Cancer chi khat, a bik takin thalai zingah, kal (kidney)-a lo awm, a tlem em em leh pawi tak mai hi i hre tawh em? A ni lo mai thei. Hei hi Renal Medullary Carcinoma, a tawi zawngin RMC a ni. A tam vak lo nachungin, a bik takin mi thenkhat tan chuan fimkhur a pawimawh hle thei. Hei hi thupui pawimawh tak ni mahse, hlau suh. Vawiin hian a awlsam, hriatthiam theih takin i sawi dawn nia.
RMC hi eng nge ni tak tak?
A awlsam zawngin sawi ila, Renal Medullary Carcinoma (RMC) hi kal cancer chi khat a ni. Mahse a tlem hle a, a chetsual hle a, a darh chak hle bawk. Thalaite zingah a tam ber a, a bik takin thisen lama harsatna nei `sickle cell disease` emaw `sickle cell trait` emaw nei te zingah a tam ber.
Kidney cancer chungchang kan sawi hian a chi khat chu `renal cell carcinoma` a ni. RMC hi `renal cell carcinoma` subtype a ni bawk. Mahse kidney cancer vei 100 zinga pakhat pawhin he RMC natna hi an nei lo. Chutiang khawpa rare chu a ni.
Eng thilin nge he cancer hi a thlen?
Scientist leh doctor te chuan 100% in he thil hi a chhan dik tak an la hmu lo a, mahse thil pawimawh tak pakhat chu hriatchhuah a ni.
Kan kal (kidney) hian `renal medulla` an tih hmun a nei a. `Sickle cell` condition nei chuan a chang chuan thisen sen a nei a, chu chu sickle angin a inthlak thin. Chutiang a nih chuan cell te chu an inzawm khawm thei a, kal `renal medulla` part-a thisen kalna kawngte chu an tikhawlo thei a ni.
Hetianga thisen kalna kawngkhar hian chu hmuna cell awmte chu a tichhia a ni. A bik takin, chu cell-a awm `INI1` (`SMARCB1` tia koh bawk) gene pakhat chu a chhe ta hle a ni. He `INI1` gene hian cell te cancer vei lo tura titawptu `guardian` angin hna a thawk a ni. RMC cancer cells te hi an enfiah chuan he `INI1` gene hi an chhungah hmuh tur a awm lo. Chuvangin doctor-te chuan he `INI1` gene hi a awm leh awm loh an enfiah a, tumor chu RMC a nih leh nih loh an finfiah thin.
Kei pawh RMC vei theihna hlauhawmah ka awm em?
He thil hi tuin nge ti hmasawn dawn tih chiang taka sawi a harsa khawp mai. I chhungkuaa RMC vei i neih hian i vei theihna a tipung lo. Chhungkaw hrang hranga kal thei thil a ni lo tihna a ni.
A hlauhawmna ber chu thisen lama natna `sickle hemoglobinopathy` an tih hi a ni. Chu chu `sickle cell natna` emaw `sickle cell trait` emaw nei tihna a ni. But very rarely , heng natna nei lote pawhin RMC an nei thei bawk. “Renal cell carcinoma, medullary phenotype nena thliar hran loh” (RCCU-MP) an ti a.
Statistics i en chuan:
- Hmeichhia aiin mipaah a tam zawk.
- Kidney dinglam a nghawng tam ber.
- He natna hi kum naupang, kum 11 leh 39 inkar atanga hmuhchhuah a ni tlangpui.
Thalaite tan, a bik takin sickle cell natna emaw, sickle cell trait nei te tan chuan heng symptoms te hi hriat chian a pawimawh hle a, a hmaa hriatchhuah hian enkawlna a ti awlsam thei a ni. Symptoms a awm chuan doctor pan nghal tur a ni.
RMC natna lan chhuah dan chu engte nge ni?
He natna lan chhuah dan tlangpui engemaw zat a awm. Chung zinga pakhat emaw a aia tam emaw i neih chuan a rang thei ang bera damdawi lam thurawn lak a tha ber.
| Symptom a ni | Hrilhfiahna |
|---|---|
| Kidney area ah natna a awm | Pum sir lehlamah leh hnungzang hnuai lam (groin chunglam chiah) ah natna awm reng a ni. |
| Thisen chu zun chhungah a awm | Pink, red, emaw brown emaw zun a awm. A châng chuan mit hmuh theih loh thisen a awm thei bawk. |
| Pum chhunga natna hrik | Pum sir khata lump ang maia awm lump emaw mass emaw. |
| Chhan awm lovin taksa rihna tihtlem | Hun rei lote chhungin rang taka taksa rihna tihtlem, thawhrimna awm lovin. |
| Khawsik leh zan lama thawk hah fo | Chhan dang vanga khawsik i neih fo a, zanah i thawmhnaw i thawmhnaw a hnim lutuk a nih chuan. |
Engtin nge doctor hian hei hi a hriat chian?
I natna lan chhuah dan min hrilh hian doctor-in a tih hmasak ber tur chu a enfiah hmasa phawt ang che. Tichuan heng step te hi i zawm thei ang.
1. 1. A rilru a hah lutuk chuan a rilru a buai em em a.Ultrasound scan: Hei hian kal (kidney)-ah hian tumor ang chi thil a awm em tih chu a rough idea a pe thei.
2. CT emaw MRI scan: Tumor rinhlelh a nih chuan CT scan emaw MRI emaw tih tur a ni a, chu chu tumor thlalak chiang taka hmuh theih nan a ni. Heng thlalak atang hian doctor chuan cancer a nih theih dan tur a hre thei a ni.
3. Biopsy: Cancer-a rinhlelh nasat a nih chuan he test hi tih chian a ni. Hei hian kidney tumor awmna hmunah hian needle tha tak dahin, tissue te tak te tak tak lak a, microscope hmanga enfiah a huam a ni.
4. Genetic testing: Biopsy atanga cell lakchhuah te hi a hmaa kan sawi tawh cancer dotu `INI1` gene awm leh awm loh enfiah thin a ni.
- `INI1` gene a awm loh chuan RMC tia hriat a ni.
- `INI1` gene a bo a, damloin `sickle cell` condition a neih loh chuan `RCCU-MP` a ni tih hmuhchhuah a ni.
- `INI1` gene a awm chuan RMC a ni lo va, tumor chi danglam tak a ni.
Hei hi eng enkawlna nge ni?
RMC hi cancer darh chak tak, natna khirh tak a nih avangin enkawl pawh hi a rang leh a nasat ve ve a ngai a ni.
- Chemotherapy: Hei hi enkawl hmasak ber a ni. Cancer cells that thei damdawi taksa hnena pek a huam a ni.
- Surgery: Cancer tumor leh a awm thei kidney natna te lakchhuah.
- Radiation Therapy: Radiation beam chak tak hmanga cancer cell tihchhiat.
He natna hi a tlem em avangin zirchianna a la kal zel a ni. Scientist te hian RMC enkawlna thar leh tangkai zawk an zawng fo thin.
RMC ven dan tur a awm em?
Vanduaithlak takin tunah hian RMC lo awm tur ven dan tur hriat a la awm lo a, symptoms a lan hmaa test pawh a awm lo.
I tih theih tha ber chu fimkhur hi a ni . Sickle cell natna emaw sickle cell trait emaw i nei tih i hriat chuan a chunga kan sawi tak symptoms te hi fimkhur hle ang che. Thil ngaihtuah tur i neih chuan doctor pan nghal rawh.
Vawi tam tak chu he natna hi an hriat chhuah meuh chuan cancer hi lymph node emaw, taksa peng dang, lung, thin, leh ruh-ah te a darh tawh a ni. Chuvangin, a hmaa hriatchhuah hi a tha ber tur a ni.
Take-Home Thuchah a ni
- Renal Medullary Carcinoma (RMC) hi kal cancer chi khat, a tlem hle a, mahse a na hle a, thalai te a nghawng ber a ni.
- Hei hi a lo vei theihna tur risk factor ber chu thisen natna
sickle cell diseaseemawsickle cell traitan tih hi a ni . - Back/abdominal na, zun chhunga thisen, pum chhunga lump, leh sawifiah theih loha taksa rihna tlahniam te hi a lan chhuahna ber a ni.
- Sickle cell natna i neih a, a chunga chhinchhiahna pakhat emaw a aia tam emaw i neih chuan tihkhawtlai lohvin doctor pan nghal tur a ni.
- He natnaah hian a hmaa hriatchhuah leh enkawl tan hi nunna chhanhimna chance tha ber a ni.











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