Khaw lum laiin, a bik takin Nuwara Eliya ang hmuna i kal hian kut zungtang leh ke ruh dum, sen, leh na tak tak i nei bawk em? A chang chuan hliam te te i nei thin em? Mi tam tak chuan hei hi khawsik pangngai maiah ngai mah se, a châng chuan hei hi ngaihven deuh deuh ngai natna a ni thei bawk. Vawiin hian ‘Chilblain Lupus’ kan sawi dawn a, lupus chi khat hmuh tur awm lo mahse pawimawh tak a ni.
Chilblain Lupus hi eng nge ni?
A awlsam zawngin Chilblain Lupus hi kan vun tichhe thei lupus chi khat hmuh tur awm lo tak a ni. Damdawi lamah chuan ``cutaneous lupus erythematosus emaw CLE emaw kan ti a ni.`` Hetiang natna vei hian khawsik a tawrh hian vunah natna sen emaw, sen emaw, plaques, a nei thin.
"Chilblain" tih thumal hi a awmzia takah chuan "cold sore" tihna a ni. Hetiang dinhmunah hian hetiang chiah hian a thleng thin. Khua lum hian heng symptoms te hi a thlen thei a, a nih loh leh dinhmun awmsa chu a ti na zual thei bawk.
Vawi tam tak chu mi thenkhat chuan lupus chi khat ber, ``systemic lupus erythematosus'' an vei tih hmuhchhuah a nih hnuah Chilblain Lupus an vei thin. Mahse, mi dangte chuan hriat hmasak lohvin he natna hi an nei thei a ni. Mahse, he natna avanga natna leh lungawi lohna hi a na hle. I kut zungtangah, a bik takin i kut zungtang leh ke ruh-ah itchy, raised spot i hmuh chuan doctor pan nghal a, enkawl a tha ber.
Hetiang natna lan chhuah dan hi engte nge ni?
Chilblain Lupus hi vunah hian a sen emaw, a sen emaw a awm emaw, a hliam emaw a awm tlangpui. Hengte hi a tam ber chu:
- Kut kut zungtang chungah chuan
- A kekawrte chungah
- Kephah hnuai lamah
- Ke ruh chhungah
Mahse a tlem hle a, heng hliamte hi kutphah, khup, hnar emaw beng emaw-ah pawh a awm thei bawk. Chung zawng zawng chu khaw lum emaw, khaw vawt emaw-ah a na ber.
Heng symptom lian ber berte bakah hian symptom dang engemaw zat hmuh theih a awm bawk. Eng nge an nih i en ang u.
| Symptom a ni | A sawifiahna awlsam tak |
|---|---|
| Blisters emaw ulcer emaw a awm thei | Thisen kal tha lo avanga vun chunglama hliam dam lo. |
| Vun rawng danglam (Depigmentation) . | Vun hmun thenkhatah chuan a rawng a hloh a, a hring vek bawk. |
| Heel fissures a awm | Heels vunah hian deep cracks a awm. |
| Vun a thim (Hyperkeratosis) . | Vun natna hmuna vun thicking. |
| Raynaud-a phenomenon chu a ni | Khua a awm chuan kut zungtang leh ke ruh thlenga thisen kal chu hun eng emaw chen a khap tlat a ni. Hei hian kut zungtangte chu a var emaw, a sen emaw, a sen emaw a siam thei a ni. |
Engvangin nge Chilblain Lupus hi a lo awm? A chhante chu engte nge ni?
Chilblain Lupus hi a chhan lian ber pahnih a awm a. Pakhat chu genetic a ni a , pakhat chu sporadic a ni .
Hereditary avanga lo awm a ni
Hetiang dinhmun hi kan genes-a inthlak danglamna engemaw zat avanga lo awm thei a ni. A bik takin, gene `(TREX1)` leh `(SAMHD1)` inthlak danglamna hian hei hi a nghawng tih hmuhchhuah a ni. A awlsam zawngin sawi ila, `TREX1` gene hian kan DNA siamthatna kawngah a pui a, `SAMHD1` gene hian kan immune system hnathawhnaah a inrawlh bawk. Heng genes-ah hian chhiatna a awm chuan chhungkua leh naupang tête zingah Chilblain Lupus thlentu a ni thei.
Chhan awm lovin a thleng
Mi thenkhat tan chuan hei hi rochun a ni lo. Puitlingah a lo lang nghal thei. A chhan dik tak erawh hriat a la ni lo.
Tute nge hetiang hi vei theihna hlauhawm zawk?
He natna hian tu pawh a nghawng thei a, mahse puitling kum upa zawkah a tam ber . Khaw lum leh vawt rengna hmuna chengte pawh hi an hlauhawm zawk bawk.
Tin, damdawi dang thenkhat chuan Chilblain Lupus vei theihna a tipung thei bawk.
- Anorexia nervosa: Hei hi ei leh in lama harsatna lian tak, nunna atana hlauhawm tak a ni.
- Intestinal lymphoma: Hei hi cancer chi khat, kan intestine te tak te lymphatic system-a awm thin a ni.
- Naupai: Hmeichhe thenkhat chu naupai lai pawhin he natna hi an vei theihna hlauhawm tak an ni.
Enkawl loh chuan eng harsatna nge thleng thei?
He natna hi enkawl tha a nih loh chuan vun hliamte chu bacteria in a kai thei a ni . Heng mite hian vun natna ``cellulitis`` ang chi an vei theihna a sang hle.
Tin, Chilblain Lupus vei chuan a tawpah chuan systemic lupus erythematosus a nei thei a, chu chu lupus natna na ber, taksa system hrang hrang tichhe thei a ni.
Hei vang hian i vunah thil danglam bik, a bik takin hliam dam lo i hmuh chuan ngaihthah lo la, Doctor i pan tur a ni kan ti.
Engtin nge doctor hian hei hi a hriat chian tak tak?
Heng symptoms te hi i neih chuan dermatologist emaw rheumatologist emaw hnenah i refer thei ang .
He natna hriat theihna atana test ber chu vun biopsy a ni . Hei hian i vunah hliam pakhat atanga vun te tak te tak tak lak a, laboratory-a microscope hmanga enfiah a huam a ni. He test hian Chilblain Lupus emaw vun natna dang emaw i neih leh neih loh a finfiah thei a ni.
Hei hi eng enkawlna nge ni?
I Chilblain Lupus hi a na lutuk lo a nih chuan khawsik laka inven mai mai a ngai mai thei. Tin, i zuk chuan i doctor chuan bânsan turin a fuih ngei ang che. Meizial zuk hian kan thisen kalna kawng a tikhawtlai a, chu chuan heng symptoms te hi a ti na zual thei a ni.
A lan chhuah dan a hniam emaw, a na emaw a nih chuan doctor chuan damdawi chi hrang hrang a pe thei a ni.
| Ruihhlo chi hrang hrang | Hna a thawh thin chu |
|---|---|
| Antibiotics damdawi a ni | Vun hliam bacteria infection enkawl nan. Entirnan: `dicloxacillin`, `erythromycin` tih te hi a ni. |
| Malaria dona atana hman tur a ni | Taksa chhunga inflammation, hahna, leh ruh natna tihziaawm nan. Entirnan: `hydroxychloroquine` tih te hi a ni. |
| Immune tichhe thei damdawi (Calcineurin inhibitors) te hi a tha hle. | Immune system hnathawh tihtlem leh inflammation control nan. Entirnan: `tacrolimus`, `mycophenolate mofetil` tih te hi a ni. |
| Calcium channel blocker a ni | Thisen kalna kawng hawn leh thisen kal awlsam zawk nan. Entirnan: `nifedipine` tih te hi a ni. |
| Steroid oint hmanga siam a ni | Vun hring leh vun natna tihziaawmna turin. Entirnan: `fluocinolone acetonide` tih te hi a ni. |
| Systemic steroid hmanga siam a ni | Taksa pum huapa hring leh inflammation tihziaawmna turin. Entirnan: `prednisone` tih te hi a ni. |
A tlem hle a, i doctor chuan operation neih a rawt mai thei. Hei hian a hliam chu surgery hmanga lakchhuah a, taksa hmun hrisel dang atanga vun graft hmanga thlak a ni.
Engtikah nge Doctor ka hmuh ang?
I kut zungtang emaw, i ke ruh emaw, i kephah emaw, i kephah emaw, a sen emaw, a sen emaw, a hring emaw, a na emaw i hmuh chuan doctor pan vat vat rawh . I dinhmun chu a hmuchhuak thei ang a, a tul anga enkawlna a tan thei ang.
Doctor i hmuh hunah heng zawhnate hi i zawt thei bawk ang:
- "Doctor, hei hi ka lo neih chhan lian ber chu eng nge ni thei ang?"
- "Ka tan chuan systemic lupus ka vei thei em?"
- "Hetiang hliamte hi a awm loh nan eng nge ka tih ang?"
- "Tuna inhliamte hi engtin nge tih theih ang?"
Chilblain Lupus hi a veng thei ang em?
Hetiang natna i vei theihna tur tihziaawmna tur tha ber chu khawsik laka inven hi a ni . Chutiang ti tur chuan heng thilte hi i zawm thei a ni.
- Exercise neih fo thin ang che:Exercise hian thisen kal a titha a, taksa lum leh vawt a tidanglam bawk.
- I in leh hnathawhna hmun lum takin vawng la: Khaw lum laka inven nan i chhehvel siamrem rawh.
- I kut leh ke tui lumah hnim la: Ni khatah vawi tam tak i tih chuan thisen kal a ti \ha ang.
- Kawng leh ke lumte chu zawi zawiin vawt rawh: Meipuiah khawih nghal mai ang chi thil hi ti suh. Thisen kal dan tur a siam that theih nan zawi zawiin warm up rawh.
- Thawmhnaw lum ha rawh: Khaw lum laiah chuan socks thick, gloves, leh pheikhawk lum ha la.
Vun natna dang ang bawkin Chilblain Lupus hian symptom harsa tak tak a thlen thei a, a chang chuan damdawi dik tak hmuh nan hun rei tak a ngai thin. Mahse, beiseina bansan suh. I rintlak doctor nena thawhhona chuan i tana tha tur solution i hmuh theih nan a pui thei che a ni. Chutih lai chuan, chutiang dinhmun inang nei midangte nena inbiakna neih theihna tur support group-a tel chu ṭanpuina nasa tak a ni thei.
Take-Home Thuchah a ni
- Chilblain Lupus hi vun natna hmuh tur awm lo tak a ni a, vunah hian na tak tak purple/red lesions a awm a, chu chu khawsik vangin a na zual hle.
- I taksa peng hrang hrangah heng symptoms te hi i hmuh chuan a pangngai angin ngaihthah suh la, a rang thei ang bera doctor rawn la.
- Hetiang dinhmun venna leh control nana pawimawh ber chu khawsik laka inven hi a ni.
- Meizial zuk loh vek a pawimawh hle a, meizuk hian thisen kalna a tikhawtlai a, natna lan chhuah dan a ti na zual bawk.
- Hei hi damchhung dinhmun ni mah se, enkawl dan dik leh enkawlna tha tak a awm chuan a natna lanchhuahna te chu a thunun tha thei a, nun pangngaiin a nung thei bawk.











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