I kal chhungah hian tumor te tak te a lo thang lian thei tih i ngaihtuah ngai em? A châng chuan, hengte hi chhinchhiahna awm lovin a awm thei bawk. Vawiin hian kidney-a tumor chi khat, kidney-a lo awm thei chungchang kan sawi dawn a ni. Angiomyolipoma an ti a, mi thenkhat chuan renal angiomyolipoma an ti bawk. A hming hi a sei deuhin a ri a ni lawm ni? Mahse, lungngai suh, awlsam takin i vawng ang u.
Angiomyolipoma hi eng nge ni tak tak?
A awlsam zawngin sawi ila, angiomyolipoma chu i kal chhunga cell thenkhat a lo thanglian dan pangngai lo taka lo thanglian a ni. Doctor te chuan tumor emaw neoplasm emaw an ti bawk . Mahse thu lawmawm tak chu angiomyolipoma tam zawk hi cancer (benign) an ni lo tih hi a ni. Hei hian harsatna lian tham an thlen a rinawm loh tihna a ni.
Heng nut te hi a bulpui pathum atanga siam a ni a:
- Adipose tissue , chu chu oil layer ang mai a ni.
- Smooth muscle a ni .
- Thisen kalna kawng (Blood vessels) hi thisen phurtu tube te tak te a ni.
Mahse, he tumor hi a lian zawk a nih chuan symptom thenkhat a lang thei. Entirnan, thisen chhuah , thisen tlakchhamna , khawsik , emaw, kal hmuna natna a awm thei.
Tute nge angiomyolipoma vei tam zawk?
Tu chungah pawh a thleng thei tak tak. Mahse, zirchianna chuan hmeichhiate hian he natna hi an vei tam zawk tih hmuhchhuah a ni a, a bik takin kum 40 leh 60 inkar te hian an vei tam zawk a ni .
Tin, hriselna lama harsatna thenkhat nei te hian angiomyolipomas an vei tam zawk bawk. Chutiang condition pahnih chu:
- Lymphangioleiomyomatosis (LAM) natna hi a awm thei lo.
- Tuberous Sclerosis Complex (TSC) a awm a, a chhuahna tur hmun leh a hmanna tur a awm lo.
Hei hi a buaithlak deuh a, mahse hetiang dinhmun hi i neih chuan doctor biak a, a chanchin hriat a pawimawh hle.
Engtiang chiahin nge angiomyolipomas hi kal (kidney) a awm?
Angiomyolipomas hi mipui zawng zawng 1% aia tlem lovah a awm thin. Chu chu an tlem tihna a ni lo, mahse mi zawng zawng chungah pawh a thleng lo. Mahse, benign kidney tumor chi khat zingah chuan an tam ber a ni.
Hei hi a chunga kan sawi tak tuberous sclerosis complex (TSC) vei zingah a awm fo thin. Chumi awmzia chu TSC vei zinga a chanve aia tam chuan angiomyolipomas an vei thei tihna a ni.
Angiomyolipomas chi hrang hrang a awm em?
Ni e, angiomyolipomas hi he tumor chhunga cell leh tissue awm chi hrang hrang a zirin chi thum ah then theih a ni:
1. 1. A rilru a hah lutuk chuan a rilru a buai em em a.Classic (triphasic) AMLs: Hei hi a tam ber chi a ni. A hmaa kan sawi tawh cell chi thum zawng zawng an nei vek a: thisen kalna kawng, thau tissue, leh smooth muscle .
2. Monophasic AMLs: Heng tumor chi hrang hrangah hian tissue chi khat a awm tam ber . Entirnan, smooth muscle chauh an nei thei a, thau tissue chauh an nei thei bawk.
3. Epithelioid angiomyolipomas: Hengte hi kal thisen kalna kawng chhunga line awm epithelioid cell atanga siam a ni ber. Hetiang tumor chi hi a dang aiin cancer a nih theihna a sang deuh hlek a ni . Chuvangin hei hi a bik takin ngaihven a ni.
Angiomyolipoma hi engtiang chiahin nge a nasat theih ang?
Vawi tam tak chu angiomyolipomas vei tam tak chuan an nei tih pawh an hre lo. Chu chu eng symptoms an neih loh fo vang a ni.
Mahse, he tumor hi centimetre 4 aia lian (chu chu kan ei tlangpui walnut ang vel a ni) a lo lian a nih chuan thisen a chhuak tan thei (hemorrhage) Hetianga thisen chhuah hi a hun taka enkawl loh chuan nunna atana hlauhawm a ni thei . Chuvang chuan heng tumor te hi fimkhur a pawimawh hle.
Angiomyolipoma hi engtiang chiahin nge a lo thang chak?
Classic angiomyolipomas tam zawk hi chu an thang lo tak tak lo . A nih loh leh, an tih chuan an ṭhang zawi zawi hle . A vaiin heng tumor te hi kum khatah centimetre 0.19 vel (inch sawm leh parukna hmun khat vel) velin an thang lian thin.
Mahse, heng tumor te hi naupai lai hian a lo thang chak zawk thei a ni . Chuvangin, angiomyolipoma i vei a, naute i beisei a nih chuan, i naupai hmain tumor enkawl hmasak phawt chu a finthlak mai thei . Hemi chungchang hi Doctor nen inbiak a tha ber.
Eng thilin nge angiomyolipoma hi a thlen?
Doctor-te chuan he tissue hi engvangin nge a khawlkhawm a, kidney tumor a siam tih chiang takin an la hre lo . Mahse, zirchiangtute chuan kan gene-a inthlak danglamna (mutations) thenkhat hian chanvo a nei thei niin an ngai.
Angiomyolipoma natna lan chhuah dan chu engte nge ni?
Kan sawi tawh ang khan angiomyolipoma vei tam zawk chuan symptom engmah an nei lo . Mahse, tumor a lo lian zel chuan symptom thenkhat a lang thei. Chung zingah chuan:
- Thisen chhuah avanga thisen tlakchhamna (anemia ) .
- Khawsik (fever) nei .
- Flank natna emaw, kal vel thisen chhuak avanga kal natna emaw .
- Thisen sang (hypertension) .
- Nausea leh luak chhuak .
Heng symptoms pakhat emaw a aia tam emaw i neih chuan a rang thei ang bera doctor pan a pawimawh hle.
Engtin nge angiomyolipoma i vei tih i hriat theih ang?
A châng chuan, i doctor chuan hrisêlna dang i neih theih nân imaging test , scan ang chi i neih hunah tumor chu a hmu mai thei a ni. A nih loh leh, a chunga kan sawi tak symptoms i neih chuan i doctor chuan a chhan zawng turin heng test te hi a ti thei bawk.
Eng ang test nge he thil hi a hriatchhuah?
Doctor-te chuan hetiang ang imaging test hi an rawt tlangpui:
- CT scan a ni
- MRI hmanga tih a ni
- Ultrasound hmanga tih a ni
Mahse, angiomyolipomas chi thenkhat chu heng scan-ah hian kidney cancer ang maiin a lang thei . Chuvangin, a dik tak chuan i doctor chuan kidney biopsy neih a rawt mai thei a, chu chu kidney tlemte la a, test a ngai a ni .
Engtin nge ka angiomyolipoma hi enkawl a ngai em tih ka hriat theih ang?
Angiomyolipoma vei zawng zawng hian enkawl an mamawh vek dawn lo. Enkawlna i mamawh leh mamawh loh chu tumor lian leh te , symptom i neih leh neih loh leh nakin lawka naupai i tum leh neih lohah a innghat a ni
A tlangpuiin kum khatah vawi khat vel doctor i pan a ngai ang a, chu chuan tumor a lo thang lian zel ang. Tumor chu centimetre 4 aia lian a nih chuan i doctor chuan enkawl a rawt thei ang.
Angiomyolipomas hi engtin nge enkawl an nih?
Doctor chuan tumor lian zel tur tihtawp nan emaw, paih chhuah nan emaw enkawlna a rawt thei a ni. Chung zinga ṭhenkhat chu:
- Ablation therapy: He enkawlnaah hian doctor-te chuan chakna (entir nan , radiofrequency waves ), lum lutuk, a nih loh leh boruak lum lutuk hmangin angiomyolipoma chu an tichhia a ni.
- Arterial embolization: Hetiang tih danah hian i kekawr chhungah hian incision te tak te siam a ni a, tube te tak te (catheter) dah a ni a, chuta tang chuan bead te te te dah a ni. Heng beads te hian angiomyolipoma-a thisen kal chu a titawp a ni. Hei hian tumor chu a ti tlem a, thisen kal a ti tlem a, thisen chhuah theihna a ti tlem bawk.
- Complete nephrectomy: He surgery hian angiomyolipoma awmna kal zawng zawng a paih chhuak vek a ni .
- Partial nephrectomy: Hei hian kal pumpui a la chhuak lo. Kidney atanga angiomyolipoma awmna hmun chauh lakchhuah a ni . Hei hi open partial nephrectomy emaw robotic partial nephrectomy emaw angin tih theih a ni .
A pawimawh ber chu i doctor nen inbia a, i tana tha ber tur enkawl dan tur thlang la.
Enkawl hnuah harsatna emaw, side effect emaw a awm em?
Kidney surgery leh angiomyolipoma enkawlna dang hnuah pawh hlauhawmna engemaw zat a awm thei. Entir nan:
- Thisen chhuak
- Kaichhawng
- Scars a awm
A chang chuan kal (kidney) enkawl hnuah kal (kidney failure) a awm thei bawk. Mahse hei hi a tlem hle. I doctor chuan enkawl hmain heng hlauhawmnate hi a sawipui ang che a, tihtlem nan hma a la ang. Kidney failure a awm chuan i doctor chuan i symptoms te enkawl dan tur leh a hrisel thei ang bera awm theihna tur treatment plan a siam ang che.
Enkawl hnua dam leh theih nan eng chen nge a duh?
Nephrectomy kimchang emaw, a then emaw i neih tawh chuan ni engemaw zat damdawi inah i awm a ngai ang. Doctor-te pawhin i kal (kidney) hnathawh dan an enfiah ang a, i dam tha em tih an enfiah bawk ang.
Ablation therapy emaw arterial embolization emaw i neih chuan darkar engemaw zat emaw zan khat emaw damdawi inah i awm a ngai ang.
Angiomyolipoma hi ven theih a ni em?
Dik tak chuan angiomyolipomas lo awm tur venna tur kawng bik a awm lo . Heng tumor te hi a takin a lo awm fo thin a, a chhan chiang tak a awm lo . Chumi awmzia chu AML thlen chhan bik sawi a harsa tihna a ni.
Angiomyolipoma vei theihna chance sang zawka min siamtu dinhmun dang a awm em?
Awle. Tuberous sclerosis complex (TSC) emaw lymphangioleiomyotosis (LAM) emaw i neih chuan angiomyolipoma i vei theihna a sang hle. Chuvangin, i hriselna enkawl dan tur leh i hlauhawmna tihziaawmna tura hmalakna tur i doctor nen sawiho rawh.
Angiomyolipoma ka neih chuan eng nge ka beisei ang?
Angiomyolipoma nei mahse symptom i neih loh chuan kum khatah vawi khat vel doctor i pan a ngai dawn a ni . Tumor chu a lo thang lian em tih hriat nan imaging test i neih a ngai thei bawk.
If you have symptoms , i doctor chuan thisen chhuah theihna tur venna atan enkawlna a rawt thei ang.
Angiomyolipomas hian hun rei tak chhung nghawng a nei thei em?
Angiomyolipomas a lian chuan thisen a chhuak thei a, a rupture thei bawk . Chuvangin i doctor chuan tumor lian leh te a enfiah fo ang a, i hlauhawm a nih chuan enkawl turin a rawt ang che.
Angiomyolipoma hi vawi khat aia tam ka vei thei ang em?
Yes , angiomyolipoma hi enkawl hnuah a lo thang leh thei .Tin, angiomyolipoma pakhat aia tam a awm thei bawk a, AMLs hi kidney pahnih ah a lo awm thei bawk .
Angiomyolipoma hi cancer a ni thei em?
Chutiang tumor chi khat kan sawi tawh, epithelioid angiomyolipoma tia koh chu a châng chuan cancer-ah a chang thei a ni . Chutiang a nih chuan i doctor chuan ngun takin a lo en reng ang che a, i tih tur chungchang a sawipui ang che.
Angiomyolipoma ka neih chuan engzat nge doctor ka hmuh ang?
I doctor nen thawk ho la , enkawlna tur ruahmanna siam rawh . Follow-up appointment zawng zawng chu vawng reng la, tumor-ah hian a lo thang lian em tih enfiah rawh.
Engtikah nge ka doctor ka biak ang?
Heng symptom thar te hi i neih chuan doctor ko nghal rawh :
- Pum natna
- Hnung lam natna
- Khawsik
- Nausea leh luak chhuak
- Hematuria - zun chhunga thisen awm
A tawp berah chuan thil hriat reng tur (Take-Home Message) .
Angiomyolipoma hi benign tumor a ni a, a tlangpuiin kidney-ah a lo awm thin. Symptoms i nei lo mai thei. I doctor chuan kum tin tumor chu a lo thang lian em tih a enfiah ang. Tumor centimetre 4 aia lian chuan thisen chhuah loh nan enkawl a ngai thei.
A pawimawh ber chu symptoms i neih chuan hlauthawng suh la, i doctor nen inbia nghal rawh. I mamawh enkawlna leh kaihhruaina tha ber an pe ang che.
` Angiomyolipoma, kal cyst, kal natna, benign tumor, kal natna, thisen tlakchhamna, tuberous sclerosis











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