I naute hian a thinlungah tumor a nei em? Cardiac Rhabdomyoma chungchang hi i zir dawn teh ang!

Nu emaw, pa emaw i nih angin i fate hriselna i ngaihtuah hian thil tenawm ber pawh hi a lianin i hria a ni lawm ni? A bik takin doctor-in, "I naute thinlungah hian tumor te tak te ang chi a awm," a tih hian thinlung a ti na thei hle. Mahse, lungngai suh . Vawiin hian hetiang hun laia i hriat thin, mahse a tlangpuiin hlauhawm lo tak dinhmun kan sawi dawn a ni. Chu chu Cardiac Rhabdomyoma a ni .

Cardiac Rhabdomyoma tih hi eng nge ni?

A awlsam zawngin, cardiac rhabdomyoma chu cancer nei lo, i naute thinlung ruh- a lo awm , natna ṭha lo tak a ni . Hengte hi a tlem hle. Mahse, mak tak maiin, nausen lai, chu chu naute nu pum chhunga a la awm lai (`gestation`)-a lo awm, heart tumor chi khat, a tam ber an ni. A tam zawkah chuan heng cardiac rhabdomyomas te hi naute chu a pum chhunga a la awm lai emaw, a dam kum khatna emaw chhungin a lo lang thin.

Heng tumor te hi heart muscle atanga lo chhuak a ni. Thil danglam bik chu anmahni chauhva hmuh tur an ni lo va, cluster-a hmuh an ni tlangpui . Hei hi fibromas, tumor chi dang, thinlunga lo awm, hlauhawm lo tak atanga an danglamna chu a ni. A chhan chu fibromas pawh hi heart muscle atang ngeia lo chhuak a ni a, mahse tumor pakhat angin a lo chhuak a, cluster-ah a lo chhuak lo.

A pawimawh ber chu cardiac rhabdomyomas hi malignant emaw cancerous emaw a ni lo . Chumi awmzia chu taksa peng dangah an darh lo tihna a ni. An hlauhawm theihna awmchhun chu i fa thinlung hnathawh dan pangngai tibuaitu a nih chuan a ni. Mahse chu chu a tlem hle. A tam zawkah chuan heng tumor te hi an lo tlem a, anmahni chauhin an bo a , harsatna lian tham an thlen lo.

Heng tumor te hi naupang thinlung dinglam emaw veilam emaw ah a lo awm thei a ni. Thinlung hnuai lam chamber , right ventricle emaw left ventricle emaw ah an awm tam ber . A châng chuan thinlung pindan chung lam, atria , emaw, pindan pahnih inṭhenna bang emaw-ah pawh an lo ṭhang lian thei bawk. Tumor lian leh te hi millimeter tlemte atanga centimetre engemaw zat thlengin a inang lo thei. Mit atang chuan sen emaw, var emaw angin an lang.

Cardiac rhabdomyoma hi natna tha lo, cancer nei lo, heart muscle-a cluster hrang hranga lo awm a ni.

Hetiang hi tuin nge nei tam zawk?

Nausen leh naupang, tuberous sclerosis an tih, genetic condition nei te chu cardiac rhabdomyomas vei theihna a sang hle. Dik tak chuan cardiac rhabdomyomas nei naupang 10 zinga 8 vel pawhin tuberous sclerosis an nei ve bawk. Tuberous sclerosis hi genetic condition a awm lo hle bawk. Entîr nân, United States-a nau piang thar 6,000 zînga 1 vêl chu a vei a ni.

Research-ah chuan mipa leh hmeichhia, hnam emaw, chi emaw hian he natna lo awm dan hi a nghawng tih finfiahna a hmu lo.

Hetiang dinhmun hi engtiang chiahin nge a awm?

Cardiac rhabdomyomas hi nausen leh naupang te zingah heart tumor chi khat a ni ber a . Mahse, a pum puiin, cardiac tumor hi a tlem em em a, cardiac rhabdomyomas hi a tlem hle nia ngaih a ni . Lung chhung ngeia intan tumor (`primary cardiac tumors` tia koh) hian mi 2,000 zinga pakhat aia tlem loin a nghawng a ni.

Engvangin nge cardiac rhabdomyoma hi a lo awm?

Cardiac rhabdomyomas hi nau piang hmaa genetic changes avanga lo awm niin an ngai . Heng genetic changes te hian tuberous sclerosis tih natna a thlen bawk. Tuberous sclerosis vei te hian genes `TSC1` emaw `TSC2` emaw ah mutations an nei thin. Heng gene pahnih hnathawh ber chu taksaa tumor siam dan control hi a ni. Chuvangin, cardiac rhabdomyomas nei naupang tam tak pawh hian tuberous sclerosis an nei ve bawk.

Mahse, naupang thenkhat chuan tuberous sclerosis nei lovin cardiac rhabdomyoma an nei thei a ni. Chutiang hunah chuan he tumor lo awm chhan dik tak hi hmuhchhuah a la ni lo .

Hei hi pian tirh atanga lo chhuak thil a ni em? Hrilhfiahna a ni em?

Cardiac rhabdomyoma hi pianpui atanga lo chhuak a ni tlangpui . Chuvangin pianpui (congenital) anga ngaih a ni. Mahse, chu chu hereditary nen a inang lo . Condition pakhat chu hereditary a nih chuan chhungkaw genes kaltlangin a kai darh thei a ni.

Cardiac rhabdomyoma hi thlahtute atanga lo chhuak a ni thei a, mahse a awm lo. Hei hi a chhan chu he tumor nena inzawm, tuberous sclerosis an tih, genetic condition hi a takin a lo awm fo thin a, hei hi hereditary link a awm lo.

Tuberous sclerosis vei nu leh pa chuan an fate hnena kai theihna chance 50% an nei a ni. Mahse, he "inheritance" hi tuberous sclerosis vei hmun thuma ṭhena hmun khat vel chauhah hmuh a ni. Thil dang tam zawkah chuan naupang hmuhchhuah thar, chhungkaw history nei loah hian a vawi khat nan genetic mutation hi a thleng thin . Hei hian a awmzia chu cardiac rhabdomyoma hi a chang chuan beisei angin a lang thei a, a chang chuan vaukhânna chhinchhiahna awm lovin random occurrence angin a lang thei bawk.

Hei hi thil buaithlak tak angin a lang thei a, mahse, genes hi thawnthua tel ve chauh a ni tih hre reng ang che. Cardiac rhabdomyoma emaw tuberous sclerosis emaw chungchanga zawhna emaw, ngaihtuahna emaw i neih chuan i doctor nen inbiakna neihpui ngei ang che . I chhûngkaw chanchin leh chu chuan nangmah emaw, i fa emaw a nghawng theih dân sawiho rawh.

Hei hi eng symptoms nge ni?

A tam zawkah chuan cardiac rhabdomyoma hian symptom a nei lo.. Mahse, a tlem hle a, tumor emaw, tumor cluster emaw a lian chuan naute thinlung chhungah harsatna a thlen thei a, symptoms a siam thei bawk. Entirnan, tumor lian tak takte hian thisen kal dan a tikhawlo thei a, thinlung rhythm a tibuai thei bawk. Naupai laia hetiang thil hi a thleng a nih chuan nausen tan a pawi hle thei a ni. Heart failure emaw hydrops tih hming pu natna khirh tak a thlen thei bawk .

I doctor chuan naupai laiin heng harsatna chi hrang hrangte hi imaging test hmangin a enfiah fo ang.

Nausen leh naupang tê têa heng tumor te hi anmahni chauhin an bo lo va, an awm reng a nih chuan, a nih loh leh an lo lian a nih chuan heart failure emaw heartbeat mumal lo (arrhythmias) emaw a thlen thei a ni. Hei pawh hi a tlem hle. Mahse i fa doctor chuan he dinhmun hi a enfiah ang a, harsatna a awm em tih a enfiah ang.

I fain a hnuaia symptoms te hi a lantir chuan 1990 ah call nghal la, a nih loh leh damdawi in hnai ber ah hruai rawh:

• Heart rhythm inthlak danglamna.
• Lungphun chak tak ( tachycardia ).
• Thâwk harsa emaw thawk harsa emaw, a bik takin mut lai ( dyspnea ).
• Chest na emaw tightness emaw, thut atanga tihdam theih.
• Khuh.
• Luak chhuak emaw, muhil emaw.
• Chau emaw chak lo emaw tih hriat.
• Ke, ke ruh emaw, pum chhungah emaw a hring chhuak.

Engtin nge hei hi i hriat chian?

Cardiac rhabdomyoma hi imaging test hmanga hriat theih a ni . Heng test te hi naupai lai emaw, naute pian hnuah emaw tih theih a ni.

Cardiac rhabdomyoma hriat theihna tur test neih thin

He tumor hi naupai laiin nau neih hmaa ultrasound scan-ah hmuhchhuah hmasak ber a ni fo thin. He tumor hi naupai kar 20 leh kar 30 inkarah ultrasound hmangin a lang tan thin. Scan bik hmanga hriat theih a ni bawk a , chu chu fetal echocardiogram an ti a ni . Hei pawh hi ultrasound chi khat a ni a, mahse a bik takin nausen pum chhunga nausen a lo thanglian lai hian thinlung lama harsatna awm apiang a zawng chhuak thin.

Naute pian hnua cardiac rhabdomyoma hmuhchhuah leh tehna atana hman test-te chu:

• Electrocardiogram (EKG/ECG) hmanga tih a ni.
• Echocardiogram (echo) tih a ni.
• Magnetic Resonance Imaging (MRI) hmanga tihchhuah a ni.

I fa chu test neih fo a ngai mai thei, chu chu EKG emaw echo emaw a ni thei. Doctor chuan cyst te chu anmahni chauhin an tlahniam em tih a enfiah ang . Cyst eng pawh mahni chauha bo lo chu enkawl a ngai dawn a ni.

Cardiac rhabdomyoma hi tuberous sclerosis tia sawi sual a ni fo.Natna chhinchhiahna hmasa ber a ni thei. Chuvangin, naupang hian taksa peng dangah tuberous sclerosis symptoms a nei em tih hriat nan test dang neih belh a ngai mai thei.

I fa chu tuberous sclerosis a vei tih hmuhchhuah a nih chuan i doctor nen genetic testing chungchang sawipui rawh . A châng chuan nu leh pate chuan he natna hi a na lo hle thei a, an vei tih hriat chhuah an ni ngai lo. Chuvangin, i doctor chuan nangmah emaw, i kawppui emaw hian natna thlentu gene mutation hi in nei em tih a en duh mai thei.

Enkawlnate chu engte nge ni?

Thu lawmawm tak chu cardiac rhabdomyomas hi a lo tlem fo thin a , a bo fo thin avangin enkawl a ngai lo . A tam zawkah chuan heng tumor te hi naute pian tirh lamah chuan a lian ber an thleng tawh a ni. Chumi hnuah chuan tumor te chu anmahni chauhin an tlahniam , harsatna siam lovin.

Mahse, a tlem hle a, heng tumor te hian thinlung hnathawh a tibuai a, enkawl a ngai thin. A chang chuan naupai lai hian hetiang hi a thleng thei bawk. Chutiang hunah chuan nu chuan tumor tihtlem nan damdawi a ei a ngai mai thei.

A chang chuan naute pian hnuah harsatna a awm thei. Cyst emaw cyst cluster emaw chu a mah chauhin a bo lo a nih chuan , a lian zawk a nih chuan naute thinlung hnathawh a tibuai thei a ni. Hei hian heart failure emaw heartbeat mumal lo (arrhythmia) emaw a thlen thei a ni.

Chutiang a nih chuan i fa chuan heng ang damdawi hi a mamawh mai thei:

• Angiotensin tidanglam thei enzyme (ACE) titawp thei a ni
• Diuretics (hei hi taksa atanga tui tam lutuk paih chhuaktu damdawi a ni) .
• Anti-arrhythmic damdawi hman tur a ni

I doctor chuan enkawlna kawng hrang hrang a sawipui ang che a, i fate tana tha ber tur ruahmanna thlang turin a pui ang che. Surgery hi a ngai tlem hle .

Hetiang natna vei te tan hian eng nge an hmalam hun? (Hmuh dan tur) .

Cardiac rhabdomyoma vei tam zawk chuan enkawl an ngai lo . Mahse, natna dang, tuberous sclerosis ang chi an neih chuan an hmalam hun hriselna a nghawng thei a ni.

I fain tuberous sclerosis a vei chuan damdawi lam checkup leh test neih fo a ngai ang . Mi thenkhat tan chuan an natna hi a na lo hle a, hriat lohvin a awm thei bawk. Midang tan chuan harsatna lian tak a thlen thei a, nunphung pawh nasa takin a nghawng thei bawk. I doctor chuan i fate damdawi lam mamawh bik leh prognosis chungchang a sawipui ang che. In pahnih hian in fa enkawl dan tur tha ber ber in siam thei a ni.

Doctor hnenah eng nge ka zawh ang?

I naute dinhmun leh a thlir dan tur chu i doctor nen sawiho rawh. Naupai laiin cardiac rhabdomyoma i vei tih hmuhchhuah a nih chuan khawi atanga tan tur nge tih i hre lo mai thei. I doctor chuan zawhna pawh i zawh hmain thil tam tak a hrilhfiah ngei ang. Mahse, thu belhchian dawl zawk hriat theih nan hetiang zawhna hi zawh hi a \angkai thei ang:

• Engtin nge ka fa rhabdomyoma hi kan enkawl theih ang?
• Ka fa hian damdawi emaw, operation emaw a mamawh ang em?
• Ka fa hian tuberous sclerosis a nei em?
• Tuberous sclerosis hian engtin nge ka fa chu a nghawng ang?
• Tuberous sclerosis a awm leh awm loh genetic test ka nei tur em ni?
• Tuberous sclerosis vei te tanpui thin support group nen min inzawm thei ang em?

I fain damdawi lam natna a nei tih hriat chu nangmah ngeiin i neih ai chuan a hlauhawm zawk thei. Mahse , thu leh hla dik tak i neih chuan i fa chu a dinhmun enkawl tûr leh a dam theih nân i ṭanpui thei a ni . I fain cardiac rhabdomyoma a vei a nih chuan i doctor nen inbia la, a zir belh zel ang che. I doctor chuan "watchful waiting" tih strategy a rawt thei a, chu chu lumps te chu en reng a, anmahni chauha a bo leh bo loh enfiah a ni . Thil tam takah chuan hetiang approach hi a mamawh vek a ni. Amaherawhchu, enkawl ngai a nih chuan i doctor chuan a hriattir ang che.

Thupui tawi (Take-Home Message) 1.1.

Dear Mom and Dad, Cardiac Rhabdomyoma tih hming hi hlauhawm tak angin lang mah se, a tam zawkah chuan benign, non-cancerous tumor a ni tih hre reng ang che . Nauteah a tam hle a, enkawlna engmah awm lovin a mah chauhin a bo fo thin .

A pawimawh ber chu thlamuang taka awm a, damdawi lam thurawn zawm a, i fa dinhmun chungchangah doctor nen inbiak reng hi a ni. Tuberous sclerosis ang chi natna kaihhnawih te chu hre reng la, a tul anga test leh follow-up tihsak rawh.

I fa chu dam thuai turin duhsakna hlanin!

` Cardiac Rhabdomyoma, Cardiac Rhabdomyoma, Lung natna, Nausen Lung Natna, Tuberous Sclerosis, Tuberous Sclerosis, Nausen Lung Natna