I fate mit i en hian mit pakhat emaw, pahnih emaw chu a dang aiin a lian deuh niin i hre ngai em? A nih loh leh, thla a lo kal zel a, naute mit chu zawi zawiin a lian chho zel tih i hmu em? A châng chuan hei hi Buphthalmos tih hming pu dinhmun chhinchhiahna a ni thei bawk . Ngaihtuah buai suh, vawiinah hian thumal awlsam takin kan sawi vek ang.
Buphthalmos hi eng nge a nih i hria em?
A awlsam zawngin, buphthalmos hi naute mit emaw, a mit pahnih emaw chu a pian tirh emaw, a pian tirh thla engemaw zat chhunga a pian tirh emaw, a pian tirh emawa a mit emaw, a mit pahnih emaw chu a tlangpui aia lian a nih chuan a ni. Hei hi congenital condition , pian tirh atanga awm tihna a ni. Nausen thenkhat chuan mit pakhat chauh (unilateral)-ah he enlargement hi an nei thei a, thenkhat erawh chuan mit pahnih (bilateral)-ah an nei thei thung.
Ngaihtuah teh, hetiang hian "buphthalmos" tih hming hi a lo piang ta a ni. Greek tawngin "bu" tih hi bawng tihna a ni a, "ophthalmos" tih hi mit tihna a ni. Chuvangin bawng ang maia mit lian tak a neih avangin a hming a pu ta a ni. Hmanlai Greek doctor Hippocrates-a chuan he natna hi a hmuchhuak hmasa ber a ni.
Hei hi autosomal recessive genetic condition a ni a . Chumi awmzia chu naupangin he natna hi a neih theih nan chuan naupangin a nghawng gene chu nu leh pa pahnih hnen atangin a dawng tur a ni tihna a ni. Lottery ang maiin han ngaihtuah teh. Nu leh pa pahnih hian gene hi an nei ve ve thei a, mahse an hre lo mai thei. A vaiin chutiang nupa fa pali zinga pakhat chuan he natna hi a nei ang.
Hetiang dinhmun hi engtiang chiahin nge a awm?
Buphthalmos hi natna hlauhawm tak a ni. Nau piang 30,000 zinga pakhat vel ah a awm thin . Mipa leh hmeichhia a nghawng thei. Mahse, zirchianna ṭhenkhatah chuan hmun ṭhenkhat, Slovakia, Saudi Arabia leh India khawthlang lama mite chu he natna hi an vei theihna a sang zawk tih hmuhchhuah a ni.
Buphthalmos natna lan chhuah dan chu engte nge ni?
Nausen piang thar emaw, nausen thla engemaw zat a upa emaw chhinchhiahna langsar leh langsar ber chu an mit a lianin a lang. Mit pakhat emaw, mit pahnih emaw pawh a lian thei. Hei hi a chhan azirin i naute hian symptom dang a nei thei bawk. Chung zingah chuan:
- Mit atang chuan mittui a luang chhuak reng a, mit chu a sen angin a lang a, mit chu a danglamin a hnim reng bawk .
- Eng laka hriatna (photophobia) . Chumi awmzia chu naute chuan êng chu a en duh lo va, a mit a chhing a, a buai hle tihna a ni.
- Mitdel tam lutuk, a nih loh leh mitmeng tichhe deuh tih hriatna.
- Mit , a tlangpuiin mit thianghlim tak chu cornea , chu chu chhum ang maiin a lang a, vur tlain a khuh ang maiin a lang.
- Cornea chu a inzawm khawm a, a hring a, a châng chuan a hrual hrual pawh a ni .
I naute hian heng symptoms pakhat emaw a aia tam emaw a neih chuan doctor i pan ngei ngei tur a ni.
Engvangin nge kan naute chungah hetiang hian a thleng? A chhan engte nge ni?
Buphthalmos vei chhan ber chu primary congenital glaucoma emaw primary infantile glaucoma emaw an tih a ni. Glaucoma chungchang hi i hre tawh mai thei. Glaucoma hian mit chhunga optic nerve a tichhia a, chu chuan mit a tichhe thei a ni. Hei hi mit chhunga tui chi khat siam chhuah a chhuah that loh vang niin an ngai a, chu chuan mit chhungah pressure a tipung (intraocular pressure emaw IOP)
- Primary congenital glaucoma chu pian tirh atanga tan thin glaucoma a ni.
- Primary infantile glaucoma chu pian leh kum thum inkar atanga tan thin glaucoma a ni.
He a chhan ber bakah hian buphthalmos hi chhan dang engemaw zat avang hian a lo awm thei bawk:
- Aniridia: Hei hi thil awm lo tak a ni. Mit rawng chi hrang hrang, iris , a awm loh vek emaw, a then emaw a awm loh vang a ni. Aniridia hian mit hmuhna a nghawng thei.
- Neurofibromatosis type 1: Hei pawh hi thlahtute atanga lo chhuak a ni fo bawk. Nerve-ah tumor a lo awm thei a, chu chuan mit lama harsatna a thlen thei bawk.
- Sturge-Weber syndrome: Hei hi genetic condition a ni bawk. Thisen kalna kawng a tipung nasa lutuk a, angiomas tih hming pu lump a siam thin. Hetiang dinhmun hian vun, thluak leh mit a nghawng thei a ni.
- Nau piang hliam: Naute pian laia mit a chhiat chuan chu pawh chu a chhan a ni thei bawk.
Hei hi hmuchhuak tur hian eng ang test nge tih thin?
Nu leh pate hian an fate mitmenga danglamna an hmu hmasa ber fo thin. I fate mit hmuhnaah thil dik lo a awm nia i rinhlelh chuan damdawi lam thurawn zawng nghal rawh . I naupang enkawltu doctor chuan mit enkawltu specialist hnenah a refer mai thei che.
Hei hi buphthalmos leh congenital glaucoma ang chi dinhmunah chuan a pawimawh hle a, a hmaa enkawl hian naupang mit a tichhe thei zawk a ni
Buphthalmos dik taka hriat theih nan doctor chuan naupang chu anesthesia hnuaiah dahin test engemaw zat a tih a ngai thei a, chungte chu:
- Mit enfiahna uluk tak: Hei hian doctor chuan mitmeng (cornea)-a chhum, hliam emaw, a hring emaw a awm leh awm loh a enfiah thei ang. Tin, mit an teh ang a, mit atanga optic nerve a chhuahna optic disc cupping a awm leh awm loh an enfiah bawk ang.
- Retinoscopy: He test hmang hian doctor chuan naupangin a nei em tih a en thei a niRefractive error, myopia (nearsightedness) ang chi a awm em?
- Gonioscopy: He test hian mit drainage system a thawk tha em tih a enfiah thin. Mit hrisel chuan tui a siam chhuak a, a chhuah fo bawk. Glaucoma-ah chuan he tui hi a chhuak tha lo va, a pungkhawm a, pressure a tisang a, mit nerve a tichhe bawk.
- Ultrasound biomicroscopy: Hei hi natna nei lo test a ni. Mit hmalam thlalak chiang tak a la thei a, fluid drainage lama harsatna awmte pawh a hmu thei bawk. Ultrasound pangngai (sonogram) aiin thlalak chipchiar zawk a siam thei.
Buphthalmos natna enkawl dan tur chu engte nge ni?
Buphthalmos enkawl hian mit chhunga pressure (ocular pressure) control a pawimawh hle . Hetiang pressure tihziaawmna tur kawng hrang hrang a awm. Damdawi hi chutiang zinga mi a ni.
- Hemi atan hian eye drops emaw topical items emaw hman a ni. Heng zingah hian damdawi beta blocker , prostaglandin analogs , carbonic anhydrase inhibitor te a awm a ni .
Mit chhunga tui awm chu chhuah tir thei tur leh pressure tihhniam thei tur surgical procedure pawh a awm bawk:
- Mit chhungah implant te te dah.
- Mit structure- a cut te te siam.
- Mit atanga tissue lakchhuah.
Dik tak chuan, i fain buphthalmos a vei a nih chuan, enkawl ngai natna dang (neurofibromatosis type 1, Sturge-Weber syndrome, emaw aniridia ang chi) pawh a nei thei bawk. Doctor pawhin chutiang dinhmun chu a enkawl bawk ang.
Hei hi ven dan tur a awm em?
Buphthalmos hi ven theih dan tur a awm lo va , mahse naupang dam tirh atanga a natna hriatchhuah a, enkawl hmaa tan chuan a rah chhuah pawi tak a awm loh nan a pui thei a ni
Buphthalmos i neih chuan eng nge thleng? Eng nge i beisei theih ang?
A tha ber chu buphthalmos hi enkawl theih a ni . Mit a hloh loh nan a rang thei ang bera hriatchhuah leh enkawl a tha ber.
Hetiang dinhmunah hian engtin nge ka fa chu ka enkawl ang?
Mi zawng zawng tan mit enfiah fo a pawimawh. Hei hi pianpui mit natna nei tan chuan a pawimawh hle. I fate mit hmuh danah inthlak danglamna a awm leh awm loh leh engtikah nge doctor an hmuh tur tih i doctor zawt la.
Heng test bakah hian mit hrisel tak neih theih nan theihtawp chhuah thin ang che. Mit hriselna tha neih nan heng thilte hi a pawimawh a ni:
- Ei leh in hrisel leh tui in tam.
- Mut tam leh taksa tihchakna .
- Ni chhuahnaah te, hnathawh lai te, infiamna khelh lai te pawhin invenna glasses vuah thin ang che.
- Meizial zuk loh tur (hei hi naupang chhehvela puitlingte tan pawh a hman theih).
Naupang mit hriselna hi a pian tirh atanga puitlin thlenga enkawl a pawimawh hle. Hei hi mit natna, pian tirh atanga tan emaw, naupan lai thla engemaw zat atanga tan emaw tan chuan a dik hle. Ringhlelna i neih emaw, i fa mit hmuh danah danglamna i hriat chuan Doctor pan nghal rawh.
A tawp berah chuan thil hriat reng tur (Take-Home Message) .
I naute mit chu a danglam bik taka lian anga a lan chuan buphthalmos . Hei hi congenital glaucoma nen a inzawm fo thin .
- Don't worry , hei hi enkawl theih a ni.
- A hmaa hriatchhuah leh enkawl hi naupang mit hmuhna venhimna tha ber a ni.
- Ringhlelna tlemte i neih chuan mit lam doctor pan nghal rawh .
- Damdawi lam thurawn zawm a pawimawh a, follow-up neih reng a pawimawh bawk .
Nangmah chauh i ni lo tih hre reng ang che. Doctor leh health worker ten nang leh i naute tanpui turin an inpeih reng a ni.
` buphthalmos, nausen glaucoma, pianpui glaucoma, mit tizau, mit pressure, optic nerve, cornea











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