I naute thluak hmasawnna tur ngaihtuah em? Dandy-Walker Syndrome chungchang hi han sawi ila

I fate lu chu a lian deuh niin a lang em? A nih loh leh an kum atana thil tih tur chu i tlai lutuk niin i hria em? A chang chuan hetiang thil i hmuh hian hlauhna tlem a neih hi thil pangngai a ni. Vawiin hian nu leh pa tan lu na deuh thei, mahse i hriat chuan enkawl theih tur dinhmun kan sawi dawn a ni. Chu chu Dandy-Walker Syndrome a ni. Ngaihtuah buai suh, chipchiar leh awlsam takin kan sawi dawn a ni.

Dandy-Walker Syndrome hi eng nge ni?

A awlsam zawngin, Dandy-Walker Syndrome hi naute pian tirh atanga an thluak lo thanglian dan inthlak danglam a nih chuan a lo awm thin a ni . Hei hi Dandy-Walker Malformation an ti \hin. Hei hi naute pum chhunga a la awm lai, thluak a lo thanlen lai hian a thleng thin. Hei hian pianpui (congenital condition) a ni tihna a ni.

Hei hian kan thluak hnung lama awm thluak te tak te, thluak bul , leh a chhehvel hmun (space)-a awm cerebellum a nghawng ber a ni. He cerebellum an tih hi kan Central Nervous System a pawimawh ber a ni tih i hria em . Kan taksa chetna inrualremtu a ni. Chu mai ni lovin thil dang tam takah a pui bawk. En teh:

• Kan taksa balance , coordination, leh posture te a control a ni.
• Vision- related thilah pawh a pui bawk.
• Kan ngaihtuahna (cognition) hi thil hriatthiam leh hriatrengna ang chi thil nen pawh a inzawm tlat a ni.
• Motor skills hi taksa peng hrang hrang manipulate ang chi thil a ni.
• Nungchang thununnaah pawh a pui bawk.

Hei hi kum 1900 chhoa he dinhmun sawitu neurosurgeon pahnih , Walter Dandy, MD, leh Arthur Walker, MD te chawimawina atan Dandy-Walker tia koh a ni.

Dandy-Walker nei mi pakhat thluak chu eng nge thleng?

Okay, chuti a nih chuan Dandy-Walker nei mi pakhat thluak hi engtin nge a awm? Thil thleng thei thenkhat chu hetiang hi a ni:

• Thluak ventricle palina chu a lian chho zel a. Hei hi cerebellum chhehvel hmun a ni. Hei hian thluak chunglam leh hnuai lam leh ruhro inkar ah cerebrospinal fluid (CSF) a kal theih nan a pui a ni .
• Cerebellum hemisphere pahnih, chu chu a sir pahnih inzawmkhawmna lai tak chu cerebellar vermis , an ti a, a bo vek emaw, a then emaw pawh a awm thei.
• Cyst , tui bubble ang maia lang chu ventricle palina bulah a lo awm a.
• Luruh bul, chu chu hnunglam fossa chu a lian ta hle a ni.
• A chang chuan cerebrospinal fluid (CSF) a lo pungkhawm thei a, luruh chhungah pressure a tisang a, a ti hring thei bawk. Hei hi hydrocephalus kan tih chu a ni .

Dandy-Walker Syndrome hi engtiang chiahin nge a awm?

United States atanga data atanga a lan dan chuan Dandy-Walker Malformation hian naute 25,000 atanga 35,000 zinga pakhat vel a vei a ni . Mipa aiin hmeichhiaah a tam zawk .

Dandy-Walker Syndrome hi eng thilin nge a thlen?

Hetiang dinhmun hi nausen pum chhunga thluak (cerebellum) lo piang chhuak chungchangah harsatna a awm chuan a lo awm thin . Thil engemaw takah chuan he dinhmun hi genetic mutation vang a ni thei .

Dandy-Walker vei thenkhat chuan chromosomal condition an nei thei . Chumi awmzia chu chromosome thenkhat chu a bo emaw, a tam emaw a ni tihna a ni. I hria em, chromosomes hi kan genes kengtu package ang mai a ni. Dandy-Walker Syndrome hi nau piangsual dang engemaw zat nena lo awm thin, genetic disorder pakhatah pawh a tel thei bawk.

A chhan dang engemaw zat a awm thei bawk:

• Virus chi thenkhat chu naupai laiin nu atanga naute hnenah a kai thei a .
• Naupai laiin toxin emaw damdawi emaw thenkhat nena inzawmna .
• Ka nu hian zunthlum a nei a .

Dandy-Walker symptoms hi engtikah nge a intan?

A châng chuan, symptoms chu rang tak leh chiang takin a lang . A châng dangah chuan nu leh pate chuan thil dik lo a awm tih hre lovin symptoms an nei thei bawk.

A tam zawkah chuan naute dam chhung thla engemaw zat chhungin natna lan chhuah dan a lang thin a, mahse naupang thenkhat chu kum 3 emaw kum 4 emaw an tlin hma loh chuan hmuhchhuah theih a ni lo.

Dandy-Walker Syndrome natna lan chhuah dan chu engte nge ni?

Nausen a symptom hmuh theih te chu:

• Hmasawnna tihkhawtlai chu kum nena inmil hmasawnna atana thil pawimawh tihhlawhtlinna tihkhawtlai a ni . Entîr nân, ṭhut, hrual, leh kal hun sawn hlat.
• Luruh hi a pangngai aia lian a ni.
• Hypotonia , chu chu taksa chu a limp mai tihna a ni.
• Spasticity tih awmzia chu taksa ruhte chu a nghet a, ben harsa a ni tihna a ni.

Naupang kum upa zawka natna lan chhuah dan:

• Vomiting, seizures, leh irritability – hengte hi thluak chhunga pressure sang zawk chhinchhiahna a ni.
• Coordination hloh, kea kal dan (wobbly gait), leh mit tichhe ang chi chetna danglam tak tak – hengte hi cerebellum-a harsatna awm chhinchhiahna a ni.

Symptom dang engemaw zat a awm thei bawk:

• Luruh hnung lama hring emaw, lump emaw a awm .
• Kawng, hmai leh mit thununtu nerve-te harsatna .
• Thâwk lak dan dik lo .
• Seizures a awm thin .
• Thinlung lama harsatna nei te .
• Hydrocephalus natna lan chhuah dan .

Dandy-Walker Complex leh Dandy-Walker Syndrome hi eng nge an danglamna?

Hei hi a buaithlak deuhin a lang thei a, mahse ka sawi awlsam ang. Dandy-Walker Complex hi natna chi hrang hrang, a lan chhuah dan inang chiah chiah a ni. Dandy-Walker Syndrome hi chutiang natna zinga pakhat chauh a ni.

Dandy-Walker Complex-a tel condition dang pawh a awm bawk:

• Isolated Cerebellar Vermis Hypoplasia emaw Dandy-Walker Variant : Hetiang dinhmunah hian cerebellar vermis hi a te emaw, a lo thang kim lo emaw a ni. Mahse, Dandy-Walker Syndrome vei naupang thluaka structural change dangte chu hmuh tur a awm lo. Hetiang natna vei nia hriat naupang tam zawk hi chu a pangngaiin an lo thanglian thin.
• Mega Cisterna Magna : Hetiang dinhmunah hian luruh hnung lama posterior fossa chu a lian a, mahse cerebellum erawh a normal thung. Mega Cisterna Magna hian hriselna lamah harsatna a thlen lo tlangpui.
• Posterior Fossa Arachnoid Cyst : Hei hi hnunglam fossa-a lo awm thin a ni. Hetiang cyst hi nei mahse naupangte hian symptom an nei hi a tlem hle.

Dandy-Walker Syndrome nen hian eng natna dang nge inzawm?

Dandy-Walker vei naupangte hian central nervous system hmun dangah pawh harsatna an nei thei bawk. Entir nan:

• Corpus Callosum (ACC) awm lohna hi a awm lo va, pianpui atanga lo chhuak a ni.
• Ke leh ke, hmai, thinlung, kut zungtang ang chi thil siam danah harsatna a awm.

Ka fa hian rilru lama harsatna a nei dawn em ni?

Dandy-Walker vei naupang zinga a chanve aia tlem lo chu rilru lama harsatna nei an ni . Intellectual disability hi Dandy-Walker vei naupang, a hnuaia natna nei te zingah a tam ber a ni:

• Hydrocephalus na tak a awm .
• Chromosomal dinhmun .
• Pianpui natna dangte .

Naupang tin hi an danglam vek a, chuvangin naupang pakhatin a tawn dan chu a dang tawn nen a inang lovang tih hre reng ang che.

Engtin nge Dandy-Walker Syndrome hi hmuhchhuah a nih?

A châng chuan doctor emaw, nu leh pate emaw chuan naupang lu a lian lutuk tih an hmu thei . A nih loh leh naupangin hmasawnna tur thil a tlin lo tih an hmu thei bawk . Doctor-te chuan Dandy-Walker-a natna hriat theih nan thluak imaging test neih tir an ti thei a ni. Heng test-ah hian:

• Ultrasound hmanga enfiah a ni.
• CT scan a ni.
• MRI scan a ni.

A chang chuan naute pian hmaa prenatal ultrasound emaw fetal MRI scan emaw hmangin he natna hi hriat theih a ni.

Ka fa hian Dandy-Walker a nei a nih chuan chhungkua hian genetic testing neih a ngai em?

I fain Dandy-Walker Malformation a neih chuan i doctor nen genetic counseling chungchang sawipui a pawimawh hle . Hetiang natna vei zinga za zela tlemte hian chhungte pawhin he natna hi an nei thei bawk. A chhungah hian genetic component a awm thei avângin, doctor tam tak chuan genetic test neih an rawt a ni .

Dandy-Walker Syndrome hi eng enkawlna nge ni?

Enkawlna chu Dandy-Walker Syndrome natna lan chhuah danah a innghat a ni. Enkawl tan hmain doctor-in uluk taka enfiah hmasak phawt a pawimawh. Entîr nân, doctor-te chuan a hnuaia mite hi an rawt thei a ni:

• Ventriculoperitoneal (VP) Shunt : Surgeon-te chuan thluaka tui tam lutuk paih chhuah nan hmanraw te tak te VP shunt an tih chu an dah lut a. He shunt hian thluaka pressure a tihziaawm bakah symptoms a ti tha thei bawk.
• Damdawi : I fa doctor chuan seizures control nan damdawi a pe thei ang.
• Therapy : Physical therapy leh occupational therapy hian naupangte chu taksa chakna (muscle strength) vawng reng turin a pui thin. Therapist-te pawhin naupangte chu nitin hna thawh dan thar an zirtir thei bawk. Speech therapy hian tawng leh thusawi tihhmasawn nan a pui a ni.
• Special Education : Zirna hmun remchang siam hian naupangte chu an zirna leh khawtlang thil tumte tihlawhtling turin a pui thin.

Dandy-Walker Syndrome vei naupangte hmalam hun chu eng nge ni?

I fa hmalam hun leh dam rei zawng chu a dinhmun a zirin a innghat a ni.It depends on how severe it is , leh naupangin a neih theih tur congenital condition dang a awm chuan.

Hetiang natna vei te hian thil tawn hrang hrang an nei thei a ni. Ṭhenkhat chuan symptoms na lo tak tak an nei bawk . Mi dangte chuan rualbanlo thuk tak an nei bawk . Naupang thenkhat chuan enkawlna tur ruahmanna fel tak siamin hriatna (cognitive abilities) pangngai an nei thei a ni. Mi dangte tan chuan an medical team-in an natna chu rang taka hmuchhuakin enkawl mah se, chutiang level chu an thleng thei lo mai thei.

Dandy-Walker Syndrome hi a veng thei ang em?

Dandy-Walker Syndrome ven dan tur hriat a la ni lo . Mahse, nau neih hmaa enkawlna mumal tak hian naupai hrisel tak neih theihna hun tha ber a pe che a ni. Naupai laia hrisel taka awm turin doctor thurawn zawm rawh.

Dandy-Walker hmang hian engtin nge ka fa hi ka enkawl ang?

A hmaa inrawlh hian i fa chu enkawlna hlawhtling tak neih theihna hun tha ber a pe thei a ni. I fain a hun taka thut, kea kal, emaw, inbiakna emaw ang chi hmasawnna atana thil pawimawh tak takte a tlin loh tih i hriat chuan i doctor hmu rawh. Chumi hnuah chuan diagnosis dik tak an siam thei a, i fa tan enkawlna ruahmanna tha ber an pe thei bawk.

I fate Dandy-Walker enkawltu team-ah hian:

• Naupang enkawltu doctor .
• Hmasawnna lama mithiamte .
• Thusawi, Hnathawh leh Taksa lam Therapist te .
• Zirna bik lama mithiamte .

Dandy-Walker Syndrome chungchangah hian ka doctor hnenah eng nge ka zawh ang?

I fa chu Dandy-Walker vei nia hriat a nih chuan i doctor hnenah a hnuaia mite hi zawt la:

• Ka fa hian shunt a mamawh dawn em ni ?
• Ka fa hian eng damdawi lam natna dang nge a neih?
• Ka fa hmalam hun (outlook) chu eng ang nge ni ang?
• Engtin nge ka fa symptoms hi kan tihchangtlun theih ang ?
• Genetic testing kan ti tur em ni ?

A tawp berah chuan hei hi hre reng ang che.

Dandy-Walker Syndrome, Dandy-Walker Malformation tia hriat bawk hi thluak natna, naute pian hmaa lo awm thin a ni. Dandy-Walker vei naute hian an hmasawnna tur milestone an thleng tlai fo thin. Naupang thenkhat chuan thluak atanga tui tam lutuk lakchhuah nan shunt an mamawh thin. Enkawlna hian naupangte chu nitin hnathawh dan tur a enkawl thei a, sikul hlawhtling turin a pui thei a, nun hlimawm tak nei turin a pui thei bawk. I fate lu a lian lutuk emaw, beisei angin an ṭhut loh emaw, an kal lo emaw, an inbia lo emaw tih i hriat chuan i doctor nen inbia ang che. Hriat hmasak leh enkawl dan dik a pawimawh. Ngaihtuah buai suh, he natna hi damdawi lam thurawn hmanga enkawl theih a ni.

` Dandy-Walker Syndrome, Thluak chhiatna, Nau piangsual, Cerebellum, Hydrocephalus, Hmasawnna tlai, Naupang hriselna