi obw’amangu.
Bibuuzo ki by’osaanidde okubuuza omusawo?
Bw’ogenda okulaba omusawo, totya kubuuza kibuuzo kyonna ky’olina. Bino bye bimu ku bibuuzo by’oyinza okubuuza:
- Bujjanjabi ki obusinga okunkwatako?
- Njawulo ki eriwo wakati w’ebika eby’enjawulo eby’okukyusa vvaalu? (i.e., vvaalu ey’obutonde vs. vvaalu y’ebiramu)
- Nneetaaga okulongoosebwa amangu ki?
- Valiva empya essiddwaawo ewangaala bbanga ki?
Bw’owulira nti ekintu ekiri mu mutima gwo tekikola bulungi, si kyangu. Kyokka ekiseera bwe kigenda kiyitawo, abasawo bafunye obujjanjabi obulungi ku mbeera eno. Yogerako n’omusawo wo ku kisinga obulungi gy’oli. Since this is a rare condition , kirungi nnyo okufuna omusawo alina obumanyirivu ku yo. Ng’ekyokulabirako, abanoonyereza bagamba nti omusawo alongoosa alina okukola emirimu gya Ross egitakka wansi wa 15 buli mwaka.
N’ekisembayo, ekisinga obukulu okujjukira (Obubaka bw’okutwala awaka) .
Okay, kale nsuubira kati olina okutegeera okulungi ku bulwadde bw'omutima buno obuyitibwa (Unicuspid Aortic Valve) bwe twogeddeko leero. Jjukira nti kino kintu ekizaalibwa nakyo era ekitatera kulabibwa. Kyokka, singa ozuulibwa bulungi era n’ojjanjabwa mu budde, osobola okubeera n’obulamu obulungi . Bw’oba ggwe oba omuntu gw’omanyi alina obubonero buno, totya kulaba musawo n’ofuna amagezi. Naddala, kikulu nnyo okufuna obuwagizi bwa ttiimu y’abasawo abalina obumanyirivu ng’ojjanjaba embeera ng’ezo ezitatera kubaawo. Faayo ku mutima gwo. Kye kintu ekisinga okuba eky’omuwendo mu bulamu bwo!
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