I fapa te hian zun a harsat angin i inhriat ngai em ? A nih loh leh a urethra chu a tawi hle a, a dribble ang maiin a hria em? Nu leh pa ṭhenkhat chuan heng thilte hi an ngaihven vak lo mai thei a, mahse hei hi pianpui harsatna, mipa naupangte chauh nghawng thei chhinchhiahna a ni thei. Vawiin hian chutiang dinhmun pakhat, Posterior Urethral Valves (PUV) chungchang kan sawi dawn a ni.
Posterior Urethral Valves (PUV) hi eng nge ni tak tak?
A awlsam zawngin sawi ila, Posterior Urethral Valves (PUV) hi piansualna a ni a, mipa naupang chauh a nghawng a ni. Hetiang a nih chuan thil thleng chu zun phur tube chhungah hian extra membrane ang chi part a lo piang chhuak a (hei hi urethra kan ti a ni). Tui pipe chhunga thil awm ang maiin ngaihtuah rawh. Chutiang chuan zun avang hian membrane chu a luang tha thei lo.
Hemi avang hian eng nge thleng? Naute zun (bladder) chu a hrufai tha lo. Chuvangin he zun khawlkhawm hi hnunglam hawiin a luang lut a , bladder leh kidney te a tichhia tan thin . Hetiang dinhmun hi naute chu a pum chhunga a la awm laiin a thleng thin. Chuvangin, a chang chuan naute pian hma emaw, a pian hnu emaw, naupan lai emaw scan hmangin a hriat theih a ni. Chumi hming dang chu `(Congenital Obstructive Posterior Urethral Membrane - COPUM)` tih a ni.
Hei hi thil awmdan pangngai tak a ni em?
Ni lo, hei hi mi zawng zawng tuar thei natna a ni lo. Mahse he natna, PUV tia koh hi mipa naupangte zun kawng (urinary tract obstruction) thlentu ber a ni.
Hetiang natna lan chhuah dan hi engte nge ni?
Heng symptoms te hi nausen hrang hrangah a inang lo thei. A châng chuan, Doctor-te chuan naute pian hmain nu scan-ah heng symptoms te hi an hmuchhuak ṭhin. Hun dangah chuan naute pian hnuah heng symptoms te hi a lo lang thei bawk.
| Mihring ziarang | A sawifiahna awlsam tak |
|---|---|
| Urine output chak lo emaw dribbly emaw | Naupangin a zun hian , zun chu chak takin a chhuak lo va, a tlem hle a, trickle ang maiin a chhuak zawk a ni. |
| Urinary tract infection (UTI) awm fo thin . | Zun a chhuah that loh avangin bacteria hi awlsam takin a thang lian thei a, natna hrik a thlen thei bawk. |
| Naute rihna tihtlem | Naupangin a thanlenna atana a mamawh ei tur dik tak a dawn loh avangin taksa rihna hi a hniam thei hle. |
| Zun chhuah laiin natna (dysuria) . | I fa chu zun laiin a tap emaw, a nuam lo emaw a nih chuan , natna vang a ni thei. |
| Zun harsatna | Naupangin zun chhuah tumin a strain a ngai a nih chuan chu pawh chu chhinchhiahna a ni. |
| Amniotic fluid hniam `(oligohydramnios)` | Hei hi naute pum chhunga a awm laiin scan an tih laiin hmuh tur a awm. |
| Kal natna (hydronephrosis) . | Doctor-te pawhin naupai laiin scan hmangin an hre thei bawk. |
Engvangin nge hetiang hi a lo awm?
Hei hi a chhan dik tak hi hriat a la ni lo a, mahse a lo awm chhan chu nausen pum chhunga naute lo pian tirh lamah he extra membrane hi urethra-ah a lo awm thin vang a ni tih kan hria.
A pawimawh ber chu hei hi i thil tihsual a ni lo tih hriat reng hi a ni . Hei hi naupang taksa thanlenna kawng khat chauh a ni.
Hei hian eng harsatna nge a thlen theih?
He natna hi a hun taka enkawl a nih loh chuan hriselna lama harsatna lian tak a thlen thei a, a chhan chu zun hnunglam a luang avangin kal a chhe chhunzawm zel a ni.
| Complication awm thei | Chu chu eng nge a awmzia? |
|---|---|
| Kidney-a zun lut kir leh (vesicoureteral reflux/VUR) . | Bladder tikhat zun chu a chho leh a, chu chu kal lam hawiin a kal leh a ni. Hei hian kal (kidney) a tichhia a ni. |
| Bladder empty vek thei lo (urinary retention) . | Bladder-ah hian zun engemaw zat a awm fo thin. Hei hi hri kai thlentu lian tak a ni. |
| Kidney a hring chhuak | Zun pressure vangin kidney a lo hring tan thin. |
| Kidney tha lo a awm | Hei hi natna khirh ber a ni thei. Hun rei tak chhung chu kal (kidney) a chhe thei a, hna a thawk tawh lo thei bawk. |
Doctor-te hian engtin nge hei hi an hmuh?
Doctor chuan naupang chu a enfiah ang a, a tul chuan heng test engemaw zat hi a rawt ang.
| Fiahna | Hei hi engtin nge i tih? |
|---|---|
| Ultrasound scan hmanga kal (kidney) a awm | Hei hian naupang kal (kidney), bladder, leh urinary tract te hmel a en ang a, a tibuaitu a awm leh awm loh a enfiah ang. |
| Voiding Cystourethrogram (VCUG) hmanga tihchhuah a ni. | Hei hi X-ray test bik a ni a, chu chuan bladder a fill leh empty dan dik tak a entir thei a, urethra-a blockage awmna hmun a ni bawk. |
| Cystoscopy hmanga enfiah a ni | Camera te tak te nei tube chu urethra hnuai lamah an pass a, a chhunga blockage awm chu direct-a en a ni. |
| Kidney function test a ni | Thisen leh zun test hian naupang kal (kidney) a thawh that dan a teh thin. |
Hei hi eng enkawlna nge ni?
Hei hi enkawlna ber chu surgery hmanga obstructing membrane lakchhuah a ni. Hei hi ``fulguration'' tih hmanga tih a ni tlangpui.Hei hian electric atanga lumna hmanga extra tissue tihchhiat tihna a ni.
Tin, doctor chuan naupang dinhmun a zirin enkawlna dang a rawt thei bawk.
- Urinary catheterization: Bladder atanga zun chhuahna tur temporary tube (catheter) dah theih a ni.
- Antibiotics: Urinary tract infection i neih chuan a enkawl nan antibiotics pek i ni ang.
- Kal a chhiat chuan: A natna a nasat a, kal a chhiat chuan dialysis emaw, kal thlak emaw pawh a ngai thei.
- Damdawi dang: Zun awlsam zawk nan antispasmodics pawh pek theih a ni bawk.
A tlem hle a, naute chu a pum chhunga a la awm laiin operation tih theih a ni.
Enkawl hnuah eng nge thleng? Eng ang thlirna nge ni ang?
PUV nei naupang chuan a dam chhung zawng damdawi lam enkawlna a mamawh ang a, enkawl a nih hnuah pawh. Thisen test, scan, leh kal hnathawh dan enfiah fo a ngai.
Naupang thenkhat chuan naupan lai emaw, puitling an nih laiin zun insum theih lohna an nei thei bawk. Zirna hrang hrangah chuan he natna vei naupang 15% vel chu kal (kidney failure) vei theihna an nei tih hmuhchhuah a ni. Mahse, a flip side chu naupang 100 zinga 85 chuan he natna khirh tak hi an nei lo . Chuvangin, a hmaa hriat chian a, uluk taka enkawl a, doctor nena inbiak reng a pawimawh hle.
Engtikah nge Doctor ka hmuh ang?
Kan sawi tawh ang khan i fa hian symptoms a nei nia i rinhlelh chuan tihkhawtlai suh.I fa chu a rang thei ang bera doctor hnenah hruai rawh. Enkawl loh chuan hei hian hriselna lama harsatna lian tak a thlen thei a ni.
Doctor hnenah eng zawhna nge i zawh tur?
Doctor hmu tura i kal hunah heng zawhnate hi zawh a \angkai hle ang.
- Hei hi enkawl dan tur engte nge ni?
- Engtin chiah nge he enkawlna hi tih a nih?
- Enkawlna hnua dam leh hun chhung hian eng nge i beisei tur?
- Chumi chhung chuan engtin nge naupang chu ka enkawl ang?
- Engtikah nge doctor rawn hmuh leh tur?
I naute hian hetiang hriselna lama harsatna a nei tih i hriat chuan hlauhna i neih hi thil pangngai a ni. Mahse a pawimawh ber chu hei hi i sualna a ni lo tih hriatthiam hi a ni. I doctor leh healthcare team te chuan i kalna apiangah an pui ang che. Chuvangin hlau suh. I doctor thupek dik takin zawm la, zawhna i neih apiang zawt rawh.
Take-Home Thuchah a ni
- Posterior Urethral Valves (PUV) hi piansualna a ni a, mipa naupang chauh a nghawng a, zun kalna tur a tikhawlo a ni.
- Urinary tract chak lo, urinary tract infection awm fo te, naupang taksa rihna tlahniam te hi a natna lanchhuahna ber a ni thei.
- He natna hi naute pian hmain scan hmangin pawh hriat theih a ni.
- Enkawlna ber chu operation hmanga urethra-a blockage awm chu paih chhuah a ni.
- Inenkawl hnuah pawh nausen kal (kidney) hriselna humhalh nan dam chhung damdawi lam enkawl hi a pawimawh hle.
- Hei hi nu leh pa sualna a ni lo tih hi hriatthiam a pawimawh.











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