I taksa hmun dangah lump emaw, swelling emaw danglam tak i hmu a, i lungngai tawh em? A châng chuan heng thilte hi chutiang chuan a hlauhawm lo mai thei. Amaherawhchu, vawiinah hian tumor chi khat, tlem a danglam bik leh ngaihven bik tlak tak chungchang kan sawi dawn a ni. Chungte chu desmoid tumor an ti a. Eng nge an nih, engvangin nge an siam, engtin nge an hriat theih ang, engtin nge an enkawl ang tih hi han thlir ila.
Desmoid Tumors hi eng nge ni? A awlsam zawngin i zawng chhuak ang u!
A awlsam zawngin, desmoid tumor hi cancer a ni lo . Mahse aggressive fibromatosis an ti bawk. Chumi awmzia chu a chang chuan rang tak leh nasa takin an thang thei tihna a ni. Kan taksa chhunga connective tissue -ah an lo piang a ni. Kan taksa peng hrang hrang inzawmkhawmtu glue angin han ngaihtuah teh.
Heng tumor te hi taksa khawi hmunah pawh lo awm thei mahse, pum, kut, ke, leh a chang chuan lu leh kawr ah te hmuh tur a tam ber a ni .
A pawimawh ber chu heng tumor te hi cancer angin taksa hmun khat atanga hmun dangah an darh lo (an metastasize lo) tih hi a ni.
Mahse, buaina pakhat a awm. Heng tumor te hi a lo thang zawi zawi fo thin . Mahse, thenkhat chu an thang chak hle a, a bul hnaia tissue (locally infiltrative)-ah an darh thei bawk. Chutiang a nih chuan operation hmanga lakchhuah a harsa hle. Thil dang pakhat chu enkawl hnuah pawh an lo let leh (recur) duh zawk a ni. Mahse mi zawng zawng dinhmun a inang vek lo va, chu chu hriat reng a pawimawh.
Heng nut chi hrang hrang hi a awm em?
Ni e, desmoid tumor hi chi hrang hrangah then theih a ni a, an awmna hmun a zirin:
- Abdominal wall desmoid tumors: Hengte hi kan pum chhunga taksa peng hrang hrang (riltam ang chi) hualtu tissue wall (abdominal wall)-ah a lo piang chhuak thin.
- Intra-abdominal desmoid tumors: Hengte hi intestines vel tissue lining (mesentery) ah a lo awm thin.
- Extra-abdominal desmoid tumors: Hengte hi pum pawn leh pum chhung bang pawnah a lo awm thin. An bul tan ber chu kekawrte, kut chunglam, rilru bang leh ke chunglam atanga tan a ni. Lu leh kawr ah pawh an lo thang lian thei bawk.
Eng nge a lan chhuah dan? Engtin nge kan neih leh neih loh kan hriat theih ang?
Desmoid tumor hian symptom lian tham a thlen ngai lo. Mahse, natna lan chhuahna chu tumor chu a lian tawk a, a bul hnaia nerve emaw, taksa peng emaw a press thei chauhvin a lang thin. Chûng zîngah chuan:
- Lump emaw swelling emaw: Hei hi kut, ke emaw, pum emaw-ah hmuh tur a tam ber.
- Nausea leh vomiting: Heng symptoms te hi pum chhungah tumor a awm chuan a awm thei.
- Natna emaw, rilru hahna emaw: Hei hi tumor-in tumor bula nerve, organ emaw thisen kalna kawng a press hian hriat theih a ni.
- Kut emaw, ke emaw pawh sawn a harsa khawp mai.
Pawimawh: Taksa chunga lump lo awm zawng zawng hi desmoid tumor a ni vek lo. Mahse, inches hnih (centimetre 5 vel) aia lian, a lo thang chhunzawm zel, emaw, a na emaw i neih chuan doctor pan a, thurawn dil a tha ber.
Engvangin nge heng desmoid tumor te hi an lo awm? A chhante chu engte nge ni?
Heng tumor te hi connective tissue-a cell-te’n mutation an neih a, rang tak leh thunun theih loha an inthen tan chuan a lo awm thin. Hun a kal zel a, heng cell tam lutuk te hi an pungkhawm a, tumor an siam thin.
Doctor-te chuan a tir atanga heng cell te hi engvangin nge an inthlak tih chiang takin an la hre lo. Mahse, zirchiannaah chuan desmoid tumor nena inzawm gene mutations engemaw zat hmuhchhuah a ni. He information hian chutiang mutations target tur leh tumor te thanlenna control thei tur treatment siamnaah a pui thei ang.
Hengte hi tuin nge nei tam zawk? (Risk Factor hrang hrang) 1.1.
Mi thenkhat chuan desmoid tumor an nei tam zawk. Tute nge an nih hi han thlir ila:
- Kum naupang: He natna hi kum 30 leh 40 inkar te zingah a awm tam ber.
- Hmeichhia nih: Hmeichhia hian heng tumor te hi an nei tam zawk a, a bik takin naupai lai emaw, nau neih hnu rei vak lovah emaw hian an nei tam zawk. Pum bangah an lang fo thin. Naupai laiin estrogen level a san avangin mithiam thenkhat chuan estrogen leh desmoid tumor te hi inzawmna a awm niin an ngai.
- Familial Adenomatous Polyposis (FAP) tih natna nei: Hei hi rochun natna a ni. FAP vei zinga 5% leh 10% inkar chuan desmoid tumor an nei thin. A tam zawkah chuan heng tumor te hi a hmaa operation an neihna hmunah an lo awm a, chu chu colon-a a lo thang lian lo (colon polyp) te chu paih chhuah a ni.
- Trauma: Research atanga a lan dan chuan hliam na tak, emaw hmun khata hliam na tak (entir nan, infiamna khelh laiin hmun khata hliam nawn leh) hian desmoid tumor a vei theihna a tipung a ni.
Engtin nge doctor-te hian hei hi an hriat chian? (Diagnosis) tih a ni.
Heng symptoms te hi i neih chuan i doctor chuan physical exam a ti hmasa ang a, i symptoms te chu a zawt hmasa ang. Tichuan, a hnuaia test te hi an ti thei ang:
- Imaging test: A tam ber chu CT scan leh MRI a ni. Hengte hian taksa chhunga tumor awm chu chiang takin a hmu thei a ni.
- Biopsy: Hei hi test tih tur pawimawh ber a ni . Hei hian tumor atanga tissue te tak te lak a, microscope hmanga cell te enfiah a huam a ni. Hei chauh hi eng tumor chi nge tih chiang taka hriat theihna a ni.
I doctor-in FAP i neih a rinhlelh chuan test dang an ti leh thei bawk. Desmoid cyst nei zawng zawng hian FAP an nei vek lo. Mahse, i neih leh neih loh hriat a pawimawh a, a chhan chu FAP vei te hian colon cancer an vei theihna a sang zawk a ni.
Engtin nge enkawl ang? (Tihdamna)
Desmoid tumor hi cancer tumor ang bawkin enkawl a ni fo. Chumi awmzia chu specialty hrang hranga doctor team, oncologist pawh tiamin i thawk dun mai thei tihna a ni.
Tun hma chuan heng tumor te hi surgery hi a enkawl ber a ni. Mahse, heng tumor te hi operation hnuah lo kir leh theihna chance sang tak an nei tih hmuhchhuah a nih avangin tuna enkawlna hi damdawi hmanga enkawl a ni ber. Enkawlna dangte chu:
- Active surveillance (or watchful waiting): I tumor chu zawi zawiin a lo thang lian a, symptom lian tham a neih loh chuan i doctor chuan a enkawl reng ang che. Regular scan an ti dawn a ni. I dinhmun a danglam chuan a rang thei ang bera enkawl tan theih a ni.
- Surgery: Tumor hi a lo thang chak em em emaw, symptom na tak a awm emaw a nih chuan surgery neih a ngai mai thei. A nih loh leh, tumor hian harsatna lian tak, bowel obstruction ang chi a thlen theihna tur a nih chuan operation pawh tih theih a ni.
- Targeted therapy: Heng damdawi te hian desmoid tumor tihpunna tura puitu genes emaw proteins bik target-in hna an thawk a ni. I doctor chuan damdawi chi khat Tyrosine Kinase Inhibitor (TKI) tih a rawn rawt thei ang.
- Cryoablation: Hei hi surgery ai chuan a danglamna dang a ni. Tumor tihchhiat nan extreme cold a hmang thin. He enkawlna hi pum pawn lama awm desmoid tumor te tak te (entir nan, kut leh ke-a awm) tan pawh hman theih a ni.
- Chemotherapy: Heng damdawi te hi desmoid tumor te tihtlem emaw, tihbo vek emaw nan an hmang thin. Mahse, he enkawlna hlawhtlinna chungchangah hian ngaihdan hrang hrang a awm.
- Hormone therapy: Tamoxifen ang chi hormone damdawi te hian desmoid tumor te hi a tipung thei lo.
- Radiation therapy: Radiation hmang hian tumor chu a ti tlem emaw, a tichhia emaw a ni thei. Amah chauh emaw, enkawlna dang nena hman dun emaw a ni.
Doctor hmuh fo a ngai em? (Chhunzawmna)
Ni e, a dik ngei ang. Enkawlna i neih zawh hnuah pawh i doctor pan fo a ngai dawn a, a chhan chu desmoid tumor a lo awm leh theihna chance a sang hle.A tlangpuiin kum thum hmasa berah thla ruk danah test leh scan i neih a ngai ang. Chumi hnuah harsatna a awm loh chuan kum khatah vawi khat emaw kum hnih danah emaw check-up neih a ngai dawn a ni. I doctor chuan eng chen nge i lo kal tur tih a rel ang a, i dinhmun a zirin.
Hetiang dinhmun hi eng nge ka beisei theih ang? (Prognosis) tih a ni.
Desmoid tumor hi mi zawng zawng tan a inang vek lo. Mi thenkhat chuan nei mahse symptom an nei lo. Mi sawm zinga pahnih velin an nei a, enkawl ngai lovin an kal bo thin. Mahse, mi dangte tan chuan an thang lian thei a, hriselna atana hlauhawm an ni thei bawk.
Tumor-a genetic mutation awm dan azirin doctor-te chuan tumor chu engtiang chiahin nge a nasat dawn tih leh enkawl hnua a lo kir leh theihna tur chungchangah rinhlelhna engemaw zat an siam thei a ni. Mahse engmah sawi chian theih a ni lo.
Cancer ni lo mahse, chu chu nghah mai tur tihna a ni lo. Desmoid tumor hi natna khirh tak a ni a, doctor-in a enfiah tur a ni.
Engtin nge damchhuahna rate hi a awm? (Dam damchhuah zat) 1.1.
Desmoid tumor hi nunna atana hlauhawm a ni tlangpui lo a, mahse i enkawl chhunzawm zel theih nan harsatna a ni thei.
Hetah hian a pawimawh ber chu recurrence-free survival rate (`recurrence-free survival rate`) hi a ni. Kum nga hnuah chuan he rate hi 23% atanga 65% thleng a ni thei. Hei hi tumor-a genetic mutation awm danah a innghat nasa hle.
I doctor chuan i diagnosis a zirin i beisei theih turte a hrilhfiah ang che.
A pawimawh ber chu: mithiamte puihna
Desmoid tumor hi sawi lawk theih loh khawpin a awm thei. Natna an thlen thei a, chetna a tikhawtlai thei a, a bul hnaia taksa peng hrang hrangte pawh a nghawng thei bawk. He rinhlelhna hian a ti buai hle thei a ni. Tumor thenkhat chu a thang zawi a, enkawl vat a ngai lo mai thei a, mahse thenkhat erawh chu uluk taka enkawl a ngai thung.
Desmoid cyst hi thil awm lo tak a nih avangin mi tin a nghawng dan a inang lo a, chuvangin heng natna khirh tak tak enkawlna lama tawnhriat nei specialist team hnen atanga enkawlna lak a pawimawh hle. Multidisciplinary approach hian symptoms enkawlna leh nunphung tihchangtlunna hun tha ber a pe a ni.
Hemi atanga kan zir tur (Take-Home Message) .
Okay, chuvangin, kan sawi tawh atang hian thil pawimawh tlemte i hriat reng tur a awm:
- Desmoid tumor hi cancer ni lo mahse, ngaihthah tur a ni lo.
- I taksaah lump emaw swelling danglam tak i neih chuan, a bik takin a lo thang chhunzawm zel emaw, a na emaw a nih chuan hun khawhral suh la, doctor pan nghal rawh.
- He natna hi a buaithlak deuh thei a, chuvangin diagnosis dik tak neih leh medical team tawnhriat ngah tak takte puihna chuan he natna hi hlawhtling taka nunpui kawngah nasa takin a pui ang che.
- Hlauthawng suh, fimkhur zawk rawh. A pawimawh ber chu damdawi lam thurawn mumal tak zawm hi a ni.
Hemi chungchanga zawhna dang i neih chuan i doctor nen inbia ngei ang che. Hrisel takin awm rawh!
` Desmoid tumor, aggressive fibromatosis, connective tissue tumor, cancer ni lo tumor, tumor symptoms, tumor enkawlna, Sri Lanka Health











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