Kidney stone hi min ti hlauhawm deuh vek a ni lawm ni? Chu hrehawmna chu i hre tawh ngei ang. Mahse, kal (kidney stone) hi chi hrang hrang a awm tih i hria em? Vawiin hian lung chi khat hmuh tur awm lo mahse pawimawh tak kan sawi dawn a ni. Chu chu cystine lung a ni. Engvangin nge an lo insiam tih te, an natna lan chhuah dan te, eng nge tih theih tih te i lo en ang u.
A awlsam zawngin, cystine lung hi eng nge ni?
Cystine Stones hi kal (kidney stone) chi khat a ni bawk. Kidney stone hi kan zun chhunga chemical chi hrang hrang awmkhawm atanga siam, lung ang maia khauh tak a ni. Cystine lung hi chemical pakhat cystine an tih atanga siam a ni a . Cystine hi kan taksa tana amino acid pawimawh tak a ni. A dik tak chuan kan taksaa taksa ruh siamna leh tissue siamthatna atana puitu proteins zinga a tlem ber a ni.
A tlangpuiin kan kal (kidney) hian he cystine hi taksaah a la lut leh thin. Mahse mi thenkhatah chuan he kalphung hi a thawk tha lo hle. Tichuan, cystine hip theih loh chu zun-ah a pung khawm a, hun kal zelah lung a siam ta a ni. Heng cystine lungte hi kal lung dang aiin a lian deuh thei a ni. Chuvangin a chang chuan kal emaw zun kawng emaw chhiatna tihtawp nan operation hmanga lakchhuah a ngai thin.
Chuti a nih chuan Cystinuria chu eng nge ni?
Heng cystine lungte lo awm chhan ber chu genetic condition cystinuria an tih a ni . Hei hi thil awm lo tak, thlahtute atanga lo chhuak a ni. A awlsam zawngin, he natna hi i neih chuan i taksa hian cystine an tih chemical chu a tifai tha thei lo. Chuvangin i zun ah a lo pungkhawm a, lung a siam thin.
A pawimawh ber chu cystinuria hi dam chhung zawnga natna a ni. Damdawi a awm lo. Mahse , enkawlna dik tak i neih chuan, i dinhmun chu i enkawl ṭha thei a, nun pangngaiin i nung thei bawk .
Hei hi genetic condition a nih avângin, naupangin a neih theih nân a nu leh pa aṭangin gene chu a rochun a ngai a ni . Hetiang natna vei hian a dam chhungin vawi tam tak cystine stone a nei thei a ni.
Hetiang dinhmun hi engtiang chiahin nge a awm? Eng nge a lan chhuah dan?
Hei hi mi zawng zawng chunga thleng tur a ni lo va, a tlem deuh hlek a ni. A tlangpuiin kidney stone nei mi 100 zinga 1 emaw 2 emaw i ei chuan pakhat emaw pahnih emaw chauhvin cystine stone an nei ang. Mahse mak tak maiin, he dinhmun hi naupang leh puitling tleirawlte zingah hmuh tur a tam zawk . Cystine lung nei zinga 80% vel chuan kum 20 an tlin hmain lung hmasa ber an nei a, mahse heng lungte hi kum eng pawhah a lo awm thei a ni.
A natna lan chhuah dan erawh chu kal lung dang nen an inang hle. Lung a lo awm hma chuan symptoms hi hriat a ni lo tlangpui.
| Symptom a ni | Hrilhfiahna |
|---|---|
| Hnunglam emaw, pelvis emaw ah natna nasa tak a awm | Stabbing pain na tak ang maiin a lang thei. Hei hi a sir khatah hriat a ni tlangpui. |
| Pum hnuai lam emaw, kawr hnuai lam emaw a na | Lung chu zun kawng hnuai lam a pan chuan pum hnuai lam ah natna a awm thei. |
| Thisen chu zun chhungah a awm | Zun chu pink, red, brown emaw a ni thei. |
| Luak chhuak leh luak chhuak | Nausea leh vomiting hi natna nasa tak nen a awm thei bawk. |
| Zun laiin natna | Lung chu bladder hnaihah a awm chuan zun laiin kang emaw, na emaw i nei thei. |
A châng chuan, heng cystine lungte hi a lian tawk a, zun kawng a tikhawlo thei a, zun kawng infection (UTI) a thlen thei bawk .
Eng harsatna nge thleng thei?
Cystinuria hi dam chhung zawnga natna a ni a, uluk taka enkawl loh chuan harsatna a thlen thei a ni. Hetiang dinhmun hi enkawl turin doctor nen thawhhona tha tak neih a pawimawh.
Harsatna awm thei te chu:
- Kidney infection: Lung hian zun kalna a tikhawlo thei a, kal chhungah natna hrik a lut thei bawk.
- Ureteral obstruction: Kidney atanga bladder (ureter) thlenga zun phurtu tube chu lungin a block thei.
- Urinary tract infection (UTI) awm fo thin.
- Kidney chhiatna awm reng:Hun rei tak enkawl loh chuan kal hnathawh a tlahniam thei.
Engtin nge doctor hian hei hi a hriat chian? Enkawlnate chu engte nge ni?
Kidney stone ang chi symptom i neih chuan i doctor chuan test eng emaw zat a nei ang a, hengte hi cystine stone a ni em tih a hriat theih ang.
Diagnostic dan hrang hrang
- A chipchiar zawka zawh che: Doctor chuan i natna lan chhuah dan leh i chhungte zingah hetiang harsatna nei an awm leh awm loh a zawt ang.
- Test: Zun test leh imaging test, ultrasound scan emaw CT scan emaw tih tur a ni.
- Lung test dan: I zun atanga lung lo chhuak i neih chuan lab-ah test turin thawn theih a ni a, chu chu eng lung chi nge a nih chiah tih hriat theih a ni. Hei hi cystine stone a nihzia 100% a finfiah theihna awmchhun a ni.
Enkawl dan tur
Cystine lung enkawl tum ber chu lung thar lo piang tur venna leh lung awmsa tihbo hi a ni. I doctor chuan i tana tha tur treatment plan a siam ang.
- Nunphung leh ei leh in lama inthlak danglamna
- Tui in tam: Hei hi a pawimawh ber a ni. I doctor chuan ni khatah tui litre 3-4 tal in turin a ti thei che a ni. Chumi awmzia chu darkar tin tui glass khat in hi tih danah i siam tur a ni. Zanah tui in tura i tho chuan mak ti suh. Tui hian i zun a ti tithianghlim a, cystine a pungkhawm pawh a ti tlem bawk.
- Salt (sodium) control: I chaw eiah chi i dah zat tihtlem. Canned food leh frozen emaw packaged foods ang chi ei tur, chi tamna ei loh tur.
- Rannung protein tihtlem: Sa, sangha, leh artui ang chi rannung protein i ei tlem thei a, chu ai chuan thlai atanga siam protein i ngaihtuah zawk thei bawk.
- Damdawi chi hrang hrang
Lung avanga natna i neih chuan i doctor chuan natna tidamtu damdawi a pe ang che. Hei bakah hian damdawi bik a awm a, chu chuan cystine lung thar a lo awm loh nan a pui thei a ni. Tiopronin leh d-penicillamine te hi chutiang damdawi chu a ni. Hengte hian cystine chu a tithianghlim thei a ni. Heng damdawi te hi damdawi lam enkawlna hnuaiah chauh ei tur a ni .
- Inzai
Lungte hi a lian hle a, zun kawng a tikhawlo a, a na lutuk a nih chuan surgery hmanga lakchhuah a ngai mai thei.
- Ureteroscopy: Camera te tak te, flexible tak mai chu urethra hnuaiah an pass a, chu chu lung awmna hmun zawn chhuah a ni a, a then a then emaw, a paih vek emaw a ni.
- Percutaneous Nephrolithotomy hmanga tihchhuah a ni:A hnungzang vunah hian incision te tak te siam a, chuta tang chuan tube hmangin kidney chhungah lut a, lung chu lakchhuah a ni. Hei hi lung lian tak tak tan chuan tih a ni tlangpui.
Hetiang dinhmun hi engtin nge i nunpui? Hlauh tur thil a ni em?
Cystinuria hi dam chhung zawnga natna a ni. Mahse, uluk taka enkawl a nih chuan ngaihtuahawm tur a awm lo. He dinhmun hi nunna atana hlauhawm a ni tlem hle. Enkawl that a nih chuan kal (kidney failure) ang chi natna khirh takah a kal tam lo hle.
A pawimawh ber chu i doctor nen inlaichinna tha tak neih reng hi a ni. Thupek dik taka zawm a, a hun taka clinic-a kal chuan he natna hi i control tha zawk thei ang.
Enkawlna hlawhtlinna enfiah turin doctor chuan zun test a nei fo ang a, zun chhunga cystine awm zat a enfiah ang. A tul chuan enkawl dan tur ruahmanna chu a tul angin siamrem a ni ang. Hei hi genetic condition a nih avangin chhungkaw din i tum a nih chuan genetic counseling lak pawh a tha mai thei.
Take-Home Thuchah a ni
- Cystine stone hi kidney stone chi khat a ni a, chu chu thil awm lo, genetic condition cystinuria an tih avanga lo awm a ni.
- He natna hi dam chhung zawng ni mahse, enkawl dan dik leh nunphung thlak danglam chuan a enkawl tha hle.
- Nilengin tui tam tak in hi lung siam loh nan a pawimawh ber leh awlsam ber a ni.
- Chi leh rannung protein tlemna ei leh in zawm a pawimawh hle.
- I hnungzang, i pelvis, emaw i pum hnuai lam natna nasa tak, i zun-a thisen awm ang chi symptoms i neih chuan hun khawhral suh la, doctor pan nghal rawh
- I doctor thupek leh damdawi te dik takin zawm rawh. Lungngai suh, he natna nen hian nun hrisel takin i hmang thei ang.











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